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'en:deafness due to bilateral cochlear malformation (rare)'
(id=6815147 ; fe=en:deafness due to bilateral cochlear malformation (rare) ; type=1 ; niveau=200 ; luminosité=25 ; somme entrante=27857 creation date=2017-06-25 touchdate=2025-10-08 08:51:21.000)
≈ 738 relations sortantes

  1. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 43 / 1 -> en:hearing impairment, sensorineural, mild
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing impairment, sensorineural, mild | rel=r_associated | relid=0 | w=43
  2. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 43 / 1 -> en:large anteverted pinnae (90% males, 40% females)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:large anteverted pinnae (90% males, 40% females) | rel=r_associated | relid=0 | w=43
  3. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 43 / 1 -> en:sensorineural hearing loss (in 1 of 3 patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural hearing loss (in 1 of 3 patients) | rel=r_associated | relid=0 | w=43
  4. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 42 / 0.977 -> en:cupped pinna
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:cupped pinna | rel=r_associated | relid=0 | w=42
  5. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 42 / 0.977 -> en:hearing loss, conductive (in one family)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, conductive (in one family) | rel=r_associated | relid=0 | w=42
  6. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 42 / 0.977 -> en:narrow ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:narrow ears | rel=r_associated | relid=0 | w=42
  7. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 42 / 0.977 -> en:progressive cartilaginous ossification of pinnae
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:progressive cartilaginous ossification of pinnae | rel=r_associated | relid=0 | w=42
  8. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 42 / 0.977 -> en:rudimentary ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:rudimentary ear | rel=r_associated | relid=0 | w=42
  9. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 42 / 0.977 -> en:vertiginous syndrome
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:vertiginous syndrome | rel=r_associated | relid=0 | w=42
  10. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 42 / 0.977 -> en:vertigo, single occurrence (in 2 patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:vertigo, single occurrence (in 2 patients) | rel=r_associated | relid=0 | w=42
  11. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 41 / 0.953 -> en:dorsally rotated ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:dorsally rotated ears | rel=r_associated | relid=0 | w=41
  12. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 41 / 0.953 -> en:malformations of the auditory ossicles
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:malformations of the auditory ossicles | rel=r_associated | relid=0 | w=41
  13. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 41 / 0.953 -> en:mild to moderate hearing loss across most frequencies
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:mild to moderate hearing loss across most frequencies | rel=r_associated | relid=0 | w=41
  14. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 41 / 0.953 -> en:posteriorly rotated ears (2p21del)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:posteriorly rotated ears (2p21del) | rel=r_associated | relid=0 | w=41
  15. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 40 / 0.93 -> en:audiogram shows sloping configuration
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:audiogram shows sloping configuration | rel=r_associated | relid=0 | w=40
  16. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 40 / 0.93 -> en:deep-set ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deep-set ears | rel=r_associated | relid=0 | w=40
  17. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 40 / 0.93 -> en:disproportionately large ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:disproportionately large ears | rel=r_associated | relid=0 | w=40
  18. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 40 / 0.93 -> en:hypoacusia (1 patient)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hypoacusia (1 patient) | rel=r_associated | relid=0 | w=40
  19. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 40 / 0.93 -> en:large, floppy ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:large, floppy ears | rel=r_associated | relid=0 | w=40
  20. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 40 / 0.93 -> en:pale, stiff pinnae
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:pale, stiff pinnae | rel=r_associated | relid=0 | w=40
  21. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 40 / 0.93 -> en:protruding right ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:protruding right ear | rel=r_associated | relid=0 | w=40
  22. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 39 / 0.907 -> en:flat audiogram
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:flat audiogram | rel=r_associated | relid=0 | w=39
  23. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 39 / 0.907 -> en:hearing loss (rare)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss (rare) | rel=r_associated | relid=0 | w=39
  24. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 39 / 0.907 -> en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges) | rel=r_associated | relid=0 | w=39
  25. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 38 / 0.884 -> en:deafness (sensorineural or mixed sensorineural and conductive)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness (sensorineural or mixed sensorineural and conductive) | rel=r_associated | relid=0 | w=38
  26. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 38 / 0.884 -> en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies) | rel=r_associated | relid=0 | w=38
  27. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 38 / 0.884 -> en:hypoplastic helices
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hypoplastic helices | rel=r_associated | relid=0 | w=38
  28. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 38 / 0.884 -> en:hypoplastic malleus (1 patient)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hypoplastic malleus (1 patient) | rel=r_associated | relid=0 | w=38
  29. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 38 / 0.884 -> en:narrowed external ear canal (30% of patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:narrowed external ear canal (30% of patients) | rel=r_associated | relid=0 | w=38
  30. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 38 / 0.884 -> en:protruding ears (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:protruding ears (in some patients) | rel=r_associated | relid=0 | w=38
  31. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 37 / 0.86 -> en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile) | rel=r_associated | relid=0 | w=37
  32. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 37 / 0.86 -> en:deafness, sensorineural, especially affecting high frequencies
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, sensorineural, especially affecting high frequencies | rel=r_associated | relid=0 | w=37
  33. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 37 / 0.86 -> en:deafness, stable bilateral symmetric prelingual
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, stable bilateral symmetric prelingual | rel=r_associated | relid=0 | w=37
  34. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 36 / 0.837 -> en:absence of vestibular evoked myogenic potentials (rare)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:absence of vestibular evoked myogenic potentials (rare) | rel=r_associated | relid=0 | w=36
  35. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 36 / 0.837 -> en:internal auditory canal hypoplasia
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:internal auditory canal hypoplasia | rel=r_associated | relid=0 | w=36
  36. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 36 / 0.837 -> en:large pinnae
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:large pinnae | rel=r_associated | relid=0 | w=36
  37. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 36 / 0.837 -> en:preauricular pits (70-80% of patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:preauricular pits (70-80% of patients) | rel=r_associated | relid=0 | w=36
  38. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 36 / 0.837 -> en:raised earlobes
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:raised earlobes | rel=r_associated | relid=0 | w=36
  39. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:abnormal amplitude modulation detection
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormal amplitude modulation detection | rel=r_associated | relid=0 | w=35
  40. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:abnormal auricles
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormal auricles | rel=r_associated | relid=0 | w=35
  41. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:abnormality of the middle ear ossicles
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormality of the middle ear ossicles | rel=r_associated | relid=0 | w=35
  42. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:abnormality of the pinna
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormality of the pinna | rel=r_associated | relid=0 | w=35
  43. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:abnormally folded helix
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormally folded helix | rel=r_associated | relid=0 | w=35
  44. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:absent brainstem auditory responses
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:absent brainstem auditory responses | rel=r_associated | relid=0 | w=35
  45. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:absent vestibular function (caloric test)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:absent vestibular function (caloric test) | rel=r_associated | relid=0 | w=35
  46. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:anteverted pinnae
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:anteverted pinnae | rel=r_associated | relid=0 | w=35
  47. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:attached ear lobes
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:attached ear lobes | rel=r_associated | relid=0 | w=35
  48. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:attached ear lobules
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:attached ear lobules | rel=r_associated | relid=0 | w=35
  49. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:auditory impairment
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:auditory impairment | rel=r_associated | relid=0 | w=35
  50. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:auriculo-condylar syndrome
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:auriculo-condylar syndrome | rel=r_associated | relid=0 | w=35
  51. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:bilateral congenital profound sensorineural hearing loss
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:bilateral congenital profound sensorineural hearing loss | rel=r_associated | relid=0 | w=35
  52. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:bilateral dys-synchronized auditory brainstem responses
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:bilateral dys-synchronized auditory brainstem responses | rel=r_associated | relid=0 | w=35
  53. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:blind fistula
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:blind fistula | rel=r_associated | relid=0 | w=35
  54. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:cochlear malformation
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:cochlear malformation | rel=r_associated | relid=0 | w=35
  55. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:congenital ear anomaly nos (disorder)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:congenital ear anomaly nos (disorder) | rel=r_associated | relid=0 | w=35
  56. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:congenital sensorineural hearing loss
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:congenital sensorineural hearing loss | rel=r_associated | relid=0 | w=35
  57. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:cup-shaped auricles
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:cup-shaped auricles | rel=r_associated | relid=0 | w=35
  58. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:deafness
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness | rel=r_associated | relid=0 | w=35
  59. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:deafness (variable)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness (variable) | rel=r_associated | relid=0 | w=35
  60. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:downward sloping or flat audiogram
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:downward sloping or flat audiogram | rel=r_associated | relid=0 | w=35
  61. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:ear constriction (97%)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:ear constriction (97%) | rel=r_associated | relid=0 | w=35
  62. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:flat ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:flat ears | rel=r_associated | relid=0 | w=35
  63. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:hearing impairment may occur
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing impairment may occur | rel=r_associated | relid=0 | w=35
  64. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:hearing loss (affecting all frequencies), moderate to severe
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss (affecting all frequencies), moderate to severe | rel=r_associated | relid=0 | w=35
  65. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:hearing loss, high-frequency (onset in childhood-adolescence)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, high-frequency (onset in childhood-adolescence) | rel=r_associated | relid=0 | w=35
  66. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:hearing loss, mild (rare)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, mild (rare) | rel=r_associated | relid=0 | w=35
  67. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:hearing loss, moderate to severe, bilateral, nonprogressive
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, moderate to severe, bilateral, nonprogressive | rel=r_associated | relid=0 | w=35
  68. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:hearing loss, progressive (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, progressive (in some patients) | rel=r_associated | relid=0 | w=35
  69. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies) | rel=r_associated | relid=0 | w=35
  70. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:hearing loss, sensorineural (in patients with larger deletions)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural (in patients with larger deletions) | rel=r_associated | relid=0 | w=35
  71. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:hearing loss, sensorineural (in some cases)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural (in some cases) | rel=r_associated | relid=0 | w=35
  72. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:hearing loss, sensorineural, mild progressive (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural, mild progressive (in some patients) | rel=r_associated | relid=0 | w=35
  73. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:hearing loss, sensorineural, severe to profound
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural, severe to profound | rel=r_associated | relid=0 | w=35
  74. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:hypoplastic pinnae (30-60% of patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hypoplastic pinnae (30-60% of patients) | rel=r_associated | relid=0 | w=35
  75. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:inner ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:inner ear | rel=r_associated | relid=0 | w=35
  76. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:large fleshy ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:large fleshy ears | rel=r_associated | relid=0 | w=35
  77. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:linear ear lobe creases
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:linear ear lobe creases | rel=r_associated | relid=0 | w=35
  78. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:lobule may be separately from the rest of the external ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:lobule may be separately from the rest of the external ear | rel=r_associated | relid=0 | w=35
  79. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:low-frequency sensorineural hearing impairment
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:low-frequency sensorineural hearing impairment | rel=r_associated | relid=0 | w=35
  80. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:malformed ossicular chain
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:malformed ossicular chain | rel=r_associated | relid=0 | w=35
  81. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:malformed pinnae (30-60% of patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:malformed pinnae (30-60% of patients) | rel=r_associated | relid=0 | w=35
  82. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:mild hearing impairment (13%)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:mild hearing impairment (13%) | rel=r_associated | relid=0 | w=35
  83. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:mild to moderate hearing loss
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:mild to moderate hearing loss | rel=r_associated | relid=0 | w=35
  84. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:misshapen ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:misshapen ear | rel=r_associated | relid=0 | w=35
  85. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:narrow intertragic notch
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:narrow intertragic notch | rel=r_associated | relid=0 | w=35
  86. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:normal cochlear microphonics
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:normal cochlear microphonics | rel=r_associated | relid=0 | w=35
  87. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:otitis externa
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:otitis externa | rel=r_associated | relid=0 | w=35
  88. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:partial aplasia of external auditory canal ending in blind fistula (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:partial aplasia of external auditory canal ending in blind fistula (in some patients) | rel=r_associated | relid=0 | w=35
  89. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:preauricular sinus, bilateral
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:preauricular sinus, bilateral | rel=r_associated | relid=0 | w=35
  90. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:preauricular skin furrow
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:preauricular skin furrow | rel=r_associated | relid=0 | w=35
  91. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:prelingual onset
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:prelingual onset | rel=r_associated | relid=0 | w=35
  92. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:progressive high-frequency hearing loss (onset 20-30 years)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:progressive high-frequency hearing loss (onset 20-30 years) | rel=r_associated | relid=0 | w=35
  93. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:prominent helices
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:prominent helices | rel=r_associated | relid=0 | w=35
  94. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:recurrent otitis media
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:recurrent otitis media | rel=r_associated | relid=0 | w=35
  95. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:right ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:right ear | rel=r_associated | relid=0 | w=35
  96. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:secretory otitis media
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:secretory otitis media | rel=r_associated | relid=0 | w=35
  97. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:sensorineural hearing loss (described in 1 family)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural hearing loss (described in 1 family) | rel=r_associated | relid=0 | w=35
  98. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:sensorineural hearing loss has been reported
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural hearing loss has been reported | rel=r_associated | relid=0 | w=35
  99. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:simple auricles
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:simple auricles | rel=r_associated | relid=0 | w=35
  100. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:simplified helices
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:simplified helices | rel=r_associated | relid=0 | w=35
  101. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:small cavum conchae
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:small cavum conchae | rel=r_associated | relid=0 | w=35
  102. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:small external auditory canals
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:small external auditory canals | rel=r_associated | relid=0 | w=35
  103. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:small external auditory meatus
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:small external auditory meatus | rel=r_associated | relid=0 | w=35
  104. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:stenosis of external auditory canal
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:stenosis of external auditory canal | rel=r_associated | relid=0 | w=35
  105. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 35 / 0.814 -> en:synotus
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:synotus | rel=r_associated | relid=0 | w=35
  106. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:abnormal gap detection
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormal gap detection | rel=r_associated | relid=0 | w=34
  107. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:abnormal or absent auditory nerve and brainstem responses
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormal or absent auditory nerve and brainstem responses | rel=r_associated | relid=0 | w=34
  108. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:absence of acoustic reflex
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:absence of acoustic reflex | rel=r_associated | relid=0 | w=34
  109. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:absent ipsilateral middle ear muscle reflexes (in older patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:absent ipsilateral middle ear muscle reflexes (in older patients) | rel=r_associated | relid=0 | w=34
  110. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:absent or decreased auditory brainstem responses
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:absent or decreased auditory brainstem responses | rel=r_associated | relid=0 | w=34
  111. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:anterior creases of earlobe
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:anterior creases of earlobe | rel=r_associated | relid=0 | w=34
  112. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:apical cartilage deformity
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:apical cartilage deformity | rel=r_associated | relid=0 | w=34
  113. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:asymmetry of the ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:asymmetry of the ears | rel=r_associated | relid=0 | w=34
  114. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:cochlear malformation defect (mondini dysplasia) (less common)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:cochlear malformation defect (mondini dysplasia) (less common) | rel=r_associated | relid=0 | w=34
  115. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:cupped ears (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:cupped ears (in some patients) | rel=r_associated | relid=0 | w=34
  116. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:deafness (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness (in some patients) | rel=r_associated | relid=0 | w=34
  117. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:deafness, congenital sensorineural, severe to profound
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, congenital sensorineural, severe to profound | rel=r_associated | relid=0 | w=34
  118. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:deafness, prelingual, profound (affects all frequencies)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, prelingual, profound (affects all frequencies) | rel=r_associated | relid=0 | w=34
  119. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:deafness, profound congenital sensorineural
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, profound congenital sensorineural | rel=r_associated | relid=0 | w=34
  120. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:deafness, profound, by 6th decade
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, profound, by 6th decade | rel=r_associated | relid=0 | w=34
  121. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:deafness, secondary to cranial hyperostosis
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, secondary to cranial hyperostosis | rel=r_associated | relid=0 | w=34
  122. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:deafness, sensorineural (45%)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, sensorineural (45%) | rel=r_associated | relid=0 | w=34
  123. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:deafness, sensorineural, mild (rare)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, sensorineural, mild (rare) | rel=r_associated | relid=0 | w=34
  124. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:decreased auditory brainstem responses
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:decreased auditory brainstem responses | rel=r_associated | relid=0 | w=34
  125. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:disjunction of otherwise normal lobule from remainder of ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:disjunction of otherwise normal lobule from remainder of ear | rel=r_associated | relid=0 | w=34
  126. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:dysplastic pinnae
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:dysplastic pinnae | rel=r_associated | relid=0 | w=34
  127. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:ear cartilage calcification
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:ear cartilage calcification | rel=r_associated | relid=0 | w=34
  128. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:ear neoplasm
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:ear neoplasm | rel=r_associated | relid=0 | w=34
  129. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:ear tag
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:ear tag | rel=r_associated | relid=0 | w=34
  130. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:entire ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:entire ear | rel=r_associated | relid=0 | w=34
  131. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:external ear defects (47%)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:external ear defects (47%) | rel=r_associated | relid=0 | w=34
  132. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:external ears rudimentary
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:external ears rudimentary | rel=r_associated | relid=0 | w=34
  133. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:fleshy and overfolded helices
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:fleshy and overfolded helices | rel=r_associated | relid=0 | w=34
  134. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:folded helix
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:folded helix | rel=r_associated | relid=0 | w=34
  135. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:hearing complaints (excluding h84-86)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing complaints (excluding h84-86) | rel=r_associated | relid=0 | w=34
  136. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:hearing impairment, sensorineural, fluctuating
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing impairment, sensorineural, fluctuating | rel=r_associated | relid=0 | w=34
  137. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:hearing loss (1 patient)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss (1 patient) | rel=r_associated | relid=0 | w=34
  138. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:hearing loss (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss (in some patients) | rel=r_associated | relid=0 | w=34
  139. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:hearing loss first affects high frequencies
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss first affects high frequencies | rel=r_associated | relid=0 | w=34
  140. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:hearing loss, conductive (rare)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, conductive (rare) | rel=r_associated | relid=0 | w=34
  141. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:hearing loss, congenital sensorineural, severe to profound
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, congenital sensorineural, severe to profound | rel=r_associated | relid=0 | w=34
  142. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:hearing loss, mild
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, mild | rel=r_associated | relid=0 | w=34
  143. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:hearing loss, more severe at lower frequencies
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, more severe at lower frequencies | rel=r_associated | relid=0 | w=34
  144. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:hearing loss, postlingual sensorineural
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, postlingual sensorineural | rel=r_associated | relid=0 | w=34
  145. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:hearing loss, profound congenital sensorineural
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, profound congenital sensorineural | rel=r_associated | relid=0 | w=34
  146. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:hearing loss, progressive conductive and/or sensorineural, during adulthood
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, progressive conductive and/or sensorineural, during adulthood | rel=r_associated | relid=0 | w=34
  147. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:hearing loss, sensorineural (in sister)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural (in sister) | rel=r_associated | relid=0 | w=34
  148. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:hearing loss, unilateral or bilateral, conductive, sensorineural, or mixed
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, unilateral or bilateral, conductive, sensorineural, or mixed | rel=r_associated | relid=0 | w=34
  149. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:hearing normal
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing normal | rel=r_associated | relid=0 | w=34
  150. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:high-frequency tinnitus at onset
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:high-frequency tinnitus at onset | rel=r_associated | relid=0 | w=34
  151. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:high-tone sensorineural deafness (67% of patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:high-tone sensorineural deafness (67% of patients) | rel=r_associated | relid=0 | w=34
  152. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:hyperacusis
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hyperacusis | rel=r_associated | relid=0 | w=34
  153. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:hypoplastic ears fused to the scalp
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hypoplastic ears fused to the scalp | rel=r_associated | relid=0 | w=34
  154. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:large anteverted ears (rare)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:large anteverted ears (rare) | rel=r_associated | relid=0 | w=34
  155. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:large ears (2p21del)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:large ears (2p21del) | rel=r_associated | relid=0 | w=34
  156. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:large ears (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:large ears (in some patients) | rel=r_associated | relid=0 | w=34
  157. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:large, dysmorphic ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:large, dysmorphic ears | rel=r_associated | relid=0 | w=34
  158. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:loss of mid- and low-frequencies later
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:loss of mid- and low-frequencies later | rel=r_associated | relid=0 | w=34
  159. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:low-set ears (28%)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:low-set ears (28%) | rel=r_associated | relid=0 | w=34
  160. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:low-set, posteriorly rotated ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:low-set, posteriorly rotated ears | rel=r_associated | relid=0 | w=34
  161. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies | rel=r_associated | relid=0 | w=34
  162. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:no deafness
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:no deafness | rel=r_associated | relid=0 | w=34
  163. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:poorly folded ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:poorly folded ears | rel=r_associated | relid=0 | w=34
  164. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:pre- and post-auricular skin or cartilaginous tags
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:pre- and post-auricular skin or cartilaginous tags | rel=r_associated | relid=0 | w=34
  165. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:preauricular fistulas, bilateral
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:preauricular fistulas, bilateral | rel=r_associated | relid=0 | w=34
  166. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face) | rel=r_associated | relid=0 | w=34
  167. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:prominence and protrusion of upper third of the ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:prominence and protrusion of upper third of the ear | rel=r_associated | relid=0 | w=34
  168. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:prominent antitragus (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:prominent antitragus (in some patients) | rel=r_associated | relid=0 | w=34
  169. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:prominent ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:prominent ear | rel=r_associated | relid=0 | w=34
  170. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:retroverted ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:retroverted ears | rel=r_associated | relid=0 | w=34
  171. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:sensorineural deafness, postlingual, progressive
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural deafness, postlingual, progressive | rel=r_associated | relid=0 | w=34
  172. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:sensorineural deafness, variable (in 1 family)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural deafness, variable (in 1 family) | rel=r_associated | relid=0 | w=34
  173. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:sensorineural hearing loss
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural hearing loss | rel=r_associated | relid=0 | w=34
  174. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:sensory hearing loss
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensory hearing loss | rel=r_associated | relid=0 | w=34
  175. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:serous otitis media
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:serous otitis media | rel=r_associated | relid=0 | w=34
  176. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:shallow skin dimple on posterior surface of ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:shallow skin dimple on posterior surface of ear | rel=r_associated | relid=0 | w=34
  177. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:simple ear structure
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:simple ear structure | rel=r_associated | relid=0 | w=34
  178. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:small ears (female)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:small ears (female) | rel=r_associated | relid=0 | w=34
  179. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:structure of lymphatic vessel of ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:structure of lymphatic vessel of ear | rel=r_associated | relid=0 | w=34
  180. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:thick earlobes
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:thick earlobes | rel=r_associated | relid=0 | w=34
  181. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:tinnitus (variable)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:tinnitus (variable) | rel=r_associated | relid=0 | w=34
  182. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:underdeveloped nasal alae
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:underdeveloped nasal alae | rel=r_associated | relid=0 | w=34
  183. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:uplift of earlobes (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:uplift of earlobes (in some patients) | rel=r_associated | relid=0 | w=34
  184. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:vestibular abnormalities (variable)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:vestibular abnormalities (variable) | rel=r_associated | relid=0 | w=34
  185. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:vestibular hypofunction (rare)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:vestibular hypofunction (rare) | rel=r_associated | relid=0 | w=34
  186. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 34 / 0.791 -> en:vestibular involvement (variable)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:vestibular involvement (variable) | rel=r_associated | relid=0 | w=34
  187. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:abnormal auditory temporal processes
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormal auditory temporal processes | rel=r_associated | relid=0 | w=32
  188. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:abnormal bridge connecting the crus of the helix and antihelix
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormal bridge connecting the crus of the helix and antihelix | rel=r_associated | relid=0 | w=32
  189. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:absent external auditory canals
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:absent external auditory canals | rel=r_associated | relid=0 | w=32
  190. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:affects all frequencies
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:affects all frequencies | rel=r_associated | relid=0 | w=32
  191. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:aplasia of the inner ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:aplasia of the inner ear | rel=r_associated | relid=0 | w=32
  192. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:atresia of the external auditory canal
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:atresia of the external auditory canal | rel=r_associated | relid=0 | w=32
  193. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:atretic auditory canal
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:atretic auditory canal | rel=r_associated | relid=0 | w=32
  194. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:atretic ear canals
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:atretic ear canals | rel=r_associated | relid=0 | w=32
  195. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:audiogram is gently sloping or flat
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:audiogram is gently sloping or flat | rel=r_associated | relid=0 | w=32
  196. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:aural fullness
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:aural fullness | rel=r_associated | relid=0 | w=32
  197. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:cleft at the junction of the lobule and helix
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:cleft at the junction of the lobule and helix | rel=r_associated | relid=0 | w=32
  198. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:cleft at the superior portion of the pinna
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:cleft at the superior portion of the pinna | rel=r_associated | relid=0 | w=32
  199. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:conductive hearing loss (30% of patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:conductive hearing loss (30% of patients) | rel=r_associated | relid=0 | w=32
  200. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:conductive hearing loss to due otitis media
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:conductive hearing loss to due otitis media | rel=r_associated | relid=0 | w=32
  201. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:cupped ears (finding)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:cupped ears (finding) | rel=r_associated | relid=0 | w=32
  202. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:cystic dilatation of cochlea and vestibulum
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:cystic dilatation of cochlea and vestibulum | rel=r_associated | relid=0 | w=32
  203. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:deafness in 30-50% of patients with skull involvement
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness in 30-50% of patients with skull involvement | rel=r_associated | relid=0 | w=32
  204. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:deafness, sensorineural (reported in 1 family)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, sensorineural (reported in 1 family) | rel=r_associated | relid=0 | w=32
  205. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:dilatated internal auditory canal
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:dilatated internal auditory canal | rel=r_associated | relid=0 | w=32
  206. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:dysplastic helices
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:dysplastic helices | rel=r_associated | relid=0 | w=32
  207. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:earlobe pits
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:earlobe pits | rel=r_associated | relid=0 | w=32
  208. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:ears deficient in cartilage
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:ears deficient in cartilage | rel=r_associated | relid=0 | w=32
  209. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:flat or shallow u-shaped audiogram
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:flat or shallow u-shaped audiogram | rel=r_associated | relid=0 | w=32
  210. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:flattened
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:flattened | rel=r_associated | relid=0 | w=32
  211. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:hearing disorder (1 patient)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing disorder (1 patient) | rel=r_associated | relid=0 | w=32
  212. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:hearing loss (2 patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss (2 patients) | rel=r_associated | relid=0 | w=32
  213. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:hearing loss (reported in 2 patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss (reported in 2 patients) | rel=r_associated | relid=0 | w=32
  214. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:hearing loss, postlingual
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, postlingual | rel=r_associated | relid=0 | w=32
  215. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:hearing loss, prelingual, severe to profound (affecting all frequencies)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, prelingual, severe to profound (affecting all frequencies) | rel=r_associated | relid=0 | w=32
  216. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies) | rel=r_associated | relid=0 | w=32
  217. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:hearing loss, sensorineural (variable)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural (variable) | rel=r_associated | relid=0 | w=32
  218. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:hearing loss, sensorineural, moderate, postlingual
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural, moderate, postlingual | rel=r_associated | relid=0 | w=32
  219. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected) | rel=r_associated | relid=0 | w=32
  220. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:large auricle
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:large auricle | rel=r_associated | relid=0 | w=32
  221. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:lobule creases
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:lobule creases | rel=r_associated | relid=0 | w=32
  222. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:loss of vestibular reflexes
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:loss of vestibular reflexes | rel=r_associated | relid=0 | w=32
  223. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:low-set ears (3 patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:low-set ears (3 patients) | rel=r_associated | relid=0 | w=32
  224. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:low-set, malformed ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:low-set, malformed ears | rel=r_associated | relid=0 | w=32
  225. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:microtia (wws)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:microtia (wws) | rel=r_associated | relid=0 | w=32
  226. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:narrow ear lobes
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:narrow ear lobes | rel=r_associated | relid=0 | w=32
  227. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:narrow external ear canals (1 patient)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:narrow external ear canals (1 patient) | rel=r_associated | relid=0 | w=32
  228. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:nonprogressive
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:nonprogressive | rel=r_associated | relid=0 | w=32
  229. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:other auditory injuries
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:other auditory injuries | rel=r_associated | relid=0 | w=32
  230. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:overfolding of the superior helices
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:overfolding of the superior helices | rel=r_associated | relid=0 | w=32
  231. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:poorly formed ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:poorly formed ears | rel=r_associated | relid=0 | w=32
  232. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:posteriorly rotated ears (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:posteriorly rotated ears (in some patients) | rel=r_associated | relid=0 | w=32
  233. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:recurrent otitis media in infancy and childhood
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:recurrent otitis media in infancy and childhood | rel=r_associated | relid=0 | w=32
  234. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:recurrent serous otitis
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:recurrent serous otitis | rel=r_associated | relid=0 | w=32
  235. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:rudimentary tympanic membrane (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:rudimentary tympanic membrane (in some patients) | rel=r_associated | relid=0 | w=32
  236. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:sensorineural hearing loss, progressive bilateral postlingual
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural hearing loss, progressive bilateral postlingual | rel=r_associated | relid=0 | w=32
  237. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:short ears (in 1 family)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:short ears (in 1 family) | rel=r_associated | relid=0 | w=32
  238. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:soft auricles
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:soft auricles | rel=r_associated | relid=0 | w=32
  239. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:squared-off ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:squared-off ears | rel=r_associated | relid=0 | w=32
  240. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:squared-off superior helices
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:squared-off superior helices | rel=r_associated | relid=0 | w=32
  241. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:strabismus (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:strabismus (in some patients) | rel=r_associated | relid=0 | w=32
  242. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:structural inner ear abnormalities (in patients with larger deletions)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:structural inner ear abnormalities (in patients with larger deletions) | rel=r_associated | relid=0 | w=32
  243. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:supraauricular pit
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:supraauricular pit | rel=r_associated | relid=0 | w=32
  244. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:thick, firm earlobes
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:thick, firm earlobes | rel=r_associated | relid=0 | w=32
  245. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:tinnitus
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:tinnitus | rel=r_associated | relid=0 | w=32
  246. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 32 / 0.744 -> en:unconnected or fused stapes and incus
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:unconnected or fused stapes and incus | rel=r_associated | relid=0 | w=32
  247. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:abnormally folded ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormally folded ears | rel=r_associated | relid=0 | w=31
  248. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:absent distortion product otoacoustic emissions (oaes)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:absent distortion product otoacoustic emissions (oaes) | rel=r_associated | relid=0 | w=31
  249. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:absent earlobe
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:absent earlobe | rel=r_associated | relid=0 | w=31
  250. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:absent lobules
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:absent lobules | rel=r_associated | relid=0 | w=31
  251. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:air-bone gap of greater than 20 db across 0.5 to 2 khz
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:air-bone gap of greater than 20 db across 0.5 to 2 khz | rel=r_associated | relid=0 | w=31
  252. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:anteriorly displaced ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:anteriorly displaced ears | rel=r_associated | relid=0 | w=31
  253. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion | rel=r_associated | relid=0 | w=31
  254. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:conductive and sensorineural hearing loss
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:conductive and sensorineural hearing loss | rel=r_associated | relid=0 | w=31
  255. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:conductive hearing loss, bilateral
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:conductive hearing loss, bilateral | rel=r_associated | relid=0 | w=31
  256. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:congenital absence of external ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:congenital absence of external ear | rel=r_associated | relid=0 | w=31
  257. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:deafness (in 1 of 2 families)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness (in 1 of 2 families) | rel=r_associated | relid=0 | w=31
  258. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:deafness labyrinthine
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness labyrinthine | rel=r_associated | relid=0 | w=31
  259. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:deafness, bilateral sensorineural, high frequency (100% of patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, bilateral sensorineural, high frequency (100% of patients) | rel=r_associated | relid=0 | w=31
  260. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:deafness, conductive (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, conductive (in some patients) | rel=r_associated | relid=0 | w=31
  261. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:deafness, congenital nonprogressive sensorineural symmetric, moderate
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, congenital nonprogressive sensorineural symmetric, moderate | rel=r_associated | relid=0 | w=31
  262. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:deafness, early-onset
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, early-onset | rel=r_associated | relid=0 | w=31
  263. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:deafness, nonprogressive, moderate
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, nonprogressive, moderate | rel=r_associated | relid=0 | w=31
  264. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:deafness, profound, affects all frequencies
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, profound, affects all frequencies | rel=r_associated | relid=0 | w=31
  265. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:deafness, sensorineural, especially affecting high frequencies (in about 55% of males and 45% of females)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, sensorineural, especially affecting high frequencies (in about 55% of males and 45% of females) | rel=r_associated | relid=0 | w=31
  266. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:downsloping audiogram
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:downsloping audiogram | rel=r_associated | relid=0 | w=31
  267. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:ear dimple
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:ear dimple | rel=r_associated | relid=0 | w=31
  268. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:fear of ear disease
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:fear of ear disease | rel=r_associated | relid=0 | w=31
  269. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:fleshy ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:fleshy ears | rel=r_associated | relid=0 | w=31
  270. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:hearing impairment
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing impairment | rel=r_associated | relid=0 | w=31
  271. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:hearing impairment, mild (2 patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing impairment, mild (2 patients) | rel=r_associated | relid=0 | w=31
  272. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:hearing loss has been reported in some adults with severe disease
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss has been reported in some adults with severe disease | rel=r_associated | relid=0 | w=31
  273. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:hearing loss, congenital sensorineural, moderate-severe
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, congenital sensorineural, moderate-severe | rel=r_associated | relid=0 | w=31
  274. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:hearing loss, profound prelingual sensorineural
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, profound prelingual sensorineural | rel=r_associated | relid=0 | w=31
  275. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:hearing loss, sensorineural, bilateral, moderate-to-severe
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
  276. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:hearing loss, sensorineural, prelingual
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural, prelingual | rel=r_associated | relid=0 | w=31
  277. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:hearing loss, unilateral (rare)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, unilateral (rare) | rel=r_associated | relid=0 | w=31
  278. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:incomplete separation of the cochlea from the internal auditory canal
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:incomplete separation of the cochlea from the internal auditory canal | rel=r_associated | relid=0 | w=31
  279. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:large appearing ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:large appearing ears | rel=r_associated | relid=0 | w=31
  280. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:large dysplastic ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:large dysplastic ears | rel=r_associated | relid=0 | w=31
  281. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:large earlobe
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:large earlobe | rel=r_associated | relid=0 | w=31
  282. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:large, prominent ears (59%)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:large, prominent ears (59%) | rel=r_associated | relid=0 | w=31
  283. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:loss of outer hair cell function
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:loss of outer hair cell function | rel=r_associated | relid=0 | w=31
  284. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:low-set ears (in 2/4 patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:low-set ears (in 2/4 patients) | rel=r_associated | relid=0 | w=31
  285. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:low-set ears (in one family)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:low-set ears (in one family) | rel=r_associated | relid=0 | w=31
  286. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:middle ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:middle ear | rel=r_associated | relid=0 | w=31
  287. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:mondini defect
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:mondini defect | rel=r_associated | relid=0 | w=31
  288. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:neural hearing loss
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:neural hearing loss | rel=r_associated | relid=0 | w=31
  289. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:nonsyndromic sensorineural hearing loss
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:nonsyndromic sensorineural hearing loss | rel=r_associated | relid=0 | w=31
  290. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:ossified pinnae
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:ossified pinnae | rel=r_associated | relid=0 | w=31
  291. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:otitis media, recurrent (rare)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:otitis media, recurrent (rare) | rel=r_associated | relid=0 | w=31
  292. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:overfolded, rumpled ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:overfolded, rumpled ears | rel=r_associated | relid=0 | w=31
  293. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:pointed upper helix
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:pointed upper helix | rel=r_associated | relid=0 | w=31
  294. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:profound deafness
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:profound deafness | rel=r_associated | relid=0 | w=31
  295. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:progressive hearing impairment
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:progressive hearing impairment | rel=r_associated | relid=0 | w=31
  296. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:progressive mixed conductive and sensorineural hearing loss
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:progressive mixed conductive and sensorineural hearing loss | rel=r_associated | relid=0 | w=31
  297. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:prolonged brainstem auditory evoked potentials (baep)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:prolonged brainstem auditory evoked potentials (baep) | rel=r_associated | relid=0 | w=31
  298. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:prominent ears (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:prominent ears (in some patients) | rel=r_associated | relid=0 | w=31
  299. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:prominent ears (rare)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:prominent ears (rare) | rel=r_associated | relid=0 | w=31
  300. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:protruding ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:protruding ears | rel=r_associated | relid=0 | w=31
  301. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:rotated ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:rotated ears | rel=r_associated | relid=0 | w=31
  302. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:sensorineural deafness (reported in 1 family)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural deafness (reported in 1 family) | rel=r_associated | relid=0 | w=31
  303. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:sensorineural deafness, progressive, late-onset
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural deafness, progressive, late-onset | rel=r_associated | relid=0 | w=31
  304. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:sensorineural hearing impairment (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural hearing impairment (in some patients) | rel=r_associated | relid=0 | w=31
  305. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:severe loss in the higher frequencies by the fifth decade
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:severe loss in the higher frequencies by the fifth decade | rel=r_associated | relid=0 | w=31
  306. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:severe to profound deafness
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:severe to profound deafness | rel=r_associated | relid=0 | w=31
  307. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:small ears with large lobules
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:small ears with large lobules | rel=r_associated | relid=0 | w=31
  308. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:small triangular pinnae
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:small triangular pinnae | rel=r_associated | relid=0 | w=31
  309. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:small, simple ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:small, simple ears | rel=r_associated | relid=0 | w=31
  310. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:stapes fixation
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:stapes fixation | rel=r_associated | relid=0 | w=31
  311. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:stiff, prominent pinnae
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:stiff, prominent pinnae | rel=r_associated | relid=0 | w=31
  312. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:structure of superior auricularis muscle
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:structure of superior auricularis muscle | rel=r_associated | relid=0 | w=31
  313. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:superficial injury of ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:superficial injury of ear | rel=r_associated | relid=0 | w=31
  314. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:tinnitus (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:tinnitus (in some patients) | rel=r_associated | relid=0 | w=31
  315. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:triangular-shaped ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:triangular-shaped ears | rel=r_associated | relid=0 | w=31
  316. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:underdeveloped tragus
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:underdeveloped tragus | rel=r_associated | relid=0 | w=31
  317. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:upturned lobes
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:upturned lobes | rel=r_associated | relid=0 | w=31
  318. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 31 / 0.721 -> en:vestibular hypofunction
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:vestibular hypofunction | rel=r_associated | relid=0 | w=31
  319. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:abnormal semicircular canals
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormal semicircular canals | rel=r_associated | relid=0 | w=30
  320. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:absence of earlobe
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:absence of earlobe | rel=r_associated | relid=0 | w=30
  321. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:approximately 0.7db per year hearing loss at all frequencies
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:approximately 0.7db per year hearing loss at all frequencies | rel=r_associated | relid=0 | w=30
  322. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:atrophy of cochlear and vestibular fibrocytes
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:atrophy of cochlear and vestibular fibrocytes | rel=r_associated | relid=0 | w=30
  323. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:bleeding from ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:bleeding from ear | rel=r_associated | relid=0 | w=30
  324. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:chronic otitis
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:chronic otitis | rel=r_associated | relid=0 | w=30
  325. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:chronic otitis media
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:chronic otitis media | rel=r_associated | relid=0 | w=30
  326. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:chronic otitis other infection ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:chronic otitis other infection ear | rel=r_associated | relid=0 | w=30
  327. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:congenital atresia of external auditory canal
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:congenital atresia of external auditory canal | rel=r_associated | relid=0 | w=30
  328. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:congenital secretory diarrhea, sodium type (disorder)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:congenital secretory diarrhea, sodium type (disorder) | rel=r_associated | relid=0 | w=30
  329. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:deafness affects all frequencies
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness affects all frequencies | rel=r_associated | relid=0 | w=30
  330. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:deafness, moderate-severe (onset in third decade)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, moderate-severe (onset in third decade) | rel=r_associated | relid=0 | w=30
  331. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:deafness, postlingual
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, postlingual | rel=r_associated | relid=0 | w=30
  332. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:deafness, sensorineural, severe to profound affecting all frequencies
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, sensorineural, severe to profound affecting all frequencies | rel=r_associated | relid=0 | w=30
  333. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:deafness, sensorineural, variable
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, sensorineural, variable | rel=r_associated | relid=0 | w=30
  334. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:ear | rel=r_associated | relid=0 | w=30
  335. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:ear pain/earache
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:ear pain/earache | rel=r_associated | relid=0 | w=30
  336. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:ear pits, posterior helical
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:ear pits, posterior helical | rel=r_associated | relid=0 | w=30
  337. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:endolymphatic sac tumors (elsts)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:endolymphatic sac tumors (elsts) | rel=r_associated | relid=0 | w=30
  338. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:hearing impairment (in 1/4 patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing impairment (in 1/4 patients) | rel=r_associated | relid=0 | w=30
  339. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:hearing loss (95% of patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss (95% of patients) | rel=r_associated | relid=0 | w=30
  340. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:hearing loss (conductive and/or sensorineural)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss (conductive and/or sensorineural) | rel=r_associated | relid=0 | w=30
  341. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:hearing loss, mixed, mild to severe (in heterozygotes)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, mixed, mild to severe (in heterozygotes) | rel=r_associated | relid=0 | w=30
  342. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:hearing loss, progressive, starting in infancy
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, progressive, starting in infancy | rel=r_associated | relid=0 | w=30
  343. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:hearing loss, sensorineural (in 2 patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural (in 2 patients) | rel=r_associated | relid=0 | w=30
  344. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:hearing loss, sensorineural (in some)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural (in some) | rel=r_associated | relid=0 | w=30
  345. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=30
  346. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:hearing loss, sensorineural, progressive (childhood-onset)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural, progressive (childhood-onset) | rel=r_associated | relid=0 | w=30
  347. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:hearing loss, severe to profound, affecting all frequencies
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, severe to profound, affecting all frequencies | rel=r_associated | relid=0 | w=30
  348. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:hypermobile
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hypermobile | rel=r_associated | relid=0 | w=30
  349. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:incomplete atretic plate
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:incomplete atretic plate | rel=r_associated | relid=0 | w=30
  350. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:increased posterior angulation
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:increased posterior angulation | rel=r_associated | relid=0 | w=30
  351. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:large ears (37%)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:large ears (37%) | rel=r_associated | relid=0 | w=30
  352. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:large fleshy earlobes
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:large fleshy earlobes | rel=r_associated | relid=0 | w=30
  353. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:loss of hearing (45%)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:loss of hearing (45%) | rel=r_associated | relid=0 | w=30
  354. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:low-set ears (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:low-set ears (in some patients) | rel=r_associated | relid=0 | w=30
  355. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:low-set ears (severe form)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:low-set ears (severe form) | rel=r_associated | relid=0 | w=30
  356. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:meniere disease
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:meniere disease | rel=r_associated | relid=0 | w=30
  357. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:microtia (30-60% of patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:microtia (30-60% of patients) | rel=r_associated | relid=0 | w=30
  358. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:microtia hearing loss, conductive
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:microtia hearing loss, conductive | rel=r_associated | relid=0 | w=30
  359. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:mixed hearing loss (50% of patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:mixed hearing loss (50% of patients) | rel=r_associated | relid=0 | w=30
  360. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:neonatal cystic lesions of the pinnae
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:neonatal cystic lesions of the pinnae | rel=r_associated | relid=0 | w=30
  361. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:normal middle ear pressures on tympanometry
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:normal middle ear pressures on tympanometry | rel=r_associated | relid=0 | w=30
  362. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:normal vestibular response
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:normal vestibular response | rel=r_associated | relid=0 | w=30
  363. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:poorly formed pinnae
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:poorly formed pinnae | rel=r_associated | relid=0 | w=30
  364. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:posteriorly rotated ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:posteriorly rotated ear | rel=r_associated | relid=0 | w=30
  365. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:presbycusis
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:presbycusis | rel=r_associated | relid=0 | w=30
  366. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:profound sensorineural hearing loss
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:profound sensorineural hearing loss | rel=r_associated | relid=0 | w=30
  367. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:prominent antitragus
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:prominent antitragus | rel=r_associated | relid=0 | w=30
  368. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:prominent lobules
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:prominent lobules | rel=r_associated | relid=0 | w=30
  369. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:protuberant ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:protuberant ear | rel=r_associated | relid=0 | w=30
  370. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:recurrent otitis
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:recurrent otitis | rel=r_associated | relid=0 | w=30
  371. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:relatively long ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:relatively long ears | rel=r_associated | relid=0 | w=30
  372. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:retinitis (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:retinitis (in some patients) | rel=r_associated | relid=0 | w=30
  373. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:rudimentary
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:rudimentary | rel=r_associated | relid=0 | w=30
  374. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:sensation of blocked ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensation of blocked ears | rel=r_associated | relid=0 | w=30
  375. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:sensorineural deafness (onset in the second decade in 25 to 30% of patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural deafness (onset in the second decade in 25 to 30% of patients) | rel=r_associated | relid=0 | w=30
  376. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:sensorineural hearing loss (20% of patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural hearing loss (20% of patients) | rel=r_associated | relid=0 | w=30
  377. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:sensorineural hearing loss (rare)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural hearing loss (rare) | rel=r_associated | relid=0 | w=30
  378. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:sensorineural hearing loss, mild (rare)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural hearing loss, mild (rare) | rel=r_associated | relid=0 | w=30
  379. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:sensorineural hearing loss, mild to moderate
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural hearing loss, mild to moderate | rel=r_associated | relid=0 | w=30
  380. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:severe to profound hearing impairment by early adulthood
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:severe to profound hearing impairment by early adulthood | rel=r_associated | relid=0 | w=30
  381. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:small, posteriorly rotated ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:small, posteriorly rotated ears | rel=r_associated | relid=0 | w=30
  382. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:superior semicircular canal dehiscence syndrome
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:superior semicircular canal dehiscence syndrome | rel=r_associated | relid=0 | w=30
  383. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:symmetric deterioration of hearing loss and speech reception with age
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:symmetric deterioration of hearing loss and speech reception with age | rel=r_associated | relid=0 | w=30
  384. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:thick ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:thick ears | rel=r_associated | relid=0 | w=30
  385. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:thickened lobes
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:thickened lobes | rel=r_associated | relid=0 | w=30
  386. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:transient evoked otoacoustic emissions cannot be detected
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:transient evoked otoacoustic emissions cannot be detected | rel=r_associated | relid=0 | w=30
  387. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:unilateral external ear deformity
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:unilateral external ear deformity | rel=r_associated | relid=0 | w=30
  388. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> en:wide bulbous internal auditory meatus
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:wide bulbous internal auditory meatus | rel=r_associated | relid=0 | w=30
  389. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> lésion traumatique superficielle de l'oreille
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=lésion traumatique superficielle de l'oreille | rel=r_associated | relid=0 | w=30
  390. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 30 / 0.698 -> perte d'audition sensorineurale
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=perte d'audition sensorineurale | rel=r_associated | relid=0 | w=30
  391. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:abnormal auditory brainstem responses
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormal auditory brainstem responses | rel=r_associated | relid=0 | w=29
  392. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:abnormal brain auditory evoked responses (baer)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormal brain auditory evoked responses (baer) | rel=r_associated | relid=0 | w=29
  393. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:abnormal middle ear ossicles
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormal middle ear ossicles | rel=r_associated | relid=0 | w=29
  394. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:abnormality of the middle ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormality of the middle ear | rel=r_associated | relid=0 | w=29
  395. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:absent external auditory meatus
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:absent external auditory meatus | rel=r_associated | relid=0 | w=29
  396. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:absent or abnormal otoacoustic emissions
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:absent or abnormal otoacoustic emissions | rel=r_associated | relid=0 | w=29
  397. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:anomalous middle ear bones
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:anomalous middle ear bones | rel=r_associated | relid=0 | w=29
  398. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:anteverted ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:anteverted ears | rel=r_associated | relid=0 | w=29
  399. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:aural atresia, congenital
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:aural atresia, congenital | rel=r_associated | relid=0 | w=29
  400. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:bat ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:bat ear | rel=r_associated | relid=0 | w=29
  401. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:complete bony atresia of medial portion of external auditory canal (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:complete bony atresia of medial portion of external auditory canal (in some patients) | rel=r_associated | relid=0 | w=29
  402. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:congenital deafness
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:congenital deafness | rel=r_associated | relid=0 | w=29
  403. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:congenital hearing loss (1 family)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:congenital hearing loss (1 family) | rel=r_associated | relid=0 | w=29
  404. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:deafness (often in third decade)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness (often in third decade) | rel=r_associated | relid=0 | w=29
  405. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:deafness, congenital sensorineural, profound (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, congenital sensorineural, profound (in some patients) | rel=r_associated | relid=0 | w=29
  406. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:deafness, sensorineural, prelingual, profound
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, sensorineural, prelingual, profound | rel=r_associated | relid=0 | w=29
  407. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:decreased otoacoustic emission amplitude
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:decreased otoacoustic emission amplitude | rel=r_associated | relid=0 | w=29
  408. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:downward sloping audiogram
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:downward sloping audiogram | rel=r_associated | relid=0 | w=29
  409. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:ear part
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:ear part | rel=r_associated | relid=0 | w=29
  410. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:enlarged vestibular aqueduct
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:enlarged vestibular aqueduct | rel=r_associated | relid=0 | w=29
  411. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:everted ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
  412. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:folded superior edge of helix
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:folded superior edge of helix | rel=r_associated | relid=0 | w=29
  413. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:hearing loss begins with loss of high frequencies
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss begins with loss of high frequencies | rel=r_associated | relid=0 | w=29
  414. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:hearing loss, congenital profound
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, congenital profound | rel=r_associated | relid=0 | w=29
  415. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:hearing loss, postlingual progressive sensorineural
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, postlingual progressive sensorineural | rel=r_associated | relid=0 | w=29
  416. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:hearing loss, prelingual sensorineural, moderate to severe
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, prelingual sensorineural, moderate to severe | rel=r_associated | relid=0 | w=29
  417. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:hearing loss, progressive sensorineural, affecting high frequencies
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, progressive sensorineural, affecting high frequencies | rel=r_associated | relid=0 | w=29
  418. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:hearing loss, sensorineural (in 1 ashkenazi patient)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural (in 1 ashkenazi patient) | rel=r_associated | relid=0 | w=29
  419. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:hearing loss, sensorineural (type ii)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural (type ii) | rel=r_associated | relid=0 | w=29
  420. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:hearing loss, sensorineural, associated with elsts
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural, associated with elsts | rel=r_associated | relid=0 | w=29
  421. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural | rel=r_associated | relid=0 | w=29
  422. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:hearing threshold at or above 90 db at all frequencies tested (0.25-8.0 khz)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing threshold at or above 90 db at all frequencies tested (0.25-8.0 khz) | rel=r_associated | relid=0 | w=29
  423. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:hypertrophic auricular cartilage
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hypertrophic auricular cartilage | rel=r_associated | relid=0 | w=29
  424. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:hypoplasia of the cochlea
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hypoplasia of the cochlea | rel=r_associated | relid=0 | w=29
  425. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies | rel=r_associated | relid=0 | w=29
  426. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:large anteverted ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:large anteverted ears | rel=r_associated | relid=0 | w=29
  427. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:large protruding ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:large protruding ears | rel=r_associated | relid=0 | w=29
  428. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:large, low-set ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:large, low-set ears | rel=r_associated | relid=0 | w=29
  429. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:left ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:left ear | rel=r_associated | relid=0 | w=29
  430. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:low-frequency conductive hearing loss
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:low-frequency conductive hearing loss | rel=r_associated | relid=0 | w=29
  431. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:low-set and rotated ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:low-set and rotated ears | rel=r_associated | relid=0 | w=29
  432. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:microtia, type i
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:microtia, type i | rel=r_associated | relid=0 | w=29
  433. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:minor ear anomalies (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:minor ear anomalies (in some patients) | rel=r_associated | relid=0 | w=29
  434. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:mixed hearing loss
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:mixed hearing loss | rel=r_associated | relid=0 | w=29
  435. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:morphological abnormality of the middle ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:morphological abnormality of the middle ear | rel=r_associated | relid=0 | w=29
  436. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:narrowing of ear canal
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:narrowing of ear canal | rel=r_associated | relid=0 | w=29
  437. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:near-stenosis of bony portion of auditory canal (in homozygotes)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:near-stenosis of bony portion of auditory canal (in homozygotes) | rel=r_associated | relid=0 | w=29
  438. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:no hearing impairment
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:no hearing impairment | rel=r_associated | relid=0 | w=29
  439. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:normal otoacoustic emissions
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:normal otoacoustic emissions | rel=r_associated | relid=0 | w=29
  440. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:normal outer hair cell functions
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:normal outer hair cell functions | rel=r_associated | relid=0 | w=29
  441. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:oae responses may decrease with age or use of hearing aids
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:oae responses may decrease with age or use of hearing aids | rel=r_associated | relid=0 | w=29
  442. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:occasional conductive hearing loss
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:occasional conductive hearing loss | rel=r_associated | relid=0 | w=29
  443. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:otitis externa, recurrent, due to infection with staphylococcus aureus
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:otitis externa, recurrent, due to infection with staphylococcus aureus | rel=r_associated | relid=0 | w=29
  444. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:pinna modeling anomalies
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:pinna modeling anomalies | rel=r_associated | relid=0 | w=29
  445. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:posteriorly rotated ears (female)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:posteriorly rotated ears (female) | rel=r_associated | relid=0 | w=29
  446. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:preauricular dimple
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:preauricular dimple | rel=r_associated | relid=0 | w=29
  447. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:preauricular skin tag
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:preauricular skin tag | rel=r_associated | relid=0 | w=29
  448. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:progressive conductive hearing impairment
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:progressive conductive hearing impairment | rel=r_associated | relid=0 | w=29
  449. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:progressive hearing loss (in some)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:progressive hearing loss (in some) | rel=r_associated | relid=0 | w=29
  450. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:sensorineural deafness (rare)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural deafness (rare) | rel=r_associated | relid=0 | w=29
  451. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:sensorineural hearing impairment (less common)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural hearing impairment (less common) | rel=r_associated | relid=0 | w=29
  452. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:sensorineural hearing loss (1 family)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural hearing loss (1 family) | rel=r_associated | relid=0 | w=29
  453. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:sensorineural hearing loss (less common)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural hearing loss (less common) | rel=r_associated | relid=0 | w=29
  454. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:severe narrowing of cartilagenous auditory canal
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:severe narrowing of cartilagenous auditory canal | rel=r_associated | relid=0 | w=29
  455. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:small auricles
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:small auricles | rel=r_associated | relid=0 | w=29
  456. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:small lobes
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:small lobes | rel=r_associated | relid=0 | w=29
  457. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:small pits anterior to the helix (1 patient)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:small pits anterior to the helix (1 patient) | rel=r_associated | relid=0 | w=29
  458. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:tinnitus (rare)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:tinnitus (rare) | rel=r_associated | relid=0 | w=29
  459. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:underfolded helix
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:underfolded helix | rel=r_associated | relid=0 | w=29
  460. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:uplifted earlobes
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:uplifted earlobes | rel=r_associated | relid=0 | w=29
  461. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:vertigo, episodic
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:vertigo, episodic | rel=r_associated | relid=0 | w=29
  462. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:vestibular areflexia, complete
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:vestibular areflexia, complete | rel=r_associated | relid=0 | w=29
  463. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:vestibular dysfunction
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:vestibular dysfunction | rel=r_associated | relid=0 | w=29
  464. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 29 / 0.674 -> en:vestibular hyporeflexia
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:vestibular hyporeflexia | rel=r_associated | relid=0 | w=29
  465. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:a subset of patients have hearing loss
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:a subset of patients have hearing loss | rel=r_associated | relid=0 | w=28
  466. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:abnormal ear configuration
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormal ear configuration | rel=r_associated | relid=0 | w=28
  467. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:abnormal speech discrimination
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormal speech discrimination | rel=r_associated | relid=0 | w=28
  468. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:abnormality of the helix
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormality of the helix | rel=r_associated | relid=0 | w=28
  469. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:absence of the helix and distal scapha in middle third of the ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:absence of the helix and distal scapha in middle third of the ear | rel=r_associated | relid=0 | w=28
  470. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:absent brainstem auditory-evoked responses
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:absent brainstem auditory-evoked responses | rel=r_associated | relid=0 | w=28
  471. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:absent stapedial reflexes or intraoperative stapes immobility
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:absent stapedial reflexes or intraoperative stapes immobility | rel=r_associated | relid=0 | w=28
  472. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:accessory tragus
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:accessory tragus | rel=r_associated | relid=0 | w=28
  473. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:angular ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:angular ears | rel=r_associated | relid=0 | w=28
  474. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:anteriorly rotated ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:anteriorly rotated ears | rel=r_associated | relid=0 | w=28
  475. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:auricular clefts
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:auricular clefts | rel=r_associated | relid=0 | w=28
  476. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:conductive hearing loss (in a subset of patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:conductive hearing loss (in a subset of patients) | rel=r_associated | relid=0 | w=28
  477. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss) | rel=r_associated | relid=0 | w=28
  478. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:congenital small ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:congenital small ears | rel=r_associated | relid=0 | w=28
  479. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:cup-shaped ears (30-60% of patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:cup-shaped ears (30-60% of patients) | rel=r_associated | relid=0 | w=28
  480. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:deafness, sensorineural (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, sensorineural (in some patients) | rel=r_associated | relid=0 | w=28
  481. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:deafness, unilateral, childhood onset
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, unilateral, childhood onset | rel=r_associated | relid=0 | w=28
  482. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:endolymphatic hydrops, delayed onset
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:endolymphatic hydrops, delayed onset | rel=r_associated | relid=0 | w=28
  483. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:external ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:external ear | rel=r_associated | relid=0 | w=28
  484. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:first branchial arch anomalies
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:first branchial arch anomalies | rel=r_associated | relid=0 | w=28
  485. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:foreign body in auditory canal
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:foreign body in auditory canal | rel=r_associated | relid=0 | w=28
  486. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:hearing impairment, asymmetric (in some patients with hsan2d)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing impairment, asymmetric (in some patients with hsan2d) | rel=r_associated | relid=0 | w=28
  487. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:hearing loss (cvs+)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss (cvs+) | rel=r_associated | relid=0 | w=28
  488. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:hearing loss (variable)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss (variable) | rel=r_associated | relid=0 | w=28
  489. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:hearing loss, sensorineural, mid-frequency (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural, mid-frequency (in some patients) | rel=r_associated | relid=0 | w=28
  490. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:hyperfolded ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hyperfolded ears | rel=r_associated | relid=0 | w=28
  491. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients) | rel=r_associated | relid=0 | w=28
  492. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:keratotic plaque around ear meatus
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:keratotic plaque around ear meatus | rel=r_associated | relid=0 | w=28
  493. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:large ear pinnae
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:large ear pinnae | rel=r_associated | relid=0 | w=28
  494. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:large, low-set ears (uncommon)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:large, low-set ears (uncommon) | rel=r_associated | relid=0 | w=28
  495. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:lobular aplasia
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:lobular aplasia | rel=r_associated | relid=0 | w=28
  496. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:loss of high frequencies at onset
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:loss of high frequencies at onset | rel=r_associated | relid=0 | w=28
  497. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:low-set ears (rare)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:low-set ears (rare) | rel=r_associated | relid=0 | w=28
  498. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:mild cochlear hearing loss (1 patient)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:mild cochlear hearing loss (1 patient) | rel=r_associated | relid=0 | w=28
  499. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:mondini malformation
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:mondini malformation | rel=r_associated | relid=0 | w=28
  500. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:narrow auditory canals (rare)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:narrow auditory canals (rare) | rel=r_associated | relid=0 | w=28
  501. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:near-stenosis of bony portion of auditory canal
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:near-stenosis of bony portion of auditory canal | rel=r_associated | relid=0 | w=28
  502. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:no vestibular dysfunction
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:no vestibular dysfunction | rel=r_associated | relid=0 | w=28
  503. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:normal otoacoustic emissions (oae), indicating intact outer ear hair cell function
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:normal otoacoustic emissions (oae), indicating intact outer ear hair cell function | rel=r_associated | relid=0 | w=28
  504. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:normal vestibular function
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:normal vestibular function | rel=r_associated | relid=0 | w=28
  505. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:otoneurologic disturbances
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
  506. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:otosclerosis
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:otosclerosis | rel=r_associated | relid=0 | w=28
  507. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:overfolded helix
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:overfolded helix | rel=r_associated | relid=0 | w=28
  508. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:preauricular sinus
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:preauricular sinus | rel=r_associated | relid=0 | w=28
  509. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:prominent crura
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:prominent crura | rel=r_associated | relid=0 | w=28
  510. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:protruding lobules
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:protruding lobules | rel=r_associated | relid=0 | w=28
  511. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:protruding, simple ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:protruding, simple ears | rel=r_associated | relid=0 | w=28
  512. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:recurrent otitis media in infancy
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:recurrent otitis media in infancy | rel=r_associated | relid=0 | w=28
  513. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:sclerosis of semicircular canals
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sclerosis of semicircular canals | rel=r_associated | relid=0 | w=28
  514. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:sensorineural hearing loss (1 patient)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural hearing loss (1 patient) | rel=r_associated | relid=0 | w=28
  515. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:sensorineural hearing loss (onset early childhood)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural hearing loss (onset early childhood) | rel=r_associated | relid=0 | w=28
  516. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:sensorineural hearing loss, bilateral
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural hearing loss, bilateral | rel=r_associated | relid=0 | w=28
  517. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:severe narrowing of cartilagenous auditory canal (in homozygotes)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:severe narrowing of cartilagenous auditory canal (in homozygotes) | rel=r_associated | relid=0 | w=28
  518. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:simple ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:simple ear | rel=r_associated | relid=0 | w=28
  519. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:small earlobe
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:small earlobe | rel=r_associated | relid=0 | w=28
  520. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:stenotic ear canals (30%)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:stenotic ear canals (30%) | rel=r_associated | relid=0 | w=28
  521. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:unravelling of superior helices
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:unravelling of superior helices | rel=r_associated | relid=0 | w=28
  522. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:vestibular anomalies (less common)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:vestibular anomalies (less common) | rel=r_associated | relid=0 | w=28
  523. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:vestibular areflexia
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:vestibular areflexia | rel=r_associated | relid=0 | w=28
  524. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:vestibular function defect (decreased in some, normal in other patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:vestibular function defect (decreased in some, normal in other patients) | rel=r_associated | relid=0 | w=28
  525. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> en:wide, flattened earlobes
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:wide, flattened earlobes | rel=r_associated | relid=0 | w=28
  526. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 28 / 0.651 -> surdité congénitale
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=surdité congénitale | rel=r_associated | relid=0 | w=28
  527. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:abnormal brainstem auditory evoked potentials (baep)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormal brainstem auditory evoked potentials (baep) | rel=r_associated | relid=0 | w=27
  528. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:abnormal communication between the subarachnoid space in the meatus and the perilymph
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormal communication between the subarachnoid space in the meatus and the perilymph | rel=r_associated | relid=0 | w=27
  529. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:abnormal ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormal ears | rel=r_associated | relid=0 | w=27
  530. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:abnormal folded pinna
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormal folded pinna | rel=r_associated | relid=0 | w=27
  531. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:abnormal helices, antihelices and lobules
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormal helices, antihelices and lobules | rel=r_associated | relid=0 | w=27
  532. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:abnormal middle ear reflexes
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormal middle ear reflexes | rel=r_associated | relid=0 | w=27
  533. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:abnormally shaped ears (in one family)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormally shaped ears (in one family) | rel=r_associated | relid=0 | w=27
  534. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:absence of the cochlear nerves (reported in 1 patient)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:absence of the cochlear nerves (reported in 1 patient) | rel=r_associated | relid=0 | w=27
  535. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:absent cochlear microphonic (in older patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:absent cochlear microphonic (in older patients) | rel=r_associated | relid=0 | w=27
  536. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:acoustic trauma
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:acoustic trauma | rel=r_associated | relid=0 | w=27
  537. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:acute otitis media/myringitis
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:acute otitis media/myringitis | rel=r_associated | relid=0 | w=27
  538. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:asymmetric dysplastic ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:asymmetric dysplastic ears | rel=r_associated | relid=0 | w=27
  539. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient) | rel=r_associated | relid=0 | w=27
  540. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:auditory neuropathy spectrum disorder
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:auditory neuropathy spectrum disorder | rel=r_associated | relid=0 | w=27
  541. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:bilateral conductive hearing loss (rare)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:bilateral conductive hearing loss (rare) | rel=r_associated | relid=0 | w=27
  542. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:bilateral hypoplastic cochlea
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=27
  543. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:cauliflower ear deformity (rare)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:cauliflower ear deformity (rare) | rel=r_associated | relid=0 | w=27
  544. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:cochlear degeneration
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:cochlear degeneration | rel=r_associated | relid=0 | w=27
  545. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:cochleosaccular dysplasia
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:cochleosaccular dysplasia | rel=r_associated | relid=0 | w=27
  546. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:conductive hearing loss
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:conductive hearing loss | rel=r_associated | relid=0 | w=27
  547. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:deafness, early-onset mixed conductive and sensorineural
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, early-onset mixed conductive and sensorineural | rel=r_associated | relid=0 | w=27
  548. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:deafness, sensorineural, profound (prelingual onset)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, sensorineural, profound (prelingual onset) | rel=r_associated | relid=0 | w=27
  549. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation | rel=r_associated | relid=0 | w=27
  550. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:deficient auricle
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deficient auricle | rel=r_associated | relid=0 | w=27
  551. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:dizziness
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:dizziness | rel=r_associated | relid=0 | w=27
  552. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:dysplastic ears (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:dysplastic ears (in some patients) | rel=r_associated | relid=0 | w=27
  553. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:excessive cerumen
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:excessive cerumen | rel=r_associated | relid=0 | w=27
  554. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:flattened antihelix
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:flattened antihelix | rel=r_associated | relid=0 | w=27
  555. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:hearing deficits (28% of adults)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing deficits (28% of adults) | rel=r_associated | relid=0 | w=27
  556. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:hearing loss (uncommon)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss (uncommon) | rel=r_associated | relid=0 | w=27
  557. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:hearing loss affects all frequencies
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss affects all frequencies | rel=r_associated | relid=0 | w=27
  558. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:hearing loss, bilateral
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, bilateral | rel=r_associated | relid=0 | w=27
  559. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:hearing loss, bilateral progressive post-lingual
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, bilateral progressive post-lingual | rel=r_associated | relid=0 | w=27
  560. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:hearing loss, conductive (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, conductive (in some patients) | rel=r_associated | relid=0 | w=27
  561. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:hearing loss, conductive or mixed
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, conductive or mixed | rel=r_associated | relid=0 | w=27
  562. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:hearing loss, congenital, profound (250-8,000 hz)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, congenital, profound (250-8,000 hz) | rel=r_associated | relid=0 | w=27
  563. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:hearing loss, high frequency, slowly progressive (onset in early childhood)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, high frequency, slowly progressive (onset in early childhood) | rel=r_associated | relid=0 | w=27
  564. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:hearing loss, sensorineural (bilateral, prelingual)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural (bilateral, prelingual) | rel=r_associated | relid=0 | w=27
  565. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:hearing loss, sensorineural (high frequency)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural (high frequency) | rel=r_associated | relid=0 | w=27
  566. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:hearing loss, sensorineural (in one family)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural (in one family) | rel=r_associated | relid=0 | w=27
  567. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:hearing loss, sensorineural (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural (in some patients) | rel=r_associated | relid=0 | w=27
  568. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:hearing loss, sensorineural (reported in 1 patient)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural (reported in 1 patient) | rel=r_associated | relid=0 | w=27
  569. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:hearing loss, sensorineural and conductive, severe to profound
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural and conductive, severe to profound | rel=r_associated | relid=0 | w=27
  570. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:hearing loss, unilateral, mild
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, unilateral, mild | rel=r_associated | relid=0 | w=27
  571. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:hypercompliant tympanic membranes
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hypercompliant tympanic membranes | rel=r_associated | relid=0 | w=27
  572. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:hypoplasia of the upper part of the helix
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hypoplasia of the upper part of the helix | rel=r_associated | relid=0 | w=27
  573. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:hypoplastic semicircular canals
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hypoplastic semicircular canals | rel=r_associated | relid=0 | w=27
  574. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:hypoplastic superior helix
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hypoplastic superior helix | rel=r_associated | relid=0 | w=27
  575. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:large prominent ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:large prominent ears | rel=r_associated | relid=0 | w=27
  576. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:large simple ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:large simple ears | rel=r_associated | relid=0 | w=27
  577. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:limited auditory function
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:limited auditory function | rel=r_associated | relid=0 | w=27
  578. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:long and prominent ear crus
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:long and prominent ear crus | rel=r_associated | relid=0 | w=27
  579. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:long ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:long ear | rel=r_associated | relid=0 | w=27
  580. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:long, lobulated ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:long, lobulated ears | rel=r_associated | relid=0 | w=27
  581. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:malformed auricle (1 patient)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:malformed auricle (1 patient) | rel=r_associated | relid=0 | w=27
  582. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:minor auricular anomalies
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:minor auricular anomalies | rel=r_associated | relid=0 | w=27
  583. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:narrowed external ear canal
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:narrowed external ear canal | rel=r_associated | relid=0 | w=27
  584. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:no auditory brainstem response to 100-db stimulus
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:no auditory brainstem response to 100-db stimulus | rel=r_associated | relid=0 | w=27
  585. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:no hearing loss
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:no hearing loss | rel=r_associated | relid=0 | w=27
  586. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:no vestibular impairment
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:no vestibular impairment | rel=r_associated | relid=0 | w=27
  587. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:nonprogressive deafness
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:nonprogressive deafness | rel=r_associated | relid=0 | w=27
  588. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:normal static compliance on tympanometry
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:normal static compliance on tympanometry | rel=r_associated | relid=0 | w=27
  589. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:organ of corti degeneration
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:organ of corti degeneration | rel=r_associated | relid=0 | w=27
  590. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:other diseases of ear/mastoid
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:other diseases of ear/mastoid | rel=r_associated | relid=0 | w=27
  591. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:otitis media
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:otitis media | rel=r_associated | relid=0 | w=27
  592. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:otitis media, chronic (rare)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:otitis media, chronic (rare) | rel=r_associated | relid=0 | w=27
  593. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:otorrhea
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:otorrhea | rel=r_associated | relid=0 | w=27
  594. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:outer ear abnormalities (deletion patients) prominent ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:outer ear abnormalities (deletion patients) prominent ears | rel=r_associated | relid=0 | w=27
  595. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:partial hearing loss
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:partial hearing loss | rel=r_associated | relid=0 | w=27
  596. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:phonophobia
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:phonophobia | rel=r_associated | relid=0 | w=27
  597. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:pigmentation of the ear cartilage
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:pigmentation of the ear cartilage | rel=r_associated | relid=0 | w=27
  598. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:poorly shaped ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:poorly shaped ears | rel=r_associated | relid=0 | w=27
  599. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:posterior helical indentations
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:posterior helical indentations | rel=r_associated | relid=0 | w=27
  600. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:preauricular skin tags (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:preauricular skin tags (in some patients) | rel=r_associated | relid=0 | w=27
  601. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:progressive, low frequency sensorineural hearing loss
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:progressive, low frequency sensorineural hearing loss | rel=r_associated | relid=0 | w=27
  602. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:prominent antihelix
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:prominent antihelix | rel=r_associated | relid=0 | w=27
  603. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:prominent earlobes (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:prominent earlobes (in some patients) | rel=r_associated | relid=0 | w=27
  604. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:protruding ears (rare)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:protruding ears (rare) | rel=r_associated | relid=0 | w=27
  605. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:pseudomembranous inflammation of the middle ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:pseudomembranous inflammation of the middle ear | rel=r_associated | relid=0 | w=27
  606. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:satyr ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:satyr ear | rel=r_associated | relid=0 | w=27
  607. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:sensorineural hearing loss (3 patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural hearing loss (3 patients) | rel=r_associated | relid=0 | w=27
  608. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:sensorineural hearing loss (early-onset form)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural hearing loss (early-onset form) | rel=r_associated | relid=0 | w=27
  609. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:sensorineural hearing loss (males only)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural hearing loss (males only) | rel=r_associated | relid=0 | w=27
  610. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:sensorineural, conductive, or mixed hearing loss
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural, conductive, or mixed hearing loss | rel=r_associated | relid=0 | w=27
  611. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:slit-like opening of the exterior auditory meatus
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:slit-like opening of the exterior auditory meatus | rel=r_associated | relid=0 | w=27
  612. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:small pinna
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:small pinna | rel=r_associated | relid=0 | w=27
  613. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:small/rudimentary tragus, antitragus and lobule
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:small/rudimentary tragus, antitragus and lobule | rel=r_associated | relid=0 | w=27
  614. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:stapes ankylosis
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:stapes ankylosis | rel=r_associated | relid=0 | w=27
  615. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:superiorly displaced ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:superiorly displaced ears | rel=r_associated | relid=0 | w=27
  616. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:thickened helices
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:thickened helices | rel=r_associated | relid=0 | w=27
  617. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:u-shaped audiogram
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:u-shaped audiogram | rel=r_associated | relid=0 | w=27
  618. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:unfolded superior helices
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:unfolded superior helices | rel=r_associated | relid=0 | w=27
  619. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:upsloping audiograms
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:upsloping audiograms | rel=r_associated | relid=0 | w=27
  620. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:vertigo
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:vertigo | rel=r_associated | relid=0 | w=27
  621. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:vestibular dysfunction (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:vestibular dysfunction (in some patients) | rel=r_associated | relid=0 | w=27
  622. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 27 / 0.628 -> en:vestibulopathy, bilateral, progressive
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:vestibulopathy, bilateral, progressive | rel=r_associated | relid=0 | w=27
  623. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:'tilted' ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:'tilted' ears | rel=r_associated | relid=0 | w=26
  624. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:abnormality of the outer ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormality of the outer ear | rel=r_associated | relid=0 | w=26
  625. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:abnormally formed ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:abnormally formed ears | rel=r_associated | relid=0 | w=26
  626. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:absent auditory canals (wws)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:absent auditory canals (wws) | rel=r_associated | relid=0 | w=26
  627. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:absent helices, bilaterally
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:absent helices, bilaterally | rel=r_associated | relid=0 | w=26
  628. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:absent stapedial reflex
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:absent stapedial reflex | rel=r_associated | relid=0 | w=26
  629. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:affects mid- to high-frequencies
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:affects mid- to high-frequencies | rel=r_associated | relid=0 | w=26
  630. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:audiogram may be ascending
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:audiogram may be ascending | rel=r_associated | relid=0 | w=26
  631. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:bilateral sensorineural hearing loss (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:bilateral sensorineural hearing loss (in some patients) | rel=r_associated | relid=0 | w=26
  632. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:cleft lobules
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:cleft lobules | rel=r_associated | relid=0 | w=26
  633. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:concern with appearance of ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:concern with appearance of ears | rel=r_associated | relid=0 | w=26
  634. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:conductive hearing loss, mild bilateral (rare)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:conductive hearing loss, mild bilateral (rare) | rel=r_associated | relid=0 | w=26
  635. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:crumpled ear (76%)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:crumpled ear (76%) | rel=r_associated | relid=0 | w=26
  636. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years | rel=r_associated | relid=0 | w=26
  637. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:deafness, sensorineural (severe to profound)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, sensorineural (severe to profound) | rel=r_associated | relid=0 | w=26
  638. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:deafness, sensorineural, profound
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deafness, sensorineural, profound | rel=r_associated | relid=0 | w=26
  639. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v | rel=r_associated | relid=0 | w=26
  640. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea | rel=r_associated | relid=0 | w=26
  641. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:dysmorphic ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:dysmorphic ears | rel=r_associated | relid=0 | w=26
  642. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:eustachian tube salpingitis
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:eustachian tube salpingitis | rel=r_associated | relid=0 | w=26
  643. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:expansion of helical fold at superior point of true longitudinal axis of ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:expansion of helical fold at superior point of true longitudinal axis of ear | rel=r_associated | relid=0 | w=26
  644. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:external auditory canal narrow
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:external auditory canal narrow | rel=r_associated | relid=0 | w=26
  645. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:external ear defects
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:external ear defects | rel=r_associated | relid=0 | w=26
  646. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:floppy ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:floppy ears | rel=r_associated | relid=0 | w=26
  647. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:hearing impairment (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing impairment (in some patients) | rel=r_associated | relid=0 | w=26
  648. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:hearing impairment (rare)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing impairment (rare) | rel=r_associated | relid=0 | w=26
  649. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:hearing loss, bilateral sensorineural (profound)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, bilateral sensorineural (profound) | rel=r_associated | relid=0 | w=26
  650. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:hearing loss, initially conductive, later mixed conductive-sensorineural
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, initially conductive, later mixed conductive-sensorineural | rel=r_associated | relid=0 | w=26
  651. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:hearing loss, late-onset sensorineural, mild-to moderate (less common)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, late-onset sensorineural, mild-to moderate (less common) | rel=r_associated | relid=0 | w=26
  652. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:hearing loss, mixed (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, mixed (in some patients) | rel=r_associated | relid=0 | w=26
  653. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:hearing loss, neural type
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, neural type | rel=r_associated | relid=0 | w=26
  654. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:hearing loss, sensorineural, due to auditory neuropathy
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural, due to auditory neuropathy | rel=r_associated | relid=0 | w=26
  655. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:hypoplastic ear lobes
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hypoplastic ear lobes | rel=r_associated | relid=0 | w=26
  656. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:hypoplastic, overfolded helices
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hypoplastic, overfolded helices | rel=r_associated | relid=0 | w=26
  657. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:impaired tympanic membrane mobility
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:impaired tympanic membrane mobility | rel=r_associated | relid=0 | w=26
  658. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:inferior displacement of the ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:inferior displacement of the ears | rel=r_associated | relid=0 | w=26
  659. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:loss of vestibular caloric response
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:loss of vestibular caloric response | rel=r_associated | relid=0 | w=26
  660. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:low set ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:low set ears | rel=r_associated | relid=0 | w=26
  661. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:low-set ears (1 patient)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:low-set ears (1 patient) | rel=r_associated | relid=0 | w=26
  662. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:low-set ears (45%)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:low-set ears (45%) | rel=r_associated | relid=0 | w=26
  663. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:macrotia
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:macrotia | rel=r_associated | relid=0 | w=26
  664. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:malformed earlobes
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:malformed earlobes | rel=r_associated | relid=0 | w=26
  665. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:michel aplasia (complete absence of inner ear structures)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:michel aplasia (complete absence of inner ear structures) | rel=r_associated | relid=0 | w=26
  666. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:misshapen, small ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:misshapen, small ear | rel=r_associated | relid=0 | w=26
  667. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:no auditory brainstem response (abr)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:no auditory brainstem response (abr) | rel=r_associated | relid=0 | w=26
  668. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:no reproducible waves i, iii, or v at high intensities
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:no reproducible waves i, iii, or v at high intensities | rel=r_associated | relid=0 | w=26
  669. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:other symptom/complaint of ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:other symptom/complaint of ear | rel=r_associated | relid=0 | w=26
  670. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:postauricular pit
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:postauricular pit | rel=r_associated | relid=0 | w=26
  671. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:posteriorly rotated ears (1/4 patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:posteriorly rotated ears (1/4 patients) | rel=r_associated | relid=0 | w=26
  672. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:progressive sensorineural hearing impairment
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:progressive sensorineural hearing impairment | rel=r_associated | relid=0 | w=26
  673. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:pulsatile tinnitus (tympanic paraganglioma)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:pulsatile tinnitus (tympanic paraganglioma) | rel=r_associated | relid=0 | w=26
  674. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:recurrent ear infections
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:recurrent ear infections | rel=r_associated | relid=0 | w=26
  675. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:recurrent otitis media (18%)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:recurrent otitis media (18%) | rel=r_associated | relid=0 | w=26
  676. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:sensorineural hearing loss (uncommon)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:sensorineural hearing loss (uncommon) | rel=r_associated | relid=0 | w=26
  677. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:short ear
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:short ear | rel=r_associated | relid=0 | w=26
  678. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:simple helix
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:simple helix | rel=r_associated | relid=0 | w=26
  679. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:small, malformed ears
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:small, malformed ears | rel=r_associated | relid=0 | w=26
  680. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves | rel=r_associated | relid=0 | w=26
  681. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:tympanic membrane perforation
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:tympanic membrane perforation | rel=r_associated | relid=0 | w=26
  682. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 26 / 0.605 -> en:u- or bowl-shaped audiogram
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:u- or bowl-shaped audiogram | rel=r_associated | relid=0 | w=26
  683. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 25 / 0.581 -> otite moyenne séreuse
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=otite moyenne séreuse | rel=r_associated | relid=0 | w=25
  684. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 25 / 0.581 -> surdité héréditaire
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=surdité héréditaire | rel=r_associated | relid=0 | w=25
  685. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 23 / 0.535 -> surdité du labyrinthe
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=surdité du labyrinthe | rel=r_associated | relid=0 | w=23
  686. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 23 / 0.535 -> traumatisme superficiel oreille
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=traumatisme superficiel oreille | rel=r_associated | relid=0 | w=23
  687. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> déficience auditive
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=déficience auditive | rel=r_associated | relid=0 | w=20
  688. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> en:balance problem
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:balance problem | rel=r_associated | relid=0 | w=20
  689. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> en:chronic otitis media (25%)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:chronic otitis media (25%) | rel=r_associated | relid=0 | w=20
  690. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> en:cutlet
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:cutlet | rel=r_associated | relid=0 | w=20
  691. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> en:disorder of equilibrium
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:disorder of equilibrium | rel=r_associated | relid=0 | w=20
  692. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> en:dysplastic ears (jbts)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:dysplastic ears (jbts) | rel=r_associated | relid=0 | w=20
  693. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> en:ENT doctor
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:ENT doctor | rel=r_associated | relid=0 | w=20
  694. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> en:ENT specialist
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:ENT specialist | rel=r_associated | relid=0 | w=20
  695. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> en:escalope
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:escalope | rel=r_associated | relid=0 | w=20
  696. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> en:hearing impairment (1 patient)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing impairment (1 patient) | rel=r_associated | relid=0 | w=20
  697. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> en:hearing impairment, progressive (family a)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing impairment, progressive (family a) | rel=r_associated | relid=0 | w=20
  698. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> en:hearing loss (in 2 members of 1 family)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss (in 2 members of 1 family) | rel=r_associated | relid=0 | w=20
  699. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> en:hearing loss, sensorineural, progressive (all frequencies)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural, progressive (all frequencies) | rel=r_associated | relid=0 | w=20
  700. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> en:hereditary deafness
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hereditary deafness | rel=r_associated | relid=0 | w=20
  701. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> en:microtia (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:microtia (in some patients) | rel=r_associated | relid=0 | w=20
  702. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> en:mild dysplasia of concha, unilateral
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:mild dysplasia of concha, unilateral | rel=r_associated | relid=0 | w=20
  703. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> en:no vestibular symptoms
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:no vestibular symptoms | rel=r_associated | relid=0 | w=20
  704. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> en:nose and throat specialist
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:nose and throat specialist | rel=r_associated | relid=0 | w=20
  705. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> en:otolaryngologist
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:otolaryngologist | rel=r_associated | relid=0 | w=20
  706. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> en:otorhinolaryngologist
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:otorhinolaryngologist | rel=r_associated | relid=0 | w=20
  707. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> en:problem with balance
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:problem with balance | rel=r_associated | relid=0 | w=20
  708. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> en:rotary vertigo
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:rotary vertigo | rel=r_associated | relid=0 | w=20
  709. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> en:tinnitus, bilateral (in some patients)
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:tinnitus, bilateral (in some patients) | rel=r_associated | relid=0 | w=20
  710. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> état nébuleux
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=état nébuleux | rel=r_associated | relid=0 | w=20
  711. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> état vertigineux
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=état vertigineux | rel=r_associated | relid=0 | w=20
  712. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> étourdissement
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=étourdissement | rel=r_associated | relid=0 | w=20
  713. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> hyperacousie
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=hyperacousie | rel=r_associated | relid=0 | w=20
  714. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> hyperacousies
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=hyperacousies | rel=r_associated | relid=0 | w=20
  715. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> hyperacusie
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=hyperacusie | rel=r_associated | relid=0 | w=20
  716. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> hyperlaxe
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=hyperlaxe | rel=r_associated | relid=0 | w=20
  717. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> hypermobile
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=hypermobile | rel=r_associated | relid=0 | w=20
  718. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> médecin ORL
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=médecin ORL | rel=r_associated | relid=0 | w=20
  719. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> otite séreuse
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=otite séreuse | rel=r_associated | relid=0 | w=20
  720. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> otite séromuqueuse
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=otite séromuqueuse | rel=r_associated | relid=0 | w=20
  721. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> oto-rhino
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=oto-rhino | rel=r_associated | relid=0 | w=20
  722. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> oto-rhino-laryngologiste
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=oto-rhino-laryngologiste | rel=r_associated | relid=0 | w=20
  723. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> otorhinolaryngologiste
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=otorhinolaryngologiste | rel=r_associated | relid=0 | w=20
  724. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> pavillon de l'oreille de morphologie rudimentaire
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=pavillon de l'oreille de morphologie rudimentaire | rel=r_associated | relid=0 | w=20
  725. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> sensation de rotation
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=sensation de rotation | rel=r_associated | relid=0 | w=20
  726. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> sensation de tournoiement
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=sensation de tournoiement | rel=r_associated | relid=0 | w=20
  727. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> sensation rotatoire
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=sensation rotatoire | rel=r_associated | relid=0 | w=20
  728. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> sensation vertigineuse
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=sensation vertigineuse | rel=r_associated | relid=0 | w=20
  729. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> sténose du canal auriculaire
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=sténose du canal auriculaire | rel=r_associated | relid=0 | w=20
  730. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> surdimutité
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=surdimutité | rel=r_associated | relid=0 | w=20
  731. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> surdité neurosensorielle bilatérale
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=surdité neurosensorielle bilatérale | rel=r_associated | relid=0 | w=20
  732. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> tête pivotante
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=tête pivotante | rel=r_associated | relid=0 | w=20
  733. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> trouble de l'équilibre
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=trouble de l'équilibre | rel=r_associated | relid=0 | w=20
  734. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> vertige
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=vertige | rel=r_associated | relid=0 | w=20
  735. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> vertige rotatoire
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=vertige rotatoire | rel=r_associated | relid=0 | w=20
  736. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> vertige subjectif
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=vertige subjectif | rel=r_associated | relid=0 | w=20
  737. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> vertigo
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=vertigo | rel=r_associated | relid=0 | w=20
  738. en:deafness due to bilateral cochlear malformation (rare) -- r_associated #0: 20 / 0.465 -> vertigo rotatoire
    n1=en:deafness due to bilateral cochlear malformation (rare) | n2=vertigo rotatoire | rel=r_associated | relid=0 | w=20
≈ 778 relations entrantes

  1. en:congenital deafness --- r_associated #0: 300 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:congenital deafness | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=300
  2. surdité congénitale --- r_associated #0: 297 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=surdité congénitale | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=297
  3. surdité héréditaire --- r_associated #0: 295 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=surdité héréditaire | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=295
  4. surdité du labyrinthe --- r_associated #0: 271 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=surdité du labyrinthe | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=271
  5. en:deafness labyrinthine --- r_associated #0: 270 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness labyrinthine | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=270
  6. otite moyenne séreuse --- r_associated #0: 222 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=otite moyenne séreuse | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=222
  7. en:serous otitis media --- r_associated #0: 220 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:serous otitis media | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=220
  8. sensation de tournoiement --- r_associated #0: 200 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=sensation de tournoiement | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=200
  9. sensation vertigineuse --- r_associated #0: 200 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=sensation vertigineuse | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=200
  10. vertige rotatoire --- r_associated #0: 200 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=vertige rotatoire | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=200
  11. vertige subjectif --- r_associated #0: 200 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=vertige subjectif | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=200
  12. vertigo rotatoire --- r_associated #0: 200 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=vertigo rotatoire | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=200
  13. sensation de rotation --- r_associated #0: 199 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=sensation de rotation | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=199
  14. état nébuleux --- r_associated #0: 195 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=état nébuleux | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=195
  15. état vertigineux --- r_associated #0: 195 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=état vertigineux | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=195
  16. sensation rotatoire --- r_associated #0: 192 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=sensation rotatoire | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=192
  17. tête pivotante --- r_associated #0: 190 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=tête pivotante | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=190
  18. en:sensorineural hearing loss --- r_associated #0: 188 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural hearing loss | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=188
  19. traumatisme superficiel oreille --- r_associated #0: 185 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=traumatisme superficiel oreille | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=185
  20. perte d'audition sensorineurale --- r_associated #0: 184 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=perte d'audition sensorineurale | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=184
  21. en:superficial injury of ear --- r_associated #0: 181 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:superficial injury of ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=181
  22. en:sensorineural hearing loss, bilateral --- r_associated #0: 168 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural hearing loss, bilateral | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=168
  23. en:vertigo --- r_associated #0: 167 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:vertigo | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=167
  24. en:dizziness --- r_associated #0: 165 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:dizziness | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=165
  25. surdité neurosensorielle bilatérale --- r_associated #0: 165 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=surdité neurosensorielle bilatérale | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=165
  26. hyperacousie --- r_associated #0: 140 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=hyperacousie | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=140
  27. hyperacusie --- r_associated #0: 140 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=hyperacusie | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=140
  28. en:hyperacusis --- r_associated #0: 136 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hyperacusis | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=136
  29. vertigo --- r_associated #0: 129 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=vertigo | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=129
  30. hyperacousies --- r_associated #0: 120 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=hyperacousies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=120
  31. en:balance problem --- r_associated #0: 115 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:balance problem | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=115
  32. en:disorder of equilibrium --- r_associated #0: 115 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:disorder of equilibrium | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=115
  33. en:problem with balance --- r_associated #0: 115 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:problem with balance | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=115
  34. trouble de l'équilibre --- r_associated #0: 115 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=trouble de l'équilibre | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=115
  35. vertige --- r_associated #0: 95 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=vertige | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=95
  36. en:secretory otitis media --- r_associated #0: 87 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:secretory otitis media | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=87
  37. otite séromuqueuse --- r_associated #0: 85 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=otite séromuqueuse | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=85
  38. étourdissement --- r_associated #0: 80 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=étourdissement | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=80
  39. lésion traumatique superficielle de l'oreille --- r_associated #0: 58 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=lésion traumatique superficielle de l'oreille | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=58
  40. en:ENT specialist --- r_associated #0: 50 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:ENT specialist | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=50
  41. oto-rhino --- r_associated #0: 50 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=oto-rhino | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=50
  42. déficience auditive --- r_associated #0: 48 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=déficience auditive | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=48
  43. en:hereditary deafness --- r_associated #0: 47 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hereditary deafness | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=47
  44. en:nose and throat specialist --- r_associated #0: 46 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:nose and throat specialist | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=46
  45. oto-rhino-laryngologiste --- r_associated #0: 45 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=oto-rhino-laryngologiste | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=45
  46. otorhinolaryngologiste --- r_associated #0: 45 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=otorhinolaryngologiste | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=45
  47. en:hearing impairment --- r_associated #0: 44 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing impairment | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=44
  48. en:deficient auricle --- r_associated #0: 43 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deficient auricle | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=43
  49. en:hearing loss (cvs+) --- r_associated #0: 43 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss (cvs+) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=43
  50. en:hearing loss, more severe at lower frequencies --- r_associated #0: 43 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, more severe at lower frequencies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=43
  51. en:oae responses may decrease with age or use of hearing aids --- r_associated #0: 43 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:oae responses may decrease with age or use of hearing aids | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=43
  52. en:occasional conductive hearing loss --- r_associated #0: 43 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:occasional conductive hearing loss | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=43
  53. en:rotary vertigo --- r_associated #0: 43 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:rotary vertigo | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=43
  54. en:tinnitus, bilateral (in some patients) --- r_associated #0: 43 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:tinnitus, bilateral (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=43
  55. en:vestibular areflexia --- r_associated #0: 43 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:vestibular areflexia | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=43
  56. en:audiogram may be ascending --- r_associated #0: 42 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:audiogram may be ascending | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=42
  57. en:folded superior edge of helix --- r_associated #0: 42 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:folded superior edge of helix | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=42
  58. en:hearing loss, mixed (in some patients) --- r_associated #0: 42 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, mixed (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=42
  59. en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile) --- r_associated #0: 41 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=41
  60. en:flat ears --- r_associated #0: 41 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:flat ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=41
  61. en:loss of mid- and low-frequencies later --- r_associated #0: 41 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:loss of mid- and low-frequencies later | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=41
  62. en:abnormal ear configuration --- r_associated #0: 40 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormal ear configuration | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=40
  63. en:absence of the helix and distal scapha in middle third of the ear --- r_associated #0: 40 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:absence of the helix and distal scapha in middle third of the ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=40
  64. en:congenital sensorineural hearing loss --- r_associated #0: 40 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:congenital sensorineural hearing loss | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=40
  65. en:deafness, early-onset mixed conductive and sensorineural --- r_associated #0: 40 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, early-onset mixed conductive and sensorineural | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=40
  66. en:hypermobile --- r_associated #0: 39 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hypermobile | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=39
  67. en:stapes ankylosis --- r_associated #0: 39 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:stapes ankylosis | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=39
  68. en:everted ears --- r_associated #0: 38 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:everted ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=38
  69. en:hearing loss (affecting all frequencies), moderate to severe --- r_associated #0: 38 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss (affecting all frequencies), moderate to severe | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=38
  70. en:large, low-set ears --- r_associated #0: 38 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:large, low-set ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=38
  71. en:nonprogressive deafness --- r_associated #0: 38 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:nonprogressive deafness | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=38
  72. en:ear cartilage calcification --- r_associated #0: 37 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:ear cartilage calcification | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=37
  73. en:flattened antihelix --- r_associated #0: 37 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:flattened antihelix | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=37
  74. en:hearing impairment, sensorineural, fluctuating --- r_associated #0: 37 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing impairment, sensorineural, fluctuating | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=37
  75. en:otoneurologic disturbances --- r_associated #0: 37 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:otoneurologic disturbances | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=37
  76. en:rudimentary tympanic membrane (in some patients) --- r_associated #0: 37 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:rudimentary tympanic membrane (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=37
  77. en:sclerosis of semicircular canals --- r_associated #0: 37 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sclerosis of semicircular canals | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=37
  78. en:sensorineural hearing loss (1 family) --- r_associated #0: 37 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural hearing loss (1 family) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=37
  79. en:sensorineural hearing loss, mild (rare) --- r_associated #0: 37 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural hearing loss, mild (rare) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=37
  80. en:short ear --- r_associated #0: 37 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:short ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=37
  81. hypermobile --- r_associated #0: 37 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=hypermobile | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=37
  82. surdimutité --- r_associated #0: 37 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=surdimutité | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=37
  83. en:bilateral sensorineural hearing loss (in some patients) --- r_associated #0: 36 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:bilateral sensorineural hearing loss (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=36
  84. en:dilatated internal auditory canal --- r_associated #0: 36 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:dilatated internal auditory canal | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=36
  85. en:hearing loss, sensorineural, due to auditory neuropathy --- r_associated #0: 36 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural, due to auditory neuropathy | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=36
  86. en:minor ear anomalies (in some patients) --- r_associated #0: 36 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:minor ear anomalies (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=36
  87. en:pseudomembranous inflammation of the middle ear --- r_associated #0: 36 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:pseudomembranous inflammation of the middle ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=36
  88. surdi-mutité --- r_associated #0: 36 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=surdi-mutité | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=36
  89. en:ENT doctor --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:ENT doctor | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  90. en:abnormal gap detection --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormal gap detection | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  91. en:anomalous middle ear bones --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:anomalous middle ear bones | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  92. en:asymmetric dysplastic ears --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:asymmetric dysplastic ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  93. en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient) --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  94. en:audiogram shows sloping configuration --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:audiogram shows sloping configuration | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  95. en:auditory impairment --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:auditory impairment | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  96. en:auricular clefts --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:auricular clefts | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  97. en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  98. en:chronic otitis media --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:chronic otitis media | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  99. en:cleft lobules --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:cleft lobules | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  100. en:cupped ears (in some patients) --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:cupped ears (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  101. en:deafness, congenital sensorineural, severe to profound --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, congenital sensorineural, severe to profound | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  102. en:deafness, moderate-severe (onset in third decade) --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, moderate-severe (onset in third decade) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  103. en:deafness, sensorineural (reported in 1 family) --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, sensorineural (reported in 1 family) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  104. en:deafness, sensorineural, especially affecting high frequencies --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, sensorineural, especially affecting high frequencies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  105. en:deafness, sensorineural, profound --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, sensorineural, profound | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  106. en:deafness, stable bilateral symmetric prelingual --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, stable bilateral symmetric prelingual | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  107. en:downward sloping audiogram --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:downward sloping audiogram | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  108. en:hearing loss, prelingual sensorineural, moderate to severe --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, prelingual sensorineural, moderate to severe | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  109. en:hearing loss, sensorineural (in 2 patients) --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural (in 2 patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  110. en:hearing loss, sensorineural, progressive (all frequencies) --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural, progressive (all frequencies) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  111. en:hearing loss, severe to profound, affecting all frequencies --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, severe to profound, affecting all frequencies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  112. en:hyperfolded ears --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hyperfolded ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  113. en:hypertrophic auricular cartilage --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hypertrophic auricular cartilage | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  114. en:large ears (2p21del) --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:large ears (2p21del) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  115. en:long and prominent ear crus --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:long and prominent ear crus | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  116. en:loss of vestibular caloric response --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:loss of vestibular caloric response | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  117. en:low set ears --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:low set ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  118. en:malformations of the auditory ossicles --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:malformations of the auditory ossicles | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  119. en:mondini malformation --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:mondini malformation | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  120. en:narrowed external ear canal (30% of patients) --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:narrowed external ear canal (30% of patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  121. en:normal middle ear pressures on tympanometry --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:normal middle ear pressures on tympanometry | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  122. en:normal static compliance on tympanometry --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:normal static compliance on tympanometry | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  123. en:posterior helical indentations --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:posterior helical indentations | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  124. en:pre- and post-auricular skin or cartilaginous tags --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:pre- and post-auricular skin or cartilaginous tags | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  125. en:profound deafness --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:profound deafness | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  126. en:prominence and protrusion of upper third of the ear --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:prominence and protrusion of upper third of the ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  127. en:prominent antitragus (in some patients) --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:prominent antitragus (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  128. en:protruding ears (in some patients) --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:protruding ears (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  129. en:satyr ear --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:satyr ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  130. en:sensorineural deafness (rare) --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural deafness (rare) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  131. en:sensorineural deafness, postlingual, progressive --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural deafness, postlingual, progressive | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  132. en:sensorineural hearing loss (early-onset form) --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural hearing loss (early-onset form) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  133. en:sensorineural hearing loss (uncommon) --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural hearing loss (uncommon) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  134. en:sensory hearing loss --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensory hearing loss | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  135. en:small ears (female) --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:small ears (female) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  136. en:small external auditory meatus --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:small external auditory meatus | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  137. en:small, simple ears --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:small, simple ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  138. en:stapes fixation --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:stapes fixation | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  139. en:stenosis of external auditory canal --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:stenosis of external auditory canal | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  140. en:tympanic membrane perforation --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:tympanic membrane perforation | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  141. en:unconnected or fused stapes and incus --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:unconnected or fused stapes and incus | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  142. en:unfolded superior helices --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:unfolded superior helices | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  143. en:vestibular involvement (variable) --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:vestibular involvement (variable) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  144. sténose du canal auriculaire --- r_associated #0: 35 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=sténose du canal auriculaire | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=35
  145. en:abnormal brain auditory evoked responses (baer) --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormal brain auditory evoked responses (baer) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  146. en:abnormal or absent auditory nerve and brainstem responses --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormal or absent auditory nerve and brainstem responses | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  147. en:abnormally folded ears --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormally folded ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  148. en:absence of the cochlear nerves (reported in 1 patient) --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:absence of the cochlear nerves (reported in 1 patient) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  149. en:absent helices, bilaterally --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:absent helices, bilaterally | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  150. en:attached ear lobes --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:attached ear lobes | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  151. en:congenital hearing loss (1 family) --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:congenital hearing loss (1 family) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  152. en:cup-shaped auricles --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:cup-shaped auricles | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  153. en:deafness (often in third decade) --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness (often in third decade) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  154. en:deafness, congenital nonprogressive sensorineural symmetric, moderate --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, congenital nonprogressive sensorineural symmetric, moderate | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  155. en:deafness, congenital sensorineural, profound (in some patients) --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, congenital sensorineural, profound (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  156. en:deafness, early-onset --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, early-onset | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  157. en:deafness, sensorineural (45%) --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, sensorineural (45%) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  158. en:disproportionately large ears --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:disproportionately large ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  159. en:ear --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  160. en:ear tag --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:ear tag | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  161. en:hearing loss (2 patients) --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss (2 patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  162. en:hearing loss, bilateral --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, bilateral | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  163. en:hearing loss, conductive (in some patients) --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, conductive (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  164. en:hearing loss, conductive or mixed --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, conductive or mixed | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  165. en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies) --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  166. en:hearing loss, sensorineural, bilateral, moderate-to-severe --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  167. en:hearing loss, sensorineural, prelingual --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural, prelingual | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  168. en:hearing loss, unilateral (rare) --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, unilateral (rare) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  169. en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  170. en:hearing normal --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing normal | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  171. en:hypoplastic helices --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hypoplastic helices | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  172. en:large ears (37%) --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:large ears (37%) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  173. en:low-frequency conductive hearing loss --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:low-frequency conductive hearing loss | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  174. en:low-set ears (45%) --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:low-set ears (45%) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  175. en:low-set ears (rare) --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:low-set ears (rare) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  176. en:low-set, malformed ears --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:low-set, malformed ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  177. en:microtia (30-60% of patients) --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:microtia (30-60% of patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  178. en:microtia, type i --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:microtia, type i | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  179. en:near-stenosis of bony portion of auditory canal (in homozygotes) --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:near-stenosis of bony portion of auditory canal (in homozygotes) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  180. en:no deafness --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:no deafness | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  181. en:pointed upper helix --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:pointed upper helix | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  182. en:poorly formed ears --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:poorly formed ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  183. en:preauricular skin furrow --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:preauricular skin furrow | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  184. en:protruding, simple ears --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:protruding, simple ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  185. en:recurrent otitis media (18%) --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:recurrent otitis media (18%) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  186. en:recurrent otitis media in infancy and childhood --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:recurrent otitis media in infancy and childhood | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  187. en:sensorineural hearing loss (1 patient) --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural hearing loss (1 patient) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  188. en:sensorineural hearing loss (less common) --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural hearing loss (less common) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  189. en:sensorineural, conductive, or mixed hearing loss --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural, conductive, or mixed hearing loss | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  190. en:small auricles --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:small auricles | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  191. en:small lobes --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:small lobes | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  192. en:small, malformed ears --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:small, malformed ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  193. en:stenotic ear canals (30%) --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:stenotic ear canals (30%) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  194. en:thick earlobes --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:thick earlobes | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  195. en:thickened helices --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:thickened helices | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  196. en:thickened lobes --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:thickened lobes | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  197. en:u- or bowl-shaped audiogram --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:u- or bowl-shaped audiogram | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  198. en:underdeveloped tragus --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:underdeveloped tragus | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  199. en:vestibular dysfunction (in some patients) --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:vestibular dysfunction (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  200. en:vestibular hypofunction --- r_associated #0: 34 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:vestibular hypofunction | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
  201. en:abnormal middle ear ossicles --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormal middle ear ossicles | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  202. en:abnormality of the helix --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormality of the helix | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  203. en:abnormally folded helix --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormally folded helix | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  204. en:abnormally formed ears --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormally formed ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  205. en:absence of earlobe --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:absence of earlobe | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  206. en:absence of vestibular evoked myogenic potentials (rare) --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:absence of vestibular evoked myogenic potentials (rare) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  207. en:absent cochlear microphonic (in older patients) --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:absent cochlear microphonic (in older patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  208. en:chronic otitis media (25%) --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:chronic otitis media (25%) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  209. en:conductive hearing loss (30% of patients) --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:conductive hearing loss (30% of patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  210. en:crumpled ear (76%) --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:crumpled ear (76%) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  211. en:deafness, sensorineural, prelingual, profound --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, sensorineural, prelingual, profound | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  212. en:dysplastic helices --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:dysplastic helices | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  213. en:hearing loss (in 2 members of 1 family) --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss (in 2 members of 1 family) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  214. en:hearing loss affects all frequencies --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss affects all frequencies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  215. en:hearing loss, mild (rare) --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, mild (rare) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  216. en:hearing loss, progressive, starting in infancy --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, progressive, starting in infancy | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  217. en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies) --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  218. en:hearing loss, sensorineural (type ii) --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural (type ii) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  219. en:hypoplastic ear lobes --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hypoplastic ear lobes | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  220. en:hypoplastic, overfolded helices --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hypoplastic, overfolded helices | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  221. en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients) --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  222. en:mild dysplasia of concha, unilateral --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:mild dysplasia of concha, unilateral | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  223. en:mild hearing impairment (13%) --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:mild hearing impairment (13%) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  224. en:normal cochlear microphonics --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:normal cochlear microphonics | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  225. en:otitis media, chronic (rare) --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:otitis media, chronic (rare) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  226. en:overfolded helix --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:overfolded helix | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  227. en:prominent antihelix --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:prominent antihelix | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  228. en:prominent ear --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:prominent ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  229. en:recurrent ear infections --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:recurrent ear infections | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  230. en:severe loss in the higher frequencies by the fifth decade --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:severe loss in the higher frequencies by the fifth decade | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  231. en:simplified helices --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:simplified helices | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  232. en:superiorly displaced ears --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:superiorly displaced ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  233. en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  234. en:vestibular abnormalities (variable) --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:vestibular abnormalities (variable) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  235. en:vestibular hypofunction (rare) --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:vestibular hypofunction (rare) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  236. otite séreuse --- r_associated #0: 32 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=otite séreuse | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=32
  237. en:abnormal auditory brainstem responses --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormal auditory brainstem responses | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  238. en:abnormal auditory temporal processes --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormal auditory temporal processes | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  239. en:abnormal communication between the subarachnoid space in the meatus and the perilymph --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormal communication between the subarachnoid space in the meatus and the perilymph | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  240. en:abnormality of the middle ear ossicles --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormality of the middle ear ossicles | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  241. en:absent brainstem auditory responses --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:absent brainstem auditory responses | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  242. en:absent external auditory canals --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:absent external auditory canals | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  243. en:absent external auditory meatus --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:absent external auditory meatus | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  244. en:acoustic trauma --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:acoustic trauma | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  245. en:atretic auditory canal --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:atretic auditory canal | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  246. en:atretic ear canals --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:atretic ear canals | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  247. en:aural fullness --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:aural fullness | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  248. en:conductive hearing loss --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:conductive hearing loss | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  249. en:conductive hearing loss (in a subset of patients) --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:conductive hearing loss (in a subset of patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  250. en:cup-shaped ears (30-60% of patients) --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:cup-shaped ears (30-60% of patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  251. en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  252. en:entire ear --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:entire ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  253. en:hearing loss (rare) --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss (rare) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  254. en:hearing loss, profound prelingual sensorineural --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, profound prelingual sensorineural | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  255. en:hearing loss, progressive conductive and/or sensorineural, during adulthood --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, progressive conductive and/or sensorineural, during adulthood | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  256. en:hearing loss, sensorineural (in patients with larger deletions) --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural (in patients with larger deletions) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  257. en:keratotic plaque around ear meatus --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:keratotic plaque around ear meatus | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  258. en:large dysplastic ears --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:large dysplastic ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  259. en:lobule creases --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:lobule creases | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  260. en:loss of hearing (45%) --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:loss of hearing (45%) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  261. en:misshapen ear --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:misshapen ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  262. en:narrow auditory canals (rare) --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:narrow auditory canals (rare) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  263. en:normal vestibular function --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:normal vestibular function | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  264. en:pale, stiff pinnae --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:pale, stiff pinnae | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  265. en:partial hearing loss --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:partial hearing loss | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  266. en:pigmentation of the ear cartilage --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:pigmentation of the ear cartilage | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  267. en:posteriorly rotated ears (2p21del) --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:posteriorly rotated ears (2p21del) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  268. en:progressive, low frequency sensorineural hearing loss --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:progressive, low frequency sensorineural hearing loss | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  269. en:prolonged brainstem auditory evoked potentials (baep) --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:prolonged brainstem auditory evoked potentials (baep) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  270. en:simple auricles --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:simple auricles | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  271. en:small ears with large lobules --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:small ears with large lobules | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  272. en:supraauricular pit --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:supraauricular pit | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  273. en:tinnitus (rare) --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:tinnitus (rare) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  274. en:upturned lobes --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:upturned lobes | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  275. en:vestibulopathy, bilateral, progressive --- r_associated #0: 31 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:vestibulopathy, bilateral, progressive | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=31
  276. en:abnormal ears --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormal ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  277. en:abnormality of the middle ear --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormality of the middle ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  278. en:absence of acoustic reflex --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:absence of acoustic reflex | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  279. en:absent or abnormal otoacoustic emissions --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:absent or abnormal otoacoustic emissions | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  280. en:anterior creases of earlobe --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:anterior creases of earlobe | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  281. en:apical cartilage deformity --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:apical cartilage deformity | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  282. en:bilateral conductive hearing loss (rare) --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:bilateral conductive hearing loss (rare) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  283. en:complete bony atresia of medial portion of external auditory canal (in some patients) --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:complete bony atresia of medial portion of external auditory canal (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  284. en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss) --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  285. en:deafness, bilateral sensorineural, high frequency (100% of patients) --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, bilateral sensorineural, high frequency (100% of patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  286. en:deafness, conductive (in some patients) --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, conductive (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  287. en:deafness, nonprogressive, moderate --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, nonprogressive, moderate | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  288. en:deafness, sensorineural, especially affecting high frequencies (in about 55% of males and 45% of females) --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, sensorineural, especially affecting high frequencies (in about 55% of males and 45% of females) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  289. en:deafness, sensorineural, profound (prelingual onset) --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, sensorineural, profound (prelingual onset) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  290. en:deafness, unilateral, childhood onset --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, unilateral, childhood onset | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  291. en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  292. en:dorsally rotated ears --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:dorsally rotated ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  293. en:dysplastic ears (jbts) --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:dysplastic ears (jbts) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  294. en:dysplastic pinnae --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:dysplastic pinnae | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  295. en:ear pain/earache --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:ear pain/earache | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  296. en:ears deficient in cartilage --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:ears deficient in cartilage | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  297. en:escalope --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:escalope | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  298. en:external ear defects (47%) --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:external ear defects (47%) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  299. en:fleshy ears --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:fleshy ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  300. en:floppy ears --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:floppy ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  301. en:hearing impairment, asymmetric (in some patients with hsan2d) --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing impairment, asymmetric (in some patients with hsan2d) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  302. en:hearing loss (95% of patients) --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss (95% of patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  303. en:hearing loss (conductive and/or sensorineural) --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss (conductive and/or sensorineural) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  304. en:hearing loss has been reported in some adults with severe disease --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss has been reported in some adults with severe disease | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  305. en:hearing loss, congenital sensorineural, moderate-severe --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, congenital sensorineural, moderate-severe | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  306. en:hearing loss, progressive (in some patients) --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, progressive (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  307. en:hearing loss, sensorineural (in one family) --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural (in one family) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  308. en:hearing loss, unilateral, mild --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, unilateral, mild | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  309. en:hypercompliant tympanic membranes --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hypercompliant tympanic membranes | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  310. en:large anteverted ears --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:large anteverted ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  311. en:low-frequency sensorineural hearing impairment --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:low-frequency sensorineural hearing impairment | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  312. en:low-set ears (severe form) --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:low-set ears (severe form) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  313. en:malformed pinnae (30-60% of patients) --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:malformed pinnae (30-60% of patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  314. en:narrow ear lobes --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:narrow ear lobes | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  315. en:no vestibular symptoms --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:no vestibular symptoms | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  316. en:otitis externa, recurrent, due to infection with staphylococcus aureus --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:otitis externa, recurrent, due to infection with staphylococcus aureus | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  317. en:profound sensorineural hearing loss --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:profound sensorineural hearing loss | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  318. en:protruding lobules --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:protruding lobules | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  319. en:protuberant ear --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:protuberant ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  320. en:raised earlobes --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:raised earlobes | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  321. en:rotated ears --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:rotated ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  322. en:sensorineural deafness (reported in 1 family) --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural deafness (reported in 1 family) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  323. en:sensorineural hearing impairment (less common) --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural hearing impairment (less common) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  324. en:sensorineural hearing loss (3 patients) --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural hearing loss (3 patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  325. en:sensorineural hearing loss (described in 1 family) --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural hearing loss (described in 1 family) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  326. en:sensorineural hearing loss (in 1 of 3 patients) --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural hearing loss (in 1 of 3 patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  327. en:sensorineural hearing loss, mild to moderate --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural hearing loss, mild to moderate | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  328. en:simple ear structure --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:simple ear structure | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  329. en:simple helix --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:simple helix | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  330. en:small pinna --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:small pinna | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  331. en:squared-off superior helices --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:squared-off superior helices | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  332. en:structure of superior auricularis muscle --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:structure of superior auricularis muscle | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  333. en:thick, firm earlobes --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:thick, firm earlobes | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  334. en:vertigo, episodic --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:vertigo, episodic | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  335. médecin ORL --- r_associated #0: 30 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=médecin ORL | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=30
  336. en:abnormal auricles --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormal auricles | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  337. en:abnormality of the pinna --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormality of the pinna | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  338. en:absent stapedial reflex --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:absent stapedial reflex | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  339. en:absent stapedial reflexes or intraoperative stapes immobility --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:absent stapedial reflexes or intraoperative stapes immobility | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  340. en:bilateral hypoplastic cochlea --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:bilateral hypoplastic cochlea | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  341. en:cauliflower ear deformity (rare) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:cauliflower ear deformity (rare) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  342. en:cleft at the junction of the lobule and helix --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:cleft at the junction of the lobule and helix | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  343. en:conductive hearing loss, mild bilateral (rare) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:conductive hearing loss, mild bilateral (rare) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  344. en:cupped ears (finding) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:cupped ears (finding) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  345. en:cupped pinna --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:cupped pinna | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  346. en:deafness (in some patients) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  347. en:deafness, profound, affects all frequencies --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, profound, affects all frequencies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  348. en:decreased otoacoustic emission amplitude --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:decreased otoacoustic emission amplitude | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  349. en:ear pits, posterior helical --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:ear pits, posterior helical | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  350. en:earlobe pits --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:earlobe pits | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  351. en:hearing loss (reported in 2 patients) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss (reported in 2 patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  352. en:hearing loss, high frequency, slowly progressive (onset in early childhood) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, high frequency, slowly progressive (onset in early childhood) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  353. en:hearing loss, initially conductive, later mixed conductive-sensorineural --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, initially conductive, later mixed conductive-sensorineural | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  354. en:hearing loss, sensorineural (in some) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural (in some) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  355. en:hearing loss, sensorineural (reported in 1 patient) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural (reported in 1 patient) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  356. en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  357. en:high-tone sensorineural deafness (67% of patients) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:high-tone sensorineural deafness (67% of patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  358. en:hypoplastic ears fused to the scalp --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hypoplastic ears fused to the scalp | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  359. en:large ear pinnae --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:large ear pinnae | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  360. en:large protruding ears --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:large protruding ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  361. en:large simple ears --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:large simple ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  362. en:lobule may be separately from the rest of the external ear --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:lobule may be separately from the rest of the external ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  363. en:low-set ears (1 patient) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:low-set ears (1 patient) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  364. en:low-set ears (28%) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:low-set ears (28%) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  365. en:low-set ears (in 2/4 patients) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:low-set ears (in 2/4 patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  366. en:malformed auricle (1 patient) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:malformed auricle (1 patient) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  367. en:malformed earlobes --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:malformed earlobes | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  368. en:middle ear --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:middle ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  369. en:minor auricular anomalies --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:minor auricular anomalies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  370. en:mixed hearing loss (50% of patients) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:mixed hearing loss (50% of patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  371. en:no auditory brainstem response (abr) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:no auditory brainstem response (abr) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  372. en:no reproducible waves i, iii, or v at high intensities --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:no reproducible waves i, iii, or v at high intensities | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  373. en:nonsyndromic sensorineural hearing loss --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:nonsyndromic sensorineural hearing loss | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  374. en:organ of corti degeneration --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:organ of corti degeneration | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  375. en:otitis externa --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:otitis externa | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  376. en:outer ear abnormalities (deletion patients) prominent ears --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:outer ear abnormalities (deletion patients) prominent ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  377. en:poorly formed pinnae --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:poorly formed pinnae | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  378. en:poorly shaped ears --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:poorly shaped ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  379. en:posteriorly rotated ears (in some patients) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:posteriorly rotated ears (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  380. en:preauricular skin tag --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:preauricular skin tag | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  381. en:prelingual onset --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:prelingual onset | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  382. en:prominent ears (rare) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:prominent ears (rare) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  383. en:prominent lobules --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:prominent lobules | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  384. en:pulsatile tinnitus (tympanic paraganglioma) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:pulsatile tinnitus (tympanic paraganglioma) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  385. en:recurrent otitis --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:recurrent otitis | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  386. en:rudimentary ear --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:rudimentary ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  387. en:sensorineural deafness, variable (in 1 family) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural deafness, variable (in 1 family) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  388. en:sensorineural hearing impairment (in some patients) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural hearing impairment (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  389. en:sensorineural hearing loss, progressive bilateral postlingual --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural hearing loss, progressive bilateral postlingual | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  390. en:short ears (in 1 family) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:short ears (in 1 family) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  391. en:simple ear --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:simple ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  392. en:small earlobe --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:small earlobe | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  393. en:small pits anterior to the helix (1 patient) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:small pits anterior to the helix (1 patient) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  394. en:small, posteriorly rotated ears --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:small, posteriorly rotated ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  395. en:stiff, prominent pinnae --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:stiff, prominent pinnae | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  396. en:strabismus (in some patients) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:strabismus (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  397. en:structural inner ear abnormalities (in patients with larger deletions) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:structural inner ear abnormalities (in patients with larger deletions) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  398. en:tinnitus (in some patients) --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:tinnitus (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  399. en:triangular-shaped ears --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:triangular-shaped ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  400. en:unravelling of superior helices --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:unravelling of superior helices | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  401. en:upsloping audiograms --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:upsloping audiograms | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  402. en:wide, flattened earlobes --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:wide, flattened earlobes | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  403. pavillon de l'oreille de morphologie rudimentaire --- r_associated #0: 29 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=pavillon de l'oreille de morphologie rudimentaire | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=29
  404. en:a subset of patients have hearing loss --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:a subset of patients have hearing loss | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  405. en:abnormal brainstem auditory evoked potentials (baep) --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormal brainstem auditory evoked potentials (baep) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  406. en:abnormal folded pinna --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormal folded pinna | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  407. en:absent distortion product otoacoustic emissions (oaes) --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:absent distortion product otoacoustic emissions (oaes) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  408. en:absent or decreased auditory brainstem responses --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:absent or decreased auditory brainstem responses | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  409. en:affects all frequencies --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:affects all frequencies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  410. en:affects mid- to high-frequencies --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:affects mid- to high-frequencies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  411. en:angular ears --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:angular ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  412. en:asymmetry of the ears --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:asymmetry of the ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  413. en:attached ear lobules --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:attached ear lobules | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  414. en:audiogram is gently sloping or flat --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:audiogram is gently sloping or flat | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  415. en:chronic otitis --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:chronic otitis | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  416. en:conductive hearing loss to due otitis media --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:conductive hearing loss to due otitis media | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  417. en:cystic dilatation of cochlea and vestibulum --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:cystic dilatation of cochlea and vestibulum | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  418. en:deafness, profound congenital sensorineural --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, profound congenital sensorineural | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  419. en:deafness, sensorineural (severe to profound) --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, sensorineural (severe to profound) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  420. en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  421. en:endolymphatic sac tumors (elsts) --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:endolymphatic sac tumors (elsts) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  422. en:excessive cerumen --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:excessive cerumen | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  423. en:external ear defects --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:external ear defects | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  424. en:first branchial arch anomalies --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:first branchial arch anomalies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  425. en:fleshy and overfolded helices --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:fleshy and overfolded helices | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  426. en:hearing impairment, progressive (family a) --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing impairment, progressive (family a) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  427. en:hearing loss (in some patients) --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  428. en:hearing loss first affects high frequencies --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss first affects high frequencies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  429. en:hearing loss, bilateral sensorineural (profound) --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, bilateral sensorineural (profound) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  430. en:hearing loss, congenital profound --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, congenital profound | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  431. en:hearing loss, congenital, profound (250-8,000 hz) --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, congenital, profound (250-8,000 hz) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  432. en:hearing loss, late-onset sensorineural, mild-to moderate (less common) --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, late-onset sensorineural, mild-to moderate (less common) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  433. en:hearing loss, sensorineural (in sister) --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural (in sister) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  434. en:hearing loss, sensorineural and conductive, severe to profound --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural and conductive, severe to profound | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  435. en:hypoplasia of the cochlea --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hypoplasia of the cochlea | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  436. en:hypoplastic semicircular canals --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hypoplastic semicircular canals | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  437. en:hypoplastic superior helix --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hypoplastic superior helix | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  438. en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  439. en:internal auditory canal hypoplasia --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:internal auditory canal hypoplasia | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  440. en:large anteverted pinnae (90% males, 40% females) --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:large anteverted pinnae (90% males, 40% females) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  441. en:large earlobe --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:large earlobe | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  442. en:large prominent ears --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:large prominent ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  443. en:lobular aplasia --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:lobular aplasia | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  444. en:loss of outer hair cell function --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:loss of outer hair cell function | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  445. en:low-set ears (in some patients) --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:low-set ears (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  446. en:malformed ossicular chain --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:malformed ossicular chain | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  447. en:microtia (in some patients) --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:microtia (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  448. en:neonatal cystic lesions of the pinnae --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:neonatal cystic lesions of the pinnae | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  449. en:no hearing loss --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:no hearing loss | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  450. en:no vestibular dysfunction --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:no vestibular dysfunction | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  451. en:nonprogressive --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:nonprogressive | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  452. en:normal outer hair cell functions --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:normal outer hair cell functions | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  453. en:otolaryngologist --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:otolaryngologist | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  454. en:preauricular dimple --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:preauricular dimple | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  455. en:preauricular sinus --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:preauricular sinus | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  456. en:progressive conductive hearing impairment --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:progressive conductive hearing impairment | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  457. en:progressive sensorineural hearing impairment --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:progressive sensorineural hearing impairment | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  458. en:prominent ears (in some patients) --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:prominent ears (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  459. en:recurrent serous otitis --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:recurrent serous otitis | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  460. en:relatively long ears --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:relatively long ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  461. en:severe narrowing of cartilagenous auditory canal --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:severe narrowing of cartilagenous auditory canal | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  462. en:severe narrowing of cartilagenous auditory canal (in homozygotes) --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:severe narrowing of cartilagenous auditory canal (in homozygotes) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  463. en:synotus --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:synotus | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  464. en:tinnitus --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:tinnitus | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  465. en:underfolded helix --- r_associated #0: 28 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:underfolded helix | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=28
  466. en:'tilted' ears --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:'tilted' ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  467. en:abnormal bridge connecting the crus of the helix and antihelix --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormal bridge connecting the crus of the helix and antihelix | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  468. en:abnormal semicircular canals --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormal semicircular canals | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  469. en:abnormal speech discrimination --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormal speech discrimination | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  470. en:abnormally shaped ears (in one family) --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormally shaped ears (in one family) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  471. en:absent auditory canals (wws) --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:absent auditory canals (wws) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  472. en:absent brainstem auditory-evoked responses --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:absent brainstem auditory-evoked responses | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  473. en:absent lobules --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:absent lobules | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  474. en:absent vestibular function (caloric test) --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:absent vestibular function (caloric test) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  475. en:anteriorly displaced ears --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:anteriorly displaced ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  476. en:anteverted pinnae --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:anteverted pinnae | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  477. en:aplasia of the inner ear --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:aplasia of the inner ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  478. en:approximately 0.7db per year hearing loss at all frequencies --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:approximately 0.7db per year hearing loss at all frequencies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  479. en:atrophy of cochlear and vestibular fibrocytes --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:atrophy of cochlear and vestibular fibrocytes | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  480. en:auditory neuropathy spectrum disorder --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:auditory neuropathy spectrum disorder | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  481. en:aural atresia, congenital --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:aural atresia, congenital | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  482. en:cleft at the superior portion of the pinna --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:cleft at the superior portion of the pinna | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  483. en:cochlear malformation defect (mondini dysplasia) (less common) --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:cochlear malformation defect (mondini dysplasia) (less common) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  484. en:conductive and sensorineural hearing loss --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:conductive and sensorineural hearing loss | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  485. en:cutlet --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:cutlet | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  486. en:deafness (variable) --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness (variable) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  487. en:deafness affects all frequencies --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness affects all frequencies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  488. en:deafness, profound, by 6th decade --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, profound, by 6th decade | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  489. en:deafness, sensorineural, mild (rare) --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, sensorineural, mild (rare) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  490. en:deafness, sensorineural, severe to profound affecting all frequencies --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, sensorineural, severe to profound affecting all frequencies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  491. en:deafness, sensorineural, variable --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, sensorineural, variable | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  492. en:decreased auditory brainstem responses --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:decreased auditory brainstem responses | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  493. en:downward sloping or flat audiogram --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:downward sloping or flat audiogram | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  494. en:flat audiogram --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:flat audiogram | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  495. en:hearing complaints (excluding h84-86) --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing complaints (excluding h84-86) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  496. en:hearing impairment (1 patient) --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing impairment (1 patient) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  497. en:hearing impairment (rare) --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing impairment (rare) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  498. en:hearing loss, congenital sensorineural, severe to profound --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, congenital sensorineural, severe to profound | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  499. en:hearing loss, postlingual sensorineural --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, postlingual sensorineural | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  500. en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies) --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  501. en:hearing loss, sensorineural (bilateral, prelingual) --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural (bilateral, prelingual) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  502. en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  503. en:hearing loss, sensorineural, associated with elsts --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural, associated with elsts | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  504. en:high-frequency tinnitus at onset --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:high-frequency tinnitus at onset | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  505. en:impaired tympanic membrane mobility --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:impaired tympanic membrane mobility | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  506. en:inferior displacement of the ears --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:inferior displacement of the ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  507. en:large anteverted ears (rare) --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:large anteverted ears (rare) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  508. en:large ears (in some patients) --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:large ears (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  509. en:long, lobulated ears --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:long, lobulated ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  510. en:michel aplasia (complete absence of inner ear structures) --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:michel aplasia (complete absence of inner ear structures) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  511. en:microtia hearing loss, conductive --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:microtia hearing loss, conductive | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  512. en:mild to moderate hearing loss across most frequencies --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:mild to moderate hearing loss across most frequencies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  513. en:narrow intertragic notch --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:narrow intertragic notch | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  514. en:no vestibular impairment --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:no vestibular impairment | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  515. en:normal otoacoustic emissions (oae), indicating intact outer ear hair cell function --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:normal otoacoustic emissions (oae), indicating intact outer ear hair cell function | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  516. en:normal vestibular response --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:normal vestibular response | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  517. en:ossified pinnae --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:ossified pinnae | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  518. en:other diseases of ear/mastoid --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:other diseases of ear/mastoid | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  519. en:other symptom/complaint of ear --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:other symptom/complaint of ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  520. en:otorhinolaryngologist --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:otorhinolaryngologist | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  521. en:pinna modeling anomalies --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:pinna modeling anomalies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  522. en:preauricular sinus, bilateral --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:preauricular sinus, bilateral | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  523. en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face) --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  524. en:progressive hearing loss (in some) --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:progressive hearing loss (in some) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  525. en:progressive mixed conductive and sensorineural hearing loss --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:progressive mixed conductive and sensorineural hearing loss | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  526. en:prominent antitragus --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:prominent antitragus | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  527. en:protruding ears (rare) --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:protruding ears (rare) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  528. en:retroverted ears --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:retroverted ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  529. en:sensation of blocked ears --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensation of blocked ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  530. en:sensorineural hearing loss (onset early childhood) --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural hearing loss (onset early childhood) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  531. en:sensorineural hearing loss (rare) --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural hearing loss (rare) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  532. en:soft auricles --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:soft auricles | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  533. en:structure of lymphatic vessel of ear --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:structure of lymphatic vessel of ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  534. en:symmetric deterioration of hearing loss and speech reception with age --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:symmetric deterioration of hearing loss and speech reception with age | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  535. en:thick ears --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:thick ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  536. en:unilateral external ear deformity --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:unilateral external ear deformity | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  537. en:uplift of earlobes (in some patients) --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:uplift of earlobes (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  538. en:uplifted earlobes --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:uplifted earlobes | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  539. en:vestibular dysfunction --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:vestibular dysfunction | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  540. hyperlaxe --- r_associated #0: 27 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=hyperlaxe | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=27
  541. en:abnormality of the outer ear --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormality of the outer ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  542. en:air-bone gap of greater than 20 db across 0.5 to 2 khz --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:air-bone gap of greater than 20 db across 0.5 to 2 khz | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  543. en:anteriorly rotated ears --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:anteriorly rotated ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  544. en:atresia of the external auditory canal --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:atresia of the external auditory canal | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  545. en:bilateral dys-synchronized auditory brainstem responses --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:bilateral dys-synchronized auditory brainstem responses | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  546. en:cochlear degeneration --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:cochlear degeneration | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  547. en:deafness (in 1 of 2 families) --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness (in 1 of 2 families) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  548. en:deafness, postlingual --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, postlingual | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  549. en:deafness, secondary to cranial hyperostosis --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, secondary to cranial hyperostosis | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  550. en:dysmorphic ears --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:dysmorphic ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  551. en:eustachian tube salpingitis --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:eustachian tube salpingitis | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  552. en:external auditory canal narrow --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:external auditory canal narrow | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  553. en:external ear --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:external ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  554. en:external ears rudimentary --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:external ears rudimentary | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  555. en:fear of ear disease --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:fear of ear disease | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  556. en:folded helix --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:folded helix | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  557. en:hearing disorder (1 patient) --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing disorder (1 patient) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  558. en:hearing impairment (in 1/4 patients) --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing impairment (in 1/4 patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  559. en:hearing loss (1 patient) --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss (1 patient) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  560. en:hearing loss (uncommon) --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss (uncommon) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  561. en:hearing loss, neural type --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, neural type | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  562. en:hearing loss, postlingual --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, postlingual | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  563. en:hearing loss, profound congenital sensorineural --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, profound congenital sensorineural | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  564. en:hearing loss, progressive sensorineural, affecting high frequencies --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, progressive sensorineural, affecting high frequencies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  565. en:hearing loss, sensorineural (in some patients) --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  566. en:hearing loss, sensorineural, mild progressive (in some patients) --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural, mild progressive (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  567. en:hearing loss, sensorineural, moderate, postlingual --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural, moderate, postlingual | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  568. en:hypoplastic malleus (1 patient) --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hypoplastic malleus (1 patient) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  569. en:incomplete separation of the cochlea from the internal auditory canal --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:incomplete separation of the cochlea from the internal auditory canal | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  570. en:large fleshy earlobes --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:large fleshy earlobes | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  571. en:large fleshy ears --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:large fleshy ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  572. en:large, floppy ears --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:large, floppy ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  573. en:large, low-set ears (uncommon) --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:large, low-set ears (uncommon) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  574. en:large, prominent ears (59%) --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:large, prominent ears (59%) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  575. en:low-set and rotated ears --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:low-set and rotated ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  576. en:low-set ears (in one family) --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:low-set ears (in one family) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  577. en:mild to moderate hearing loss --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:mild to moderate hearing loss | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  578. en:misshapen, small ear --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:misshapen, small ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  579. en:morphological abnormality of the middle ear --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:morphological abnormality of the middle ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  580. en:narrowed external ear canal --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:narrowed external ear canal | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  581. en:neural hearing loss --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:neural hearing loss | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  582. en:normal otoacoustic emissions --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:normal otoacoustic emissions | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  583. en:other auditory injuries --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:other auditory injuries | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  584. en:otorrhea --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:otorrhea | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  585. en:otosclerosis --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:otosclerosis | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  586. en:poorly folded ears --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:poorly folded ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  587. en:postauricular pit --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:postauricular pit | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  588. en:posteriorly rotated ears (female) --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:posteriorly rotated ears (female) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  589. en:preauricular fistulas, bilateral --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:preauricular fistulas, bilateral | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  590. en:preauricular skin tags (in some patients) --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:preauricular skin tags (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  591. en:prominent helices --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:prominent helices | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  592. en:rudimentary --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:rudimentary | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  593. en:sensorineural deafness (onset in the second decade in 25 to 30% of patients) --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural deafness (onset in the second decade in 25 to 30% of patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  594. en:severe to profound deafness --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:severe to profound deafness | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  595. en:severe to profound hearing impairment by early adulthood --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:severe to profound hearing impairment by early adulthood | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  596. en:small cavum conchae --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:small cavum conchae | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  597. en:small external auditory canals --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:small external auditory canals | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  598. en:small triangular pinnae --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:small triangular pinnae | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  599. en:squared-off ears --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:squared-off ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  600. en:superior semicircular canal dehiscence syndrome --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:superior semicircular canal dehiscence syndrome | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  601. en:transient evoked otoacoustic emissions cannot be detected --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:transient evoked otoacoustic emissions cannot be detected | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  602. en:u-shaped audiogram --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:u-shaped audiogram | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  603. en:underdeveloped nasal alae --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:underdeveloped nasal alae | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  604. en:vestibular function defect (decreased in some, normal in other patients) --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:vestibular function defect (decreased in some, normal in other patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  605. en:wide bulbous internal auditory meatus --- r_associated #0: 26 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:wide bulbous internal auditory meatus | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=26
  606. en:anteverted ears --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:anteverted ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  607. en:bleeding from ear --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:bleeding from ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  608. en:blind fistula --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:blind fistula | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  609. en:chronic otitis other infection ear --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:chronic otitis other infection ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  610. en:cochleosaccular dysplasia --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:cochleosaccular dysplasia | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  611. en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  612. en:glue ear --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:glue ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  613. en:hearing impairment, sensorineural, mild --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing impairment, sensorineural, mild | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  614. en:hearing loss begins with loss of high frequencies --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss begins with loss of high frequencies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  615. en:hearing loss, conductive (in one family) --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, conductive (in one family) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  616. en:hearing loss, mild --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, mild | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  617. en:hearing loss, sensorineural (high frequency) --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural (high frequency) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  618. en:hearing loss, sensorineural (in 1 ashkenazi patient) --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural (in 1 ashkenazi patient) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  619. en:hearing loss, sensorineural, mid-frequency (in some patients) --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural, mid-frequency (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  620. en:hearing loss, sensorineural, progressive (childhood-onset) --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural, progressive (childhood-onset) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  621. en:hearing loss, unilateral or bilateral, conductive, sensorineural, or mixed --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, unilateral or bilateral, conductive, sensorineural, or mixed | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  622. en:hypoplasia of the upper part of the helix --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hypoplasia of the upper part of the helix | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  623. en:increased posterior angulation --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:increased posterior angulation | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  624. en:large pinnae --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:large pinnae | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  625. en:limited auditory function --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:limited auditory function | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  626. en:long ear --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:long ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  627. en:loss of vestibular reflexes --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:loss of vestibular reflexes | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  628. en:meniere disease --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:meniere disease | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  629. en:microtia (wws) --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:microtia (wws) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  630. en:narrowing of ear canal --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:narrowing of ear canal | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  631. en:otitis media, recurrent (rare) --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:otitis media, recurrent (rare) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  632. en:overfolding of the superior helices --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:overfolding of the superior helices | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  633. en:posteriorly rotated ear --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:posteriorly rotated ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  634. en:posteriorly rotated ears (1/4 patients) --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:posteriorly rotated ears (1/4 patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  635. en:presbycusis --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:presbycusis | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  636. en:progressive high-frequency hearing loss (onset 20-30 years) --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:progressive high-frequency hearing loss (onset 20-30 years) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  637. en:recurrent otitis media in infancy --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:recurrent otitis media in infancy | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  638. en:roll-head --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:roll-head | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  639. en:slit-like opening of the exterior auditory meatus --- r_associated #0: 25 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:slit-like opening of the exterior auditory meatus | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=25
  640. en:abnormal amplitude modulation detection --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormal amplitude modulation detection | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  641. en:acute otitis media/myringitis --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:acute otitis media/myringitis | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  642. en:auriculo-condylar syndrome --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:auriculo-condylar syndrome | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  643. en:bat ear --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:bat ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  644. en:congenital ear anomaly nos (disorder) --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:congenital ear anomaly nos (disorder) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  645. en:congenital small ears --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:congenital small ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  646. en:deep-set ears --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deep-set ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  647. en:disjunction of otherwise normal lobule from remainder of ear --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:disjunction of otherwise normal lobule from remainder of ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  648. en:disturbance of equilibrium --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:disturbance of equilibrium | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  649. en:downsloping audiogram --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:downsloping audiogram | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  650. en:hearing impairment (in some patients) --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing impairment (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  651. en:hearing impairment may occur --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing impairment may occur | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  652. en:hearing impairment, mild (2 patients) --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing impairment, mild (2 patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  653. en:hearing loss, sensorineural (in some cases) --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural (in some cases) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  654. en:hearing loss, sensorineural, severe to profound --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural, severe to profound | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  655. en:hearing threshold at or above 90 db at all frequencies tested (0.25-8.0 khz) --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing threshold at or above 90 db at all frequencies tested (0.25-8.0 khz) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  656. en:large, dysmorphic ears --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:large, dysmorphic ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  657. en:left ear --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:left ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  658. en:macrotia --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:macrotia | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  659. en:near-stenosis of bony portion of auditory canal --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:near-stenosis of bony portion of auditory canal | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  660. en:no auditory brainstem response to 100-db stimulus --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:no auditory brainstem response to 100-db stimulus | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  661. en:no hearing impairment --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:no hearing impairment | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  662. en:otitis with effusion --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:otitis with effusion | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  663. en:partial aplasia of external auditory canal ending in blind fistula (in some patients) --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:partial aplasia of external auditory canal ending in blind fistula (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  664. en:preauricular pits (70-80% of patients) --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:preauricular pits (70-80% of patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  665. en:progressive hearing impairment --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:progressive hearing impairment | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  666. en:right ear --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:right ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  667. en:sensorineural deafness, progressive, late-onset --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural deafness, progressive, late-onset | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  668. en:sensorineural hearing loss (males only) --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural hearing loss (males only) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  669. en:small/rudimentary tragus, antitragus and lobule --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:small/rudimentary tragus, antitragus and lobule | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  670. en:tinnitus (variable) --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:tinnitus (variable) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  671. en:vertiginous syndrome --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:vertiginous syndrome | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  672. en:vertigo, single occurrence (in 2 patients) --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:vertigo, single occurrence (in 2 patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  673. en:vestibular areflexia, complete --- r_associated #0: 24 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:vestibular areflexia, complete | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=24
  674. en:cochlear malformation --- r_associated #0: 23 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:cochlear malformation | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=23
  675. en:conductive hearing loss, bilateral --- r_associated #0: 23 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:conductive hearing loss, bilateral | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=23
  676. en:congenital absence of external ear --- r_associated #0: 23 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:congenital absence of external ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=23
  677. en:congenital secretory diarrhea, sodium type (disorder) --- r_associated #0: 23 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:congenital secretory diarrhea, sodium type (disorder) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=23
  678. en:deafness (sensorineural or mixed sensorineural and conductive) --- r_associated #0: 23 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness (sensorineural or mixed sensorineural and conductive) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=23
  679. en:dysplastic ears (in some patients) --- r_associated #0: 23 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:dysplastic ears (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=23
  680. en:expansion of helical fold at superior point of true longitudinal axis of ear --- r_associated #0: 23 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:expansion of helical fold at superior point of true longitudinal axis of ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=23
  681. en:hearing loss (variable) --- r_associated #0: 23 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss (variable) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=23
  682. en:hearing loss, sensorineural (variable) --- r_associated #0: 23 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural (variable) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=23
  683. en:incomplete atretic plate --- r_associated #0: 23 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:incomplete atretic plate | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=23
  684. en:inner ear --- r_associated #0: 23 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:inner ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=23
  685. en:large appearing ears --- r_associated #0: 23 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:large appearing ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=23
  686. en:loss of high frequencies at onset --- r_associated #0: 23 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:loss of high frequencies at onset | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=23
  687. en:low-set ears (3 patients) --- r_associated #0: 23 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:low-set ears (3 patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=23
  688. en:mild cochlear hearing loss (1 patient) --- r_associated #0: 23 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:mild cochlear hearing loss (1 patient) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=23
  689. en:narrow ears --- r_associated #0: 23 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:narrow ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=23
  690. en:phonophobia --- r_associated #0: 23 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:phonophobia | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=23
  691. en:protruding right ear --- r_associated #0: 23 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:protruding right ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=23
  692. en:vestibular hyporeflexia --- r_associated #0: 23 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:vestibular hyporeflexia | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=23
  693. en:absent earlobe --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:absent earlobe | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  694. en:accessory tragus --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:accessory tragus | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  695. en:bilateral congenital profound sensorineural hearing loss --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:bilateral congenital profound sensorineural hearing loss | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  696. en:concern with appearance of ears --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:concern with appearance of ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  697. en:deafness --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  698. en:deafness, prelingual, profound (affects all frequencies) --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, prelingual, profound (affects all frequencies) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  699. en:deafness, sensorineural (in some patients) --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness, sensorineural (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  700. en:ear dimple --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:ear dimple | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  701. en:ear neoplasm --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:ear neoplasm | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  702. en:endolymphatic hydrops, delayed onset --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:endolymphatic hydrops, delayed onset | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  703. en:hearing deficits (28% of adults) --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing deficits (28% of adults) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  704. en:hearing loss, conductive (rare) --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, conductive (rare) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  705. en:hearing loss, mixed, mild to severe (in heterozygotes) --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, mixed, mild to severe (in heterozygotes) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  706. en:hearing loss, postlingual progressive sensorineural --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, postlingual progressive sensorineural | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  707. en:hearing loss, prelingual, severe to profound (affecting all frequencies) --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, prelingual, severe to profound (affecting all frequencies) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  708. en:large auricle --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:large auricle | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  709. en:narrow external ear canals (1 patient) --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:narrow external ear canals (1 patient) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  710. en:otitis media --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:otitis media | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  711. en:overfolded, rumpled ears --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:overfolded, rumpled ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  712. en:progressive cartilaginous ossification of pinnae --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:progressive cartilaginous ossification of pinnae | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  713. en:protruding ears --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:protruding ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  714. en:recurrent otitis media --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:recurrent otitis media | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  715. en:serous otitis --- r_associated #0: 22 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:serous otitis | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=22
  716. en:abnormal helices, antihelices and lobules --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormal helices, antihelices and lobules | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  717. en:abnormal middle ear reflexes --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:abnormal middle ear reflexes | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  718. en:absent ipsilateral middle ear muscle reflexes (in older patients) --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:absent ipsilateral middle ear muscle reflexes (in older patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  719. en:congenital atresia of external auditory canal --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:congenital atresia of external auditory canal | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  720. en:deafness in 30-50% of patients with skull involvement --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deafness in 30-50% of patients with skull involvement | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  721. en:ear constriction (97%) --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:ear constriction (97%) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  722. en:ear part --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:ear part | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  723. en:enlarged vestibular aqueduct --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:enlarged vestibular aqueduct | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  724. en:flat or shallow u-shaped audiogram --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:flat or shallow u-shaped audiogram | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  725. en:flattened --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:flattened | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  726. en:foreign body in auditory canal --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:foreign body in auditory canal | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  727. en:hearing loss, bilateral progressive post-lingual --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, bilateral progressive post-lingual | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  728. en:hearing loss, high-frequency (onset in childhood-adolescence) --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, high-frequency (onset in childhood-adolescence) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  729. en:hearing loss, moderate to severe, bilateral, nonprogressive --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, moderate to severe, bilateral, nonprogressive | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  730. en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges) --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  731. en:hypoacusia (1 patient) --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hypoacusia (1 patient) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  732. en:hypoplastic pinnae (30-60% of patients) --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hypoplastic pinnae (30-60% of patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  733. en:linear ear lobe creases --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:linear ear lobe creases | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  734. en:low-set, posteriorly rotated ears --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:low-set, posteriorly rotated ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  735. en:mixed hearing loss --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:mixed hearing loss | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  736. en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  737. en:mondini defect --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:mondini defect | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  738. en:prominent crura --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:prominent crura | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  739. en:prominent earlobes (in some patients) --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:prominent earlobes (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  740. en:retinitis (in some patients) --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:retinitis (in some patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  741. en:sensorineural hearing loss (20% of patients) --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural hearing loss (20% of patients) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  742. en:sensorineural hearing loss has been reported --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:sensorineural hearing loss has been reported | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  743. en:shallow skin dimple on posterior surface of ear --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:shallow skin dimple on posterior surface of ear | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  744. en:vestibular anomalies (less common) --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:vestibular anomalies (less common) | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  745. esgourde --- r_associated #0: 21 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=esgourde | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=21
  746. Trouble de l'équilibre --- r_associated #0: 15 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=Trouble de l'équilibre | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=15
  747. en:dizzy spells --- r_associated #0: 15 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:dizzy spells | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=15
  748. en:giddiness --- r_associated #0: 15 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:giddiness | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=15
  749. en:scatterbrain --- r_associated #0: 15 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:scatterbrain | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=15
  750. vertiges --- r_associated #0: 15 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=vertiges | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=15
  751. vertigineux --- r_associated #0: 15 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=vertigineux | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=15
  752. Étourdi --- r_associated #0: 15 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=Étourdi | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=15
  753. Étourdie --- r_associated #0: 15 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=Étourdie | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=15
  754. étourdie --- r_associated #0: 15 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=étourdie | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=15
  755. étourdies --- r_associated #0: 15 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=étourdies | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=15
  756. étourdis --- r_associated #0: 15 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=étourdis | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=15
  757. étourdissements --- r_associated #0: 15 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=étourdissements | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=15
  758. Hyperacousie --- r_associated #0: 10 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=Hyperacousie | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=10
  759. Oto-rhino-laryngologiste --- r_associated #0: 10 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=Oto-rhino-laryngologiste | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=10
  760. Otorhinolaryngologiste --- r_associated #0: 10 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=Otorhinolaryngologiste | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=10
  761. ankylose stapédo-vestibulaire --- r_associated #0: 10 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=ankylose stapédo-vestibulaire | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=10
  762. ankylose stapédo-vestibulaire l.f. --- r_associated #0: 10 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=ankylose stapédo-vestibulaire l.f. | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=10
  763. aplati --- r_associated #0: 10 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=aplati | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=10
  764. en:deaf-muteness --- r_associated #0: 10 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deaf-muteness | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=10
  765. en:deaf-mutism --- r_associated #0: 10 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:deaf-mutism | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=10
  766. en:hearing defect --- r_associated #0: 10 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing defect | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=10
  767. en:hearing deficiency --- r_associated #0: 10 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:hearing deficiency | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=10
  768. en:lughole --- r_associated #0: 10 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:lughole | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=10
  769. en:schitzel --- r_associated #0: 10 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:schitzel | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=10
  770. en:speech difficulties due to deafness --- r_associated #0: 10 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=en:speech difficulties due to deafness | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=10
  771. oreille moyenne --- r_associated #0: 10 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=oreille moyenne | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=10
  772. otite moyenne adhésive --- r_associated #0: 10 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=otite moyenne adhésive | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=10
  773. surdité --- r_associated #0: 10 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=surdité | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=10
  774. tête de linotte --- r_associated #0: 10 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=tête de linotte | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=10
  775. Étourdissements --- r_associated #0: 10 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=Étourdissements | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=10
  776. à priori --- r_associated #0: 10 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=à priori | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=10
  777. Sensation de rotation --- r_associated #0: 5 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=Sensation de rotation | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=5
  778. escalope --- r_associated #0: -20 --> en:deafness due to bilateral cochlear malformation (rare)
    n1=escalope | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=-20
Le service Rézo permet d'énumérer les relations existant pour un terme. Ce service est interrogeable par programme.
Projet JeuxDeMots - url: http://www.jeuxdemots.org
contact: mathieu.lafourcade@lirmm.fr