'en:hearing loss, sensorineural, bilateral, moderate-to-severe'
(id=6815239 ; fe=en:hearing loss, sensorineural, bilateral, moderate-to-severe ; type=1 ; niveau=200 ;
luminosité=25 ;
somme entrante=28284 creation date=2017-06-25 touchdate=2025-12-28 23:09:07.000) ≈ 741 relations sortantes
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 43 / 1 ->
en:deafness, early-onset
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, early-onset | rel=r_associated | relid=0 | w=43
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 43 / 1 ->
en:downsloping audiogram
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:downsloping audiogram | rel=r_associated | relid=0 | w=43
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 43 / 1 ->
en:external ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:external ear | rel=r_associated | relid=0 | w=43
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 43 / 1 ->
en:fleshy ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:fleshy ears | rel=r_associated | relid=0 | w=43
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 43 / 1 ->
en:hearing loss, initially conductive, later mixed conductive-sensorineural
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, initially conductive, later mixed conductive-sensorineural | rel=r_associated | relid=0 | w=43
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 43 / 1 ->
en:hypoplastic pinnae (30-60% of patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hypoplastic pinnae (30-60% of patients) | rel=r_associated | relid=0 | w=43
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 43 / 1 ->
en:narrow external ear canals (1 patient)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:narrow external ear canals (1 patient) | rel=r_associated | relid=0 | w=43
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 43 / 1 ->
en:poorly formed ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:poorly formed ears | rel=r_associated | relid=0 | w=43
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 43 / 1 ->
en:prominent crura
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:prominent crura | rel=r_associated | relid=0 | w=43
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 43 / 1 ->
en:small, posteriorly rotated ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:small, posteriorly rotated ears | rel=r_associated | relid=0 | w=43
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 42 / 0.977 ->
en:deafness, profound congenital sensorineural
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, profound congenital sensorineural | rel=r_associated | relid=0 | w=42
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 42 / 0.977 ->
en:inner ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:inner ear | rel=r_associated | relid=0 | w=42
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 42 / 0.977 ->
en:near-stenosis of bony portion of auditory canal
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:near-stenosis of bony portion of auditory canal | rel=r_associated | relid=0 | w=42
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 42 / 0.977 ->
en:near-stenosis of bony portion of auditory canal (in homozygotes)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:near-stenosis of bony portion of auditory canal (in homozygotes) | rel=r_associated | relid=0 | w=42
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 42 / 0.977 ->
en:severe to profound deafness
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:severe to profound deafness | rel=r_associated | relid=0 | w=42
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 42 / 0.977 ->
en:vertigo, single occurrence (in 2 patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:vertigo, single occurrence (in 2 patients) | rel=r_associated | relid=0 | w=42
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 41 / 0.953 ->
en:conductive hearing loss (30% of patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:conductive hearing loss (30% of patients) | rel=r_associated | relid=0 | w=41
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 41 / 0.953 ->
en:hearing loss, sensorineural, progressive (childhood-onset)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural, progressive (childhood-onset) | rel=r_associated | relid=0 | w=41
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 41 / 0.953 ->
en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural | rel=r_associated | relid=0 | w=41
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 41 / 0.953 ->
en:low-set ears (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:low-set ears (rare) | rel=r_associated | relid=0 | w=41
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 41 / 0.953 ->
en:oae responses may decrease with age or use of hearing aids
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:oae responses may decrease with age or use of hearing aids | rel=r_associated | relid=0 | w=41
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 41 / 0.953 ->
en:pointed upper helix
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:pointed upper helix | rel=r_associated | relid=0 | w=41
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 41 / 0.953 ->
en:preauricular fistulas, bilateral
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:preauricular fistulas, bilateral | rel=r_associated | relid=0 | w=41
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 40 / 0.93 ->
en:dysmorphic ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:dysmorphic ears | rel=r_associated | relid=0 | w=40
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 40 / 0.93 ->
en:hearing loss, sensorineural, prelingual
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural, prelingual | rel=r_associated | relid=0 | w=40
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 40 / 0.93 ->
en:impaired tympanic membrane mobility
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:impaired tympanic membrane mobility | rel=r_associated | relid=0 | w=40
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 40 / 0.93 ->
en:loss of hearing (45%)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:loss of hearing (45%) | rel=r_associated | relid=0 | w=40
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 40 / 0.93 ->
en:neonatal cystic lesions of the pinnae
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:neonatal cystic lesions of the pinnae | rel=r_associated | relid=0 | w=40
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 40 / 0.93 ->
en:simplified helices
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:simplified helices | rel=r_associated | relid=0 | w=40
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 40 / 0.93 ->
en:stapes ankylosis
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:stapes ankylosis | rel=r_associated | relid=0 | w=40
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 39 / 0.907 ->
en:deafness, sensorineural (severe to profound)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, sensorineural (severe to profound) | rel=r_associated | relid=0 | w=39
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 39 / 0.907 ->
en:flat or shallow u-shaped audiogram
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:flat or shallow u-shaped audiogram | rel=r_associated | relid=0 | w=39
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 39 / 0.907 ->
en:large dysplastic ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:large dysplastic ears | rel=r_associated | relid=0 | w=39
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 39 / 0.907 ->
en:large ears (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:large ears (in some patients) | rel=r_associated | relid=0 | w=39
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 38 / 0.884 ->
en:auditory impairment
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:auditory impairment | rel=r_associated | relid=0 | w=38
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 38 / 0.884 ->
en:conductive hearing loss to due otitis media
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:conductive hearing loss to due otitis media | rel=r_associated | relid=0 | w=38
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 38 / 0.884 ->
en:deafness, sensorineural, variable
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, sensorineural, variable | rel=r_associated | relid=0 | w=38
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 38 / 0.884 ->
en:hearing loss, sensorineural (in one family)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural (in one family) | rel=r_associated | relid=0 | w=38
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 37 / 0.86 ->
en:acute otitis media/myringitis
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:acute otitis media/myringitis | rel=r_associated | relid=0 | w=37
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 37 / 0.86 ->
en:chronic otitis media
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:chronic otitis media | rel=r_associated | relid=0 | w=37
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 37 / 0.86 ->
en:deafness, sensorineural, profound
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, sensorineural, profound | rel=r_associated | relid=0 | w=37
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 37 / 0.86 ->
en:deafness, sensorineural, profound (prelingual onset)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, sensorineural, profound (prelingual onset) | rel=r_associated | relid=0 | w=37
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 37 / 0.86 ->
en:normal otoacoustic emissions (oae), indicating intact outer ear hair cell function
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:normal otoacoustic emissions (oae), indicating intact outer ear hair cell function | rel=r_associated | relid=0 | w=37
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 37 / 0.86 ->
en:rotated ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:rotated ears | rel=r_associated | relid=0 | w=37
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 37 / 0.86 ->
en:severe to profound hearing impairment by early adulthood
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:severe to profound hearing impairment by early adulthood | rel=r_associated | relid=0 | w=37
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 36 / 0.837 ->
en:abnormal communication between the subarachnoid space in the meatus and the perilymph
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormal communication between the subarachnoid space in the meatus and the perilymph | rel=r_associated | relid=0 | w=36
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 36 / 0.837 ->
en:absent helices, bilaterally
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:absent helices, bilaterally | rel=r_associated | relid=0 | w=36
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 36 / 0.837 ->
en:complete bony atresia of medial portion of external auditory canal (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:complete bony atresia of medial portion of external auditory canal (in some patients) | rel=r_associated | relid=0 | w=36
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 36 / 0.837 ->
en:everted ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:everted ears | rel=r_associated | relid=0 | w=36
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 36 / 0.837 ->
en:hearing deficits (28% of adults)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing deficits (28% of adults) | rel=r_associated | relid=0 | w=36
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 36 / 0.837 ->
en:hyperacusis
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hyperacusis | rel=r_associated | relid=0 | w=36
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 36 / 0.837 ->
en:low-frequency sensorineural hearing impairment
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:low-frequency sensorineural hearing impairment | rel=r_associated | relid=0 | w=36
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 36 / 0.837 ->
en:microtia, type i
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:microtia, type i | rel=r_associated | relid=0 | w=36
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 36 / 0.837 ->
en:raised earlobes
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:raised earlobes | rel=r_associated | relid=0 | w=36
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:abnormal auditory brainstem responses
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormal auditory brainstem responses | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:abnormal bridge connecting the crus of the helix and antihelix
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormal bridge connecting the crus of the helix and antihelix | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:abnormally folded ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormally folded ears | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:anteriorly rotated ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:anteriorly rotated ears | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:apical cartilage deformity
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:apical cartilage deformity | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:attached ear lobes
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:attached ear lobes | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:audiogram shows sloping configuration
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:audiogram shows sloping configuration | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:bleeding from ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:bleeding from ear | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:cochlear degeneration
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:cochlear degeneration | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:cochlear malformation defect (mondini dysplasia) (less common)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:cochlear malformation defect (mondini dysplasia) (less common) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:cochleosaccular dysplasia
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:cochleosaccular dysplasia | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:congenital absence of external ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:congenital absence of external ear | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:deafness, autosomal recessive 101
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, autosomal recessive 101 | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:dizziness
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:dizziness | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:dysplastic helices
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:dysplastic helices | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:ear dimple
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:ear dimple | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:entire ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:entire ear | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:eustachian tube salpingitis
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:eustachian tube salpingitis | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:excessive cerumen
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:excessive cerumen | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:hearing impairment, mild (2 patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing impairment, mild (2 patients) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:hearing loss, conductive or mixed
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, conductive or mixed | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:hearing loss, late-onset sensorineural, mild-to moderate (less common)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, late-onset sensorineural, mild-to moderate (less common) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:hearing loss, mixed (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, mixed (in some patients) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:hearing loss, progressive sensorineural, affecting high frequencies
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, progressive sensorineural, affecting high frequencies | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:hearing loss, sensorineural (bilateral, prelingual)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural (bilateral, prelingual) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:hearing loss, sensorineural (in patients with larger deletions)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural (in patients with larger deletions) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:hearing loss, sensorineural (reported in 1 patient)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural (reported in 1 patient) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:hearing loss, sensorineural (type ii)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural (type ii) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:hearing loss, unilateral (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, unilateral (rare) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:hearing loss, unilateral or bilateral, conductive, sensorineural, or mixed
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, unilateral or bilateral, conductive, sensorineural, or mixed | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:large, floppy ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:large, floppy ears | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:long ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:long ear | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:loss of vestibular caloric response
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:loss of vestibular caloric response | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:low set ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:low set ears | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:low-set ears (1 patient)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:low-set ears (1 patient) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:low-set ears (3 patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:low-set ears (3 patients) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:low-set ears (severe form)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:low-set ears (severe form) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:narrow ear lobes
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:narrow ear lobes | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:nonsyndromic sensorineural hearing loss
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:nonsyndromic sensorineural hearing loss | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:other symptom/complaint of ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:other symptom/complaint of ear | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:otitis media
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:otitis media | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:preauricular sinus
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:preauricular sinus | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:profound deafness
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:profound deafness | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:progressive conductive hearing impairment
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:progressive conductive hearing impairment | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:progressive mixed conductive and sensorineural hearing loss
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:progressive mixed conductive and sensorineural hearing loss | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:prominence and protrusion of upper third of the ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:prominence and protrusion of upper third of the ear | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:prominent ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:prominent ear | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:prominent helices
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:prominent helices | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:pseudomembranous inflammation of the middle ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:pseudomembranous inflammation of the middle ear | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:recurrent otitis
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:recurrent otitis | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:sensorineural deafness (onset in the second decade in 25 to 30% of patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural deafness (onset in the second decade in 25 to 30% of patients) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:sensorineural deafness, postlingual, progressive
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural deafness, postlingual, progressive | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:sensorineural deafness, progressive, late-onset
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural deafness, progressive, late-onset | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:sensorineural hearing impairment (less common)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural hearing impairment (less common) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:sensorineural hearing loss (described in 1 family)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural hearing loss (described in 1 family) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:sensorineural hearing loss, mild to moderate
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural hearing loss, mild to moderate | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:severe narrowing of cartilagenous auditory canal (in homozygotes)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:severe narrowing of cartilagenous auditory canal (in homozygotes) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:simple helix
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:simple helix | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:small lobes
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:small lobes | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:stenosis of external auditory canal
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:stenosis of external auditory canal | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:strabismus (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:strabismus (in some patients) | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:thickened lobes
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:thickened lobes | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:transient evoked otoacoustic emissions cannot be detected
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:transient evoked otoacoustic emissions cannot be detected | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:u- or bowl-shaped audiogram
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:u- or bowl-shaped audiogram | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:unconnected or fused stapes and incus
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:unconnected or fused stapes and incus | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:vestibular hyporeflexia
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:vestibular hyporeflexia | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 35 / 0.814 ->
en:wide, flattened earlobes
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:wide, flattened earlobes | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:abnormality of the outer ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormality of the outer ear | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:abnormally shaped ears (in one family)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormally shaped ears (in one family) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:absent or abnormal otoacoustic emissions
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:absent or abnormal otoacoustic emissions | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:affects mid- to high-frequencies
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:affects mid- to high-frequencies | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:atretic auditory canal
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:atretic auditory canal | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:bilateral dys-synchronized auditory brainstem responses
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:bilateral dys-synchronized auditory brainstem responses | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:bilateral sensorineural hearing loss (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:bilateral sensorineural hearing loss (in some patients) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:cochlear malformation
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:cochlear malformation | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:conductive hearing loss
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:conductive hearing loss | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:congenital deafness
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:congenital deafness | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:cupped ears (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:cupped ears (in some patients) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:cystic dilatation of cochlea and vestibulum
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:cystic dilatation of cochlea and vestibulum | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:deafness (in 1 of 2 families)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness (in 1 of 2 families) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:deafness affects all frequencies
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness affects all frequencies | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:deafness due to bilateral cochlear malformation (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:deafness, prelingual, profound (affects all frequencies)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, prelingual, profound (affects all frequencies) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:deafness, sensorineural (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, sensorineural (in some patients) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:deafness, sensorineural (reported in 1 family)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, sensorineural (reported in 1 family) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:deep-set ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deep-set ears | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:ear | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:ear neoplasm
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:ear neoplasm | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:ear pits, posterior helical
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:ear pits, posterior helical | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:folded helix
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:folded helix | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:hearing loss (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss (rare) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:hearing loss begins with loss of high frequencies
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss begins with loss of high frequencies | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:hearing loss, congenital sensorineural, severe to profound
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, congenital sensorineural, severe to profound | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:hearing loss, progressive (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, progressive (in some patients) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:hearing loss, progressive, starting in infancy
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, progressive, starting in infancy | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:hearing loss, severe to profound, affecting all frequencies
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, severe to profound, affecting all frequencies | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:hypertrophic auricular cartilage
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hypertrophic auricular cartilage | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:internal auditory canal hypoplasia
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:internal auditory canal hypoplasia | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:keratotic plaque around ear meatus
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:keratotic plaque around ear meatus | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:large simple ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:large simple ears | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:large, dysmorphic ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:large, dysmorphic ears | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:lobule creases
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:lobule creases | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:meniere disease
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:meniere disease | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:mild to moderate hearing loss across most frequencies
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:mild to moderate hearing loss across most frequencies | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:narrow ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:narrow ears | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:no auditory brainstem response (abr)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:no auditory brainstem response (abr) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:no hearing loss
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:no hearing loss | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:normal vestibular function
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:normal vestibular function | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:organ of corti degeneration
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:organ of corti degeneration | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:other auditory injuries
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:other auditory injuries | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:overfolding of the superior helices
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:overfolding of the superior helices | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:pale, stiff pinnae
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:pale, stiff pinnae | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:pigmentation of the ear cartilage
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:pigmentation of the ear cartilage | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:posteriorly rotated ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:posteriorly rotated ear | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:posteriorly rotated ears (1/4 patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:posteriorly rotated ears (1/4 patients) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:posteriorly rotated ears (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:posteriorly rotated ears (in some patients) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:profound sensorineural hearing loss
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:profound sensorineural hearing loss | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:prominent ears (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:prominent ears (in some patients) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:recurrent otitis media (18%)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:recurrent otitis media (18%) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:retinitis (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:retinitis (in some patients) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:right ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:right ear | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:sensation of blocked ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensation of blocked ears | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:sensorineural deafness (reported in 1 family)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural deafness (reported in 1 family) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:sensorineural hearing loss (1 family)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural hearing loss (1 family) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:sensorineural hearing loss (3 patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural hearing loss (3 patients) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:sensorineural hearing loss (early-onset form)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural hearing loss (early-onset form) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:sensorineural hearing loss (uncommon)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural hearing loss (uncommon) | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:sensorineural, conductive, or mixed hearing loss
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural, conductive, or mixed hearing loss | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:small auricles
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:small auricles | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:squared-off superior helices
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:squared-off superior helices | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:stapes fixation
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:stapes fixation | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:stiff, prominent pinnae
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:stiff, prominent pinnae | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:unravelling of superior helices
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:unravelling of superior helices | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:vertigo
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:vertigo | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:vestibular areflexia
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:vestibular areflexia | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:vestibular areflexia, complete
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:vestibular areflexia, complete | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:vestibular hypofunction
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:vestibular hypofunction | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 34 / 0.791 ->
en:vestibulopathy, bilateral, progressive
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:vestibulopathy, bilateral, progressive | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:abnormal amplitude modulation detection
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormal amplitude modulation detection | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:abnormal brain auditory evoked responses (baer)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormal brain auditory evoked responses (baer) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:abnormal ear configuration
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormal ear configuration | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:absence of the helix and distal scapha in middle third of the ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:absence of the helix and distal scapha in middle third of the ear | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:absent ipsilateral middle ear muscle reflexes (in older patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:absent ipsilateral middle ear muscle reflexes (in older patients) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:absent lobules
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:absent lobules | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:anteriorly displaced ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:anteriorly displaced ears | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:anteverted pinnae
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:anteverted pinnae | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:atretic ear canals
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:atretic ear canals | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:audiogram may be ascending
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:audiogram may be ascending | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:aural atresia, congenital
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:aural atresia, congenital | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:bat ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:bat ear | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:bilateral congenital profound sensorineural hearing loss
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:bilateral congenital profound sensorineural hearing loss | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:concern with appearance of ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:concern with appearance of ears | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:deafness (sensorineural or mixed sensorineural and conductive)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness (sensorineural or mixed sensorineural and conductive) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:deafness labyrinthine
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness labyrinthine | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:deafness, secondary to cranial hyperostosis
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, secondary to cranial hyperostosis | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:deafness, sensorineural, especially affecting high frequencies
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, sensorineural, especially affecting high frequencies | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:downward sloping or flat audiogram
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:downward sloping or flat audiogram | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:ear cartilage calcification
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:ear cartilage calcification | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:hearing impairment may occur
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing impairment may occur | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:hearing loss (1 patient)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss (1 patient) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:hearing loss (95% of patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss (95% of patients) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:hearing loss (conductive and/or sensorineural)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss (conductive and/or sensorineural) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:hearing loss, bilateral
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, bilateral | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:hearing loss, congenital profound
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, congenital profound | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:hearing loss, high-frequency (onset in childhood-adolescence)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, high-frequency (onset in childhood-adolescence) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:hearing loss, more severe at lower frequencies
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, more severe at lower frequencies | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:hearing loss, sensorineural (high frequency)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural (high frequency) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:hearing loss, sensorineural (variable)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural (variable) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:hearing loss, sensorineural, mid-frequency (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural, mid-frequency (in some patients) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:hearing normal
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing normal | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:hypermobile
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hypermobile | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:large fleshy earlobes
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:large fleshy earlobes | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:loss of high frequencies at onset
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:loss of high frequencies at onset | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:loss of outer hair cell function
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:loss of outer hair cell function | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:mild cochlear hearing loss (1 patient)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:mild cochlear hearing loss (1 patient) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:mondini malformation
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:mondini malformation | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:morphological abnormality of the middle ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:morphological abnormality of the middle ear | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:narrowed external ear canal (30% of patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:narrowed external ear canal (30% of patients) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:narrowing of ear canal
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:narrowing of ear canal | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:no vestibular impairment
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:no vestibular impairment | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:nonprogressive deafness
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:nonprogressive deafness | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:normal otoacoustic emissions
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:normal otoacoustic emissions | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:otorrhea
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:otorrhea | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:poorly formed pinnae
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:poorly formed pinnae | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:posteriorly rotated ears (female)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:posteriorly rotated ears (female) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:pre- and post-auricular skin or cartilaginous tags
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:pre- and post-auricular skin or cartilaginous tags | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:prolonged brainstem auditory evoked potentials (baep)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:prolonged brainstem auditory evoked potentials (baep) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:protruding ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:protruding ears | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:protruding ears (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:protruding ears (in some patients) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:protruding ears (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:protruding ears (rare) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:protruding, simple ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:protruding, simple ears | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:sensorineural hearing loss (less common)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural hearing loss (less common) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:simple auricles
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:simple auricles | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:small ears with large lobules
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:small ears with large lobules | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:superiorly displaced ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:superiorly displaced ears | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:thick earlobes
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:thick earlobes | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:thick, firm earlobes
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:thick, firm earlobes | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:thickened helices
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:thickened helices | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:tympanic membrane perforation
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:tympanic membrane perforation | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:uplifted earlobes
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:uplifted earlobes | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:upsloping audiograms
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:upsloping audiograms | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:vestibular anomalies (less common)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:vestibular anomalies (less common) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 32 / 0.744 ->
en:vestibular function defect (decreased in some, normal in other patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:vestibular function defect (decreased in some, normal in other patients) | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:abnormal gap detection
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormal gap detection | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:abnormal or absent auditory nerve and brainstem responses
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormal or absent auditory nerve and brainstem responses | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:abnormal speech discrimination
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormal speech discrimination | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:absence of acoustic reflex
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:absence of acoustic reflex | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:absent brainstem auditory responses
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:absent brainstem auditory responses | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:absent vestibular function (caloric test)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:absent vestibular function (caloric test) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:air-bone gap of greater than 20 db across 0.5 to 2 khz
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:air-bone gap of greater than 20 db across 0.5 to 2 khz | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:asymmetry of the ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:asymmetry of the ears | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:auditory neuropathy spectrum disorder
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:auditory neuropathy spectrum disorder | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:chronic otitis
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:chronic otitis | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:cleft at the junction of the lobule and helix
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:cleft at the junction of the lobule and helix | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:conductive and sensorineural hearing loss
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:conductive and sensorineural hearing loss | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:conductive hearing loss, mild bilateral (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:conductive hearing loss, mild bilateral (rare) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:cup-shaped auricles
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:cup-shaped auricles | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:deafness (variable)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness (variable) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:deafness, congenital sensorineural, profound (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, congenital sensorineural, profound (in some patients) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:deafness, profound, affects all frequencies
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, profound, affects all frequencies | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:decreased auditory brainstem responses
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:decreased auditory brainstem responses | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:dysplastic ears (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:dysplastic ears (in some patients) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:enlarged vestibular aqueduct
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:enlarged vestibular aqueduct | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:external auditory canal narrow
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:external auditory canal narrow | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:folded superior edge of helix
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:folded superior edge of helix | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:hearing disorder (1 patient)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing disorder (1 patient) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:hearing impairment
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing impairment | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:hearing impairment (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing impairment (rare) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:hearing loss (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss (in some patients) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:hearing loss (variable)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss (variable) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:hearing loss affects all frequencies
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss affects all frequencies | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:hearing loss, conductive (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, conductive (in some patients) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:hearing loss, prelingual, severe to profound (affecting all frequencies)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, prelingual, severe to profound (affecting all frequencies) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:hearing loss, progressive conductive and/or sensorineural, during adulthood
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, progressive conductive and/or sensorineural, during adulthood | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:hearing loss, sensorineural (in some cases)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural (in some cases) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:hearing loss, unilateral, mild
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, unilateral, mild | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:high-frequency tinnitus at onset
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:high-frequency tinnitus at onset | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:hypoplastic ear lobes
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hypoplastic ear lobes | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:hypoplastic malleus (1 patient)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hypoplastic malleus (1 patient) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:increased posterior angulation
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:increased posterior angulation | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:long, lobulated ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:long, lobulated ears | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:malformed auricle (1 patient)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:malformed auricle (1 patient) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:malformed earlobes
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:malformed earlobes | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:narrow auditory canals (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:narrow auditory canals (rare) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:narrow intertragic notch
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:narrow intertragic notch | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:no deafness
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:no deafness | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:occasional conductive hearing loss
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:occasional conductive hearing loss | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:ossified pinnae
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:ossified pinnae | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:overfolded helix
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:overfolded helix | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:partial hearing loss
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:partial hearing loss | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:postauricular pit
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:postauricular pit | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:preauricular skin tags (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:preauricular skin tags (in some patients) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:prominent antihelix
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:prominent antihelix | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:prominent ears (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:prominent ears (rare) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:pulsatile tinnitus (tympanic paraganglioma)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:pulsatile tinnitus (tympanic paraganglioma) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:recurrent serous otitis
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:recurrent serous otitis | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:sensorineural hearing loss (20% of patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural hearing loss (20% of patients) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:sensorineural hearing loss (males only)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural hearing loss (males only) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:sensorineural hearing loss, progressive bilateral postlingual
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural hearing loss, progressive bilateral postlingual | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:serous otitis media
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:serous otitis media | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:small pinna
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:small pinna | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:small pits anterior to the helix (1 patient)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:small pits anterior to the helix (1 patient) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:thick ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:thick ears | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:triangular-shaped ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:triangular-shaped ears | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:underdeveloped nasal alae
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:underdeveloped nasal alae | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:underdeveloped tragus
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:underdeveloped tragus | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:unfolded superior helices
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:unfolded superior helices | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:uplift of earlobes (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:uplift of earlobes (in some patients) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 31 / 0.721 ->
en:vestibular dysfunction (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:vestibular dysfunction (in some patients) | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:'tilted' ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:'tilted' ears | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:a subset of patients have hearing loss
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:a subset of patients have hearing loss | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:abnormal auditory temporal processes
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormal auditory temporal processes | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:abnormal brainstem auditory evoked potentials (baep)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormal brainstem auditory evoked potentials (baep) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:abnormal folded pinna
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormal folded pinna | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:abnormality of the middle ear ossicles
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormality of the middle ear ossicles | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:abnormally formed ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormally formed ears | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:absent auditory canals (wws)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:absent auditory canals (wws) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:absent external auditory canals
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:absent external auditory canals | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:acoustic trauma
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:acoustic trauma | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:affects all frequencies
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:affects all frequencies | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:approximately 0.7db per year hearing loss at all frequencies
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:approximately 0.7db per year hearing loss at all frequencies | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:asymmetric dysplastic ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:asymmetric dysplastic ears | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:audiogram is gently sloping or flat
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:audiogram is gently sloping or flat | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:aural fullness
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:aural fullness | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:bilateral hypoplastic cochlea
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:chronic otitis other infection ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:chronic otitis other infection ear | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:cleft lobules
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:cleft lobules | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:conductive hearing loss, bilateral
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:conductive hearing loss, bilateral | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:crumpled ear (76%)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:crumpled ear (76%) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:cup-shaped ears (30-60% of patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:cup-shaped ears (30-60% of patients) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:cupped pinna
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:cupped pinna | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:deafness
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:deafness (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness (in some patients) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:deafness, bilateral sensorineural, high frequency (100% of patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, bilateral sensorineural, high frequency (100% of patients) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:deafness, sensorineural, severe to profound affecting all frequencies
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, sensorineural, severe to profound affecting all frequencies | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:deafness, stable bilateral symmetric prelingual
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, stable bilateral symmetric prelingual | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:downward sloping audiogram
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:downward sloping audiogram | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:ear pain/earache
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:ear pain/earache | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:ear tag
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:ear tag | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:external ear defects
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:external ear defects | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:hearing complaints (excluding h84-86)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing complaints (excluding h84-86) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:hearing impairment (in 1/4 patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing impairment (in 1/4 patients) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:hearing loss (affecting all frequencies), moderate to severe
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss (affecting all frequencies), moderate to severe | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:hearing loss has been reported in some adults with severe disease
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss has been reported in some adults with severe disease | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:hearing loss, conductive (in one family)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, conductive (in one family) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:hearing loss, congenital, profound (250-8,000 hz)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, congenital, profound (250-8,000 hz) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:hearing loss, postlingual progressive sensorineural
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, postlingual progressive sensorineural | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:hearing loss, sensorineural, associated with elsts
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural, associated with elsts | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:inferior displacement of the ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:inferior displacement of the ears | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:large ears (2p21del)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:large ears (2p21del) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:large protruding ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:large protruding ears | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:large, low-set ears (uncommon)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:large, low-set ears (uncommon) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:left ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:left ear | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:limited auditory function
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:limited auditory function | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:loss of mid- and low-frequencies later
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:loss of mid- and low-frequencies later | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:malformations of the auditory ossicles
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:malformations of the auditory ossicles | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:misshapen ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:misshapen ear | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:mixed hearing loss
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:mixed hearing loss | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:mondini defect
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:mondini defect | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:normal cochlear microphonics
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:normal cochlear microphonics | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:normal outer hair cell functions
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:normal outer hair cell functions | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:otosclerosis
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:otosclerosis | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:pinna modeling anomalies
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:pinna modeling anomalies | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:presbycusis
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:presbycusis | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:progressive hearing impairment
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:progressive hearing impairment | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:progressive sensorineural hearing impairment
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:progressive sensorineural hearing impairment | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:prominent antitragus
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:prominent antitragus | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:protuberant ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:protuberant ear | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:recurrent otitis media in infancy
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:recurrent otitis media in infancy | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:recurrent otitis media in infancy and childhood
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:recurrent otitis media in infancy and childhood | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:relatively long ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:relatively long ears | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:rudimentary ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:rudimentary ear | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:secretory otitis media
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:secretory otitis media | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:sensorineural hearing loss
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural hearing loss | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:sensorineural hearing loss (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural hearing loss (rare) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:sensorineural hearing loss, bilateral
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural hearing loss, bilateral | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:shallow skin dimple on posterior surface of ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:shallow skin dimple on posterior surface of ear | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:short ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:short ear | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:short ears (in 1 family)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:short ears (in 1 family) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:simple ear structure
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:simple ear structure | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:small, simple ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:small, simple ears | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:squared-off ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:squared-off ears | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:structure of superior auricularis muscle
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:structure of superior auricularis muscle | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:superficial injury of ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:superficial injury of ear | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:synotus
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:synotus | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:tinnitus
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:tinnitus | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:tinnitus (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:tinnitus (in some patients) | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
en:vertiginous syndrome
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:vertiginous syndrome | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 30 / 0.698 ->
traumatisme superficiel oreille
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=traumatisme superficiel oreille | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:abnormal middle ear ossicles
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormal middle ear ossicles | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:abnormality of the middle ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormality of the middle ear | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:absent or decreased auditory brainstem responses
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:absent or decreased auditory brainstem responses | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:anomalous middle ear bones
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:anomalous middle ear bones | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:anterior creases of earlobe
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:anterior creases of earlobe | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:aplasia of the inner ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:aplasia of the inner ear | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:atrophy of cochlear and vestibular fibrocytes
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:atrophy of cochlear and vestibular fibrocytes | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:auricular clefts
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:auricular clefts | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:congenital small ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:congenital small ears | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:deafness, conductive (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, conductive (in some patients) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:deafness, congenital sensorineural, severe to profound
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, congenital sensorineural, severe to profound | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:deafness, sensorineural, prelingual, profound
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, sensorineural, prelingual, profound | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:deafness, unilateral, childhood onset
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, unilateral, childhood onset | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:decreased otoacoustic emission amplitude
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:decreased otoacoustic emission amplitude | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:dorsally rotated ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:dorsally rotated ears | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:ear part
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:ear part | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:earlobe pits
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:earlobe pits | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:external ear defects (47%)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:external ear defects (47%) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:external ears rudimentary
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:external ears rudimentary | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:fear of ear disease
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:fear of ear disease | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:fleshy and overfolded helices
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:fleshy and overfolded helices | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:floppy ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:floppy ears | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:foreign body in auditory canal
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:foreign body in auditory canal | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:hearing loss, congenital sensorineural, moderate-severe
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, congenital sensorineural, moderate-severe | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:hearing loss, high frequency, slowly progressive (onset in early childhood)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, high frequency, slowly progressive (onset in early childhood) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:hearing loss, mild
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, mild | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:hearing loss, mixed, mild to severe (in heterozygotes)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, mixed, mild to severe (in heterozygotes) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:hearing loss, moderate to severe, bilateral, nonprogressive
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, moderate to severe, bilateral, nonprogressive | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:hearing loss, postlingual sensorineural
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, postlingual sensorineural | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:hypercompliant tympanic membranes
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hypercompliant tympanic membranes | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:large anteverted ears (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:large anteverted ears (rare) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:large auricle
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:large auricle | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:large ear pinnae
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:large ear pinnae | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:low-set ears (in 2/4 patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:low-set ears (in 2/4 patients) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:microtia (30-60% of patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:microtia (30-60% of patients) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:middle ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:middle ear | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:nonprogressive
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:nonprogressive | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:normal middle ear pressures on tympanometry
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:normal middle ear pressures on tympanometry | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:other diseases of ear/mastoid
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:other diseases of ear/mastoid | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:outer ear abnormalities (deletion patients) prominent ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:outer ear abnormalities (deletion patients) prominent ears | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:phonophobia
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:phonophobia | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:poorly folded ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:poorly folded ears | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:preauricular pits (70-80% of patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:preauricular pits (70-80% of patients) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:preauricular skin tag
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:preauricular skin tag | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:progressive cartilaginous ossification of pinnae
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:progressive cartilaginous ossification of pinnae | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:progressive hearing loss (in some)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:progressive hearing loss (in some) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:prominent lobules
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:prominent lobules | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:protruding lobules
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:protruding lobules | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:sensorineural deafness (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural deafness (rare) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:sensorineural hearing loss (onset early childhood)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural hearing loss (onset early childhood) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:sensorineural hearing loss, mild (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural hearing loss, mild (rare) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:severe narrowing of cartilagenous auditory canal
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:severe narrowing of cartilagenous auditory canal | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:small external auditory meatus
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:small external auditory meatus | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:small, malformed ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:small, malformed ears | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:stenotic ear canals (30%)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:stenotic ear canals (30%) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:structure of lymphatic vessel of ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:structure of lymphatic vessel of ear | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:superior semicircular canal dehiscence syndrome
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:superior semicircular canal dehiscence syndrome | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:tinnitus (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:tinnitus (rare) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:u-shaped audiogram
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:u-shaped audiogram | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:unilateral external ear deformity
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:unilateral external ear deformity | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:upturned lobes
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:upturned lobes | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 29 / 0.674 ->
en:vestibular hypofunction (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:vestibular hypofunction (rare) | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:abnormal middle ear reflexes
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormal middle ear reflexes | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:abnormality of the pinna
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormality of the pinna | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:abnormally folded helix
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormally folded helix | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:absence of vestibular evoked myogenic potentials (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:absence of vestibular evoked myogenic potentials (rare) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:absent cochlear microphonic (in older patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:absent cochlear microphonic (in older patients) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:absent earlobe
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:absent earlobe | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:bilateral conductive hearing loss (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:bilateral conductive hearing loss (rare) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:blind fistula
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:blind fistula | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:cauliflower ear deformity (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:cauliflower ear deformity (rare) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:cleft at the superior portion of the pinna
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:cleft at the superior portion of the pinna | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:cupped ears (finding)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:cupped ears (finding) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:deafness in 30-50% of patients with skull involvement
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness in 30-50% of patients with skull involvement | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:deafness, moderate-severe (onset in third decade)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, moderate-severe (onset in third decade) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:deafness, sensorineural, especially affecting high frequencies (in about 55% of males and 45% of females)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, sensorineural, especially affecting high frequencies (in about 55% of males and 45% of females) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:deficient auricle
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deficient auricle | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:dilatated internal auditory canal
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:dilatated internal auditory canal | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:first branchial arch anomalies
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:first branchial arch anomalies | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:flattened
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:flattened | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:flattened antihelix
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:flattened antihelix | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:hearing impairment, asymmetric (in some patients with hsan2d)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing impairment, asymmetric (in some patients with hsan2d) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:hearing loss first affects high frequencies
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss first affects high frequencies | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:hearing loss, bilateral sensorineural (profound)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, bilateral sensorineural (profound) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:hearing loss, neural type
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, neural type | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:hearing loss, prelingual sensorineural, moderate to severe
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, prelingual sensorineural, moderate to severe | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:hearing loss, sensorineural and conductive, severe to profound
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural and conductive, severe to profound | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:hearing threshold at or above 90 db at all frequencies tested (0.25-8.0 khz)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing threshold at or above 90 db at all frequencies tested (0.25-8.0 khz) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:high-tone sensorineural deafness (67% of patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:high-tone sensorineural deafness (67% of patients) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:hypoplasia of the upper part of the helix
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hypoplasia of the upper part of the helix | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:hypoplastic semicircular canals
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hypoplastic semicircular canals | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:hypoplastic superior helix
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hypoplastic superior helix | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:incomplete separation of the cochlea from the internal auditory canal
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:incomplete separation of the cochlea from the internal auditory canal | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:large earlobe
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:large earlobe | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:large fleshy ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:large fleshy ears | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:large prominent ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:large prominent ears | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:linear ear lobe creases
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:linear ear lobe creases | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:loss of vestibular reflexes
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:loss of vestibular reflexes | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:low-frequency conductive hearing loss
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:low-frequency conductive hearing loss | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:low-set and rotated ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:low-set and rotated ears | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:low-set ears (45%)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:low-set ears (45%) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:malformed pinnae (30-60% of patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:malformed pinnae (30-60% of patients) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:mild to moderate hearing loss
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:mild to moderate hearing loss | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:mixed hearing loss (50% of patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:mixed hearing loss (50% of patients) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:narrowed external ear canal
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:narrowed external ear canal | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:no hearing impairment
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:no hearing impairment | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:normal static compliance on tympanometry
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:normal static compliance on tympanometry | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:otitis externa
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:otitis externa | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:otitis media, chronic (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:otitis media, chronic (rare) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:overfolded, rumpled ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:overfolded, rumpled ears | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:poorly shaped ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:poorly shaped ears | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:progressive high-frequency hearing loss (onset 20-30 years)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:progressive high-frequency hearing loss (onset 20-30 years) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:progressive, low frequency sensorineural hearing loss
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:progressive, low frequency sensorineural hearing loss | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:prominent antitragus (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:prominent antitragus (in some patients) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:protruding right ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:protruding right ear | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:recurrent ear infections
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:recurrent ear infections | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:retroverted ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:retroverted ears | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:sensorineural deafness, variable (in 1 family)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural deafness, variable (in 1 family) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:sensorineural hearing loss (1 patient)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural hearing loss (1 patient) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:sensorineural hearing loss (in 1 of 3 patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural hearing loss (in 1 of 3 patients) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:sensorineural hearing loss has been reported
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural hearing loss has been reported | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:slit-like opening of the exterior auditory meatus
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:slit-like opening of the exterior auditory meatus | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:small earlobe
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:small earlobe | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:soft auricles
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:soft auricles | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:supraauricular pit
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:supraauricular pit | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:symmetric deterioration of hearing loss and speech reception with age
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:symmetric deterioration of hearing loss and speech reception with age | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:vertigo, episodic
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:vertigo, episodic | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:vestibular abnormalities (variable)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:vestibular abnormalities (variable) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 28 / 0.651 ->
en:vestibular involvement (variable)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:vestibular involvement (variable) | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:abnormal ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormal ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:abnormal helices, antihelices and lobules
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormal helices, antihelices and lobules | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:abnormal semicircular canals
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormal semicircular canals | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:absence of earlobe
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:absence of earlobe | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:accessory tragus
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:accessory tragus | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:angular ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:angular ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:attached ear lobules
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:attached ear lobules | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:auriculo-condylar syndrome
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:auriculo-condylar syndrome | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:conductive hearing loss (in a subset of patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:conductive hearing loss (in a subset of patients) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:deafness (often in third decade)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness (often in third decade) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:deafness, early-onset mixed conductive and sensorineural
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, early-onset mixed conductive and sensorineural | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:deafness, postlingual
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, postlingual | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:deafness, profound, by 6th decade
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, profound, by 6th decade | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:disjunction of otherwise normal lobule from remainder of ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:disjunction of otherwise normal lobule from remainder of ear | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:disproportionately large ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:disproportionately large ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:dysplastic pinnae
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:dysplastic pinnae | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:endolymphatic hydrops, delayed onset
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:endolymphatic hydrops, delayed onset | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:endolymphatic sac tumors (elsts)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:endolymphatic sac tumors (elsts) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:hearing loss (uncommon)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss (uncommon) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:hearing loss, conductive (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, conductive (rare) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:hearing loss, mild (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, mild (rare) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:hearing loss, postlingual
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, postlingual | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:hearing loss, profound congenital sensorineural
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, profound congenital sensorineural | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:hearing loss, sensorineural (in 1 ashkenazi patient)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural (in 1 ashkenazi patient) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:hearing loss, sensorineural (in 2 patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural (in 2 patients) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:hearing loss, sensorineural (in sister)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural (in sister) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:hearing loss, sensorineural (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural (in some patients) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:hearing loss, sensorineural, due to auditory neuropathy
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural, due to auditory neuropathy | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:hearing loss, sensorineural, mild progressive (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural, mild progressive (in some patients) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:hearing loss, sensorineural, moderate, postlingual
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural, moderate, postlingual | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:hyperfolded ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hyperfolded ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:hypoplastic ears fused to the scalp
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hypoplastic ears fused to the scalp | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:hypoplastic helices
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hypoplastic helices | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:incomplete atretic plate
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:incomplete atretic plate | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:large anteverted pinnae (90% males, 40% females)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:large anteverted pinnae (90% males, 40% females) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:large appearing ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:large appearing ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:large pinnae
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:large pinnae | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:large, low-set ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:large, low-set ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:lobular aplasia
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:lobular aplasia | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:lobule may be separately from the rest of the external ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:lobule may be separately from the rest of the external ear | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:low-set ears (28%)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:low-set ears (28%) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:low-set ears (in one family)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:low-set ears (in one family) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:low-set ears (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:low-set ears (in some patients) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:low-set, malformed ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:low-set, malformed ears | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:macrotia
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:macrotia | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:malformed ossicular chain
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:malformed ossicular chain | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:michel aplasia (complete absence of inner ear structures)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:michel aplasia (complete absence of inner ear structures) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:mild hearing impairment (13%)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:mild hearing impairment (13%) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:minor auricular anomalies
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:minor auricular anomalies | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:minor ear anomalies (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:minor ear anomalies (in some patients) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:no auditory brainstem response to 100-db stimulus
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:no auditory brainstem response to 100-db stimulus | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:no vestibular dysfunction
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:no vestibular dysfunction | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:normal vestibular response
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:normal vestibular response | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:posterior helical indentations
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:posterior helical indentations | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:posteriorly rotated ears (2p21del)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:posteriorly rotated ears (2p21del) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:preauricular dimple
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:preauricular dimple | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:preauricular skin furrow
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:preauricular skin furrow | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:recurrent otitis media
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:recurrent otitis media | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:sclerosis of semicircular canals
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sclerosis of semicircular canals | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:sensory hearing loss
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensory hearing loss | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:small ears (female)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:small ears (female) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:small external auditory canals
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:small external auditory canals | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:small/rudimentary tragus, antitragus and lobule
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:small/rudimentary tragus, antitragus and lobule | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:tinnitus (variable)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:tinnitus (variable) | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
en:underfolded helix
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:underfolded helix | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
lésion traumatique superficielle de l'oreille
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=lésion traumatique superficielle de l'oreille | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 27 / 0.628 ->
surdité congénitale
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=surdité congénitale | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:abnormal auricles
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormal auricles | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:abnormality of the helix
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:abnormality of the helix | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:absence of the cochlear nerves (reported in 1 patient)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:absence of the cochlear nerves (reported in 1 patient) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:absent brainstem auditory-evoked responses
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:absent brainstem auditory-evoked responses | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:absent distortion product otoacoustic emissions (oaes)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:absent distortion product otoacoustic emissions (oaes) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:absent external auditory meatus
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:absent external auditory meatus | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:absent stapedial reflex
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:absent stapedial reflex | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:absent stapedial reflexes or intraoperative stapes immobility
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:absent stapedial reflexes or intraoperative stapes immobility | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:anteverted ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:anteverted ears | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:atresia of the external auditory canal
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:atresia of the external auditory canal | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:congenital atresia of external auditory canal
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:congenital atresia of external auditory canal | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:congenital ear anomaly nos (disorder)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:congenital ear anomaly nos (disorder) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:congenital hearing loss (1 family)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:congenital hearing loss (1 family) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:congenital sensorineural hearing loss
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:congenital sensorineural hearing loss | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:deafness, congenital nonprogressive sensorineural symmetric, moderate
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, congenital nonprogressive sensorineural symmetric, moderate | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:deafness, nonprogressive, moderate
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, nonprogressive, moderate | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:deafness, sensorineural (45%)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, sensorineural (45%) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:deafness, sensorineural, mild (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:deafness, sensorineural, mild (rare) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:ear constriction (97%)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:ear constriction (97%) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:ears deficient in cartilage
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:ears deficient in cartilage | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:expansion of helical fold at superior point of true longitudinal axis of ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:expansion of helical fold at superior point of true longitudinal axis of ear | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:flat audiogram
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:flat audiogram | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:flat ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:flat ears | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:hearing impairment (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing impairment (in some patients) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:hearing impairment, sensorineural, fluctuating
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing impairment, sensorineural, fluctuating | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:hearing impairment, sensorineural, mild
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing impairment, sensorineural, mild | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:hearing loss (2 patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss (2 patients) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:hearing loss (cvs+)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss (cvs+) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:hearing loss (reported in 2 patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss (reported in 2 patients) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:hearing loss, bilateral progressive post-lingual
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, bilateral progressive post-lingual | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:hearing loss, profound prelingual sensorineural
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, profound prelingual sensorineural | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:hearing loss, sensorineural (in some)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural (in some) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:hearing loss, sensorineural, severe to profound
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural, severe to profound | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:hypoacusia (1 patient)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hypoacusia (1 patient) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:hypoplasia of the cochlea
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hypoplasia of the cochlea | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:hypoplastic, overfolded helices
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hypoplastic, overfolded helices | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:large anteverted ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:large anteverted ears | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:large ears (37%)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:large ears (37%) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:large, prominent ears (59%)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:large, prominent ears (59%) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:long and prominent ear crus
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:long and prominent ear crus | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:low-set, posteriorly rotated ears
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:low-set, posteriorly rotated ears | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:microtia (wws)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:microtia (wws) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:microtia hearing loss, conductive
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:microtia hearing loss, conductive | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:misshapen, small ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:misshapen, small ear | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:neural hearing loss
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:neural hearing loss | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:no reproducible waves i, iii, or v at high intensities
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:no reproducible waves i, iii, or v at high intensities | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:otitis externa, recurrent, due to infection with staphylococcus aureus
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:otitis externa, recurrent, due to infection with staphylococcus aureus | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:otitis media, recurrent (rare)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:otitis media, recurrent (rare) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:partial aplasia of external auditory canal ending in blind fistula (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:partial aplasia of external auditory canal ending in blind fistula (in some patients) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:preauricular sinus, bilateral
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:preauricular sinus, bilateral | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:prelingual onset
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:prelingual onset | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:prominent earlobes (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:prominent earlobes (in some patients) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:rudimentary
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:rudimentary | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:rudimentary tympanic membrane (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:rudimentary tympanic membrane (in some patients) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:satyr ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:satyr ear | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:sensorineural hearing impairment (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:sensorineural hearing impairment (in some patients) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:severe loss in the higher frequencies by the fifth decade
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:severe loss in the higher frequencies by the fifth decade | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:simple ear
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:simple ear | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:small cavum conchae
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:small cavum conchae | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:small triangular pinnae
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:small triangular pinnae | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:structural inner ear abnormalities (in patients with larger deletions)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:structural inner ear abnormalities (in patients with larger deletions) | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:vestibular dysfunction
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:vestibular dysfunction | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
en:wide bulbous internal auditory meatus
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:wide bulbous internal auditory meatus | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 26 / 0.605 ->
surdité du labyrinthe
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=surdité du labyrinthe | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 25 / 0.581 ->
en:hearing
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 25 / 0.581 ->
perte d'audition sensorineurale
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=perte d'audition sensorineurale | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 23 / 0.535 ->
otite moyenne séreuse
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=otite moyenne séreuse | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 23 / 0.535 ->
surdité héréditaire
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=surdité héréditaire | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
déficience auditive
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=déficience auditive | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:auditory canal stenosis
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:auditory canal stenosis | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:balance problem
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:balance problem | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:chronic otitis media (25%)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:chronic otitis media (25%) | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:cutlet
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:cutlet | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:disorder of equilibrium
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:disorder of equilibrium | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:dysplastic ears (jbts)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:dysplastic ears (jbts) | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:ENT doctor
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:ENT doctor | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:ENT specialist
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:ENT specialist | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:hearing impairment (1 patient)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing impairment (1 patient) | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:hearing impairment, progressive (family a)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing impairment, progressive (family a) | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:hearing loss (in 2 members of 1 family)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss (in 2 members of 1 family) | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:hearing loss, sensorineural, progressive (all frequencies)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hearing loss, sensorineural, progressive (all frequencies) | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:hereditary deafness
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:hereditary deafness | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:microtia (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:microtia (in some patients) | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:mild dysplasia of concha, unilateral
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:mild dysplasia of concha, unilateral | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:no vestibular symptoms
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:no vestibular symptoms | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:nose and throat specialist
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:nose and throat specialist | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:otitis with effusion
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:otitis with effusion | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:otolaryngologist
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:otolaryngologist | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:otorhinolaryngologist
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:otorhinolaryngologist | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:problem with balance
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:problem with balance | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:rotary vertigo
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:rotary vertigo | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:serous otitis
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:serous otitis | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
en:tinnitus, bilateral (in some patients)
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:tinnitus, bilateral (in some patients) | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
esgourde
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=esgourde | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
état nébuleux
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=état nébuleux | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
état vertigineux
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=état vertigineux | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
étourdissement
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=étourdissement | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
hyperacousie
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=hyperacousie | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
hyperacousies
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=hyperacousies | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
hyperacusie
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=hyperacusie | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
hyperlaxe
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=hyperlaxe | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
hypermobile
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=hypermobile | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
médecin ORL
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=médecin ORL | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
otite séreuse
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=otite séreuse | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
otite séromuqueuse
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=otite séromuqueuse | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
oto-rhino
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=oto-rhino | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
oto-rhino-laryngologiste
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=oto-rhino-laryngologiste | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
otorhinolaryngologiste
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=otorhinolaryngologiste | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
pavillon de l'oreille de morphologie rudimentaire
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=pavillon de l'oreille de morphologie rudimentaire | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
sensation de rotation
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=sensation de rotation | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
sensation de tournoiement
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=sensation de tournoiement | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
sensation rotatoire
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=sensation rotatoire | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
sensation vertigineuse
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=sensation vertigineuse | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
sténose du canal auriculaire
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=sténose du canal auriculaire | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
surdité neurosensorielle bilatérale
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=surdité neurosensorielle bilatérale | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
tête pivotante
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=tête pivotante | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
trouble de l'équilibre
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=trouble de l'équilibre | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
vertige
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=vertige | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
vertige rotatoire
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=vertige rotatoire | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
vertige subjectif
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=vertige subjectif | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
vertigo
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=vertigo | rel=r_associated | relid=0 | w=20
- en:hearing loss, sensorineural, bilateral, moderate-to-severe --
r_associated #0: 20 / 0.465 ->
vertigo rotatoire
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=vertigo rotatoire | rel=r_associated | relid=0 | w=20
| ≈ 782 relations entrantes
- en:congenital deafness ---
r_associated #0: 300 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:congenital deafness | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=300
- surdité congénitale ---
r_associated #0: 297 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=surdité congénitale | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=297
- surdité héréditaire ---
r_associated #0: 295 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=surdité héréditaire | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=295
- surdité du labyrinthe ---
r_associated #0: 271 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=surdité du labyrinthe | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=271
- en:deafness labyrinthine ---
r_associated #0: 270 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness labyrinthine | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=270
- sensation vertigineuse ---
r_associated #0: 230 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=sensation vertigineuse | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=230
- vertige subjectif ---
r_associated #0: 230 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=vertige subjectif | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=230
- vertigo rotatoire ---
r_associated #0: 230 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=vertigo rotatoire | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=230
- otite moyenne séreuse ---
r_associated #0: 229 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=otite moyenne séreuse | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=229
- sensation de tournoiement ---
r_associated #0: 229 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=sensation de tournoiement | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=229
- en:serous otitis media ---
r_associated #0: 225 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:serous otitis media | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=225
- sensation de rotation ---
r_associated #0: 224 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=sensation de rotation | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=224
- vertige rotatoire ---
r_associated #0: 220 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=vertige rotatoire | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=220
- tête pivotante ---
r_associated #0: 215 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=tête pivotante | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=215
- sensation rotatoire ---
r_associated #0: 205 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=sensation rotatoire | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=205
- état nébuleux ---
r_associated #0: 205 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=état nébuleux | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=205
- état vertigineux ---
r_associated #0: 205 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=état vertigineux | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=205
- traumatisme superficiel oreille ---
r_associated #0: 190 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=traumatisme superficiel oreille | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=190
- en:superficial injury of ear ---
r_associated #0: 186 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:superficial injury of ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=186
- en:sensorineural hearing loss ---
r_associated #0: 181 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural hearing loss | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=181
- perte d'audition sensorineurale ---
r_associated #0: 179 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=perte d'audition sensorineurale | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=179
- en:sensorineural hearing loss, bilateral ---
r_associated #0: 168 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural hearing loss, bilateral | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=168
- en:vertigo ---
r_associated #0: 168 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:vertigo | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=168
- en:dizziness ---
r_associated #0: 165 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:dizziness | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=165
- surdité neurosensorielle bilatérale ---
r_associated #0: 165 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=surdité neurosensorielle bilatérale | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=165
- hyperacousie ---
r_associated #0: 140 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=hyperacousie | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=140
- hyperacusie ---
r_associated #0: 140 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=hyperacusie | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=140
- en:hyperacusis ---
r_associated #0: 139 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hyperacusis | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=139
- vertigo ---
r_associated #0: 131 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=vertigo | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=131
- hyperacousies ---
r_associated #0: 130 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=hyperacousies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=130
- en:balance problem ---
r_associated #0: 115 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:balance problem | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=115
- en:disorder of equilibrium ---
r_associated #0: 115 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:disorder of equilibrium | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=115
- en:problem with balance ---
r_associated #0: 115 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:problem with balance | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=115
- trouble de l'équilibre ---
r_associated #0: 115 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=trouble de l'équilibre | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=115
- vertige ---
r_associated #0: 95 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=vertige | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=95
- étourdissement ---
r_associated #0: 71 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=étourdissement | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=71
- hypermobile ---
r_associated #0: 67 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=hypermobile | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=67
- en:secretory otitis media ---
r_associated #0: 66 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:secretory otitis media | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=66
- otite séromuqueuse ---
r_associated #0: 61 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=otite séromuqueuse | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=61
- en:hypermobile ---
r_associated #0: 58 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hypermobile | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=58
- lésion traumatique superficielle de l'oreille ---
r_associated #0: 58 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=lésion traumatique superficielle de l'oreille | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=58
- en:hereditary deafness ---
r_associated #0: 46 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hereditary deafness | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=46
- oto-rhino-laryngologiste ---
r_associated #0: 45 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=oto-rhino-laryngologiste | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=45
- déficience auditive ---
r_associated #0: 44 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=déficience auditive | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=44
- otorhinolaryngologiste ---
r_associated #0: 44 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=otorhinolaryngologiste | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=44
- en:hearing impairment, sensorineural, fluctuating ---
r_associated #0: 43 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing impairment, sensorineural, fluctuating | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=43
- en:low set ears ---
r_associated #0: 43 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:low set ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=43
- en:low-set ears (rare) ---
r_associated #0: 43 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:low-set ears (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=43
- en:small auricles ---
r_associated #0: 43 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:small auricles | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=43
- pavillon de l'oreille de morphologie rudimentaire ---
r_associated #0: 43 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=pavillon de l'oreille de morphologie rudimentaire | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=43
- en:deafness, secondary to cranial hyperostosis ---
r_associated #0: 42 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, secondary to cranial hyperostosis | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=42
- en:hearing impairment ---
r_associated #0: 42 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing impairment | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=42
- en:high-frequency tinnitus at onset ---
r_associated #0: 42 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:high-frequency tinnitus at onset | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=42
- en:sensorineural hearing loss (onset early childhood) ---
r_associated #0: 42 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural hearing loss (onset early childhood) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=42
- en:small, simple ears ---
r_associated #0: 42 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:small, simple ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=42
- en:stapes fixation ---
r_associated #0: 42 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:stapes fixation | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=42
- en:auditory impairment ---
r_associated #0: 41 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:auditory impairment | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=41
- en:normal otoacoustic emissions ---
r_associated #0: 41 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:normal otoacoustic emissions | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=41
- en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation ---
r_associated #0: 40 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=40
- en:disjunction of otherwise normal lobule from remainder of ear ---
r_associated #0: 40 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:disjunction of otherwise normal lobule from remainder of ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=40
- en:hearing loss, bilateral sensorineural (profound) ---
r_associated #0: 40 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, bilateral sensorineural (profound) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=40
- en:pigmentation of the ear cartilage ---
r_associated #0: 40 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:pigmentation of the ear cartilage | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=40
- oto-rhino ---
r_associated #0: 40 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=oto-rhino | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=40
- en:a subset of patients have hearing loss ---
r_associated #0: 39 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:a subset of patients have hearing loss | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=39
- en:cochlear malformation defect (mondini dysplasia) (less common) ---
r_associated #0: 39 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:cochlear malformation defect (mondini dysplasia) (less common) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=39
- en:flat audiogram ---
r_associated #0: 39 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:flat audiogram | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=39
- en:incomplete separation of the cochlea from the internal auditory canal ---
r_associated #0: 39 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:incomplete separation of the cochlea from the internal auditory canal | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=39
- en:sensorineural hearing loss (less common) ---
r_associated #0: 39 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural hearing loss (less common) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=39
- en:simple ear ---
r_associated #0: 39 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:simple ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=39
- en:structure of lymphatic vessel of ear ---
r_associated #0: 39 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:structure of lymphatic vessel of ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=39
- en:ENT doctor ---
r_associated #0: 38 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:ENT doctor | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=38
- en:absence of the helix and distal scapha in middle third of the ear ---
r_associated #0: 38 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:absence of the helix and distal scapha in middle third of the ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=38
- en:air-bone gap of greater than 20 db across 0.5 to 2 khz ---
r_associated #0: 38 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:air-bone gap of greater than 20 db across 0.5 to 2 khz | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=38
- en:dysplastic helices ---
r_associated #0: 38 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:dysplastic helices | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=38
- en:normal outer hair cell functions ---
r_associated #0: 38 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:normal outer hair cell functions | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=38
- en:prominent antihelix ---
r_associated #0: 38 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:prominent antihelix | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=38
- en:sensorineural hearing loss, mild (rare) ---
r_associated #0: 38 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural hearing loss, mild (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=38
- en:otitis media, chronic (rare) ---
r_associated #0: 37 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:otitis media, chronic (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=37
- en:rotary vertigo ---
r_associated #0: 37 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:rotary vertigo | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=37
- surdimutité ---
r_associated #0: 37 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=surdimutité | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=37
- en:hearing loss, mixed (in some patients) ---
r_associated #0: 36 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, mixed (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=36
- en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients) ---
r_associated #0: 36 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=36
- en:partial hearing loss ---
r_associated #0: 36 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:partial hearing loss | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=36
- en:ENT specialist ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:ENT specialist | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:aplasia of the inner ear ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:aplasia of the inner ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:aural fullness ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:aural fullness | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:conductive hearing loss (30% of patients) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:conductive hearing loss (30% of patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:conductive hearing loss (in a subset of patients) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:conductive hearing loss (in a subset of patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:cupped ears (in some patients) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:cupped ears (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:deafness (variable) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness (variable) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:deafness affects all frequencies ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness affects all frequencies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:deafness, sensorineural, mild (rare) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, sensorineural, mild (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:deafness, sensorineural, profound ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, sensorineural, profound | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:dilatated internal auditory canal ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:dilatated internal auditory canal | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:disproportionately large ears ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:disproportionately large ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:dysmorphic ears ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:dysmorphic ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:ear pits, posterior helical ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:ear pits, posterior helical | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:ears deficient in cartilage ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:ears deficient in cartilage | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:entire ear ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:entire ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:external ear defects ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:external ear defects | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:flat ears ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:flat ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:hearing impairment (1 patient) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing impairment (1 patient) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:hearing loss (cvs+) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss (cvs+) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:hearing loss, conductive or mixed ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, conductive or mixed | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:hearing loss, congenital sensorineural, severe to profound ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, congenital sensorineural, severe to profound | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:hearing loss, high-frequency (onset in childhood-adolescence) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, high-frequency (onset in childhood-adolescence) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:hearing loss, progressive (in some patients) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, progressive (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural (in patients with larger deletions) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural (in patients with larger deletions) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:large prominent ears ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:large prominent ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:large simple ears ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:large simple ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:loss of mid- and low-frequencies later ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:loss of mid- and low-frequencies later | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:low-set ears (28%) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:low-set ears (28%) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:low-set ears (45%) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:low-set ears (45%) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:low-set ears (in one family) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:low-set ears (in one family) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:malformed earlobes ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:malformed earlobes | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:mixed hearing loss (50% of patients) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:mixed hearing loss (50% of patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:morphological abnormality of the middle ear ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:morphological abnormality of the middle ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:nose and throat specialist ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:nose and throat specialist | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:organ of corti degeneration ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:organ of corti degeneration | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:poorly folded ears ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:poorly folded ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:preauricular sinus, bilateral ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:preauricular sinus, bilateral | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:profound deafness ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:profound deafness | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:protruding ears (in some patients) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:protruding ears (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:sensorineural hearing loss (3 patients) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural hearing loss (3 patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:severe narrowing of cartilagenous auditory canal ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:severe narrowing of cartilagenous auditory canal | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:small triangular pinnae ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:small triangular pinnae | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:soft auricles ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:soft auricles | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:squared-off ears ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:squared-off ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:stenosis of external auditory canal ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:stenosis of external auditory canal | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:strabismus (in some patients) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:strabismus (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:thickened helices ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:thickened helices | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:thickened lobes ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:thickened lobes | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:unconnected or fused stapes and incus ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:unconnected or fused stapes and incus | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:unfolded superior helices ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:unfolded superior helices | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:uplifted earlobes ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:uplifted earlobes | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:vestibular function defect (decreased in some, normal in other patients) ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:vestibular function defect (decreased in some, normal in other patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- sténose du canal auriculaire ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=sténose du canal auriculaire | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- surdi-mutité ---
r_associated #0: 35 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=surdi-mutité | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=35
- en:abnormal middle ear ossicles ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormal middle ear ossicles | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:absent distortion product otoacoustic emissions (oaes) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:absent distortion product otoacoustic emissions (oaes) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:absent vestibular function (caloric test) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:absent vestibular function (caloric test) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:attached ear lobules ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:attached ear lobules | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:cauliflower ear deformity (rare) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:cauliflower ear deformity (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:chronic otitis media ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:chronic otitis media | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:deafness, bilateral sensorineural, high frequency (100% of patients) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, bilateral sensorineural, high frequency (100% of patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:deafness, congenital sensorineural, profound (in some patients) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, congenital sensorineural, profound (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:deafness, early-onset ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, early-onset | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:deafness, sensorineural (severe to profound) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, sensorineural (severe to profound) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:deficient auricle ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deficient auricle | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:ear ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:ear constriction (97%) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:ear constriction (97%) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:external auditory canal narrow ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:external auditory canal narrow | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:floppy ears ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:floppy ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:hearing impairment, progressive (family a) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing impairment, progressive (family a) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:hearing loss (2 patients) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss (2 patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:hearing loss (uncommon) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss (uncommon) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:hearing loss, bilateral progressive post-lingual ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, bilateral progressive post-lingual | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:hearing loss, conductive (in some patients) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, conductive (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:hearing loss, high frequency, slowly progressive (onset in early childhood) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, high frequency, slowly progressive (onset in early childhood) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:hearing loss, postlingual ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, postlingual | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:hearing loss, postlingual sensorineural ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, postlingual sensorineural | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:hearing loss, progressive, starting in infancy ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, progressive, starting in infancy | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural (in 2 patients) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural (in 2 patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, mild progressive (in some patients) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural, mild progressive (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:hearing loss, sensorineural, progressive (all frequencies) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural, progressive (all frequencies) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:hearing loss, severe to profound, affecting all frequencies ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, severe to profound, affecting all frequencies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:hypertrophic auricular cartilage ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hypertrophic auricular cartilage | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:hypoplastic ear lobes ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hypoplastic ear lobes | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:hypoplastic semicircular canals ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hypoplastic semicircular canals | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:hypoplastic, overfolded helices ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hypoplastic, overfolded helices | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:large anteverted pinnae (90% males, 40% females) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:large anteverted pinnae (90% males, 40% females) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:large, low-set ears ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:large, low-set ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:large, prominent ears (59%) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:large, prominent ears (59%) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:low-frequency sensorineural hearing impairment ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:low-frequency sensorineural hearing impairment | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:malformations of the auditory ossicles ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:malformations of the auditory ossicles | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:michel aplasia (complete absence of inner ear structures) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:michel aplasia (complete absence of inner ear structures) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:minor ear anomalies (in some patients) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:minor ear anomalies (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:neonatal cystic lesions of the pinnae ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:neonatal cystic lesions of the pinnae | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:normal cochlear microphonics ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:normal cochlear microphonics | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:oae responses may decrease with age or use of hearing aids ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:oae responses may decrease with age or use of hearing aids | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:poorly formed ears ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:poorly formed ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:posterior helical indentations ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:posterior helical indentations | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:prolonged brainstem auditory evoked potentials (baep) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:prolonged brainstem auditory evoked potentials (baep) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:prominent antitragus (in some patients) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:prominent antitragus (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:prominent ears (rare) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:prominent ears (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:pulsatile tinnitus (tympanic paraganglioma) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:pulsatile tinnitus (tympanic paraganglioma) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:recurrent otitis ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:recurrent otitis | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:sensorineural hearing impairment (in some patients) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural hearing impairment (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:sensorineural hearing loss (early-onset form) ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural hearing loss (early-onset form) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:sensorineural, conductive, or mixed hearing loss ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural, conductive, or mixed hearing loss | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:severe to profound deafness ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:severe to profound deafness | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:simplified helices ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:simplified helices | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:small ears with large lobules ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:small ears with large lobules | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:stiff, prominent pinnae ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:stiff, prominent pinnae | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:supraauricular pit ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:supraauricular pit | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:underfolded helix ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:underfolded helix | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:upsloping audiograms ---
r_associated #0: 34 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:upsloping audiograms | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:abnormal auditory brainstem responses ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormal auditory brainstem responses | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:abnormally folded ears ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormally folded ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:absence of the cochlear nerves (reported in 1 patient) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:absence of the cochlear nerves (reported in 1 patient) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:atretic ear canals ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:atretic ear canals | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:auditory canal stenosis ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:auditory canal stenosis | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:deafness, early-onset mixed conductive and sensorineural ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, early-onset mixed conductive and sensorineural | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:deafness, profound, affects all frequencies ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, profound, affects all frequencies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:deafness, sensorineural, especially affecting high frequencies ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, sensorineural, especially affecting high frequencies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:dorsally rotated ears ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:dorsally rotated ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:downward sloping or flat audiogram ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:downward sloping or flat audiogram | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:first branchial arch anomalies ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:first branchial arch anomalies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:folded superior edge of helix ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:folded superior edge of helix | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:hearing impairment, sensorineural, mild ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing impairment, sensorineural, mild | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:hearing loss (affecting all frequencies), moderate to severe ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss (affecting all frequencies), moderate to severe | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:hearing loss has been reported in some adults with severe disease ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss has been reported in some adults with severe disease | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:hearing loss, congenital sensorineural, moderate-severe ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, congenital sensorineural, moderate-severe | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:hearing loss, profound prelingual sensorineural ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, profound prelingual sensorineural | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, prelingual ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural, prelingual | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:keratotic plaque around ear meatus ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:keratotic plaque around ear meatus | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:large dysplastic ears ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:large dysplastic ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:large ears (2p21del) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:large ears (2p21del) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:loss of vestibular caloric response ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:loss of vestibular caloric response | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:low-set, malformed ears ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:low-set, malformed ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:misshapen ear ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:misshapen ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:narrow ear lobes ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:narrow ear lobes | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:narrowed external ear canal (30% of patients) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:narrowed external ear canal (30% of patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:neural hearing loss ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:neural hearing loss | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:no vestibular symptoms ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:no vestibular symptoms | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:pointed upper helix ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:pointed upper helix | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:posteriorly rotated ears (in some patients) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:posteriorly rotated ears (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:preauricular skin furrow ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:preauricular skin furrow | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:progressive conductive hearing impairment ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:progressive conductive hearing impairment | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:prominent ears (in some patients) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:prominent ears (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:prominent helices ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:prominent helices | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:sensorineural hearing loss, mild to moderate ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural hearing loss, mild to moderate | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:short ear ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:short ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:simple auricles ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:simple auricles | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:small ears (female) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:small ears (female) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:superior semicircular canal dehiscence syndrome ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:superior semicircular canal dehiscence syndrome | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:vertigo, episodic ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:vertigo, episodic | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:vestibular hypofunction (rare) ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:vestibular hypofunction (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- otite séreuse ---
r_associated #0: 32 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=otite séreuse | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=32
- en:abnormal auricles ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormal auricles | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:abnormal ear configuration ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormal ear configuration | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:abnormally formed ears ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormally formed ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:absent helices, bilaterally ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:absent helices, bilaterally | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:approximately 0.7db per year hearing loss at all frequencies ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:approximately 0.7db per year hearing loss at all frequencies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:atretic auditory canal ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:atretic auditory canal | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:bilateral conductive hearing loss (rare) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:bilateral conductive hearing loss (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:chronic otitis media (25%) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:chronic otitis media (25%) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:cleft lobules ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:cleft lobules | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:cochlear degeneration ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:cochlear degeneration | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:conductive hearing loss ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:conductive hearing loss | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:cystic dilatation of cochlea and vestibulum ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:cystic dilatation of cochlea and vestibulum | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:deafness (in 1 of 2 families) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness (in 1 of 2 families) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:deafness (in some patients) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:deafness due to bilateral cochlear malformation (rare) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:deafness in 30-50% of patients with skull involvement ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness in 30-50% of patients with skull involvement | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:deafness, moderate-severe (onset in third decade) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, moderate-severe (onset in third decade) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:ear pain/earache ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:ear pain/earache | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:hearing deficits (28% of adults) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing deficits (28% of adults) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:hearing impairment (in 1/4 patients) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing impairment (in 1/4 patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:hearing loss first affects high frequencies ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss first affects high frequencies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:hearing loss, congenital profound ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, congenital profound | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural (bilateral, prelingual) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural (bilateral, prelingual) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, due to auditory neuropathy ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural, due to auditory neuropathy | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:hyperfolded ears ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hyperfolded ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:hypoplastic helices ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hypoplastic helices | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:lobular aplasia ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:lobular aplasia | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:loss of hearing (45%) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:loss of hearing (45%) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:narrow auditory canals (rare) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:narrow auditory canals (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:near-stenosis of bony portion of auditory canal (in homozygotes) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:near-stenosis of bony portion of auditory canal (in homozygotes) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:nonprogressive deafness ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:nonprogressive deafness | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:normal vestibular function ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:normal vestibular function | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:otitis externa, recurrent, due to infection with staphylococcus aureus ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:otitis externa, recurrent, due to infection with staphylococcus aureus | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:recurrent ear infections ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:recurrent ear infections | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:relatively long ears ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:relatively long ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:sensorineural deafness (reported in 1 family) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural deafness (reported in 1 family) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:sensorineural hearing loss (1 family) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural hearing loss (1 family) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:sensory hearing loss ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensory hearing loss | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:structural inner ear abnormalities (in patients with larger deletions) ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:structural inner ear abnormalities (in patients with larger deletions) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:structure of superior auricularis muscle ---
r_associated #0: 31 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:structure of superior auricularis muscle | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=31
- en:abnormal speech discrimination ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormal speech discrimination | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:abnormality of the middle ear ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormality of the middle ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:abnormally shaped ears (in one family) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormally shaped ears (in one family) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:absence of acoustic reflex ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:absence of acoustic reflex | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:absent auditory canals (wws) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:absent auditory canals (wws) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:absent earlobe ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:absent earlobe | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:absent external auditory meatus ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:absent external auditory meatus | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:absent lobules ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:absent lobules | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:absent stapedial reflex ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:absent stapedial reflex | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:accessory tragus ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:accessory tragus | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:anteriorly displaced ears ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:anteriorly displaced ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:anteverted pinnae ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:anteverted pinnae | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:apical cartilage deformity ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:apical cartilage deformity | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:attached ear lobes ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:attached ear lobes | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:auricular clefts ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:auricular clefts | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:bilateral sensorineural hearing loss (in some patients) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:bilateral sensorineural hearing loss (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:cochlear malformation ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:cochlear malformation | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:conductive hearing loss to due otitis media ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:conductive hearing loss to due otitis media | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:congenital absence of external ear ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:congenital absence of external ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:congenital atresia of external auditory canal ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:congenital atresia of external auditory canal | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:cup-shaped ears (30-60% of patients) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:cup-shaped ears (30-60% of patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:cupped pinna ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:cupped pinna | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:deafness ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:deafness, profound congenital sensorineural ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, profound congenital sensorineural | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:deafness, sensorineural (45%) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, sensorineural (45%) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:deafness, sensorineural, profound (prelingual onset) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, sensorineural, profound (prelingual onset) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:deafness, stable bilateral symmetric prelingual ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, stable bilateral symmetric prelingual | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:deep-set ears ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deep-set ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:dysplastic ears (jbts) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:dysplastic ears (jbts) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:external ears rudimentary ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:external ears rudimentary | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:hearing complaints (excluding h84-86) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing complaints (excluding h84-86) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:hearing impairment (in some patients) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing impairment (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:hearing loss (variable) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss (variable) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:hearing loss, conductive (in one family) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, conductive (in one family) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:hearing loss, initially conductive, later mixed conductive-sensorineural ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, initially conductive, later mixed conductive-sensorineural | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:hearing loss, mild (rare) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, mild (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural (high frequency) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural (high frequency) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural (in some) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural (in some) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:hypoplastic ears fused to the scalp ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hypoplastic ears fused to the scalp | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:inner ear ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:inner ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:large ear pinnae ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:large ear pinnae | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:large fleshy ears ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:large fleshy ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:large, floppy ears ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:large, floppy ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:linear ear lobe creases ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:linear ear lobe creases | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:lobule may be separately from the rest of the external ear ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:lobule may be separately from the rest of the external ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:long ear ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:long ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:low-set ears (severe form) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:low-set ears (severe form) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:malformed auricle (1 patient) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:malformed auricle (1 patient) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:meniere disease ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:meniere disease | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:microtia (in some patients) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:microtia (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:mild dysplasia of concha, unilateral ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:mild dysplasia of concha, unilateral | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:mild hearing impairment (13%) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:mild hearing impairment (13%) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:mild to moderate hearing loss ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:mild to moderate hearing loss | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:nonsyndromic sensorineural hearing loss ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:nonsyndromic sensorineural hearing loss | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:normal static compliance on tympanometry ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:normal static compliance on tympanometry | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:normal vestibular response ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:normal vestibular response | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:other symptom/complaint of ear ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:other symptom/complaint of ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:otitis with effusion ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:otitis with effusion | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:outer ear abnormalities (deletion patients) prominent ears ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:outer ear abnormalities (deletion patients) prominent ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:presbycusis ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:presbycusis | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:progressive cartilaginous ossification of pinnae ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:progressive cartilaginous ossification of pinnae | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:prominent antitragus ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:prominent antitragus | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:recurrent otitis media in infancy and childhood ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:recurrent otitis media in infancy and childhood | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:recurrent serous otitis ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:recurrent serous otitis | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:retroverted ears ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:retroverted ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:sclerosis of semicircular canals ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sclerosis of semicircular canals | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:shallow skin dimple on posterior surface of ear ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:shallow skin dimple on posterior surface of ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:small cavum conchae ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:small cavum conchae | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:small lobes ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:small lobes | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:transient evoked otoacoustic emissions cannot be detected ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:transient evoked otoacoustic emissions cannot be detected | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:u- or bowl-shaped audiogram ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:u- or bowl-shaped audiogram | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:unravelling of superior helices ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:unravelling of superior helices | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:vestibular dysfunction (in some patients) ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:vestibular dysfunction (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:vestibulopathy, bilateral, progressive ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:vestibulopathy, bilateral, progressive | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- médecin ORL ---
r_associated #0: 30 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=médecin ORL | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=30
- en:abnormal ears ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormal ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:abnormal folded pinna ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormal folded pinna | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:abnormality of the middle ear ossicles ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormality of the middle ear ossicles | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:abnormality of the pinna ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormality of the pinna | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:absent brainstem auditory responses ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:absent brainstem auditory responses | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:absent ipsilateral middle ear muscle reflexes (in older patients) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:absent ipsilateral middle ear muscle reflexes (in older patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:atresia of the external auditory canal ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:atresia of the external auditory canal | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:audiogram may be ascending ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:audiogram may be ascending | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:bilateral congenital profound sensorineural hearing loss ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:bilateral congenital profound sensorineural hearing loss | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:chronic otitis ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:chronic otitis | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:congenital ear anomaly nos (disorder) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:congenital ear anomaly nos (disorder) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:congenital hearing loss (1 family) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:congenital hearing loss (1 family) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:cutlet ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:cutlet | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:deafness, conductive (in some patients) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, conductive (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:deafness, nonprogressive, moderate ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, nonprogressive, moderate | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:deafness, sensorineural (reported in 1 family) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, sensorineural (reported in 1 family) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:dysplastic ears (in some patients) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:dysplastic ears (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:ear part ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:ear part | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:enlarged vestibular aqueduct ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:enlarged vestibular aqueduct | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:external ear defects (47%) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:external ear defects (47%) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:flattened ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:flattened | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:hearing disorder (1 patient) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing disorder (1 patient) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:hearing impairment, mild (2 patients) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing impairment, mild (2 patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:hearing loss, late-onset sensorineural, mild-to moderate (less common) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, late-onset sensorineural, mild-to moderate (less common) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:hearing loss, mild ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, mild | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:hearing loss, neural type ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, neural type | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural (variable) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural (variable) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, associated with elsts ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural, associated with elsts | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, moderate, postlingual ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural, moderate, postlingual | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:hearing normal ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing normal | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:hypoplasia of the cochlea ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hypoplasia of the cochlea | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:impaired tympanic membrane mobility ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:impaired tympanic membrane mobility | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:incomplete atretic plate ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:incomplete atretic plate | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:large anteverted ears ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:large anteverted ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:large ears (in some patients) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:large ears (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:left ear ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:left ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:microtia (30-60% of patients) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:microtia (30-60% of patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:microtia hearing loss, conductive ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:microtia hearing loss, conductive | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:mild cochlear hearing loss (1 patient) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:mild cochlear hearing loss (1 patient) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:narrowing of ear canal ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:narrowing of ear canal | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:no deafness ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:no deafness | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:no reproducible waves i, iii, or v at high intensities ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:no reproducible waves i, iii, or v at high intensities | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:normal middle ear pressures on tympanometry ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:normal middle ear pressures on tympanometry | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:ossified pinnae ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:ossified pinnae | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:overfolding of the superior helices ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:overfolding of the superior helices | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:pinna modeling anomalies ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:pinna modeling anomalies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:poorly shaped ears ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:poorly shaped ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:posteriorly rotated ears (2p21del) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:posteriorly rotated ears (2p21del) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:protruding lobules ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:protruding lobules | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:raised earlobes ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:raised earlobes | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:recurrent otitis media ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:recurrent otitis media | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:recurrent otitis media in infancy ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:recurrent otitis media in infancy | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:right ear ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:right ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:rudimentary ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:rudimentary | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:satyr ear ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:satyr ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:sensorineural deafness (rare) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural deafness (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:sensorineural deafness, postlingual, progressive ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural deafness, postlingual, progressive | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:sensorineural deafness, variable (in 1 family) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural deafness, variable (in 1 family) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:sensorineural hearing loss (uncommon) ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural hearing loss (uncommon) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:sensorineural hearing loss has been reported ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural hearing loss has been reported | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:severe loss in the higher frequencies by the fifth decade ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:severe loss in the higher frequencies by the fifth decade | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:small external auditory meatus ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:small external auditory meatus | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:underdeveloped tragus ---
r_associated #0: 29 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:underdeveloped tragus | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=29
- en:abnormal auditory temporal processes ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormal auditory temporal processes | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:abnormal communication between the subarachnoid space in the meatus and the perilymph ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormal communication between the subarachnoid space in the meatus and the perilymph | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:absence of earlobe ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:absence of earlobe | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:absent external auditory canals ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:absent external auditory canals | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:absent or decreased auditory brainstem responses ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:absent or decreased auditory brainstem responses | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:absent stapedial reflexes or intraoperative stapes immobility ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:absent stapedial reflexes or intraoperative stapes immobility | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:acoustic trauma ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:acoustic trauma | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:asymmetric dysplastic ears ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:asymmetric dysplastic ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:auditory neuropathy spectrum disorder ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:auditory neuropathy spectrum disorder | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:complete bony atresia of medial portion of external auditory canal (in some patients) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:complete bony atresia of medial portion of external auditory canal (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:crumpled ear (76%) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:crumpled ear (76%) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:cup-shaped auricles ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:cup-shaped auricles | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:deafness, congenital sensorineural, severe to profound ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, congenital sensorineural, severe to profound | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:deafness, postlingual ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, postlingual | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:deafness, sensorineural, severe to profound affecting all frequencies ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, sensorineural, severe to profound affecting all frequencies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:decreased otoacoustic emission amplitude ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:decreased otoacoustic emission amplitude | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:downward sloping audiogram ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:downward sloping audiogram | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:ear cartilage calcification ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:ear cartilage calcification | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:ear tag ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:ear tag | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:fear of ear disease ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:fear of ear disease | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:hearing impairment (rare) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing impairment (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:hearing loss (1 patient) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss (1 patient) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:hearing loss (95% of patients) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss (95% of patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:hearing loss (in 2 members of 1 family) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss (in 2 members of 1 family) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:hearing loss (in some patients) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:hearing loss affects all frequencies ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss affects all frequencies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:hearing loss, bilateral ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, bilateral | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:hearing loss, profound congenital sensorineural ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, profound congenital sensorineural | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:hearing loss, progressive conductive and/or sensorineural, during adulthood ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, progressive conductive and/or sensorineural, during adulthood | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:hearing loss, progressive sensorineural, affecting high frequencies ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, progressive sensorineural, affecting high frequencies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural (in one family) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural (in one family) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural, severe to profound ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural, severe to profound | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:hearing loss, unilateral, mild ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, unilateral, mild | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:hypoplasia of the upper part of the helix ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hypoplasia of the upper part of the helix | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:hypoplastic pinnae (30-60% of patients) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hypoplastic pinnae (30-60% of patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:large, dysmorphic ears ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:large, dysmorphic ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:long and prominent ear crus ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:long and prominent ear crus | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:mild to moderate hearing loss across most frequencies ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:mild to moderate hearing loss across most frequencies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:minor auricular anomalies ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:minor auricular anomalies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:narrow intertragic notch ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:narrow intertragic notch | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:occasional conductive hearing loss ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:occasional conductive hearing loss | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:otolaryngologist ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:otolaryngologist | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:otorhinolaryngologist ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:otorhinolaryngologist | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:overfolded helix ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:overfolded helix | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:posteriorly rotated ears (female) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:posteriorly rotated ears (female) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:preauricular fistulas, bilateral ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:preauricular fistulas, bilateral | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:profound sensorineural hearing loss ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:profound sensorineural hearing loss | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:progressive mixed conductive and sensorineural hearing loss ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:progressive mixed conductive and sensorineural hearing loss | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:progressive, low frequency sensorineural hearing loss ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:progressive, low frequency sensorineural hearing loss | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:protruding ears ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:protruding ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:pseudomembranous inflammation of the middle ear ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:pseudomembranous inflammation of the middle ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:sensorineural deafness (onset in the second decade in 25 to 30% of patients) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural deafness (onset in the second decade in 25 to 30% of patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:sensorineural hearing loss (1 patient) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural hearing loss (1 patient) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:sensorineural hearing loss (20% of patients) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural hearing loss (20% of patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:severe narrowing of cartilagenous auditory canal (in homozygotes) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:severe narrowing of cartilagenous auditory canal (in homozygotes) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:severe to profound hearing impairment by early adulthood ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:severe to profound hearing impairment by early adulthood | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:small, malformed ears ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:small, malformed ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:small, posteriorly rotated ears ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:small, posteriorly rotated ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:stenotic ear canals (30%) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:stenotic ear canals (30%) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:symmetric deterioration of hearing loss and speech reception with age ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:symmetric deterioration of hearing loss and speech reception with age | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:thick ears ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:thick ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:thick, firm earlobes ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:thick, firm earlobes | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:tinnitus (rare) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:tinnitus (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:tinnitus (variable) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:tinnitus (variable) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:u-shaped audiogram ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:u-shaped audiogram | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:uplift of earlobes (in some patients) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:uplift of earlobes (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:upturned lobes ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:upturned lobes | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:vertigo, single occurrence (in 2 patients) ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:vertigo, single occurrence (in 2 patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:vestibular areflexia ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:vestibular areflexia | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:vestibular hypofunction ---
r_associated #0: 28 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:vestibular hypofunction | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=28
- en:abnormal gap detection ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormal gap detection | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:absence of vestibular evoked myogenic potentials (rare) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:absence of vestibular evoked myogenic potentials (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:acute otitis media/myringitis ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:acute otitis media/myringitis | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:affects all frequencies ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:affects all frequencies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:angular ears ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:angular ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:anterior creases of earlobe ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:anterior creases of earlobe | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:aural atresia, congenital ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:aural atresia, congenital | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:bilateral dys-synchronized auditory brainstem responses ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:bilateral dys-synchronized auditory brainstem responses | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:bleeding from ear ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:bleeding from ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:cochleosaccular dysplasia ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:cochleosaccular dysplasia | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:concern with appearance of ears ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:concern with appearance of ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:congenital sensorineural hearing loss ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:congenital sensorineural hearing loss | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:deafness, sensorineural (in some patients) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, sensorineural (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:deafness, unilateral, childhood onset ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, unilateral, childhood onset | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:endolymphatic hydrops, delayed onset ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:endolymphatic hydrops, delayed onset | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:endolymphatic sac tumors (elsts) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:endolymphatic sac tumors (elsts) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:hearing loss, congenital, profound (250-8,000 hz) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, congenital, profound (250-8,000 hz) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:high-tone sensorineural deafness (67% of patients) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:high-tone sensorineural deafness (67% of patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:hypoplastic malleus (1 patient) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hypoplastic malleus (1 patient) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:long, lobulated ears ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:long, lobulated ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:loss of vestibular reflexes ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:loss of vestibular reflexes | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:low-frequency conductive hearing loss ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:low-frequency conductive hearing loss | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:macrotia ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:macrotia | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:microtia (wws) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:microtia (wws) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:microtia, type i ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:microtia, type i | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:mixed hearing loss ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:mixed hearing loss | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:mondini defect ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:mondini defect | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:mondini malformation ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:mondini malformation | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:narrow external ear canals (1 patient) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:narrow external ear canals (1 patient) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:no auditory brainstem response (abr) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:no auditory brainstem response (abr) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:overfolded, rumpled ears ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:overfolded, rumpled ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:pale, stiff pinnae ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:pale, stiff pinnae | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:phonophobia ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:phonophobia | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:posteriorly rotated ear ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:posteriorly rotated ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:posteriorly rotated ears (1/4 patients) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:posteriorly rotated ears (1/4 patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:preauricular dimple ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:preauricular dimple | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:preauricular sinus ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:preauricular sinus | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:preauricular skin tags (in some patients) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:preauricular skin tags (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:progressive hearing loss (in some) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:progressive hearing loss (in some) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:prominent ear ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:prominent ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:recurrent otitis media (18%) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:recurrent otitis media (18%) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:rudimentary ear ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:rudimentary ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:rudimentary tympanic membrane (in some patients) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:rudimentary tympanic membrane (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:sensorineural hearing impairment (less common) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural hearing impairment (less common) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:serous otitis ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:serous otitis | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:simple ear structure ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:simple ear structure | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:slit-like opening of the exterior auditory meatus ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:slit-like opening of the exterior auditory meatus | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:small/rudimentary tragus, antitragus and lobule ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:small/rudimentary tragus, antitragus and lobule | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:stapes ankylosis ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:stapes ankylosis | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:tinnitus (in some patients) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:tinnitus (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:triangular-shaped ears ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:triangular-shaped ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:tympanic membrane perforation ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:tympanic membrane perforation | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:underdeveloped nasal alae ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:underdeveloped nasal alae | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:unilateral external ear deformity ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:unilateral external ear deformity | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:vestibular abnormalities (variable) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:vestibular abnormalities (variable) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:vestibular dysfunction ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:vestibular dysfunction | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:vestibular involvement (variable) ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:vestibular involvement (variable) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:wide bulbous internal auditory meatus ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:wide bulbous internal auditory meatus | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:wide, flattened earlobes ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:wide, flattened earlobes | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- esgourde ---
r_associated #0: 27 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=esgourde | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=27
- en:abnormal brain auditory evoked responses (baer) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormal brain auditory evoked responses (baer) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:abnormal or absent auditory nerve and brainstem responses ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormal or absent auditory nerve and brainstem responses | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:abnormality of the helix ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormality of the helix | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:abnormally folded helix ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormally folded helix | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:absent brainstem auditory-evoked responses ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:absent brainstem auditory-evoked responses | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:affects mid- to high-frequencies ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:affects mid- to high-frequencies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:cleft at the superior portion of the pinna ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:cleft at the superior portion of the pinna | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:conductive hearing loss, mild bilateral (rare) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:conductive hearing loss, mild bilateral (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:deafness (often in third decade) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness (often in third decade) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:deafness, sensorineural, prelingual, profound ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, sensorineural, prelingual, profound | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:ear dimple ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:ear dimple | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:earlobe pits ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:earlobe pits | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:everted ears ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:everted ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:excessive cerumen ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:excessive cerumen | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:flattened antihelix ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:flattened antihelix | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:fleshy and overfolded helices ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:fleshy and overfolded helices | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:fleshy ears ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:fleshy ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:hearing impairment, asymmetric (in some patients with hsan2d) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing impairment, asymmetric (in some patients with hsan2d) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:hearing loss (rare) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:hearing loss, moderate to severe, bilateral, nonprogressive ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, moderate to severe, bilateral, nonprogressive | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:hearing loss, more severe at lower frequencies ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, more severe at lower frequencies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:hearing loss, prelingual sensorineural, moderate to severe ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, prelingual sensorineural, moderate to severe | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural (in some patients) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural (type ii) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural (type ii) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:hearing loss, unilateral (rare) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, unilateral (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:hypoacusia (1 patient) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hypoacusia (1 patient) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:large earlobe ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:large earlobe | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:large ears (37%) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:large ears (37%) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:large fleshy earlobes ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:large fleshy earlobes | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:large, low-set ears (uncommon) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:large, low-set ears (uncommon) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:lobule creases ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:lobule creases | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:low-set and rotated ears ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:low-set and rotated ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:low-set ears (3 patients) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:low-set ears (3 patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:malformed ossicular chain ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:malformed ossicular chain | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:malformed pinnae (30-60% of patients) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:malformed pinnae (30-60% of patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:middle ear ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:middle ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:no hearing loss ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:no hearing loss | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:no vestibular dysfunction ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:no vestibular dysfunction | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:no vestibular impairment ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:no vestibular impairment | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:normal otoacoustic emissions (oae), indicating intact outer ear hair cell function ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:normal otoacoustic emissions (oae), indicating intact outer ear hair cell function | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:partial aplasia of external auditory canal ending in blind fistula (in some patients) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:partial aplasia of external auditory canal ending in blind fistula (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:postauricular pit ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:postauricular pit | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:pre- and post-auricular skin or cartilaginous tags ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:pre- and post-auricular skin or cartilaginous tags | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:prelingual onset ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:prelingual onset | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:prominence and protrusion of upper third of the ear ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:prominence and protrusion of upper third of the ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:prominent crura ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:prominent crura | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:protruding ears (rare) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:protruding ears (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:protruding, simple ears ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:protruding, simple ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:retinitis (in some patients) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:retinitis (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:rotated ears ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:rotated ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:sensorineural deafness, progressive, late-onset ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural deafness, progressive, late-onset | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:sensorineural hearing loss, progressive bilateral postlingual ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural hearing loss, progressive bilateral postlingual | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:small earlobe ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:small earlobe | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:small external auditory canals ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:small external auditory canals | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:small pinna ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:small pinna | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:superiorly displaced ears ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:superiorly displaced ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:thick earlobes ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:thick earlobes | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:tinnitus, bilateral (in some patients) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:tinnitus, bilateral (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:vestibular anomalies (less common) ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:vestibular anomalies (less common) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- hyperlaxe ---
r_associated #0: 26 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=hyperlaxe | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=26
- en:anteriorly rotated ears ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:anteriorly rotated ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:asymmetry of the ears ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:asymmetry of the ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:atrophy of cochlear and vestibular fibrocytes ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:atrophy of cochlear and vestibular fibrocytes | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:audiogram is gently sloping or flat ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:audiogram is gently sloping or flat | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:deafness (sensorineural or mixed sensorineural and conductive) ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness (sensorineural or mixed sensorineural and conductive) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:deafness, autosomal recessive 101 ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, autosomal recessive 101 | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:deafness, prelingual, profound (affects all frequencies) ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, prelingual, profound (affects all frequencies) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:deafness, sensorineural, especially affecting high frequencies (in about 55% of males and 45% of females) ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, sensorineural, especially affecting high frequencies (in about 55% of males and 45% of females) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:ear neoplasm ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:ear neoplasm | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:flat or shallow u-shaped audiogram ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:flat or shallow u-shaped audiogram | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:folded helix ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:folded helix | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:hearing loss, mixed, mild to severe (in heterozygotes) ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, mixed, mild to severe (in heterozygotes) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:hearing loss, postlingual progressive sensorineural ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, postlingual progressive sensorineural | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural (in some cases) ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural (in some cases) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:hearing loss, sensorineural and conductive, severe to profound ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural and conductive, severe to profound | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:hearing threshold at or above 90 db at all frequencies tested (0.25-8.0 khz) ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing threshold at or above 90 db at all frequencies tested (0.25-8.0 khz) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:hypercompliant tympanic membranes ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hypercompliant tympanic membranes | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:large appearing ears ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:large appearing ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:large pinnae ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:large pinnae | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:large protruding ears ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:large protruding ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:loss of high frequencies at onset ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:loss of high frequencies at onset | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:loss of outer hair cell function ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:loss of outer hair cell function | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:low-set ears (in 2/4 patients) ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:low-set ears (in 2/4 patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:otitis externa ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:otitis externa | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:otitis media ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:otitis media | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:poorly formed pinnae ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:poorly formed pinnae | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:preauricular skin tag ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:preauricular skin tag | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:progressive sensorineural hearing impairment ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:progressive sensorineural hearing impairment | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:prominent earlobes (in some patients) ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:prominent earlobes (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:roll-head ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:roll-head | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:vestibular areflexia, complete ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:vestibular areflexia, complete | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:vestibular hyporeflexia ---
r_associated #0: 25 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:vestibular hyporeflexia | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=25
- en:'tilted' ears ---
r_associated #0: 24 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:'tilted' ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=24
- en:abnormal helices, antihelices and lobules ---
r_associated #0: 24 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormal helices, antihelices and lobules | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=24
- en:anomalous middle ear bones ---
r_associated #0: 24 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:anomalous middle ear bones | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=24
- en:anteverted ears ---
r_associated #0: 24 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:anteverted ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=24
- en:bat ear ---
r_associated #0: 24 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:bat ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=24
- en:chronic otitis other infection ear ---
r_associated #0: 24 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:chronic otitis other infection ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=24
- en:conductive and sensorineural hearing loss ---
r_associated #0: 24 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:conductive and sensorineural hearing loss | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=24
- en:deafness, sensorineural, variable ---
r_associated #0: 24 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, sensorineural, variable | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=24
- en:decreased auditory brainstem responses ---
r_associated #0: 24 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:decreased auditory brainstem responses | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=24
- en:expansion of helical fold at superior point of true longitudinal axis of ear ---
r_associated #0: 24 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:expansion of helical fold at superior point of true longitudinal axis of ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=24
- en:glue ear ---
r_associated #0: 24 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:glue ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural (in sister) ---
r_associated #0: 24 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural (in sister) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges) ---
r_associated #0: 24 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural, mid-frequency (in some patients) ---
r_associated #0: 24 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural, mid-frequency (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=24
- en:limited auditory function ---
r_associated #0: 24 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:limited auditory function | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=24
- en:narrow ears ---
r_associated #0: 24 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:narrow ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=24
- en:preauricular pits (70-80% of patients) ---
r_associated #0: 24 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:preauricular pits (70-80% of patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=24
- en:abnormal amplitude modulation detection ---
r_associated #0: 23 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormal amplitude modulation detection | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=23
- en:abnormal brainstem auditory evoked potentials (baep) ---
r_associated #0: 23 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormal brainstem auditory evoked potentials (baep) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=23
- en:absent cochlear microphonic (in older patients) ---
r_associated #0: 23 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:absent cochlear microphonic (in older patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=23
- en:auriculo-condylar syndrome ---
r_associated #0: 23 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:auriculo-condylar syndrome | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=23
- en:cleft at the junction of the lobule and helix ---
r_associated #0: 23 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:cleft at the junction of the lobule and helix | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=23
- en:congenital small ears ---
r_associated #0: 23 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:congenital small ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=23
- en:downsloping audiogram ---
r_associated #0: 23 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:downsloping audiogram | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=23
- en:hearing loss begins with loss of high frequencies ---
r_associated #0: 23 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss begins with loss of high frequencies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural (in 1 ashkenazi patient) ---
r_associated #0: 23 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural (in 1 ashkenazi patient) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural, progressive (childhood-onset) ---
r_associated #0: 23 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural, progressive (childhood-onset) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=23
- en:hearing loss, unilateral or bilateral, conductive, sensorineural, or mixed ---
r_associated #0: 23 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, unilateral or bilateral, conductive, sensorineural, or mixed | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=23
- en:low-set ears (1 patient) ---
r_associated #0: 23 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:low-set ears (1 patient) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=23
- en:narrowed external ear canal ---
r_associated #0: 23 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:narrowed external ear canal | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=23
- en:no hearing impairment ---
r_associated #0: 23 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:no hearing impairment | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=23
- en:nonprogressive ---
r_associated #0: 23 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:nonprogressive | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=23
- en:other auditory injuries ---
r_associated #0: 23 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:other auditory injuries | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=23
- en:otorrhea ---
r_associated #0: 23 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:otorrhea | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=23
- en:otosclerosis ---
r_associated #0: 23 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:otosclerosis | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=23
- en:protruding right ear ---
r_associated #0: 23 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:protruding right ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=23
- en:simple helix ---
r_associated #0: 23 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:simple helix | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=23
- en:abnormal bridge connecting the crus of the helix and antihelix ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormal bridge connecting the crus of the helix and antihelix | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:abnormal middle ear reflexes ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormal middle ear reflexes | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:abnormality of the outer ear ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormality of the outer ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:blind fistula ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:blind fistula | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:conductive hearing loss, bilateral ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:conductive hearing loss, bilateral | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:cupped ears (finding) ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:cupped ears (finding) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:deafness, congenital nonprogressive sensorineural symmetric, moderate ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, congenital nonprogressive sensorineural symmetric, moderate | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:deafness, profound, by 6th decade ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, profound, by 6th decade | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:escalope ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:escalope | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:increased posterior angulation ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:increased posterior angulation | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:inferior displacement of the ears ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:inferior displacement of the ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:internal auditory canal hypoplasia ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:internal auditory canal hypoplasia | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:large auricle ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:large auricle | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:misshapen, small ear ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:misshapen, small ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:no auditory brainstem response to 100-db stimulus ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:no auditory brainstem response to 100-db stimulus | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:prominent lobules ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:prominent lobules | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:protuberant ear ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:protuberant ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:sensation of blocked ears ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensation of blocked ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:sensorineural hearing loss (described in 1 family) ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural hearing loss (described in 1 family) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:sensorineural hearing loss (in 1 of 3 patients) ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural hearing loss (in 1 of 3 patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:short ears (in 1 family) ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:short ears (in 1 family) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:small pits anterior to the helix (1 patient) ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:small pits anterior to the helix (1 patient) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:squared-off superior helices ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:squared-off superior helices | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:tinnitus ---
r_associated #0: 22 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:tinnitus | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=22
- en:abnormal semicircular canals ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:abnormal semicircular canals | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:absent or abnormal otoacoustic emissions ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:absent or abnormal otoacoustic emissions | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:audiogram shows sloping configuration ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:audiogram shows sloping configuration | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:bilateral hypoplastic cochlea ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:bilateral hypoplastic cochlea | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:disturbance of equilibrium ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:disturbance of equilibrium | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:dysplastic pinnae ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:dysplastic pinnae | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:eustachian tube salpingitis ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:eustachian tube salpingitis | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:external ear ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:external ear | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:foreign body in auditory canal ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:foreign body in auditory canal | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:hearing impairment may occur ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing impairment may occur | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:hearing loss (conductive and/or sensorineural) ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss (conductive and/or sensorineural) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:hearing loss (reported in 2 patients) ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss (reported in 2 patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:hearing loss, conductive (rare) ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, conductive (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:hearing loss, prelingual, severe to profound (affecting all frequencies) ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, prelingual, severe to profound (affecting all frequencies) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies) ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:hearing loss, sensorineural (reported in 1 patient) ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing loss, sensorineural (reported in 1 patient) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:hypoplastic superior helix ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hypoplastic superior helix | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:large anteverted ears (rare) ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:large anteverted ears (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:low-set ears (in some patients) ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:low-set ears (in some patients) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:low-set, posteriorly rotated ears ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:low-set, posteriorly rotated ears | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:near-stenosis of bony portion of auditory canal ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:near-stenosis of bony portion of auditory canal | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:other diseases of ear/mastoid ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:other diseases of ear/mastoid | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:otitis media, recurrent (rare) ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:otitis media, recurrent (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:progressive hearing impairment ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:progressive hearing impairment | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:progressive high-frequency hearing loss (onset 20-30 years) ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:progressive high-frequency hearing loss (onset 20-30 years) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:sensorineural hearing loss (males only) ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural hearing loss (males only) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:sensorineural hearing loss (rare) ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:sensorineural hearing loss (rare) | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:synotus ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:synotus | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:vertiginous syndrome ---
r_associated #0: 21 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:vertiginous syndrome | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=21
- en:and throat ---
r_associated #0: 20 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:and throat | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=20
- en:nose and throat ---
r_associated #0: 20 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:nose and throat | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=20
- nose ---
r_associated #0: 20 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=nose | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=20
- Trouble de l'équilibre ---
r_associated #0: 15 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=Trouble de l'équilibre | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=15
- en:dizzy spells ---
r_associated #0: 15 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:dizzy spells | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=15
- en:giddiness ---
r_associated #0: 15 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:giddiness | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=15
- en:scatterbrain ---
r_associated #0: 15 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:scatterbrain | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=15
- vertiges ---
r_associated #0: 15 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=vertiges | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=15
- vertigineux ---
r_associated #0: 15 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=vertigineux | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=15
- Étourdi ---
r_associated #0: 15 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=Étourdi | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=15
- Étourdie ---
r_associated #0: 15 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=Étourdie | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=15
- étourdie ---
r_associated #0: 15 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=étourdie | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=15
- étourdies ---
r_associated #0: 15 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=étourdies | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=15
- étourdis ---
r_associated #0: 15 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=étourdis | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=15
- étourdissements ---
r_associated #0: 15 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=étourdissements | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=15
- Hyperacousie ---
r_associated #0: 10 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=Hyperacousie | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=10
- Oto-rhino-laryngologiste ---
r_associated #0: 10 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=Oto-rhino-laryngologiste | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=10
- Otorhinolaryngologiste ---
r_associated #0: 10 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=Otorhinolaryngologiste | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=10
- ankylose stapédo-vestibulaire ---
r_associated #0: 10 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=ankylose stapédo-vestibulaire | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=10
- ankylose stapédo-vestibulaire l.f. ---
r_associated #0: 10 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=ankylose stapédo-vestibulaire l.f. | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=10
- aplati ---
r_associated #0: 10 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=aplati | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=10
- en:deaf-muteness ---
r_associated #0: 10 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deaf-muteness | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=10
- en:deaf-mutism ---
r_associated #0: 10 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:deaf-mutism | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=10
- en:hearing defect ---
r_associated #0: 10 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing defect | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=10
- en:hearing deficiency ---
r_associated #0: 10 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:hearing deficiency | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=10
- en:lughole ---
r_associated #0: 10 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:lughole | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=10
- en:schitzel ---
r_associated #0: 10 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:schitzel | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=10
- en:speech difficulties due to deafness ---
r_associated #0: 10 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:speech difficulties due to deafness | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=10
- oreille moyenne ---
r_associated #0: 10 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=oreille moyenne | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=10
- otite moyenne adhésive ---
r_associated #0: 10 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=otite moyenne adhésive | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=10
- surdité ---
r_associated #0: 10 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=surdité | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=10
- tête de linotte ---
r_associated #0: 10 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=tête de linotte | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=10
- Étourdissements ---
r_associated #0: 10 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=Étourdissements | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=10
- à priori ---
r_associated #0: 10 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=à priori | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=10
- Sensation de rotation ---
r_associated #0: 5 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=Sensation de rotation | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=5
- escalope ---
r_associated #0: -20 -->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=escalope | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=-20
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