'en:bilateral hypoplastic cochlea'
(id=6814458 ; fe=en:bilateral hypoplastic cochlea ; type=1 ; niveau=200 ; luminosité=25 ; somme entrante=27144 creation date=2017-06-25 touchdate=2025-12-23 11:10:49.000)

≈ 680 relations sortantes en:bilateral hypoplastic cochlea -- r_associated #0: 43 / 1 -> en:abnormal helices, antihelices and lobules n1=en:bilateral hypoplastic cochlea | n2=en:abnormal helices, antihelices and lobules | rel=r_associated | relid=0 | w=43 en:bilateral hypoplastic cochlea -- r_associated #0: 42 / 0.977 -> en:presbycusis n1=en:bilateral hypoplastic cochlea | n2=en:presbycusis | rel=r_associated | relid=0 | w=42 en:bilateral hypoplastic cochlea -- r_associated #0: 41 / 0.953 -> en:abnormal middle ear reflexes n1=en:bilateral hypoplastic cochlea | n2=en:abnormal middle ear reflexes | rel=r_associated | relid=0 | w=41 en:bilateral hypoplastic cochlea -- r_associated #0: 41 / 0.953 -> en:absent earlobe n1=en:bilateral hypoplastic cochlea | n2=en:absent earlobe | rel=r_associated | relid=0 | w=41 en:bilateral hypoplastic cochlea -- r_associated #0: 40 / 0.93 -> en:absence of vestibular evoked myogenic potentials (rare) n1=en:bilateral hypoplastic cochlea | n2=en:absence of vestibular evoked myogenic potentials (rare) | rel=r_associated | relid=0 | w=40 en:bilateral hypoplastic cochlea -- r_associated #0: 37 / 0.86 -> en:bilateral sensorineural hearing loss (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:bilateral sensorineural hearing loss (in some patients) | rel=r_associated | relid=0 | w=37 en:bilateral hypoplastic cochlea -- r_associated #0: 35 / 0.814 -> en:abnormally folded ears n1=en:bilateral hypoplastic cochlea | n2=en:abnormally folded ears | rel=r_associated | relid=0 | w=35 en:bilateral hypoplastic cochlea -- r_associated #0: 35 / 0.814 -> en:absent cochlear microphonic (in older patients) n1=en:bilateral hypoplastic cochlea | n2=en:absent cochlear microphonic (in older patients) | rel=r_associated | relid=0 | w=35 en:bilateral hypoplastic cochlea -- r_associated #0: 35 / 0.814 -> en:absent external auditory meatus n1=en:bilateral hypoplastic cochlea | n2=en:absent external auditory meatus | rel=r_associated | relid=0 | w=35 en:bilateral hypoplastic cochlea -- r_associated #0: 35 / 0.814 -> en:air-bone gap of greater than 20 db across 0.5 to 2 khz n1=en:bilateral hypoplastic cochlea | n2=en:air-bone gap of greater than 20 db across 0.5 to 2 khz | rel=r_associated | relid=0 | w=35 en:bilateral hypoplastic cochlea -- r_associated #0: 35 / 0.814 -> en:anteverted ears n1=en:bilateral hypoplastic cochlea | n2=en:anteverted ears | rel=r_associated | relid=0 | w=35 en:bilateral hypoplastic cochlea -- r_associated #0: 35 / 0.814 -> en:atretic auditory canal n1=en:bilateral hypoplastic cochlea | n2=en:atretic auditory canal | rel=r_associated | relid=0 | w=35 en:bilateral hypoplastic cochlea -- r_associated #0: 35 / 0.814 -> en:atrophy of cochlear and vestibular fibrocytes n1=en:bilateral hypoplastic cochlea | n2=en:atrophy of cochlear and vestibular fibrocytes | rel=r_associated | relid=0 | w=35 en:bilateral hypoplastic cochlea -- r_associated #0: 35 / 0.814 -> en:bat ear n1=en:bilateral hypoplastic cochlea | n2=en:bat ear | rel=r_associated | relid=0 | w=35 en:bilateral hypoplastic cochlea -- r_associated #0: 35 / 0.814 -> en:chronic otitis media n1=en:bilateral hypoplastic cochlea | n2=en:chronic otitis media | rel=r_associated | relid=0 | w=35 en:bilateral hypoplastic cochlea -- r_associated #0: 35 / 0.814 -> en:chronic otitis other infection ear n1=en:bilateral hypoplastic cochlea | n2=en:chronic otitis other infection ear | rel=r_associated | relid=0 | w=35 en:bilateral hypoplastic cochlea -- r_associated #0: 35 / 0.814 -> en:cochlear malformation defect (mondini dysplasia) (less common) n1=en:bilateral hypoplastic cochlea | n2=en:cochlear malformation defect (mondini dysplasia) (less common) | rel=r_associated | relid=0 | w=35 en:bilateral hypoplastic cochlea -- r_associated #0: 35 / 0.814 -> en:cup-shaped ears (30-60% of patients) n1=en:bilateral hypoplastic cochlea | n2=en:cup-shaped ears (30-60% of patients) | rel=r_associated | relid=0 | w=35 en:bilateral hypoplastic cochlea -- r_associated #0: 35 / 0.814 -> en:deafness, bilateral sensorineural, high frequency (100% of patients) n1=en:bilateral hypoplastic cochlea | n2=en:deafness, bilateral sensorineural, high frequency (100% of patients) | rel=r_associated | relid=0 | w=35 en:bilateral hypoplastic cochlea -- r_associated #0: 35 / 0.814 -> en:deafness, early-onset n1=en:bilateral hypoplastic cochlea | n2=en:deafness, early-onset | rel=r_associated | relid=0 | w=35 en:bilateral hypoplastic cochlea -- r_associated #0: 34 / 0.791 -> en:abnormal ears n1=en:bilateral hypoplastic cochlea | n2=en:abnormal ears | rel=r_associated | relid=0 | w=34 en:bilateral hypoplastic cochlea -- r_associated #0: 34 / 0.791 -> en:affects all frequencies n1=en:bilateral hypoplastic cochlea | n2=en:affects all frequencies | rel=r_associated | relid=0 | w=34 en:bilateral hypoplastic cochlea -- r_associated #0: 34 / 0.791 -> en:anomalous middle ear bones n1=en:bilateral hypoplastic cochlea | n2=en:anomalous middle ear bones | rel=r_associated | relid=0 | w=34 en:bilateral hypoplastic cochlea -- r_associated #0: 34 / 0.791 -> en:cauliflower ear deformity (rare) n1=en:bilateral hypoplastic cochlea | n2=en:cauliflower ear deformity (rare) | rel=r_associated | relid=0 | w=34 en:bilateral hypoplastic cochlea -- r_associated #0: 34 / 0.791 -> en:congenital ear anomaly nos (disorder) n1=en:bilateral hypoplastic cochlea | n2=en:congenital ear anomaly nos (disorder) | rel=r_associated | relid=0 | w=34 en:bilateral hypoplastic cochlea -- r_associated #0: 34 / 0.791 -> en:deafness, conductive (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:deafness, conductive (in some patients) | rel=r_associated | relid=0 | w=34 en:bilateral hypoplastic cochlea -- r_associated #0: 34 / 0.791 -> en:inner ear n1=en:bilateral hypoplastic cochlea | n2=en:inner ear | rel=r_associated | relid=0 | w=34 en:bilateral hypoplastic cochlea -- r_associated #0: 34 / 0.791 -> en:middle ear n1=en:bilateral hypoplastic cochlea | n2=en:middle ear | rel=r_associated | relid=0 | w=34 en:bilateral hypoplastic cochlea -- r_associated #0: 34 / 0.791 -> en:other symptom/complaint of ear n1=en:bilateral hypoplastic cochlea | n2=en:other symptom/complaint of ear | rel=r_associated | relid=0 | w=34 en:bilateral hypoplastic cochlea -- r_associated #0: 32 / 0.744 -> en:'tilted' ears n1=en:bilateral hypoplastic cochlea | n2=en:'tilted' ears | rel=r_associated | relid=0 | w=32 en:bilateral hypoplastic cochlea -- r_associated #0: 32 / 0.744 -> en:abnormal semicircular canals n1=en:bilateral hypoplastic cochlea | n2=en:abnormal semicircular canals | rel=r_associated | relid=0 | w=32 en:bilateral hypoplastic cochlea -- r_associated #0: 32 / 0.744 -> en:abnormality of the middle ear n1=en:bilateral hypoplastic cochlea | n2=en:abnormality of the middle ear | rel=r_associated | relid=0 | w=32 en:bilateral hypoplastic cochlea -- r_associated #0: 32 / 0.744 -> en:absence of acoustic reflex n1=en:bilateral hypoplastic cochlea | n2=en:absence of acoustic reflex | rel=r_associated | relid=0 | w=32 en:bilateral hypoplastic cochlea -- r_associated #0: 32 / 0.744 -> en:acute otitis media/myringitis n1=en:bilateral hypoplastic cochlea | n2=en:acute otitis media/myringitis | rel=r_associated | relid=0 | w=32 en:bilateral hypoplastic cochlea -- r_associated #0: 32 / 0.744 -> en:auditory neuropathy spectrum disorder n1=en:bilateral hypoplastic cochlea | n2=en:auditory neuropathy spectrum disorder | rel=r_associated | relid=0 | w=32 en:bilateral hypoplastic cochlea -- r_associated #0: 32 / 0.744 -> en:auriculo-condylar syndrome n1=en:bilateral hypoplastic cochlea | n2=en:auriculo-condylar syndrome | rel=r_associated | relid=0 | w=32 en:bilateral hypoplastic cochlea -- r_associated #0: 32 / 0.744 -> en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion n1=en:bilateral hypoplastic cochlea | n2=en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion | rel=r_associated | relid=0 | w=32 en:bilateral hypoplastic cochlea -- r_associated #0: 32 / 0.744 -> en:conductive hearing loss (in a subset of patients) n1=en:bilateral hypoplastic cochlea | n2=en:conductive hearing loss (in a subset of patients) | rel=r_associated | relid=0 | w=32 en:bilateral hypoplastic cochlea -- r_associated #0: 32 / 0.744 -> en:deafness, postlingual n1=en:bilateral hypoplastic cochlea | n2=en:deafness, postlingual | rel=r_associated | relid=0 | w=32 en:bilateral hypoplastic cochlea -- r_associated #0: 32 / 0.744 -> en:hearing complaints (excluding h84-86) n1=en:bilateral hypoplastic cochlea | n2=en:hearing complaints (excluding h84-86) | rel=r_associated | relid=0 | w=32 en:bilateral hypoplastic cochlea -- r_associated #0: 32 / 0.744 -> en:sensation of blocked ears n1=en:bilateral hypoplastic cochlea | n2=en:sensation of blocked ears | rel=r_associated | relid=0 | w=32 en:bilateral hypoplastic cochlea -- r_associated #0: 31 / 0.721 -> en:abnormality of the outer ear n1=en:bilateral hypoplastic cochlea | n2=en:abnormality of the outer ear | rel=r_associated | relid=0 | w=31 en:bilateral hypoplastic cochlea -- r_associated #0: 31 / 0.721 -> en:abnormally formed ears n1=en:bilateral hypoplastic cochlea | n2=en:abnormally formed ears | rel=r_associated | relid=0 | w=31 en:bilateral hypoplastic cochlea -- r_associated #0: 31 / 0.721 -> en:absent brainstem auditory-evoked responses n1=en:bilateral hypoplastic cochlea | n2=en:absent brainstem auditory-evoked responses | rel=r_associated | relid=0 | w=31 en:bilateral hypoplastic cochlea -- r_associated #0: 31 / 0.721 -> en:asymmetry of the ears n1=en:bilateral hypoplastic cochlea | n2=en:asymmetry of the ears | rel=r_associated | relid=0 | w=31 en:bilateral hypoplastic cochlea -- r_associated #0: 31 / 0.721 -> en:congenital hearing loss (1 family) n1=en:bilateral hypoplastic cochlea | n2=en:congenital hearing loss (1 family) | rel=r_associated | relid=0 | w=31 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:abnormal amplitude modulation detection n1=en:bilateral hypoplastic cochlea | n2=en:abnormal amplitude modulation detection | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:abnormal auricles n1=en:bilateral hypoplastic cochlea | n2=en:abnormal auricles | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:absent or abnormal otoacoustic emissions n1=en:bilateral hypoplastic cochlea | n2=en:absent or abnormal otoacoustic emissions | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient) n1=en:bilateral hypoplastic cochlea | n2=en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient) | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:audiogram may be ascending n1=en:bilateral hypoplastic cochlea | n2=en:audiogram may be ascending | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:auditory impairment n1=en:bilateral hypoplastic cochlea | n2=en:auditory impairment | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:bilateral dys-synchronized auditory brainstem responses n1=en:bilateral hypoplastic cochlea | n2=en:bilateral dys-synchronized auditory brainstem responses | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:chronic otitis n1=en:bilateral hypoplastic cochlea | n2=en:chronic otitis | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:conductive hearing loss (30% of patients) n1=en:bilateral hypoplastic cochlea | n2=en:conductive hearing loss (30% of patients) | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:conductive hearing loss to due otitis media n1=en:bilateral hypoplastic cochlea | n2=en:conductive hearing loss to due otitis media | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:cystic dilatation of cochlea and vestibulum n1=en:bilateral hypoplastic cochlea | n2=en:cystic dilatation of cochlea and vestibulum | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:deafness (variable) n1=en:bilateral hypoplastic cochlea | n2=en:deafness (variable) | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:deafness affects all frequencies n1=en:bilateral hypoplastic cochlea | n2=en:deafness affects all frequencies | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:deafness, profound, by 6th decade n1=en:bilateral hypoplastic cochlea | n2=en:deafness, profound, by 6th decade | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:deafness, sensorineural, profound (prelingual onset) n1=en:bilateral hypoplastic cochlea | n2=en:deafness, sensorineural, profound (prelingual onset) | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:deafness, unilateral, childhood onset n1=en:bilateral hypoplastic cochlea | n2=en:deafness, unilateral, childhood onset | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:decreased auditory brainstem responses n1=en:bilateral hypoplastic cochlea | n2=en:decreased auditory brainstem responses | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation n1=en:bilateral hypoplastic cochlea | n2=en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:deficient auricle n1=en:bilateral hypoplastic cochlea | n2=en:deficient auricle | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:endolymphatic hydrops, delayed onset n1=en:bilateral hypoplastic cochlea | n2=en:endolymphatic hydrops, delayed onset | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:excessive cerumen n1=en:bilateral hypoplastic cochlea | n2=en:excessive cerumen | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:first branchial arch anomalies n1=en:bilateral hypoplastic cochlea | n2=en:first branchial arch anomalies | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:hearing deficits (28% of adults) n1=en:bilateral hypoplastic cochlea | n2=en:hearing deficits (28% of adults) | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:hearing disorder (1 patient) n1=en:bilateral hypoplastic cochlea | n2=en:hearing disorder (1 patient) | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:hearing impairment (in 1/4 patients) n1=en:bilateral hypoplastic cochlea | n2=en:hearing impairment (in 1/4 patients) | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:hearing loss, postlingual sensorineural n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, postlingual sensorineural | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:hearing loss, progressive sensorineural, affecting high frequencies n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, progressive sensorineural, affecting high frequencies | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:hearing loss, sensorineural (in one family) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural (in one family) | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:hearing loss, unilateral, mild n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, unilateral, mild | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:impaired tympanic membrane mobility n1=en:bilateral hypoplastic cochlea | n2=en:impaired tympanic membrane mobility | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:large anteverted pinnae (90% males, 40% females) n1=en:bilateral hypoplastic cochlea | n2=en:large anteverted pinnae (90% males, 40% females) | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:large auricle n1=en:bilateral hypoplastic cochlea | n2=en:large auricle | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:large, floppy ears n1=en:bilateral hypoplastic cochlea | n2=en:large, floppy ears | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:long, lobulated ears n1=en:bilateral hypoplastic cochlea | n2=en:long, lobulated ears | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:loss of outer hair cell function n1=en:bilateral hypoplastic cochlea | n2=en:loss of outer hair cell function | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:low-set and rotated ears n1=en:bilateral hypoplastic cochlea | n2=en:low-set and rotated ears | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:low-set ears (1 patient) n1=en:bilateral hypoplastic cochlea | n2=en:low-set ears (1 patient) | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:misshapen ear n1=en:bilateral hypoplastic cochlea | n2=en:misshapen ear | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:morphological abnormality of the middle ear n1=en:bilateral hypoplastic cochlea | n2=en:morphological abnormality of the middle ear | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:neonatal cystic lesions of the pinnae n1=en:bilateral hypoplastic cochlea | n2=en:neonatal cystic lesions of the pinnae | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:normal otoacoustic emissions (oae), indicating intact outer ear hair cell function n1=en:bilateral hypoplastic cochlea | n2=en:normal otoacoustic emissions (oae), indicating intact outer ear hair cell function | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:ossified pinnae n1=en:bilateral hypoplastic cochlea | n2=en:ossified pinnae | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:otitis externa, recurrent, due to infection with staphylococcus aureus n1=en:bilateral hypoplastic cochlea | n2=en:otitis externa, recurrent, due to infection with staphylococcus aureus | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:pinna modeling anomalies n1=en:bilateral hypoplastic cochlea | n2=en:pinna modeling anomalies | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:posteriorly rotated ears (female) n1=en:bilateral hypoplastic cochlea | n2=en:posteriorly rotated ears (female) | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:profound deafness n1=en:bilateral hypoplastic cochlea | n2=en:profound deafness | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:prolonged brainstem auditory evoked potentials (baep) n1=en:bilateral hypoplastic cochlea | n2=en:prolonged brainstem auditory evoked potentials (baep) | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:prominence and protrusion of upper third of the ear n1=en:bilateral hypoplastic cochlea | n2=en:prominence and protrusion of upper third of the ear | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:prominent ears (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:prominent ears (in some patients) | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:protruding ears (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:protruding ears (in some patients) | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:protruding right ear n1=en:bilateral hypoplastic cochlea | n2=en:protruding right ear | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:protruding, simple ears n1=en:bilateral hypoplastic cochlea | n2=en:protruding, simple ears | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:raised earlobes n1=en:bilateral hypoplastic cochlea | n2=en:raised earlobes | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:recurrent otitis media in infancy and childhood n1=en:bilateral hypoplastic cochlea | n2=en:recurrent otitis media in infancy and childhood | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:retinitis (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:retinitis (in some patients) | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:secretory otitis media n1=en:bilateral hypoplastic cochlea | n2=en:secretory otitis media | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:sensorineural hearing loss n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural hearing loss | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:sensorineural hearing loss (1 patient) n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural hearing loss (1 patient) | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:sensorineural hearing loss (20% of patients) n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural hearing loss (20% of patients) | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:sensorineural hearing loss has been reported n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural hearing loss has been reported | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:sensorineural hearing loss, mild to moderate n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural hearing loss, mild to moderate | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:sensorineural, conductive, or mixed hearing loss n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural, conductive, or mixed hearing loss | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:small external auditory meatus n1=en:bilateral hypoplastic cochlea | n2=en:small external auditory meatus | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:small pinna n1=en:bilateral hypoplastic cochlea | n2=en:small pinna | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:small pits anterior to the helix (1 patient) n1=en:bilateral hypoplastic cochlea | n2=en:small pits anterior to the helix (1 patient) | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:squared-off ears n1=en:bilateral hypoplastic cochlea | n2=en:squared-off ears | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:stapes fixation n1=en:bilateral hypoplastic cochlea | n2=en:stapes fixation | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:thickened lobes n1=en:bilateral hypoplastic cochlea | n2=en:thickened lobes | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:tinnitus n1=en:bilateral hypoplastic cochlea | n2=en:tinnitus | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:tinnitus (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:tinnitus (in some patients) | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:unconnected or fused stapes and incus n1=en:bilateral hypoplastic cochlea | n2=en:unconnected or fused stapes and incus | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:vestibular areflexia n1=en:bilateral hypoplastic cochlea | n2=en:vestibular areflexia | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:vestibular hypofunction (rare) n1=en:bilateral hypoplastic cochlea | n2=en:vestibular hypofunction (rare) | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 30 / 0.698 -> en:wide bulbous internal auditory meatus n1=en:bilateral hypoplastic cochlea | n2=en:wide bulbous internal auditory meatus | rel=r_associated | relid=0 | w=30 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:abnormal auditory brainstem responses n1=en:bilateral hypoplastic cochlea | n2=en:abnormal auditory brainstem responses | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:abnormal brainstem auditory evoked potentials (baep) n1=en:bilateral hypoplastic cochlea | n2=en:abnormal brainstem auditory evoked potentials (baep) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:abnormal gap detection n1=en:bilateral hypoplastic cochlea | n2=en:abnormal gap detection | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:anteverted pinnae n1=en:bilateral hypoplastic cochlea | n2=en:anteverted pinnae | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:atretic ear canals n1=en:bilateral hypoplastic cochlea | n2=en:atretic ear canals | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:aural fullness n1=en:bilateral hypoplastic cochlea | n2=en:aural fullness | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:cleft at the superior portion of the pinna n1=en:bilateral hypoplastic cochlea | n2=en:cleft at the superior portion of the pinna | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:cochlear degeneration n1=en:bilateral hypoplastic cochlea | n2=en:cochlear degeneration | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:congenital deafness n1=en:bilateral hypoplastic cochlea | n2=en:congenital deafness | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:deafness due to bilateral cochlear malformation (rare) n1=en:bilateral hypoplastic cochlea | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:deafness, prelingual, profound (affects all frequencies) n1=en:bilateral hypoplastic cochlea | n2=en:deafness, prelingual, profound (affects all frequencies) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:deafness, sensorineural (severe to profound) n1=en:bilateral hypoplastic cochlea | n2=en:deafness, sensorineural (severe to profound) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:deafness, sensorineural, mild (rare) n1=en:bilateral hypoplastic cochlea | n2=en:deafness, sensorineural, mild (rare) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v n1=en:bilateral hypoplastic cochlea | n2=en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:dorsally rotated ears n1=en:bilateral hypoplastic cochlea | n2=en:dorsally rotated ears | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:dysplastic ears (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:dysplastic ears (in some patients) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:everted ears n1=en:bilateral hypoplastic cochlea | n2=en:everted ears | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:external ear n1=en:bilateral hypoplastic cochlea | n2=en:external ear | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:hearing loss (uncommon) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss (uncommon) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:hearing loss (variable) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss (variable) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:hearing loss, bilateral sensorineural (profound) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, bilateral sensorineural (profound) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:hearing loss, congenital sensorineural, moderate-severe n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, congenital sensorineural, moderate-severe | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:hearing loss, congenital, profound (250-8,000 hz) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, congenital, profound (250-8,000 hz) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:hearing loss, sensorineural (in sister) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural (in sister) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:hearing loss, sensorineural (reported in 1 patient) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural (reported in 1 patient) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:hearing loss, sensorineural and conductive, severe to profound n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural and conductive, severe to profound | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:high-tone sensorineural deafness (67% of patients) n1=en:bilateral hypoplastic cochlea | n2=en:high-tone sensorineural deafness (67% of patients) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:hypoacusia (1 patient) n1=en:bilateral hypoplastic cochlea | n2=en:hypoacusia (1 patient) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients) n1=en:bilateral hypoplastic cochlea | n2=en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:large anteverted ears (rare) n1=en:bilateral hypoplastic cochlea | n2=en:large anteverted ears (rare) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:large ear pinnae n1=en:bilateral hypoplastic cochlea | n2=en:large ear pinnae | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:large ears (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:large ears (in some patients) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:large simple ears n1=en:bilateral hypoplastic cochlea | n2=en:large simple ears | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:large, low-set ears n1=en:bilateral hypoplastic cochlea | n2=en:large, low-set ears | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:left ear n1=en:bilateral hypoplastic cochlea | n2=en:left ear | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:lobular aplasia n1=en:bilateral hypoplastic cochlea | n2=en:lobular aplasia | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:loss of high frequencies at onset n1=en:bilateral hypoplastic cochlea | n2=en:loss of high frequencies at onset | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:low-frequency conductive hearing loss n1=en:bilateral hypoplastic cochlea | n2=en:low-frequency conductive hearing loss | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:low-set ears (3 patients) n1=en:bilateral hypoplastic cochlea | n2=en:low-set ears (3 patients) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:malformed pinnae (30-60% of patients) n1=en:bilateral hypoplastic cochlea | n2=en:malformed pinnae (30-60% of patients) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:meniere disease n1=en:bilateral hypoplastic cochlea | n2=en:meniere disease | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:near-stenosis of bony portion of auditory canal n1=en:bilateral hypoplastic cochlea | n2=en:near-stenosis of bony portion of auditory canal | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:nonprogressive deafness n1=en:bilateral hypoplastic cochlea | n2=en:nonprogressive deafness | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:oae responses may decrease with age or use of hearing aids n1=en:bilateral hypoplastic cochlea | n2=en:oae responses may decrease with age or use of hearing aids | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:other auditory injuries n1=en:bilateral hypoplastic cochlea | n2=en:other auditory injuries | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:otorrhea n1=en:bilateral hypoplastic cochlea | n2=en:otorrhea | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:poorly formed pinnae n1=en:bilateral hypoplastic cochlea | n2=en:poorly formed pinnae | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:preauricular skin tags (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:preauricular skin tags (in some patients) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:prominent helices n1=en:bilateral hypoplastic cochlea | n2=en:prominent helices | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:right ear n1=en:bilateral hypoplastic cochlea | n2=en:right ear | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:rudimentary n1=en:bilateral hypoplastic cochlea | n2=en:rudimentary | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:sensorineural hearing loss (early-onset form) n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural hearing loss (early-onset form) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:severe to profound hearing impairment by early adulthood n1=en:bilateral hypoplastic cochlea | n2=en:severe to profound hearing impairment by early adulthood | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:short ear n1=en:bilateral hypoplastic cochlea | n2=en:short ear | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:small auricles n1=en:bilateral hypoplastic cochlea | n2=en:small auricles | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:small ears with large lobules n1=en:bilateral hypoplastic cochlea | n2=en:small ears with large lobules | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:structure of superior auricularis muscle n1=en:bilateral hypoplastic cochlea | n2=en:structure of superior auricularis muscle | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:supraauricular pit n1=en:bilateral hypoplastic cochlea | n2=en:supraauricular pit | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:u- or bowl-shaped audiogram n1=en:bilateral hypoplastic cochlea | n2=en:u- or bowl-shaped audiogram | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:unilateral external ear deformity n1=en:bilateral hypoplastic cochlea | n2=en:unilateral external ear deformity | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 29 / 0.674 -> en:vestibular dysfunction (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:vestibular dysfunction (in some patients) | rel=r_associated | relid=0 | w=29 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:abnormal folded pinna n1=en:bilateral hypoplastic cochlea | n2=en:abnormal folded pinna | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:abnormality of the helix n1=en:bilateral hypoplastic cochlea | n2=en:abnormality of the helix | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:absence of earlobe n1=en:bilateral hypoplastic cochlea | n2=en:absence of earlobe | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:absent ipsilateral middle ear muscle reflexes (in older patients) n1=en:bilateral hypoplastic cochlea | n2=en:absent ipsilateral middle ear muscle reflexes (in older patients) | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:affects mid- to high-frequencies n1=en:bilateral hypoplastic cochlea | n2=en:affects mid- to high-frequencies | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:anterior creases of earlobe n1=en:bilateral hypoplastic cochlea | n2=en:anterior creases of earlobe | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:anteriorly rotated ears n1=en:bilateral hypoplastic cochlea | n2=en:anteriorly rotated ears | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:audiogram is gently sloping or flat n1=en:bilateral hypoplastic cochlea | n2=en:audiogram is gently sloping or flat | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:auricular clefts n1=en:bilateral hypoplastic cochlea | n2=en:auricular clefts | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:congenital absence of external ear n1=en:bilateral hypoplastic cochlea | n2=en:congenital absence of external ear | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:crumpled ear (76%) n1=en:bilateral hypoplastic cochlea | n2=en:crumpled ear (76%) | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:cupped pinna n1=en:bilateral hypoplastic cochlea | n2=en:cupped pinna | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:deafness (in 1 of 2 families) n1=en:bilateral hypoplastic cochlea | n2=en:deafness (in 1 of 2 families) | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:deafness in 30-50% of patients with skull involvement n1=en:bilateral hypoplastic cochlea | n2=en:deafness in 30-50% of patients with skull involvement | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:deafness, congenital sensorineural, profound (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:deafness, congenital sensorineural, profound (in some patients) | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:deafness, moderate-severe (onset in third decade) n1=en:bilateral hypoplastic cochlea | n2=en:deafness, moderate-severe (onset in third decade) | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:deafness, sensorineural, prelingual, profound n1=en:bilateral hypoplastic cochlea | n2=en:deafness, sensorineural, prelingual, profound | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:dilatated internal auditory canal n1=en:bilateral hypoplastic cochlea | n2=en:dilatated internal auditory canal | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:disproportionately large ears n1=en:bilateral hypoplastic cochlea | n2=en:disproportionately large ears | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:downward sloping audiogram n1=en:bilateral hypoplastic cochlea | n2=en:downward sloping audiogram | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:ear neoplasm n1=en:bilateral hypoplastic cochlea | n2=en:ear neoplasm | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:external ears rudimentary n1=en:bilateral hypoplastic cochlea | n2=en:external ears rudimentary | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:fear of ear disease n1=en:bilateral hypoplastic cochlea | n2=en:fear of ear disease | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:folded superior edge of helix n1=en:bilateral hypoplastic cochlea | n2=en:folded superior edge of helix | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:hearing impairment (rare) n1=en:bilateral hypoplastic cochlea | n2=en:hearing impairment (rare) | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:hearing loss affects all frequencies n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss affects all frequencies | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:hearing loss, neural type n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, neural type | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:hearing loss, sensorineural, due to auditory neuropathy n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural, due to auditory neuropathy | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:hearing loss, sensorineural, prelingual n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural, prelingual | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:hearing loss, unilateral (rare) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, unilateral (rare) | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:hearing normal n1=en:bilateral hypoplastic cochlea | n2=en:hearing normal | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:hearing threshold at or above 90 db at all frequencies tested (0.25-8.0 khz) n1=en:bilateral hypoplastic cochlea | n2=en:hearing threshold at or above 90 db at all frequencies tested (0.25-8.0 khz) | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:high-frequency tinnitus at onset n1=en:bilateral hypoplastic cochlea | n2=en:high-frequency tinnitus at onset | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:hyperfolded ears n1=en:bilateral hypoplastic cochlea | n2=en:hyperfolded ears | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:hypoplasia of the upper part of the helix n1=en:bilateral hypoplastic cochlea | n2=en:hypoplasia of the upper part of the helix | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:increased posterior angulation n1=en:bilateral hypoplastic cochlea | n2=en:increased posterior angulation | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:inferior displacement of the ears n1=en:bilateral hypoplastic cochlea | n2=en:inferior displacement of the ears | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:large earlobe n1=en:bilateral hypoplastic cochlea | n2=en:large earlobe | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:large prominent ears n1=en:bilateral hypoplastic cochlea | n2=en:large prominent ears | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:low-set ears (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:low-set ears (in some patients) | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:low-set, malformed ears n1=en:bilateral hypoplastic cochlea | n2=en:low-set, malformed ears | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:mild cochlear hearing loss (1 patient) n1=en:bilateral hypoplastic cochlea | n2=en:mild cochlear hearing loss (1 patient) | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:mild hearing impairment (13%) n1=en:bilateral hypoplastic cochlea | n2=en:mild hearing impairment (13%) | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:minor auricular anomalies n1=en:bilateral hypoplastic cochlea | n2=en:minor auricular anomalies | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:minor ear anomalies (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:minor ear anomalies (in some patients) | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:mondini defect n1=en:bilateral hypoplastic cochlea | n2=en:mondini defect | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:otoneurologic disturbances n1=en:bilateral hypoplastic cochlea | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:outer ear abnormalities (deletion patients) prominent ears n1=en:bilateral hypoplastic cochlea | n2=en:outer ear abnormalities (deletion patients) prominent ears | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:poorly formed ears n1=en:bilateral hypoplastic cochlea | n2=en:poorly formed ears | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:posterior helical indentations n1=en:bilateral hypoplastic cochlea | n2=en:posterior helical indentations | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:preauricular pits (70-80% of patients) n1=en:bilateral hypoplastic cochlea | n2=en:preauricular pits (70-80% of patients) | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face) n1=en:bilateral hypoplastic cochlea | n2=en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face) | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:progressive hearing impairment n1=en:bilateral hypoplastic cochlea | n2=en:progressive hearing impairment | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:prominent antitragus n1=en:bilateral hypoplastic cochlea | n2=en:prominent antitragus | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:prominent antitragus (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:prominent antitragus (in some patients) | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:recurrent otitis media (18%) n1=en:bilateral hypoplastic cochlea | n2=en:recurrent otitis media (18%) | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:rotated ears n1=en:bilateral hypoplastic cochlea | n2=en:rotated ears | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:sensorineural deafness, postlingual, progressive n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural deafness, postlingual, progressive | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:sensorineural hearing loss (3 patients) n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural hearing loss (3 patients) | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:sensorineural hearing loss (less common) n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural hearing loss (less common) | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:sensorineural hearing loss, mild (rare) n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural hearing loss, mild (rare) | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:severe narrowing of cartilagenous auditory canal n1=en:bilateral hypoplastic cochlea | n2=en:severe narrowing of cartilagenous auditory canal | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:small cavum conchae n1=en:bilateral hypoplastic cochlea | n2=en:small cavum conchae | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:soft auricles n1=en:bilateral hypoplastic cochlea | n2=en:soft auricles | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:squared-off superior helices n1=en:bilateral hypoplastic cochlea | n2=en:squared-off superior helices | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:stenotic ear canals (30%) n1=en:bilateral hypoplastic cochlea | n2=en:stenotic ear canals (30%) | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:symmetric deterioration of hearing loss and speech reception with age n1=en:bilateral hypoplastic cochlea | n2=en:symmetric deterioration of hearing loss and speech reception with age | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:tinnitus (variable) n1=en:bilateral hypoplastic cochlea | n2=en:tinnitus (variable) | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> en:vestibular involvement (variable) n1=en:bilateral hypoplastic cochlea | n2=en:vestibular involvement (variable) | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 28 / 0.651 -> lésion traumatique superficielle de l'oreille n1=en:bilateral hypoplastic cochlea | n2=lésion traumatique superficielle de l'oreille | rel=r_associated | relid=0 | w=28 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:abnormal auditory temporal processes n1=en:bilateral hypoplastic cochlea | n2=en:abnormal auditory temporal processes | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:abnormal brain auditory evoked responses (baer) n1=en:bilateral hypoplastic cochlea | n2=en:abnormal brain auditory evoked responses (baer) | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:abnormal or absent auditory nerve and brainstem responses n1=en:bilateral hypoplastic cochlea | n2=en:abnormal or absent auditory nerve and brainstem responses | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:absent auditory canals (wws) n1=en:bilateral hypoplastic cochlea | n2=en:absent auditory canals (wws) | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:absent lobules n1=en:bilateral hypoplastic cochlea | n2=en:absent lobules | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:apical cartilage deformity n1=en:bilateral hypoplastic cochlea | n2=en:apical cartilage deformity | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:aplasia of the inner ear n1=en:bilateral hypoplastic cochlea | n2=en:aplasia of the inner ear | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:approximately 0.7db per year hearing loss at all frequencies n1=en:bilateral hypoplastic cochlea | n2=en:approximately 0.7db per year hearing loss at all frequencies | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:atresia of the external auditory canal n1=en:bilateral hypoplastic cochlea | n2=en:atresia of the external auditory canal | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:attached ear lobes n1=en:bilateral hypoplastic cochlea | n2=en:attached ear lobes | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:complete bony atresia of medial portion of external auditory canal (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:complete bony atresia of medial portion of external auditory canal (in some patients) | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:conductive hearing loss, mild bilateral (rare) n1=en:bilateral hypoplastic cochlea | n2=en:conductive hearing loss, mild bilateral (rare) | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:congenital sensorineural hearing loss n1=en:bilateral hypoplastic cochlea | n2=en:congenital sensorineural hearing loss | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:cupped ears (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:cupped ears (in some patients) | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:deafness (often in third decade) n1=en:bilateral hypoplastic cochlea | n2=en:deafness (often in third decade) | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:deafness, congenital sensorineural, severe to profound n1=en:bilateral hypoplastic cochlea | n2=en:deafness, congenital sensorineural, severe to profound | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:decreased otoacoustic emission amplitude n1=en:bilateral hypoplastic cochlea | n2=en:decreased otoacoustic emission amplitude | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:deep-set ears n1=en:bilateral hypoplastic cochlea | n2=en:deep-set ears | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:disjunction of otherwise normal lobule from remainder of ear n1=en:bilateral hypoplastic cochlea | n2=en:disjunction of otherwise normal lobule from remainder of ear | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:downsloping audiogram n1=en:bilateral hypoplastic cochlea | n2=en:downsloping audiogram | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:eustachian tube salpingitis n1=en:bilateral hypoplastic cochlea | n2=en:eustachian tube salpingitis | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:flattened antihelix n1=en:bilateral hypoplastic cochlea | n2=en:flattened antihelix | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:hearing impairment may occur n1=en:bilateral hypoplastic cochlea | n2=en:hearing impairment may occur | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:hearing impairment, asymmetric (in some patients with hsan2d) n1=en:bilateral hypoplastic cochlea | n2=en:hearing impairment, asymmetric (in some patients with hsan2d) | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:hearing loss (affecting all frequencies), moderate to severe n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss (affecting all frequencies), moderate to severe | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:hearing loss (cvs+) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss (cvs+) | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:hearing loss first affects high frequencies n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss first affects high frequencies | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:hearing loss, bilateral progressive post-lingual n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, bilateral progressive post-lingual | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:hearing loss, high-frequency (onset in childhood-adolescence) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, high-frequency (onset in childhood-adolescence) | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:hearing loss, moderate to severe, bilateral, nonprogressive n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, moderate to severe, bilateral, nonprogressive | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:hearing loss, postlingual n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, postlingual | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:hearing loss, profound congenital sensorineural n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, profound congenital sensorineural | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:hearing loss, progressive conductive and/or sensorineural, during adulthood n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, progressive conductive and/or sensorineural, during adulthood | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies) | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:hearing loss, progressive, starting in infancy n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, progressive, starting in infancy | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:hearing loss, sensorineural (high frequency) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural (high frequency) | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:hearing loss, sensorineural (in 1 ashkenazi patient) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural (in 1 ashkenazi patient) | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:hearing loss, sensorineural (in patients with larger deletions) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural (in patients with larger deletions) | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges) | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:hearing loss, sensorineural, severe to profound n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural, severe to profound | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:hypoplastic ear lobes n1=en:bilateral hypoplastic cochlea | n2=en:hypoplastic ear lobes | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:large appearing ears n1=en:bilateral hypoplastic cochlea | n2=en:large appearing ears | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:lobule may be separately from the rest of the external ear n1=en:bilateral hypoplastic cochlea | n2=en:lobule may be separately from the rest of the external ear | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:loss of mid- and low-frequencies later n1=en:bilateral hypoplastic cochlea | n2=en:loss of mid- and low-frequencies later | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:low-set ears (rare) n1=en:bilateral hypoplastic cochlea | n2=en:low-set ears (rare) | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:low-set, posteriorly rotated ears n1=en:bilateral hypoplastic cochlea | n2=en:low-set, posteriorly rotated ears | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:malformed ossicular chain n1=en:bilateral hypoplastic cochlea | n2=en:malformed ossicular chain | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:mondini malformation n1=en:bilateral hypoplastic cochlea | n2=en:mondini malformation | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:narrow ears n1=en:bilateral hypoplastic cochlea | n2=en:narrow ears | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:no vestibular dysfunction n1=en:bilateral hypoplastic cochlea | n2=en:no vestibular dysfunction | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:normal cochlear microphonics n1=en:bilateral hypoplastic cochlea | n2=en:normal cochlear microphonics | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:normal otoacoustic emissions n1=en:bilateral hypoplastic cochlea | n2=en:normal otoacoustic emissions | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:normal vestibular response n1=en:bilateral hypoplastic cochlea | n2=en:normal vestibular response | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:posteriorly rotated ears (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:posteriorly rotated ears (in some patients) | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:prelingual onset n1=en:bilateral hypoplastic cochlea | n2=en:prelingual onset | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:progressive mixed conductive and sensorineural hearing loss n1=en:bilateral hypoplastic cochlea | n2=en:progressive mixed conductive and sensorineural hearing loss | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:prominent earlobes (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:prominent earlobes (in some patients) | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:prominent lobules n1=en:bilateral hypoplastic cochlea | n2=en:prominent lobules | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:protruding ears n1=en:bilateral hypoplastic cochlea | n2=en:protruding ears | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:protuberant ear n1=en:bilateral hypoplastic cochlea | n2=en:protuberant ear | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:sensorineural deafness (reported in 1 family) n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural deafness (reported in 1 family) | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:sensorineural deafness, progressive, late-onset n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural deafness, progressive, late-onset | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:severe to profound deafness n1=en:bilateral hypoplastic cochlea | n2=en:severe to profound deafness | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:simple helix n1=en:bilateral hypoplastic cochlea | n2=en:simple helix | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:simplified helices n1=en:bilateral hypoplastic cochlea | n2=en:simplified helices | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:superficial injury of ear n1=en:bilateral hypoplastic cochlea | n2=en:superficial injury of ear | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:thick ears n1=en:bilateral hypoplastic cochlea | n2=en:thick ears | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:thick, firm earlobes n1=en:bilateral hypoplastic cochlea | n2=en:thick, firm earlobes | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:u-shaped audiogram n1=en:bilateral hypoplastic cochlea | n2=en:u-shaped audiogram | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 27 / 0.628 -> en:vestibulopathy, bilateral, progressive n1=en:bilateral hypoplastic cochlea | n2=en:vestibulopathy, bilateral, progressive | rel=r_associated | relid=0 | w=27 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:a subset of patients have hearing loss n1=en:bilateral hypoplastic cochlea | n2=en:a subset of patients have hearing loss | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:abnormal bridge connecting the crus of the helix and antihelix n1=en:bilateral hypoplastic cochlea | n2=en:abnormal bridge connecting the crus of the helix and antihelix | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:absence of the cochlear nerves (reported in 1 patient) n1=en:bilateral hypoplastic cochlea | n2=en:absence of the cochlear nerves (reported in 1 patient) | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:absent or decreased auditory brainstem responses n1=en:bilateral hypoplastic cochlea | n2=en:absent or decreased auditory brainstem responses | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:absent stapedial reflex n1=en:bilateral hypoplastic cochlea | n2=en:absent stapedial reflex | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:absent vestibular function (caloric test) n1=en:bilateral hypoplastic cochlea | n2=en:absent vestibular function (caloric test) | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:audiogram shows sloping configuration n1=en:bilateral hypoplastic cochlea | n2=en:audiogram shows sloping configuration | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:aural atresia, congenital n1=en:bilateral hypoplastic cochlea | n2=en:aural atresia, congenital | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:bilateral congenital profound sensorineural hearing loss n1=en:bilateral hypoplastic cochlea | n2=en:bilateral congenital profound sensorineural hearing loss | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:conductive hearing loss n1=en:bilateral hypoplastic cochlea | n2=en:conductive hearing loss | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:cup-shaped auricles n1=en:bilateral hypoplastic cochlea | n2=en:cup-shaped auricles | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:deafness labyrinthine n1=en:bilateral hypoplastic cochlea | n2=en:deafness labyrinthine | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years n1=en:bilateral hypoplastic cochlea | n2=en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:deafness, early-onset mixed conductive and sensorineural n1=en:bilateral hypoplastic cochlea | n2=en:deafness, early-onset mixed conductive and sensorineural | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:deafness, profound, affects all frequencies n1=en:bilateral hypoplastic cochlea | n2=en:deafness, profound, affects all frequencies | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:dysplastic helices n1=en:bilateral hypoplastic cochlea | n2=en:dysplastic helices | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:ear n1=en:bilateral hypoplastic cochlea | n2=en:ear | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:ear tag n1=en:bilateral hypoplastic cochlea | n2=en:ear tag | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:entire ear n1=en:bilateral hypoplastic cochlea | n2=en:entire ear | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:flat audiogram n1=en:bilateral hypoplastic cochlea | n2=en:flat audiogram | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:folded helix n1=en:bilateral hypoplastic cochlea | n2=en:folded helix | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:hearing impairment (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:hearing impairment (in some patients) | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:hearing loss, conductive or mixed n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, conductive or mixed | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:hearing loss, sensorineural (in 2 patients) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural (in 2 patients) | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:hearing loss, sensorineural (type ii) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural (type ii) | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:hearing loss, sensorineural, mid-frequency (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural, mid-frequency (in some patients) | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:hearing loss, sensorineural, moderate, postlingual n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural, moderate, postlingual | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:hearing loss, severe to profound, affecting all frequencies n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, severe to profound, affecting all frequencies | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:lobule creases n1=en:bilateral hypoplastic cochlea | n2=en:lobule creases | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:long and prominent ear crus n1=en:bilateral hypoplastic cochlea | n2=en:long and prominent ear crus | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:low-set ears (in 2/4 patients) n1=en:bilateral hypoplastic cochlea | n2=en:low-set ears (in 2/4 patients) | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies n1=en:bilateral hypoplastic cochlea | n2=en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:neural hearing loss n1=en:bilateral hypoplastic cochlea | n2=en:neural hearing loss | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:overfolded, rumpled ears n1=en:bilateral hypoplastic cochlea | n2=en:overfolded, rumpled ears | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:pigmentation of the ear cartilage n1=en:bilateral hypoplastic cochlea | n2=en:pigmentation of the ear cartilage | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:pointed upper helix n1=en:bilateral hypoplastic cochlea | n2=en:pointed upper helix | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:pre- and post-auricular skin or cartilaginous tags n1=en:bilateral hypoplastic cochlea | n2=en:pre- and post-auricular skin or cartilaginous tags | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:progressive, low frequency sensorineural hearing loss n1=en:bilateral hypoplastic cochlea | n2=en:progressive, low frequency sensorineural hearing loss | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:prominent crura n1=en:bilateral hypoplastic cochlea | n2=en:prominent crura | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:protruding ears (rare) n1=en:bilateral hypoplastic cochlea | n2=en:protruding ears (rare) | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:sensorineural deafness (onset in the second decade in 25 to 30% of patients) n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural deafness (onset in the second decade in 25 to 30% of patients) | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:sensorineural hearing loss (described in 1 family) n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural hearing loss (described in 1 family) | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:small earlobe n1=en:bilateral hypoplastic cochlea | n2=en:small earlobe | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:small lobes n1=en:bilateral hypoplastic cochlea | n2=en:small lobes | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:superior semicircular canal dehiscence syndrome n1=en:bilateral hypoplastic cochlea | n2=en:superior semicircular canal dehiscence syndrome | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:tinnitus (rare) n1=en:bilateral hypoplastic cochlea | n2=en:tinnitus (rare) | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:underdeveloped tragus n1=en:bilateral hypoplastic cochlea | n2=en:underdeveloped tragus | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:vertiginous syndrome n1=en:bilateral hypoplastic cochlea | n2=en:vertiginous syndrome | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> en:vestibular function defect (decreased in some, normal in other patients) n1=en:bilateral hypoplastic cochlea | n2=en:vestibular function defect (decreased in some, normal in other patients) | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 26 / 0.605 -> surdité congénitale n1=en:bilateral hypoplastic cochlea | n2=surdité congénitale | rel=r_associated | relid=0 | w=26 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:abnormal communication between the subarachnoid space in the meatus and the perilymph n1=en:bilateral hypoplastic cochlea | n2=en:abnormal communication between the subarachnoid space in the meatus and the perilymph | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:abnormality of the pinna n1=en:bilateral hypoplastic cochlea | n2=en:abnormality of the pinna | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:absent external auditory canals n1=en:bilateral hypoplastic cochlea | n2=en:absent external auditory canals | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:bilateral n1=en:bilateral hypoplastic cochlea | n2=en:bilateral | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:deafness, sensorineural (45%) n1=en:bilateral hypoplastic cochlea | n2=en:deafness, sensorineural (45%) | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:deafness, stable bilateral symmetric prelingual n1=en:bilateral hypoplastic cochlea | n2=en:deafness, stable bilateral symmetric prelingual | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:ear pain/earache n1=en:bilateral hypoplastic cochlea | n2=en:ear pain/earache | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:ears deficient in cartilage n1=en:bilateral hypoplastic cochlea | n2=en:ears deficient in cartilage | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:hearing impairment, mild (2 patients) n1=en:bilateral hypoplastic cochlea | n2=en:hearing impairment, mild (2 patients) | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:hearing impairment, sensorineural, mild n1=en:bilateral hypoplastic cochlea | n2=en:hearing impairment, sensorineural, mild | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:hearing loss, bilateral n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, bilateral | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:hearing loss, conductive (rare) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, conductive (rare) | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:hearing loss, congenital sensorineural, severe to profound n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, congenital sensorineural, severe to profound | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:hearing loss, progressive (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, progressive (in some patients) | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:hearing loss, sensorineural (in some) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural (in some) | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:hearing loss, sensorineural (variable) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural (variable) | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:hypercompliant tympanic membranes n1=en:bilateral hypoplastic cochlea | n2=en:hypercompliant tympanic membranes | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:hypoplastic semicircular canals n1=en:bilateral hypoplastic cochlea | n2=en:hypoplastic semicircular canals | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:large ears (2p21del) n1=en:bilateral hypoplastic cochlea | n2=en:large ears (2p21del) | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:large ears (37%) n1=en:bilateral hypoplastic cochlea | n2=en:large ears (37%) | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:large pinnae n1=en:bilateral hypoplastic cochlea | n2=en:large pinnae | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:large protruding ears n1=en:bilateral hypoplastic cochlea | n2=en:large protruding ears | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:large, dysmorphic ears n1=en:bilateral hypoplastic cochlea | n2=en:large, dysmorphic ears | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:loss of hearing (45%) n1=en:bilateral hypoplastic cochlea | n2=en:loss of hearing (45%) | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:loss of vestibular reflexes n1=en:bilateral hypoplastic cochlea | n2=en:loss of vestibular reflexes | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:mixed hearing loss (50% of patients) n1=en:bilateral hypoplastic cochlea | n2=en:mixed hearing loss (50% of patients) | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:narrow external ear canals (1 patient) n1=en:bilateral hypoplastic cochlea | n2=en:narrow external ear canals (1 patient) | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:normal vestibular function n1=en:bilateral hypoplastic cochlea | n2=en:normal vestibular function | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:overfolded helix n1=en:bilateral hypoplastic cochlea | n2=en:overfolded helix | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:pale, stiff pinnae n1=en:bilateral hypoplastic cochlea | n2=en:pale, stiff pinnae | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:postauricular pit n1=en:bilateral hypoplastic cochlea | n2=en:postauricular pit | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:progressive hearing loss (in some) n1=en:bilateral hypoplastic cochlea | n2=en:progressive hearing loss (in some) | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:pseudomembranous inflammation of the middle ear n1=en:bilateral hypoplastic cochlea | n2=en:pseudomembranous inflammation of the middle ear | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:rudimentary tympanic membrane (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:rudimentary tympanic membrane (in some patients) | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:sensorineural deafness, variable (in 1 family) n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural deafness, variable (in 1 family) | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:small, malformed ears n1=en:bilateral hypoplastic cochlea | n2=en:small, malformed ears | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:small/rudimentary tragus, antitragus and lobule n1=en:bilateral hypoplastic cochlea | n2=en:small/rudimentary tragus, antitragus and lobule | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:stiff, prominent pinnae n1=en:bilateral hypoplastic cochlea | n2=en:stiff, prominent pinnae | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:strabismus (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:strabismus (in some patients) | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:thickened helices n1=en:bilateral hypoplastic cochlea | n2=en:thickened helices | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:uplifted earlobes n1=en:bilateral hypoplastic cochlea | n2=en:uplifted earlobes | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> en:upsloping audiograms n1=en:bilateral hypoplastic cochlea | n2=en:upsloping audiograms | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 25 / 0.581 -> perte d'audition sensorineurale n1=en:bilateral hypoplastic cochlea | n2=perte d'audition sensorineurale | rel=r_associated | relid=0 | w=25 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:abnormal speech discrimination n1=en:bilateral hypoplastic cochlea | n2=en:abnormal speech discrimination | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:bilateral conductive hearing loss (rare) n1=en:bilateral hypoplastic cochlea | n2=en:bilateral conductive hearing loss (rare) | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss) n1=en:bilateral hypoplastic cochlea | n2=en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss) | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:deafness, secondary to cranial hyperostosis n1=en:bilateral hypoplastic cochlea | n2=en:deafness, secondary to cranial hyperostosis | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:deafness, sensorineural, severe to profound affecting all frequencies n1=en:bilateral hypoplastic cochlea | n2=en:deafness, sensorineural, severe to profound affecting all frequencies | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea n1=en:bilateral hypoplastic cochlea | n2=en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:ear cartilage calcification n1=en:bilateral hypoplastic cochlea | n2=en:ear cartilage calcification | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:ear pits, posterior helical n1=en:bilateral hypoplastic cochlea | n2=en:ear pits, posterior helical | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:endolymphatic sac tumors (elsts) n1=en:bilateral hypoplastic cochlea | n2=en:endolymphatic sac tumors (elsts) | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:external ear defects n1=en:bilateral hypoplastic cochlea | n2=en:external ear defects | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:external ear defects (47%) n1=en:bilateral hypoplastic cochlea | n2=en:external ear defects (47%) | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:hearing loss (1 patient) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss (1 patient) | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:hearing loss (2 patients) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss (2 patients) | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:hearing loss has been reported in some adults with severe disease n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss has been reported in some adults with severe disease | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:hearing loss, congenital profound n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, congenital profound | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:hypoplastic malleus (1 patient) n1=en:bilateral hypoplastic cochlea | n2=en:hypoplastic malleus (1 patient) | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:hypoplastic pinnae (30-60% of patients) n1=en:bilateral hypoplastic cochlea | n2=en:hypoplastic pinnae (30-60% of patients) | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:hypoplastic superior helix n1=en:bilateral hypoplastic cochlea | n2=en:hypoplastic superior helix | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:incomplete atretic plate n1=en:bilateral hypoplastic cochlea | n2=en:incomplete atretic plate | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:large dysplastic ears n1=en:bilateral hypoplastic cochlea | n2=en:large dysplastic ears | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:large fleshy earlobes n1=en:bilateral hypoplastic cochlea | n2=en:large fleshy earlobes | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:large, low-set ears (uncommon) n1=en:bilateral hypoplastic cochlea | n2=en:large, low-set ears (uncommon) | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:low-frequency sensorineural hearing impairment n1=en:bilateral hypoplastic cochlea | n2=en:low-frequency sensorineural hearing impairment | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:low-set ears (28%) n1=en:bilateral hypoplastic cochlea | n2=en:low-set ears (28%) | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:malformations of the auditory ossicles n1=en:bilateral hypoplastic cochlea | n2=en:malformations of the auditory ossicles | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:microtia (wws) n1=en:bilateral hypoplastic cochlea | n2=en:microtia (wws) | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:mild to moderate hearing loss across most frequencies n1=en:bilateral hypoplastic cochlea | n2=en:mild to moderate hearing loss across most frequencies | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:normal middle ear pressures on tympanometry n1=en:bilateral hypoplastic cochlea | n2=en:normal middle ear pressures on tympanometry | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:organ of corti degeneration n1=en:bilateral hypoplastic cochlea | n2=en:organ of corti degeneration | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:partial hearing loss n1=en:bilateral hypoplastic cochlea | n2=en:partial hearing loss | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:posteriorly rotated ears (1/4 patients) n1=en:bilateral hypoplastic cochlea | n2=en:posteriorly rotated ears (1/4 patients) | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:preauricular skin furrow n1=en:bilateral hypoplastic cochlea | n2=en:preauricular skin furrow | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:progressive cartilaginous ossification of pinnae n1=en:bilateral hypoplastic cochlea | n2=en:progressive cartilaginous ossification of pinnae | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:progressive conductive hearing impairment n1=en:bilateral hypoplastic cochlea | n2=en:progressive conductive hearing impairment | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:protruding lobules n1=en:bilateral hypoplastic cochlea | n2=en:protruding lobules | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:pulsatile tinnitus (tympanic paraganglioma) n1=en:bilateral hypoplastic cochlea | n2=en:pulsatile tinnitus (tympanic paraganglioma) | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:recurrent otitis media n1=en:bilateral hypoplastic cochlea | n2=en:recurrent otitis media | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:sensorineural hearing loss (in 1 of 3 patients) n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural hearing loss (in 1 of 3 patients) | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:sensorineural hearing loss, progressive bilateral postlingual n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural hearing loss, progressive bilateral postlingual | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:severe narrowing of cartilagenous auditory canal (in homozygotes) n1=en:bilateral hypoplastic cochlea | n2=en:severe narrowing of cartilagenous auditory canal (in homozygotes) | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:shallow skin dimple on posterior surface of ear n1=en:bilateral hypoplastic cochlea | n2=en:shallow skin dimple on posterior surface of ear | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:simple ear n1=en:bilateral hypoplastic cochlea | n2=en:simple ear | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:simple ear structure n1=en:bilateral hypoplastic cochlea | n2=en:simple ear structure | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:small triangular pinnae n1=en:bilateral hypoplastic cochlea | n2=en:small triangular pinnae | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:stenosis of external auditory canal n1=en:bilateral hypoplastic cochlea | n2=en:stenosis of external auditory canal | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:structure of lymphatic vessel of ear n1=en:bilateral hypoplastic cochlea | n2=en:structure of lymphatic vessel of ear | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:transient evoked otoacoustic emissions cannot be detected n1=en:bilateral hypoplastic cochlea | n2=en:transient evoked otoacoustic emissions cannot be detected | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:vertigo n1=en:bilateral hypoplastic cochlea | n2=en:vertigo | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 24 / 0.558 -> en:vestibular abnormalities (variable) n1=en:bilateral hypoplastic cochlea | n2=en:vestibular abnormalities (variable) | rel=r_associated | relid=0 | w=24 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:absent brainstem auditory responses n1=en:bilateral hypoplastic cochlea | n2=en:absent brainstem auditory responses | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:attached ear lobules n1=en:bilateral hypoplastic cochlea | n2=en:attached ear lobules | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:dysplastic pinnae n1=en:bilateral hypoplastic cochlea | n2=en:dysplastic pinnae | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:external auditory canal narrow n1=en:bilateral hypoplastic cochlea | n2=en:external auditory canal narrow | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:flat ears n1=en:bilateral hypoplastic cochlea | n2=en:flat ears | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:fleshy and overfolded helices n1=en:bilateral hypoplastic cochlea | n2=en:fleshy and overfolded helices | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:hearing loss begins with loss of high frequencies n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss begins with loss of high frequencies | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:hearing loss, conductive (in one family) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, conductive (in one family) | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:hearing loss, mixed (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, mixed (in some patients) | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:hearing loss, more severe at lower frequencies n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, more severe at lower frequencies | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:hearing loss, prelingual, severe to profound (affecting all frequencies) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, prelingual, severe to profound (affecting all frequencies) | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:hyperacusis n1=en:bilateral hypoplastic cochlea | n2=en:hyperacusis | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:hypertrophic auricular cartilage n1=en:bilateral hypoplastic cochlea | n2=en:hypertrophic auricular cartilage | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:hypoplasia of the cochlea n1=en:bilateral hypoplastic cochlea | n2=en:hypoplasia of the cochlea | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:hypoplastic, overfolded helices n1=en:bilateral hypoplastic cochlea | n2=en:hypoplastic, overfolded helices | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:keratotic plaque around ear meatus n1=en:bilateral hypoplastic cochlea | n2=en:keratotic plaque around ear meatus | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:malformed earlobes n1=en:bilateral hypoplastic cochlea | n2=en:malformed earlobes | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:microtia (30-60% of patients) n1=en:bilateral hypoplastic cochlea | n2=en:microtia (30-60% of patients) | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:microtia hearing loss, conductive n1=en:bilateral hypoplastic cochlea | n2=en:microtia hearing loss, conductive | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:microtia, type i n1=en:bilateral hypoplastic cochlea | n2=en:microtia, type i | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:narrow auditory canals (rare) n1=en:bilateral hypoplastic cochlea | n2=en:narrow auditory canals (rare) | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:narrow intertragic notch n1=en:bilateral hypoplastic cochlea | n2=en:narrow intertragic notch | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:narrowed external ear canal (30% of patients) n1=en:bilateral hypoplastic cochlea | n2=en:narrowed external ear canal (30% of patients) | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:nonsyndromic sensorineural hearing loss n1=en:bilateral hypoplastic cochlea | n2=en:nonsyndromic sensorineural hearing loss | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:normal static compliance on tympanometry n1=en:bilateral hypoplastic cochlea | n2=en:normal static compliance on tympanometry | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:otitis media, chronic (rare) n1=en:bilateral hypoplastic cochlea | n2=en:otitis media, chronic (rare) | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:recurrent otitis media in infancy n1=en:bilateral hypoplastic cochlea | n2=en:recurrent otitis media in infancy | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:recurrent serous otitis n1=en:bilateral hypoplastic cochlea | n2=en:recurrent serous otitis | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:retroverted ears n1=en:bilateral hypoplastic cochlea | n2=en:retroverted ears | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:rudimentary ear n1=en:bilateral hypoplastic cochlea | n2=en:rudimentary ear | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:sensorineural hearing loss (1 family) n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural hearing loss (1 family) | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:sensorineural hearing loss (uncommon) n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural hearing loss (uncommon) | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:severe loss in the higher frequencies by the fifth decade n1=en:bilateral hypoplastic cochlea | n2=en:severe loss in the higher frequencies by the fifth decade | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:short ears (in 1 family) n1=en:bilateral hypoplastic cochlea | n2=en:short ears (in 1 family) | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:simple auricles n1=en:bilateral hypoplastic cochlea | n2=en:simple auricles | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:small external auditory canals n1=en:bilateral hypoplastic cochlea | n2=en:small external auditory canals | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:small, simple ears n1=en:bilateral hypoplastic cochlea | n2=en:small, simple ears | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:stapes ankylosis n1=en:bilateral hypoplastic cochlea | n2=en:stapes ankylosis | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:unravelling of superior helices n1=en:bilateral hypoplastic cochlea | n2=en:unravelling of superior helices | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> en:upturned lobes n1=en:bilateral hypoplastic cochlea | n2=en:upturned lobes | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> surdité du labyrinthe n1=en:bilateral hypoplastic cochlea | n2=surdité du labyrinthe | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 23 / 0.535 -> surdité héréditaire n1=en:bilateral hypoplastic cochlea | n2=surdité héréditaire | rel=r_associated | relid=0 | w=23 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:abnormal ear configuration n1=en:bilateral hypoplastic cochlea | n2=en:abnormal ear configuration | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:abnormality of the middle ear ossicles n1=en:bilateral hypoplastic cochlea | n2=en:abnormality of the middle ear ossicles | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:absence of the helix and distal scapha in middle third of the ear n1=en:bilateral hypoplastic cochlea | n2=en:absence of the helix and distal scapha in middle third of the ear | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:absent helices, bilaterally n1=en:bilateral hypoplastic cochlea | n2=en:absent helices, bilaterally | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:angular ears n1=en:bilateral hypoplastic cochlea | n2=en:angular ears | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:anteriorly displaced ears n1=en:bilateral hypoplastic cochlea | n2=en:anteriorly displaced ears | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:asymmetric dysplastic ears n1=en:bilateral hypoplastic cochlea | n2=en:asymmetric dysplastic ears | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile) n1=en:bilateral hypoplastic cochlea | n2=en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile) | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:cleft lobules n1=en:bilateral hypoplastic cochlea | n2=en:cleft lobules | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:deafness (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:deafness (in some patients) | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:deafness (sensorineural or mixed sensorineural and conductive) n1=en:bilateral hypoplastic cochlea | n2=en:deafness (sensorineural or mixed sensorineural and conductive) | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:deafness, congenital nonprogressive sensorineural symmetric, moderate n1=en:bilateral hypoplastic cochlea | n2=en:deafness, congenital nonprogressive sensorineural symmetric, moderate | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:deafness, sensorineural (reported in 1 family) n1=en:bilateral hypoplastic cochlea | n2=en:deafness, sensorineural (reported in 1 family) | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:deafness, sensorineural, profound n1=en:bilateral hypoplastic cochlea | n2=en:deafness, sensorineural, profound | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:hearing loss, conductive (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, conductive (in some patients) | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:hearing loss, late-onset sensorineural, mild-to moderate (less common) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, late-onset sensorineural, mild-to moderate (less common) | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:hearing loss, mild (rare) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, mild (rare) | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:hearing loss, profound prelingual sensorineural n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, profound prelingual sensorineural | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies) | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies) | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:hearing loss, sensorineural (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural (in some patients) | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:incomplete separation of the cochlea from the internal auditory canal n1=en:bilateral hypoplastic cochlea | n2=en:incomplete separation of the cochlea from the internal auditory canal | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:large anteverted ears n1=en:bilateral hypoplastic cochlea | n2=en:large anteverted ears | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:large, prominent ears (59%) n1=en:bilateral hypoplastic cochlea | n2=en:large, prominent ears (59%) | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:linear ear lobe creases n1=en:bilateral hypoplastic cochlea | n2=en:linear ear lobe creases | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:loss of vestibular caloric response n1=en:bilateral hypoplastic cochlea | n2=en:loss of vestibular caloric response | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:low-set ears (severe form) n1=en:bilateral hypoplastic cochlea | n2=en:low-set ears (severe form) | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:michel aplasia (complete absence of inner ear structures) n1=en:bilateral hypoplastic cochlea | n2=en:michel aplasia (complete absence of inner ear structures) | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:narrow ear lobes n1=en:bilateral hypoplastic cochlea | n2=en:narrow ear lobes | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:narrowed external ear canal n1=en:bilateral hypoplastic cochlea | n2=en:narrowed external ear canal | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:near-stenosis of bony portion of auditory canal (in homozygotes) n1=en:bilateral hypoplastic cochlea | n2=en:near-stenosis of bony portion of auditory canal (in homozygotes) | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:no auditory brainstem response (abr) n1=en:bilateral hypoplastic cochlea | n2=en:no auditory brainstem response (abr) | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:no auditory brainstem response to 100-db stimulus n1=en:bilateral hypoplastic cochlea | n2=en:no auditory brainstem response to 100-db stimulus | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:no deafness n1=en:bilateral hypoplastic cochlea | n2=en:no deafness | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:no hearing loss n1=en:bilateral hypoplastic cochlea | n2=en:no hearing loss | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:normal outer hair cell functions n1=en:bilateral hypoplastic cochlea | n2=en:normal outer hair cell functions | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:partial aplasia of external auditory canal ending in blind fistula (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:partial aplasia of external auditory canal ending in blind fistula (in some patients) | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:preauricular fistulas, bilateral n1=en:bilateral hypoplastic cochlea | n2=en:preauricular fistulas, bilateral | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:preauricular sinus n1=en:bilateral hypoplastic cochlea | n2=en:preauricular sinus | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:preauricular skin tag n1=en:bilateral hypoplastic cochlea | n2=en:preauricular skin tag | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:prominent ear n1=en:bilateral hypoplastic cochlea | n2=en:prominent ear | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:prominent ears (rare) n1=en:bilateral hypoplastic cochlea | n2=en:prominent ears (rare) | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:sclerosis of semicircular canals n1=en:bilateral hypoplastic cochlea | n2=en:sclerosis of semicircular canals | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:sensorineural hearing impairment (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural hearing impairment (in some patients) | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:sensorineural hearing impairment (less common) n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural hearing impairment (less common) | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:sensorineural hearing loss (onset early childhood) n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural hearing loss (onset early childhood) | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:sensory hearing loss n1=en:bilateral hypoplastic cochlea | n2=en:sensory hearing loss | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves n1=en:bilateral hypoplastic cochlea | n2=en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:triangular-shaped ears n1=en:bilateral hypoplastic cochlea | n2=en:triangular-shaped ears | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:unfolded superior helices n1=en:bilateral hypoplastic cochlea | n2=en:unfolded superior helices | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:vertigo, single occurrence (in 2 patients) n1=en:bilateral hypoplastic cochlea | n2=en:vertigo, single occurrence (in 2 patients) | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:vestibular hypofunction n1=en:bilateral hypoplastic cochlea | n2=en:vestibular hypofunction | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:warsaw breakage syndrome n1=en:bilateral hypoplastic cochlea | n2=en:warsaw breakage syndrome | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 22 / 0.512 -> en:wide, flattened earlobes n1=en:bilateral hypoplastic cochlea | n2=en:wide, flattened earlobes | rel=r_associated | relid=0 | w=22 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:abnormally folded helix n1=en:bilateral hypoplastic cochlea | n2=en:abnormally folded helix | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:absent stapedial reflexes or intraoperative stapes immobility n1=en:bilateral hypoplastic cochlea | n2=en:absent stapedial reflexes or intraoperative stapes immobility | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:deafness, nonprogressive, moderate n1=en:bilateral hypoplastic cochlea | n2=en:deafness, nonprogressive, moderate | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:deafness, profound congenital sensorineural n1=en:bilateral hypoplastic cochlea | n2=en:deafness, profound congenital sensorineural | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:deafness, sensorineural, especially affecting high frequencies n1=en:bilateral hypoplastic cochlea | n2=en:deafness, sensorineural, especially affecting high frequencies | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:downward sloping or flat audiogram n1=en:bilateral hypoplastic cochlea | n2=en:downward sloping or flat audiogram | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:dysmorphic ears n1=en:bilateral hypoplastic cochlea | n2=en:dysmorphic ears | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:ear constriction (97%) n1=en:bilateral hypoplastic cochlea | n2=en:ear constriction (97%) | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:earlobe pits n1=en:bilateral hypoplastic cochlea | n2=en:earlobe pits | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:enlarged vestibular aqueduct n1=en:bilateral hypoplastic cochlea | n2=en:enlarged vestibular aqueduct | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:flat or shallow u-shaped audiogram n1=en:bilateral hypoplastic cochlea | n2=en:flat or shallow u-shaped audiogram | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:fleshy ears n1=en:bilateral hypoplastic cochlea | n2=en:fleshy ears | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:floppy ears n1=en:bilateral hypoplastic cochlea | n2=en:floppy ears | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:hearing impairment, sensorineural, fluctuating n1=en:bilateral hypoplastic cochlea | n2=en:hearing impairment, sensorineural, fluctuating | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:hearing loss (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss (in some patients) | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:hearing loss (rare) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss (rare) | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:hearing loss, high frequency, slowly progressive (onset in early childhood) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, high frequency, slowly progressive (onset in early childhood) | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:hearing loss, mild n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, mild | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:hearing loss, postlingual progressive sensorineural n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, postlingual progressive sensorineural | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:hearing loss, prelingual sensorineural, moderate to severe n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, prelingual sensorineural, moderate to severe | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:hearing loss, sensorineural (bilateral, prelingual) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural (bilateral, prelingual) | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:hearing loss, sensorineural, bilateral, moderate-to-severe n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:hearing loss, sensorineural, mild progressive (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural, mild progressive (in some patients) | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:hearing loss, sensorineural, progressive (childhood-onset) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural, progressive (childhood-onset) | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:hypoplastic ears fused to the scalp n1=en:bilateral hypoplastic cochlea | n2=en:hypoplastic ears fused to the scalp | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies n1=en:bilateral hypoplastic cochlea | n2=en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:internal auditory canal hypoplasia n1=en:bilateral hypoplastic cochlea | n2=en:internal auditory canal hypoplasia | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:large fleshy ears n1=en:bilateral hypoplastic cochlea | n2=en:large fleshy ears | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:low-set ears (45%) n1=en:bilateral hypoplastic cochlea | n2=en:low-set ears (45%) | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:low-set ears (in one family) n1=en:bilateral hypoplastic cochlea | n2=en:low-set ears (in one family) | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:misshapen, small ear n1=en:bilateral hypoplastic cochlea | n2=en:misshapen, small ear | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:no hearing impairment n1=en:bilateral hypoplastic cochlea | n2=en:no hearing impairment | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:no reproducible waves i, iii, or v at high intensities n1=en:bilateral hypoplastic cochlea | n2=en:no reproducible waves i, iii, or v at high intensities | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:no vestibular impairment n1=en:bilateral hypoplastic cochlea | n2=en:no vestibular impairment | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:occasional conductive hearing loss n1=en:bilateral hypoplastic cochlea | n2=en:occasional conductive hearing loss | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:otitis media, recurrent (rare) n1=en:bilateral hypoplastic cochlea | n2=en:otitis media, recurrent (rare) | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:poorly folded ears n1=en:bilateral hypoplastic cochlea | n2=en:poorly folded ears | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:poorly shaped ears n1=en:bilateral hypoplastic cochlea | n2=en:poorly shaped ears | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:posteriorly rotated ears (2p21del) n1=en:bilateral hypoplastic cochlea | n2=en:posteriorly rotated ears (2p21del) | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:preauricular sinus, bilateral n1=en:bilateral hypoplastic cochlea | n2=en:preauricular sinus, bilateral | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:progressive high-frequency hearing loss (onset 20-30 years) n1=en:bilateral hypoplastic cochlea | n2=en:progressive high-frequency hearing loss (onset 20-30 years) | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:progressive sensorineural hearing impairment n1=en:bilateral hypoplastic cochlea | n2=en:progressive sensorineural hearing impairment | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:prominent antihelix n1=en:bilateral hypoplastic cochlea | n2=en:prominent antihelix | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:recurrent ear infections n1=en:bilateral hypoplastic cochlea | n2=en:recurrent ear infections | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:recurrent otitis n1=en:bilateral hypoplastic cochlea | n2=en:recurrent otitis | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:relatively long ears n1=en:bilateral hypoplastic cochlea | n2=en:relatively long ears | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:sensorineural deafness (rare) n1=en:bilateral hypoplastic cochlea | n2=en:sensorineural deafness (rare) | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:small ears (female) n1=en:bilateral hypoplastic cochlea | n2=en:small ears (female) | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:structural inner ear abnormalities (in patients with larger deletions) n1=en:bilateral hypoplastic cochlea | n2=en:structural inner ear abnormalities (in patients with larger deletions) | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:superiorly displaced ears n1=en:bilateral hypoplastic cochlea | n2=en:superiorly displaced ears | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:thick earlobes n1=en:bilateral hypoplastic cochlea | n2=en:thick earlobes | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:underdeveloped nasal alae n1=en:bilateral hypoplastic cochlea | n2=en:underdeveloped nasal alae | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:uplift of earlobes (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:uplift of earlobes (in some patients) | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:vertigo, episodic n1=en:bilateral hypoplastic cochlea | n2=en:vertigo, episodic | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:vestibular areflexia, complete n1=en:bilateral hypoplastic cochlea | n2=en:vestibular areflexia, complete | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> en:vestibular dysfunction n1=en:bilateral hypoplastic cochlea | n2=en:vestibular dysfunction | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 21 / 0.488 -> traumatisme superficiel oreille n1=en:bilateral hypoplastic cochlea | n2=traumatisme superficiel oreille | rel=r_associated | relid=0 | w=21 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> déficience auditive n1=en:bilateral hypoplastic cochlea | n2=déficience auditive | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:acoustic trauma n1=en:bilateral hypoplastic cochlea | n2=en:acoustic trauma | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:auditory canal stenosis n1=en:bilateral hypoplastic cochlea | n2=en:auditory canal stenosis | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:balance problem n1=en:bilateral hypoplastic cochlea | n2=en:balance problem | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:chronic otitis media (25%) n1=en:bilateral hypoplastic cochlea | n2=en:chronic otitis media (25%) | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:cutlet n1=en:bilateral hypoplastic cochlea | n2=en:cutlet | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:disorder of equilibrium n1=en:bilateral hypoplastic cochlea | n2=en:disorder of equilibrium | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:disturbance of equilibrium n1=en:bilateral hypoplastic cochlea | n2=en:disturbance of equilibrium | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:dizziness n1=en:bilateral hypoplastic cochlea | n2=en:dizziness | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:dysplastic ears (jbts) n1=en:bilateral hypoplastic cochlea | n2=en:dysplastic ears (jbts) | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:ENT doctor n1=en:bilateral hypoplastic cochlea | n2=en:ENT doctor | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:ENT specialist n1=en:bilateral hypoplastic cochlea | n2=en:ENT specialist | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:glue ear n1=en:bilateral hypoplastic cochlea | n2=en:glue ear | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:hearing impairment n1=en:bilateral hypoplastic cochlea | n2=en:hearing impairment | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:hearing impairment (1 patient) n1=en:bilateral hypoplastic cochlea | n2=en:hearing impairment (1 patient) | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:hearing impairment, progressive (family a) n1=en:bilateral hypoplastic cochlea | n2=en:hearing impairment, progressive (family a) | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:hearing loss (in 2 members of 1 family) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss (in 2 members of 1 family) | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:hearing loss, sensorineural, progressive (all frequencies) n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural, progressive (all frequencies) | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:hereditary deafness n1=en:bilateral hypoplastic cochlea | n2=en:hereditary deafness | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:microtia (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:microtia (in some patients) | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:mild dysplasia of concha, unilateral n1=en:bilateral hypoplastic cochlea | n2=en:mild dysplasia of concha, unilateral | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:no vestibular symptoms n1=en:bilateral hypoplastic cochlea | n2=en:no vestibular symptoms | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:nose and throat specialist n1=en:bilateral hypoplastic cochlea | n2=en:nose and throat specialist | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:otitis with effusion n1=en:bilateral hypoplastic cochlea | n2=en:otitis with effusion | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:presbyacusis n1=en:bilateral hypoplastic cochlea | n2=en:presbyacusis | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:presbycousis n1=en:bilateral hypoplastic cochlea | n2=en:presbycousis | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:problem with balance n1=en:bilateral hypoplastic cochlea | n2=en:problem with balance | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:rotary vertigo n1=en:bilateral hypoplastic cochlea | n2=en:rotary vertigo | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:serous otitis n1=en:bilateral hypoplastic cochlea | n2=en:serous otitis | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:serous otitis media n1=en:bilateral hypoplastic cochlea | n2=en:serous otitis media | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:sticking-out ear n1=en:bilateral hypoplastic cochlea | n2=en:sticking-out ear | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> en:tinnitus, bilateral (in some patients) n1=en:bilateral hypoplastic cochlea | n2=en:tinnitus, bilateral (in some patients) | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> esgourde n1=en:bilateral hypoplastic cochlea | n2=esgourde | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> état nébuleux n1=en:bilateral hypoplastic cochlea | n2=état nébuleux | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> état vertigineux n1=en:bilateral hypoplastic cochlea | n2=état vertigineux | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> étourdissement n1=en:bilateral hypoplastic cochlea | n2=étourdissement | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> hyperacousie n1=en:bilateral hypoplastic cochlea | n2=hyperacousie | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> hyperacousies n1=en:bilateral hypoplastic cochlea | n2=hyperacousies | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> hyperacusie n1=en:bilateral hypoplastic cochlea | n2=hyperacusie | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> médecin ORL n1=en:bilateral hypoplastic cochlea | n2=médecin ORL | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> oreille décollée n1=en:bilateral hypoplastic cochlea | n2=oreille décollée | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> otite moyenne séreuse n1=en:bilateral hypoplastic cochlea | n2=otite moyenne séreuse | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> otite séreuse n1=en:bilateral hypoplastic cochlea | n2=otite séreuse | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> otite séromuqueuse n1=en:bilateral hypoplastic cochlea | n2=otite séromuqueuse | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> oto-rhino n1=en:bilateral hypoplastic cochlea | n2=oto-rhino | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> oto-rhino-laryngologiste n1=en:bilateral hypoplastic cochlea | n2=oto-rhino-laryngologiste | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> otorhinolaryngologiste n1=en:bilateral hypoplastic cochlea | n2=otorhinolaryngologiste | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> pavillon de l'oreille de morphologie rudimentaire n1=en:bilateral hypoplastic cochlea | n2=pavillon de l'oreille de morphologie rudimentaire | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> presbyacousie n1=en:bilateral hypoplastic cochlea | n2=presbyacousie | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> sensation de rotation n1=en:bilateral hypoplastic cochlea | n2=sensation de rotation | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> sensation de tournoiement n1=en:bilateral hypoplastic cochlea | n2=sensation de tournoiement | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> sensation rotatoire n1=en:bilateral hypoplastic cochlea | n2=sensation rotatoire | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> sensation vertigineuse n1=en:bilateral hypoplastic cochlea | n2=sensation vertigineuse | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> sténose du canal auriculaire n1=en:bilateral hypoplastic cochlea | n2=sténose du canal auriculaire | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> tête pivotante n1=en:bilateral hypoplastic cochlea | n2=tête pivotante | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> trouble de l'équilibre n1=en:bilateral hypoplastic cochlea | n2=trouble de l'équilibre | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> vertige n1=en:bilateral hypoplastic cochlea | n2=vertige | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> vertige rotatoire n1=en:bilateral hypoplastic cochlea | n2=vertige rotatoire | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> vertige subjectif n1=en:bilateral hypoplastic cochlea | n2=vertige subjectif | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> vertigo n1=en:bilateral hypoplastic cochlea | n2=vertigo | rel=r_associated | relid=0 | w=20 en:bilateral hypoplastic cochlea -- r_associated #0: 20 / 0.465 -> vertigo rotatoire n1=en:bilateral hypoplastic cochlea | n2=vertigo rotatoire | rel=r_associated | relid=0 | w=20

≈ 726 relations entrantes en:congenital deafness --- r_associated #0: 300 --> en:bilateral hypoplastic cochlea n1=en:congenital deafness | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=300 surdité congénitale --- r_associated #0: 297 --> en:bilateral hypoplastic cochlea n1=surdité congénitale | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=297 surdité héréditaire --- r_associated #0: 295 --> en:bilateral hypoplastic cochlea n1=surdité héréditaire | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=295 surdité du labyrinthe --- r_associated #0: 271 --> en:bilateral hypoplastic cochlea n1=surdité du labyrinthe | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=271 en:deafness labyrinthine --- r_associated #0: 270 --> en:bilateral hypoplastic cochlea n1=en:deafness labyrinthine | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=270 sensation vertigineuse --- r_associated #0: 245 --> en:bilateral hypoplastic cochlea n1=sensation vertigineuse | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=245 vertige subjectif --- r_associated #0: 240 --> en:bilateral hypoplastic cochlea n1=vertige subjectif | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=240 vertigo rotatoire --- r_associated #0: 240 --> en:bilateral hypoplastic cochlea n1=vertigo rotatoire | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=240 vertige rotatoire --- r_associated #0: 230 --> en:bilateral hypoplastic cochlea n1=vertige rotatoire | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=230 sensation de tournoiement --- r_associated #0: 229 --> en:bilateral hypoplastic cochlea n1=sensation de tournoiement | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=229 sensation de rotation --- r_associated #0: 226 --> en:bilateral hypoplastic cochlea n1=sensation de rotation | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=226 tête pivotante --- r_associated #0: 220 --> en:bilateral hypoplastic cochlea n1=tête pivotante | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=220 état nébuleux --- r_associated #0: 215 --> en:bilateral hypoplastic cochlea n1=état nébuleux | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=215 état vertigineux --- r_associated #0: 215 --> en:bilateral hypoplastic cochlea n1=état vertigineux | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=215 sensation rotatoire --- r_associated #0: 211 --> en:bilateral hypoplastic cochlea n1=sensation rotatoire | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=211 otite moyenne séreuse --- r_associated #0: 200 --> en:bilateral hypoplastic cochlea n1=otite moyenne séreuse | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=200 en:serous otitis media --- r_associated #0: 199 --> en:bilateral hypoplastic cochlea n1=en:serous otitis media | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=199 traumatisme superficiel oreille --- r_associated #0: 185 --> en:bilateral hypoplastic cochlea n1=traumatisme superficiel oreille | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=185 en:sensorineural hearing loss --- r_associated #0: 183 --> en:bilateral hypoplastic cochlea n1=en:sensorineural hearing loss | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=183 en:superficial injury of ear --- r_associated #0: 181 --> en:bilateral hypoplastic cochlea n1=en:superficial injury of ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=181 perte d'audition sensorineurale --- r_associated #0: 179 --> en:bilateral hypoplastic cochlea n1=perte d'audition sensorineurale | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=179 en:vertigo --- r_associated #0: 167 --> en:bilateral hypoplastic cochlea n1=en:vertigo | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=167 en:dizziness --- r_associated #0: 165 --> en:bilateral hypoplastic cochlea n1=en:dizziness | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=165 hyperacousie --- r_associated #0: 140 --> en:bilateral hypoplastic cochlea n1=hyperacousie | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=140 hyperacusie --- r_associated #0: 140 --> en:bilateral hypoplastic cochlea n1=hyperacusie | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=140 en:hyperacusis --- r_associated #0: 139 --> en:bilateral hypoplastic cochlea n1=en:hyperacusis | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=139 vertigo --- r_associated #0: 131 --> en:bilateral hypoplastic cochlea n1=vertigo | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=131 hyperacousies --- r_associated #0: 120 --> en:bilateral hypoplastic cochlea n1=hyperacousies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=120 en:balance problem --- r_associated #0: 115 --> en:bilateral hypoplastic cochlea n1=en:balance problem | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=115 en:disorder of equilibrium --- r_associated #0: 115 --> en:bilateral hypoplastic cochlea n1=en:disorder of equilibrium | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=115 en:problem with balance --- r_associated #0: 115 --> en:bilateral hypoplastic cochlea n1=en:problem with balance | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=115 trouble de l'équilibre --- r_associated #0: 115 --> en:bilateral hypoplastic cochlea n1=trouble de l'équilibre | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=115 vertige --- r_associated #0: 95 --> en:bilateral hypoplastic cochlea n1=vertige | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=95 en:secretory otitis media --- r_associated #0: 78 --> en:bilateral hypoplastic cochlea n1=en:secretory otitis media | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=78 otite séromuqueuse --- r_associated #0: 76 --> en:bilateral hypoplastic cochlea n1=otite séromuqueuse | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=76 étourdissement --- r_associated #0: 71 --> en:bilateral hypoplastic cochlea n1=étourdissement | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=71 en:stenosis of external auditory canal --- r_associated #0: 68 --> en:bilateral hypoplastic cochlea n1=en:stenosis of external auditory canal | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=68 sténose du canal auriculaire --- r_associated #0: 64 --> en:bilateral hypoplastic cochlea n1=sténose du canal auriculaire | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=64 lésion traumatique superficielle de l'oreille --- r_associated #0: 58 --> en:bilateral hypoplastic cochlea n1=lésion traumatique superficielle de l'oreille | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=58 déficience auditive --- r_associated #0: 55 --> en:bilateral hypoplastic cochlea n1=déficience auditive | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=55 en:hearing impairment --- r_associated #0: 53 --> en:bilateral hypoplastic cochlea n1=en:hearing impairment | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=53 en:ENT specialist --- r_associated #0: 50 --> en:bilateral hypoplastic cochlea n1=en:ENT specialist | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=50 oto-rhino --- r_associated #0: 50 --> en:bilateral hypoplastic cochlea n1=oto-rhino | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=50 oto-rhino-laryngologiste --- r_associated #0: 50 --> en:bilateral hypoplastic cochlea n1=oto-rhino-laryngologiste | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=50 en:nose and throat specialist --- r_associated #0: 49 --> en:bilateral hypoplastic cochlea n1=en:nose and throat specialist | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=49 otorhinolaryngologiste --- r_associated #0: 48 --> en:bilateral hypoplastic cochlea n1=otorhinolaryngologiste | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=48 en:hereditary deafness --- r_associated #0: 46 --> en:bilateral hypoplastic cochlea n1=en:hereditary deafness | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=46 en:absence of acoustic reflex --- r_associated #0: 43 --> en:bilateral hypoplastic cochlea n1=en:absence of acoustic reflex | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=43 en:bilateral dys-synchronized auditory brainstem responses --- r_associated #0: 43 --> en:bilateral hypoplastic cochlea n1=en:bilateral dys-synchronized auditory brainstem responses | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=43 en:hypoplastic ears fused to the scalp --- r_associated #0: 43 --> en:bilateral hypoplastic cochlea n1=en:hypoplastic ears fused to the scalp | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=43 en:pigmentation of the ear cartilage --- r_associated #0: 43 --> en:bilateral hypoplastic cochlea n1=en:pigmentation of the ear cartilage | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=43 en:sensorineural deafness, progressive, late-onset --- r_associated #0: 43 --> en:bilateral hypoplastic cochlea n1=en:sensorineural deafness, progressive, late-onset | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=43 en:auditory neuropathy spectrum disorder --- r_associated #0: 42 --> en:bilateral hypoplastic cochlea n1=en:auditory neuropathy spectrum disorder | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=42 en:no vestibular dysfunction --- r_associated #0: 42 --> en:bilateral hypoplastic cochlea n1=en:no vestibular dysfunction | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=42 en:prominent crura --- r_associated #0: 42 --> en:bilateral hypoplastic cochlea n1=en:prominent crura | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=42 en:prominent lobules --- r_associated #0: 42 --> en:bilateral hypoplastic cochlea n1=en:prominent lobules | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=42 pavillon de l'oreille de morphologie rudimentaire --- r_associated #0: 42 --> en:bilateral hypoplastic cochlea n1=pavillon de l'oreille de morphologie rudimentaire | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=42 en:dysplastic ears (jbts) --- r_associated #0: 41 --> en:bilateral hypoplastic cochlea n1=en:dysplastic ears (jbts) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=41 en:hearing loss, moderate to severe, bilateral, nonprogressive --- r_associated #0: 41 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, moderate to severe, bilateral, nonprogressive | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=41 en:hearing normal --- r_associated #0: 41 --> en:bilateral hypoplastic cochlea n1=en:hearing normal | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=41 en:partial hearing loss --- r_associated #0: 41 --> en:bilateral hypoplastic cochlea n1=en:partial hearing loss | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=41 en:rotary vertigo --- r_associated #0: 41 --> en:bilateral hypoplastic cochlea n1=en:rotary vertigo | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=41 en:simple ear --- r_associated #0: 41 --> en:bilateral hypoplastic cochlea n1=en:simple ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=41 en:hearing impairment, sensorineural, fluctuating --- r_associated #0: 40 --> en:bilateral hypoplastic cochlea n1=en:hearing impairment, sensorineural, fluctuating | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=40 en:no deafness --- r_associated #0: 40 --> en:bilateral hypoplastic cochlea n1=en:no deafness | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=40 en:deafness, unilateral, childhood onset --- r_associated #0: 39 --> en:bilateral hypoplastic cochlea n1=en:deafness, unilateral, childhood onset | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=39 en:earlobe pits --- r_associated #0: 39 --> en:bilateral hypoplastic cochlea n1=en:earlobe pits | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=39 en:large fleshy ears --- r_associated #0: 39 --> en:bilateral hypoplastic cochlea n1=en:large fleshy ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=39 en:malformed earlobes --- r_associated #0: 39 --> en:bilateral hypoplastic cochlea n1=en:malformed earlobes | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=39 en:prominent ears (in some patients) --- r_associated #0: 39 --> en:bilateral hypoplastic cochlea n1=en:prominent ears (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=39 oreille décollée --- r_associated #0: 39 --> en:bilateral hypoplastic cochlea n1=oreille décollée | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=39 en:endolymphatic hydrops, delayed onset --- r_associated #0: 38 --> en:bilateral hypoplastic cochlea n1=en:endolymphatic hydrops, delayed onset | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=38 en:hearing loss (in some patients) --- r_associated #0: 38 --> en:bilateral hypoplastic cochlea n1=en:hearing loss (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=38 en:superiorly displaced ears --- r_associated #0: 38 --> en:bilateral hypoplastic cochlea n1=en:superiorly displaced ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=38 en:ENT doctor --- r_associated #0: 37 --> en:bilateral hypoplastic cochlea n1=en:ENT doctor | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=37 en:conductive hearing loss (30% of patients) --- r_associated #0: 37 --> en:bilateral hypoplastic cochlea n1=en:conductive hearing loss (30% of patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=37 en:disproportionately large ears --- r_associated #0: 37 --> en:bilateral hypoplastic cochlea n1=en:disproportionately large ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=37 en:hearing loss, sensorineural and conductive, severe to profound --- r_associated #0: 37 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural and conductive, severe to profound | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=37 en:prolonged brainstem auditory evoked potentials (baep) --- r_associated #0: 37 --> en:bilateral hypoplastic cochlea n1=en:prolonged brainstem auditory evoked potentials (baep) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=37 otite séreuse --- r_associated #0: 37 --> en:bilateral hypoplastic cochlea n1=otite séreuse | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=37 en:abnormal communication between the subarachnoid space in the meatus and the perilymph --- r_associated #0: 36 --> en:bilateral hypoplastic cochlea n1=en:abnormal communication between the subarachnoid space in the meatus and the perilymph | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=36 en:ear tag --- r_associated #0: 36 --> en:bilateral hypoplastic cochlea n1=en:ear tag | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=36 en:hearing loss, conductive (rare) --- r_associated #0: 36 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, conductive (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=36 en:no hearing loss --- r_associated #0: 36 --> en:bilateral hypoplastic cochlea n1=en:no hearing loss | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=36 en:small lobes --- r_associated #0: 36 --> en:bilateral hypoplastic cochlea n1=en:small lobes | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=36 en:abnormal middle ear reflexes --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:abnormal middle ear reflexes | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:abnormality of the pinna --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:abnormality of the pinna | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:absence of earlobe --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:absence of earlobe | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:absent helices, bilaterally --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:absent helices, bilaterally | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:asymmetric dysplastic ears --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:asymmetric dysplastic ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:cauliflower ear deformity (rare) --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:cauliflower ear deformity (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:congenital hearing loss (1 family) --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:congenital hearing loss (1 family) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:deafness (often in third decade) --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:deafness (often in third decade) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:deafness, sensorineural (severe to profound) --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:deafness, sensorineural (severe to profound) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:deafness, sensorineural, profound --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:deafness, sensorineural, profound | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:deafness, sensorineural, severe to profound affecting all frequencies --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:deafness, sensorineural, severe to profound affecting all frequencies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:deep-set ears --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:deep-set ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:dysplastic pinnae --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:dysplastic pinnae | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:flat ears --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:flat ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:fleshy and overfolded helices --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:fleshy and overfolded helices | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:hearing impairment (1 patient) --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:hearing impairment (1 patient) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:hearing impairment (rare) --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:hearing impairment (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:hearing impairment, progressive (family a) --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:hearing impairment, progressive (family a) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:hearing loss (rare) --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:hearing loss (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:hearing loss, postlingual sensorineural --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, postlingual sensorineural | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:hearing loss, prelingual sensorineural, moderate to severe --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, prelingual sensorineural, moderate to severe | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:hearing loss, unilateral (rare) --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, unilateral (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:hearing loss, unilateral, mild --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, unilateral, mild | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:hypoplastic pinnae (30-60% of patients) --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:hypoplastic pinnae (30-60% of patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:keratotic plaque around ear meatus --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:keratotic plaque around ear meatus | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:large earlobe --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:large earlobe | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:low-set ears (severe form) --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:low-set ears (severe form) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:microtia hearing loss, conductive --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:microtia hearing loss, conductive | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:mixed hearing loss (50% of patients) --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:mixed hearing loss (50% of patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:morphological abnormality of the middle ear --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:morphological abnormality of the middle ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:no auditory brainstem response to 100-db stimulus --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:no auditory brainstem response to 100-db stimulus | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:no hearing impairment --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:no hearing impairment | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:no vestibular symptoms --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:no vestibular symptoms | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:nonprogressive deafness --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:nonprogressive deafness | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:nonsyndromic sensorineural hearing loss --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:nonsyndromic sensorineural hearing loss | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:organ of corti degeneration --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:organ of corti degeneration | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:ossified pinnae --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:ossified pinnae | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:otitis externa, recurrent, due to infection with staphylococcus aureus --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:otitis externa, recurrent, due to infection with staphylococcus aureus | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:otitis media, chronic (rare) --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:otitis media, chronic (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:outer ear abnormalities (deletion patients) prominent ears --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:outer ear abnormalities (deletion patients) prominent ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:partial aplasia of external auditory canal ending in blind fistula (in some patients) --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:partial aplasia of external auditory canal ending in blind fistula (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:posteriorly rotated ears (1/4 patients) --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:posteriorly rotated ears (1/4 patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:prominent antihelix --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:prominent antihelix | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:prominent antitragus --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:prominent antitragus | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:prominent ear --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:prominent ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:protruding ears (rare) --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:protruding ears (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:protruding right ear --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:protruding right ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:protuberant ear --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:protuberant ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:rotated ears --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:rotated ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:sensorineural deafness (reported in 1 family) --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:sensorineural deafness (reported in 1 family) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:sensorineural hearing impairment (in some patients) --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:sensorineural hearing impairment (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:severe loss in the higher frequencies by the fifth decade --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:severe loss in the higher frequencies by the fifth decade | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:severe narrowing of cartilagenous auditory canal --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:severe narrowing of cartilagenous auditory canal | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:simple auricles --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:simple auricles | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:small earlobe --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:small earlobe | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:stapes fixation --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:stapes fixation | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:strabismus (in some patients) --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:strabismus (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:upsloping audiograms --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:upsloping audiograms | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:vertigo, single occurrence (in 2 patients) --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:vertigo, single occurrence (in 2 patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:vestibulopathy, bilateral, progressive --- r_associated #0: 35 --> en:bilateral hypoplastic cochlea n1=en:vestibulopathy, bilateral, progressive | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35 en:angular ears --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:angular ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:bilateral sensorineural hearing loss (in some patients) --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:bilateral sensorineural hearing loss (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:complete bony atresia of medial portion of external auditory canal (in some patients) --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:complete bony atresia of medial portion of external auditory canal (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:conductive hearing loss to due otitis media --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:conductive hearing loss to due otitis media | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:deafness (in some patients) --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:deafness (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:deafness, sensorineural, especially affecting high frequencies --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:deafness, sensorineural, especially affecting high frequencies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:dysmorphic ears --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:dysmorphic ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:dysplastic helices --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:dysplastic helices | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:ear --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:first branchial arch anomalies --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:first branchial arch anomalies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:fleshy ears --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:fleshy ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:hearing impairment (in some patients) --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:hearing impairment (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:hearing loss (affecting all frequencies), moderate to severe --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:hearing loss (affecting all frequencies), moderate to severe | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:hearing loss (cvs+) --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:hearing loss (cvs+) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:hearing loss begins with loss of high frequencies --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:hearing loss begins with loss of high frequencies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:hearing loss, conductive (in one family) --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, conductive (in one family) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:hearing loss, conductive or mixed --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, conductive or mixed | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:hearing loss, congenital sensorineural, severe to profound --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, congenital sensorineural, severe to profound | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:hearing loss, mild --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, mild | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:hearing loss, mild (rare) --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, mild (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:hearing loss, postlingual --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, postlingual | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:hearing loss, progressive conductive and/or sensorineural, during adulthood --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, progressive conductive and/or sensorineural, during adulthood | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:hearing loss, progressive sensorineural, affecting high frequencies --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, progressive sensorineural, affecting high frequencies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies) --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:hearing loss, sensorineural (bilateral, prelingual) --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural (bilateral, prelingual) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:hearing loss, sensorineural (in 1 ashkenazi patient) --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural (in 1 ashkenazi patient) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:hearing loss, sensorineural, moderate, postlingual --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural, moderate, postlingual | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:hypercompliant tympanic membranes --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:hypercompliant tympanic membranes | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:hypoacusia (1 patient) --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:hypoacusia (1 patient) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:hypoplasia of the upper part of the helix --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:hypoplasia of the upper part of the helix | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:internal auditory canal hypoplasia --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:internal auditory canal hypoplasia | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:large anteverted ears --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:large anteverted ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:large auricle --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:large auricle | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:large ear pinnae --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:large ear pinnae | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:large simple ears --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:large simple ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:large, low-set ears (uncommon) --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:large, low-set ears (uncommon) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:loss of outer hair cell function --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:loss of outer hair cell function | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:low-set and rotated ears --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:low-set and rotated ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:meniere disease --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:meniere disease | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:mild dysplasia of concha, unilateral --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:mild dysplasia of concha, unilateral | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:misshapen, small ear --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:misshapen, small ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:mondini defect --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:mondini defect | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:normal otoacoustic emissions --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:normal otoacoustic emissions | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:normal static compliance on tympanometry --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:normal static compliance on tympanometry | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:overfolded helix --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:overfolded helix | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:postauricular pit --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:postauricular pit | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:posteriorly rotated ears (2p21del) --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:posteriorly rotated ears (2p21del) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:preauricular skin tags (in some patients) --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:preauricular skin tags (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face) --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:progressive high-frequency hearing loss (onset 20-30 years) --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:progressive high-frequency hearing loss (onset 20-30 years) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:prominent antitragus (in some patients) --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:prominent antitragus (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:protruding, simple ears --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:protruding, simple ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:raised earlobes --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:raised earlobes | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:recurrent otitis media in infancy and childhood --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:recurrent otitis media in infancy and childhood | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:recurrent serous otitis --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:recurrent serous otitis | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:retinitis (in some patients) --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:retinitis (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:sensorineural hearing loss (onset early childhood) --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:sensorineural hearing loss (onset early childhood) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:sensory hearing loss --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:sensory hearing loss | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:small external auditory meatus --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:small external auditory meatus | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:small triangular pinnae --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:small triangular pinnae | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:squared-off superior helices --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:squared-off superior helices | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:stapes ankylosis --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:stapes ankylosis | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:superior semicircular canal dehiscence syndrome --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:superior semicircular canal dehiscence syndrome | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:symmetric deterioration of hearing loss and speech reception with age --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:symmetric deterioration of hearing loss and speech reception with age | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:thick, firm earlobes --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:thick, firm earlobes | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:thickened lobes --- r_associated #0: 34 --> en:bilateral hypoplastic cochlea n1=en:thickened lobes | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=34 en:abnormal ear configuration --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:abnormal ear configuration | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:absence of the helix and distal scapha in middle third of the ear --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:absence of the helix and distal scapha in middle third of the ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:absent brainstem auditory responses --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:absent brainstem auditory responses | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile) --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:chronic otitis --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:chronic otitis | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:conductive hearing loss (in a subset of patients) --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:conductive hearing loss (in a subset of patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:congenital sensorineural hearing loss --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:congenital sensorineural hearing loss | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:deafness (variable) --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:deafness (variable) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:deafness in 30-50% of patients with skull involvement --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:deafness in 30-50% of patients with skull involvement | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:deafness, early-onset --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:deafness, early-onset | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:deafness, postlingual --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:deafness, postlingual | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:deafness, profound, by 6th decade --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:deafness, profound, by 6th decade | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:deafness, sensorineural, prelingual, profound --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:deafness, sensorineural, prelingual, profound | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:deafness, stable bilateral symmetric prelingual --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:deafness, stable bilateral symmetric prelingual | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:decreased otoacoustic emission amplitude --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:decreased otoacoustic emission amplitude | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:everted ears --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:everted ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:hearing deficits (28% of adults) --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:hearing deficits (28% of adults) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:hearing impairment, sensorineural, mild --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:hearing impairment, sensorineural, mild | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:hearing loss (1 patient) --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:hearing loss (1 patient) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:hearing loss (2 patients) --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:hearing loss (2 patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:hearing loss, bilateral --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, bilateral | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:hearing loss, sensorineural (high frequency) --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural (high frequency) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:hearing loss, sensorineural (in some patients) --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:hearing loss, sensorineural (reported in 1 patient) --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural (reported in 1 patient) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:hearing loss, sensorineural, progressive (all frequencies) --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural, progressive (all frequencies) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:hypoplastic semicircular canals --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:hypoplastic semicircular canals | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients) --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:inferior displacement of the ears --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:inferior displacement of the ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:large ears (in some patients) --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:large ears (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:large prominent ears --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:large prominent ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:large protruding ears --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:large protruding ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:long and prominent ear crus --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:long and prominent ear crus | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:microtia, type i --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:microtia, type i | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:mild hearing impairment (13%) --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:mild hearing impairment (13%) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:normal outer hair cell functions --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:normal outer hair cell functions | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:pale, stiff pinnae --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:pale, stiff pinnae | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:pointed upper helix --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:pointed upper helix | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:preauricular sinus, bilateral --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:preauricular sinus, bilateral | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:preauricular skin tag --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:preauricular skin tag | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:profound deafness --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:profound deafness | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:prominence and protrusion of upper third of the ear --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:prominence and protrusion of upper third of the ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:protruding ears (in some patients) --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:protruding ears (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:pulsatile tinnitus (tympanic paraganglioma) --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:pulsatile tinnitus (tympanic paraganglioma) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:recurrent otitis --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:recurrent otitis | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:rudimentary tympanic membrane (in some patients) --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:rudimentary tympanic membrane (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:sclerosis of semicircular canals --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:sclerosis of semicircular canals | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:sensorineural hearing loss (1 patient) --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:sensorineural hearing loss (1 patient) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:sensorineural hearing loss (described in 1 family) --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:sensorineural hearing loss (described in 1 family) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:severe to profound hearing impairment by early adulthood --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:severe to profound hearing impairment by early adulthood | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:simple ear structure --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:simple ear structure | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:small cavum conchae --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:small cavum conchae | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:structure of superior auricularis muscle --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:structure of superior auricularis muscle | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:u- or bowl-shaped audiogram --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:u- or bowl-shaped audiogram | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:vestibular dysfunction --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:vestibular dysfunction | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:vestibular function defect (decreased in some, normal in other patients) --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:vestibular function defect (decreased in some, normal in other patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:vestibular involvement (variable) --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:vestibular involvement (variable) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:wide bulbous internal auditory meatus --- r_associated #0: 32 --> en:bilateral hypoplastic cochlea n1=en:wide bulbous internal auditory meatus | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32 en:abnormal auricles --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:abnormal auricles | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:absent stapedial reflexes or intraoperative stapes immobility --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:absent stapedial reflexes or intraoperative stapes immobility | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:anteriorly displaced ears --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:anteriorly displaced ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:attached ear lobules --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:attached ear lobules | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:auditory impairment --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:auditory impairment | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:chronic otitis media --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:chronic otitis media | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:chronic otitis media (25%) --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:chronic otitis media (25%) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:cochlear degeneration --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:cochlear degeneration | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:deafness, bilateral sensorineural, high frequency (100% of patients) --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:deafness, bilateral sensorineural, high frequency (100% of patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:deafness, congenital nonprogressive sensorineural symmetric, moderate --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:deafness, congenital nonprogressive sensorineural symmetric, moderate | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:deafness, nonprogressive, moderate --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:deafness, nonprogressive, moderate | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:deafness, sensorineural (45%) --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:deafness, sensorineural (45%) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:decreased auditory brainstem responses --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:decreased auditory brainstem responses | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:deficient auricle --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:deficient auricle | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:dilatated internal auditory canal --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:dilatated internal auditory canal | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:downward sloping or flat audiogram --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:downward sloping or flat audiogram | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:ear constriction (97%) --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:ear constriction (97%) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:ears deficient in cartilage --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:ears deficient in cartilage | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:enlarged vestibular aqueduct --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:enlarged vestibular aqueduct | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:external ears rudimentary --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:external ears rudimentary | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:floppy ears --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:floppy ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:folded superior edge of helix --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:folded superior edge of helix | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:hearing loss (uncommon) --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:hearing loss (uncommon) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:hearing loss, bilateral progressive post-lingual --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, bilateral progressive post-lingual | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:hearing loss, neural type --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, neural type | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:hearing loss, prelingual, severe to profound (affecting all frequencies) --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, prelingual, severe to profound (affecting all frequencies) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:hearing loss, sensorineural, due to auditory neuropathy --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural, due to auditory neuropathy | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:hearing loss, sensorineural, prelingual --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural, prelingual | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:high-tone sensorineural deafness (67% of patients) --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:high-tone sensorineural deafness (67% of patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:hypoplastic ear lobes --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:hypoplastic ear lobes | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:hypoplastic superior helix --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:hypoplastic superior helix | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:impaired tympanic membrane mobility --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:impaired tympanic membrane mobility | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:large, prominent ears (59%) --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:large, prominent ears (59%) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:lobular aplasia --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:lobular aplasia | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:lobule may be separately from the rest of the external ear --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:lobule may be separately from the rest of the external ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:loss of mid- and low-frequencies later --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:loss of mid- and low-frequencies later | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:loss of vestibular caloric response --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:loss of vestibular caloric response | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:low-set ears (in one family) --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:low-set ears (in one family) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:low-set ears (in some patients) --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:low-set ears (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:low-set, posteriorly rotated ears --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:low-set, posteriorly rotated ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:michel aplasia (complete absence of inner ear structures) --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:michel aplasia (complete absence of inner ear structures) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:microtia (wws) --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:microtia (wws) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:neonatal cystic lesions of the pinnae --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:neonatal cystic lesions of the pinnae | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:normal cochlear microphonics --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:normal cochlear microphonics | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:preauricular fistulas, bilateral --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:preauricular fistulas, bilateral | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:preauricular skin furrow --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:preauricular skin furrow | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:presbycusis --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:presbycusis | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:recurrent ear infections --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:recurrent ear infections | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:recurrent otitis media --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:recurrent otitis media | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:sensorineural deafness (onset in the second decade in 25 to 30% of patients) --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:sensorineural deafness (onset in the second decade in 25 to 30% of patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:sensorineural hearing loss (20% of patients) --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:sensorineural hearing loss (20% of patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:sensorineural hearing loss, mild (rare) --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:sensorineural hearing loss, mild (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:sensorineural, conductive, or mixed hearing loss --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:sensorineural, conductive, or mixed hearing loss | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:short ear --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:short ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:simplified helices --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:simplified helices | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:small external auditory canals --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:small external auditory canals | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:small pits anterior to the helix (1 patient) --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:small pits anterior to the helix (1 patient) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:stenotic ear canals (30%) --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:stenotic ear canals (30%) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:unconnected or fused stapes and incus --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:unconnected or fused stapes and incus | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:unfolded superior helices --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:unfolded superior helices | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:unilateral external ear deformity --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:unilateral external ear deformity | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:uplifted earlobes --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:uplifted earlobes | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:upturned lobes --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=en:upturned lobes | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 presbyacousie --- r_associated #0: 31 --> en:bilateral hypoplastic cochlea n1=presbyacousie | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=31 en:a subset of patients have hearing loss --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:a subset of patients have hearing loss | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:abnormal amplitude modulation detection --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:abnormal amplitude modulation detection | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:abnormally folded helix --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:abnormally folded helix | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:abnormally formed ears --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:abnormally formed ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:absent earlobe --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:absent earlobe | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:atrophy of cochlear and vestibular fibrocytes --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:atrophy of cochlear and vestibular fibrocytes | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:auditory canal stenosis --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:auditory canal stenosis | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:aural atresia, congenital --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:aural atresia, congenital | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:cleft at the superior portion of the pinna --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:cleft at the superior portion of the pinna | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:cutlet --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:cutlet | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:cystic dilatation of cochlea and vestibulum --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:cystic dilatation of cochlea and vestibulum | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:deafness, congenital sensorineural, severe to profound --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:deafness, congenital sensorineural, severe to profound | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:deafness, prelingual, profound (affects all frequencies) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:deafness, prelingual, profound (affects all frequencies) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:deafness, profound, affects all frequencies --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:deafness, profound, affects all frequencies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:disjunction of otherwise normal lobule from remainder of ear --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:disjunction of otherwise normal lobule from remainder of ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:dorsally rotated ears --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:dorsally rotated ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:ear neoplasm --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:ear neoplasm | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:excessive cerumen --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:excessive cerumen | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:external ear defects (47%) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:external ear defects (47%) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:flat audiogram --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:flat audiogram | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:hearing impairment (in 1/4 patients) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:hearing impairment (in 1/4 patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:hearing impairment, mild (2 patients) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:hearing impairment, mild (2 patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:hearing loss has been reported in some adults with severe disease --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:hearing loss has been reported in some adults with severe disease | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:hearing loss, congenital profound --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, congenital profound | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:hearing loss, progressive (in some patients) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, progressive (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:hearing loss, sensorineural (in 2 patients) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural (in 2 patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:hearing loss, sensorineural (in patients with larger deletions) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural (in patients with larger deletions) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:hearing loss, sensorineural (type ii) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural (type ii) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:hearing loss, sensorineural (variable) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural (variable) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:hearing loss, sensorineural, bilateral, moderate-to-severe --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:hearing loss, sensorineural, severe to profound --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural, severe to profound | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:hearing loss, severe to profound, affecting all frequencies --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, severe to profound, affecting all frequencies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:hearing threshold at or above 90 db at all frequencies tested (0.25-8.0 khz) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:hearing threshold at or above 90 db at all frequencies tested (0.25-8.0 khz) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:hypoplastic malleus (1 patient) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:hypoplastic malleus (1 patient) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:hypoplastic, overfolded helices --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:hypoplastic, overfolded helices | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:increased posterior angulation --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:increased posterior angulation | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:large dysplastic ears --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:large dysplastic ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:large ears (37%) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:large ears (37%) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:large pinnae --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:large pinnae | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:lobule creases --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:lobule creases | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:low-set ears (45%) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:low-set ears (45%) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:low-set ears (in 2/4 patients) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:low-set ears (in 2/4 patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:low-set ears (rare) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:low-set ears (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:low-set, malformed ears --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:low-set, malformed ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:malformed pinnae (30-60% of patients) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:malformed pinnae (30-60% of patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:microtia (30-60% of patients) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:microtia (30-60% of patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:microtia (in some patients) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:microtia (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:middle ear --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:middle ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:mild cochlear hearing loss (1 patient) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:mild cochlear hearing loss (1 patient) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:mondini malformation --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:mondini malformation | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:narrow external ear canals (1 patient) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:narrow external ear canals (1 patient) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:no vestibular impairment --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:no vestibular impairment | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:oae responses may decrease with age or use of hearing aids --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:oae responses may decrease with age or use of hearing aids | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:pinna modeling anomalies --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:pinna modeling anomalies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:prelingual onset --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:prelingual onset | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:progressive, low frequency sensorineural hearing loss --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:progressive, low frequency sensorineural hearing loss | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:recurrent otitis media (18%) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:recurrent otitis media (18%) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:rudimentary --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:rudimentary | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:sensorineural hearing loss (3 patients) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:sensorineural hearing loss (3 patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:sensorineural hearing loss (in 1 of 3 patients) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:sensorineural hearing loss (in 1 of 3 patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:sensorineural hearing loss (uncommon) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:sensorineural hearing loss (uncommon) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:serous otitis --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:serous otitis | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:small, simple ears --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:small, simple ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:squared-off ears --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:squared-off ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:tinnitus (variable) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:tinnitus (variable) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:tinnitus, bilateral (in some patients) --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:tinnitus, bilateral (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:u-shaped audiogram --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:u-shaped audiogram | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:underdeveloped tragus --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=en:underdeveloped tragus | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 médecin ORL --- r_associated #0: 30 --> en:bilateral hypoplastic cochlea n1=médecin ORL | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30 en:abnormal auditory temporal processes --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:abnormal auditory temporal processes | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:abnormal brain auditory evoked responses (baer) --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:abnormal brain auditory evoked responses (baer) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:abnormal folded pinna --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:abnormal folded pinna | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:abnormal speech discrimination --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:abnormal speech discrimination | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:abnormality of the middle ear --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:abnormality of the middle ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:absent lobules --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:absent lobules | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:absent or abnormal otoacoustic emissions --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:absent or abnormal otoacoustic emissions | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:absent vestibular function (caloric test) --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:absent vestibular function (caloric test) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:acute otitis media/myringitis --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:acute otitis media/myringitis | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:air-bone gap of greater than 20 db across 0.5 to 2 khz --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:air-bone gap of greater than 20 db across 0.5 to 2 khz | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:atresia of the external auditory canal --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:atresia of the external auditory canal | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:atretic ear canals --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:atretic ear canals | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:audiogram may be ascending --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:audiogram may be ascending | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:conductive hearing loss --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:conductive hearing loss | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:crumpled ear (76%) --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:crumpled ear (76%) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:cupped pinna --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:cupped pinna | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:deafness, early-onset mixed conductive and sensorineural --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:deafness, early-onset mixed conductive and sensorineural | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:deafness, moderate-severe (onset in third decade) --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:deafness, moderate-severe (onset in third decade) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:deafness, sensorineural, mild (rare) --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:deafness, sensorineural, mild (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:external ear defects --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:external ear defects | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:flattened antihelix --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:flattened antihelix | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:folded helix --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:folded helix | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:hearing impairment may occur --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:hearing impairment may occur | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:hearing loss affects all frequencies --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:hearing loss affects all frequencies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:hearing loss, bilateral sensorineural (profound) --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, bilateral sensorineural (profound) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:hearing loss, late-onset sensorineural, mild-to moderate (less common) --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, late-onset sensorineural, mild-to moderate (less common) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:hearing loss, postlingual progressive sensorineural --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, postlingual progressive sensorineural | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies) --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies) --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:hearing loss, sensorineural, progressive (childhood-onset) --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural, progressive (childhood-onset) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:high-frequency tinnitus at onset --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:high-frequency tinnitus at onset | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:large anteverted ears (rare) --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:large anteverted ears (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:large anteverted pinnae (90% males, 40% females) --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:large anteverted pinnae (90% males, 40% females) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:large, floppy ears --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:large, floppy ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:left ear --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:left ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:low-frequency sensorineural hearing impairment --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:low-frequency sensorineural hearing impairment | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:minor auricular anomalies --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:minor auricular anomalies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:minor ear anomalies (in some patients) --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:minor ear anomalies (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:misshapen ear --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:misshapen ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:narrowed external ear canal (30% of patients) --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:narrowed external ear canal (30% of patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:other symptom/complaint of ear --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:other symptom/complaint of ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:otorrhea --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:otorrhea | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:overfolded, rumpled ears --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:overfolded, rumpled ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:poorly formed ears --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:poorly formed ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:posterior helical indentations --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:posterior helical indentations | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:posteriorly rotated ears (female) --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:posteriorly rotated ears (female) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:presbyacusis --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:presbyacusis | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:progressive cartilaginous ossification of pinnae --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:progressive cartilaginous ossification of pinnae | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:prominent ears (rare) --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:prominent ears (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:recurrent otitis media in infancy --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:recurrent otitis media in infancy | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:relatively long ears --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:relatively long ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:right ear --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:right ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:sensorineural deafness (rare) --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:sensorineural deafness (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:sensorineural hearing impairment (less common) --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:sensorineural hearing impairment (less common) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:sensorineural hearing loss (1 family) --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:sensorineural hearing loss (1 family) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:sensorineural hearing loss (early-onset form) --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:sensorineural hearing loss (early-onset form) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:soft auricles --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:soft auricles | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:tinnitus --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:tinnitus | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:tinnitus (in some patients) --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:tinnitus (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:transient evoked otoacoustic emissions cannot be detected --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:transient evoked otoacoustic emissions cannot be detected | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:unravelling of superior helices --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:unravelling of superior helices | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:vestibular dysfunction (in some patients) --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:vestibular dysfunction (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:vestibular hypofunction --- r_associated #0: 29 --> en:bilateral hypoplastic cochlea n1=en:vestibular hypofunction | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=29 en:abnormal brainstem auditory evoked potentials (baep) --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:abnormal brainstem auditory evoked potentials (baep) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:abnormal gap detection --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:abnormal gap detection | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:abnormality of the helix --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:abnormality of the helix | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:absent ipsilateral middle ear muscle reflexes (in older patients) --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:absent ipsilateral middle ear muscle reflexes (in older patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:absent or decreased auditory brainstem responses --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:absent or decreased auditory brainstem responses | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:anterior creases of earlobe --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:anterior creases of earlobe | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:anteverted ears --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:anteverted ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:anteverted pinnae --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:anteverted pinnae | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:cleft lobules --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:cleft lobules | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:conductive hearing loss, mild bilateral (rare) --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:conductive hearing loss, mild bilateral (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:cup-shaped ears (30-60% of patients) --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:cup-shaped ears (30-60% of patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:deafness, conductive (in some patients) --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:deafness, conductive (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:deafness, secondary to cranial hyperostosis --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:deafness, secondary to cranial hyperostosis | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:deafness, sensorineural (reported in 1 family) --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:deafness, sensorineural (reported in 1 family) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:downward sloping audiogram --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:downward sloping audiogram | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:hearing loss first affects high frequencies --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:hearing loss first affects high frequencies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:hearing loss, congenital sensorineural, moderate-severe --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, congenital sensorineural, moderate-severe | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:hearing loss, more severe at lower frequencies --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, more severe at lower frequencies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:hearing loss, profound prelingual sensorineural --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, profound prelingual sensorineural | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:hearing loss, progressive, starting in infancy --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, progressive, starting in infancy | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:hearing loss, sensorineural (in one family) --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural (in one family) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:hearing loss, sensorineural (in some) --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural (in some) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:hearing loss, sensorineural, mid-frequency (in some patients) --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural, mid-frequency (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:incomplete separation of the cochlea from the internal auditory canal --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:incomplete separation of the cochlea from the internal auditory canal | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:large ears (2p21del) --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:large ears (2p21del) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:long, lobulated ears --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:long, lobulated ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:loss of high frequencies at onset --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:loss of high frequencies at onset | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:low-set ears (28%) --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:low-set ears (28%) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:malformations of the auditory ossicles --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:malformations of the auditory ossicles | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:narrow intertragic notch --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:narrow intertragic notch | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:no reproducible waves i, iii, or v at high intensities --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:no reproducible waves i, iii, or v at high intensities | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:normal otoacoustic emissions (oae), indicating intact outer ear hair cell function --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:normal otoacoustic emissions (oae), indicating intact outer ear hair cell function | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:occasional conductive hearing loss --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:occasional conductive hearing loss | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:poorly shaped ears --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:poorly shaped ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:posteriorly rotated ears (in some patients) --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:posteriorly rotated ears (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:preauricular pits (70-80% of patients) --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:preauricular pits (70-80% of patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:progressive conductive hearing impairment --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:progressive conductive hearing impairment | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:progressive mixed conductive and sensorineural hearing loss --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:progressive mixed conductive and sensorineural hearing loss | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:prominent helices --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:prominent helices | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:protruding lobules --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:protruding lobules | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:pseudomembranous inflammation of the middle ear --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:pseudomembranous inflammation of the middle ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:sensation of blocked ears --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:sensation of blocked ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:sensorineural deafness, postlingual, progressive --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:sensorineural deafness, postlingual, progressive | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:sensorineural deafness, variable (in 1 family) --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:sensorineural deafness, variable (in 1 family) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:sensorineural hearing loss (less common) --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:sensorineural hearing loss (less common) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:severe narrowing of cartilagenous auditory canal (in homozygotes) --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:severe narrowing of cartilagenous auditory canal (in homozygotes) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:shallow skin dimple on posterior surface of ear --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:shallow skin dimple on posterior surface of ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:small auricles --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:small auricles | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:small ears with large lobules --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:small ears with large lobules | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:small pinna --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:small pinna | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:stiff, prominent pinnae --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:stiff, prominent pinnae | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:structural inner ear abnormalities (in patients with larger deletions) --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:structural inner ear abnormalities (in patients with larger deletions) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:vestibular areflexia --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:vestibular areflexia | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:vestibular areflexia, complete --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:vestibular areflexia, complete | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:vestibular hypofunction (rare) --- r_associated #0: 28 --> en:bilateral hypoplastic cochlea n1=en:vestibular hypofunction (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=28 en:abnormal semicircular canals --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:abnormal semicircular canals | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:absent auditory canals (wws) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:absent auditory canals (wws) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:absent brainstem auditory-evoked responses --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:absent brainstem auditory-evoked responses | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:absent external auditory canals --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:absent external auditory canals | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:affects all frequencies --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:affects all frequencies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:asymmetry of the ears --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:asymmetry of the ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:aural fullness --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:aural fullness | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:auricular clefts --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:auricular clefts | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:congenital ear anomaly nos (disorder) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:congenital ear anomaly nos (disorder) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:cup-shaped auricles --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:cup-shaped auricles | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:cupped ears (in some patients) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:cupped ears (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:deafness (in 1 of 2 families) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:deafness (in 1 of 2 families) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:deafness (sensorineural or mixed sensorineural and conductive) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:deafness (sensorineural or mixed sensorineural and conductive) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:deafness affects all frequencies --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:deafness affects all frequencies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:deafness due to bilateral cochlear malformation (rare) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:deafness, congenital sensorineural, profound (in some patients) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:deafness, congenital sensorineural, profound (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:deafness, sensorineural, profound (prelingual onset) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:deafness, sensorineural, profound (prelingual onset) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:disturbance of equilibrium --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:disturbance of equilibrium | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:downsloping audiogram --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:downsloping audiogram | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:ear cartilage calcification --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:ear cartilage calcification | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:ear pain/earache --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:ear pain/earache | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:ear pits, posterior helical --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:ear pits, posterior helical | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:endolymphatic sac tumors (elsts) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:endolymphatic sac tumors (elsts) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:external auditory canal narrow --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:external auditory canal narrow | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:fear of ear disease --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:fear of ear disease | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:glue ear --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:glue ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:hearing loss (variable) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:hearing loss (variable) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:hearing loss, conductive (in some patients) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, conductive (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:hearing loss, high frequency, slowly progressive (onset in early childhood) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, high frequency, slowly progressive (onset in early childhood) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:hearing loss, mixed (in some patients) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, mixed (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:hearing loss, sensorineural (in sister) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural (in sister) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:hearing loss, sensorineural, mild progressive (in some patients) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural, mild progressive (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:hyperfolded ears --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:hyperfolded ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:hypertrophic auricular cartilage --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:hypertrophic auricular cartilage | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:incomplete atretic plate --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:incomplete atretic plate | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:large fleshy earlobes --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:large fleshy earlobes | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:linear ear lobe creases --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:linear ear lobe creases | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:loss of hearing (45%) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:loss of hearing (45%) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:low-set ears (1 patient) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:low-set ears (1 patient) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:narrow ear lobes --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:narrow ear lobes | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:narrow ears --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:narrow ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:narrowed external ear canal --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:narrowed external ear canal | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:near-stenosis of bony portion of auditory canal --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:near-stenosis of bony portion of auditory canal | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:otitis media, recurrent (rare) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:otitis media, recurrent (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:otitis with effusion --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:otitis with effusion | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:poorly formed pinnae --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:poorly formed pinnae | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:pre- and post-auricular skin or cartilaginous tags --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:pre- and post-auricular skin or cartilaginous tags | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:preauricular sinus --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:preauricular sinus | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:presbycousis --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:presbycousis | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:progressive hearing impairment --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:progressive hearing impairment | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:progressive hearing loss (in some) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:progressive hearing loss (in some) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:progressive sensorineural hearing impairment --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:progressive sensorineural hearing impairment | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:prominent earlobes (in some patients) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:prominent earlobes (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:protruding ears --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:protruding ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:sensorineural hearing loss, progressive bilateral postlingual --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:sensorineural hearing loss, progressive bilateral postlingual | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:simple helix --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:simple helix | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:small, malformed ears --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:small, malformed ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:supraauricular pit --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:supraauricular pit | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:thick earlobes --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:thick earlobes | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:thick ears --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:thick ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:tinnitus (rare) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:tinnitus (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:triangular-shaped ears --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:triangular-shaped ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:uplift of earlobes (in some patients) --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:uplift of earlobes (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:vertigo, episodic --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:vertigo, episodic | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:warsaw breakage syndrome --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:warsaw breakage syndrome | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:wide, flattened earlobes --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=en:wide, flattened earlobes | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 esgourde --- r_associated #0: 27 --> en:bilateral hypoplastic cochlea n1=esgourde | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27 en:'tilted' ears --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:'tilted' ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:abnormal auditory brainstem responses --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:abnormal auditory brainstem responses | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:abnormal helices, antihelices and lobules --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:abnormal helices, antihelices and lobules | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:abnormal or absent auditory nerve and brainstem responses --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:abnormal or absent auditory nerve and brainstem responses | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:abnormality of the middle ear ossicles --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:abnormality of the middle ear ossicles | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:absence of the cochlear nerves (reported in 1 patient) --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:absence of the cochlear nerves (reported in 1 patient) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:absent stapedial reflex --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:absent stapedial reflex | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:acoustic trauma --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:acoustic trauma | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:affects mid- to high-frequencies --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:affects mid- to high-frequencies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:aplasia of the inner ear --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:aplasia of the inner ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:bat ear --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:bat ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:bilateral conductive hearing loss (rare) --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:bilateral conductive hearing loss (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:cochlear malformation defect (mondini dysplasia) (less common) --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:cochlear malformation defect (mondini dysplasia) (less common) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:deafness, profound congenital sensorineural --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:deafness, profound congenital sensorineural | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:dysplastic ears (in some patients) --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:dysplastic ears (in some patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:entire ear --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:entire ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:eustachian tube salpingitis --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:eustachian tube salpingitis | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:flat or shallow u-shaped audiogram --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:flat or shallow u-shaped audiogram | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:hearing disorder (1 patient) --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:hearing disorder (1 patient) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:hearing impairment, asymmetric (in some patients with hsan2d) --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:hearing impairment, asymmetric (in some patients with hsan2d) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:hearing loss (in 2 members of 1 family) --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:hearing loss (in 2 members of 1 family) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:hearing loss, congenital, profound (250-8,000 hz) --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, congenital, profound (250-8,000 hz) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:hearing loss, high-frequency (onset in childhood-adolescence) --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, high-frequency (onset in childhood-adolescence) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:hearing loss, profound congenital sensorineural --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, profound congenital sensorineural | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges) --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:hypoplasia of the cochlea --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:hypoplasia of the cochlea | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:large appearing ears --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:large appearing ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:large, dysmorphic ears --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:large, dysmorphic ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:large, low-set ears --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:large, low-set ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:loss of vestibular reflexes --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:loss of vestibular reflexes | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:low-frequency conductive hearing loss --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:low-frequency conductive hearing loss | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:low-set ears (3 patients) --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:low-set ears (3 patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:malformed ossicular chain --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:malformed ossicular chain | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:mild to moderate hearing loss across most frequencies --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:mild to moderate hearing loss across most frequencies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:narrow auditory canals (rare) --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:narrow auditory canals (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:near-stenosis of bony portion of auditory canal (in homozygotes) --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:near-stenosis of bony portion of auditory canal (in homozygotes) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:neural hearing loss --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:neural hearing loss | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:no auditory brainstem response (abr) --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:no auditory brainstem response (abr) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:normal middle ear pressures on tympanometry --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:normal middle ear pressures on tympanometry | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:normal vestibular function --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:normal vestibular function | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:normal vestibular response --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:normal vestibular response | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:otoneurologic disturbances --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:otoneurologic disturbances | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:poorly folded ears --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:poorly folded ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:retroverted ears --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:retroverted ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:rudimentary ear --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:rudimentary ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:sensorineural hearing loss has been reported --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:sensorineural hearing loss has been reported | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:sensorineural hearing loss, mild to moderate --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:sensorineural hearing loss, mild to moderate | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:severe to profound deafness --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:severe to profound deafness | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:short ears (in 1 family) --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:short ears (in 1 family) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:small ears (female) --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:small ears (female) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:small/rudimentary tragus, antitragus and lobule --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:small/rudimentary tragus, antitragus and lobule | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:sticking-out ear --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:sticking-out ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:structure of lymphatic vessel of ear --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:structure of lymphatic vessel of ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:thickened helices --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:thickened helices | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:underdeveloped nasal alae --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:underdeveloped nasal alae | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:vertiginous syndrome --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:vertiginous syndrome | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:vestibular abnormalities (variable) --- r_associated #0: 26 --> en:bilateral hypoplastic cochlea n1=en:vestibular abnormalities (variable) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26 en:abnormal ears --- r_associated #0: 25 --> en:bilateral hypoplastic cochlea n1=en:abnormal ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=25 en:absent external auditory meatus --- r_associated #0: 25 --> en:bilateral hypoplastic cochlea n1=en:absent external auditory meatus | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=25 en:anomalous middle ear bones --- r_associated #0: 25 --> en:bilateral hypoplastic cochlea n1=en:anomalous middle ear bones | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=25 en:congenital absence of external ear --- r_associated #0: 25 --> en:bilateral hypoplastic cochlea n1=en:congenital absence of external ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=25 en:roll-head --- r_associated #0: 25 --> en:bilateral hypoplastic cochlea n1=en:roll-head | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=25 en:abnormally folded ears --- r_associated #0: 24 --> en:bilateral hypoplastic cochlea n1=en:abnormally folded ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=24 en:absence of vestibular evoked myogenic potentials (rare) --- r_associated #0: 24 --> en:bilateral hypoplastic cochlea n1=en:absence of vestibular evoked myogenic potentials (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=24 en:chronic otitis other infection ear --- r_associated #0: 24 --> en:bilateral hypoplastic cochlea n1=en:chronic otitis other infection ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=24 en:external ear --- r_associated #0: 24 --> en:bilateral hypoplastic cochlea n1=en:external ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=24 en:inner ear --- r_associated #0: 24 --> en:bilateral hypoplastic cochlea n1=en:inner ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=24 en:absent cochlear microphonic (in older patients) --- r_associated #0: 23 --> en:bilateral hypoplastic cochlea n1=en:absent cochlear microphonic (in older patients) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=23 en:approximately 0.7db per year hearing loss at all frequencies --- r_associated #0: 23 --> en:bilateral hypoplastic cochlea n1=en:approximately 0.7db per year hearing loss at all frequencies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=23 en:atretic auditory canal --- r_associated #0: 23 --> en:bilateral hypoplastic cochlea n1=en:atretic auditory canal | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=23 en:attached ear lobes --- r_associated #0: 23 --> en:bilateral hypoplastic cochlea n1=en:attached ear lobes | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=23 en:audiogram is gently sloping or flat --- r_associated #0: 23 --> en:bilateral hypoplastic cochlea n1=en:audiogram is gently sloping or flat | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=23 en:audiogram shows sloping configuration --- r_associated #0: 23 --> en:bilateral hypoplastic cochlea n1=en:audiogram shows sloping configuration | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=23 en:abnormality of the outer ear --- r_associated #0: 22 --> en:bilateral hypoplastic cochlea n1=en:abnormality of the outer ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=22 en:anteriorly rotated ears --- r_associated #0: 22 --> en:bilateral hypoplastic cochlea n1=en:anteriorly rotated ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=22 en:auriculo-condylar syndrome --- r_associated #0: 22 --> en:bilateral hypoplastic cochlea n1=en:auriculo-condylar syndrome | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=22 en:bilateral congenital profound sensorineural hearing loss --- r_associated #0: 22 --> en:bilateral hypoplastic cochlea n1=en:bilateral congenital profound sensorineural hearing loss | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=22 en:escalope --- r_associated #0: 22 --> en:bilateral hypoplastic cochlea n1=en:escalope | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=22 en:hearing complaints (excluding h84-86) --- r_associated #0: 22 --> en:bilateral hypoplastic cochlea n1=en:hearing complaints (excluding h84-86) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=22 surdi-mutité --- r_associated #0: 22 --> en:bilateral hypoplastic cochlea n1=surdi-mutité | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=22 surdimutité --- r_associated #0: 22 --> en:bilateral hypoplastic cochlea n1=surdimutité | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=22 en:abnormal bridge connecting the crus of the helix and antihelix --- r_associated #0: 21 --> en:bilateral hypoplastic cochlea n1=en:abnormal bridge connecting the crus of the helix and antihelix | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=21 en:apical cartilage deformity --- r_associated #0: 21 --> en:bilateral hypoplastic cochlea n1=en:apical cartilage deformity | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=21 en:other auditory injuries --- r_associated #0: 21 --> en:bilateral hypoplastic cochlea n1=en:other auditory injuries | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=21 en:otolaryngologist --- r_associated #0: 21 --> en:bilateral hypoplastic cochlea n1=en:otolaryngologist | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=21 en:otorhinolaryngologist --- r_associated #0: 21 --> en:bilateral hypoplastic cochlea n1=en:otorhinolaryngologist | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=21 en:and throat --- r_associated #0: 20 --> en:bilateral hypoplastic cochlea n1=en:and throat | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=20 en:nose and throat --- r_associated #0: 20 --> en:bilateral hypoplastic cochlea n1=en:nose and throat | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=20 nose --- r_associated #0: 20 --> en:bilateral hypoplastic cochlea n1=nose | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=20 Trouble de l'équilibre --- r_associated #0: 15 --> en:bilateral hypoplastic cochlea n1=Trouble de l'équilibre | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=15 en:dizzy spells --- r_associated #0: 15 --> en:bilateral hypoplastic cochlea n1=en:dizzy spells | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=15 en:giddiness --- r_associated #0: 15 --> en:bilateral hypoplastic cochlea n1=en:giddiness | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=15 en:scatterbrain --- r_associated #0: 15 --> en:bilateral hypoplastic cochlea n1=en:scatterbrain | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=15 vertiges --- r_associated #0: 15 --> en:bilateral hypoplastic cochlea n1=vertiges | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=15 vertigineux --- r_associated #0: 15 --> en:bilateral hypoplastic cochlea n1=vertigineux | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=15 Étourdi --- r_associated #0: 15 --> en:bilateral hypoplastic cochlea n1=Étourdi | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=15 Étourdie --- r_associated #0: 15 --> en:bilateral hypoplastic cochlea n1=Étourdie | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=15 étourdie --- r_associated #0: 15 --> en:bilateral hypoplastic cochlea n1=étourdie | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=15 étourdies --- r_associated #0: 15 --> en:bilateral hypoplastic cochlea n1=étourdies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=15 étourdis --- r_associated #0: 15 --> en:bilateral hypoplastic cochlea n1=étourdis | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=15 étourdissements --- r_associated #0: 15 --> en:bilateral hypoplastic cochlea n1=étourdissements | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=15 Hyperacousie --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=Hyperacousie | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 Oto-rhino-laryngologiste --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=Oto-rhino-laryngologiste | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 Otorhinolaryngologiste --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=Otorhinolaryngologiste | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 Presbyacousie --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=Presbyacousie | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 ankylose stapédo-vestibulaire --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=ankylose stapédo-vestibulaire | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 ankylose stapédo-vestibulaire l.f. --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=ankylose stapédo-vestibulaire l.f. | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 en:deaf-muteness --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=en:deaf-muteness | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 en:deaf-mutism --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=en:deaf-mutism | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 en:forward protrusion of the ear --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=en:forward protrusion of the ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 en:hearing defect --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=en:hearing defect | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 en:hearing deficiency --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=en:hearing deficiency | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 en:lughole --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=en:lughole | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 en:prominent shell ear --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=en:prominent shell ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 en:protruding ear --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=en:protruding ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 en:schitzel --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=en:schitzel | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 en:shell ear --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=en:shell ear | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 en:speech difficulties due to deafness --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=en:speech difficulties due to deafness | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 oreille moyenne --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=oreille moyenne | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 otite moyenne adhésive --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=otite moyenne adhésive | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 prérupture utérine (syndrome de) --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=prérupture utérine (syndrome de) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 tête de linotte --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=tête de linotte | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 Étourdissements --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=Étourdissements | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 à priori --- r_associated #0: 10 --> en:bilateral hypoplastic cochlea n1=à priori | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=10 Sensation de rotation --- r_associated #0: 5 --> en:bilateral hypoplastic cochlea n1=Sensation de rotation | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=5 ordinateur (anesthésie pilotée par) --- r_associated #0: 5 --> en:bilateral hypoplastic cochlea n1=ordinateur (anesthésie pilotée par) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=5 escalope --- r_associated #0: -20 --> en:bilateral hypoplastic cochlea n1=escalope | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=-20