'en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies'
(id=6814641 ; fe=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies ; type=1 ; niveau=200 ;
luminosité=25 ;
somme entrante=25980 creation date=2017-06-25 touchdate=2025-12-23 11:10:46.000) ≈ 658 relations sortantes
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 43 / 1 ->
en:hearing loss, neural type
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, neural type | rel=r_associated | relid=0 | w=43
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 42 / 0.977 ->
en:deafness, prelingual, profound (affects all frequencies)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, prelingual, profound (affects all frequencies) | rel=r_associated | relid=0 | w=42
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 42 / 0.977 ->
en:external ears rudimentary
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:external ears rudimentary | rel=r_associated | relid=0 | w=42
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 42 / 0.977 ->
en:hearing loss, sensorineural, progressive (childhood-onset)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural, progressive (childhood-onset) | rel=r_associated | relid=0 | w=42
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 42 / 0.977 ->
en:inner ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:inner ear | rel=r_associated | relid=0 | w=42
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 41 / 0.953 ->
en:acute otitis media/myringitis
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:acute otitis media/myringitis | rel=r_associated | relid=0 | w=41
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 41 / 0.953 ->
en:hearing deficits (28% of adults)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing deficits (28% of adults) | rel=r_associated | relid=0 | w=41
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 41 / 0.953 ->
en:large anteverted ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:large anteverted ears | rel=r_associated | relid=0 | w=41
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 40 / 0.93 ->
en:abnormal helices, antihelices and lobules
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormal helices, antihelices and lobules | rel=r_associated | relid=0 | w=40
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 39 / 0.907 ->
en:anteriorly rotated ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:anteriorly rotated ears | rel=r_associated | relid=0 | w=39
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 39 / 0.907 ->
en:deafness, unilateral, childhood onset
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, unilateral, childhood onset | rel=r_associated | relid=0 | w=39
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 38 / 0.884 ->
en:hearing loss, congenital sensorineural, moderate-severe
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, congenital sensorineural, moderate-severe | rel=r_associated | relid=0 | w=38
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 36 / 0.837 ->
en:absent ipsilateral middle ear muscle reflexes (in older patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:absent ipsilateral middle ear muscle reflexes (in older patients) | rel=r_associated | relid=0 | w=36
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 36 / 0.837 ->
en:conductive hearing loss, bilateral
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:conductive hearing loss, bilateral | rel=r_associated | relid=0 | w=36
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:abnormally folded ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormally folded ears | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:absent earlobe
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:absent earlobe | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:affects all frequencies
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:affects all frequencies | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:anomalous middle ear bones
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:anomalous middle ear bones | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:asymmetry of the ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:asymmetry of the ears | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:aural fullness
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:aural fullness | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:bilateral hypoplastic cochlea
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:chronic otitis other infection ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:chronic otitis other infection ear | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:cochleosaccular dysplasia
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:cochleosaccular dysplasia | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:deafness, profound, by 6th decade
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, profound, by 6th decade | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:deafness, sensorineural (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, sensorineural (in some patients) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:deafness, sensorineural, especially affecting high frequencies (in about 55% of males and 45% of females)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, sensorineural, especially affecting high frequencies (in about 55% of males and 45% of females) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:deafness, sensorineural, profound (prelingual onset)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, sensorineural, profound (prelingual onset) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:dizziness
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:dizziness | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:ear constriction (97%)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:ear constriction (97%) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:endolymphatic hydrops, delayed onset
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:endolymphatic hydrops, delayed onset | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:eustachian tube salpingitis
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:eustachian tube salpingitis | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:fear of ear disease
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:fear of ear disease | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:flat or shallow u-shaped audiogram
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:flat or shallow u-shaped audiogram | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:hearing impairment (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing impairment (in some patients) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:hearing impairment, sensorineural, mild
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing impairment, sensorineural, mild | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:hearing loss, bilateral progressive post-lingual
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, bilateral progressive post-lingual | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:hearing loss, congenital, profound (250-8,000 hz)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, congenital, profound (250-8,000 hz) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:hearing loss, sensorineural (reported in 1 patient)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural (reported in 1 patient) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:hearing loss, sensorineural, severe to profound
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural, severe to profound | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:impaired tympanic membrane mobility
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:impaired tympanic membrane mobility | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:large prominent ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:large prominent ears | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:lobule may be separately from the rest of the external ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:lobule may be separately from the rest of the external ear | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:loss of vestibular caloric response
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:loss of vestibular caloric response | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:low-frequency conductive hearing loss
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:low-frequency conductive hearing loss | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:low-set and rotated ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:low-set and rotated ears | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:low-set ears (28%)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:low-set ears (28%) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:middle ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:middle ear | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:other auditory injuries
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:other auditory injuries | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 35 / 0.814 ->
en:right ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:right ear | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:abnormal amplitude modulation detection
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormal amplitude modulation detection | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:absent vestibular function (caloric test)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:absent vestibular function (caloric test) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:air-bone gap of greater than 20 db across 0.5 to 2 khz
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:air-bone gap of greater than 20 db across 0.5 to 2 khz | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:apical cartilage deformity
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:apical cartilage deformity | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:atretic auditory canal
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:atretic auditory canal | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:audiogram is gently sloping or flat
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:audiogram is gently sloping or flat | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:cup-shaped auricles
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:cup-shaped auricles | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:deafness
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:deafness, sensorineural (severe to profound)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, sensorineural (severe to profound) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:ear pits, posterior helical
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:ear pits, posterior helical | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:ears deficient in cartilage
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:ears deficient in cartilage | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:expansion of helical fold at superior point of true longitudinal axis of ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:expansion of helical fold at superior point of true longitudinal axis of ear | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:flattened
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:flattened | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:hearing complaints (excluding h84-86)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing complaints (excluding h84-86) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:hearing loss affects all frequencies
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss affects all frequencies | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:hearing loss, conductive (in one family)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, conductive (in one family) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:hearing loss, conductive (rare)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, conductive (rare) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:hearing loss, mixed, mild to severe (in heterozygotes)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, mixed, mild to severe (in heterozygotes) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:large auricle
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:large auricle | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:large earlobe
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:large earlobe | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:large, low-set ears (uncommon)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:large, low-set ears (uncommon) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:sensation of blocked ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensation of blocked ears | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 34 / 0.791 ->
en:tinnitus
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:tinnitus | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 32 / 0.744 ->
en:abnormal folded pinna
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormal folded pinna | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 32 / 0.744 ->
en:abnormal semicircular canals
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormal semicircular canals | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 32 / 0.744 ->
en:absence of vestibular evoked myogenic potentials (rare)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:absence of vestibular evoked myogenic potentials (rare) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 32 / 0.744 ->
en:absent stapedial reflex
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:absent stapedial reflex | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 32 / 0.744 ->
en:conductive and sensorineural hearing loss
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:conductive and sensorineural hearing loss | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 32 / 0.744 ->
en:cupped pinna
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:cupped pinna | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 32 / 0.744 ->
en:deafness in 30-50% of patients with skull involvement
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness in 30-50% of patients with skull involvement | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 32 / 0.744 ->
en:deafness, sensorineural, prelingual, profound
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, sensorineural, prelingual, profound | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 32 / 0.744 ->
en:deep-set ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deep-set ears | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 32 / 0.744 ->
en:hearing impairment
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing impairment | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 32 / 0.744 ->
en:hearing loss, sensorineural (in 1 ashkenazi patient)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural (in 1 ashkenazi patient) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 32 / 0.744 ->
en:hearing loss, sensorineural (in some cases)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural (in some cases) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 32 / 0.744 ->
en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 32 / 0.744 ->
en:hypoplastic malleus (1 patient)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hypoplastic malleus (1 patient) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 32 / 0.744 ->
en:hypoplastic semicircular canals
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hypoplastic semicircular canals | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 32 / 0.744 ->
en:keratotic plaque around ear meatus
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:keratotic plaque around ear meatus | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 32 / 0.744 ->
en:left ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:left ear | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 31 / 0.721 ->
en:absent brainstem auditory-evoked responses
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:absent brainstem auditory-evoked responses | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 31 / 0.721 ->
en:absent external auditory meatus
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:absent external auditory meatus | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 31 / 0.721 ->
en:atrophy of cochlear and vestibular fibrocytes
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:atrophy of cochlear and vestibular fibrocytes | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 31 / 0.721 ->
en:cochlear malformation
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:cochlear malformation | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 31 / 0.721 ->
en:conductive hearing loss to due otitis media
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:conductive hearing loss to due otitis media | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 31 / 0.721 ->
en:congenital small ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:congenital small ears | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 31 / 0.721 ->
en:decreased auditory brainstem responses
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:decreased auditory brainstem responses | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 31 / 0.721 ->
en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 31 / 0.721 ->
en:downward sloping or flat audiogram
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:downward sloping or flat audiogram | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 31 / 0.721 ->
en:fleshy ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:fleshy ears | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 31 / 0.721 ->
en:hearing impairment may occur
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing impairment may occur | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 31 / 0.721 ->
en:hearing loss, mild
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, mild | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 31 / 0.721 ->
en:hearing loss, moderate to severe, bilateral, nonprogressive
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, moderate to severe, bilateral, nonprogressive | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 31 / 0.721 ->
en:hearing loss, prelingual, severe to profound (affecting all frequencies)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, prelingual, severe to profound (affecting all frequencies) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 31 / 0.721 ->
en:hearing loss, sensorineural (in sister)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural (in sister) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 31 / 0.721 ->
en:large ear pinnae
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:large ear pinnae | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 31 / 0.721 ->
en:loss of hearing (45%)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:loss of hearing (45%) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 31 / 0.721 ->
en:low set ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:low set ears | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 31 / 0.721 ->
en:other symptom/complaint of ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:other symptom/complaint of ear | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 31 / 0.721 ->
en:otorrhea
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:otorrhea | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 31 / 0.721 ->
en:presbycusis
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:presbycusis | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:a subset of patients have hearing loss
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:a subset of patients have hearing loss | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:abnormal auditory brainstem responses
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormal auditory brainstem responses | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:abnormality of the pinna
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormality of the pinna | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:absent or abnormal otoacoustic emissions
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:absent or abnormal otoacoustic emissions | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:absent or decreased auditory brainstem responses
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:absent or decreased auditory brainstem responses | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:affects mid- to high-frequencies
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:affects mid- to high-frequencies | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:bat ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:bat ear | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:bilateral congenital profound sensorineural hearing loss
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:bilateral congenital profound sensorineural hearing loss | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:bilateral sensorineural hearing loss (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:bilateral sensorineural hearing loss (in some patients) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:cochlear degeneration
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:cochlear degeneration | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:complete bony atresia of medial portion of external auditory canal (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:complete bony atresia of medial portion of external auditory canal (in some patients) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:conductive hearing loss (in a subset of patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:conductive hearing loss (in a subset of patients) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:congenital atresia of external auditory canal
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:congenital atresia of external auditory canal | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:congenital ear anomaly nos (disorder)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:congenital ear anomaly nos (disorder) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:crumpled ear (76%)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:crumpled ear (76%) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:deafness, congenital sensorineural, profound (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, congenital sensorineural, profound (in some patients) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:deafness, sensorineural, variable
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, sensorineural, variable | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:disproportionately large ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:disproportionately large ears | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:downsloping audiogram
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:downsloping audiogram | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:ear | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:ear tag
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:ear tag | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:entire ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:entire ear | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:everted ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:external ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:external ear | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:external ear defects
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:external ear defects | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:hearing loss, congenital profound
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, congenital profound | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:hearing loss, initially conductive, later mixed conductive-sensorineural
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, initially conductive, later mixed conductive-sensorineural | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:hearing loss, sensorineural, due to auditory neuropathy
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural, due to auditory neuropathy | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:hearing normal
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing normal | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:hypoplastic superior helix
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hypoplastic superior helix | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:internal auditory canal hypoplasia
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:internal auditory canal hypoplasia | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:large, low-set ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:large, low-set ears | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:low-set, malformed ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:low-set, malformed ears | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:narrowed external ear canal
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:narrowed external ear canal | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:near-stenosis of bony portion of auditory canal (in homozygotes)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:near-stenosis of bony portion of auditory canal (in homozygotes) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:no deafness
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:no deafness | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:ossified pinnae
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:ossified pinnae | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:partial hearing loss
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:partial hearing loss | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:pointed upper helix
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:pointed upper helix | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:protruding right ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:protruding right ear | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:rudimentary ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:rudimentary ear | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:sclerosis of semicircular canals
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sclerosis of semicircular canals | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:sensorineural deafness (onset in the second decade in 25 to 30% of patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural deafness (onset in the second decade in 25 to 30% of patients) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:sensorineural deafness, variable (in 1 family)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural deafness, variable (in 1 family) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:sensorineural hearing impairment (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural hearing impairment (in some patients) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:sensorineural hearing loss (less common)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural hearing loss (less common) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:sensorineural hearing loss (uncommon)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural hearing loss (uncommon) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:sensorineural hearing loss, mild (rare)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural hearing loss, mild (rare) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:small ears with large lobules
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:small ears with large lobules | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:triangular-shaped ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:triangular-shaped ears | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:vertigo, episodic
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:vertigo, episodic | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:vestibular function defect (decreased in some, normal in other patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:vestibular function defect (decreased in some, normal in other patients) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 30 / 0.698 ->
en:vestibular hypofunction (rare)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:vestibular hypofunction (rare) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:aplasia of the inner ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:aplasia of the inner ear | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:auriculo-condylar syndrome
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:auriculo-condylar syndrome | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:blind fistula
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:blind fistula | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:chronic otitis media
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:chronic otitis media | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:cleft at the superior portion of the pinna
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:cleft at the superior portion of the pinna | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:cup-shaped ears (30-60% of patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:cup-shaped ears (30-60% of patients) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:cupped ears (finding)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:cupped ears (finding) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:deafness (variable)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness (variable) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:deafness, conductive (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, conductive (in some patients) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:deafness, profound congenital sensorineural
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, profound congenital sensorineural | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:deafness, profound, affects all frequencies
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, profound, affects all frequencies | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:deafness, sensorineural (45%)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, sensorineural (45%) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:deficient auricle
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deficient auricle | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:disjunction of otherwise normal lobule from remainder of ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:disjunction of otherwise normal lobule from remainder of ear | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:external auditory canal narrow
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:external auditory canal narrow | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:external ear defects (47%)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:external ear defects (47%) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:hearing loss (1 patient)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss (1 patient) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:hearing loss, bilateral sensorineural (profound)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, bilateral sensorineural (profound) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:hearing loss, sensorineural (in some)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural (in some) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:hearing loss, unilateral (rare)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, unilateral (rare) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:high-frequency tinnitus at onset
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:high-frequency tinnitus at onset | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:hypertrophic auricular cartilage
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hypertrophic auricular cartilage | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:hypoplasia of the cochlea
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hypoplasia of the cochlea | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:hypoplastic, overfolded helices
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hypoplastic, overfolded helices | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:large fleshy ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:large fleshy ears | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:long and prominent ear crus
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:long and prominent ear crus | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:malformations of the auditory ossicles
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:malformations of the auditory ossicles | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:microtia (30-60% of patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:microtia (30-60% of patients) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:minor auricular anomalies
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:minor auricular anomalies | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:minor ear anomalies (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:minor ear anomalies (in some patients) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:misshapen ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:misshapen ear | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:narrow ear lobes
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:narrow ear lobes | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:no hearing loss
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:no hearing loss | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:nonsyndromic sensorineural hearing loss
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:nonsyndromic sensorineural hearing loss | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:poorly formed ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:poorly formed ears | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:postauricular pit
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:postauricular pit | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:prelingual onset
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:prelingual onset | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:profound deafness
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:profound deafness | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:prominent lobules
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:prominent lobules | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:pulsatile tinnitus (tympanic paraganglioma)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:pulsatile tinnitus (tympanic paraganglioma) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:secretory otitis media
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:secretory otitis media | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:sensorineural deafness, postlingual, progressive
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural deafness, postlingual, progressive | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:sensorineural hearing loss
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural hearing loss | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:sensorineural hearing loss (early-onset form)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural hearing loss (early-onset form) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:sensorineural hearing loss (in 1 of 3 patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural hearing loss (in 1 of 3 patients) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:simplified helices
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:simplified helices | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:squared-off ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:squared-off ears | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:stenotic ear canals (30%)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:stenotic ear canals (30%) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:strabismus (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:strabismus (in some patients) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:structure of superior auricularis muscle
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:structure of superior auricularis muscle | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:superior semicircular canal dehiscence syndrome
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:superior semicircular canal dehiscence syndrome | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:tinnitus (variable)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:tinnitus (variable) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:upturned lobes
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:upturned lobes | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:vertiginous syndrome
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:vertiginous syndrome | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
en:vestibular hypofunction
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:vestibular hypofunction | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 29 / 0.674 ->
lésion traumatique superficielle de l'oreille
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=lésion traumatique superficielle de l'oreille | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:abnormal auditory temporal processes
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormal auditory temporal processes | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:absence of the cochlear nerves (reported in 1 patient)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:absence of the cochlear nerves (reported in 1 patient) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:anteverted ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:anteverted ears | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:atretic ear canals
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:atretic ear canals | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:attached ear lobes
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:attached ear lobes | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:attached ear lobules
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:attached ear lobules | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:audiogram shows sloping configuration
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:audiogram shows sloping configuration | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:cleft at the junction of the lobule and helix
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:cleft at the junction of the lobule and helix | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:cleft lobules
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:cleft lobules | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:cupped ears (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:cupped ears (in some patients) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:deafness, congenital sensorineural, severe to profound
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, congenital sensorineural, severe to profound | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:deafness, nonprogressive, moderate
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, nonprogressive, moderate | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:deafness, sensorineural, severe to profound affecting all frequencies
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, sensorineural, severe to profound affecting all frequencies | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:earlobe pits
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:earlobe pits | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:enlarged vestibular aqueduct
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:enlarged vestibular aqueduct | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:hearing impairment (in 1/4 patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing impairment (in 1/4 patients) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:hearing loss (cvs+)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss (cvs+) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:hearing loss (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss (in some patients) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:hearing loss (uncommon)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss (uncommon) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:hearing loss first affects high frequencies
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss first affects high frequencies | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:hearing loss, conductive or mixed
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, conductive or mixed | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:hearing loss, postlingual progressive sensorineural
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, postlingual progressive sensorineural | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:hearing loss, progressive (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, progressive (in some patients) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:hearing loss, sensorineural (high frequency)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural (high frequency) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:hearing loss, sensorineural (in one family)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural (in one family) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:hearing loss, sensorineural, associated with elsts
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural, associated with elsts | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:hearing loss, severe to profound, affecting all frequencies
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, severe to profound, affecting all frequencies | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:hypoplastic ear lobes
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hypoplastic ear lobes | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:loss of mid- and low-frequencies later
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:loss of mid- and low-frequencies later | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:low-set ears (1 patient)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:low-set ears (1 patient) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:low-set ears (45%)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:low-set ears (45%) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:low-set ears (in 2/4 patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:low-set ears (in 2/4 patients) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:low-set ears (in one family)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:low-set ears (in one family) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:malformed pinnae (30-60% of patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:malformed pinnae (30-60% of patients) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:microtia hearing loss, conductive
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:microtia hearing loss, conductive | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:no vestibular dysfunction
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:no vestibular dysfunction | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:nonprogressive deafness
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:nonprogressive deafness | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:normal static compliance on tympanometry
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:normal static compliance on tympanometry | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:oae responses may decrease with age or use of hearing aids
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:oae responses may decrease with age or use of hearing aids | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:otitis externa, recurrent, due to infection with staphylococcus aureus
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:otitis externa, recurrent, due to infection with staphylococcus aureus | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:otitis media, recurrent (rare)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:otitis media, recurrent (rare) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:overfolded, rumpled ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:overfolded, rumpled ears | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:pigmentation of the ear cartilage
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:pigmentation of the ear cartilage | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:posteriorly rotated ears (2p21del)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:posteriorly rotated ears (2p21del) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:preauricular pits (70-80% of patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:preauricular pits (70-80% of patients) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:progressive conductive hearing impairment
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:progressive conductive hearing impairment | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:prominent antitragus (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:prominent antitragus (in some patients) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:pseudomembranous inflammation of the middle ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:pseudomembranous inflammation of the middle ear | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:raised earlobes
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:raised earlobes | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:recurrent ear infections
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:recurrent ear infections | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:recurrent otitis
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:recurrent otitis | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:recurrent otitis media in infancy and childhood
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:recurrent otitis media in infancy and childhood | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:relatively long ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:relatively long ears | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:rudimentary
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:rudimentary | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:sensorineural deafness (reported in 1 family)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural deafness (reported in 1 family) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:sensorineural hearing loss (1 patient)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural hearing loss (1 patient) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:severe to profound deafness
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:severe to profound deafness | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:severe to profound hearing impairment by early adulthood
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:severe to profound hearing impairment by early adulthood | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:simple ear structure
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:simple ear structure | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:simple helix
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:simple helix | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:small cavum conchae
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:small cavum conchae | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:small earlobe
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:small earlobe | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:small external auditory canals
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:small external auditory canals | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:thick ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:thick ears | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:unconnected or fused stapes and incus
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:unconnected or fused stapes and incus | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:uplift of earlobes (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:uplift of earlobes (in some patients) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:vestibular involvement (variable)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:vestibular involvement (variable) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:wide bulbous internal auditory meatus
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:wide bulbous internal auditory meatus | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 28 / 0.651 ->
en:wide, flattened earlobes
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:wide, flattened earlobes | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:'tilted' ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:'tilted' ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:abnormal auricles
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormal auricles | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:abnormal brainstem auditory evoked potentials (baep)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormal brainstem auditory evoked potentials (baep) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:abnormal middle ear reflexes
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormal middle ear reflexes | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:abnormal speech discrimination
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormal speech discrimination | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:abnormality of the outer ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormality of the outer ear | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:abnormally formed ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormally formed ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:absence of acoustic reflex
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:absence of acoustic reflex | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:absence of earlobe
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:absence of earlobe | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:absent cochlear microphonic (in older patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:absent cochlear microphonic (in older patients) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:auditory neuropathy spectrum disorder
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:auditory neuropathy spectrum disorder | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:bilateral conductive hearing loss (rare)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:bilateral conductive hearing loss (rare) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:cauliflower ear deformity (rare)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:cauliflower ear deformity (rare) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:chronic otitis
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:chronic otitis | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:conductive hearing loss (30% of patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:conductive hearing loss (30% of patients) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:congenital sensorineural hearing loss
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:congenital sensorineural hearing loss | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:deafness (in 1 of 2 families)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness (in 1 of 2 families) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:deafness (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness (in some patients) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:deafness affects all frequencies
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness affects all frequencies | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:deafness due to bilateral cochlear malformation (rare)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:deafness, bilateral sensorineural, high frequency (100% of patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, bilateral sensorineural, high frequency (100% of patients) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:deafness, congenital nonprogressive sensorineural symmetric, moderate
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, congenital nonprogressive sensorineural symmetric, moderate | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:deafness, early-onset mixed conductive and sensorineural
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, early-onset mixed conductive and sensorineural | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:deafness, sensorineural, profound
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, sensorineural, profound | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:dysplastic pinnae
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:dysplastic pinnae | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:flat audiogram
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:flat audiogram | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:folded helix
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:folded helix | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:hearing impairment, asymmetric (in some patients with hsan2d)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing impairment, asymmetric (in some patients with hsan2d) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:hearing loss (2 patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss (2 patients) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:hearing loss (affecting all frequencies), moderate to severe
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss (affecting all frequencies), moderate to severe | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:hearing loss (rare)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss (rare) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:hearing loss, high frequency, slowly progressive (onset in early childhood)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, high frequency, slowly progressive (onset in early childhood) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:hearing loss, high-frequency (onset in childhood-adolescence)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, high-frequency (onset in childhood-adolescence) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:hearing loss, sensorineural (variable)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural (variable) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:hearing loss, sensorineural, mid-frequency (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural, mid-frequency (in some patients) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:hypercompliant tympanic membranes
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hypercompliant tympanic membranes | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:hyperfolded ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hyperfolded ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:incomplete atretic plate
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:incomplete atretic plate | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:incomplete separation of the cochlea from the internal auditory canal
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:incomplete separation of the cochlea from the internal auditory canal | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:large ears (2p21del)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:large ears (2p21del) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:large ears (37%)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:large ears (37%) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:lobular aplasia
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:lobular aplasia | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:malformed ossicular chain
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:malformed ossicular chain | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:mixed hearing loss (50% of patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:mixed hearing loss (50% of patients) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:narrowed external ear canal (30% of patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:narrowed external ear canal (30% of patients) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:neural hearing loss
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:neural hearing loss | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:pale, stiff pinnae
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:pale, stiff pinnae | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:poorly formed pinnae
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:poorly formed pinnae | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:posteriorly rotated ears (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:posteriorly rotated ears (in some patients) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:pre- and post-auricular skin or cartilaginous tags
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:pre- and post-auricular skin or cartilaginous tags | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:prolonged brainstem auditory evoked potentials (baep)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:prolonged brainstem auditory evoked potentials (baep) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:sensorineural hearing impairment (less common)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural hearing impairment (less common) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:sensorineural hearing loss (1 family)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural hearing loss (1 family) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:sensory hearing loss
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensory hearing loss | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:severe narrowing of cartilagenous auditory canal
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:severe narrowing of cartilagenous auditory canal | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:severe narrowing of cartilagenous auditory canal (in homozygotes)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:severe narrowing of cartilagenous auditory canal (in homozygotes) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:simple auricles
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:simple auricles | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:stiff, prominent pinnae
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:stiff, prominent pinnae | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:thickened helices
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:thickened helices | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:thickened lobes
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:thickened lobes | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:transient evoked otoacoustic emissions cannot be detected
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:transient evoked otoacoustic emissions cannot be detected | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:vestibular abnormalities (variable)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:vestibular abnormalities (variable) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 27 / 0.628 ->
en:vestibular dysfunction
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:vestibular dysfunction | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:abnormal bridge connecting the crus of the helix and antihelix
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormal bridge connecting the crus of the helix and antihelix | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:abnormal ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormal ears | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:abnormality of the middle ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormality of the middle ear | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:abnormality of the middle ear ossicles
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormality of the middle ear ossicles | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:absent auditory canals (wws)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:absent auditory canals (wws) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:absent brainstem auditory responses
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:absent brainstem auditory responses | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:approximately 0.7db per year hearing loss at all frequencies
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:approximately 0.7db per year hearing loss at all frequencies | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:cochlear malformation defect (mondini dysplasia) (less common)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:cochlear malformation defect (mondini dysplasia) (less common) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:deafness (often in third decade)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness (often in third decade) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:deafness (sensorineural or mixed sensorineural and conductive)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness (sensorineural or mixed sensorineural and conductive) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:deafness, secondary to cranial hyperostosis
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, secondary to cranial hyperostosis | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:deafness, sensorineural, especially affecting high frequencies
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, sensorineural, especially affecting high frequencies | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:dysplastic ears (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:dysplastic ears (in some patients) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:ear neoplasm
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:ear neoplasm | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:fleshy and overfolded helices
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:fleshy and overfolded helices | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:folded superior edge of helix
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:folded superior edge of helix | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:hearing impairment, mild (2 patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing impairment, mild (2 patients) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:hearing impairment, sensorineural, fluctuating
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing impairment, sensorineural, fluctuating | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:hearing loss, profound congenital sensorineural
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, profound congenital sensorineural | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:hearing loss, progressive sensorineural, affecting high frequencies
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, progressive sensorineural, affecting high frequencies | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:hearing loss, sensorineural (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural (in some patients) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:hearing loss, sensorineural (type ii)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural (type ii) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:hearing loss, sensorineural, mild progressive (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural, mild progressive (in some patients) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:hearing loss, sensorineural, moderate, postlingual
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural, moderate, postlingual | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:hyperacusis
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hyperacusis | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:large anteverted pinnae (90% males, 40% females)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:large anteverted pinnae (90% males, 40% females) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:large simple ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:large simple ears | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:large, floppy ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:large, floppy ears | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:low-set ears (rare)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:low-set ears (rare) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:mild to moderate hearing loss across most frequencies
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:mild to moderate hearing loss across most frequencies | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:misshapen, small ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:misshapen, small ear | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:poorly shaped ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:poorly shaped ears | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:preauricular fistulas, bilateral
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:preauricular fistulas, bilateral | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:progressive hearing impairment
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:progressive hearing impairment | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:prominence and protrusion of upper third of the ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:prominence and protrusion of upper third of the ear | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:prominent antihelix
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:prominent antihelix | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:prominent antitragus
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:prominent antitragus | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:protruding ears (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:protruding ears (in some patients) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:protruding lobules
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:protruding lobules | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:rotated ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:rotated ears | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:sensorineural deafness, progressive, late-onset
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural deafness, progressive, late-onset | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:sensorineural hearing loss (20% of patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural hearing loss (20% of patients) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:short ears (in 1 family)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:short ears (in 1 family) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:simple ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:simple ear | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:symmetric deterioration of hearing loss and speech reception with age
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:symmetric deterioration of hearing loss and speech reception with age | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:upsloping audiograms
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:upsloping audiograms | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
en:vestibular areflexia
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:vestibular areflexia | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 26 / 0.605 ->
perte d'audition sensorineurale
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=perte d'audition sensorineurale | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:abnormally folded helix
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormally folded helix | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:absent helices, bilaterally
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:absent helices, bilaterally | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:anterior creases of earlobe
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:anterior creases of earlobe | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:anteriorly displaced ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:anteriorly displaced ears | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:anteverted pinnae
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:anteverted pinnae | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:atresia of the external auditory canal
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:atresia of the external auditory canal | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:bilateral dys-synchronized auditory brainstem responses
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:bilateral dys-synchronized auditory brainstem responses | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:congenital hearing loss (1 family)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:congenital hearing loss (1 family) | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:deafness, moderate-severe (onset in third decade)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, moderate-severe (onset in third decade) | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:downward sloping audiogram
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:downward sloping audiogram | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:dysplastic helices
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:dysplastic helices | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:ear cartilage calcification
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:ear cartilage calcification | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:flat ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:flat ears | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:hearing
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:hearing loss, congenital sensorineural, severe to profound
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, congenital sensorineural, severe to profound | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:hearing loss, mixed (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, mixed (in some patients) | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:hearing loss, sensorineural (in patients with larger deletions)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural (in patients with larger deletions) | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected) | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:large, prominent ears (59%)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:large, prominent ears (59%) | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:loss of high frequencies at onset
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:loss of high frequencies at onset | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:loss of vestibular reflexes
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:loss of vestibular reflexes | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:low-set ears (severe form)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:low-set ears (severe form) | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:malformed earlobes
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:malformed earlobes | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:normal cochlear microphonics
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:normal cochlear microphonics | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:posterior helical indentations
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:posterior helical indentations | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:preauricular sinus, bilateral
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:preauricular sinus, bilateral | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:preauricular skin furrow
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:preauricular skin furrow | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:preauricular skin tag
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:preauricular skin tag | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:sensorineural deafness (rare)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural deafness (rare) | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:sensorineural hearing loss (described in 1 family)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural hearing loss (described in 1 family) | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:severe loss in the higher frequencies by the fifth decade
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:severe loss in the higher frequencies by the fifth decade | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:small external auditory meatus
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:small external auditory meatus | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:small, malformed ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:small, malformed ears | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:stenosis of external auditory canal
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:stenosis of external auditory canal | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:structural inner ear abnormalities (in patients with larger deletions)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:structural inner ear abnormalities (in patients with larger deletions) | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:structure of lymphatic vessel of ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:structure of lymphatic vessel of ear | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:supraauricular pit
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:supraauricular pit | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:u-shaped audiogram
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:u-shaped audiogram | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 25 / 0.581 ->
en:unravelling of superior helices
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:unravelling of superior helices | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:absence of the helix and distal scapha in middle third of the ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:absence of the helix and distal scapha in middle third of the ear | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:absent stapedial reflexes or intraoperative stapes immobility
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:absent stapedial reflexes or intraoperative stapes immobility | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:audiogram may be ascending
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:audiogram may be ascending | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:aural atresia, congenital
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:aural atresia, congenital | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:auricular clefts
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:auricular clefts | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:conductive hearing loss
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:conductive hearing loss | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:deafness, stable bilateral symmetric prelingual
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, stable bilateral symmetric prelingual | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:ear pain/earache
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:ear pain/earache | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:first branchial arch anomalies
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:first branchial arch anomalies | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:flattened antihelix
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:flattened antihelix | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:hearing loss (variable)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss (variable) | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:hearing loss, conductive (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, conductive (in some patients) | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:hearing loss, profound prelingual sensorineural
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, profound prelingual sensorineural | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies) | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:hearing loss, sensorineural, prelingual
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural, prelingual | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:lobule creases
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:lobule creases | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:michel aplasia (complete absence of inner ear structures)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:michel aplasia (complete absence of inner ear structures) | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:narrow external ear canals (1 patient)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:narrow external ear canals (1 patient) | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:near-stenosis of bony portion of auditory canal
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:near-stenosis of bony portion of auditory canal | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:no auditory brainstem response (abr)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:no auditory brainstem response (abr) | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:organ of corti degeneration
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:organ of corti degeneration | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:outer ear abnormalities (deletion patients) prominent ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:outer ear abnormalities (deletion patients) prominent ears | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:overfolded helix
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:overfolded helix | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:posteriorly rotated ears (1/4 patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:posteriorly rotated ears (1/4 patients) | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:posteriorly rotated ears (female)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:posteriorly rotated ears (female) | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face) | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:progressive mixed conductive and sensorineural hearing loss
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:progressive mixed conductive and sensorineural hearing loss | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:prominent ears (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:prominent ears (in some patients) | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:protruding, simple ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:protruding, simple ears | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:recurrent otitis media (18%)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:recurrent otitis media (18%) | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:recurrent serous otitis
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:recurrent serous otitis | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:short ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:short ear | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:soft auricles
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:soft auricles | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:stapes ankylosis
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:stapes ankylosis | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:superiorly displaced ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:superiorly displaced ears | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:tinnitus (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:tinnitus (in some patients) | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:u- or bowl-shaped audiogram
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:u- or bowl-shaped audiogram | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
en:unfolded superior helices
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:unfolded superior helices | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 24 / 0.558 ->
surdité congénitale
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=surdité congénitale | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:abnormal ear configuration
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormal ear configuration | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:angular ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:angular ears | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:asymmetric dysplastic ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:asymmetric dysplastic ears | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:cystic dilatation of cochlea and vestibulum
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:cystic dilatation of cochlea and vestibulum | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:deafness labyrinthine
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness labyrinthine | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:deafness, postlingual
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, postlingual | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:dysmorphic ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:dysmorphic ears | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:endolymphatic sac tumors (elsts)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:endolymphatic sac tumors (elsts) | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:hearing loss, late-onset sensorineural, mild-to moderate (less common)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, late-onset sensorineural, mild-to moderate (less common) | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:hearing loss, more severe at lower frequencies
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, more severe at lower frequencies | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:hearing loss, postlingual sensorineural
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, postlingual sensorineural | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:hearing loss, sensorineural (bilateral, prelingual)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural (bilateral, prelingual) | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:hypoplastic ears fused to the scalp
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hypoplastic ears fused to the scalp | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:hypoplastic pinnae (30-60% of patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hypoplastic pinnae (30-60% of patients) | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:increased posterior angulation
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:increased posterior angulation | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:inferior displacement of the ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:inferior displacement of the ears | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:large appearing ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:large appearing ears | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:large dysplastic ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:large dysplastic ears | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:low-set ears (3 patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:low-set ears (3 patients) | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:low-set, posteriorly rotated ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:low-set, posteriorly rotated ears | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:microtia, type i
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:microtia, type i | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:mild cochlear hearing loss (1 patient)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:mild cochlear hearing loss (1 patient) | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:mondini malformation
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:mondini malformation | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:morphological abnormality of the middle ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:morphological abnormality of the middle ear | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:normal outer hair cell functions
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:normal outer hair cell functions | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:normal vestibular response
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:normal vestibular response | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:poorly folded ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:poorly folded ears | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:prominent crura
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:prominent crura | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:prominent ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:prominent ear | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:recurrent otitis media in infancy
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:recurrent otitis media in infancy | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:rudimentary tympanic membrane (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:rudimentary tympanic membrane (in some patients) | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:sensorineural hearing loss has been reported
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural hearing loss has been reported | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:sensorineural hearing loss, progressive bilateral postlingual
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural hearing loss, progressive bilateral postlingual | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:sensorineural, conductive, or mixed hearing loss
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural, conductive, or mixed hearing loss | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:small lobes
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:small lobes | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:small pinna
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:small pinna | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:small triangular pinnae
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:small triangular pinnae | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:thick earlobes
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:thick earlobes | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:thick, firm earlobes
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:thick, firm earlobes | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:underdeveloped nasal alae
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:underdeveloped nasal alae | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:unilateral external ear deformity
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:unilateral external ear deformity | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:vertigo, single occurrence (in 2 patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:vertigo, single occurrence (in 2 patients) | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 23 / 0.535 ->
en:vestibulopathy, bilateral, progressive
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:vestibulopathy, bilateral, progressive | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:abnormal or absent auditory nerve and brainstem responses
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormal or absent auditory nerve and brainstem responses | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:auditory impairment
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:auditory impairment | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:conductive hearing loss, mild bilateral (rare)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:conductive hearing loss, mild bilateral (rare) | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:congenital deafness
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:congenital deafness | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:deafness, early-onset
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, early-onset | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:deafness, sensorineural (reported in 1 family)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, sensorineural (reported in 1 family) | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:deafness, sensorineural, mild (rare)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness, sensorineural, mild (rare) | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:decreased otoacoustic emission amplitude
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:decreased otoacoustic emission amplitude | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:dilatated internal auditory canal
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:dilatated internal auditory canal | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:dorsally rotated ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:dorsally rotated ears | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:floppy ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:floppy ears | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:hearing disorder (1 patient)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing disorder (1 patient) | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:hearing loss has been reported in some adults with severe disease
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss has been reported in some adults with severe disease | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:hearing loss, prelingual sensorineural, moderate to severe
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, prelingual sensorineural, moderate to severe | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:hearing loss, progressive, starting in infancy
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, progressive, starting in infancy | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:hearing loss, sensorineural (in 2 patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural (in 2 patients) | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:large protruding ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:large protruding ears | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:large, dysmorphic ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:large, dysmorphic ears | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:linear ear lobe creases
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:linear ear lobe creases | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:low-frequency sensorineural hearing impairment
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:low-frequency sensorineural hearing impairment | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:low-set ears (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:low-set ears (in some patients) | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:narrow auditory canals (rare)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:narrow auditory canals (rare) | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:narrow intertragic notch
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:narrow intertragic notch | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:neonatal cystic lesions of the pinnae
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:neonatal cystic lesions of the pinnae | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:no reproducible waves i, iii, or v at high intensities
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:no reproducible waves i, iii, or v at high intensities | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:occasional conductive hearing loss
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:occasional conductive hearing loss | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:otitis media, chronic (rare)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:otitis media, chronic (rare) | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:preauricular sinus
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:preauricular sinus | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:progressive hearing loss (in some)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:progressive hearing loss (in some) | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:progressive, low frequency sensorineural hearing loss
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:progressive, low frequency sensorineural hearing loss | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:retroverted ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:retroverted ears | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:sensorineural hearing loss, mild to moderate
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural hearing loss, mild to moderate | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:small auricles
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:small auricles | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:small ears (female)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:small ears (female) | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:small/rudimentary tragus, antitragus and lobule
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:small/rudimentary tragus, antitragus and lobule | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:superficial injury of ear
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:superficial injury of ear | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:tinnitus (rare)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:tinnitus (rare) | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:underdeveloped tragus
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:underdeveloped tragus | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
en:vestibular dysfunction (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:vestibular dysfunction (in some patients) | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 22 / 0.512 ->
surdité héréditaire
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=surdité héréditaire | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:abnormal communication between the subarachnoid space in the meatus and the perilymph
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormal communication between the subarachnoid space in the meatus and the perilymph | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:abnormality of the helix
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:abnormality of the helix | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:absent external auditory canals
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:absent external auditory canals | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:absent lobules
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:absent lobules | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient) | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:excessive cerumen
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:excessive cerumen | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:hearing impairment (rare)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing impairment (rare) | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:hearing loss, bilateral
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, bilateral | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:hearing loss, mild (rare)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, mild (rare) | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:hearing loss, postlingual
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, postlingual | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:hearing loss, progressive conductive and/or sensorineural, during adulthood
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, progressive conductive and/or sensorineural, during adulthood | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:mild hearing impairment (13%)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:mild hearing impairment (13%) | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:narrow ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:narrow ears | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:normal middle ear pressures on tympanometry
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:normal middle ear pressures on tympanometry | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:normal otoacoustic emissions
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:normal otoacoustic emissions | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:normal vestibular function
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:normal vestibular function | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:pinna modeling anomalies
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:pinna modeling anomalies | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:preauricular skin tags (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:preauricular skin tags (in some patients) | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:progressive cartilaginous ossification of pinnae
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:progressive cartilaginous ossification of pinnae | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:progressive high-frequency hearing loss (onset 20-30 years)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:progressive high-frequency hearing loss (onset 20-30 years) | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:prominent ears (rare)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:prominent ears (rare) | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:prominent helices
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:prominent helices | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:sensorineural hearing loss (3 patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural hearing loss (3 patients) | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:sensorineural hearing loss (onset early childhood)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:sensorineural hearing loss (onset early childhood) | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:small, simple ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:small, simple ears | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:squared-off superior helices
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:squared-off superior helices | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:stapes fixation
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:stapes fixation | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:uplifted earlobes
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:uplifted earlobes | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:vertigo
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:vertigo | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
en:vestibular areflexia, complete
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:vestibular areflexia, complete | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
surdité du labyrinthe
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=surdité du labyrinthe | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 21 / 0.488 ->
traumatisme superficiel oreille
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=traumatisme superficiel oreille | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
déficience auditive
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=déficience auditive | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
en:acoustic trauma
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:acoustic trauma | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
en:auditory canal stenosis
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:auditory canal stenosis | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
en:balance problem
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:balance problem | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
en:chronic otitis media (25%)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:chronic otitis media (25%) | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
en:cutlet
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:cutlet | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
en:disorder of equilibrium
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:disorder of equilibrium | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
en:dysplastic ears (jbts)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:dysplastic ears (jbts) | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
en:ENT doctor
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:ENT doctor | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
en:ENT specialist
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:ENT specialist | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
en:hearing impairment (1 patient)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing impairment (1 patient) | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
en:hearing impairment, progressive (family a)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing impairment, progressive (family a) | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
en:hearing loss (in 2 members of 1 family)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss (in 2 members of 1 family) | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
en:hearing loss, sensorineural, progressive (all frequencies)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural, progressive (all frequencies) | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
en:hereditary deafness
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hereditary deafness | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
en:microtia (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:microtia (in some patients) | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
en:mild dysplasia of concha, unilateral
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:mild dysplasia of concha, unilateral | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
en:no vestibular symptoms
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:no vestibular symptoms | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
en:nose and throat specialist
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:nose and throat specialist | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
en:problem with balance
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:problem with balance | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
en:rotary vertigo
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:rotary vertigo | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
en:serous otitis media
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:serous otitis media | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
en:tinnitus, bilateral (in some patients)
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:tinnitus, bilateral (in some patients) | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
état nébuleux
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=état nébuleux | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
état vertigineux
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=état vertigineux | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
étourdissement
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=étourdissement | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
hyperacousie
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=hyperacousie | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
hyperacousies
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=hyperacousies | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
hyperacusie
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=hyperacusie | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
médecin ORL
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=médecin ORL | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
otite moyenne séreuse
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=otite moyenne séreuse | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
otite séreuse
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=otite séreuse | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
otite séromuqueuse
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=otite séromuqueuse | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
oto-rhino
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=oto-rhino | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
oto-rhino-laryngologiste
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=oto-rhino-laryngologiste | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
otorhinolaryngologiste
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=otorhinolaryngologiste | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
pavillon de l'oreille de morphologie rudimentaire
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=pavillon de l'oreille de morphologie rudimentaire | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
presbyacousie
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=presbyacousie | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
sensation de rotation
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=sensation de rotation | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
sensation de tournoiement
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=sensation de tournoiement | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
sensation rotatoire
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=sensation rotatoire | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
sensation vertigineuse
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=sensation vertigineuse | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
sténose du canal auriculaire
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=sténose du canal auriculaire | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
surdimutité
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=surdimutité | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
tête pivotante
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=tête pivotante | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
trouble de l'équilibre
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=trouble de l'équilibre | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
vertige
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=vertige | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
vertige rotatoire
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=vertige rotatoire | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
vertige subjectif
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=vertige subjectif | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
vertigo
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=vertigo | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --
r_associated #0: 20 / 0.465 ->
vertigo rotatoire
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=vertigo rotatoire | rel=r_associated | relid=0 | w=20
| ≈ 707 relations entrantes
- en:congenital deafness ---
r_associated #0: 300 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:congenital deafness | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=300
- surdité congénitale ---
r_associated #0: 297 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=surdité congénitale | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=297
- surdité héréditaire ---
r_associated #0: 295 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=surdité héréditaire | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=295
- surdité du labyrinthe ---
r_associated #0: 271 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=surdité du labyrinthe | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=271
- en:deafness labyrinthine ---
r_associated #0: 270 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness labyrinthine | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=270
- sensation vertigineuse ---
r_associated #0: 240 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=sensation vertigineuse | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=240
- vertige subjectif ---
r_associated #0: 240 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=vertige subjectif | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=240
- vertigo rotatoire ---
r_associated #0: 240 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=vertigo rotatoire | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=240
- sensation de tournoiement ---
r_associated #0: 237 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=sensation de tournoiement | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=237
- sensation de rotation ---
r_associated #0: 232 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=sensation de rotation | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=232
- vertige rotatoire ---
r_associated #0: 230 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=vertige rotatoire | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=230
- tête pivotante ---
r_associated #0: 225 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=tête pivotante | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=225
- état nébuleux ---
r_associated #0: 215 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=état nébuleux | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=215
- état vertigineux ---
r_associated #0: 215 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=état vertigineux | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=215
- sensation rotatoire ---
r_associated #0: 213 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=sensation rotatoire | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=213
- otite moyenne séreuse ---
r_associated #0: 200 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=otite moyenne séreuse | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=200
- en:serous otitis media ---
r_associated #0: 199 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:serous otitis media | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=199
- en:sensorineural hearing loss ---
r_associated #0: 188 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural hearing loss | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=188
- traumatisme superficiel oreille ---
r_associated #0: 185 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=traumatisme superficiel oreille | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=185
- perte d'audition sensorineurale ---
r_associated #0: 184 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=perte d'audition sensorineurale | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=184
- en:superficial injury of ear ---
r_associated #0: 182 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:superficial injury of ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=182
- en:vertigo ---
r_associated #0: 172 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:vertigo | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=172
- en:dizziness ---
r_associated #0: 170 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:dizziness | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=170
- hyperacousie ---
r_associated #0: 140 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=hyperacousie | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=140
- hyperacusie ---
r_associated #0: 140 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=hyperacusie | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=140
- en:hyperacusis ---
r_associated #0: 139 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hyperacusis | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=139
- vertigo ---
r_associated #0: 135 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=vertigo | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=135
- hyperacousies ---
r_associated #0: 120 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=hyperacousies | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=120
- en:balance problem ---
r_associated #0: 115 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:balance problem | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=115
- en:disorder of equilibrium ---
r_associated #0: 115 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:disorder of equilibrium | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=115
- en:problem with balance ---
r_associated #0: 115 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:problem with balance | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=115
- trouble de l'équilibre ---
r_associated #0: 115 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=trouble de l'équilibre | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=115
- vertige ---
r_associated #0: 95 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=vertige | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=95
- étourdissement ---
r_associated #0: 76 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=étourdissement | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=76
- en:secretory otitis media ---
r_associated #0: 60 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:secretory otitis media | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=60
- lésion traumatique superficielle de l'oreille ---
r_associated #0: 58 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=lésion traumatique superficielle de l'oreille | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=58
- otite séromuqueuse ---
r_associated #0: 55 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=otite séromuqueuse | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=55
- en:ENT specialist ---
r_associated #0: 50 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:ENT specialist | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=50
- oto-rhino ---
r_associated #0: 50 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=oto-rhino | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=50
- oto-rhino-laryngologiste ---
r_associated #0: 50 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=oto-rhino-laryngologiste | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=50
- otorhinolaryngologiste ---
r_associated #0: 49 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=otorhinolaryngologiste | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=49
- en:nose and throat specialist ---
r_associated #0: 46 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:nose and throat specialist | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=46
- en:hereditary deafness ---
r_associated #0: 44 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hereditary deafness | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=44
- en:aural atresia, congenital ---
r_associated #0: 43 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:aural atresia, congenital | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=43
- en:prominent ear ---
r_associated #0: 43 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:prominent ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=43
- en:sensorineural hearing loss (in 1 of 3 patients) ---
r_associated #0: 43 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural hearing loss (in 1 of 3 patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=43
- en:structural inner ear abnormalities (in patients with larger deletions) ---
r_associated #0: 43 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:structural inner ear abnormalities (in patients with larger deletions) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=43
- en:tinnitus (variable) ---
r_associated #0: 43 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:tinnitus (variable) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=43
- en:hypoplastic semicircular canals ---
r_associated #0: 42 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hypoplastic semicircular canals | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=42
- en:incomplete atretic plate ---
r_associated #0: 42 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:incomplete atretic plate | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=42
- déficience auditive ---
r_associated #0: 41 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=déficience auditive | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=41
- en:anteverted pinnae ---
r_associated #0: 41 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:anteverted pinnae | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=41
- en:complete bony atresia of medial portion of external auditory canal (in some patients) ---
r_associated #0: 41 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:complete bony atresia of medial portion of external auditory canal (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=41
- en:first branchial arch anomalies ---
r_associated #0: 41 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:first branchial arch anomalies | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=41
- en:hearing loss, sensorineural (in 2 patients) ---
r_associated #0: 41 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural (in 2 patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=41
- en:loss of hearing (45%) ---
r_associated #0: 41 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:loss of hearing (45%) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=41
- en:ENT doctor ---
r_associated #0: 40 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:ENT doctor | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=40
- en:audiogram may be ascending ---
r_associated #0: 40 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:audiogram may be ascending | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=40
- en:hypoplastic pinnae (30-60% of patients) ---
r_associated #0: 40 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hypoplastic pinnae (30-60% of patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=40
- en:malformed ossicular chain ---
r_associated #0: 40 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:malformed ossicular chain | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=40
- en:pre- and post-auricular skin or cartilaginous tags ---
r_associated #0: 39 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:pre- and post-auricular skin or cartilaginous tags | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=39
- en:prolonged brainstem auditory evoked potentials (baep) ---
r_associated #0: 39 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:prolonged brainstem auditory evoked potentials (baep) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=39
- en:recurrent otitis ---
r_associated #0: 39 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:recurrent otitis | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=39
- en:small ears with large lobules ---
r_associated #0: 39 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:small ears with large lobules | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=39
- surdimutité ---
r_associated #0: 39 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=surdimutité | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=39
- en:absent external auditory canals ---
r_associated #0: 38 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:absent external auditory canals | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=38
- en:conductive hearing loss ---
r_associated #0: 38 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:conductive hearing loss | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=38
- en:hearing impairment ---
r_associated #0: 38 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing impairment | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=38
- en:hypoplastic ear lobes ---
r_associated #0: 38 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hypoplastic ear lobes | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=38
- en:large protruding ears ---
r_associated #0: 38 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:large protruding ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=38
- en:large simple ears ---
r_associated #0: 38 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:large simple ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=38
- en:rotary vertigo ---
r_associated #0: 38 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:rotary vertigo | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=38
- en:small lobes ---
r_associated #0: 38 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:small lobes | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=38
- en:anteriorly displaced ears ---
r_associated #0: 37 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:anteriorly displaced ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=37
- en:cystic dilatation of cochlea and vestibulum ---
r_associated #0: 37 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:cystic dilatation of cochlea and vestibulum | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=37
- en:hearing loss, congenital sensorineural, moderate-severe ---
r_associated #0: 37 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, congenital sensorineural, moderate-severe | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=37
- en:small external auditory meatus ---
r_associated #0: 37 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:small external auditory meatus | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=37
- en:hearing loss (in 2 members of 1 family) ---
r_associated #0: 36 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss (in 2 members of 1 family) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=36
- en:high-frequency tinnitus at onset ---
r_associated #0: 36 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:high-frequency tinnitus at onset | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=36
- en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves ---
r_associated #0: 36 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=36
- en:thick ears ---
r_associated #0: 36 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:thick ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=36
- otite séreuse ---
r_associated #0: 36 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=otite séreuse | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=36
- surdi-mutité ---
r_associated #0: 36 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=surdi-mutité | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=36
- en:abnormality of the pinna ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormality of the pinna | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:auditory impairment ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:auditory impairment | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:chronic otitis media (25%) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:chronic otitis media (25%) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:cochlear malformation ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:cochlear malformation | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:deafness, profound congenital sensorineural ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, profound congenital sensorineural | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:decreased otoacoustic emission amplitude ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:decreased otoacoustic emission amplitude | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:hearing disorder (1 patient) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing disorder (1 patient) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:hearing impairment, progressive (family a) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing impairment, progressive (family a) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:hearing loss (affecting all frequencies), moderate to severe ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss (affecting all frequencies), moderate to severe | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:hearing loss affects all frequencies ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss affects all frequencies | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:hearing loss, congenital profound ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, congenital profound | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:hearing loss, high frequency, slowly progressive (onset in early childhood) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, high frequency, slowly progressive (onset in early childhood) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:hearing loss, late-onset sensorineural, mild-to moderate (less common) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, late-onset sensorineural, mild-to moderate (less common) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:hearing loss, more severe at lower frequencies ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, more severe at lower frequencies | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:hearing loss, postlingual sensorineural ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, postlingual sensorineural | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:hearing loss, progressive, starting in infancy ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, progressive, starting in infancy | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, moderate, postlingual ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural, moderate, postlingual | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, progressive (all frequencies) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural, progressive (all frequencies) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:internal auditory canal hypoplasia ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:internal auditory canal hypoplasia | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:large earlobe ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:large earlobe | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:large prominent ears ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:large prominent ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:large, dysmorphic ears ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:large, dysmorphic ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:low-set and rotated ears ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:low-set and rotated ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:low-set ears (28%) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:low-set ears (28%) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:mild to moderate hearing loss across most frequencies ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:mild to moderate hearing loss across most frequencies | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:minor ear anomalies (in some patients) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:minor ear anomalies (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:narrowed external ear canal (30% of patients) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:narrowed external ear canal (30% of patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:nonprogressive deafness ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:nonprogressive deafness | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:otitis media, chronic (rare) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:otitis media, chronic (rare) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:pale, stiff pinnae ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:pale, stiff pinnae | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:postauricular pit ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:postauricular pit | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:preauricular fistulas, bilateral ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:preauricular fistulas, bilateral | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:preauricular pits (70-80% of patients) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:preauricular pits (70-80% of patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:preauricular sinus, bilateral ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:preauricular sinus, bilateral | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:prominent antitragus ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:prominent antitragus | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:prominent ears (rare) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:prominent ears (rare) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:sensorineural hearing loss (3 patients) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural hearing loss (3 patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:sensorineural hearing loss (onset early childhood) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural hearing loss (onset early childhood) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:sensorineural hearing loss, mild (rare) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural hearing loss, mild (rare) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:simple ear ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:simple ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:soft auricles ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:soft auricles | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:stenosis of external auditory canal ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:stenosis of external auditory canal | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:structure of superior auricularis muscle ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:structure of superior auricularis muscle | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:thick earlobes ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:thick earlobes | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:triangular-shaped ears ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:triangular-shaped ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:vestibular areflexia ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:vestibular areflexia | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:wide bulbous internal auditory meatus ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:wide bulbous internal auditory meatus | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- pavillon de l'oreille de morphologie rudimentaire ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=pavillon de l'oreille de morphologie rudimentaire | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- sténose du canal auriculaire ---
r_associated #0: 35 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=sténose du canal auriculaire | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=35
- en:absent brainstem auditory responses ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:absent brainstem auditory responses | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:absent helices, bilaterally ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:absent helices, bilaterally | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:atresia of the external auditory canal ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:atresia of the external auditory canal | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:deafness (often in third decade) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness (often in third decade) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:deafness, postlingual ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, postlingual | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:downward sloping audiogram ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:downward sloping audiogram | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:everted ears ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:everted ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:hearing impairment (rare) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing impairment (rare) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:hearing loss (cvs+) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss (cvs+) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:hearing loss (variable) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss (variable) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:hearing loss, conductive (in some patients) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, conductive (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:hearing loss, profound prelingual sensorineural ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, profound prelingual sensorineural | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural (in patients with larger deletions) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural (in patients with larger deletions) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, due to auditory neuropathy ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural, due to auditory neuropathy | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:hearing loss, unilateral (rare) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, unilateral (rare) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:hypoplastic ears fused to the scalp ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hypoplastic ears fused to the scalp | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:increased posterior angulation ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:increased posterior angulation | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:large ears (37%) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:large ears (37%) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:large, low-set ears ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:large, low-set ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:large, prominent ears (59%) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:large, prominent ears (59%) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:loss of vestibular caloric response ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:loss of vestibular caloric response | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:low-frequency conductive hearing loss ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:low-frequency conductive hearing loss | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:low-set ears (in some patients) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:low-set ears (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:misshapen, small ear ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:misshapen, small ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:neonatal cystic lesions of the pinnae ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:neonatal cystic lesions of the pinnae | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:no hearing loss ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:no hearing loss | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:normal static compliance on tympanometry ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:normal static compliance on tympanometry | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:ossified pinnae ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:ossified pinnae | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:poorly folded ears ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:poorly folded ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:poorly formed ears ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:poorly formed ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:preauricular skin tag ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:preauricular skin tag | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:profound deafness ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:profound deafness | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:progressive conductive hearing impairment ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:progressive conductive hearing impairment | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:progressive hearing loss (in some) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:progressive hearing loss (in some) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:progressive high-frequency hearing loss (onset 20-30 years) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:progressive high-frequency hearing loss (onset 20-30 years) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:prominent antihelix ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:prominent antihelix | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:pseudomembranous inflammation of the middle ear ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:pseudomembranous inflammation of the middle ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:recurrent otitis media in infancy and childhood ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:recurrent otitis media in infancy and childhood | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:recurrent serous otitis ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:recurrent serous otitis | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:sclerosis of semicircular canals ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sclerosis of semicircular canals | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:sensorineural deafness (reported in 1 family) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural deafness (reported in 1 family) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:small, malformed ears ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:small, malformed ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:symmetric deterioration of hearing loss and speech reception with age ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:symmetric deterioration of hearing loss and speech reception with age | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:thickened helices ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:thickened helices | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:uplift of earlobes (in some patients) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:uplift of earlobes (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:upsloping audiograms ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:upsloping audiograms | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:wide, flattened earlobes ---
r_associated #0: 34 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:wide, flattened earlobes | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:a subset of patients have hearing loss ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:a subset of patients have hearing loss | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:abnormality of the helix ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormality of the helix | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:abnormality of the middle ear ossicles ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormality of the middle ear ossicles | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:angular ears ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:angular ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:bilateral sensorineural hearing loss (in some patients) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:bilateral sensorineural hearing loss (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:cleft at the superior portion of the pinna ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:cleft at the superior portion of the pinna | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:deafness, profound, affects all frequencies ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, profound, affects all frequencies | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:deafness, sensorineural (45%) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, sensorineural (45%) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:hearing loss (uncommon) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss (uncommon) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:hearing loss has been reported in some adults with severe disease ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss has been reported in some adults with severe disease | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:hearing loss, bilateral ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, bilateral | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:hearing loss, mild (rare) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, mild (rare) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:hearing loss, progressive (in some patients) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, progressive (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural (in some patients) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural (in some) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural (in some) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, prelingual ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural, prelingual | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:hearing loss, severe to profound, affecting all frequencies ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, severe to profound, affecting all frequencies | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:hypercompliant tympanic membranes ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hypercompliant tympanic membranes | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:incomplete separation of the cochlea from the internal auditory canal ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:incomplete separation of the cochlea from the internal auditory canal | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:inferior displacement of the ears ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:inferior displacement of the ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:large anteverted pinnae (90% males, 40% females) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:large anteverted pinnae (90% males, 40% females) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:long and prominent ear crus ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:long and prominent ear crus | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:low-frequency sensorineural hearing impairment ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:low-frequency sensorineural hearing impairment | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:low-set ears (3 patients) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:low-set ears (3 patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:misshapen ear ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:misshapen ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:mixed hearing loss (50% of patients) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:mixed hearing loss (50% of patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:narrow ears ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:narrow ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:narrow intertragic notch ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:narrow intertragic notch | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:neural hearing loss ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:neural hearing loss | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:pointed upper helix ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:pointed upper helix | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:preauricular sinus ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:preauricular sinus | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:progressive hearing impairment ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:progressive hearing impairment | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:progressive mixed conductive and sensorineural hearing loss ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:progressive mixed conductive and sensorineural hearing loss | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:rudimentary ear ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:rudimentary ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:sensorineural hearing loss (described in 1 family) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural hearing loss (described in 1 family) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:sensorineural, conductive, or mixed hearing loss ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural, conductive, or mixed hearing loss | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:severe narrowing of cartilagenous auditory canal (in homozygotes) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:severe narrowing of cartilagenous auditory canal (in homozygotes) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:short ears (in 1 family) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:short ears (in 1 family) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:simple auricles ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:simple auricles | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:simple helix ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:simple helix | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:simplified helices ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:simplified helices | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:superior semicircular canal dehiscence syndrome ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:superior semicircular canal dehiscence syndrome | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:supraauricular pit ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:supraauricular pit | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:thick, firm earlobes ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:thick, firm earlobes | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:underdeveloped nasal alae ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:underdeveloped nasal alae | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:vestibular dysfunction ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:vestibular dysfunction | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:vestibular involvement (variable) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:vestibular involvement (variable) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=32
- en:abnormal auditory brainstem responses ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormal auditory brainstem responses | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:abnormal communication between the subarachnoid space in the meatus and the perilymph ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormal communication between the subarachnoid space in the meatus and the perilymph | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:abnormality of the middle ear ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormality of the middle ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:cauliflower ear deformity (rare) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:cauliflower ear deformity (rare) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:deafness, early-onset ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, early-onset | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:deafness, stable bilateral symmetric prelingual ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, stable bilateral symmetric prelingual | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:dilatated internal auditory canal ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:dilatated internal auditory canal | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:ear ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:ear cartilage calcification ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:ear cartilage calcification | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:ear tag ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:ear tag | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:endolymphatic sac tumors (elsts) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:endolymphatic sac tumors (elsts) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:folded superior edge of helix ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:folded superior edge of helix | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:hearing impairment (1 patient) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing impairment (1 patient) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:hearing impairment (in 1/4 patients) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing impairment (in 1/4 patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:hearing loss, congenital sensorineural, severe to profound ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, congenital sensorineural, severe to profound | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:hearing loss, prelingual sensorineural, moderate to severe ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, prelingual sensorineural, moderate to severe | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:hypoplastic, overfolded helices ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hypoplastic, overfolded helices | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:large anteverted ears ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:large anteverted ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:large dysplastic ears ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:large dysplastic ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:lobular aplasia ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:lobular aplasia | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:loss of vestibular reflexes ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:loss of vestibular reflexes | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:low-set ears (in one family) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:low-set ears (in one family) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:microtia hearing loss, conductive ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:microtia hearing loss, conductive | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:microtia, type i ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:microtia, type i | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:mild dysplasia of concha, unilateral ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:mild dysplasia of concha, unilateral | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:mild hearing impairment (13%) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:mild hearing impairment (13%) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:minor auricular anomalies ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:minor auricular anomalies | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:morphological abnormality of the middle ear ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:morphological abnormality of the middle ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:no vestibular dysfunction ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:no vestibular dysfunction | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:nonsyndromic sensorineural hearing loss ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:nonsyndromic sensorineural hearing loss | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:normal cochlear microphonics ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:normal cochlear microphonics | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:partial hearing loss ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:partial hearing loss | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:poorly formed pinnae ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:poorly formed pinnae | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:prelingual onset ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:prelingual onset | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:progressive, low frequency sensorineural hearing loss ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:progressive, low frequency sensorineural hearing loss | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:prominent ears (in some patients) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:prominent ears (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:prominent helices ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:prominent helices | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:protruding right ear ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:protruding right ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:raised earlobes ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:raised earlobes | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:recurrent otitis media (18%) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:recurrent otitis media (18%) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:relatively long ears ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:relatively long ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:rudimentary ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:rudimentary | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:sensorineural deafness (onset in the second decade in 25 to 30% of patients) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural deafness (onset in the second decade in 25 to 30% of patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:sensorineural hearing impairment (less common) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural hearing impairment (less common) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:sensorineural hearing loss (1 family) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural hearing loss (1 family) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:sensorineural hearing loss (1 patient) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural hearing loss (1 patient) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:sensorineural hearing loss, mild to moderate ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural hearing loss, mild to moderate | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:sensory hearing loss ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensory hearing loss | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:small ears (female) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:small ears (female) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:small pinna ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:small pinna | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:small triangular pinnae ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:small triangular pinnae | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:unconnected or fused stapes and incus ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:unconnected or fused stapes and incus | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:underdeveloped tragus ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:underdeveloped tragus | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:unilateral external ear deformity ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:unilateral external ear deformity | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:unravelling of superior helices ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:unravelling of superior helices | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:upturned lobes ---
r_associated #0: 31 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:upturned lobes | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=31
- en:abnormal auricles ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormal auricles | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:abnormally folded helix ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormally folded helix | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:absence of acoustic reflex ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:absence of acoustic reflex | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:absence of the helix and distal scapha in middle third of the ear ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:absence of the helix and distal scapha in middle third of the ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:absent auditory canals (wws) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:absent auditory canals (wws) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:acoustic trauma ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:acoustic trauma | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:anterior creases of earlobe ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:anterior creases of earlobe | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:anteverted ears ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:anteverted ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:asymmetric dysplastic ears ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:asymmetric dysplastic ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:bilateral hypoplastic cochlea ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:chronic otitis media ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:chronic otitis media | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:cochlear malformation defect (mondini dysplasia) (less common) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:cochlear malformation defect (mondini dysplasia) (less common) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:cup-shaped ears (30-60% of patients) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:cup-shaped ears (30-60% of patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:cupped ears (in some patients) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:cupped ears (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:cutlet ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:cutlet | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:deafness (in 1 of 2 families) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness (in 1 of 2 families) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:deafness (sensorineural or mixed sensorineural and conductive) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness (sensorineural or mixed sensorineural and conductive) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:deafness (variable) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness (variable) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:deafness due to bilateral cochlear malformation (rare) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:deafness, early-onset mixed conductive and sensorineural ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, early-onset mixed conductive and sensorineural | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:deafness, sensorineural (in some patients) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, sensorineural (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:deafness, sensorineural (reported in 1 family) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, sensorineural (reported in 1 family) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:dorsally rotated ears ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:dorsally rotated ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:entire ear ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:entire ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:excessive cerumen ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:excessive cerumen | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:external ear defects ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:external ear defects | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:hearing impairment, sensorineural, fluctuating ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing impairment, sensorineural, fluctuating | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:hearing loss (1 patient) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss (1 patient) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:hearing loss (in some patients) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:hearing loss, initially conductive, later mixed conductive-sensorineural ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, initially conductive, later mixed conductive-sensorineural | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:hypoplasia of the cochlea ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hypoplasia of the cochlea | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:large fleshy ears ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:large fleshy ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:large, floppy ears ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:large, floppy ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:large, low-set ears (uncommon) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:large, low-set ears (uncommon) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:linear ear lobe creases ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:linear ear lobe creases | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:malformed pinnae (30-60% of patients) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:malformed pinnae (30-60% of patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:microtia (30-60% of patients) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:microtia (30-60% of patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:normal outer hair cell functions ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:normal outer hair cell functions | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:organ of corti degeneration ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:organ of corti degeneration | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:otitis externa, recurrent, due to infection with staphylococcus aureus ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:otitis externa, recurrent, due to infection with staphylococcus aureus | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:overfolded helix ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:overfolded helix | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:pinna modeling anomalies ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:pinna modeling anomalies | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:posteriorly rotated ears (female) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:posteriorly rotated ears (female) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:preauricular skin furrow ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:preauricular skin furrow | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:protruding, simple ears ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:protruding, simple ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:pulsatile tinnitus (tympanic paraganglioma) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:pulsatile tinnitus (tympanic paraganglioma) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:rudimentary tympanic membrane (in some patients) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:rudimentary tympanic membrane (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:sensorineural deafness, progressive, late-onset ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural deafness, progressive, late-onset | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:sensorineural hearing loss (20% of patients) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural hearing loss (20% of patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:sensorineural hearing loss (uncommon) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural hearing loss (uncommon) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:simple ear structure ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:simple ear structure | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:small, simple ears ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:small, simple ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:tinnitus (in some patients) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:tinnitus (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:vertigo, single occurrence (in 2 patients) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:vertigo, single occurrence (in 2 patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:vestibular dysfunction (in some patients) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:vestibular dysfunction (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:vestibular function defect (decreased in some, normal in other patients) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:vestibular function defect (decreased in some, normal in other patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- médecin ORL ---
r_associated #0: 30 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=médecin ORL | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
- en:'tilted' ears ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:'tilted' ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:abnormal folded pinna ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormal folded pinna | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:absent or decreased auditory brainstem responses ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:absent or decreased auditory brainstem responses | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:atretic auditory canal ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:atretic auditory canal | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:atrophy of cochlear and vestibular fibrocytes ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:atrophy of cochlear and vestibular fibrocytes | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:aural fullness ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:aural fullness | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:bilateral conductive hearing loss (rare) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:bilateral conductive hearing loss (rare) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:congenital atresia of external auditory canal ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:congenital atresia of external auditory canal | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:crumpled ear (76%) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:crumpled ear (76%) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:deafness, sensorineural, mild (rare) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, sensorineural, mild (rare) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:dysplastic helices ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:dysplastic helices | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:ear neoplasm ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:ear neoplasm | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:endolymphatic hydrops, delayed onset ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:endolymphatic hydrops, delayed onset | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:enlarged vestibular aqueduct ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:enlarged vestibular aqueduct | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:external auditory canal narrow ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:external auditory canal narrow | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:fleshy ears ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:fleshy ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:floppy ears ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:floppy ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:folded helix ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:folded helix | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:hearing impairment, asymmetric (in some patients with hsan2d) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing impairment, asymmetric (in some patients with hsan2d) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:hearing loss, mixed (in some patients) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, mixed (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:hearing loss, neural type ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, neural type | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:hearing loss, progressive conductive and/or sensorineural, during adulthood ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, progressive conductive and/or sensorineural, during adulthood | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural (reported in 1 patient) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural (reported in 1 patient) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:hypoplastic superior helix ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hypoplastic superior helix | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:inner ear ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:inner ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:left ear ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:left ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:low-set ears (45%) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:low-set ears (45%) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:mild cochlear hearing loss (1 patient) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:mild cochlear hearing loss (1 patient) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:narrow auditory canals (rare) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:narrow auditory canals (rare) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:near-stenosis of bony portion of auditory canal (in homozygotes) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:near-stenosis of bony portion of auditory canal (in homozygotes) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:no auditory brainstem response (abr) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:no auditory brainstem response (abr) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:no vestibular symptoms ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:no vestibular symptoms | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:normal otoacoustic emissions ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:normal otoacoustic emissions | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:preauricular skin tags (in some patients) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:preauricular skin tags (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:protruding ears (in some patients) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:protruding ears (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:recurrent otitis media in infancy ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:recurrent otitis media in infancy | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:sensorineural hearing loss (less common) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural hearing loss (less common) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:severe to profound deafness ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:severe to profound deafness | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:severe to profound hearing impairment by early adulthood ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:severe to profound hearing impairment by early adulthood | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:small auricles ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:small auricles | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:stenotic ear canals (30%) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:stenotic ear canals (30%) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:stiff, prominent pinnae ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:stiff, prominent pinnae | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:thickened lobes ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:thickened lobes | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:vestibular areflexia, complete ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:vestibular areflexia, complete | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:vestibular hypofunction ---
r_associated #0: 29 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:vestibular hypofunction | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=29
- en:abnormal ear configuration ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormal ear configuration | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:abnormal speech discrimination ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormal speech discrimination | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:absence of earlobe ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:absence of earlobe | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:absence of vestibular evoked myogenic potentials (rare) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:absence of vestibular evoked myogenic potentials (rare) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:absent cochlear microphonic (in older patients) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:absent cochlear microphonic (in older patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:absent ipsilateral middle ear muscle reflexes (in older patients) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:absent ipsilateral middle ear muscle reflexes (in older patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:anomalous middle ear bones ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:anomalous middle ear bones | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:auditory canal stenosis ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:auditory canal stenosis | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:auricular clefts ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:auricular clefts | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:chronic otitis other infection ear ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:chronic otitis other infection ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:congenital hearing loss (1 family) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:congenital hearing loss (1 family) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:congenital sensorineural hearing loss ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:congenital sensorineural hearing loss | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:deafness (in some patients) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:deafness, sensorineural (severe to profound) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, sensorineural (severe to profound) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:deafness, sensorineural, especially affecting high frequencies ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, sensorineural, especially affecting high frequencies | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:deafness, sensorineural, profound (prelingual onset) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, sensorineural, profound (prelingual onset) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:ear pain/earache ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:ear pain/earache | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:external ear ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:external ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:flat ears ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:flat ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:flattened ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:flattened | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:flattened antihelix ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:flattened antihelix | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:fleshy and overfolded helices ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:fleshy and overfolded helices | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:hearing complaints (excluding h84-86) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing complaints (excluding h84-86) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:hearing loss (rare) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss (rare) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:hearing loss, prelingual, severe to profound (affecting all frequencies) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, prelingual, severe to profound (affecting all frequencies) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:hearing normal ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing normal | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:hyperfolded ears ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hyperfolded ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:hypoplastic malleus (1 patient) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hypoplastic malleus (1 patient) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:keratotic plaque around ear meatus ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:keratotic plaque around ear meatus | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:large appearing ears ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:large appearing ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:large ear pinnae ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:large ear pinnae | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:lobule may be separately from the rest of the external ear ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:lobule may be separately from the rest of the external ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:low-set ears (1 patient) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:low-set ears (1 patient) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:low-set ears (rare) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:low-set ears (rare) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:low-set ears (severe form) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:low-set ears (severe form) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:low-set, malformed ears ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:low-set, malformed ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:malformations of the auditory ossicles ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:malformations of the auditory ossicles | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:malformed earlobes ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:malformed earlobes | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:michel aplasia (complete absence of inner ear structures) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:michel aplasia (complete absence of inner ear structures) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:normal middle ear pressures on tympanometry ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:normal middle ear pressures on tympanometry | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:oae responses may decrease with age or use of hearing aids ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:oae responses may decrease with age or use of hearing aids | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:other auditory injuries ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:other auditory injuries | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:otorrhea ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:otorrhea | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:pigmentation of the ear cartilage ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:pigmentation of the ear cartilage | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:poorly shaped ears ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:poorly shaped ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:posteriorly rotated ears (in some patients) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:posteriorly rotated ears (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:prominence and protrusion of upper third of the ear ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:prominence and protrusion of upper third of the ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:prominent crura ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:prominent crura | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:recurrent ear infections ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:recurrent ear infections | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:retroverted ears ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:retroverted ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:rotated ears ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:rotated ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:sensorineural deafness, postlingual, progressive ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural deafness, postlingual, progressive | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:sensorineural deafness, variable (in 1 family) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural deafness, variable (in 1 family) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:severe loss in the higher frequencies by the fifth decade ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:severe loss in the higher frequencies by the fifth decade | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:small earlobe ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:small earlobe | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:small external auditory canals ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:small external auditory canals | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:structure of lymphatic vessel of ear ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:structure of lymphatic vessel of ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:tinnitus (rare) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:tinnitus (rare) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:transient evoked otoacoustic emissions cannot be detected ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:transient evoked otoacoustic emissions cannot be detected | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:u- or bowl-shaped audiogram ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:u- or bowl-shaped audiogram | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:vertigo, episodic ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:vertigo, episodic | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:vestibular abnormalities (variable) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:vestibular abnormalities (variable) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:vestibular hypofunction (rare) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:vestibular hypofunction (rare) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:abnormal auditory temporal processes ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormal auditory temporal processes | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:abnormal or absent auditory nerve and brainstem responses ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormal or absent auditory nerve and brainstem responses | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:absent lobules ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:absent lobules | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:air-bone gap of greater than 20 db across 0.5 to 2 khz ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:air-bone gap of greater than 20 db across 0.5 to 2 khz | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:aplasia of the inner ear ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:aplasia of the inner ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:attached ear lobules ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:attached ear lobules | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:auriculo-condylar syndrome ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:auriculo-condylar syndrome | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:bilateral congenital profound sensorineural hearing loss ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:bilateral congenital profound sensorineural hearing loss | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:cochlear degeneration ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:cochlear degeneration | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:conductive hearing loss, mild bilateral (rare) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:conductive hearing loss, mild bilateral (rare) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:deafness ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:deafness, bilateral sensorineural, high frequency (100% of patients) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, bilateral sensorineural, high frequency (100% of patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:deafness, sensorineural, prelingual, profound ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, sensorineural, prelingual, profound | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:deafness, sensorineural, severe to profound affecting all frequencies ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, sensorineural, severe to profound affecting all frequencies | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:deficient auricle ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deficient auricle | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:ear constriction (97%) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:ear constriction (97%) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:earlobe pits ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:earlobe pits | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:eustachian tube salpingitis ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:eustachian tube salpingitis | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:external ears rudimentary ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:external ears rudimentary | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:fear of ear disease ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:fear of ear disease | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:hearing deficits (28% of adults) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing deficits (28% of adults) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:hearing impairment may occur ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing impairment may occur | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:hearing loss (2 patients) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss (2 patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:hearing loss, conductive or mixed ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, conductive or mixed | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:hearing loss, postlingual ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, postlingual | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural (bilateral, prelingual) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural (bilateral, prelingual) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural (in 1 ashkenazi patient) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural (in 1 ashkenazi patient) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural (type ii) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural (type ii) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, mild progressive (in some patients) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural, mild progressive (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, progressive (childhood-onset) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural, progressive (childhood-onset) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, severe to profound ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural, severe to profound | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:hypertrophic auricular cartilage ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hypertrophic auricular cartilage | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:loss of mid- and low-frequencies later ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:loss of mid- and low-frequencies later | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:low set ears ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:low set ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:low-set, posteriorly rotated ears ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:low-set, posteriorly rotated ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:narrow ear lobes ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:narrow ear lobes | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:near-stenosis of bony portion of auditory canal ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:near-stenosis of bony portion of auditory canal | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:no deafness ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:no deafness | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:no reproducible waves i, iii, or v at high intensities ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:no reproducible waves i, iii, or v at high intensities | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:normal vestibular function ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:normal vestibular function | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:normal vestibular response ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:normal vestibular response | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:otitis media, recurrent (rare) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:otitis media, recurrent (rare) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:outer ear abnormalities (deletion patients) prominent ears ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:outer ear abnormalities (deletion patients) prominent ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:overfolded, rumpled ears ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:overfolded, rumpled ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:posteriorly rotated ears (2p21del) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:posteriorly rotated ears (2p21del) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:prominent antitragus (in some patients) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:prominent antitragus (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:protruding lobules ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:protruding lobules | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:sensation of blocked ears ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensation of blocked ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:sensorineural deafness (rare) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural deafness (rare) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:severe narrowing of cartilagenous auditory canal ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:severe narrowing of cartilagenous auditory canal | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:squared-off ears ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:squared-off ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:stapes fixation ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:stapes fixation | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:superiorly displaced ears ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:superiorly displaced ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:u-shaped audiogram ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:u-shaped audiogram | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:unfolded superior helices ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:unfolded superior helices | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:vestibulopathy, bilateral, progressive ---
r_associated #0: 27 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:vestibulopathy, bilateral, progressive | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=27
- en:abnormally formed ears ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormally formed ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:absent external auditory meatus ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:absent external auditory meatus | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:absent stapedial reflexes or intraoperative stapes immobility ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:absent stapedial reflexes or intraoperative stapes immobility | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:affects all frequencies ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:affects all frequencies | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:affects mid- to high-frequencies ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:affects mid- to high-frequencies | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:anteriorly rotated ears ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:anteriorly rotated ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:atretic ear canals ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:atretic ear canals | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:audiogram shows sloping configuration ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:audiogram shows sloping configuration | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:bilateral dys-synchronized auditory brainstem responses ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:bilateral dys-synchronized auditory brainstem responses | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:cleft lobules ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:cleft lobules | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:conductive hearing loss (in a subset of patients) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:conductive hearing loss (in a subset of patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:deafness, conductive (in some patients) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, conductive (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:deafness, congenital sensorineural, profound (in some patients) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, congenital sensorineural, profound (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:deafness, congenital sensorineural, severe to profound ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, congenital sensorineural, severe to profound | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:deafness, moderate-severe (onset in third decade) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, moderate-severe (onset in third decade) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:deafness, sensorineural, profound ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, sensorineural, profound | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:disproportionately large ears ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:disproportionately large ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:downsloping audiogram ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:downsloping audiogram | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:dysmorphic ears ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:dysmorphic ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:dysplastic ears (jbts) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:dysplastic ears (jbts) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:flat or shallow u-shaped audiogram ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:flat or shallow u-shaped audiogram | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:hearing loss first affects high frequencies ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss first affects high frequencies | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:hearing loss, bilateral sensorineural (profound) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, bilateral sensorineural (profound) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:hearing loss, profound congenital sensorineural ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, profound congenital sensorineural | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural (high frequency) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural (high frequency) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural (in some cases) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural (in some cases) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:impaired tympanic membrane mobility ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:impaired tympanic membrane mobility | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:large ears (2p21del) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:large ears (2p21del) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:lobule creases ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:lobule creases | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:loss of high frequencies at onset ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:loss of high frequencies at onset | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:low-set ears (in 2/4 patients) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:low-set ears (in 2/4 patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:microtia (in some patients) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:microtia (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:middle ear ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:middle ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:mondini malformation ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:mondini malformation | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:narrow external ear canals (1 patient) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:narrow external ear canals (1 patient) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:narrowed external ear canal ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:narrowed external ear canal | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:occasional conductive hearing loss ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:occasional conductive hearing loss | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:posterior helical indentations ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:posterior helical indentations | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:posteriorly rotated ears (1/4 patients) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:posteriorly rotated ears (1/4 patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:presbycusis ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:presbycusis | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:progressive cartilaginous ossification of pinnae ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:progressive cartilaginous ossification of pinnae | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:prominent lobules ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:prominent lobules | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:sensorineural hearing impairment (in some patients) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural hearing impairment (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:sensorineural hearing loss (early-onset form) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural hearing loss (early-onset form) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:sensorineural hearing loss has been reported ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural hearing loss has been reported | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:sensorineural hearing loss, progressive bilateral postlingual ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:sensorineural hearing loss, progressive bilateral postlingual | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:short ear ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:short ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:small cavum conchae ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:small cavum conchae | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:small/rudimentary tragus, antitragus and lobule ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:small/rudimentary tragus, antitragus and lobule | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:squared-off superior helices ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:squared-off superior helices | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:stapes ankylosis ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:stapes ankylosis | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:strabismus (in some patients) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:strabismus (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:tinnitus, bilateral (in some patients) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:tinnitus, bilateral (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:uplifted earlobes ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:uplifted earlobes | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- presbyacousie ---
r_associated #0: 26 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=presbyacousie | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:abnormal bridge connecting the crus of the helix and antihelix ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormal bridge connecting the crus of the helix and antihelix | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:abnormal helices, antihelices and lobules ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormal helices, antihelices and lobules | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:apical cartilage deformity ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:apical cartilage deformity | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:audiogram is gently sloping or flat ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:audiogram is gently sloping or flat | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:auditory neuropathy spectrum disorder ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:auditory neuropathy spectrum disorder | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:blind fistula ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:blind fistula | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:cochleosaccular dysplasia ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:cochleosaccular dysplasia | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:conductive hearing loss (30% of patients) ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:conductive hearing loss (30% of patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:congenital small ears ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:congenital small ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:cupped ears (finding) ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:cupped ears (finding) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:deafness, profound, by 6th decade ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, profound, by 6th decade | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:deafness, secondary to cranial hyperostosis ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, secondary to cranial hyperostosis | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:disjunction of otherwise normal lobule from remainder of ear ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:disjunction of otherwise normal lobule from remainder of ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:ears deficient in cartilage ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:ears deficient in cartilage | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:hearing loss, bilateral progressive post-lingual ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, bilateral progressive post-lingual | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural (in one family) ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural (in one family) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural, associated with elsts ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural, associated with elsts | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges) ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:large auricle ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:large auricle | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:otitis with effusion ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:otitis with effusion | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:presbycousis ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:presbycousis | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:roll-head ---
r_associated #0: 25 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:roll-head | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=25
- en:abnormal middle ear reflexes ---
r_associated #0: 24 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormal middle ear reflexes | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=24
- en:absence of the cochlear nerves (reported in 1 patient) ---
r_associated #0: 24 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:absence of the cochlear nerves (reported in 1 patient) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=24
- en:absent or abnormal otoacoustic emissions ---
r_associated #0: 24 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:absent or abnormal otoacoustic emissions | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=24
- en:absent stapedial reflex ---
r_associated #0: 24 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:absent stapedial reflex | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=24
- en:acute otitis media/myringitis ---
r_associated #0: 24 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:acute otitis media/myringitis | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=24
- en:approximately 0.7db per year hearing loss at all frequencies ---
r_associated #0: 24 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:approximately 0.7db per year hearing loss at all frequencies | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=24
- en:conductive hearing loss to due otitis media ---
r_associated #0: 24 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:conductive hearing loss to due otitis media | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=24
- en:congenital ear anomaly nos (disorder) ---
r_associated #0: 24 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:congenital ear anomaly nos (disorder) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=24
- en:deafness affects all frequencies ---
r_associated #0: 24 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness affects all frequencies | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=24
- en:deafness, unilateral, childhood onset ---
r_associated #0: 24 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, unilateral, childhood onset | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=24
- en:disturbance of equilibrium ---
r_associated #0: 24 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:disturbance of equilibrium | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=24
- en:downward sloping or flat audiogram ---
r_associated #0: 24 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:downward sloping or flat audiogram | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=24
- en:expansion of helical fold at superior point of true longitudinal axis of ear ---
r_associated #0: 24 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:expansion of helical fold at superior point of true longitudinal axis of ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=24
- en:external ear defects (47%) ---
r_associated #0: 24 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:external ear defects (47%) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=24
- en:flat audiogram ---
r_associated #0: 24 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:flat audiogram | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=24
- en:hearing impairment (in some patients) ---
r_associated #0: 24 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing impairment (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=24
- en:hearing impairment, sensorineural, mild ---
r_associated #0: 24 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing impairment, sensorineural, mild | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=24
- en:hearing loss, progressive sensorineural, affecting high frequencies ---
r_associated #0: 24 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, progressive sensorineural, affecting high frequencies | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=24
- en:other symptom/complaint of ear ---
r_associated #0: 24 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:other symptom/complaint of ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=24
- en:presbyacusis ---
r_associated #0: 24 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:presbyacusis | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=24
- en:right ear ---
r_associated #0: 24 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:right ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=24
- esgourde ---
r_associated #0: 24 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=esgourde | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=24
- en:abnormal amplitude modulation detection ---
r_associated #0: 23 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormal amplitude modulation detection | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=23
- en:absent vestibular function (caloric test) ---
r_associated #0: 23 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:absent vestibular function (caloric test) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=23
- en:asymmetry of the ears ---
r_associated #0: 23 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:asymmetry of the ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=23
- en:bat ear ---
r_associated #0: 23 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:bat ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=23
- en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss) ---
r_associated #0: 23 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=23
- en:cupped pinna ---
r_associated #0: 23 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:cupped pinna | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=23
- en:deafness, sensorineural, variable ---
r_associated #0: 23 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, sensorineural, variable | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=23
- en:deep-set ears ---
r_associated #0: 23 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deep-set ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=23
- en:dysplastic ears (in some patients) ---
r_associated #0: 23 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:dysplastic ears (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=23
- en:hearing loss, congenital, profound (250-8,000 hz) ---
r_associated #0: 23 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, congenital, profound (250-8,000 hz) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=23
- en:hearing loss, postlingual progressive sensorineural ---
r_associated #0: 23 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, postlingual progressive sensorineural | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural, mid-frequency (in some patients) ---
r_associated #0: 23 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural, mid-frequency (in some patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=23
- en:serous otitis ---
r_associated #0: 23 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:serous otitis | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=23
- en:vertiginous syndrome ---
r_associated #0: 23 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:vertiginous syndrome | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=23
- en:abnormal brainstem auditory evoked potentials (baep) ---
r_associated #0: 22 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormal brainstem auditory evoked potentials (baep) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=22
- en:abnormal ears ---
r_associated #0: 22 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormal ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=22
- en:abnormal semicircular canals ---
r_associated #0: 22 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormal semicircular canals | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=22
- en:abnormality of the outer ear ---
r_associated #0: 22 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormality of the outer ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=22
- en:abnormally folded ears ---
r_associated #0: 22 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:abnormally folded ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=22
- en:attached ear lobes ---
r_associated #0: 22 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:attached ear lobes | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=22
- en:chronic otitis ---
r_associated #0: 22 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:chronic otitis | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=22
- en:cleft at the junction of the lobule and helix ---
r_associated #0: 22 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:cleft at the junction of the lobule and helix | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=22
- en:conductive and sensorineural hearing loss ---
r_associated #0: 22 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:conductive and sensorineural hearing loss | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=22
- en:deafness in 30-50% of patients with skull involvement ---
r_associated #0: 22 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness in 30-50% of patients with skull involvement | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=22
- en:deafness, congenital nonprogressive sensorineural symmetric, moderate ---
r_associated #0: 22 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, congenital nonprogressive sensorineural symmetric, moderate | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=22
- en:decreased auditory brainstem responses ---
r_associated #0: 22 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:decreased auditory brainstem responses | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=22
- en:hearing impairment, mild (2 patients) ---
r_associated #0: 22 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing impairment, mild (2 patients) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=22
- en:hearing loss, conductive (rare) ---
r_associated #0: 22 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, conductive (rare) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=22
- en:hearing loss, mild ---
r_associated #0: 22 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, mild | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural (in sister) ---
r_associated #0: 22 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural (in sister) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural (variable) ---
r_associated #0: 22 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural (variable) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=22
- en:absent brainstem auditory-evoked responses ---
r_associated #0: 21 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:absent brainstem auditory-evoked responses | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=21
- en:absent earlobe ---
r_associated #0: 21 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:absent earlobe | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=21
- en:conductive hearing loss, bilateral ---
r_associated #0: 21 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:conductive hearing loss, bilateral | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=21
- en:cup-shaped auricles ---
r_associated #0: 21 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:cup-shaped auricles | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=21
- en:deafness, nonprogressive, moderate ---
r_associated #0: 21 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, nonprogressive, moderate | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=21
- en:deafness, prelingual, profound (affects all frequencies) ---
r_associated #0: 21 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, prelingual, profound (affects all frequencies) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=21
- en:deafness, sensorineural, especially affecting high frequencies (in about 55% of males and 45% of females) ---
r_associated #0: 21 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deafness, sensorineural, especially affecting high frequencies (in about 55% of males and 45% of females) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=21
- en:dysplastic pinnae ---
r_associated #0: 21 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:dysplastic pinnae | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=21
- en:ear pits, posterior helical ---
r_associated #0: 21 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:ear pits, posterior helical | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=21
- en:escalope ---
r_associated #0: 21 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:escalope | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=21
- en:glue ear ---
r_associated #0: 21 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:glue ear | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=21
- en:hearing loss, conductive (in one family) ---
r_associated #0: 21 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, conductive (in one family) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=21
- en:hearing loss, high-frequency (onset in childhood-adolescence) ---
r_associated #0: 21 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, high-frequency (onset in childhood-adolescence) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=21
- en:hearing loss, mixed, mild to severe (in heterozygotes) ---
r_associated #0: 21 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, mixed, mild to severe (in heterozygotes) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=21
- en:hearing loss, moderate to severe, bilateral, nonprogressive ---
r_associated #0: 21 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, moderate to severe, bilateral, nonprogressive | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=21
- en:otolaryngologist ---
r_associated #0: 21 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:otolaryngologist | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=21
- en:otorhinolaryngologist ---
r_associated #0: 21 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:otorhinolaryngologist | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=21
- en:tinnitus ---
r_associated #0: 21 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:tinnitus | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=21
- en:and throat ---
r_associated #0: 20 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:and throat | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=20
- en:nose and throat ---
r_associated #0: 20 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:nose and throat | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=20
- nose ---
r_associated #0: 20 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=nose | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=20
- Trouble de l'équilibre ---
r_associated #0: 15 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=Trouble de l'équilibre | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=15
- en:dizzy spells ---
r_associated #0: 15 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:dizzy spells | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=15
- en:giddiness ---
r_associated #0: 15 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:giddiness | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=15
- en:scatterbrain ---
r_associated #0: 15 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:scatterbrain | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=15
- vertiges ---
r_associated #0: 15 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=vertiges | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=15
- vertigineux ---
r_associated #0: 15 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=vertigineux | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=15
- Étourdi ---
r_associated #0: 15 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=Étourdi | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=15
- Étourdie ---
r_associated #0: 15 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=Étourdie | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=15
- étourdie ---
r_associated #0: 15 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=étourdie | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=15
- étourdies ---
r_associated #0: 15 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=étourdies | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=15
- étourdis ---
r_associated #0: 15 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=étourdis | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=15
- étourdissements ---
r_associated #0: 15 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=étourdissements | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=15
- Hyperacousie ---
r_associated #0: 10 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=Hyperacousie | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=10
- Oto-rhino-laryngologiste ---
r_associated #0: 10 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=Oto-rhino-laryngologiste | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=10
- Otorhinolaryngologiste ---
r_associated #0: 10 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=Otorhinolaryngologiste | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=10
- Presbyacousie ---
r_associated #0: 10 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=Presbyacousie | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=10
- ankylose stapédo-vestibulaire ---
r_associated #0: 10 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=ankylose stapédo-vestibulaire | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=10
- ankylose stapédo-vestibulaire l.f. ---
r_associated #0: 10 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=ankylose stapédo-vestibulaire l.f. | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=10
- aplati ---
r_associated #0: 10 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=aplati | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=10
- en:deaf-muteness ---
r_associated #0: 10 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deaf-muteness | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=10
- en:deaf-mutism ---
r_associated #0: 10 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:deaf-mutism | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=10
- en:hearing defect ---
r_associated #0: 10 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing defect | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=10
- en:hearing deficiency ---
r_associated #0: 10 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing deficiency | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=10
- en:lughole ---
r_associated #0: 10 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:lughole | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=10
- en:schitzel ---
r_associated #0: 10 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:schitzel | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=10
- en:speech difficulties due to deafness ---
r_associated #0: 10 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:speech difficulties due to deafness | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=10
- oreille moyenne ---
r_associated #0: 10 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=oreille moyenne | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=10
- otite moyenne adhésive ---
r_associated #0: 10 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=otite moyenne adhésive | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=10
- prérupture utérine (syndrome de) ---
r_associated #0: 10 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=prérupture utérine (syndrome de) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=10
- surdité ---
r_associated #0: 10 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=surdité | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=10
- tête de linotte ---
r_associated #0: 10 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=tête de linotte | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=10
- Étourdissements ---
r_associated #0: 10 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=Étourdissements | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=10
- à priori ---
r_associated #0: 10 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=à priori | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=10
- Sensation de rotation ---
r_associated #0: 5 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=Sensation de rotation | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=5
- escalope ---
r_associated #0: -20 -->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=escalope | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=-20
|