'en:everted ears'
(id=6815176 ; fe=en:everted ears ; type=1 ; niveau=200 ;
luminosité=25 ;
somme entrante=27295 creation date=2017-06-25 touchdate=2025-10-08 08:51:21.000) ≈ 741 relations sortantes
- en:everted ears --
r_associated #0: 43 / 1 ->
en:absent cochlear microphonic (in older patients)
n1=en:everted ears | n2=en:absent cochlear microphonic (in older patients) | rel=r_associated | relid=0 | w=43
- en:everted ears --
r_associated #0: 43 / 1 ->
en:small external auditory meatus
n1=en:everted ears | n2=en:small external auditory meatus | rel=r_associated | relid=0 | w=43
- en:everted ears --
r_associated #0: 42 / 0.977 ->
en:atretic auditory canal
n1=en:everted ears | n2=en:atretic auditory canal | rel=r_associated | relid=0 | w=42
- en:everted ears --
r_associated #0: 42 / 0.977 ->
en:mixed hearing loss (50% of patients)
n1=en:everted ears | n2=en:mixed hearing loss (50% of patients) | rel=r_associated | relid=0 | w=42
- en:everted ears --
r_associated #0: 42 / 0.977 ->
en:mondini defect
n1=en:everted ears | n2=en:mondini defect | rel=r_associated | relid=0 | w=42
- en:everted ears --
r_associated #0: 42 / 0.977 ->
en:preauricular fistulas, bilateral
n1=en:everted ears | n2=en:preauricular fistulas, bilateral | rel=r_associated | relid=0 | w=42
- en:everted ears --
r_associated #0: 42 / 0.977 ->
en:severe to profound deafness
n1=en:everted ears | n2=en:severe to profound deafness | rel=r_associated | relid=0 | w=42
- en:everted ears --
r_associated #0: 41 / 0.953 ->
en:aplasia of the inner ear
n1=en:everted ears | n2=en:aplasia of the inner ear | rel=r_associated | relid=0 | w=41
- en:everted ears --
r_associated #0: 41 / 0.953 ->
en:congenital ear anomaly nos (disorder)
n1=en:everted ears | n2=en:congenital ear anomaly nos (disorder) | rel=r_associated | relid=0 | w=41
- en:everted ears --
r_associated #0: 41 / 0.953 ->
en:fear of ear disease
n1=en:everted ears | n2=en:fear of ear disease | rel=r_associated | relid=0 | w=41
- en:everted ears --
r_associated #0: 41 / 0.953 ->
en:mild to moderate hearing loss
n1=en:everted ears | n2=en:mild to moderate hearing loss | rel=r_associated | relid=0 | w=41
- en:everted ears --
r_associated #0: 41 / 0.953 ->
en:sensorineural hearing loss, mild to moderate
n1=en:everted ears | n2=en:sensorineural hearing loss, mild to moderate | rel=r_associated | relid=0 | w=41
- en:everted ears --
r_associated #0: 40 / 0.93 ->
en:abnormal auditory brainstem responses
n1=en:everted ears | n2=en:abnormal auditory brainstem responses | rel=r_associated | relid=0 | w=40
- en:everted ears --
r_associated #0: 40 / 0.93 ->
en:abnormal auricles
n1=en:everted ears | n2=en:abnormal auricles | rel=r_associated | relid=0 | w=40
- en:everted ears --
r_associated #0: 40 / 0.93 ->
en:abnormal helices, antihelices and lobules
n1=en:everted ears | n2=en:abnormal helices, antihelices and lobules | rel=r_associated | relid=0 | w=40
- en:everted ears --
r_associated #0: 40 / 0.93 ->
en:audiogram may be ascending
n1=en:everted ears | n2=en:audiogram may be ascending | rel=r_associated | relid=0 | w=40
- en:everted ears --
r_associated #0: 40 / 0.93 ->
en:hypoplasia of the cochlea
n1=en:everted ears | n2=en:hypoplasia of the cochlea | rel=r_associated | relid=0 | w=40
- en:everted ears --
r_associated #0: 40 / 0.93 ->
en:pinna modeling anomalies
n1=en:everted ears | n2=en:pinna modeling anomalies | rel=r_associated | relid=0 | w=40
- en:everted ears --
r_associated #0: 40 / 0.93 ->
en:protruding ears
n1=en:everted ears | n2=en:protruding ears | rel=r_associated | relid=0 | w=40
- en:everted ears --
r_associated #0: 40 / 0.93 ->
en:stenotic ear canals (30%)
n1=en:everted ears | n2=en:stenotic ear canals (30%) | rel=r_associated | relid=0 | w=40
- en:everted ears --
r_associated #0: 40 / 0.93 ->
en:superior semicircular canal dehiscence syndrome
n1=en:everted ears | n2=en:superior semicircular canal dehiscence syndrome | rel=r_associated | relid=0 | w=40
- en:everted ears --
r_associated #0: 40 / 0.93 ->
en:vertigo, single occurrence (in 2 patients)
n1=en:everted ears | n2=en:vertigo, single occurrence (in 2 patients) | rel=r_associated | relid=0 | w=40
- en:everted ears --
r_associated #0: 39 / 0.907 ->
en:audiogram shows sloping configuration
n1=en:everted ears | n2=en:audiogram shows sloping configuration | rel=r_associated | relid=0 | w=39
- en:everted ears --
r_associated #0: 39 / 0.907 ->
en:no vestibular dysfunction
n1=en:everted ears | n2=en:no vestibular dysfunction | rel=r_associated | relid=0 | w=39
- en:everted ears --
r_associated #0: 39 / 0.907 ->
en:sensorineural deafness, postlingual, progressive
n1=en:everted ears | n2=en:sensorineural deafness, postlingual, progressive | rel=r_associated | relid=0 | w=39
- en:everted ears --
r_associated #0: 38 / 0.884 ->
en:anteverted pinnae
n1=en:everted ears | n2=en:anteverted pinnae | rel=r_associated | relid=0 | w=38
- en:everted ears --
r_associated #0: 38 / 0.884 ->
en:deafness due to bilateral cochlear malformation (rare)
n1=en:everted ears | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=38
- en:everted ears --
r_associated #0: 37 / 0.86 ->
en:auditory neuropathy spectrum disorder
n1=en:everted ears | n2=en:auditory neuropathy spectrum disorder | rel=r_associated | relid=0 | w=37
- en:everted ears --
r_associated #0: 37 / 0.86 ->
en:ear cartilage calcification
n1=en:everted ears | n2=en:ear cartilage calcification | rel=r_associated | relid=0 | w=37
- en:everted ears --
r_associated #0: 37 / 0.86 ->
en:hearing loss, mixed (in some patients)
n1=en:everted ears | n2=en:hearing loss, mixed (in some patients) | rel=r_associated | relid=0 | w=37
- en:everted ears --
r_associated #0: 37 / 0.86 ->
en:hearing loss, prelingual, severe to profound (affecting all frequencies)
n1=en:everted ears | n2=en:hearing loss, prelingual, severe to profound (affecting all frequencies) | rel=r_associated | relid=0 | w=37
- en:everted ears --
r_associated #0: 37 / 0.86 ->
en:large auricle
n1=en:everted ears | n2=en:large auricle | rel=r_associated | relid=0 | w=37
- en:everted ears --
r_associated #0: 36 / 0.837 ->
en:absence of the helix and distal scapha in middle third of the ear
n1=en:everted ears | n2=en:absence of the helix and distal scapha in middle third of the ear | rel=r_associated | relid=0 | w=36
- en:everted ears --
r_associated #0: 36 / 0.837 ->
en:cochlear degeneration
n1=en:everted ears | n2=en:cochlear degeneration | rel=r_associated | relid=0 | w=36
- en:everted ears --
r_associated #0: 36 / 0.837 ->
en:dysplastic helices
n1=en:everted ears | n2=en:dysplastic helices | rel=r_associated | relid=0 | w=36
- en:everted ears --
r_associated #0: 36 / 0.837 ->
en:external auditory canal narrow
n1=en:everted ears | n2=en:external auditory canal narrow | rel=r_associated | relid=0 | w=36
- en:everted ears --
r_associated #0: 36 / 0.837 ->
en:low-set, posteriorly rotated ears
n1=en:everted ears | n2=en:low-set, posteriorly rotated ears | rel=r_associated | relid=0 | w=36
- en:everted ears --
r_associated #0: 36 / 0.837 ->
en:recurrent otitis media in infancy and childhood
n1=en:everted ears | n2=en:recurrent otitis media in infancy and childhood | rel=r_associated | relid=0 | w=36
- en:everted ears --
r_associated #0: 36 / 0.837 ->
en:superficial injury of ear
n1=en:everted ears | n2=en:superficial injury of ear | rel=r_associated | relid=0 | w=36
- en:everted ears --
r_associated #0: 36 / 0.837 ->
en:tinnitus (variable)
n1=en:everted ears | n2=en:tinnitus (variable) | rel=r_associated | relid=0 | w=36
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:absence of the cochlear nerves (reported in 1 patient)
n1=en:everted ears | n2=en:absence of the cochlear nerves (reported in 1 patient) | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:absent or abnormal otoacoustic emissions
n1=en:everted ears | n2=en:absent or abnormal otoacoustic emissions | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:affects all frequencies
n1=en:everted ears | n2=en:affects all frequencies | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:approximately 0.7db per year hearing loss at all frequencies
n1=en:everted ears | n2=en:approximately 0.7db per year hearing loss at all frequencies | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:atretic ear canals
n1=en:everted ears | n2=en:atretic ear canals | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:attached ear lobes
n1=en:everted ears | n2=en:attached ear lobes | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:cleft at the superior portion of the pinna
n1=en:everted ears | n2=en:cleft at the superior portion of the pinna | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:deafness (often in third decade)
n1=en:everted ears | n2=en:deafness (often in third decade) | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:deafness, bilateral sensorineural, high frequency (100% of patients)
n1=en:everted ears | n2=en:deafness, bilateral sensorineural, high frequency (100% of patients) | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:deafness, congenital nonprogressive sensorineural symmetric, moderate
n1=en:everted ears | n2=en:deafness, congenital nonprogressive sensorineural symmetric, moderate | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:deafness, prelingual, profound (affects all frequencies)
n1=en:everted ears | n2=en:deafness, prelingual, profound (affects all frequencies) | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:deafness, sensorineural, especially affecting high frequencies
n1=en:everted ears | n2=en:deafness, sensorineural, especially affecting high frequencies | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:deafness, sensorineural, profound (prelingual onset)
n1=en:everted ears | n2=en:deafness, sensorineural, profound (prelingual onset) | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:deafness, sensorineural, variable
n1=en:everted ears | n2=en:deafness, sensorineural, variable | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:disproportionately large ears
n1=en:everted ears | n2=en:disproportionately large ears | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:dorsally rotated ears
n1=en:everted ears | n2=en:dorsally rotated ears | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:dysmorphic ears
n1=en:everted ears | n2=en:dysmorphic ears | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:ear constriction (97%)
n1=en:everted ears | n2=en:ear constriction (97%) | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:ear dimple
n1=en:everted ears | n2=en:ear dimple | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:earlobe pits
n1=en:everted ears | n2=en:earlobe pits | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:enlarged vestibular aqueduct
n1=en:everted ears | n2=en:enlarged vestibular aqueduct | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:first branchial arch anomalies
n1=en:everted ears | n2=en:first branchial arch anomalies | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:hearing impairment (rare)
n1=en:everted ears | n2=en:hearing impairment (rare) | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:hearing loss (in some patients)
n1=en:everted ears | n2=en:hearing loss (in some patients) | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:hearing loss, bilateral
n1=en:everted ears | n2=en:hearing loss, bilateral | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:hearing loss, conductive or mixed
n1=en:everted ears | n2=en:hearing loss, conductive or mixed | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:hearing loss, congenital profound
n1=en:everted ears | n2=en:hearing loss, congenital profound | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:hearing loss, initially conductive, later mixed conductive-sensorineural
n1=en:everted ears | n2=en:hearing loss, initially conductive, later mixed conductive-sensorineural | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:hearing loss, profound congenital sensorineural
n1=en:everted ears | n2=en:hearing loss, profound congenital sensorineural | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:hearing loss, sensorineural (high frequency)
n1=en:everted ears | n2=en:hearing loss, sensorineural (high frequency) | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:hearing loss, sensorineural (in some)
n1=en:everted ears | n2=en:hearing loss, sensorineural (in some) | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:hearing loss, sensorineural (reported in 1 patient)
n1=en:everted ears | n2=en:hearing loss, sensorineural (reported in 1 patient) | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:hearing loss, sensorineural, moderate, postlingual
n1=en:everted ears | n2=en:hearing loss, sensorineural, moderate, postlingual | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:hearing loss, unilateral or bilateral, conductive, sensorineural, or mixed
n1=en:everted ears | n2=en:hearing loss, unilateral or bilateral, conductive, sensorineural, or mixed | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:hearing loss, unilateral, mild
n1=en:everted ears | n2=en:hearing loss, unilateral, mild | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:hearing normal
n1=en:everted ears | n2=en:hearing normal | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:hypoplastic superior helix
n1=en:everted ears | n2=en:hypoplastic superior helix | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:increased posterior angulation
n1=en:everted ears | n2=en:increased posterior angulation | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:inferior displacement of the ears
n1=en:everted ears | n2=en:inferior displacement of the ears | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:large anteverted ears (rare)
n1=en:everted ears | n2=en:large anteverted ears (rare) | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:large ears (2p21del)
n1=en:everted ears | n2=en:large ears (2p21del) | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:large fleshy earlobes
n1=en:everted ears | n2=en:large fleshy earlobes | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:large, prominent ears (59%)
n1=en:everted ears | n2=en:large, prominent ears (59%) | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:limited auditory function
n1=en:everted ears | n2=en:limited auditory function | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:low-set ears (3 patients)
n1=en:everted ears | n2=en:low-set ears (3 patients) | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:mild to moderate hearing loss across most frequencies
n1=en:everted ears | n2=en:mild to moderate hearing loss across most frequencies | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:narrow ear lobes
n1=en:everted ears | n2=en:narrow ear lobes | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:narrow intertragic notch
n1=en:everted ears | n2=en:narrow intertragic notch | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:no deafness
n1=en:everted ears | n2=en:no deafness | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:no vestibular impairment
n1=en:everted ears | n2=en:no vestibular impairment | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:nonsyndromic sensorineural hearing loss
n1=en:everted ears | n2=en:nonsyndromic sensorineural hearing loss | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:normal otoacoustic emissions
n1=en:everted ears | n2=en:normal otoacoustic emissions | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:other auditory injuries
n1=en:everted ears | n2=en:other auditory injuries | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:other symptom/complaint of ear
n1=en:everted ears | n2=en:other symptom/complaint of ear | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:otitis externa, recurrent, due to infection with staphylococcus aureus
n1=en:everted ears | n2=en:otitis externa, recurrent, due to infection with staphylococcus aureus | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:otorrhea
n1=en:everted ears | n2=en:otorrhea | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:pointed upper helix
n1=en:everted ears | n2=en:pointed upper helix | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:poorly folded ears
n1=en:everted ears | n2=en:poorly folded ears | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:progressive cartilaginous ossification of pinnae
n1=en:everted ears | n2=en:progressive cartilaginous ossification of pinnae | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:progressive mixed conductive and sensorineural hearing loss
n1=en:everted ears | n2=en:progressive mixed conductive and sensorineural hearing loss | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:prominent ears (in some patients)
n1=en:everted ears | n2=en:prominent ears (in some patients) | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:prominent lobules
n1=en:everted ears | n2=en:prominent lobules | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:recurrent otitis media (18%)
n1=en:everted ears | n2=en:recurrent otitis media (18%) | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:retroverted ears
n1=en:everted ears | n2=en:retroverted ears | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:rotated ears
n1=en:everted ears | n2=en:rotated ears | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:rudimentary ear
n1=en:everted ears | n2=en:rudimentary ear | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:sensorineural hearing loss (males only)
n1=en:everted ears | n2=en:sensorineural hearing loss (males only) | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:sensorineural hearing loss (uncommon)
n1=en:everted ears | n2=en:sensorineural hearing loss (uncommon) | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:simple auricles
n1=en:everted ears | n2=en:simple auricles | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:small cavum conchae
n1=en:everted ears | n2=en:small cavum conchae | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:small ears with large lobules
n1=en:everted ears | n2=en:small ears with large lobules | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:structure of lymphatic vessel of ear
n1=en:everted ears | n2=en:structure of lymphatic vessel of ear | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:supraauricular pit
n1=en:everted ears | n2=en:supraauricular pit | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:transient evoked otoacoustic emissions cannot be detected
n1=en:everted ears | n2=en:transient evoked otoacoustic emissions cannot be detected | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 35 / 0.814 ->
en:vestibular hypofunction
n1=en:everted ears | n2=en:vestibular hypofunction | rel=r_associated | relid=0 | w=35
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:abnormal brainstem auditory evoked potentials (baep)
n1=en:everted ears | n2=en:abnormal brainstem auditory evoked potentials (baep) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:abnormal semicircular canals
n1=en:everted ears | n2=en:abnormal semicircular canals | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:abnormality of the helix
n1=en:everted ears | n2=en:abnormality of the helix | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:abnormality of the middle ear
n1=en:everted ears | n2=en:abnormality of the middle ear | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:absent stapedial reflexes or intraoperative stapes immobility
n1=en:everted ears | n2=en:absent stapedial reflexes or intraoperative stapes immobility | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:affects mid- to high-frequencies
n1=en:everted ears | n2=en:affects mid- to high-frequencies | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:audiogram is gently sloping or flat
n1=en:everted ears | n2=en:audiogram is gently sloping or flat | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:aural atresia, congenital
n1=en:everted ears | n2=en:aural atresia, congenital | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:bilateral congenital profound sensorineural hearing loss
n1=en:everted ears | n2=en:bilateral congenital profound sensorineural hearing loss | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:cleft lobules
n1=en:everted ears | n2=en:cleft lobules | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:conductive hearing loss, bilateral
n1=en:everted ears | n2=en:conductive hearing loss, bilateral | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:cup-shaped ears (30-60% of patients)
n1=en:everted ears | n2=en:cup-shaped ears (30-60% of patients) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:cupped ears (finding)
n1=en:everted ears | n2=en:cupped ears (finding) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:cystic dilatation of cochlea and vestibulum
n1=en:everted ears | n2=en:cystic dilatation of cochlea and vestibulum | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:deafness in 30-50% of patients with skull involvement
n1=en:everted ears | n2=en:deafness in 30-50% of patients with skull involvement | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years
n1=en:everted ears | n2=en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:deafness, congenital sensorineural, profound (in some patients)
n1=en:everted ears | n2=en:deafness, congenital sensorineural, profound (in some patients) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:deafness, nonprogressive, moderate
n1=en:everted ears | n2=en:deafness, nonprogressive, moderate | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:deafness, sensorineural (45%)
n1=en:everted ears | n2=en:deafness, sensorineural (45%) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:downward sloping audiogram
n1=en:everted ears | n2=en:downward sloping audiogram | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:ear
n1=en:everted ears | n2=en:ear | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:eustachian tube salpingitis
n1=en:everted ears | n2=en:eustachian tube salpingitis | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:external ears rudimentary
n1=en:everted ears | n2=en:external ears rudimentary | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:flattened
n1=en:everted ears | n2=en:flattened | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:flattened antihelix
n1=en:everted ears | n2=en:flattened antihelix | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:fleshy and overfolded helices
n1=en:everted ears | n2=en:fleshy and overfolded helices | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hearing impairment
n1=en:everted ears | n2=en:hearing impairment | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hearing loss (affecting all frequencies), moderate to severe
n1=en:everted ears | n2=en:hearing loss (affecting all frequencies), moderate to severe | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hearing loss (uncommon)
n1=en:everted ears | n2=en:hearing loss (uncommon) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hearing loss affects all frequencies
n1=en:everted ears | n2=en:hearing loss affects all frequencies | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hearing loss has been reported in some adults with severe disease
n1=en:everted ears | n2=en:hearing loss has been reported in some adults with severe disease | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hearing loss, bilateral progressive post-lingual
n1=en:everted ears | n2=en:hearing loss, bilateral progressive post-lingual | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hearing loss, conductive (in one family)
n1=en:everted ears | n2=en:hearing loss, conductive (in one family) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hearing loss, conductive (in some patients)
n1=en:everted ears | n2=en:hearing loss, conductive (in some patients) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hearing loss, conductive (rare)
n1=en:everted ears | n2=en:hearing loss, conductive (rare) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hearing loss, moderate to severe, bilateral, nonprogressive
n1=en:everted ears | n2=en:hearing loss, moderate to severe, bilateral, nonprogressive | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hearing loss, postlingual progressive sensorineural
n1=en:everted ears | n2=en:hearing loss, postlingual progressive sensorineural | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hearing loss, prelingual sensorineural, moderate to severe
n1=en:everted ears | n2=en:hearing loss, prelingual sensorineural, moderate to severe | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies)
n1=en:everted ears | n2=en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hearing loss, sensorineural (in sister)
n1=en:everted ears | n2=en:hearing loss, sensorineural (in sister) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hearing loss, sensorineural (variable)
n1=en:everted ears | n2=en:hearing loss, sensorineural (variable) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hearing loss, sensorineural and conductive, severe to profound
n1=en:everted ears | n2=en:hearing loss, sensorineural and conductive, severe to profound | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:everted ears | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges)
n1=en:everted ears | n2=en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hearing loss, sensorineural, due to auditory neuropathy
n1=en:everted ears | n2=en:hearing loss, sensorineural, due to auditory neuropathy | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hearing loss, sensorineural, mid-frequency (in some patients)
n1=en:everted ears | n2=en:hearing loss, sensorineural, mid-frequency (in some patients) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hearing loss, unilateral (rare)
n1=en:everted ears | n2=en:hearing loss, unilateral (rare) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hyperfolded ears
n1=en:everted ears | n2=en:hyperfolded ears | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:hypoplastic malleus (1 patient)
n1=en:everted ears | n2=en:hypoplastic malleus (1 patient) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:impaired tympanic membrane mobility
n1=en:everted ears | n2=en:impaired tympanic membrane mobility | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:large anteverted pinnae (90% males, 40% females)
n1=en:everted ears | n2=en:large anteverted pinnae (90% males, 40% females) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:lobule may be separately from the rest of the external ear
n1=en:everted ears | n2=en:lobule may be separately from the rest of the external ear | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:low-frequency sensorineural hearing impairment
n1=en:everted ears | n2=en:low-frequency sensorineural hearing impairment | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:low-set ears (28%)
n1=en:everted ears | n2=en:low-set ears (28%) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:malformations of the auditory ossicles
n1=en:everted ears | n2=en:malformations of the auditory ossicles | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:microtia hearing loss, conductive
n1=en:everted ears | n2=en:microtia hearing loss, conductive | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:narrow auditory canals (rare)
n1=en:everted ears | n2=en:narrow auditory canals (rare) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:neural hearing loss
n1=en:everted ears | n2=en:neural hearing loss | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:normal outer hair cell functions
n1=en:everted ears | n2=en:normal outer hair cell functions | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:organ of corti degeneration
n1=en:everted ears | n2=en:organ of corti degeneration | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:ossified pinnae
n1=en:everted ears | n2=en:ossified pinnae | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:other diseases of ear/mastoid
n1=en:everted ears | n2=en:other diseases of ear/mastoid | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:partial hearing loss
n1=en:everted ears | n2=en:partial hearing loss | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:poorly formed pinnae
n1=en:everted ears | n2=en:poorly formed pinnae | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:prelingual onset
n1=en:everted ears | n2=en:prelingual onset | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:progressive conductive hearing impairment
n1=en:everted ears | n2=en:progressive conductive hearing impairment | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:progressive, low frequency sensorineural hearing loss
n1=en:everted ears | n2=en:progressive, low frequency sensorineural hearing loss | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:prominent earlobes (in some patients)
n1=en:everted ears | n2=en:prominent earlobes (in some patients) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:prominent helices
n1=en:everted ears | n2=en:prominent helices | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:pseudomembranous inflammation of the middle ear
n1=en:everted ears | n2=en:pseudomembranous inflammation of the middle ear | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:satyr ear
n1=en:everted ears | n2=en:satyr ear | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:sensorineural deafness (onset in the second decade in 25 to 30% of patients)
n1=en:everted ears | n2=en:sensorineural deafness (onset in the second decade in 25 to 30% of patients) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:sensorineural deafness (reported in 1 family)
n1=en:everted ears | n2=en:sensorineural deafness (reported in 1 family) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:sensorineural deafness, variable (in 1 family)
n1=en:everted ears | n2=en:sensorineural deafness, variable (in 1 family) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:sensorineural hearing loss has been reported
n1=en:everted ears | n2=en:sensorineural hearing loss has been reported | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:sensorineural, conductive, or mixed hearing loss
n1=en:everted ears | n2=en:sensorineural, conductive, or mixed hearing loss | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:severe narrowing of cartilagenous auditory canal (in homozygotes)
n1=en:everted ears | n2=en:severe narrowing of cartilagenous auditory canal (in homozygotes) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:shallow skin dimple on posterior surface of ear
n1=en:everted ears | n2=en:shallow skin dimple on posterior surface of ear | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:simple ear structure
n1=en:everted ears | n2=en:simple ear structure | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:structural inner ear abnormalities (in patients with larger deletions)
n1=en:everted ears | n2=en:structural inner ear abnormalities (in patients with larger deletions) | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:thick, firm earlobes
n1=en:everted ears | n2=en:thick, firm earlobes | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:underdeveloped nasal alae
n1=en:everted ears | n2=en:underdeveloped nasal alae | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:underdeveloped tragus
n1=en:everted ears | n2=en:underdeveloped tragus | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:unilateral external ear deformity
n1=en:everted ears | n2=en:unilateral external ear deformity | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:unravelling of superior helices
n1=en:everted ears | n2=en:unravelling of superior helices | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:vertiginous syndrome
n1=en:everted ears | n2=en:vertiginous syndrome | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:vestibular areflexia, complete
n1=en:everted ears | n2=en:vestibular areflexia, complete | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:vestibular hyporeflexia
n1=en:everted ears | n2=en:vestibular hyporeflexia | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 34 / 0.791 ->
en:wide, flattened earlobes
n1=en:everted ears | n2=en:wide, flattened earlobes | rel=r_associated | relid=0 | w=34
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:abnormal middle ear ossicles
n1=en:everted ears | n2=en:abnormal middle ear ossicles | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:abnormality of the outer ear
n1=en:everted ears | n2=en:abnormality of the outer ear | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:absent auditory canals (wws)
n1=en:everted ears | n2=en:absent auditory canals (wws) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:absent earlobe
n1=en:everted ears | n2=en:absent earlobe | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:absent external auditory canals
n1=en:everted ears | n2=en:absent external auditory canals | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:acute otitis media/myringitis
n1=en:everted ears | n2=en:acute otitis media/myringitis | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:apical cartilage deformity
n1=en:everted ears | n2=en:apical cartilage deformity | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:atrophy of cochlear and vestibular fibrocytes
n1=en:everted ears | n2=en:atrophy of cochlear and vestibular fibrocytes | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:bilateral dys-synchronized auditory brainstem responses
n1=en:everted ears | n2=en:bilateral dys-synchronized auditory brainstem responses | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:bilateral hypoplastic cochlea
n1=en:everted ears | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:bilateral sensorineural hearing loss (in some patients)
n1=en:everted ears | n2=en:bilateral sensorineural hearing loss (in some patients) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:cleft at the junction of the lobule and helix
n1=en:everted ears | n2=en:cleft at the junction of the lobule and helix | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:complete bony atresia of medial portion of external auditory canal (in some patients)
n1=en:everted ears | n2=en:complete bony atresia of medial portion of external auditory canal (in some patients) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:conductive hearing loss (in a subset of patients)
n1=en:everted ears | n2=en:conductive hearing loss (in a subset of patients) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:deafness (sensorineural or mixed sensorineural and conductive)
n1=en:everted ears | n2=en:deafness (sensorineural or mixed sensorineural and conductive) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:deafness labyrinthine
n1=en:everted ears | n2=en:deafness labyrinthine | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:deafness, moderate-severe (onset in third decade)
n1=en:everted ears | n2=en:deafness, moderate-severe (onset in third decade) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:deafness, profound, affects all frequencies
n1=en:everted ears | n2=en:deafness, profound, affects all frequencies | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:deafness, secondary to cranial hyperostosis
n1=en:everted ears | n2=en:deafness, secondary to cranial hyperostosis | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:deafness, sensorineural (severe to profound)
n1=en:everted ears | n2=en:deafness, sensorineural (severe to profound) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:deafness, sensorineural, profound
n1=en:everted ears | n2=en:deafness, sensorineural, profound | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:deep-set ears
n1=en:everted ears | n2=en:deep-set ears | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:dilatated internal auditory canal
n1=en:everted ears | n2=en:dilatated internal auditory canal | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:dysplastic ears (in some patients)
n1=en:everted ears | n2=en:dysplastic ears (in some patients) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:ear pain/earache
n1=en:everted ears | n2=en:ear pain/earache | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:ears deficient in cartilage
n1=en:everted ears | n2=en:ears deficient in cartilage | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:hearing impairment, sensorineural, mild
n1=en:everted ears | n2=en:hearing impairment, sensorineural, mild | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:hearing loss (1 patient)
n1=en:everted ears | n2=en:hearing loss (1 patient) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:hearing loss (95% of patients)
n1=en:everted ears | n2=en:hearing loss (95% of patients) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:hearing loss, mild (rare)
n1=en:everted ears | n2=en:hearing loss, mild (rare) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected)
n1=en:everted ears | n2=en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural
n1=en:everted ears | n2=en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:hypercompliant tympanic membranes
n1=en:everted ears | n2=en:hypercompliant tympanic membranes | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:hypoplasia of the upper part of the helix
n1=en:everted ears | n2=en:hypoplasia of the upper part of the helix | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:hypoplastic ear lobes
n1=en:everted ears | n2=en:hypoplastic ear lobes | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:hypoplastic ears fused to the scalp
n1=en:everted ears | n2=en:hypoplastic ears fused to the scalp | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:large ear pinnae
n1=en:everted ears | n2=en:large ear pinnae | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:low-set ears (rare)
n1=en:everted ears | n2=en:low-set ears (rare) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:michel aplasia (complete absence of inner ear structures)
n1=en:everted ears | n2=en:michel aplasia (complete absence of inner ear structures) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:microtia (30-60% of patients)
n1=en:everted ears | n2=en:microtia (30-60% of patients) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:middle ear
n1=en:everted ears | n2=en:middle ear | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:narrow ears
n1=en:everted ears | n2=en:narrow ears | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:no reproducible waves i, iii, or v at high intensities
n1=en:everted ears | n2=en:no reproducible waves i, iii, or v at high intensities | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:normal middle ear pressures on tympanometry
n1=en:everted ears | n2=en:normal middle ear pressures on tympanometry | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:oae responses may decrease with age or use of hearing aids
n1=en:everted ears | n2=en:oae responses may decrease with age or use of hearing aids | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:otitis media, recurrent (rare)
n1=en:everted ears | n2=en:otitis media, recurrent (rare) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:pale, stiff pinnae
n1=en:everted ears | n2=en:pale, stiff pinnae | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:posteriorly rotated ear
n1=en:everted ears | n2=en:posteriorly rotated ear | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:prominent antitragus
n1=en:everted ears | n2=en:prominent antitragus | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:relatively long ears
n1=en:everted ears | n2=en:relatively long ears | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:retinitis (in some patients)
n1=en:everted ears | n2=en:retinitis (in some patients) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:sensorineural hearing loss (3 patients)
n1=en:everted ears | n2=en:sensorineural hearing loss (3 patients) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:sensorineural hearing loss (described in 1 family)
n1=en:everted ears | n2=en:sensorineural hearing loss (described in 1 family) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:sensorineural hearing loss (early-onset form)
n1=en:everted ears | n2=en:sensorineural hearing loss (early-onset form) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:sensorineural hearing loss (less common)
n1=en:everted ears | n2=en:sensorineural hearing loss (less common) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:sensorineural hearing loss, mild (rare)
n1=en:everted ears | n2=en:sensorineural hearing loss, mild (rare) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:severe to profound hearing impairment by early adulthood
n1=en:everted ears | n2=en:severe to profound hearing impairment by early adulthood | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:slit-like opening of the exterior auditory meatus
n1=en:everted ears | n2=en:slit-like opening of the exterior auditory meatus | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:small auricles
n1=en:everted ears | n2=en:small auricles | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:small earlobe
n1=en:everted ears | n2=en:small earlobe | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:small external auditory canals
n1=en:everted ears | n2=en:small external auditory canals | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:small lobes
n1=en:everted ears | n2=en:small lobes | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:small pinna
n1=en:everted ears | n2=en:small pinna | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:small, malformed ears
n1=en:everted ears | n2=en:small, malformed ears | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:soft auricles
n1=en:everted ears | n2=en:soft auricles | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:stapes ankylosis
n1=en:everted ears | n2=en:stapes ankylosis | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:structure of superior auricularis muscle
n1=en:everted ears | n2=en:structure of superior auricularis muscle | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:thick earlobes
n1=en:everted ears | n2=en:thick earlobes | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:unfolded superior helices
n1=en:everted ears | n2=en:unfolded superior helices | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:uplift of earlobes (in some patients)
n1=en:everted ears | n2=en:uplift of earlobes (in some patients) | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 32 / 0.744 ->
en:vestibulopathy, bilateral, progressive
n1=en:everted ears | n2=en:vestibulopathy, bilateral, progressive | rel=r_associated | relid=0 | w=32
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:abnormal communication between the subarachnoid space in the meatus and the perilymph
n1=en:everted ears | n2=en:abnormal communication between the subarachnoid space in the meatus and the perilymph | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:abnormal middle ear reflexes
n1=en:everted ears | n2=en:abnormal middle ear reflexes | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:abnormally folded ears
n1=en:everted ears | n2=en:abnormally folded ears | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:abnormally formed ears
n1=en:everted ears | n2=en:abnormally formed ears | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:absent brainstem auditory-evoked responses
n1=en:everted ears | n2=en:absent brainstem auditory-evoked responses | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:absent helices, bilaterally
n1=en:everted ears | n2=en:absent helices, bilaterally | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:absent vestibular function (caloric test)
n1=en:everted ears | n2=en:absent vestibular function (caloric test) | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:anteriorly rotated ears
n1=en:everted ears | n2=en:anteriorly rotated ears | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:auriculo-condylar syndrome
n1=en:everted ears | n2=en:auriculo-condylar syndrome | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:chronic otitis
n1=en:everted ears | n2=en:chronic otitis | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:conductive hearing loss to due otitis media
n1=en:everted ears | n2=en:conductive hearing loss to due otitis media | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:conductive hearing loss, mild bilateral (rare)
n1=en:everted ears | n2=en:conductive hearing loss, mild bilateral (rare) | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:congenital deafness
n1=en:everted ears | n2=en:congenital deafness | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:congenital hearing loss (1 family)
n1=en:everted ears | n2=en:congenital hearing loss (1 family) | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:congenital small ears
n1=en:everted ears | n2=en:congenital small ears | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:cup-shaped auricles
n1=en:everted ears | n2=en:cup-shaped auricles | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:deafness (in some patients)
n1=en:everted ears | n2=en:deafness (in some patients) | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:deafness, congenital sensorineural, severe to profound
n1=en:everted ears | n2=en:deafness, congenital sensorineural, severe to profound | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:deafness, postlingual
n1=en:everted ears | n2=en:deafness, postlingual | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:deafness, sensorineural (in some patients)
n1=en:everted ears | n2=en:deafness, sensorineural (in some patients) | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:downsloping audiogram
n1=en:everted ears | n2=en:downsloping audiogram | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:endolymphatic hydrops, delayed onset
n1=en:everted ears | n2=en:endolymphatic hydrops, delayed onset | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:endolymphatic sac tumors (elsts)
n1=en:everted ears | n2=en:endolymphatic sac tumors (elsts) | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:hearing disorder (1 patient)
n1=en:everted ears | n2=en:hearing disorder (1 patient) | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:hearing loss, progressive sensorineural, affecting high frequencies
n1=en:everted ears | n2=en:hearing loss, progressive sensorineural, affecting high frequencies | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:hearing loss, sensorineural (in some cases)
n1=en:everted ears | n2=en:hearing loss, sensorineural (in some cases) | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:hearing loss, sensorineural, associated with elsts
n1=en:everted ears | n2=en:hearing loss, sensorineural, associated with elsts | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:hypoplastic pinnae (30-60% of patients)
n1=en:everted ears | n2=en:hypoplastic pinnae (30-60% of patients) | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:keratotic plaque around ear meatus
n1=en:everted ears | n2=en:keratotic plaque around ear meatus | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:left ear
n1=en:everted ears | n2=en:left ear | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:loss of high frequencies at onset
n1=en:everted ears | n2=en:loss of high frequencies at onset | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:low-set ears (in one family)
n1=en:everted ears | n2=en:low-set ears (in one family) | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:low-set ears (in some patients)
n1=en:everted ears | n2=en:low-set ears (in some patients) | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:malformed earlobes
n1=en:everted ears | n2=en:malformed earlobes | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:morphological abnormality of the middle ear
n1=en:everted ears | n2=en:morphological abnormality of the middle ear | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:no hearing impairment
n1=en:everted ears | n2=en:no hearing impairment | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:normal cochlear microphonics
n1=en:everted ears | n2=en:normal cochlear microphonics | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:normal otoacoustic emissions (oae), indicating intact outer ear hair cell function
n1=en:everted ears | n2=en:normal otoacoustic emissions (oae), indicating intact outer ear hair cell function | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:normal vestibular function
n1=en:everted ears | n2=en:normal vestibular function | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:normal vestibular response
n1=en:everted ears | n2=en:normal vestibular response | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:otitis media, chronic (rare)
n1=en:everted ears | n2=en:otitis media, chronic (rare) | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:overfolded helix
n1=en:everted ears | n2=en:overfolded helix | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:posterior helical indentations
n1=en:everted ears | n2=en:posterior helical indentations | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:preauricular pits (70-80% of patients)
n1=en:everted ears | n2=en:preauricular pits (70-80% of patients) | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:preauricular sinus
n1=en:everted ears | n2=en:preauricular sinus | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:progressive sensorineural hearing impairment
n1=en:everted ears | n2=en:progressive sensorineural hearing impairment | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:prominent antitragus (in some patients)
n1=en:everted ears | n2=en:prominent antitragus (in some patients) | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:rudimentary
n1=en:everted ears | n2=en:rudimentary | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:sensation of blocked ears
n1=en:everted ears | n2=en:sensation of blocked ears | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:sensorineural hearing loss (in 1 of 3 patients)
n1=en:everted ears | n2=en:sensorineural hearing loss (in 1 of 3 patients) | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:serous otitis media
n1=en:everted ears | n2=en:serous otitis media | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:small ears (female)
n1=en:everted ears | n2=en:small ears (female) | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:small triangular pinnae
n1=en:everted ears | n2=en:small triangular pinnae | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves
n1=en:everted ears | n2=en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:tinnitus
n1=en:everted ears | n2=en:tinnitus | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:tinnitus (in some patients)
n1=en:everted ears | n2=en:tinnitus (in some patients) | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:u- or bowl-shaped audiogram
n1=en:everted ears | n2=en:u- or bowl-shaped audiogram | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:uplifted earlobes
n1=en:everted ears | n2=en:uplifted earlobes | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:vestibular abnormalities (variable)
n1=en:everted ears | n2=en:vestibular abnormalities (variable) | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 31 / 0.721 ->
en:wide bulbous internal auditory meatus
n1=en:everted ears | n2=en:wide bulbous internal auditory meatus | rel=r_associated | relid=0 | w=31
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:a subset of patients have hearing loss
n1=en:everted ears | n2=en:a subset of patients have hearing loss | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:abnormal folded pinna
n1=en:everted ears | n2=en:abnormal folded pinna | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:absence of acoustic reflex
n1=en:everted ears | n2=en:absence of acoustic reflex | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:absence of vestibular evoked myogenic potentials (rare)
n1=en:everted ears | n2=en:absence of vestibular evoked myogenic potentials (rare) | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:absent external auditory meatus
n1=en:everted ears | n2=en:absent external auditory meatus | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:absent ipsilateral middle ear muscle reflexes (in older patients)
n1=en:everted ears | n2=en:absent ipsilateral middle ear muscle reflexes (in older patients) | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:air-bone gap of greater than 20 db across 0.5 to 2 khz
n1=en:everted ears | n2=en:air-bone gap of greater than 20 db across 0.5 to 2 khz | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:angular ears
n1=en:everted ears | n2=en:angular ears | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:anteverted ears
n1=en:everted ears | n2=en:anteverted ears | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient)
n1=en:everted ears | n2=en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient) | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:cochlear malformation defect (mondini dysplasia) (less common)
n1=en:everted ears | n2=en:cochlear malformation defect (mondini dysplasia) (less common) | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:cupped pinna
n1=en:everted ears | n2=en:cupped pinna | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:deafness, early-onset mixed conductive and sensorineural
n1=en:everted ears | n2=en:deafness, early-onset mixed conductive and sensorineural | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:deafness, profound congenital sensorineural
n1=en:everted ears | n2=en:deafness, profound congenital sensorineural | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:decreased auditory brainstem responses
n1=en:everted ears | n2=en:decreased auditory brainstem responses | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v
n1=en:everted ears | n2=en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation
n1=en:everted ears | n2=en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:ear part
n1=en:everted ears | n2=en:ear part | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:entire ear
n1=en:everted ears | n2=en:entire ear | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:external ear defects
n1=en:everted ears | n2=en:external ear defects | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:hearing loss (rare)
n1=en:everted ears | n2=en:hearing loss (rare) | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:hearing loss (reported in 2 patients)
n1=en:everted ears | n2=en:hearing loss (reported in 2 patients) | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:hearing loss, congenital sensorineural, severe to profound
n1=en:everted ears | n2=en:hearing loss, congenital sensorineural, severe to profound | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies)
n1=en:everted ears | n2=en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies) | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:hearing loss, sensorineural (type ii)
n1=en:everted ears | n2=en:hearing loss, sensorineural (type ii) | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:hearing loss, sensorineural, severe to profound
n1=en:everted ears | n2=en:hearing loss, sensorineural, severe to profound | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:hearing threshold at or above 90 db at all frequencies tested (0.25-8.0 khz)
n1=en:everted ears | n2=en:hearing threshold at or above 90 db at all frequencies tested (0.25-8.0 khz) | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:hypermobile
n1=en:everted ears | n2=en:hypermobile | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:hypertrophic auricular cartilage
n1=en:everted ears | n2=en:hypertrophic auricular cartilage | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:large anteverted ears
n1=en:everted ears | n2=en:large anteverted ears | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:large simple ears
n1=en:everted ears | n2=en:large simple ears | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:long ear
n1=en:everted ears | n2=en:long ear | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:loss of vestibular reflexes
n1=en:everted ears | n2=en:loss of vestibular reflexes | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:low-frequency conductive hearing loss
n1=en:everted ears | n2=en:low-frequency conductive hearing loss | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:low-set ears (1 patient)
n1=en:everted ears | n2=en:low-set ears (1 patient) | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:low-set ears (in 2/4 patients)
n1=en:everted ears | n2=en:low-set ears (in 2/4 patients) | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:low-set, malformed ears
n1=en:everted ears | n2=en:low-set, malformed ears | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:malformed auricle (1 patient)
n1=en:everted ears | n2=en:malformed auricle (1 patient) | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:microtia, type i
n1=en:everted ears | n2=en:microtia, type i | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:mild cochlear hearing loss (1 patient)
n1=en:everted ears | n2=en:mild cochlear hearing loss (1 patient) | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:mild hearing impairment (13%)
n1=en:everted ears | n2=en:mild hearing impairment (13%) | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:misshapen, small ear
n1=en:everted ears | n2=en:misshapen, small ear | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:mixed hearing loss
n1=en:everted ears | n2=en:mixed hearing loss | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:near-stenosis of bony portion of auditory canal
n1=en:everted ears | n2=en:near-stenosis of bony portion of auditory canal | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:no auditory brainstem response (abr)
n1=en:everted ears | n2=en:no auditory brainstem response (abr) | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:nonprogressive
n1=en:everted ears | n2=en:nonprogressive | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:phonophobia
n1=en:everted ears | n2=en:phonophobia | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:poorly shaped ears
n1=en:everted ears | n2=en:poorly shaped ears | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:posteriorly rotated ears (1/4 patients)
n1=en:everted ears | n2=en:posteriorly rotated ears (1/4 patients) | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:preauricular skin tag
n1=en:everted ears | n2=en:preauricular skin tag | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:prominent crura
n1=en:everted ears | n2=en:prominent crura | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:protruding ears (in some patients)
n1=en:everted ears | n2=en:protruding ears (in some patients) | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:sensorineural hearing loss (1 family)
n1=en:everted ears | n2=en:sensorineural hearing loss (1 family) | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:sensorineural hearing loss (1 patient)
n1=en:everted ears | n2=en:sensorineural hearing loss (1 patient) | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:sensorineural hearing loss, progressive bilateral postlingual
n1=en:everted ears | n2=en:sensorineural hearing loss, progressive bilateral postlingual | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:squared-off superior helices
n1=en:everted ears | n2=en:squared-off superior helices | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:synotus
n1=en:everted ears | n2=en:synotus | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:thick ears
n1=en:everted ears | n2=en:thick ears | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:triangular-shaped ears
n1=en:everted ears | n2=en:triangular-shaped ears | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:unconnected or fused stapes and incus
n1=en:everted ears | n2=en:unconnected or fused stapes and incus | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:underfolded helix
n1=en:everted ears | n2=en:underfolded helix | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:vestibular anomalies (less common)
n1=en:everted ears | n2=en:vestibular anomalies (less common) | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:vestibular dysfunction
n1=en:everted ears | n2=en:vestibular dysfunction | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 30 / 0.698 ->
en:vestibular hypofunction (rare)
n1=en:everted ears | n2=en:vestibular hypofunction (rare) | rel=r_associated | relid=0 | w=30
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:'tilted' ears
n1=en:everted ears | n2=en:'tilted' ears | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:abnormal brain auditory evoked responses (baer)
n1=en:everted ears | n2=en:abnormal brain auditory evoked responses (baer) | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:abnormality of the middle ear ossicles
n1=en:everted ears | n2=en:abnormality of the middle ear ossicles | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:abnormally folded helix
n1=en:everted ears | n2=en:abnormally folded helix | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:absent distortion product otoacoustic emissions (oaes)
n1=en:everted ears | n2=en:absent distortion product otoacoustic emissions (oaes) | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:anteriorly displaced ears
n1=en:everted ears | n2=en:anteriorly displaced ears | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:asymmetry of the ears
n1=en:everted ears | n2=en:asymmetry of the ears | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:attached ear lobules
n1=en:everted ears | n2=en:attached ear lobules | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:aural fullness
n1=en:everted ears | n2=en:aural fullness | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:auricular clefts
n1=en:everted ears | n2=en:auricular clefts | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:cauliflower ear deformity (rare)
n1=en:everted ears | n2=en:cauliflower ear deformity (rare) | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:chronic otitis media
n1=en:everted ears | n2=en:chronic otitis media | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:conductive and sensorineural hearing loss
n1=en:everted ears | n2=en:conductive and sensorineural hearing loss | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:congenital atresia of external auditory canal
n1=en:everted ears | n2=en:congenital atresia of external auditory canal | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:deafness, early-onset
n1=en:everted ears | n2=en:deafness, early-onset | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:deafness, sensorineural (reported in 1 family)
n1=en:everted ears | n2=en:deafness, sensorineural (reported in 1 family) | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:deafness, stable bilateral symmetric prelingual
n1=en:everted ears | n2=en:deafness, stable bilateral symmetric prelingual | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:deficient auricle
n1=en:everted ears | n2=en:deficient auricle | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:dysplastic pinnae
n1=en:everted ears | n2=en:dysplastic pinnae | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:external ear
n1=en:everted ears | n2=en:external ear | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:flat audiogram
n1=en:everted ears | n2=en:flat audiogram | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:floppy ears
n1=en:everted ears | n2=en:floppy ears | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:hearing impairment, asymmetric (in some patients with hsan2d)
n1=en:everted ears | n2=en:hearing impairment, asymmetric (in some patients with hsan2d) | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:hearing loss, bilateral sensorineural (profound)
n1=en:everted ears | n2=en:hearing loss, bilateral sensorineural (profound) | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:hearing loss, progressive conductive and/or sensorineural, during adulthood
n1=en:everted ears | n2=en:hearing loss, progressive conductive and/or sensorineural, during adulthood | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:hearing loss, progressive, starting in infancy
n1=en:everted ears | n2=en:hearing loss, progressive, starting in infancy | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:hearing loss, sensorineural (in 1 ashkenazi patient)
n1=en:everted ears | n2=en:hearing loss, sensorineural (in 1 ashkenazi patient) | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:hearing loss, sensorineural (in some patients)
n1=en:everted ears | n2=en:hearing loss, sensorineural (in some patients) | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:hyperacusis
n1=en:everted ears | n2=en:hyperacusis | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:incomplete separation of the cochlea from the internal auditory canal
n1=en:everted ears | n2=en:incomplete separation of the cochlea from the internal auditory canal | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:large earlobe
n1=en:everted ears | n2=en:large earlobe | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:large pinnae
n1=en:everted ears | n2=en:large pinnae | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:large prominent ears
n1=en:everted ears | n2=en:large prominent ears | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:large, dysmorphic ears
n1=en:everted ears | n2=en:large, dysmorphic ears | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:large, floppy ears
n1=en:everted ears | n2=en:large, floppy ears | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:lobular aplasia
n1=en:everted ears | n2=en:lobular aplasia | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:lobule creases
n1=en:everted ears | n2=en:lobule creases | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:long and prominent ear crus
n1=en:everted ears | n2=en:long and prominent ear crus | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:loss of vestibular caloric response
n1=en:everted ears | n2=en:loss of vestibular caloric response | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:microtia (wws)
n1=en:everted ears | n2=en:microtia (wws) | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:misshapen ear
n1=en:everted ears | n2=en:misshapen ear | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies
n1=en:everted ears | n2=en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:narrowed external ear canal (30% of patients)
n1=en:everted ears | n2=en:narrowed external ear canal (30% of patients) | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:narrowing of ear canal
n1=en:everted ears | n2=en:narrowing of ear canal | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:no auditory brainstem response to 100-db stimulus
n1=en:everted ears | n2=en:no auditory brainstem response to 100-db stimulus | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:otoneurologic disturbances
n1=en:everted ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:poorly formed ears
n1=en:everted ears | n2=en:poorly formed ears | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:profound sensorineural hearing loss
n1=en:everted ears | n2=en:profound sensorineural hearing loss | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:prolonged brainstem auditory evoked potentials (baep)
n1=en:everted ears | n2=en:prolonged brainstem auditory evoked potentials (baep) | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:secretory otitis media
n1=en:everted ears | n2=en:secretory otitis media | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:sensorineural hearing impairment (in some patients)
n1=en:everted ears | n2=en:sensorineural hearing impairment (in some patients) | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:sensorineural hearing loss (rare)
n1=en:everted ears | n2=en:sensorineural hearing loss (rare) | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:simplified helices
n1=en:everted ears | n2=en:simplified helices | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:small/rudimentary tragus, antitragus and lobule
n1=en:everted ears | n2=en:small/rudimentary tragus, antitragus and lobule | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:stenosis of external auditory canal
n1=en:everted ears | n2=en:stenosis of external auditory canal | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:thickened lobes
n1=en:everted ears | n2=en:thickened lobes | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:tympanic membrane perforation
n1=en:everted ears | n2=en:tympanic membrane perforation | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:upsloping audiograms
n1=en:everted ears | n2=en:upsloping audiograms | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
en:upturned lobes
n1=en:everted ears | n2=en:upturned lobes | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 29 / 0.674 ->
otite moyenne séreuse
n1=en:everted ears | n2=otite moyenne séreuse | rel=r_associated | relid=0 | w=29
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:abnormal ears
n1=en:everted ears | n2=en:abnormal ears | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:abnormal gap detection
n1=en:everted ears | n2=en:abnormal gap detection | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:absence of earlobe
n1=en:everted ears | n2=en:absence of earlobe | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:absent brainstem auditory responses
n1=en:everted ears | n2=en:absent brainstem auditory responses | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:acoustic trauma
n1=en:everted ears | n2=en:acoustic trauma | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:bat ear
n1=en:everted ears | n2=en:bat ear | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion
n1=en:everted ears | n2=en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile)
n1=en:everted ears | n2=en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:cochlear malformation
n1=en:everted ears | n2=en:cochlear malformation | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:cochleosaccular dysplasia
n1=en:everted ears | n2=en:cochleosaccular dysplasia | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:conductive hearing loss
n1=en:everted ears | n2=en:conductive hearing loss | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:conductive hearing loss (30% of patients)
n1=en:everted ears | n2=en:conductive hearing loss (30% of patients) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:cupped ears (in some patients)
n1=en:everted ears | n2=en:cupped ears (in some patients) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:deafness, profound, by 6th decade
n1=en:everted ears | n2=en:deafness, profound, by 6th decade | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:deafness, sensorineural, prelingual, profound
n1=en:everted ears | n2=en:deafness, sensorineural, prelingual, profound | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:decreased otoacoustic emission amplitude
n1=en:everted ears | n2=en:decreased otoacoustic emission amplitude | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea
n1=en:everted ears | n2=en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:excessive cerumen
n1=en:everted ears | n2=en:excessive cerumen | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:foreign body in auditory canal
n1=en:everted ears | n2=en:foreign body in auditory canal | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:hearing complaints (excluding h84-86)
n1=en:everted ears | n2=en:hearing complaints (excluding h84-86) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:hearing loss (variable)
n1=en:everted ears | n2=en:hearing loss (variable) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:hearing loss, congenital, profound (250-8,000 hz)
n1=en:everted ears | n2=en:hearing loss, congenital, profound (250-8,000 hz) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:hearing loss, high-frequency (onset in childhood-adolescence)
n1=en:everted ears | n2=en:hearing loss, high-frequency (onset in childhood-adolescence) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:hearing loss, late-onset sensorineural, mild-to moderate (less common)
n1=en:everted ears | n2=en:hearing loss, late-onset sensorineural, mild-to moderate (less common) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:hearing loss, postlingual
n1=en:everted ears | n2=en:hearing loss, postlingual | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:hearing loss, sensorineural (in one family)
n1=en:everted ears | n2=en:hearing loss, sensorineural (in one family) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:hearing loss, sensorineural, progressive (childhood-onset)
n1=en:everted ears | n2=en:hearing loss, sensorineural, progressive (childhood-onset) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:hearing loss, severe to profound, affecting all frequencies
n1=en:everted ears | n2=en:hearing loss, severe to profound, affecting all frequencies | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:high-tone sensorineural deafness (67% of patients)
n1=en:everted ears | n2=en:high-tone sensorineural deafness (67% of patients) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:hypoplastic, overfolded helices
n1=en:everted ears | n2=en:hypoplastic, overfolded helices | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies
n1=en:everted ears | n2=en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:inner ear
n1=en:everted ears | n2=en:inner ear | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:juberg-marsidi syndrome
n1=en:everted ears | n2=en:juberg-marsidi syndrome | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:large appearing ears
n1=en:everted ears | n2=en:large appearing ears | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:large dysplastic ears
n1=en:everted ears | n2=en:large dysplastic ears | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:large, low-set ears
n1=en:everted ears | n2=en:large, low-set ears | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:large, low-set ears (uncommon)
n1=en:everted ears | n2=en:large, low-set ears (uncommon) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:loss of hearing (45%)
n1=en:everted ears | n2=en:loss of hearing (45%) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:low-set and rotated ears
n1=en:everted ears | n2=en:low-set and rotated ears | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:low-set ears (45%)
n1=en:everted ears | n2=en:low-set ears (45%) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:malformed ossicular chain
n1=en:everted ears | n2=en:malformed ossicular chain | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:minor auricular anomalies
n1=en:everted ears | n2=en:minor auricular anomalies | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:minor ear anomalies (in some patients)
n1=en:everted ears | n2=en:minor ear anomalies (in some patients) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:mondini malformation
n1=en:everted ears | n2=en:mondini malformation | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:narrow external ear canals (1 patient)
n1=en:everted ears | n2=en:narrow external ear canals (1 patient) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:near-stenosis of bony portion of auditory canal (in homozygotes)
n1=en:everted ears | n2=en:near-stenosis of bony portion of auditory canal (in homozygotes) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:nonprogressive deafness
n1=en:everted ears | n2=en:nonprogressive deafness | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:otosclerosis
n1=en:everted ears | n2=en:otosclerosis | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:preauricular skin tags (in some patients)
n1=en:everted ears | n2=en:preauricular skin tags (in some patients) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:profound deafness
n1=en:everted ears | n2=en:profound deafness | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:prominence and protrusion of upper third of the ear
n1=en:everted ears | n2=en:prominence and protrusion of upper third of the ear | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:prominent ears (rare)
n1=en:everted ears | n2=en:prominent ears (rare) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:protuberant ear
n1=en:everted ears | n2=en:protuberant ear | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:raised earlobes
n1=en:everted ears | n2=en:raised earlobes | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:recurrent ear infections
n1=en:everted ears | n2=en:recurrent ear infections | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:recurrent otitis
n1=en:everted ears | n2=en:recurrent otitis | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:recurrent otitis media
n1=en:everted ears | n2=en:recurrent otitis media | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:right ear
n1=en:everted ears | n2=en:right ear | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:rudimentary tympanic membrane (in some patients)
n1=en:everted ears | n2=en:rudimentary tympanic membrane (in some patients) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:sensorineural hearing loss (onset early childhood)
n1=en:everted ears | n2=en:sensorineural hearing loss (onset early childhood) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:sensory hearing loss
n1=en:everted ears | n2=en:sensory hearing loss | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:severe loss in the higher frequencies by the fifth decade
n1=en:everted ears | n2=en:severe loss in the higher frequencies by the fifth decade | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:short ear
n1=en:everted ears | n2=en:short ear | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:short ears (in 1 family)
n1=en:everted ears | n2=en:short ears (in 1 family) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:small pits anterior to the helix (1 patient)
n1=en:everted ears | n2=en:small pits anterior to the helix (1 patient) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:small, posteriorly rotated ears
n1=en:everted ears | n2=en:small, posteriorly rotated ears | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:strabismus (in some patients)
n1=en:everted ears | n2=en:strabismus (in some patients) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:u-shaped audiogram
n1=en:everted ears | n2=en:u-shaped audiogram | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:vestibular areflexia
n1=en:everted ears | n2=en:vestibular areflexia | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
en:vestibular function defect (decreased in some, normal in other patients)
n1=en:everted ears | n2=en:vestibular function defect (decreased in some, normal in other patients) | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 28 / 0.651 ->
traumatisme superficiel oreille
n1=en:everted ears | n2=traumatisme superficiel oreille | rel=r_associated | relid=0 | w=28
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:abnormal amplitude modulation detection
n1=en:everted ears | n2=en:abnormal amplitude modulation detection | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:abnormal bridge connecting the crus of the helix and antihelix
n1=en:everted ears | n2=en:abnormal bridge connecting the crus of the helix and antihelix | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:abnormal ear configuration
n1=en:everted ears | n2=en:abnormal ear configuration | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:abnormality of the pinna
n1=en:everted ears | n2=en:abnormality of the pinna | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:abnormally shaped ears (in one family)
n1=en:everted ears | n2=en:abnormally shaped ears (in one family) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:absent or decreased auditory brainstem responses
n1=en:everted ears | n2=en:absent or decreased auditory brainstem responses | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:absent stapedial reflex
n1=en:everted ears | n2=en:absent stapedial reflex | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:accessory tragus
n1=en:everted ears | n2=en:accessory tragus | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:anterior creases of earlobe
n1=en:everted ears | n2=en:anterior creases of earlobe | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:atresia of the external auditory canal
n1=en:everted ears | n2=en:atresia of the external auditory canal | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:auditory impairment
n1=en:everted ears | n2=en:auditory impairment | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:bleeding from ear
n1=en:everted ears | n2=en:bleeding from ear | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:concern with appearance of ears
n1=en:everted ears | n2=en:concern with appearance of ears | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:congenital absence of external ear
n1=en:everted ears | n2=en:congenital absence of external ear | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss)
n1=en:everted ears | n2=en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:congenital sensorineural hearing loss
n1=en:everted ears | n2=en:congenital sensorineural hearing loss | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:deafness
n1=en:everted ears | n2=en:deafness | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:deafness (in 1 of 2 families)
n1=en:everted ears | n2=en:deafness (in 1 of 2 families) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:deafness, conductive (in some patients)
n1=en:everted ears | n2=en:deafness, conductive (in some patients) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:deafness, sensorineural, severe to profound affecting all frequencies
n1=en:everted ears | n2=en:deafness, sensorineural, severe to profound affecting all frequencies | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:deafness, unilateral, childhood onset
n1=en:everted ears | n2=en:deafness, unilateral, childhood onset | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:ear pits, posterior helical
n1=en:everted ears | n2=en:ear pits, posterior helical | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:ear tag
n1=en:everted ears | n2=en:ear tag | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:expansion of helical fold at superior point of true longitudinal axis of ear
n1=en:everted ears | n2=en:expansion of helical fold at superior point of true longitudinal axis of ear | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:external ear defects (47%)
n1=en:everted ears | n2=en:external ear defects (47%) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:flat or shallow u-shaped audiogram
n1=en:everted ears | n2=en:flat or shallow u-shaped audiogram | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:hearing deficits (28% of adults)
n1=en:everted ears | n2=en:hearing deficits (28% of adults) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:hearing impairment (in 1/4 patients)
n1=en:everted ears | n2=en:hearing impairment (in 1/4 patients) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:hearing impairment, sensorineural, fluctuating
n1=en:everted ears | n2=en:hearing impairment, sensorineural, fluctuating | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:hearing loss (2 patients)
n1=en:everted ears | n2=en:hearing loss (2 patients) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:hearing loss (conductive and/or sensorineural)
n1=en:everted ears | n2=en:hearing loss (conductive and/or sensorineural) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:hearing loss (cvs+)
n1=en:everted ears | n2=en:hearing loss (cvs+) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:hearing loss begins with loss of high frequencies
n1=en:everted ears | n2=en:hearing loss begins with loss of high frequencies | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:hearing loss first affects high frequencies
n1=en:everted ears | n2=en:hearing loss first affects high frequencies | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:hearing loss, congenital sensorineural, moderate-severe
n1=en:everted ears | n2=en:hearing loss, congenital sensorineural, moderate-severe | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:hearing loss, high frequency, slowly progressive (onset in early childhood)
n1=en:everted ears | n2=en:hearing loss, high frequency, slowly progressive (onset in early childhood) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:hearing loss, mixed, mild to severe (in heterozygotes)
n1=en:everted ears | n2=en:hearing loss, mixed, mild to severe (in heterozygotes) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:hearing loss, profound prelingual sensorineural
n1=en:everted ears | n2=en:hearing loss, profound prelingual sensorineural | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:hearing loss, progressive (in some patients)
n1=en:everted ears | n2=en:hearing loss, progressive (in some patients) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies)
n1=en:everted ears | n2=en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:hearing loss, sensorineural (bilateral, prelingual)
n1=en:everted ears | n2=en:hearing loss, sensorineural (bilateral, prelingual) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:hearing loss, sensorineural (in 2 patients)
n1=en:everted ears | n2=en:hearing loss, sensorineural (in 2 patients) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:hearing loss, sensorineural (in patients with larger deletions)
n1=en:everted ears | n2=en:hearing loss, sensorineural (in patients with larger deletions) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:high-frequency tinnitus at onset
n1=en:everted ears | n2=en:high-frequency tinnitus at onset | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:hypoplastic semicircular canals
n1=en:everted ears | n2=en:hypoplastic semicircular canals | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients)
n1=en:everted ears | n2=en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:internal auditory canal hypoplasia
n1=en:everted ears | n2=en:internal auditory canal hypoplasia | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:large ears (in some patients)
n1=en:everted ears | n2=en:large ears (in some patients) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:long, lobulated ears
n1=en:everted ears | n2=en:long, lobulated ears | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:low-set ears (severe form)
n1=en:everted ears | n2=en:low-set ears (severe form) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:malformed pinnae (30-60% of patients)
n1=en:everted ears | n2=en:malformed pinnae (30-60% of patients) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:occasional conductive hearing loss
n1=en:everted ears | n2=en:occasional conductive hearing loss | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:otitis externa
n1=en:everted ears | n2=en:otitis externa | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:outer ear abnormalities (deletion patients) prominent ears
n1=en:everted ears | n2=en:outer ear abnormalities (deletion patients) prominent ears | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:overfolding of the superior helices
n1=en:everted ears | n2=en:overfolding of the superior helices | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:partial aplasia of external auditory canal ending in blind fistula (in some patients)
n1=en:everted ears | n2=en:partial aplasia of external auditory canal ending in blind fistula (in some patients) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:postauricular pit
n1=en:everted ears | n2=en:postauricular pit | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:posteriorly rotated ears (female)
n1=en:everted ears | n2=en:posteriorly rotated ears (female) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:posteriorly rotated ears (in some patients)
n1=en:everted ears | n2=en:posteriorly rotated ears (in some patients) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:preauricular dimple
n1=en:everted ears | n2=en:preauricular dimple | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:preauricular sinus, bilateral
n1=en:everted ears | n2=en:preauricular sinus, bilateral | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:preauricular skin furrow
n1=en:everted ears | n2=en:preauricular skin furrow | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:presbycusis
n1=en:everted ears | n2=en:presbycusis | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:prominent antihelix
n1=en:everted ears | n2=en:prominent antihelix | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:protruding lobules
n1=en:everted ears | n2=en:protruding lobules | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:recurrent otitis media in infancy
n1=en:everted ears | n2=en:recurrent otitis media in infancy | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:recurrent serous otitis
n1=en:everted ears | n2=en:recurrent serous otitis | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:sensorineural deafness (rare)
n1=en:everted ears | n2=en:sensorineural deafness (rare) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:sensorineural hearing loss (20% of patients)
n1=en:everted ears | n2=en:sensorineural hearing loss (20% of patients) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:severe narrowing of cartilagenous auditory canal
n1=en:everted ears | n2=en:severe narrowing of cartilagenous auditory canal | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:simple ear
n1=en:everted ears | n2=en:simple ear | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:small, simple ears
n1=en:everted ears | n2=en:small, simple ears | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:stapes fixation
n1=en:everted ears | n2=en:stapes fixation | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:thickened helices
n1=en:everted ears | n2=en:thickened helices | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:tinnitus (rare)
n1=en:everted ears | n2=en:tinnitus (rare) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:vertigo
n1=en:everted ears | n2=en:vertigo | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 27 / 0.628 ->
en:vestibular involvement (variable)
n1=en:everted ears | n2=en:vestibular involvement (variable) | rel=r_associated | relid=0 | w=27
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:abnormal auditory temporal processes
n1=en:everted ears | n2=en:abnormal auditory temporal processes | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:abnormal or absent auditory nerve and brainstem responses
n1=en:everted ears | n2=en:abnormal or absent auditory nerve and brainstem responses | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:abnormal speech discrimination
n1=en:everted ears | n2=en:abnormal speech discrimination | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:absent lobules
n1=en:everted ears | n2=en:absent lobules | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:anomalous middle ear bones
n1=en:everted ears | n2=en:anomalous middle ear bones | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:asymmetric dysplastic ears
n1=en:everted ears | n2=en:asymmetric dysplastic ears | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:bilateral conductive hearing loss (rare)
n1=en:everted ears | n2=en:bilateral conductive hearing loss (rare) | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:blind fistula
n1=en:everted ears | n2=en:blind fistula | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:chronic otitis other infection ear
n1=en:everted ears | n2=en:chronic otitis other infection ear | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:crumpled ear (76%)
n1=en:everted ears | n2=en:crumpled ear (76%) | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:deafness (variable)
n1=en:everted ears | n2=en:deafness (variable) | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:deafness affects all frequencies
n1=en:everted ears | n2=en:deafness affects all frequencies | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:deafness, sensorineural, especially affecting high frequencies (in about 55% of males and 45% of females)
n1=en:everted ears | n2=en:deafness, sensorineural, especially affecting high frequencies (in about 55% of males and 45% of females) | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:deafness, sensorineural, mild (rare)
n1=en:everted ears | n2=en:deafness, sensorineural, mild (rare) | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:disjunction of otherwise normal lobule from remainder of ear
n1=en:everted ears | n2=en:disjunction of otherwise normal lobule from remainder of ear | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:dizziness
n1=en:everted ears | n2=en:dizziness | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:downward sloping or flat audiogram
n1=en:everted ears | n2=en:downward sloping or flat audiogram | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:ear neoplasm
n1=en:everted ears | n2=en:ear neoplasm | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:flat ears
n1=en:everted ears | n2=en:flat ears | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:fleshy ears
n1=en:everted ears | n2=en:fleshy ears | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:folded helix
n1=en:everted ears | n2=en:folded helix | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:folded superior edge of helix
n1=en:everted ears | n2=en:folded superior edge of helix | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:hearing impairment (in some patients)
n1=en:everted ears | n2=en:hearing impairment (in some patients) | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:hearing impairment may occur
n1=en:everted ears | n2=en:hearing impairment may occur | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:hearing impairment, mild (2 patients)
n1=en:everted ears | n2=en:hearing impairment, mild (2 patients) | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:hearing loss, mild
n1=en:everted ears | n2=en:hearing loss, mild | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:hearing loss, more severe at lower frequencies
n1=en:everted ears | n2=en:hearing loss, more severe at lower frequencies | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:hearing loss, neural type
n1=en:everted ears | n2=en:hearing loss, neural type | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:hearing loss, postlingual sensorineural
n1=en:everted ears | n2=en:hearing loss, postlingual sensorineural | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:everted ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:hearing loss, sensorineural, mild progressive (in some patients)
n1=en:everted ears | n2=en:hearing loss, sensorineural, mild progressive (in some patients) | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:hearing loss, sensorineural, prelingual
n1=en:everted ears | n2=en:hearing loss, sensorineural, prelingual | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:hypoacusia (1 patient)
n1=en:everted ears | n2=en:hypoacusia (1 patient) | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:hypoplastic helices
n1=en:everted ears | n2=en:hypoplastic helices | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:incomplete atretic plate
n1=en:everted ears | n2=en:incomplete atretic plate | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:large ears (37%)
n1=en:everted ears | n2=en:large ears (37%) | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:large fleshy ears
n1=en:everted ears | n2=en:large fleshy ears | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:large protruding ears
n1=en:everted ears | n2=en:large protruding ears | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:linear ear lobe creases
n1=en:everted ears | n2=en:linear ear lobe creases | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:loss of mid- and low-frequencies later
n1=en:everted ears | n2=en:loss of mid- and low-frequencies later | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:loss of outer hair cell function
n1=en:everted ears | n2=en:loss of outer hair cell function | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:low set ears
n1=en:everted ears | n2=en:low set ears | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:macrotia
n1=en:everted ears | n2=en:macrotia | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:meniere disease
n1=en:everted ears | n2=en:meniere disease | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:narrowed external ear canal
n1=en:everted ears | n2=en:narrowed external ear canal | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:neonatal cystic lesions of the pinnae
n1=en:everted ears | n2=en:neonatal cystic lesions of the pinnae | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:no hearing loss
n1=en:everted ears | n2=en:no hearing loss | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:normal static compliance on tympanometry
n1=en:everted ears | n2=en:normal static compliance on tympanometry | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:otitis media
n1=en:everted ears | n2=en:otitis media | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:overfolded, rumpled ears
n1=en:everted ears | n2=en:overfolded, rumpled ears | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:pigmentation of the ear cartilage
n1=en:everted ears | n2=en:pigmentation of the ear cartilage | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:posteriorly rotated ears (2p21del)
n1=en:everted ears | n2=en:posteriorly rotated ears (2p21del) | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:pre- and post-auricular skin or cartilaginous tags
n1=en:everted ears | n2=en:pre- and post-auricular skin or cartilaginous tags | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face)
n1=en:everted ears | n2=en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face) | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:progressive hearing impairment
n1=en:everted ears | n2=en:progressive hearing impairment | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:progressive hearing loss (in some)
n1=en:everted ears | n2=en:progressive hearing loss (in some) | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:progressive high-frequency hearing loss (onset 20-30 years)
n1=en:everted ears | n2=en:progressive high-frequency hearing loss (onset 20-30 years) | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:prominent ear
n1=en:everted ears | n2=en:prominent ear | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:protruding ears (rare)
n1=en:everted ears | n2=en:protruding ears (rare) | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:protruding right ear
n1=en:everted ears | n2=en:protruding right ear | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:protruding, simple ears
n1=en:everted ears | n2=en:protruding, simple ears | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:pulsatile tinnitus (tympanic paraganglioma)
n1=en:everted ears | n2=en:pulsatile tinnitus (tympanic paraganglioma) | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:sclerosis of semicircular canals
n1=en:everted ears | n2=en:sclerosis of semicircular canals | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:sensorineural deafness, progressive, late-onset
n1=en:everted ears | n2=en:sensorineural deafness, progressive, late-onset | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:sensorineural hearing impairment (less common)
n1=en:everted ears | n2=en:sensorineural hearing impairment (less common) | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:sensorineural hearing loss
n1=en:everted ears | n2=en:sensorineural hearing loss | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:sensorineural hearing loss, bilateral
n1=en:everted ears | n2=en:sensorineural hearing loss, bilateral | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:simple helix
n1=en:everted ears | n2=en:simple helix | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:squared-off ears
n1=en:everted ears | n2=en:squared-off ears | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:stiff, prominent pinnae
n1=en:everted ears | n2=en:stiff, prominent pinnae | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:superiorly displaced ears
n1=en:everted ears | n2=en:superiorly displaced ears | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:symmetric deterioration of hearing loss and speech reception with age
n1=en:everted ears | n2=en:symmetric deterioration of hearing loss and speech reception with age | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:vertigo, episodic
n1=en:everted ears | n2=en:vertigo, episodic | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
en:vestibular dysfunction (in some patients)
n1=en:everted ears | n2=en:vestibular dysfunction (in some patients) | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
lésion traumatique superficielle de l'oreille
n1=en:everted ears | n2=lésion traumatique superficielle de l'oreille | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
surdité congénitale
n1=en:everted ears | n2=surdité congénitale | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 26 / 0.605 ->
surdité héréditaire
n1=en:everted ears | n2=surdité héréditaire | rel=r_associated | relid=0 | w=26
- en:everted ears --
r_associated #0: 25 / 0.581 ->
perte d'audition sensorineurale
n1=en:everted ears | n2=perte d'audition sensorineurale | rel=r_associated | relid=0 | w=25
- en:everted ears --
r_associated #0: 25 / 0.581 ->
surdité du labyrinthe
n1=en:everted ears | n2=surdité du labyrinthe | rel=r_associated | relid=0 | w=25
- en:everted ears --
r_associated #0: 20 / 0.465 ->
déficience auditive
n1=en:everted ears | n2=déficience auditive | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:auditory canal stenosis
n1=en:everted ears | n2=en:auditory canal stenosis | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:balance problem
n1=en:everted ears | n2=en:balance problem | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:chronic otitis media (25%)
n1=en:everted ears | n2=en:chronic otitis media (25%) | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:cutlet
n1=en:everted ears | n2=en:cutlet | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:disorder of equilibrium
n1=en:everted ears | n2=en:disorder of equilibrium | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:dysplastic ears (jbts)
n1=en:everted ears | n2=en:dysplastic ears (jbts) | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:ENT doctor
n1=en:everted ears | n2=en:ENT doctor | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:ENT specialist
n1=en:everted ears | n2=en:ENT specialist | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:escalope
n1=en:everted ears | n2=en:escalope | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:glue ear
n1=en:everted ears | n2=en:glue ear | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:hearing impairment (1 patient)
n1=en:everted ears | n2=en:hearing impairment (1 patient) | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:hearing impairment, progressive (family a)
n1=en:everted ears | n2=en:hearing impairment, progressive (family a) | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:hearing loss (in 2 members of 1 family)
n1=en:everted ears | n2=en:hearing loss (in 2 members of 1 family) | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:hearing loss, sensorineural, progressive (all frequencies)
n1=en:everted ears | n2=en:hearing loss, sensorineural, progressive (all frequencies) | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:hereditary deafness
n1=en:everted ears | n2=en:hereditary deafness | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:microtia (in some patients)
n1=en:everted ears | n2=en:microtia (in some patients) | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:mild dysplasia of concha, unilateral
n1=en:everted ears | n2=en:mild dysplasia of concha, unilateral | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:no vestibular symptoms
n1=en:everted ears | n2=en:no vestibular symptoms | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:nose and throat specialist
n1=en:everted ears | n2=en:nose and throat specialist | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:otolaryngologist
n1=en:everted ears | n2=en:otolaryngologist | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:otorhinolaryngologist
n1=en:everted ears | n2=en:otorhinolaryngologist | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:problem with balance
n1=en:everted ears | n2=en:problem with balance | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:rotary vertigo
n1=en:everted ears | n2=en:rotary vertigo | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:serous otitis
n1=en:everted ears | n2=en:serous otitis | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
en:tinnitus, bilateral (in some patients)
n1=en:everted ears | n2=en:tinnitus, bilateral (in some patients) | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
esgourde
n1=en:everted ears | n2=esgourde | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
état nébuleux
n1=en:everted ears | n2=état nébuleux | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
état vertigineux
n1=en:everted ears | n2=état vertigineux | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
étourdissement
n1=en:everted ears | n2=étourdissement | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
hyperacousie
n1=en:everted ears | n2=hyperacousie | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
hyperacousies
n1=en:everted ears | n2=hyperacousies | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
hyperacusie
n1=en:everted ears | n2=hyperacusie | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
hyperlaxe
n1=en:everted ears | n2=hyperlaxe | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
hypermobile
n1=en:everted ears | n2=hypermobile | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
médecin ORL
n1=en:everted ears | n2=médecin ORL | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
otite séreuse
n1=en:everted ears | n2=otite séreuse | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
otite séromuqueuse
n1=en:everted ears | n2=otite séromuqueuse | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
oto-rhino
n1=en:everted ears | n2=oto-rhino | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
oto-rhino-laryngologiste
n1=en:everted ears | n2=oto-rhino-laryngologiste | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
otorhinolaryngologiste
n1=en:everted ears | n2=otorhinolaryngologiste | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
pavillon de l'oreille de morphologie rudimentaire
n1=en:everted ears | n2=pavillon de l'oreille de morphologie rudimentaire | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
sensation de rotation
n1=en:everted ears | n2=sensation de rotation | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
sensation de tournoiement
n1=en:everted ears | n2=sensation de tournoiement | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
sensation rotatoire
n1=en:everted ears | n2=sensation rotatoire | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
sensation vertigineuse
n1=en:everted ears | n2=sensation vertigineuse | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
sténose du canal auriculaire
n1=en:everted ears | n2=sténose du canal auriculaire | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
surdité neurosensorielle bilatérale
n1=en:everted ears | n2=surdité neurosensorielle bilatérale | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
tête pivotante
n1=en:everted ears | n2=tête pivotante | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
trouble de l'équilibre
n1=en:everted ears | n2=trouble de l'équilibre | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
vertige
n1=en:everted ears | n2=vertige | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
vertige rotatoire
n1=en:everted ears | n2=vertige rotatoire | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
vertige subjectif
n1=en:everted ears | n2=vertige subjectif | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
vertigo
n1=en:everted ears | n2=vertigo | rel=r_associated | relid=0 | w=20
- en:everted ears --
r_associated #0: 20 / 0.465 ->
vertigo rotatoire
n1=en:everted ears | n2=vertigo rotatoire | rel=r_associated | relid=0 | w=20
| ≈ 779 relations entrantes
- en:congenital deafness ---
r_associated #0: 300 -->
en:everted ears
n1=en:congenital deafness | n2=en:everted ears | rel=r_associated | relid=0 | w=300
- surdité congénitale ---
r_associated #0: 297 -->
en:everted ears
n1=surdité congénitale | n2=en:everted ears | rel=r_associated | relid=0 | w=297
- surdité héréditaire ---
r_associated #0: 295 -->
en:everted ears
n1=surdité héréditaire | n2=en:everted ears | rel=r_associated | relid=0 | w=295
- surdité du labyrinthe ---
r_associated #0: 271 -->
en:everted ears
n1=surdité du labyrinthe | n2=en:everted ears | rel=r_associated | relid=0 | w=271
- en:deafness labyrinthine ---
r_associated #0: 270 -->
en:everted ears
n1=en:deafness labyrinthine | n2=en:everted ears | rel=r_associated | relid=0 | w=270
- vertige rotatoire ---
r_associated #0: 235 -->
en:everted ears
n1=vertige rotatoire | n2=en:everted ears | rel=r_associated | relid=0 | w=235
- vertige subjectif ---
r_associated #0: 235 -->
en:everted ears
n1=vertige subjectif | n2=en:everted ears | rel=r_associated | relid=0 | w=235
- vertigo rotatoire ---
r_associated #0: 235 -->
en:everted ears
n1=vertigo rotatoire | n2=en:everted ears | rel=r_associated | relid=0 | w=235
- sensation de tournoiement ---
r_associated #0: 232 -->
en:everted ears
n1=sensation de tournoiement | n2=en:everted ears | rel=r_associated | relid=0 | w=232
- sensation de rotation ---
r_associated #0: 223 -->
en:everted ears
n1=sensation de rotation | n2=en:everted ears | rel=r_associated | relid=0 | w=223
- sensation vertigineuse ---
r_associated #0: 220 -->
en:everted ears
n1=sensation vertigineuse | n2=en:everted ears | rel=r_associated | relid=0 | w=220
- état nébuleux ---
r_associated #0: 220 -->
en:everted ears
n1=état nébuleux | n2=en:everted ears | rel=r_associated | relid=0 | w=220
- état vertigineux ---
r_associated #0: 220 -->
en:everted ears
n1=état vertigineux | n2=en:everted ears | rel=r_associated | relid=0 | w=220
- tête pivotante ---
r_associated #0: 215 -->
en:everted ears
n1=tête pivotante | n2=en:everted ears | rel=r_associated | relid=0 | w=215
- sensation rotatoire ---
r_associated #0: 214 -->
en:everted ears
n1=sensation rotatoire | n2=en:everted ears | rel=r_associated | relid=0 | w=214
- traumatisme superficiel oreille ---
r_associated #0: 190 -->
en:everted ears
n1=traumatisme superficiel oreille | n2=en:everted ears | rel=r_associated | relid=0 | w=190
- en:superficial injury of ear ---
r_associated #0: 187 -->
en:everted ears
n1=en:superficial injury of ear | n2=en:everted ears | rel=r_associated | relid=0 | w=187
- en:vertigo ---
r_associated #0: 168 -->
en:everted ears
n1=en:vertigo | n2=en:everted ears | rel=r_associated | relid=0 | w=168
- en:dizziness ---
r_associated #0: 165 -->
en:everted ears
n1=en:dizziness | n2=en:everted ears | rel=r_associated | relid=0 | w=165
- hyperacousie ---
r_associated #0: 140 -->
en:everted ears
n1=hyperacousie | n2=en:everted ears | rel=r_associated | relid=0 | w=140
- hyperacusie ---
r_associated #0: 140 -->
en:everted ears
n1=hyperacusie | n2=en:everted ears | rel=r_associated | relid=0 | w=140
- en:hyperacusis ---
r_associated #0: 137 -->
en:everted ears
n1=en:hyperacusis | n2=en:everted ears | rel=r_associated | relid=0 | w=137
- vertigo ---
r_associated #0: 132 -->
en:everted ears
n1=vertigo | n2=en:everted ears | rel=r_associated | relid=0 | w=132
- hyperacousies ---
r_associated #0: 120 -->
en:everted ears
n1=hyperacousies | n2=en:everted ears | rel=r_associated | relid=0 | w=120
- en:balance problem ---
r_associated #0: 115 -->
en:everted ears
n1=en:balance problem | n2=en:everted ears | rel=r_associated | relid=0 | w=115
- en:disorder of equilibrium ---
r_associated #0: 115 -->
en:everted ears
n1=en:disorder of equilibrium | n2=en:everted ears | rel=r_associated | relid=0 | w=115
- en:problem with balance ---
r_associated #0: 115 -->
en:everted ears
n1=en:problem with balance | n2=en:everted ears | rel=r_associated | relid=0 | w=115
- trouble de l'équilibre ---
r_associated #0: 115 -->
en:everted ears
n1=trouble de l'équilibre | n2=en:everted ears | rel=r_associated | relid=0 | w=115
- vertige ---
r_associated #0: 95 -->
en:everted ears
n1=vertige | n2=en:everted ears | rel=r_associated | relid=0 | w=95
- étourdissement ---
r_associated #0: 79 -->
en:everted ears
n1=étourdissement | n2=en:everted ears | rel=r_associated | relid=0 | w=79
- en:secretory otitis media ---
r_associated #0: 59 -->
en:everted ears
n1=en:secretory otitis media | n2=en:everted ears | rel=r_associated | relid=0 | w=59
- en:stenosis of external auditory canal ---
r_associated #0: 58 -->
en:everted ears
n1=en:stenosis of external auditory canal | n2=en:everted ears | rel=r_associated | relid=0 | w=58
- lésion traumatique superficielle de l'oreille ---
r_associated #0: 58 -->
en:everted ears
n1=lésion traumatique superficielle de l'oreille | n2=en:everted ears | rel=r_associated | relid=0 | w=58
- en:serous otitis media ---
r_associated #0: 55 -->
en:everted ears
n1=en:serous otitis media | n2=en:everted ears | rel=r_associated | relid=0 | w=55
- sténose du canal auriculaire ---
r_associated #0: 55 -->
en:everted ears
n1=sténose du canal auriculaire | n2=en:everted ears | rel=r_associated | relid=0 | w=55
- otite séromuqueuse ---
r_associated #0: 54 -->
en:everted ears
n1=otite séromuqueuse | n2=en:everted ears | rel=r_associated | relid=0 | w=54
- otite moyenne séreuse ---
r_associated #0: 50 -->
en:everted ears
n1=otite moyenne séreuse | n2=en:everted ears | rel=r_associated | relid=0 | w=50
- déficience auditive ---
r_associated #0: 47 -->
en:everted ears
n1=déficience auditive | n2=en:everted ears | rel=r_associated | relid=0 | w=47
- en:hereditary deafness ---
r_associated #0: 47 -->
en:everted ears
n1=en:hereditary deafness | n2=en:everted ears | rel=r_associated | relid=0 | w=47
- oto-rhino-laryngologiste ---
r_associated #0: 45 -->
en:everted ears
n1=oto-rhino-laryngologiste | n2=en:everted ears | rel=r_associated | relid=0 | w=45
- en:hearing impairment ---
r_associated #0: 44 -->
en:everted ears
n1=en:hearing impairment | n2=en:everted ears | rel=r_associated | relid=0 | w=44
- en:abnormally formed ears ---
r_associated #0: 43 -->
en:everted ears
n1=en:abnormally formed ears | n2=en:everted ears | rel=r_associated | relid=0 | w=43
- otorhinolaryngologiste ---
r_associated #0: 43 -->
en:everted ears
n1=otorhinolaryngologiste | n2=en:everted ears | rel=r_associated | relid=0 | w=43
- en:neural hearing loss ---
r_associated #0: 42 -->
en:everted ears
n1=en:neural hearing loss | n2=en:everted ears | rel=r_associated | relid=0 | w=42
- en:rudimentary ear ---
r_associated #0: 42 -->
en:everted ears
n1=en:rudimentary ear | n2=en:everted ears | rel=r_associated | relid=0 | w=42
- en:deafness, conductive (in some patients) ---
r_associated #0: 41 -->
en:everted ears
n1=en:deafness, conductive (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=41
- en:hyperfolded ears ---
r_associated #0: 41 -->
en:everted ears
n1=en:hyperfolded ears | n2=en:everted ears | rel=r_associated | relid=0 | w=41
- en:low-frequency conductive hearing loss ---
r_associated #0: 41 -->
en:everted ears
n1=en:low-frequency conductive hearing loss | n2=en:everted ears | rel=r_associated | relid=0 | w=41
- en:sensorineural hearing impairment (in some patients) ---
r_associated #0: 41 -->
en:everted ears
n1=en:sensorineural hearing impairment (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=41
- en:auricular clefts ---
r_associated #0: 40 -->
en:everted ears
n1=en:auricular clefts | n2=en:everted ears | rel=r_associated | relid=0 | w=40
- en:conductive hearing loss (in a subset of patients) ---
r_associated #0: 40 -->
en:everted ears
n1=en:conductive hearing loss (in a subset of patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=40
- en:decreased otoacoustic emission amplitude ---
r_associated #0: 40 -->
en:everted ears
n1=en:decreased otoacoustic emission amplitude | n2=en:everted ears | rel=r_associated | relid=0 | w=40
- en:flat ears ---
r_associated #0: 40 -->
en:everted ears
n1=en:flat ears | n2=en:everted ears | rel=r_associated | relid=0 | w=40
- en:large, low-set ears ---
r_associated #0: 40 -->
en:everted ears
n1=en:large, low-set ears | n2=en:everted ears | rel=r_associated | relid=0 | w=40
- en:recurrent ear infections ---
r_associated #0: 40 -->
en:everted ears
n1=en:recurrent ear infections | n2=en:everted ears | rel=r_associated | relid=0 | w=40
- en:unravelling of superior helices ---
r_associated #0: 40 -->
en:everted ears
n1=en:unravelling of superior helices | n2=en:everted ears | rel=r_associated | relid=0 | w=40
- oto-rhino ---
r_associated #0: 40 -->
en:everted ears
n1=oto-rhino | n2=en:everted ears | rel=r_associated | relid=0 | w=40
- en:ENT doctor ---
r_associated #0: 39 -->
en:everted ears
n1=en:ENT doctor | n2=en:everted ears | rel=r_associated | relid=0 | w=39
- en:absent vestibular function (caloric test) ---
r_associated #0: 39 -->
en:everted ears
n1=en:absent vestibular function (caloric test) | n2=en:everted ears | rel=r_associated | relid=0 | w=39
- en:angular ears ---
r_associated #0: 39 -->
en:everted ears
n1=en:angular ears | n2=en:everted ears | rel=r_associated | relid=0 | w=39
- en:malformed earlobes ---
r_associated #0: 39 -->
en:everted ears
n1=en:malformed earlobes | n2=en:everted ears | rel=r_associated | relid=0 | w=39
- en:small external auditory canals ---
r_associated #0: 39 -->
en:everted ears
n1=en:small external auditory canals | n2=en:everted ears | rel=r_associated | relid=0 | w=39
- en:tinnitus, bilateral (in some patients) ---
r_associated #0: 39 -->
en:everted ears
n1=en:tinnitus, bilateral (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=39
- en:vestibulopathy, bilateral, progressive ---
r_associated #0: 39 -->
en:everted ears
n1=en:vestibulopathy, bilateral, progressive | n2=en:everted ears | rel=r_associated | relid=0 | w=39
- surdimutité ---
r_associated #0: 39 -->
en:everted ears
n1=surdimutité | n2=en:everted ears | rel=r_associated | relid=0 | w=39
- en:absence of earlobe ---
r_associated #0: 38 -->
en:everted ears
n1=en:absence of earlobe | n2=en:everted ears | rel=r_associated | relid=0 | w=38
- en:absence of the helix and distal scapha in middle third of the ear ---
r_associated #0: 38 -->
en:everted ears
n1=en:absence of the helix and distal scapha in middle third of the ear | n2=en:everted ears | rel=r_associated | relid=0 | w=38
- en:hearing impairment, sensorineural, fluctuating ---
r_associated #0: 38 -->
en:everted ears
n1=en:hearing impairment, sensorineural, fluctuating | n2=en:everted ears | rel=r_associated | relid=0 | w=38
- en:hearing loss (cvs+) ---
r_associated #0: 38 -->
en:everted ears
n1=en:hearing loss (cvs+) | n2=en:everted ears | rel=r_associated | relid=0 | w=38
- en:otitis externa, recurrent, due to infection with staphylococcus aureus ---
r_associated #0: 38 -->
en:everted ears
n1=en:otitis externa, recurrent, due to infection with staphylococcus aureus | n2=en:everted ears | rel=r_associated | relid=0 | w=38
- en:sensorineural hearing impairment (less common) ---
r_associated #0: 38 -->
en:everted ears
n1=en:sensorineural hearing impairment (less common) | n2=en:everted ears | rel=r_associated | relid=0 | w=38
- en:abnormal bridge connecting the crus of the helix and antihelix ---
r_associated #0: 37 -->
en:everted ears
n1=en:abnormal bridge connecting the crus of the helix and antihelix | n2=en:everted ears | rel=r_associated | relid=0 | w=37
- en:cupped pinna ---
r_associated #0: 37 -->
en:everted ears
n1=en:cupped pinna | n2=en:everted ears | rel=r_associated | relid=0 | w=37
- en:deafness, sensorineural, profound ---
r_associated #0: 37 -->
en:everted ears
n1=en:deafness, sensorineural, profound | n2=en:everted ears | rel=r_associated | relid=0 | w=37
- en:hearing impairment (in 1/4 patients) ---
r_associated #0: 37 -->
en:everted ears
n1=en:hearing impairment (in 1/4 patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=37
- en:rotary vertigo ---
r_associated #0: 37 -->
en:everted ears
n1=en:rotary vertigo | n2=en:everted ears | rel=r_associated | relid=0 | w=37
- en:sensorineural hearing loss, mild (rare) ---
r_associated #0: 37 -->
en:everted ears
n1=en:sensorineural hearing loss, mild (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=37
- en:bilateral dys-synchronized auditory brainstem responses ---
r_associated #0: 36 -->
en:everted ears
n1=en:bilateral dys-synchronized auditory brainstem responses | n2=en:everted ears | rel=r_associated | relid=0 | w=36
- en:conductive hearing loss ---
r_associated #0: 36 -->
en:everted ears
n1=en:conductive hearing loss | n2=en:everted ears | rel=r_associated | relid=0 | w=36
- en:downward sloping audiogram ---
r_associated #0: 36 -->
en:everted ears
n1=en:downward sloping audiogram | n2=en:everted ears | rel=r_associated | relid=0 | w=36
- en:hearing loss, sensorineural, bilateral, moderate-to-severe ---
r_associated #0: 36 -->
en:everted ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:everted ears | rel=r_associated | relid=0 | w=36
- en:hypermobile ---
r_associated #0: 36 -->
en:everted ears
n1=en:hypermobile | n2=en:everted ears | rel=r_associated | relid=0 | w=36
- en:michel aplasia (complete absence of inner ear structures) ---
r_associated #0: 36 -->
en:everted ears
n1=en:michel aplasia (complete absence of inner ear structures) | n2=en:everted ears | rel=r_associated | relid=0 | w=36
- en:profound deafness ---
r_associated #0: 36 -->
en:everted ears
n1=en:profound deafness | n2=en:everted ears | rel=r_associated | relid=0 | w=36
- otite séreuse ---
r_associated #0: 36 -->
en:everted ears
n1=otite séreuse | n2=en:everted ears | rel=r_associated | relid=0 | w=36
- en:ENT specialist ---
r_associated #0: 35 -->
en:everted ears
n1=en:ENT specialist | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:absent external auditory canals ---
r_associated #0: 35 -->
en:everted ears
n1=en:absent external auditory canals | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:absent helices, bilaterally ---
r_associated #0: 35 -->
en:everted ears
n1=en:absent helices, bilaterally | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:absent lobules ---
r_associated #0: 35 -->
en:everted ears
n1=en:absent lobules | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss) ---
r_associated #0: 35 -->
en:everted ears
n1=en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss) | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:cup-shaped ears (30-60% of patients) ---
r_associated #0: 35 -->
en:everted ears
n1=en:cup-shaped ears (30-60% of patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:deafness (in some patients) ---
r_associated #0: 35 -->
en:everted ears
n1=en:deafness (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:deafness, early-onset ---
r_associated #0: 35 -->
en:everted ears
n1=en:deafness, early-onset | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:deafness, sensorineural (reported in 1 family) ---
r_associated #0: 35 -->
en:everted ears
n1=en:deafness, sensorineural (reported in 1 family) | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:deafness, sensorineural, prelingual, profound ---
r_associated #0: 35 -->
en:everted ears
n1=en:deafness, sensorineural, prelingual, profound | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea ---
r_associated #0: 35 -->
en:everted ears
n1=en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:dysmorphic ears ---
r_associated #0: 35 -->
en:everted ears
n1=en:dysmorphic ears | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:ears deficient in cartilage ---
r_associated #0: 35 -->
en:everted ears
n1=en:ears deficient in cartilage | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:endolymphatic sac tumors (elsts) ---
r_associated #0: 35 -->
en:everted ears
n1=en:endolymphatic sac tumors (elsts) | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:enlarged vestibular aqueduct ---
r_associated #0: 35 -->
en:everted ears
n1=en:enlarged vestibular aqueduct | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:flattened antihelix ---
r_associated #0: 35 -->
en:everted ears
n1=en:flattened antihelix | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:hearing impairment, progressive (family a) ---
r_associated #0: 35 -->
en:everted ears
n1=en:hearing impairment, progressive (family a) | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:hearing loss (in 2 members of 1 family) ---
r_associated #0: 35 -->
en:everted ears
n1=en:hearing loss (in 2 members of 1 family) | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:hearing loss first affects high frequencies ---
r_associated #0: 35 -->
en:everted ears
n1=en:hearing loss first affects high frequencies | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:hearing loss, congenital profound ---
r_associated #0: 35 -->
en:everted ears
n1=en:hearing loss, congenital profound | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural (in 2 patients) ---
r_associated #0: 35 -->
en:everted ears
n1=en:hearing loss, sensorineural (in 2 patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, moderate, postlingual ---
r_associated #0: 35 -->
en:everted ears
n1=en:hearing loss, sensorineural, moderate, postlingual | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:large ear pinnae ---
r_associated #0: 35 -->
en:everted ears
n1=en:large ear pinnae | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:large earlobe ---
r_associated #0: 35 -->
en:everted ears
n1=en:large earlobe | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:large ears (37%) ---
r_associated #0: 35 -->
en:everted ears
n1=en:large ears (37%) | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:large prominent ears ---
r_associated #0: 35 -->
en:everted ears
n1=en:large prominent ears | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:large, floppy ears ---
r_associated #0: 35 -->
en:everted ears
n1=en:large, floppy ears | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:lobule creases ---
r_associated #0: 35 -->
en:everted ears
n1=en:lobule creases | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:loss of hearing (45%) ---
r_associated #0: 35 -->
en:everted ears
n1=en:loss of hearing (45%) | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:loss of mid- and low-frequencies later ---
r_associated #0: 35 -->
en:everted ears
n1=en:loss of mid- and low-frequencies later | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:low-set ears (28%) ---
r_associated #0: 35 -->
en:everted ears
n1=en:low-set ears (28%) | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:mild dysplasia of concha, unilateral ---
r_associated #0: 35 -->
en:everted ears
n1=en:mild dysplasia of concha, unilateral | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:mild to moderate hearing loss ---
r_associated #0: 35 -->
en:everted ears
n1=en:mild to moderate hearing loss | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:neonatal cystic lesions of the pinnae ---
r_associated #0: 35 -->
en:everted ears
n1=en:neonatal cystic lesions of the pinnae | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:no deafness ---
r_associated #0: 35 -->
en:everted ears
n1=en:no deafness | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:nonprogressive deafness ---
r_associated #0: 35 -->
en:everted ears
n1=en:nonprogressive deafness | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:normal vestibular function ---
r_associated #0: 35 -->
en:everted ears
n1=en:normal vestibular function | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:nose and throat specialist ---
r_associated #0: 35 -->
en:everted ears
n1=en:nose and throat specialist | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:poorly shaped ears ---
r_associated #0: 35 -->
en:everted ears
n1=en:poorly shaped ears | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:posteriorly rotated ears (2p21del) ---
r_associated #0: 35 -->
en:everted ears
n1=en:posteriorly rotated ears (2p21del) | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:retroverted ears ---
r_associated #0: 35 -->
en:everted ears
n1=en:retroverted ears | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:rudimentary tympanic membrane (in some patients) ---
r_associated #0: 35 -->
en:everted ears
n1=en:rudimentary tympanic membrane (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:sensorineural deafness, variable (in 1 family) ---
r_associated #0: 35 -->
en:everted ears
n1=en:sensorineural deafness, variable (in 1 family) | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:sensorineural hearing loss (early-onset form) ---
r_associated #0: 35 -->
en:everted ears
n1=en:sensorineural hearing loss (early-onset form) | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:sensorineural hearing loss (uncommon) ---
r_associated #0: 35 -->
en:everted ears
n1=en:sensorineural hearing loss (uncommon) | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:sensorineural hearing loss, bilateral ---
r_associated #0: 35 -->
en:everted ears
n1=en:sensorineural hearing loss, bilateral | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:severe loss in the higher frequencies by the fifth decade ---
r_associated #0: 35 -->
en:everted ears
n1=en:severe loss in the higher frequencies by the fifth decade | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:severe narrowing of cartilagenous auditory canal ---
r_associated #0: 35 -->
en:everted ears
n1=en:severe narrowing of cartilagenous auditory canal | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:small auricles ---
r_associated #0: 35 -->
en:everted ears
n1=en:small auricles | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:small ears with large lobules ---
r_associated #0: 35 -->
en:everted ears
n1=en:small ears with large lobules | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:small external auditory meatus ---
r_associated #0: 35 -->
en:everted ears
n1=en:small external auditory meatus | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:soft auricles ---
r_associated #0: 35 -->
en:everted ears
n1=en:soft auricles | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:superiorly displaced ears ---
r_associated #0: 35 -->
en:everted ears
n1=en:superiorly displaced ears | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:upsloping audiograms ---
r_associated #0: 35 -->
en:everted ears
n1=en:upsloping audiograms | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:upturned lobes ---
r_associated #0: 35 -->
en:everted ears
n1=en:upturned lobes | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:wide bulbous internal auditory meatus ---
r_associated #0: 35 -->
en:everted ears
n1=en:wide bulbous internal auditory meatus | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- surdi-mutité ---
r_associated #0: 35 -->
en:everted ears
n1=surdi-mutité | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- surdité neurosensorielle bilatérale ---
r_associated #0: 35 -->
en:everted ears
n1=surdité neurosensorielle bilatérale | n2=en:everted ears | rel=r_associated | relid=0 | w=35
- en:'tilted' ears ---
r_associated #0: 34 -->
en:everted ears
n1=en:'tilted' ears | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:abnormal brain auditory evoked responses (baer) ---
r_associated #0: 34 -->
en:everted ears
n1=en:abnormal brain auditory evoked responses (baer) | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:abnormally folded helix ---
r_associated #0: 34 -->
en:everted ears
n1=en:abnormally folded helix | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile) ---
r_associated #0: 34 -->
en:everted ears
n1=en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile) | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:conductive hearing loss to due otitis media ---
r_associated #0: 34 -->
en:everted ears
n1=en:conductive hearing loss to due otitis media | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:deafness affects all frequencies ---
r_associated #0: 34 -->
en:everted ears
n1=en:deafness affects all frequencies | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:deafness, congenital sensorineural, profound (in some patients) ---
r_associated #0: 34 -->
en:everted ears
n1=en:deafness, congenital sensorineural, profound (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:deafness, sensorineural, profound (prelingual onset) ---
r_associated #0: 34 -->
en:everted ears
n1=en:deafness, sensorineural, profound (prelingual onset) | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v ---
r_associated #0: 34 -->
en:everted ears
n1=en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:deficient auricle ---
r_associated #0: 34 -->
en:everted ears
n1=en:deficient auricle | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:dysplastic ears (jbts) ---
r_associated #0: 34 -->
en:everted ears
n1=en:dysplastic ears (jbts) | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:ear ---
r_associated #0: 34 -->
en:everted ears
n1=en:ear | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:ear cartilage calcification ---
r_associated #0: 34 -->
en:everted ears
n1=en:ear cartilage calcification | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:ear pits, posterior helical ---
r_associated #0: 34 -->
en:everted ears
n1=en:ear pits, posterior helical | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:external auditory canal narrow ---
r_associated #0: 34 -->
en:everted ears
n1=en:external auditory canal narrow | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:hearing loss (affecting all frequencies), moderate to severe ---
r_associated #0: 34 -->
en:everted ears
n1=en:hearing loss (affecting all frequencies), moderate to severe | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:hearing loss, congenital sensorineural, moderate-severe ---
r_associated #0: 34 -->
en:everted ears
n1=en:hearing loss, congenital sensorineural, moderate-severe | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:hearing loss, high frequency, slowly progressive (onset in early childhood) ---
r_associated #0: 34 -->
en:everted ears
n1=en:hearing loss, high frequency, slowly progressive (onset in early childhood) | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:hearing loss, severe to profound, affecting all frequencies ---
r_associated #0: 34 -->
en:everted ears
n1=en:hearing loss, severe to profound, affecting all frequencies | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:high-frequency tinnitus at onset ---
r_associated #0: 34 -->
en:everted ears
n1=en:high-frequency tinnitus at onset | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:hypoplastic helices ---
r_associated #0: 34 -->
en:everted ears
n1=en:hypoplastic helices | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:incomplete separation of the cochlea from the internal auditory canal ---
r_associated #0: 34 -->
en:everted ears
n1=en:incomplete separation of the cochlea from the internal auditory canal | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:large anteverted ears ---
r_associated #0: 34 -->
en:everted ears
n1=en:large anteverted ears | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:large fleshy ears ---
r_associated #0: 34 -->
en:everted ears
n1=en:large fleshy ears | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:low-set, malformed ears ---
r_associated #0: 34 -->
en:everted ears
n1=en:low-set, malformed ears | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:overfolded helix ---
r_associated #0: 34 -->
en:everted ears
n1=en:overfolded helix | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:poorly formed ears ---
r_associated #0: 34 -->
en:everted ears
n1=en:poorly formed ears | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:posterior helical indentations ---
r_associated #0: 34 -->
en:everted ears
n1=en:posterior helical indentations | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:posteriorly rotated ears (female) ---
r_associated #0: 34 -->
en:everted ears
n1=en:posteriorly rotated ears (female) | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:pre- and post-auricular skin or cartilaginous tags ---
r_associated #0: 34 -->
en:everted ears
n1=en:pre- and post-auricular skin or cartilaginous tags | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:preauricular sinus, bilateral ---
r_associated #0: 34 -->
en:everted ears
n1=en:preauricular sinus, bilateral | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:recurrent otitis media in infancy and childhood ---
r_associated #0: 34 -->
en:everted ears
n1=en:recurrent otitis media in infancy and childhood | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:sensorineural hearing loss (onset early childhood) ---
r_associated #0: 34 -->
en:everted ears
n1=en:sensorineural hearing loss (onset early childhood) | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:small pinna ---
r_associated #0: 34 -->
en:everted ears
n1=en:small pinna | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:small, simple ears ---
r_associated #0: 34 -->
en:everted ears
n1=en:small, simple ears | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:strabismus (in some patients) ---
r_associated #0: 34 -->
en:everted ears
n1=en:strabismus (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:thickened helices ---
r_associated #0: 34 -->
en:everted ears
n1=en:thickened helices | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:triangular-shaped ears ---
r_associated #0: 34 -->
en:everted ears
n1=en:triangular-shaped ears | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:underfolded helix ---
r_associated #0: 34 -->
en:everted ears
n1=en:underfolded helix | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:vertigo, episodic ---
r_associated #0: 34 -->
en:everted ears
n1=en:vertigo, episodic | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:vestibular dysfunction (in some patients) ---
r_associated #0: 34 -->
en:everted ears
n1=en:vestibular dysfunction (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:vestibular hypofunction (rare) ---
r_associated #0: 34 -->
en:everted ears
n1=en:vestibular hypofunction (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=34
- en:abnormal communication between the subarachnoid space in the meatus and the perilymph ---
r_associated #0: 32 -->
en:everted ears
n1=en:abnormal communication between the subarachnoid space in the meatus and the perilymph | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:absent external auditory meatus ---
r_associated #0: 32 -->
en:everted ears
n1=en:absent external auditory meatus | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:air-bone gap of greater than 20 db across 0.5 to 2 khz ---
r_associated #0: 32 -->
en:everted ears
n1=en:air-bone gap of greater than 20 db across 0.5 to 2 khz | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:anterior creases of earlobe ---
r_associated #0: 32 -->
en:everted ears
n1=en:anterior creases of earlobe | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:approximately 0.7db per year hearing loss at all frequencies ---
r_associated #0: 32 -->
en:everted ears
n1=en:approximately 0.7db per year hearing loss at all frequencies | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:atretic auditory canal ---
r_associated #0: 32 -->
en:everted ears
n1=en:atretic auditory canal | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:atrophy of cochlear and vestibular fibrocytes ---
r_associated #0: 32 -->
en:everted ears
n1=en:atrophy of cochlear and vestibular fibrocytes | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:aural fullness ---
r_associated #0: 32 -->
en:everted ears
n1=en:aural fullness | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:conductive hearing loss, mild bilateral (rare) ---
r_associated #0: 32 -->
en:everted ears
n1=en:conductive hearing loss, mild bilateral (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:cupped ears (in some patients) ---
r_associated #0: 32 -->
en:everted ears
n1=en:cupped ears (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:deafness (often in third decade) ---
r_associated #0: 32 -->
en:everted ears
n1=en:deafness (often in third decade) | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:deafness (variable) ---
r_associated #0: 32 -->
en:everted ears
n1=en:deafness (variable) | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:deafness, congenital sensorineural, severe to profound ---
r_associated #0: 32 -->
en:everted ears
n1=en:deafness, congenital sensorineural, severe to profound | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:deafness, early-onset mixed conductive and sensorineural ---
r_associated #0: 32 -->
en:everted ears
n1=en:deafness, early-onset mixed conductive and sensorineural | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:dysplastic helices ---
r_associated #0: 32 -->
en:everted ears
n1=en:dysplastic helices | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:ear tag ---
r_associated #0: 32 -->
en:everted ears
n1=en:ear tag | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:endolymphatic hydrops, delayed onset ---
r_associated #0: 32 -->
en:everted ears
n1=en:endolymphatic hydrops, delayed onset | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:fleshy and overfolded helices ---
r_associated #0: 32 -->
en:everted ears
n1=en:fleshy and overfolded helices | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:folded superior edge of helix ---
r_associated #0: 32 -->
en:everted ears
n1=en:folded superior edge of helix | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:hearing loss, mixed (in some patients) ---
r_associated #0: 32 -->
en:everted ears
n1=en:hearing loss, mixed (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:hearing loss, progressive (in some patients) ---
r_associated #0: 32 -->
en:everted ears
n1=en:hearing loss, progressive (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, progressive (all frequencies) ---
r_associated #0: 32 -->
en:everted ears
n1=en:hearing loss, sensorineural, progressive (all frequencies) | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:hypoplastic ear lobes ---
r_associated #0: 32 -->
en:everted ears
n1=en:hypoplastic ear lobes | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients) ---
r_associated #0: 32 -->
en:everted ears
n1=en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:large dysplastic ears ---
r_associated #0: 32 -->
en:everted ears
n1=en:large dysplastic ears | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:large simple ears ---
r_associated #0: 32 -->
en:everted ears
n1=en:large simple ears | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:mild hearing impairment (13%) ---
r_associated #0: 32 -->
en:everted ears
n1=en:mild hearing impairment (13%) | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:mild to moderate hearing loss across most frequencies ---
r_associated #0: 32 -->
en:everted ears
n1=en:mild to moderate hearing loss across most frequencies | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:no auditory brainstem response (abr) ---
r_associated #0: 32 -->
en:everted ears
n1=en:no auditory brainstem response (abr) | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:normal outer hair cell functions ---
r_associated #0: 32 -->
en:everted ears
n1=en:normal outer hair cell functions | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:oae responses may decrease with age or use of hearing aids ---
r_associated #0: 32 -->
en:everted ears
n1=en:oae responses may decrease with age or use of hearing aids | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances ---
r_associated #0: 32 -->
en:everted ears
n1=en:otoneurologic disturbances | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:outer ear abnormalities (deletion patients) prominent ears ---
r_associated #0: 32 -->
en:everted ears
n1=en:outer ear abnormalities (deletion patients) prominent ears | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:poorly folded ears ---
r_associated #0: 32 -->
en:everted ears
n1=en:poorly folded ears | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:progressive conductive hearing impairment ---
r_associated #0: 32 -->
en:everted ears
n1=en:progressive conductive hearing impairment | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:progressive hearing loss (in some) ---
r_associated #0: 32 -->
en:everted ears
n1=en:progressive hearing loss (in some) | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:progressive mixed conductive and sensorineural hearing loss ---
r_associated #0: 32 -->
en:everted ears
n1=en:progressive mixed conductive and sensorineural hearing loss | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:prominence and protrusion of upper third of the ear ---
r_associated #0: 32 -->
en:everted ears
n1=en:prominence and protrusion of upper third of the ear | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:prominent ear ---
r_associated #0: 32 -->
en:everted ears
n1=en:prominent ear | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:raised earlobes ---
r_associated #0: 32 -->
en:everted ears
n1=en:raised earlobes | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:relatively long ears ---
r_associated #0: 32 -->
en:everted ears
n1=en:relatively long ears | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:satyr ear ---
r_associated #0: 32 -->
en:everted ears
n1=en:satyr ear | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:sclerosis of semicircular canals ---
r_associated #0: 32 -->
en:everted ears
n1=en:sclerosis of semicircular canals | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:sensorineural deafness (reported in 1 family) ---
r_associated #0: 32 -->
en:everted ears
n1=en:sensorineural deafness (reported in 1 family) | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:simplified helices ---
r_associated #0: 32 -->
en:everted ears
n1=en:simplified helices | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:superior semicircular canal dehiscence syndrome ---
r_associated #0: 32 -->
en:everted ears
n1=en:superior semicircular canal dehiscence syndrome | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:symmetric deterioration of hearing loss and speech reception with age ---
r_associated #0: 32 -->
en:everted ears
n1=en:symmetric deterioration of hearing loss and speech reception with age | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves ---
r_associated #0: 32 -->
en:everted ears
n1=en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:unilateral external ear deformity ---
r_associated #0: 32 -->
en:everted ears
n1=en:unilateral external ear deformity | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:vestibular function defect (decreased in some, normal in other patients) ---
r_associated #0: 32 -->
en:everted ears
n1=en:vestibular function defect (decreased in some, normal in other patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- hypermobile ---
r_associated #0: 32 -->
en:everted ears
n1=hypermobile | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:a subset of patients have hearing loss ---
r_associated #0: 31 -->
en:everted ears
n1=en:a subset of patients have hearing loss | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:abnormal ear configuration ---
r_associated #0: 31 -->
en:everted ears
n1=en:abnormal ear configuration | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:acoustic trauma ---
r_associated #0: 31 -->
en:everted ears
n1=en:acoustic trauma | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:affects all frequencies ---
r_associated #0: 31 -->
en:everted ears
n1=en:affects all frequencies | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient) ---
r_associated #0: 31 -->
en:everted ears
n1=en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient) | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:attached ear lobules ---
r_associated #0: 31 -->
en:everted ears
n1=en:attached ear lobules | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:aural atresia, congenital ---
r_associated #0: 31 -->
en:everted ears
n1=en:aural atresia, congenital | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:bilateral sensorineural hearing loss (in some patients) ---
r_associated #0: 31 -->
en:everted ears
n1=en:bilateral sensorineural hearing loss (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:congenital hearing loss (1 family) ---
r_associated #0: 31 -->
en:everted ears
n1=en:congenital hearing loss (1 family) | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:congenital sensorineural hearing loss ---
r_associated #0: 31 -->
en:everted ears
n1=en:congenital sensorineural hearing loss | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:cup-shaped auricles ---
r_associated #0: 31 -->
en:everted ears
n1=en:cup-shaped auricles | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:deafness, postlingual ---
r_associated #0: 31 -->
en:everted ears
n1=en:deafness, postlingual | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:deafness, secondary to cranial hyperostosis ---
r_associated #0: 31 -->
en:everted ears
n1=en:deafness, secondary to cranial hyperostosis | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:ear pain/earache ---
r_associated #0: 31 -->
en:everted ears
n1=en:ear pain/earache | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:hearing impairment, asymmetric (in some patients with hsan2d) ---
r_associated #0: 31 -->
en:everted ears
n1=en:hearing impairment, asymmetric (in some patients with hsan2d) | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:hearing loss, late-onset sensorineural, mild-to moderate (less common) ---
r_associated #0: 31 -->
en:everted ears
n1=en:hearing loss, late-onset sensorineural, mild-to moderate (less common) | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:hearing loss, mild (rare) ---
r_associated #0: 31 -->
en:everted ears
n1=en:hearing loss, mild (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, mild progressive (in some patients) ---
r_associated #0: 31 -->
en:everted ears
n1=en:hearing loss, sensorineural, mild progressive (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:large, prominent ears (59%) ---
r_associated #0: 31 -->
en:everted ears
n1=en:large, prominent ears (59%) | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:long and prominent ear crus ---
r_associated #0: 31 -->
en:everted ears
n1=en:long and prominent ear crus | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:low-set ears (45%) ---
r_associated #0: 31 -->
en:everted ears
n1=en:low-set ears (45%) | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:low-set ears (severe form) ---
r_associated #0: 31 -->
en:everted ears
n1=en:low-set ears (severe form) | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:malformed ossicular chain ---
r_associated #0: 31 -->
en:everted ears
n1=en:malformed ossicular chain | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:microtia, type i ---
r_associated #0: 31 -->
en:everted ears
n1=en:microtia, type i | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:narrow intertragic notch ---
r_associated #0: 31 -->
en:everted ears
n1=en:narrow intertragic notch | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:no hearing loss ---
r_associated #0: 31 -->
en:everted ears
n1=en:no hearing loss | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:occasional conductive hearing loss ---
r_associated #0: 31 -->
en:everted ears
n1=en:occasional conductive hearing loss | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:ossified pinnae ---
r_associated #0: 31 -->
en:everted ears
n1=en:ossified pinnae | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:partial hearing loss ---
r_associated #0: 31 -->
en:everted ears
n1=en:partial hearing loss | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:preauricular fistulas, bilateral ---
r_associated #0: 31 -->
en:everted ears
n1=en:preauricular fistulas, bilateral | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:prolonged brainstem auditory evoked potentials (baep) ---
r_associated #0: 31 -->
en:everted ears
n1=en:prolonged brainstem auditory evoked potentials (baep) | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:pseudomembranous inflammation of the middle ear ---
r_associated #0: 31 -->
en:everted ears
n1=en:pseudomembranous inflammation of the middle ear | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:pulsatile tinnitus (tympanic paraganglioma) ---
r_associated #0: 31 -->
en:everted ears
n1=en:pulsatile tinnitus (tympanic paraganglioma) | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:severe to profound deafness ---
r_associated #0: 31 -->
en:everted ears
n1=en:severe to profound deafness | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:severe to profound hearing impairment by early adulthood ---
r_associated #0: 31 -->
en:everted ears
n1=en:severe to profound hearing impairment by early adulthood | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:short ear ---
r_associated #0: 31 -->
en:everted ears
n1=en:short ear | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:small triangular pinnae ---
r_associated #0: 31 -->
en:everted ears
n1=en:small triangular pinnae | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:structure of superior auricularis muscle ---
r_associated #0: 31 -->
en:everted ears
n1=en:structure of superior auricularis muscle | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:u-shaped audiogram ---
r_associated #0: 31 -->
en:everted ears
n1=en:u-shaped audiogram | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:wide, flattened earlobes ---
r_associated #0: 31 -->
en:everted ears
n1=en:wide, flattened earlobes | n2=en:everted ears | rel=r_associated | relid=0 | w=31
- en:abnormal auditory brainstem responses ---
r_associated #0: 30 -->
en:everted ears
n1=en:abnormal auditory brainstem responses | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:abnormal speech discrimination ---
r_associated #0: 30 -->
en:everted ears
n1=en:abnormal speech discrimination | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:abnormality of the pinna ---
r_associated #0: 30 -->
en:everted ears
n1=en:abnormality of the pinna | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:abnormally folded ears ---
r_associated #0: 30 -->
en:everted ears
n1=en:abnormally folded ears | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:abnormally shaped ears (in one family) ---
r_associated #0: 30 -->
en:everted ears
n1=en:abnormally shaped ears (in one family) | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:absent auditory canals (wws) ---
r_associated #0: 30 -->
en:everted ears
n1=en:absent auditory canals (wws) | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:absent or decreased auditory brainstem responses ---
r_associated #0: 30 -->
en:everted ears
n1=en:absent or decreased auditory brainstem responses | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:acute otitis media/myringitis ---
r_associated #0: 30 -->
en:everted ears
n1=en:acute otitis media/myringitis | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:audiogram may be ascending ---
r_associated #0: 30 -->
en:everted ears
n1=en:audiogram may be ascending | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:chronic otitis ---
r_associated #0: 30 -->
en:everted ears
n1=en:chronic otitis | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:cochlear malformation ---
r_associated #0: 30 -->
en:everted ears
n1=en:cochlear malformation | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:conductive hearing loss (30% of patients) ---
r_associated #0: 30 -->
en:everted ears
n1=en:conductive hearing loss (30% of patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:cupped ears (finding) ---
r_associated #0: 30 -->
en:everted ears
n1=en:cupped ears (finding) | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:deafness (in 1 of 2 families) ---
r_associated #0: 30 -->
en:everted ears
n1=en:deafness (in 1 of 2 families) | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:deafness (sensorineural or mixed sensorineural and conductive) ---
r_associated #0: 30 -->
en:everted ears
n1=en:deafness (sensorineural or mixed sensorineural and conductive) | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:deafness, bilateral sensorineural, high frequency (100% of patients) ---
r_associated #0: 30 -->
en:everted ears
n1=en:deafness, bilateral sensorineural, high frequency (100% of patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years ---
r_associated #0: 30 -->
en:everted ears
n1=en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:deafness, profound, affects all frequencies ---
r_associated #0: 30 -->
en:everted ears
n1=en:deafness, profound, affects all frequencies | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:deafness, sensorineural (severe to profound) ---
r_associated #0: 30 -->
en:everted ears
n1=en:deafness, sensorineural (severe to profound) | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:deafness, sensorineural, severe to profound affecting all frequencies ---
r_associated #0: 30 -->
en:everted ears
n1=en:deafness, sensorineural, severe to profound affecting all frequencies | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:dilatated internal auditory canal ---
r_associated #0: 30 -->
en:everted ears
n1=en:dilatated internal auditory canal | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:dysplastic pinnae ---
r_associated #0: 30 -->
en:everted ears
n1=en:dysplastic pinnae | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:escalope ---
r_associated #0: 30 -->
en:everted ears
n1=en:escalope | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:glue ear ---
r_associated #0: 30 -->
en:everted ears
n1=en:glue ear | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:hearing disorder (1 patient) ---
r_associated #0: 30 -->
en:everted ears
n1=en:hearing disorder (1 patient) | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:hearing loss (95% of patients) ---
r_associated #0: 30 -->
en:everted ears
n1=en:hearing loss (95% of patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:hearing loss (rare) ---
r_associated #0: 30 -->
en:everted ears
n1=en:hearing loss (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:hearing loss has been reported in some adults with severe disease ---
r_associated #0: 30 -->
en:everted ears
n1=en:hearing loss has been reported in some adults with severe disease | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:hearing loss, conductive (in some patients) ---
r_associated #0: 30 -->
en:everted ears
n1=en:hearing loss, conductive (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:hearing loss, postlingual ---
r_associated #0: 30 -->
en:everted ears
n1=en:hearing loss, postlingual | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:hearing loss, postlingual progressive sensorineural ---
r_associated #0: 30 -->
en:everted ears
n1=en:hearing loss, postlingual progressive sensorineural | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:hearing loss, postlingual sensorineural ---
r_associated #0: 30 -->
en:everted ears
n1=en:hearing loss, postlingual sensorineural | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural (in patients with larger deletions) ---
r_associated #0: 30 -->
en:everted ears
n1=en:hearing loss, sensorineural (in patients with larger deletions) | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural and conductive, severe to profound ---
r_associated #0: 30 -->
en:everted ears
n1=en:hearing loss, sensorineural and conductive, severe to profound | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies ---
r_associated #0: 30 -->
en:everted ears
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:hearing loss, unilateral or bilateral, conductive, sensorineural, or mixed ---
r_associated #0: 30 -->
en:everted ears
n1=en:hearing loss, unilateral or bilateral, conductive, sensorineural, or mixed | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:hypoplastic ears fused to the scalp ---
r_associated #0: 30 -->
en:everted ears
n1=en:hypoplastic ears fused to the scalp | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:impaired tympanic membrane mobility ---
r_associated #0: 30 -->
en:everted ears
n1=en:impaired tympanic membrane mobility | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:inner ear ---
r_associated #0: 30 -->
en:everted ears
n1=en:inner ear | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:large auricle ---
r_associated #0: 30 -->
en:everted ears
n1=en:large auricle | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:lobule may be separately from the rest of the external ear ---
r_associated #0: 30 -->
en:everted ears
n1=en:lobule may be separately from the rest of the external ear | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:loss of vestibular caloric response ---
r_associated #0: 30 -->
en:everted ears
n1=en:loss of vestibular caloric response | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:microtia (30-60% of patients) ---
r_associated #0: 30 -->
en:everted ears
n1=en:microtia (30-60% of patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:microtia (in some patients) ---
r_associated #0: 30 -->
en:everted ears
n1=en:microtia (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:mild cochlear hearing loss (1 patient) ---
r_associated #0: 30 -->
en:everted ears
n1=en:mild cochlear hearing loss (1 patient) | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:narrow ear lobes ---
r_associated #0: 30 -->
en:everted ears
n1=en:narrow ear lobes | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:narrow ears ---
r_associated #0: 30 -->
en:everted ears
n1=en:narrow ears | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:no vestibular symptoms ---
r_associated #0: 30 -->
en:everted ears
n1=en:no vestibular symptoms | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:normal cochlear microphonics ---
r_associated #0: 30 -->
en:everted ears
n1=en:normal cochlear microphonics | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:otorhinolaryngologist ---
r_associated #0: 30 -->
en:everted ears
n1=en:otorhinolaryngologist | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:pigmentation of the ear cartilage ---
r_associated #0: 30 -->
en:everted ears
n1=en:pigmentation of the ear cartilage | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:prelingual onset ---
r_associated #0: 30 -->
en:everted ears
n1=en:prelingual onset | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:presbycusis ---
r_associated #0: 30 -->
en:everted ears
n1=en:presbycusis | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:progressive cartilaginous ossification of pinnae ---
r_associated #0: 30 -->
en:everted ears
n1=en:progressive cartilaginous ossification of pinnae | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:protruding, simple ears ---
r_associated #0: 30 -->
en:everted ears
n1=en:protruding, simple ears | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:retinitis (in some patients) ---
r_associated #0: 30 -->
en:everted ears
n1=en:retinitis (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:rudimentary ---
r_associated #0: 30 -->
en:everted ears
n1=en:rudimentary | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:sensorineural deafness, postlingual, progressive ---
r_associated #0: 30 -->
en:everted ears
n1=en:sensorineural deafness, postlingual, progressive | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:sensorineural hearing loss (1 family) ---
r_associated #0: 30 -->
en:everted ears
n1=en:sensorineural hearing loss (1 family) | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:sensorineural hearing loss (1 patient) ---
r_associated #0: 30 -->
en:everted ears
n1=en:sensorineural hearing loss (1 patient) | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:shallow skin dimple on posterior surface of ear ---
r_associated #0: 30 -->
en:everted ears
n1=en:shallow skin dimple on posterior surface of ear | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:stenotic ear canals (30%) ---
r_associated #0: 30 -->
en:everted ears
n1=en:stenotic ear canals (30%) | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:supraauricular pit ---
r_associated #0: 30 -->
en:everted ears
n1=en:supraauricular pit | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:tinnitus (rare) ---
r_associated #0: 30 -->
en:everted ears
n1=en:tinnitus (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:tympanic membrane perforation ---
r_associated #0: 30 -->
en:everted ears
n1=en:tympanic membrane perforation | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:underdeveloped nasal alae ---
r_associated #0: 30 -->
en:everted ears
n1=en:underdeveloped nasal alae | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:underdeveloped tragus ---
r_associated #0: 30 -->
en:everted ears
n1=en:underdeveloped tragus | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:uplift of earlobes (in some patients) ---
r_associated #0: 30 -->
en:everted ears
n1=en:uplift of earlobes (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:vestibular dysfunction ---
r_associated #0: 30 -->
en:everted ears
n1=en:vestibular dysfunction | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- hyperlaxe ---
r_associated #0: 30 -->
en:everted ears
n1=hyperlaxe | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- médecin ORL ---
r_associated #0: 30 -->
en:everted ears
n1=médecin ORL | n2=en:everted ears | rel=r_associated | relid=0 | w=30
- en:abnormal brainstem auditory evoked potentials (baep) ---
r_associated #0: 29 -->
en:everted ears
n1=en:abnormal brainstem auditory evoked potentials (baep) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:abnormal middle ear reflexes ---
r_associated #0: 29 -->
en:everted ears
n1=en:abnormal middle ear reflexes | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:absent distortion product otoacoustic emissions (oaes) ---
r_associated #0: 29 -->
en:everted ears
n1=en:absent distortion product otoacoustic emissions (oaes) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:absent stapedial reflexes or intraoperative stapes immobility ---
r_associated #0: 29 -->
en:everted ears
n1=en:absent stapedial reflexes or intraoperative stapes immobility | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:accessory tragus ---
r_associated #0: 29 -->
en:everted ears
n1=en:accessory tragus | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:asymmetry of the ears ---
r_associated #0: 29 -->
en:everted ears
n1=en:asymmetry of the ears | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:atretic ear canals ---
r_associated #0: 29 -->
en:everted ears
n1=en:atretic ear canals | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:bat ear ---
r_associated #0: 29 -->
en:everted ears
n1=en:bat ear | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:bilateral hypoplastic cochlea ---
r_associated #0: 29 -->
en:everted ears
n1=en:bilateral hypoplastic cochlea | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:cauliflower ear deformity (rare) ---
r_associated #0: 29 -->
en:everted ears
n1=en:cauliflower ear deformity (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:cochlear malformation defect (mondini dysplasia) (less common) ---
r_associated #0: 29 -->
en:everted ears
n1=en:cochlear malformation defect (mondini dysplasia) (less common) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:cochleosaccular dysplasia ---
r_associated #0: 29 -->
en:everted ears
n1=en:cochleosaccular dysplasia | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:complete bony atresia of medial portion of external auditory canal (in some patients) ---
r_associated #0: 29 -->
en:everted ears
n1=en:complete bony atresia of medial portion of external auditory canal (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:conductive and sensorineural hearing loss ---
r_associated #0: 29 -->
en:everted ears
n1=en:conductive and sensorineural hearing loss | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:congenital absence of external ear ---
r_associated #0: 29 -->
en:everted ears
n1=en:congenital absence of external ear | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:cystic dilatation of cochlea and vestibulum ---
r_associated #0: 29 -->
en:everted ears
n1=en:cystic dilatation of cochlea and vestibulum | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:deafness due to bilateral cochlear malformation (rare) ---
r_associated #0: 29 -->
en:everted ears
n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:deafness, nonprogressive, moderate ---
r_associated #0: 29 -->
en:everted ears
n1=en:deafness, nonprogressive, moderate | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:deafness, profound, by 6th decade ---
r_associated #0: 29 -->
en:everted ears
n1=en:deafness, profound, by 6th decade | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:deafness, sensorineural, mild (rare) ---
r_associated #0: 29 -->
en:everted ears
n1=en:deafness, sensorineural, mild (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:downsloping audiogram ---
r_associated #0: 29 -->
en:everted ears
n1=en:downsloping audiogram | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:earlobe pits ---
r_associated #0: 29 -->
en:everted ears
n1=en:earlobe pits | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:external ears rudimentary ---
r_associated #0: 29 -->
en:everted ears
n1=en:external ears rudimentary | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:foreign body in auditory canal ---
r_associated #0: 29 -->
en:everted ears
n1=en:foreign body in auditory canal | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:hearing complaints (excluding h84-86) ---
r_associated #0: 29 -->
en:everted ears
n1=en:hearing complaints (excluding h84-86) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:hearing impairment (1 patient) ---
r_associated #0: 29 -->
en:everted ears
n1=en:hearing impairment (1 patient) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:hearing loss (uncommon) ---
r_associated #0: 29 -->
en:everted ears
n1=en:hearing loss (uncommon) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:hearing loss, bilateral sensorineural (profound) ---
r_associated #0: 29 -->
en:everted ears
n1=en:hearing loss, bilateral sensorineural (profound) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:hearing loss, progressive sensorineural, affecting high frequencies ---
r_associated #0: 29 -->
en:everted ears
n1=en:hearing loss, progressive sensorineural, affecting high frequencies | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies) ---
r_associated #0: 29 -->
en:everted ears
n1=en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural (in 1 ashkenazi patient) ---
r_associated #0: 29 -->
en:everted ears
n1=en:hearing loss, sensorineural (in 1 ashkenazi patient) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural (variable) ---
r_associated #0: 29 -->
en:everted ears
n1=en:hearing loss, sensorineural (variable) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, associated with elsts ---
r_associated #0: 29 -->
en:everted ears
n1=en:hearing loss, sensorineural, associated with elsts | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected) ---
r_associated #0: 29 -->
en:everted ears
n1=en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:high-tone sensorineural deafness (67% of patients) ---
r_associated #0: 29 -->
en:everted ears
n1=en:high-tone sensorineural deafness (67% of patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:hypertrophic auricular cartilage ---
r_associated #0: 29 -->
en:everted ears
n1=en:hypertrophic auricular cartilage | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:increased posterior angulation ---
r_associated #0: 29 -->
en:everted ears
n1=en:increased posterior angulation | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:low-frequency sensorineural hearing impairment ---
r_associated #0: 29 -->
en:everted ears
n1=en:low-frequency sensorineural hearing impairment | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:low-set ears (3 patients) ---
r_associated #0: 29 -->
en:everted ears
n1=en:low-set ears (3 patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:low-set ears (in one family) ---
r_associated #0: 29 -->
en:everted ears
n1=en:low-set ears (in one family) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:middle ear ---
r_associated #0: 29 -->
en:everted ears
n1=en:middle ear | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:minor ear anomalies (in some patients) ---
r_associated #0: 29 -->
en:everted ears
n1=en:minor ear anomalies (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:misshapen ear ---
r_associated #0: 29 -->
en:everted ears
n1=en:misshapen ear | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:mixed hearing loss (50% of patients) ---
r_associated #0: 29 -->
en:everted ears
n1=en:mixed hearing loss (50% of patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:no reproducible waves i, iii, or v at high intensities ---
r_associated #0: 29 -->
en:everted ears
n1=en:no reproducible waves i, iii, or v at high intensities | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:normal middle ear pressures on tympanometry ---
r_associated #0: 29 -->
en:everted ears
n1=en:normal middle ear pressures on tympanometry | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:normal static compliance on tympanometry ---
r_associated #0: 29 -->
en:everted ears
n1=en:normal static compliance on tympanometry | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:normal vestibular response ---
r_associated #0: 29 -->
en:everted ears
n1=en:normal vestibular response | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:other symptom/complaint of ear ---
r_associated #0: 29 -->
en:everted ears
n1=en:other symptom/complaint of ear | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:pale, stiff pinnae ---
r_associated #0: 29 -->
en:everted ears
n1=en:pale, stiff pinnae | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:pinna modeling anomalies ---
r_associated #0: 29 -->
en:everted ears
n1=en:pinna modeling anomalies | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:progressive, low frequency sensorineural hearing loss ---
r_associated #0: 29 -->
en:everted ears
n1=en:progressive, low frequency sensorineural hearing loss | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:prominent antitragus ---
r_associated #0: 29 -->
en:everted ears
n1=en:prominent antitragus | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:prominent antitragus (in some patients) ---
r_associated #0: 29 -->
en:everted ears
n1=en:prominent antitragus (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:protruding lobules ---
r_associated #0: 29 -->
en:everted ears
n1=en:protruding lobules | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:sensation of blocked ears ---
r_associated #0: 29 -->
en:everted ears
n1=en:sensation of blocked ears | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:sensorineural hearing loss ---
r_associated #0: 29 -->
en:everted ears
n1=en:sensorineural hearing loss | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:sensorineural hearing loss (3 patients) ---
r_associated #0: 29 -->
en:everted ears
n1=en:sensorineural hearing loss (3 patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:sensorineural hearing loss, mild to moderate ---
r_associated #0: 29 -->
en:everted ears
n1=en:sensorineural hearing loss, mild to moderate | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:simple ear structure ---
r_associated #0: 29 -->
en:everted ears
n1=en:simple ear structure | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:small earlobe ---
r_associated #0: 29 -->
en:everted ears
n1=en:small earlobe | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:small ears (female) ---
r_associated #0: 29 -->
en:everted ears
n1=en:small ears (female) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:small lobes ---
r_associated #0: 29 -->
en:everted ears
n1=en:small lobes | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:small, malformed ears ---
r_associated #0: 29 -->
en:everted ears
n1=en:small, malformed ears | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:squared-off ears ---
r_associated #0: 29 -->
en:everted ears
n1=en:squared-off ears | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:stapes ankylosis ---
r_associated #0: 29 -->
en:everted ears
n1=en:stapes ankylosis | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:structural inner ear abnormalities (in patients with larger deletions) ---
r_associated #0: 29 -->
en:everted ears
n1=en:structural inner ear abnormalities (in patients with larger deletions) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:thick earlobes ---
r_associated #0: 29 -->
en:everted ears
n1=en:thick earlobes | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:tinnitus ---
r_associated #0: 29 -->
en:everted ears
n1=en:tinnitus | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:tinnitus (in some patients) ---
r_associated #0: 29 -->
en:everted ears
n1=en:tinnitus (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:unconnected or fused stapes and incus ---
r_associated #0: 29 -->
en:everted ears
n1=en:unconnected or fused stapes and incus | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:uplifted earlobes ---
r_associated #0: 29 -->
en:everted ears
n1=en:uplifted earlobes | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- perte d'audition sensorineurale ---
r_associated #0: 29 -->
en:everted ears
n1=perte d'audition sensorineurale | n2=en:everted ears | rel=r_associated | relid=0 | w=29
- en:abnormal auricles ---
r_associated #0: 28 -->
en:everted ears
n1=en:abnormal auricles | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:abnormal ears ---
r_associated #0: 28 -->
en:everted ears
n1=en:abnormal ears | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:abnormal folded pinna ---
r_associated #0: 28 -->
en:everted ears
n1=en:abnormal folded pinna | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:absent brainstem auditory responses ---
r_associated #0: 28 -->
en:everted ears
n1=en:absent brainstem auditory responses | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:anteriorly displaced ears ---
r_associated #0: 28 -->
en:everted ears
n1=en:anteriorly displaced ears | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:anteriorly rotated ears ---
r_associated #0: 28 -->
en:everted ears
n1=en:anteriorly rotated ears | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:anteverted pinnae ---
r_associated #0: 28 -->
en:everted ears
n1=en:anteverted pinnae | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:aplasia of the inner ear ---
r_associated #0: 28 -->
en:everted ears
n1=en:aplasia of the inner ear | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:auditory impairment ---
r_associated #0: 28 -->
en:everted ears
n1=en:auditory impairment | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:auditory neuropathy spectrum disorder ---
r_associated #0: 28 -->
en:everted ears
n1=en:auditory neuropathy spectrum disorder | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:bilateral conductive hearing loss (rare) ---
r_associated #0: 28 -->
en:everted ears
n1=en:bilateral conductive hearing loss (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:blind fistula ---
r_associated #0: 28 -->
en:everted ears
n1=en:blind fistula | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:cleft at the superior portion of the pinna ---
r_associated #0: 28 -->
en:everted ears
n1=en:cleft at the superior portion of the pinna | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:cleft lobules ---
r_associated #0: 28 -->
en:everted ears
n1=en:cleft lobules | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:congenital ear anomaly nos (disorder) ---
r_associated #0: 28 -->
en:everted ears
n1=en:congenital ear anomaly nos (disorder) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:crumpled ear (76%) ---
r_associated #0: 28 -->
en:everted ears
n1=en:crumpled ear (76%) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:deafness in 30-50% of patients with skull involvement ---
r_associated #0: 28 -->
en:everted ears
n1=en:deafness in 30-50% of patients with skull involvement | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:deafness, congenital nonprogressive sensorineural symmetric, moderate ---
r_associated #0: 28 -->
en:everted ears
n1=en:deafness, congenital nonprogressive sensorineural symmetric, moderate | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:deafness, sensorineural (45%) ---
r_associated #0: 28 -->
en:everted ears
n1=en:deafness, sensorineural (45%) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:deafness, stable bilateral symmetric prelingual ---
r_associated #0: 28 -->
en:everted ears
n1=en:deafness, stable bilateral symmetric prelingual | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation ---
r_associated #0: 28 -->
en:everted ears
n1=en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:ear part ---
r_associated #0: 28 -->
en:everted ears
n1=en:ear part | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:external ear defects (47%) ---
r_associated #0: 28 -->
en:everted ears
n1=en:external ear defects (47%) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:fear of ear disease ---
r_associated #0: 28 -->
en:everted ears
n1=en:fear of ear disease | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:hearing impairment may occur ---
r_associated #0: 28 -->
en:everted ears
n1=en:hearing impairment may occur | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:hearing loss, conductive (in one family) ---
r_associated #0: 28 -->
en:everted ears
n1=en:hearing loss, conductive (in one family) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:hearing loss, congenital, profound (250-8,000 hz) ---
r_associated #0: 28 -->
en:everted ears
n1=en:hearing loss, congenital, profound (250-8,000 hz) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:hearing loss, initially conductive, later mixed conductive-sensorineural ---
r_associated #0: 28 -->
en:everted ears
n1=en:hearing loss, initially conductive, later mixed conductive-sensorineural | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:hearing loss, more severe at lower frequencies ---
r_associated #0: 28 -->
en:everted ears
n1=en:hearing loss, more severe at lower frequencies | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:hearing loss, profound congenital sensorineural ---
r_associated #0: 28 -->
en:everted ears
n1=en:hearing loss, profound congenital sensorineural | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:hearing loss, progressive conductive and/or sensorineural, during adulthood ---
r_associated #0: 28 -->
en:everted ears
n1=en:hearing loss, progressive conductive and/or sensorineural, during adulthood | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural (in one family) ---
r_associated #0: 28 -->
en:everted ears
n1=en:hearing loss, sensorineural (in one family) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, prelingual ---
r_associated #0: 28 -->
en:everted ears
n1=en:hearing loss, sensorineural, prelingual | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, severe to profound ---
r_associated #0: 28 -->
en:everted ears
n1=en:hearing loss, sensorineural, severe to profound | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:hearing normal ---
r_associated #0: 28 -->
en:everted ears
n1=en:hearing normal | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:hypoplasia of the cochlea ---
r_associated #0: 28 -->
en:everted ears
n1=en:hypoplasia of the cochlea | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:hypoplastic malleus (1 patient) ---
r_associated #0: 28 -->
en:everted ears
n1=en:hypoplastic malleus (1 patient) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies ---
r_associated #0: 28 -->
en:everted ears
n1=en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:large anteverted ears (rare) ---
r_associated #0: 28 -->
en:everted ears
n1=en:large anteverted ears (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:large anteverted pinnae (90% males, 40% females) ---
r_associated #0: 28 -->
en:everted ears
n1=en:large anteverted pinnae (90% males, 40% females) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:left ear ---
r_associated #0: 28 -->
en:everted ears
n1=en:left ear | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:lobular aplasia ---
r_associated #0: 28 -->
en:everted ears
n1=en:lobular aplasia | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:loss of outer hair cell function ---
r_associated #0: 28 -->
en:everted ears
n1=en:loss of outer hair cell function | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:malformations of the auditory ossicles ---
r_associated #0: 28 -->
en:everted ears
n1=en:malformations of the auditory ossicles | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:malformed auricle (1 patient) ---
r_associated #0: 28 -->
en:everted ears
n1=en:malformed auricle (1 patient) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:microtia hearing loss, conductive ---
r_associated #0: 28 -->
en:everted ears
n1=en:microtia hearing loss, conductive | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:misshapen, small ear ---
r_associated #0: 28 -->
en:everted ears
n1=en:misshapen, small ear | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:narrow auditory canals (rare) ---
r_associated #0: 28 -->
en:everted ears
n1=en:narrow auditory canals (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:narrowed external ear canal (30% of patients) ---
r_associated #0: 28 -->
en:everted ears
n1=en:narrowed external ear canal (30% of patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:near-stenosis of bony portion of auditory canal (in homozygotes) ---
r_associated #0: 28 -->
en:everted ears
n1=en:near-stenosis of bony portion of auditory canal (in homozygotes) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:no hearing impairment ---
r_associated #0: 28 -->
en:everted ears
n1=en:no hearing impairment | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:nonprogressive ---
r_associated #0: 28 -->
en:everted ears
n1=en:nonprogressive | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:normal otoacoustic emissions (oae), indicating intact outer ear hair cell function ---
r_associated #0: 28 -->
en:everted ears
n1=en:normal otoacoustic emissions (oae), indicating intact outer ear hair cell function | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:organ of corti degeneration ---
r_associated #0: 28 -->
en:everted ears
n1=en:organ of corti degeneration | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:otitis media, recurrent (rare) ---
r_associated #0: 28 -->
en:everted ears
n1=en:otitis media, recurrent (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:otolaryngologist ---
r_associated #0: 28 -->
en:everted ears
n1=en:otolaryngologist | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:partial aplasia of external auditory canal ending in blind fistula (in some patients) ---
r_associated #0: 28 -->
en:everted ears
n1=en:partial aplasia of external auditory canal ending in blind fistula (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:poorly formed pinnae ---
r_associated #0: 28 -->
en:everted ears
n1=en:poorly formed pinnae | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:posteriorly rotated ears (1/4 patients) ---
r_associated #0: 28 -->
en:everted ears
n1=en:posteriorly rotated ears (1/4 patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:preauricular sinus ---
r_associated #0: 28 -->
en:everted ears
n1=en:preauricular sinus | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:preauricular skin tags (in some patients) ---
r_associated #0: 28 -->
en:everted ears
n1=en:preauricular skin tags (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face) ---
r_associated #0: 28 -->
en:everted ears
n1=en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:progressive sensorineural hearing impairment ---
r_associated #0: 28 -->
en:everted ears
n1=en:progressive sensorineural hearing impairment | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:protruding ears (in some patients) ---
r_associated #0: 28 -->
en:everted ears
n1=en:protruding ears (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:sensorineural deafness (onset in the second decade in 25 to 30% of patients) ---
r_associated #0: 28 -->
en:everted ears
n1=en:sensorineural deafness (onset in the second decade in 25 to 30% of patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:sensorineural hearing loss (described in 1 family) ---
r_associated #0: 28 -->
en:everted ears
n1=en:sensorineural hearing loss (described in 1 family) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:sensorineural hearing loss (males only) ---
r_associated #0: 28 -->
en:everted ears
n1=en:sensorineural hearing loss (males only) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:sensorineural hearing loss (rare) ---
r_associated #0: 28 -->
en:everted ears
n1=en:sensorineural hearing loss (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:sensorineural hearing loss has been reported ---
r_associated #0: 28 -->
en:everted ears
n1=en:sensorineural hearing loss has been reported | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:simple auricles ---
r_associated #0: 28 -->
en:everted ears
n1=en:simple auricles | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:u- or bowl-shaped audiogram ---
r_associated #0: 28 -->
en:everted ears
n1=en:u- or bowl-shaped audiogram | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:unfolded superior helices ---
r_associated #0: 28 -->
en:everted ears
n1=en:unfolded superior helices | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:vertigo, single occurrence (in 2 patients) ---
r_associated #0: 28 -->
en:everted ears
n1=en:vertigo, single occurrence (in 2 patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:vestibular areflexia ---
r_associated #0: 28 -->
en:everted ears
n1=en:vestibular areflexia | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:vestibular hyporeflexia ---
r_associated #0: 28 -->
en:everted ears
n1=en:vestibular hyporeflexia | n2=en:everted ears | rel=r_associated | relid=0 | w=28
- en:abnormal auditory temporal processes ---
r_associated #0: 27 -->
en:everted ears
n1=en:abnormal auditory temporal processes | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:abnormal gap detection ---
r_associated #0: 27 -->
en:everted ears
n1=en:abnormal gap detection | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:abnormal middle ear ossicles ---
r_associated #0: 27 -->
en:everted ears
n1=en:abnormal middle ear ossicles | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:abnormal or absent auditory nerve and brainstem responses ---
r_associated #0: 27 -->
en:everted ears
n1=en:abnormal or absent auditory nerve and brainstem responses | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:abnormal semicircular canals ---
r_associated #0: 27 -->
en:everted ears
n1=en:abnormal semicircular canals | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:abnormality of the helix ---
r_associated #0: 27 -->
en:everted ears
n1=en:abnormality of the helix | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:absence of the cochlear nerves (reported in 1 patient) ---
r_associated #0: 27 -->
en:everted ears
n1=en:absence of the cochlear nerves (reported in 1 patient) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:absence of vestibular evoked myogenic potentials (rare) ---
r_associated #0: 27 -->
en:everted ears
n1=en:absence of vestibular evoked myogenic potentials (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:affects mid- to high-frequencies ---
r_associated #0: 27 -->
en:everted ears
n1=en:affects mid- to high-frequencies | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:anomalous middle ear bones ---
r_associated #0: 27 -->
en:everted ears
n1=en:anomalous middle ear bones | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:anteverted ears ---
r_associated #0: 27 -->
en:everted ears
n1=en:anteverted ears | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion ---
r_associated #0: 27 -->
en:everted ears
n1=en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:chronic otitis media (25%) ---
r_associated #0: 27 -->
en:everted ears
n1=en:chronic otitis media (25%) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:cochlear degeneration ---
r_associated #0: 27 -->
en:everted ears
n1=en:cochlear degeneration | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:cutlet ---
r_associated #0: 27 -->
en:everted ears
n1=en:cutlet | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:deafness ---
r_associated #0: 27 -->
en:everted ears
n1=en:deafness | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:deafness, prelingual, profound (affects all frequencies) ---
r_associated #0: 27 -->
en:everted ears
n1=en:deafness, prelingual, profound (affects all frequencies) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:deafness, unilateral, childhood onset ---
r_associated #0: 27 -->
en:everted ears
n1=en:deafness, unilateral, childhood onset | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:ear dimple ---
r_associated #0: 27 -->
en:everted ears
n1=en:ear dimple | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:external ear defects ---
r_associated #0: 27 -->
en:everted ears
n1=en:external ear defects | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:flat or shallow u-shaped audiogram ---
r_associated #0: 27 -->
en:everted ears
n1=en:flat or shallow u-shaped audiogram | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hearing impairment (rare) ---
r_associated #0: 27 -->
en:everted ears
n1=en:hearing impairment (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hearing loss (2 patients) ---
r_associated #0: 27 -->
en:everted ears
n1=en:hearing loss (2 patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hearing loss (in some patients) ---
r_associated #0: 27 -->
en:everted ears
n1=en:hearing loss (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, bilateral ---
r_associated #0: 27 -->
en:everted ears
n1=en:hearing loss, bilateral | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, conductive (rare) ---
r_associated #0: 27 -->
en:everted ears
n1=en:hearing loss, conductive (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, conductive or mixed ---
r_associated #0: 27 -->
en:everted ears
n1=en:hearing loss, conductive or mixed | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, congenital sensorineural, severe to profound ---
r_associated #0: 27 -->
en:everted ears
n1=en:hearing loss, congenital sensorineural, severe to profound | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, moderate to severe, bilateral, nonprogressive ---
r_associated #0: 27 -->
en:everted ears
n1=en:hearing loss, moderate to severe, bilateral, nonprogressive | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, neural type ---
r_associated #0: 27 -->
en:everted ears
n1=en:hearing loss, neural type | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, profound prelingual sensorineural ---
r_associated #0: 27 -->
en:everted ears
n1=en:hearing loss, profound prelingual sensorineural | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies) ---
r_associated #0: 27 -->
en:everted ears
n1=en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural (bilateral, prelingual) ---
r_associated #0: 27 -->
en:everted ears
n1=en:hearing loss, sensorineural (bilateral, prelingual) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural (in some cases) ---
r_associated #0: 27 -->
en:everted ears
n1=en:hearing loss, sensorineural (in some cases) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural (in some patients) ---
r_associated #0: 27 -->
en:everted ears
n1=en:hearing loss, sensorineural (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural (in some) ---
r_associated #0: 27 -->
en:everted ears
n1=en:hearing loss, sensorineural (in some) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural (type ii) ---
r_associated #0: 27 -->
en:everted ears
n1=en:hearing loss, sensorineural (type ii) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, due to auditory neuropathy ---
r_associated #0: 27 -->
en:everted ears
n1=en:hearing loss, sensorineural, due to auditory neuropathy | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, unilateral (rare) ---
r_associated #0: 27 -->
en:everted ears
n1=en:hearing loss, unilateral (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural ---
r_associated #0: 27 -->
en:everted ears
n1=en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hearing threshold at or above 90 db at all frequencies tested (0.25-8.0 khz) ---
r_associated #0: 27 -->
en:everted ears
n1=en:hearing threshold at or above 90 db at all frequencies tested (0.25-8.0 khz) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hypoacusia (1 patient) ---
r_associated #0: 27 -->
en:everted ears
n1=en:hypoacusia (1 patient) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hypoplastic semicircular canals ---
r_associated #0: 27 -->
en:everted ears
n1=en:hypoplastic semicircular canals | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:hypoplastic, overfolded helices ---
r_associated #0: 27 -->
en:everted ears
n1=en:hypoplastic, overfolded helices | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:internal auditory canal hypoplasia ---
r_associated #0: 27 -->
en:everted ears
n1=en:internal auditory canal hypoplasia | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:keratotic plaque around ear meatus ---
r_associated #0: 27 -->
en:everted ears
n1=en:keratotic plaque around ear meatus | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:large ears (2p21del) ---
r_associated #0: 27 -->
en:everted ears
n1=en:large ears (2p21del) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:large protruding ears ---
r_associated #0: 27 -->
en:everted ears
n1=en:large protruding ears | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:low-set ears (in some patients) ---
r_associated #0: 27 -->
en:everted ears
n1=en:low-set ears (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:low-set ears (rare) ---
r_associated #0: 27 -->
en:everted ears
n1=en:low-set ears (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:low-set, posteriorly rotated ears ---
r_associated #0: 27 -->
en:everted ears
n1=en:low-set, posteriorly rotated ears | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:malformed pinnae (30-60% of patients) ---
r_associated #0: 27 -->
en:everted ears
n1=en:malformed pinnae (30-60% of patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:meniere disease ---
r_associated #0: 27 -->
en:everted ears
n1=en:meniere disease | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:mondini malformation ---
r_associated #0: 27 -->
en:everted ears
n1=en:mondini malformation | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:no vestibular dysfunction ---
r_associated #0: 27 -->
en:everted ears
n1=en:no vestibular dysfunction | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:otitis media, chronic (rare) ---
r_associated #0: 27 -->
en:everted ears
n1=en:otitis media, chronic (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:pointed upper helix ---
r_associated #0: 27 -->
en:everted ears
n1=en:pointed upper helix | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:posteriorly rotated ears (in some patients) ---
r_associated #0: 27 -->
en:everted ears
n1=en:posteriorly rotated ears (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:preauricular dimple ---
r_associated #0: 27 -->
en:everted ears
n1=en:preauricular dimple | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:prominent ears (in some patients) ---
r_associated #0: 27 -->
en:everted ears
n1=en:prominent ears (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:prominent ears (rare) ---
r_associated #0: 27 -->
en:everted ears
n1=en:prominent ears (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:prominent helices ---
r_associated #0: 27 -->
en:everted ears
n1=en:prominent helices | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:prominent lobules ---
r_associated #0: 27 -->
en:everted ears
n1=en:prominent lobules | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:protruding ears (rare) ---
r_associated #0: 27 -->
en:everted ears
n1=en:protruding ears (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:protuberant ear ---
r_associated #0: 27 -->
en:everted ears
n1=en:protuberant ear | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:recurrent otitis media (18%) ---
r_associated #0: 27 -->
en:everted ears
n1=en:recurrent otitis media (18%) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:sensorineural hearing loss (in 1 of 3 patients) ---
r_associated #0: 27 -->
en:everted ears
n1=en:sensorineural hearing loss (in 1 of 3 patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:sensorineural hearing loss, progressive bilateral postlingual ---
r_associated #0: 27 -->
en:everted ears
n1=en:sensorineural hearing loss, progressive bilateral postlingual | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:serous otitis ---
r_associated #0: 27 -->
en:everted ears
n1=en:serous otitis | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:simple ear ---
r_associated #0: 27 -->
en:everted ears
n1=en:simple ear | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:stiff, prominent pinnae ---
r_associated #0: 27 -->
en:everted ears
n1=en:stiff, prominent pinnae | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:thickened lobes ---
r_associated #0: 27 -->
en:everted ears
n1=en:thickened lobes | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:transient evoked otoacoustic emissions cannot be detected ---
r_associated #0: 27 -->
en:everted ears
n1=en:transient evoked otoacoustic emissions cannot be detected | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:vestibular abnormalities (variable) ---
r_associated #0: 27 -->
en:everted ears
n1=en:vestibular abnormalities (variable) | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:vestibular hypofunction ---
r_associated #0: 27 -->
en:everted ears
n1=en:vestibular hypofunction | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- esgourde ---
r_associated #0: 27 -->
en:everted ears
n1=esgourde | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- pavillon de l'oreille de morphologie rudimentaire ---
r_associated #0: 27 -->
en:everted ears
n1=pavillon de l'oreille de morphologie rudimentaire | n2=en:everted ears | rel=r_associated | relid=0 | w=27
- en:abnormality of the middle ear ossicles ---
r_associated #0: 26 -->
en:everted ears
n1=en:abnormality of the middle ear ossicles | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:abnormality of the outer ear ---
r_associated #0: 26 -->
en:everted ears
n1=en:abnormality of the outer ear | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:apical cartilage deformity ---
r_associated #0: 26 -->
en:everted ears
n1=en:apical cartilage deformity | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:asymmetric dysplastic ears ---
r_associated #0: 26 -->
en:everted ears
n1=en:asymmetric dysplastic ears | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:atresia of the external auditory canal ---
r_associated #0: 26 -->
en:everted ears
n1=en:atresia of the external auditory canal | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:auditory canal stenosis ---
r_associated #0: 26 -->
en:everted ears
n1=en:auditory canal stenosis | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:bleeding from ear ---
r_associated #0: 26 -->
en:everted ears
n1=en:bleeding from ear | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:chronic otitis media ---
r_associated #0: 26 -->
en:everted ears
n1=en:chronic otitis media | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:congenital atresia of external auditory canal ---
r_associated #0: 26 -->
en:everted ears
n1=en:congenital atresia of external auditory canal | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:deafness, moderate-severe (onset in third decade) ---
r_associated #0: 26 -->
en:everted ears
n1=en:deafness, moderate-severe (onset in third decade) | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:deafness, profound congenital sensorineural ---
r_associated #0: 26 -->
en:everted ears
n1=en:deafness, profound congenital sensorineural | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:deafness, sensorineural, especially affecting high frequencies ---
r_associated #0: 26 -->
en:everted ears
n1=en:deafness, sensorineural, especially affecting high frequencies | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:disjunction of otherwise normal lobule from remainder of ear ---
r_associated #0: 26 -->
en:everted ears
n1=en:disjunction of otherwise normal lobule from remainder of ear | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:disproportionately large ears ---
r_associated #0: 26 -->
en:everted ears
n1=en:disproportionately large ears | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:dorsally rotated ears ---
r_associated #0: 26 -->
en:everted ears
n1=en:dorsally rotated ears | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:downward sloping or flat audiogram ---
r_associated #0: 26 -->
en:everted ears
n1=en:downward sloping or flat audiogram | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:dysplastic ears (in some patients) ---
r_associated #0: 26 -->
en:everted ears
n1=en:dysplastic ears (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:ear constriction (97%) ---
r_associated #0: 26 -->
en:everted ears
n1=en:ear constriction (97%) | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:entire ear ---
r_associated #0: 26 -->
en:everted ears
n1=en:entire ear | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:excessive cerumen ---
r_associated #0: 26 -->
en:everted ears
n1=en:excessive cerumen | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:first branchial arch anomalies ---
r_associated #0: 26 -->
en:everted ears
n1=en:first branchial arch anomalies | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:floppy ears ---
r_associated #0: 26 -->
en:everted ears
n1=en:floppy ears | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:hearing loss affects all frequencies ---
r_associated #0: 26 -->
en:everted ears
n1=en:hearing loss affects all frequencies | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:hearing loss, prelingual sensorineural, moderate to severe ---
r_associated #0: 26 -->
en:everted ears
n1=en:hearing loss, prelingual sensorineural, moderate to severe | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies) ---
r_associated #0: 26 -->
en:everted ears
n1=en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies) | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:hearing loss, progressive, starting in infancy ---
r_associated #0: 26 -->
en:everted ears
n1=en:hearing loss, progressive, starting in infancy | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:incomplete atretic plate ---
r_associated #0: 26 -->
en:everted ears
n1=en:incomplete atretic plate | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:large, low-set ears (uncommon) ---
r_associated #0: 26 -->
en:everted ears
n1=en:large, low-set ears (uncommon) | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:linear ear lobe creases ---
r_associated #0: 26 -->
en:everted ears
n1=en:linear ear lobe creases | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:long ear ---
r_associated #0: 26 -->
en:everted ears
n1=en:long ear | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:loss of high frequencies at onset ---
r_associated #0: 26 -->
en:everted ears
n1=en:loss of high frequencies at onset | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:low set ears ---
r_associated #0: 26 -->
en:everted ears
n1=en:low set ears | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:low-set and rotated ears ---
r_associated #0: 26 -->
en:everted ears
n1=en:low-set and rotated ears | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:minor auricular anomalies ---
r_associated #0: 26 -->
en:everted ears
n1=en:minor auricular anomalies | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:morphological abnormality of the middle ear ---
r_associated #0: 26 -->
en:everted ears
n1=en:morphological abnormality of the middle ear | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:normal otoacoustic emissions ---
r_associated #0: 26 -->
en:everted ears
n1=en:normal otoacoustic emissions | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:otitis media ---
r_associated #0: 26 -->
en:everted ears
n1=en:otitis media | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:otosclerosis ---
r_associated #0: 26 -->
en:everted ears
n1=en:otosclerosis | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:postauricular pit ---
r_associated #0: 26 -->
en:everted ears
n1=en:postauricular pit | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:preauricular skin furrow ---
r_associated #0: 26 -->
en:everted ears
n1=en:preauricular skin furrow | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:prominent antihelix ---
r_associated #0: 26 -->
en:everted ears
n1=en:prominent antihelix | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:prominent crura ---
r_associated #0: 26 -->
en:everted ears
n1=en:prominent crura | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:recurrent otitis ---
r_associated #0: 26 -->
en:everted ears
n1=en:recurrent otitis | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:recurrent otitis media in infancy ---
r_associated #0: 26 -->
en:everted ears
n1=en:recurrent otitis media in infancy | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:rotated ears ---
r_associated #0: 26 -->
en:everted ears
n1=en:rotated ears | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:sensorineural deafness (rare) ---
r_associated #0: 26 -->
en:everted ears
n1=en:sensorineural deafness (rare) | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:sensorineural deafness, progressive, late-onset ---
r_associated #0: 26 -->
en:everted ears
n1=en:sensorineural deafness, progressive, late-onset | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:sensorineural hearing loss (less common) ---
r_associated #0: 26 -->
en:everted ears
n1=en:sensorineural hearing loss (less common) | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:sensorineural, conductive, or mixed hearing loss ---
r_associated #0: 26 -->
en:everted ears
n1=en:sensorineural, conductive, or mixed hearing loss | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:sensory hearing loss ---
r_associated #0: 26 -->
en:everted ears
n1=en:sensory hearing loss | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:severe narrowing of cartilagenous auditory canal (in homozygotes) ---
r_associated #0: 26 -->
en:everted ears
n1=en:severe narrowing of cartilagenous auditory canal (in homozygotes) | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:stapes fixation ---
r_associated #0: 26 -->
en:everted ears
n1=en:stapes fixation | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:structure of lymphatic vessel of ear ---
r_associated #0: 26 -->
en:everted ears
n1=en:structure of lymphatic vessel of ear | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:vestibular involvement (variable) ---
r_associated #0: 26 -->
en:everted ears
n1=en:vestibular involvement (variable) | n2=en:everted ears | rel=r_associated | relid=0 | w=26
- en:abnormal amplitude modulation detection ---
r_associated #0: 25 -->
en:everted ears
n1=en:abnormal amplitude modulation detection | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:abnormal helices, antihelices and lobules ---
r_associated #0: 25 -->
en:everted ears
n1=en:abnormal helices, antihelices and lobules | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:abnormality of the middle ear ---
r_associated #0: 25 -->
en:everted ears
n1=en:abnormality of the middle ear | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:absent cochlear microphonic (in older patients) ---
r_associated #0: 25 -->
en:everted ears
n1=en:absent cochlear microphonic (in older patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:deafness, sensorineural (in some patients) ---
r_associated #0: 25 -->
en:everted ears
n1=en:deafness, sensorineural (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:deafness, sensorineural, especially affecting high frequencies (in about 55% of males and 45% of females) ---
r_associated #0: 25 -->
en:everted ears
n1=en:deafness, sensorineural, especially affecting high frequencies (in about 55% of males and 45% of females) | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:deep-set ears ---
r_associated #0: 25 -->
en:everted ears
n1=en:deep-set ears | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:flattened ---
r_associated #0: 25 -->
en:everted ears
n1=en:flattened | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:folded helix ---
r_associated #0: 25 -->
en:everted ears
n1=en:folded helix | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:hearing deficits (28% of adults) ---
r_associated #0: 25 -->
en:everted ears
n1=en:hearing deficits (28% of adults) | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:hearing loss (reported in 2 patients) ---
r_associated #0: 25 -->
en:everted ears
n1=en:hearing loss (reported in 2 patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:hearing loss, high-frequency (onset in childhood-adolescence) ---
r_associated #0: 25 -->
en:everted ears
n1=en:hearing loss, high-frequency (onset in childhood-adolescence) | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:hypoplastic pinnae (30-60% of patients) ---
r_associated #0: 25 -->
en:everted ears
n1=en:hypoplastic pinnae (30-60% of patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:hypoplastic superior helix ---
r_associated #0: 25 -->
en:everted ears
n1=en:hypoplastic superior helix | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:inferior displacement of the ears ---
r_associated #0: 25 -->
en:everted ears
n1=en:inferior displacement of the ears | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:large fleshy earlobes ---
r_associated #0: 25 -->
en:everted ears
n1=en:large fleshy earlobes | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:large pinnae ---
r_associated #0: 25 -->
en:everted ears
n1=en:large pinnae | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:long, lobulated ears ---
r_associated #0: 25 -->
en:everted ears
n1=en:long, lobulated ears | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:low-set ears (1 patient) ---
r_associated #0: 25 -->
en:everted ears
n1=en:low-set ears (1 patient) | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:near-stenosis of bony portion of auditory canal ---
r_associated #0: 25 -->
en:everted ears
n1=en:near-stenosis of bony portion of auditory canal | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:preauricular skin tag ---
r_associated #0: 25 -->
en:everted ears
n1=en:preauricular skin tag | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:progressive high-frequency hearing loss (onset 20-30 years) ---
r_associated #0: 25 -->
en:everted ears
n1=en:progressive high-frequency hearing loss (onset 20-30 years) | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:protruding ears ---
r_associated #0: 25 -->
en:everted ears
n1=en:protruding ears | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:protruding right ear ---
r_associated #0: 25 -->
en:everted ears
n1=en:protruding right ear | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:roll-head ---
r_associated #0: 25 -->
en:everted ears
n1=en:roll-head | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:simple helix ---
r_associated #0: 25 -->
en:everted ears
n1=en:simple helix | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:small, posteriorly rotated ears ---
r_associated #0: 25 -->
en:everted ears
n1=en:small, posteriorly rotated ears | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:vertiginous syndrome ---
r_associated #0: 25 -->
en:everted ears
n1=en:vertiginous syndrome | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:vestibular anomalies (less common) ---
r_associated #0: 25 -->
en:everted ears
n1=en:vestibular anomalies (less common) | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:vestibular areflexia, complete ---
r_associated #0: 25 -->
en:everted ears
n1=en:vestibular areflexia, complete | n2=en:everted ears | rel=r_associated | relid=0 | w=25
- en:absence of acoustic reflex ---
r_associated #0: 24 -->
en:everted ears
n1=en:absence of acoustic reflex | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:attached ear lobes ---
r_associated #0: 24 -->
en:everted ears
n1=en:attached ear lobes | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:auriculo-condylar syndrome ---
r_associated #0: 24 -->
en:everted ears
n1=en:auriculo-condylar syndrome | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:bilateral congenital profound sensorineural hearing loss ---
r_associated #0: 24 -->
en:everted ears
n1=en:bilateral congenital profound sensorineural hearing loss | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:chronic otitis other infection ear ---
r_associated #0: 24 -->
en:everted ears
n1=en:chronic otitis other infection ear | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:cleft at the junction of the lobule and helix ---
r_associated #0: 24 -->
en:everted ears
n1=en:cleft at the junction of the lobule and helix | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:congenital small ears ---
r_associated #0: 24 -->
en:everted ears
n1=en:congenital small ears | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:expansion of helical fold at superior point of true longitudinal axis of ear ---
r_associated #0: 24 -->
en:everted ears
n1=en:expansion of helical fold at superior point of true longitudinal axis of ear | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:fleshy ears ---
r_associated #0: 24 -->
en:everted ears
n1=en:fleshy ears | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:hearing impairment, sensorineural, mild ---
r_associated #0: 24 -->
en:everted ears
n1=en:hearing impairment, sensorineural, mild | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:hearing loss begins with loss of high frequencies ---
r_associated #0: 24 -->
en:everted ears
n1=en:hearing loss begins with loss of high frequencies | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:hearing loss, bilateral progressive post-lingual ---
r_associated #0: 24 -->
en:everted ears
n1=en:hearing loss, bilateral progressive post-lingual | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:hearing loss, mild ---
r_associated #0: 24 -->
en:everted ears
n1=en:hearing loss, mild | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:hearing loss, mixed, mild to severe (in heterozygotes) ---
r_associated #0: 24 -->
en:everted ears
n1=en:hearing loss, mixed, mild to severe (in heterozygotes) | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:hearing loss, prelingual, severe to profound (affecting all frequencies) ---
r_associated #0: 24 -->
en:everted ears
n1=en:hearing loss, prelingual, severe to profound (affecting all frequencies) | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:hypercompliant tympanic membranes ---
r_associated #0: 24 -->
en:everted ears
n1=en:hypercompliant tympanic membranes | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:juberg-marsidi syndrome ---
r_associated #0: 24 -->
en:everted ears
n1=en:juberg-marsidi syndrome | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:large ears (in some patients) ---
r_associated #0: 24 -->
en:everted ears
n1=en:large ears (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:large, dysmorphic ears ---
r_associated #0: 24 -->
en:everted ears
n1=en:large, dysmorphic ears | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:low-set ears (in 2/4 patients) ---
r_associated #0: 24 -->
en:everted ears
n1=en:low-set ears (in 2/4 patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:microtia (wws) ---
r_associated #0: 24 -->
en:everted ears
n1=en:microtia (wws) | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:mixed hearing loss ---
r_associated #0: 24 -->
en:everted ears
n1=en:mixed hearing loss | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:narrow external ear canals (1 patient) ---
r_associated #0: 24 -->
en:everted ears
n1=en:narrow external ear canals (1 patient) | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:nonsyndromic sensorineural hearing loss ---
r_associated #0: 24 -->
en:everted ears
n1=en:nonsyndromic sensorineural hearing loss | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:other auditory injuries ---
r_associated #0: 24 -->
en:everted ears
n1=en:other auditory injuries | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:otorrhea ---
r_associated #0: 24 -->
en:everted ears
n1=en:otorrhea | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:posteriorly rotated ear ---
r_associated #0: 24 -->
en:everted ears
n1=en:posteriorly rotated ear | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:profound sensorineural hearing loss ---
r_associated #0: 24 -->
en:everted ears
n1=en:profound sensorineural hearing loss | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:short ears (in 1 family) ---
r_associated #0: 24 -->
en:everted ears
n1=en:short ears (in 1 family) | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:squared-off superior helices ---
r_associated #0: 24 -->
en:everted ears
n1=en:squared-off superior helices | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:synotus ---
r_associated #0: 24 -->
en:everted ears
n1=en:synotus | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:thick ears ---
r_associated #0: 24 -->
en:everted ears
n1=en:thick ears | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:tinnitus (variable) ---
r_associated #0: 24 -->
en:everted ears
n1=en:tinnitus (variable) | n2=en:everted ears | rel=r_associated | relid=0 | w=24
- en:absent brainstem auditory-evoked responses ---
r_associated #0: 23 -->
en:everted ears
n1=en:absent brainstem auditory-evoked responses | n2=en:everted ears | rel=r_associated | relid=0 | w=23
- en:audiogram is gently sloping or flat ---
r_associated #0: 23 -->
en:everted ears
n1=en:audiogram is gently sloping or flat | n2=en:everted ears | rel=r_associated | relid=0 | w=23
- en:concern with appearance of ears ---
r_associated #0: 23 -->
en:everted ears
n1=en:concern with appearance of ears | n2=en:everted ears | rel=r_associated | relid=0 | w=23
- en:eustachian tube salpingitis ---
r_associated #0: 23 -->
en:everted ears
n1=en:eustachian tube salpingitis | n2=en:everted ears | rel=r_associated | relid=0 | w=23
- en:external ear ---
r_associated #0: 23 -->
en:everted ears
n1=en:external ear | n2=en:everted ears | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural (in sister) ---
r_associated #0: 23 -->
en:everted ears
n1=en:hearing loss, sensorineural (in sister) | n2=en:everted ears | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges) ---
r_associated #0: 23 -->
en:everted ears
n1=en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges) | n2=en:everted ears | rel=r_associated | relid=0 | w=23
- en:hypoplasia of the upper part of the helix ---
r_associated #0: 23 -->
en:everted ears
n1=en:hypoplasia of the upper part of the helix | n2=en:everted ears | rel=r_associated | relid=0 | w=23
- en:large appearing ears ---
r_associated #0: 23 -->
en:everted ears
n1=en:large appearing ears | n2=en:everted ears | rel=r_associated | relid=0 | w=23
- en:mondini defect ---
r_associated #0: 23 -->
en:everted ears
n1=en:mondini defect | n2=en:everted ears | rel=r_associated | relid=0 | w=23
- en:narrowing of ear canal ---
r_associated #0: 23 -->
en:everted ears
n1=en:narrowing of ear canal | n2=en:everted ears | rel=r_associated | relid=0 | w=23
- en:no auditory brainstem response to 100-db stimulus ---
r_associated #0: 23 -->
en:everted ears
n1=en:no auditory brainstem response to 100-db stimulus | n2=en:everted ears | rel=r_associated | relid=0 | w=23
- en:no vestibular impairment ---
r_associated #0: 23 -->
en:everted ears
n1=en:no vestibular impairment | n2=en:everted ears | rel=r_associated | relid=0 | w=23
- en:recurrent serous otitis ---
r_associated #0: 23 -->
en:everted ears
n1=en:recurrent serous otitis | n2=en:everted ears | rel=r_associated | relid=0 | w=23
- en:absent ipsilateral middle ear muscle reflexes (in older patients) ---
r_associated #0: 22 -->
en:everted ears
n1=en:absent ipsilateral middle ear muscle reflexes (in older patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=22
- en:audiogram shows sloping configuration ---
r_associated #0: 22 -->
en:everted ears
n1=en:audiogram shows sloping configuration | n2=en:everted ears | rel=r_associated | relid=0 | w=22
- en:conductive hearing loss, bilateral ---
r_associated #0: 22 -->
en:everted ears
n1=en:conductive hearing loss, bilateral | n2=en:everted ears | rel=r_associated | relid=0 | w=22
- en:deafness, sensorineural, variable ---
r_associated #0: 22 -->
en:everted ears
n1=en:deafness, sensorineural, variable | n2=en:everted ears | rel=r_associated | relid=0 | w=22
- en:ear neoplasm ---
r_associated #0: 22 -->
en:everted ears
n1=en:ear neoplasm | n2=en:everted ears | rel=r_associated | relid=0 | w=22
- en:flat audiogram ---
r_associated #0: 22 -->
en:everted ears
n1=en:flat audiogram | n2=en:everted ears | rel=r_associated | relid=0 | w=22
- en:hearing loss (conductive and/or sensorineural) ---
r_associated #0: 22 -->
en:everted ears
n1=en:hearing loss (conductive and/or sensorineural) | n2=en:everted ears | rel=r_associated | relid=0 | w=22
- en:hearing loss (variable) ---
r_associated #0: 22 -->
en:everted ears
n1=en:hearing loss (variable) | n2=en:everted ears | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural (reported in 1 patient) ---
r_associated #0: 22 -->
en:everted ears
n1=en:hearing loss, sensorineural (reported in 1 patient) | n2=en:everted ears | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural, mid-frequency (in some patients) ---
r_associated #0: 22 -->
en:everted ears
n1=en:hearing loss, sensorineural, mid-frequency (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=22
- en:hearing loss, sensorineural, progressive (childhood-onset) ---
r_associated #0: 22 -->
en:everted ears
n1=en:hearing loss, sensorineural, progressive (childhood-onset) | n2=en:everted ears | rel=r_associated | relid=0 | w=22
- en:limited auditory function ---
r_associated #0: 22 -->
en:everted ears
n1=en:limited auditory function | n2=en:everted ears | rel=r_associated | relid=0 | w=22
- en:macrotia ---
r_associated #0: 22 -->
en:everted ears
n1=en:macrotia | n2=en:everted ears | rel=r_associated | relid=0 | w=22
- en:other diseases of ear/mastoid ---
r_associated #0: 22 -->
en:everted ears
n1=en:other diseases of ear/mastoid | n2=en:everted ears | rel=r_associated | relid=0 | w=22
- en:overfolded, rumpled ears ---
r_associated #0: 22 -->
en:everted ears
n1=en:overfolded, rumpled ears | n2=en:everted ears | rel=r_associated | relid=0 | w=22
- en:phonophobia ---
r_associated #0: 22 -->
en:everted ears
n1=en:phonophobia | n2=en:everted ears | rel=r_associated | relid=0 | w=22
- en:progressive hearing impairment ---
r_associated #0: 22 -->
en:everted ears
n1=en:progressive hearing impairment | n2=en:everted ears | rel=r_associated | relid=0 | w=22
- en:recurrent otitis media ---
r_associated #0: 22 -->
en:everted ears
n1=en:recurrent otitis media | n2=en:everted ears | rel=r_associated | relid=0 | w=22
- en:right ear ---
r_associated #0: 22 -->
en:everted ears
n1=en:right ear | n2=en:everted ears | rel=r_associated | relid=0 | w=22
- en:small cavum conchae ---
r_associated #0: 22 -->
en:everted ears
n1=en:small cavum conchae | n2=en:everted ears | rel=r_associated | relid=0 | w=22
- en:small/rudimentary tragus, antitragus and lobule ---
r_associated #0: 22 -->
en:everted ears
n1=en:small/rudimentary tragus, antitragus and lobule | n2=en:everted ears | rel=r_associated | relid=0 | w=22
- en:thick, firm earlobes ---
r_associated #0: 22 -->
en:everted ears
n1=en:thick, firm earlobes | n2=en:everted ears | rel=r_associated | relid=0 | w=22
- en:absent earlobe ---
r_associated #0: 21 -->
en:everted ears
n1=en:absent earlobe | n2=en:everted ears | rel=r_associated | relid=0 | w=21
- en:absent or abnormal otoacoustic emissions ---
r_associated #0: 21 -->
en:everted ears
n1=en:absent or abnormal otoacoustic emissions | n2=en:everted ears | rel=r_associated | relid=0 | w=21
- en:absent stapedial reflex ---
r_associated #0: 21 -->
en:everted ears
n1=en:absent stapedial reflex | n2=en:everted ears | rel=r_associated | relid=0 | w=21
- en:decreased auditory brainstem responses ---
r_associated #0: 21 -->
en:everted ears
n1=en:decreased auditory brainstem responses | n2=en:everted ears | rel=r_associated | relid=0 | w=21
- en:disturbance of equilibrium ---
r_associated #0: 21 -->
en:everted ears
n1=en:disturbance of equilibrium | n2=en:everted ears | rel=r_associated | relid=0 | w=21
- en:hearing impairment (in some patients) ---
r_associated #0: 21 -->
en:everted ears
n1=en:hearing impairment (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=21
- en:hearing impairment, mild (2 patients) ---
r_associated #0: 21 -->
en:everted ears
n1=en:hearing impairment, mild (2 patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=21
- en:hearing loss (1 patient) ---
r_associated #0: 21 -->
en:everted ears
n1=en:hearing loss (1 patient) | n2=en:everted ears | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural (high frequency) ---
r_associated #0: 21 -->
en:everted ears
n1=en:hearing loss, sensorineural (high frequency) | n2=en:everted ears | rel=r_associated | relid=0 | w=21
- en:hearing loss, unilateral, mild ---
r_associated #0: 21 -->
en:everted ears
n1=en:hearing loss, unilateral, mild | n2=en:everted ears | rel=r_associated | relid=0 | w=21
- en:loss of vestibular reflexes ---
r_associated #0: 21 -->
en:everted ears
n1=en:loss of vestibular reflexes | n2=en:everted ears | rel=r_associated | relid=0 | w=21
- en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies ---
r_associated #0: 21 -->
en:everted ears
n1=en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies | n2=en:everted ears | rel=r_associated | relid=0 | w=21
- en:narrowed external ear canal ---
r_associated #0: 21 -->
en:everted ears
n1=en:narrowed external ear canal | n2=en:everted ears | rel=r_associated | relid=0 | w=21
- en:otitis externa ---
r_associated #0: 21 -->
en:everted ears
n1=en:otitis externa | n2=en:everted ears | rel=r_associated | relid=0 | w=21
- en:otitis with effusion ---
r_associated #0: 21 -->
en:everted ears
n1=en:otitis with effusion | n2=en:everted ears | rel=r_associated | relid=0 | w=21
- en:overfolding of the superior helices ---
r_associated #0: 21 -->
en:everted ears
n1=en:overfolding of the superior helices | n2=en:everted ears | rel=r_associated | relid=0 | w=21
- en:preauricular pits (70-80% of patients) ---
r_associated #0: 21 -->
en:everted ears
n1=en:preauricular pits (70-80% of patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=21
- en:prominent earlobes (in some patients) ---
r_associated #0: 21 -->
en:everted ears
n1=en:prominent earlobes (in some patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=21
- en:sensorineural hearing loss (20% of patients) ---
r_associated #0: 21 -->
en:everted ears
n1=en:sensorineural hearing loss (20% of patients) | n2=en:everted ears | rel=r_associated | relid=0 | w=21
- en:slit-like opening of the exterior auditory meatus ---
r_associated #0: 21 -->
en:everted ears
n1=en:slit-like opening of the exterior auditory meatus | n2=en:everted ears | rel=r_associated | relid=0 | w=21
- en:small pits anterior to the helix (1 patient) ---
r_associated #0: 21 -->
en:everted ears
n1=en:small pits anterior to the helix (1 patient) | n2=en:everted ears | rel=r_associated | relid=0 | w=21
- Trouble de l'équilibre ---
r_associated #0: 15 -->
en:everted ears
n1=Trouble de l'équilibre | n2=en:everted ears | rel=r_associated | relid=0 | w=15
- en:dizzy spells ---
r_associated #0: 15 -->
en:everted ears
n1=en:dizzy spells | n2=en:everted ears | rel=r_associated | relid=0 | w=15
- en:giddiness ---
r_associated #0: 15 -->
en:everted ears
n1=en:giddiness | n2=en:everted ears | rel=r_associated | relid=0 | w=15
- en:scatterbrain ---
r_associated #0: 15 -->
en:everted ears
n1=en:scatterbrain | n2=en:everted ears | rel=r_associated | relid=0 | w=15
- vertiges ---
r_associated #0: 15 -->
en:everted ears
n1=vertiges | n2=en:everted ears | rel=r_associated | relid=0 | w=15
- vertigineux ---
r_associated #0: 15 -->
en:everted ears
n1=vertigineux | n2=en:everted ears | rel=r_associated | relid=0 | w=15
- Étourdi ---
r_associated #0: 15 -->
en:everted ears
n1=Étourdi | n2=en:everted ears | rel=r_associated | relid=0 | w=15
- Étourdie ---
r_associated #0: 15 -->
en:everted ears
n1=Étourdie | n2=en:everted ears | rel=r_associated | relid=0 | w=15
- étourdie ---
r_associated #0: 15 -->
en:everted ears
n1=étourdie | n2=en:everted ears | rel=r_associated | relid=0 | w=15
- étourdies ---
r_associated #0: 15 -->
en:everted ears
n1=étourdies | n2=en:everted ears | rel=r_associated | relid=0 | w=15
- étourdis ---
r_associated #0: 15 -->
en:everted ears
n1=étourdis | n2=en:everted ears | rel=r_associated | relid=0 | w=15
- étourdissements ---
r_associated #0: 15 -->
en:everted ears
n1=étourdissements | n2=en:everted ears | rel=r_associated | relid=0 | w=15
- Hyperacousie ---
r_associated #0: 10 -->
en:everted ears
n1=Hyperacousie | n2=en:everted ears | rel=r_associated | relid=0 | w=10
- Oto-rhino-laryngologiste ---
r_associated #0: 10 -->
en:everted ears
n1=Oto-rhino-laryngologiste | n2=en:everted ears | rel=r_associated | relid=0 | w=10
- Otorhinolaryngologiste ---
r_associated #0: 10 -->
en:everted ears
n1=Otorhinolaryngologiste | n2=en:everted ears | rel=r_associated | relid=0 | w=10
- ankylose stapédo-vestibulaire ---
r_associated #0: 10 -->
en:everted ears
n1=ankylose stapédo-vestibulaire | n2=en:everted ears | rel=r_associated | relid=0 | w=10
- ankylose stapédo-vestibulaire l.f. ---
r_associated #0: 10 -->
en:everted ears
n1=ankylose stapédo-vestibulaire l.f. | n2=en:everted ears | rel=r_associated | relid=0 | w=10
- aplati ---
r_associated #0: 10 -->
en:everted ears
n1=aplati | n2=en:everted ears | rel=r_associated | relid=0 | w=10
- en:deaf-muteness ---
r_associated #0: 10 -->
en:everted ears
n1=en:deaf-muteness | n2=en:everted ears | rel=r_associated | relid=0 | w=10
- en:deaf-mutism ---
r_associated #0: 10 -->
en:everted ears
n1=en:deaf-mutism | n2=en:everted ears | rel=r_associated | relid=0 | w=10
- en:hearing defect ---
r_associated #0: 10 -->
en:everted ears
n1=en:hearing defect | n2=en:everted ears | rel=r_associated | relid=0 | w=10
- en:hearing deficiency ---
r_associated #0: 10 -->
en:everted ears
n1=en:hearing deficiency | n2=en:everted ears | rel=r_associated | relid=0 | w=10
- en:lughole ---
r_associated #0: 10 -->
en:everted ears
n1=en:lughole | n2=en:everted ears | rel=r_associated | relid=0 | w=10
- en:schitzel ---
r_associated #0: 10 -->
en:everted ears
n1=en:schitzel | n2=en:everted ears | rel=r_associated | relid=0 | w=10
- en:speech difficulties due to deafness ---
r_associated #0: 10 -->
en:everted ears
n1=en:speech difficulties due to deafness | n2=en:everted ears | rel=r_associated | relid=0 | w=10
- oreille moyenne ---
r_associated #0: 10 -->
en:everted ears
n1=oreille moyenne | n2=en:everted ears | rel=r_associated | relid=0 | w=10
- otite moyenne adhésive ---
r_associated #0: 10 -->
en:everted ears
n1=otite moyenne adhésive | n2=en:everted ears | rel=r_associated | relid=0 | w=10
- surdité ---
r_associated #0: 10 -->
en:everted ears
n1=surdité | n2=en:everted ears | rel=r_associated | relid=0 | w=10
- tête de linotte ---
r_associated #0: 10 -->
en:everted ears
n1=tête de linotte | n2=en:everted ears | rel=r_associated | relid=0 | w=10
- Étourdissements ---
r_associated #0: 10 -->
en:everted ears
n1=Étourdissements | n2=en:everted ears | rel=r_associated | relid=0 | w=10
- à priori ---
r_associated #0: 10 -->
en:everted ears
n1=à priori | n2=en:everted ears | rel=r_associated | relid=0 | w=10
- Sensation de rotation ---
r_associated #0: 5 -->
en:everted ears
n1=Sensation de rotation | n2=en:everted ears | rel=r_associated | relid=0 | w=5
- escalope ---
r_associated #0: -20 -->
en:everted ears
n1=escalope | n2=en:everted ears | rel=r_associated | relid=0 | w=-20
|