'en:otoneurologic disturbances'
(id=6815420 ; fe=en:otoneurologic disturbances ; type=1 ; niveau=200 ;
luminosité=25 ;
somme entrante=27207 creation date=2017-06-25 touchdate=2025-12-23 11:10:49.000) ≈ 735 relations sortantes
- en:otoneurologic disturbances --
r_associated #0: 43 / 1 ->
en:endolymphatic hydrops, delayed onset
n1=en:otoneurologic disturbances | n2=en:endolymphatic hydrops, delayed onset | rel=r_associated | relid=0 | w=43
- en:otoneurologic disturbances --
r_associated #0: 43 / 1 ->
en:enlarged vestibular aqueduct
n1=en:otoneurologic disturbances | n2=en:enlarged vestibular aqueduct | rel=r_associated | relid=0 | w=43
- en:otoneurologic disturbances --
r_associated #0: 43 / 1 ->
en:folded helix
n1=en:otoneurologic disturbances | n2=en:folded helix | rel=r_associated | relid=0 | w=43
- en:otoneurologic disturbances --
r_associated #0: 43 / 1 ->
en:hearing loss, progressive sensorineural, affecting high frequencies
n1=en:otoneurologic disturbances | n2=en:hearing loss, progressive sensorineural, affecting high frequencies | rel=r_associated | relid=0 | w=43
- en:otoneurologic disturbances --
r_associated #0: 43 / 1 ->
en:hearing loss, sensorineural and conductive, severe to profound
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural and conductive, severe to profound | rel=r_associated | relid=0 | w=43
- en:otoneurologic disturbances --
r_associated #0: 43 / 1 ->
en:loss of outer hair cell function
n1=en:otoneurologic disturbances | n2=en:loss of outer hair cell function | rel=r_associated | relid=0 | w=43
- en:otoneurologic disturbances --
r_associated #0: 43 / 1 ->
en:supraauricular pit
n1=en:otoneurologic disturbances | n2=en:supraauricular pit | rel=r_associated | relid=0 | w=43
- en:otoneurologic disturbances --
r_associated #0: 42 / 0.977 ->
en:asymmetry of the ears
n1=en:otoneurologic disturbances | n2=en:asymmetry of the ears | rel=r_associated | relid=0 | w=42
- en:otoneurologic disturbances --
r_associated #0: 42 / 0.977 ->
en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years
n1=en:otoneurologic disturbances | n2=en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years | rel=r_associated | relid=0 | w=42
- en:otoneurologic disturbances --
r_associated #0: 42 / 0.977 ->
en:external ear
n1=en:otoneurologic disturbances | n2=en:external ear | rel=r_associated | relid=0 | w=42
- en:otoneurologic disturbances --
r_associated #0: 42 / 0.977 ->
en:hearing loss (conductive and/or sensorineural)
n1=en:otoneurologic disturbances | n2=en:hearing loss (conductive and/or sensorineural) | rel=r_associated | relid=0 | w=42
- en:otoneurologic disturbances --
r_associated #0: 42 / 0.977 ->
en:large fleshy earlobes
n1=en:otoneurologic disturbances | n2=en:large fleshy earlobes | rel=r_associated | relid=0 | w=42
- en:otoneurologic disturbances --
r_associated #0: 42 / 0.977 ->
en:sensorineural hearing loss (3 patients)
n1=en:otoneurologic disturbances | n2=en:sensorineural hearing loss (3 patients) | rel=r_associated | relid=0 | w=42
- en:otoneurologic disturbances --
r_associated #0: 42 / 0.977 ->
en:vestibulopathy, bilateral, progressive
n1=en:otoneurologic disturbances | n2=en:vestibulopathy, bilateral, progressive | rel=r_associated | relid=0 | w=42
- en:otoneurologic disturbances --
r_associated #0: 41 / 0.953 ->
en:abnormal semicircular canals
n1=en:otoneurologic disturbances | n2=en:abnormal semicircular canals | rel=r_associated | relid=0 | w=41
- en:otoneurologic disturbances --
r_associated #0: 41 / 0.953 ->
en:approximately 0.7db per year hearing loss at all frequencies
n1=en:otoneurologic disturbances | n2=en:approximately 0.7db per year hearing loss at all frequencies | rel=r_associated | relid=0 | w=41
- en:otoneurologic disturbances --
r_associated #0: 41 / 0.953 ->
en:dysmorphic ears
n1=en:otoneurologic disturbances | n2=en:dysmorphic ears | rel=r_associated | relid=0 | w=41
- en:otoneurologic disturbances --
r_associated #0: 41 / 0.953 ->
en:hearing impairment may occur
n1=en:otoneurologic disturbances | n2=en:hearing impairment may occur | rel=r_associated | relid=0 | w=41
- en:otoneurologic disturbances --
r_associated #0: 41 / 0.953 ->
en:hearing loss (cvs+)
n1=en:otoneurologic disturbances | n2=en:hearing loss (cvs+) | rel=r_associated | relid=0 | w=41
- en:otoneurologic disturbances --
r_associated #0: 41 / 0.953 ->
en:hearing loss affects all frequencies
n1=en:otoneurologic disturbances | n2=en:hearing loss affects all frequencies | rel=r_associated | relid=0 | w=41
- en:otoneurologic disturbances --
r_associated #0: 41 / 0.953 ->
en:hearing loss, sensorineural, associated with elsts
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural, associated with elsts | rel=r_associated | relid=0 | w=41
- en:otoneurologic disturbances --
r_associated #0: 41 / 0.953 ->
en:hearing loss, sensorineural, moderate, postlingual
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural, moderate, postlingual | rel=r_associated | relid=0 | w=41
- en:otoneurologic disturbances --
r_associated #0: 41 / 0.953 ->
en:hearing loss, unilateral or bilateral, conductive, sensorineural, or mixed
n1=en:otoneurologic disturbances | n2=en:hearing loss, unilateral or bilateral, conductive, sensorineural, or mixed | rel=r_associated | relid=0 | w=41
- en:otoneurologic disturbances --
r_associated #0: 41 / 0.953 ->
en:mild to moderate hearing loss
n1=en:otoneurologic disturbances | n2=en:mild to moderate hearing loss | rel=r_associated | relid=0 | w=41
- en:otoneurologic disturbances --
r_associated #0: 41 / 0.953 ->
en:overfolding of the superior helices
n1=en:otoneurologic disturbances | n2=en:overfolding of the superior helices | rel=r_associated | relid=0 | w=41
- en:otoneurologic disturbances --
r_associated #0: 41 / 0.953 ->
en:preauricular sinus, bilateral
n1=en:otoneurologic disturbances | n2=en:preauricular sinus, bilateral | rel=r_associated | relid=0 | w=41
- en:otoneurologic disturbances --
r_associated #0: 41 / 0.953 ->
en:progressive, low frequency sensorineural hearing loss
n1=en:otoneurologic disturbances | n2=en:progressive, low frequency sensorineural hearing loss | rel=r_associated | relid=0 | w=41
- en:otoneurologic disturbances --
r_associated #0: 41 / 0.953 ->
en:sensorineural hearing loss has been reported
n1=en:otoneurologic disturbances | n2=en:sensorineural hearing loss has been reported | rel=r_associated | relid=0 | w=41
- en:otoneurologic disturbances --
r_associated #0: 40 / 0.93 ->
en:abnormality of the outer ear
n1=en:otoneurologic disturbances | n2=en:abnormality of the outer ear | rel=r_associated | relid=0 | w=40
- en:otoneurologic disturbances --
r_associated #0: 40 / 0.93 ->
en:complete bony atresia of medial portion of external auditory canal (in some patients)
n1=en:otoneurologic disturbances | n2=en:complete bony atresia of medial portion of external auditory canal (in some patients) | rel=r_associated | relid=0 | w=40
- en:otoneurologic disturbances --
r_associated #0: 40 / 0.93 ->
en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v
n1=en:otoneurologic disturbances | n2=en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v | rel=r_associated | relid=0 | w=40
- en:otoneurologic disturbances --
r_associated #0: 40 / 0.93 ->
en:narrow auditory canals (rare)
n1=en:otoneurologic disturbances | n2=en:narrow auditory canals (rare) | rel=r_associated | relid=0 | w=40
- en:otoneurologic disturbances --
r_associated #0: 39 / 0.907 ->
en:ear part
n1=en:otoneurologic disturbances | n2=en:ear part | rel=r_associated | relid=0 | w=39
- en:otoneurologic disturbances --
r_associated #0: 39 / 0.907 ->
en:hearing disorder (1 patient)
n1=en:otoneurologic disturbances | n2=en:hearing disorder (1 patient) | rel=r_associated | relid=0 | w=39
- en:otoneurologic disturbances --
r_associated #0: 39 / 0.907 ->
en:hearing loss, conductive or mixed
n1=en:otoneurologic disturbances | n2=en:hearing loss, conductive or mixed | rel=r_associated | relid=0 | w=39
- en:otoneurologic disturbances --
r_associated #0: 39 / 0.907 ->
en:hearing loss, neural type
n1=en:otoneurologic disturbances | n2=en:hearing loss, neural type | rel=r_associated | relid=0 | w=39
- en:otoneurologic disturbances --
r_associated #0: 39 / 0.907 ->
en:nonsyndromic sensorineural hearing loss
n1=en:otoneurologic disturbances | n2=en:nonsyndromic sensorineural hearing loss | rel=r_associated | relid=0 | w=39
- en:otoneurologic disturbances --
r_associated #0: 39 / 0.907 ->
en:presbycusis
n1=en:otoneurologic disturbances | n2=en:presbycusis | rel=r_associated | relid=0 | w=39
- en:otoneurologic disturbances --
r_associated #0: 39 / 0.907 ->
en:simple helix
n1=en:otoneurologic disturbances | n2=en:simple helix | rel=r_associated | relid=0 | w=39
- en:otoneurologic disturbances --
r_associated #0: 39 / 0.907 ->
en:small ears (female)
n1=en:otoneurologic disturbances | n2=en:small ears (female) | rel=r_associated | relid=0 | w=39
- en:otoneurologic disturbances --
r_associated #0: 38 / 0.884 ->
en:absent earlobe
n1=en:otoneurologic disturbances | n2=en:absent earlobe | rel=r_associated | relid=0 | w=38
- en:otoneurologic disturbances --
r_associated #0: 38 / 0.884 ->
en:accessory tragus
n1=en:otoneurologic disturbances | n2=en:accessory tragus | rel=r_associated | relid=0 | w=38
- en:otoneurologic disturbances --
r_associated #0: 38 / 0.884 ->
en:deafness, congenital nonprogressive sensorineural symmetric, moderate
n1=en:otoneurologic disturbances | n2=en:deafness, congenital nonprogressive sensorineural symmetric, moderate | rel=r_associated | relid=0 | w=38
- en:otoneurologic disturbances --
r_associated #0: 38 / 0.884 ->
en:deafness, moderate-severe (onset in third decade)
n1=en:otoneurologic disturbances | n2=en:deafness, moderate-severe (onset in third decade) | rel=r_associated | relid=0 | w=38
- en:otoneurologic disturbances --
r_associated #0: 38 / 0.884 ->
en:hearing loss, high frequency, slowly progressive (onset in early childhood)
n1=en:otoneurologic disturbances | n2=en:hearing loss, high frequency, slowly progressive (onset in early childhood) | rel=r_associated | relid=0 | w=38
- en:otoneurologic disturbances --
r_associated #0: 38 / 0.884 ->
en:vestibular abnormalities (variable)
n1=en:otoneurologic disturbances | n2=en:vestibular abnormalities (variable) | rel=r_associated | relid=0 | w=38
- en:otoneurologic disturbances --
r_associated #0: 38 / 0.884 ->
en:vestibular hyporeflexia
n1=en:otoneurologic disturbances | n2=en:vestibular hyporeflexia | rel=r_associated | relid=0 | w=38
- en:otoneurologic disturbances --
r_associated #0: 37 / 0.86 ->
en:absent distortion product otoacoustic emissions (oaes)
n1=en:otoneurologic disturbances | n2=en:absent distortion product otoacoustic emissions (oaes) | rel=r_associated | relid=0 | w=37
- en:otoneurologic disturbances --
r_associated #0: 37 / 0.86 ->
en:anteriorly displaced ears
n1=en:otoneurologic disturbances | n2=en:anteriorly displaced ears | rel=r_associated | relid=0 | w=37
- en:otoneurologic disturbances --
r_associated #0: 37 / 0.86 ->
en:deafness due to bilateral cochlear malformation (rare)
n1=en:otoneurologic disturbances | n2=en:deafness due to bilateral cochlear malformation (rare) | rel=r_associated | relid=0 | w=37
- en:otoneurologic disturbances --
r_associated #0: 37 / 0.86 ->
en:hearing loss, sensorineural (in 2 patients)
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural (in 2 patients) | rel=r_associated | relid=0 | w=37
- en:otoneurologic disturbances --
r_associated #0: 37 / 0.86 ->
en:malformed pinnae (30-60% of patients)
n1=en:otoneurologic disturbances | n2=en:malformed pinnae (30-60% of patients) | rel=r_associated | relid=0 | w=37
- en:otoneurologic disturbances --
r_associated #0: 37 / 0.86 ->
en:pre- and post-auricular skin or cartilaginous tags
n1=en:otoneurologic disturbances | n2=en:pre- and post-auricular skin or cartilaginous tags | rel=r_associated | relid=0 | w=37
- en:otoneurologic disturbances --
r_associated #0: 37 / 0.86 ->
en:progressive hearing impairment
n1=en:otoneurologic disturbances | n2=en:progressive hearing impairment | rel=r_associated | relid=0 | w=37
- en:otoneurologic disturbances --
r_associated #0: 36 / 0.837 ->
en:atretic auditory canal
n1=en:otoneurologic disturbances | n2=en:atretic auditory canal | rel=r_associated | relid=0 | w=36
- en:otoneurologic disturbances --
r_associated #0: 36 / 0.837 ->
en:hearing loss, sensorineural (in sister)
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural (in sister) | rel=r_associated | relid=0 | w=36
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:abnormal helices, antihelices and lobules
n1=en:otoneurologic disturbances | n2=en:abnormal helices, antihelices and lobules | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:abnormally folded helix
n1=en:otoneurologic disturbances | n2=en:abnormally folded helix | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:absence of the cochlear nerves (reported in 1 patient)
n1=en:otoneurologic disturbances | n2=en:absence of the cochlear nerves (reported in 1 patient) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:absent external auditory meatus
n1=en:otoneurologic disturbances | n2=en:absent external auditory meatus | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:air-bone gap of greater than 20 db across 0.5 to 2 khz
n1=en:otoneurologic disturbances | n2=en:air-bone gap of greater than 20 db across 0.5 to 2 khz | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:angular ears
n1=en:otoneurologic disturbances | n2=en:angular ears | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:aplasia of the inner ear
n1=en:otoneurologic disturbances | n2=en:aplasia of the inner ear | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:asymmetric dysplastic ears
n1=en:otoneurologic disturbances | n2=en:asymmetric dysplastic ears | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:auricular clefts
n1=en:otoneurologic disturbances | n2=en:auricular clefts | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:bilateral conductive hearing loss (rare)
n1=en:otoneurologic disturbances | n2=en:bilateral conductive hearing loss (rare) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:bilateral sensorineural hearing loss (in some patients)
n1=en:otoneurologic disturbances | n2=en:bilateral sensorineural hearing loss (in some patients) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion
n1=en:otoneurologic disturbances | n2=en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:conductive hearing loss (in a subset of patients)
n1=en:otoneurologic disturbances | n2=en:conductive hearing loss (in a subset of patients) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:cupped ears (finding)
n1=en:otoneurologic disturbances | n2=en:cupped ears (finding) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:deafness affects all frequencies
n1=en:otoneurologic disturbances | n2=en:deafness affects all frequencies | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:deafness, sensorineural (reported in 1 family)
n1=en:otoneurologic disturbances | n2=en:deafness, sensorineural (reported in 1 family) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:deafness, sensorineural, especially affecting high frequencies (in about 55% of males and 45% of females)
n1=en:otoneurologic disturbances | n2=en:deafness, sensorineural, especially affecting high frequencies (in about 55% of males and 45% of females) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:deafness, sensorineural, prelingual, profound
n1=en:otoneurologic disturbances | n2=en:deafness, sensorineural, prelingual, profound | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:deafness, sensorineural, profound
n1=en:otoneurologic disturbances | n2=en:deafness, sensorineural, profound | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:disjunction of otherwise normal lobule from remainder of ear
n1=en:otoneurologic disturbances | n2=en:disjunction of otherwise normal lobule from remainder of ear | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:dysplastic pinnae
n1=en:otoneurologic disturbances | n2=en:dysplastic pinnae | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:endolymphatic sac tumors (elsts)
n1=en:otoneurologic disturbances | n2=en:endolymphatic sac tumors (elsts) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:external auditory canal narrow
n1=en:otoneurologic disturbances | n2=en:external auditory canal narrow | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:fear of ear disease
n1=en:otoneurologic disturbances | n2=en:fear of ear disease | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:flattened
n1=en:otoneurologic disturbances | n2=en:flattened | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:fleshy ears
n1=en:otoneurologic disturbances | n2=en:fleshy ears | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:foreign body in auditory canal
n1=en:otoneurologic disturbances | n2=en:foreign body in auditory canal | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:hearing complaints (excluding h84-86)
n1=en:otoneurologic disturbances | n2=en:hearing complaints (excluding h84-86) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:hearing loss, bilateral
n1=en:otoneurologic disturbances | n2=en:hearing loss, bilateral | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:hearing loss, bilateral progressive post-lingual
n1=en:otoneurologic disturbances | n2=en:hearing loss, bilateral progressive post-lingual | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:hearing loss, conductive (in one family)
n1=en:otoneurologic disturbances | n2=en:hearing loss, conductive (in one family) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:hearing loss, conductive (rare)
n1=en:otoneurologic disturbances | n2=en:hearing loss, conductive (rare) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:hearing loss, congenital sensorineural, moderate-severe
n1=en:otoneurologic disturbances | n2=en:hearing loss, congenital sensorineural, moderate-severe | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:hearing loss, mild (rare)
n1=en:otoneurologic disturbances | n2=en:hearing loss, mild (rare) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:hearing loss, mixed (in some patients)
n1=en:otoneurologic disturbances | n2=en:hearing loss, mixed (in some patients) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:hearing loss, mixed, mild to severe (in heterozygotes)
n1=en:otoneurologic disturbances | n2=en:hearing loss, mixed, mild to severe (in heterozygotes) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:hearing loss, prelingual sensorineural, moderate to severe
n1=en:otoneurologic disturbances | n2=en:hearing loss, prelingual sensorineural, moderate to severe | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:hearing loss, sensorineural (variable)
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural (variable) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges)
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:hearing loss, sensorineural, prelingual
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural, prelingual | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:hypertrophic auricular cartilage
n1=en:otoneurologic disturbances | n2=en:hypertrophic auricular cartilage | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:hypoplastic malleus (1 patient)
n1=en:otoneurologic disturbances | n2=en:hypoplastic malleus (1 patient) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:incomplete separation of the cochlea from the internal auditory canal
n1=en:otoneurologic disturbances | n2=en:incomplete separation of the cochlea from the internal auditory canal | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:large dysplastic ears
n1=en:otoneurologic disturbances | n2=en:large dysplastic ears | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:large ears (2p21del)
n1=en:otoneurologic disturbances | n2=en:large ears (2p21del) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:large protruding ears
n1=en:otoneurologic disturbances | n2=en:large protruding ears | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:left ear
n1=en:otoneurologic disturbances | n2=en:left ear | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:low-set ears (45%)
n1=en:otoneurologic disturbances | n2=en:low-set ears (45%) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:narrow ears
n1=en:otoneurologic disturbances | n2=en:narrow ears | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:narrow external ear canals (1 patient)
n1=en:otoneurologic disturbances | n2=en:narrow external ear canals (1 patient) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:narrowed external ear canal
n1=en:otoneurologic disturbances | n2=en:narrowed external ear canal | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:no hearing impairment
n1=en:otoneurologic disturbances | n2=en:no hearing impairment | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:oae responses may decrease with age or use of hearing aids
n1=en:otoneurologic disturbances | n2=en:oae responses may decrease with age or use of hearing aids | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:overfolded, rumpled ears
n1=en:otoneurologic disturbances | n2=en:overfolded, rumpled ears | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:postauricular pit
n1=en:otoneurologic disturbances | n2=en:postauricular pit | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:prelingual onset
n1=en:otoneurologic disturbances | n2=en:prelingual onset | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:progressive conductive hearing impairment
n1=en:otoneurologic disturbances | n2=en:progressive conductive hearing impairment | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:progressive sensorineural hearing impairment
n1=en:otoneurologic disturbances | n2=en:progressive sensorineural hearing impairment | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:prominent antitragus
n1=en:otoneurologic disturbances | n2=en:prominent antitragus | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:prominent ears (rare)
n1=en:otoneurologic disturbances | n2=en:prominent ears (rare) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:protruding ears
n1=en:otoneurologic disturbances | n2=en:protruding ears | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:recurrent otitis media in infancy
n1=en:otoneurologic disturbances | n2=en:recurrent otitis media in infancy | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:retinitis (in some patients)
n1=en:otoneurologic disturbances | n2=en:retinitis (in some patients) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:sclerosis of semicircular canals
n1=en:otoneurologic disturbances | n2=en:sclerosis of semicircular canals | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:sensorineural deafness, progressive, late-onset
n1=en:otoneurologic disturbances | n2=en:sensorineural deafness, progressive, late-onset | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:short ears (in 1 family)
n1=en:otoneurologic disturbances | n2=en:short ears (in 1 family) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:simple ear
n1=en:otoneurologic disturbances | n2=en:simple ear | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:small earlobe
n1=en:otoneurologic disturbances | n2=en:small earlobe | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:stenosis of external auditory canal
n1=en:otoneurologic disturbances | n2=en:stenosis of external auditory canal | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:structure of superior auricularis muscle
n1=en:otoneurologic disturbances | n2=en:structure of superior auricularis muscle | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:superior semicircular canal dehiscence syndrome
n1=en:otoneurologic disturbances | n2=en:superior semicircular canal dehiscence syndrome | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:thick ears
n1=en:otoneurologic disturbances | n2=en:thick ears | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:vestibular dysfunction (in some patients)
n1=en:otoneurologic disturbances | n2=en:vestibular dysfunction (in some patients) | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 35 / 0.814 ->
en:vestibular hypofunction
n1=en:otoneurologic disturbances | n2=en:vestibular hypofunction | rel=r_associated | relid=0 | w=35
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:abnormality of the helix
n1=en:otoneurologic disturbances | n2=en:abnormality of the helix | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:abnormality of the middle ear ossicles
n1=en:otoneurologic disturbances | n2=en:abnormality of the middle ear ossicles | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:abnormality of the pinna
n1=en:otoneurologic disturbances | n2=en:abnormality of the pinna | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:absence of acoustic reflex
n1=en:otoneurologic disturbances | n2=en:absence of acoustic reflex | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:atretic ear canals
n1=en:otoneurologic disturbances | n2=en:atretic ear canals | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient)
n1=en:otoneurologic disturbances | n2=en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient) | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:cleft at the junction of the lobule and helix
n1=en:otoneurologic disturbances | n2=en:cleft at the junction of the lobule and helix | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:deafness, sensorineural, severe to profound affecting all frequencies
n1=en:otoneurologic disturbances | n2=en:deafness, sensorineural, severe to profound affecting all frequencies | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:dorsally rotated ears
n1=en:otoneurologic disturbances | n2=en:dorsally rotated ears | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:downsloping audiogram
n1=en:otoneurologic disturbances | n2=en:downsloping audiogram | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:ear cartilage calcification
n1=en:otoneurologic disturbances | n2=en:ear cartilage calcification | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:ears deficient in cartilage
n1=en:otoneurologic disturbances | n2=en:ears deficient in cartilage | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:excessive cerumen
n1=en:otoneurologic disturbances | n2=en:excessive cerumen | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:external ears rudimentary
n1=en:otoneurologic disturbances | n2=en:external ears rudimentary | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:flat ears
n1=en:otoneurologic disturbances | n2=en:flat ears | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:hearing impairment, sensorineural, mild
n1=en:otoneurologic disturbances | n2=en:hearing impairment, sensorineural, mild | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:hearing loss (2 patients)
n1=en:otoneurologic disturbances | n2=en:hearing loss (2 patients) | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:hearing loss, conductive (in some patients)
n1=en:otoneurologic disturbances | n2=en:hearing loss, conductive (in some patients) | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:hearing loss, progressive conductive and/or sensorineural, during adulthood
n1=en:otoneurologic disturbances | n2=en:hearing loss, progressive conductive and/or sensorineural, during adulthood | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:hearing loss, progressive, starting in infancy
n1=en:otoneurologic disturbances | n2=en:hearing loss, progressive, starting in infancy | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:hearing loss, sensorineural (in one family)
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural (in one family) | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:hearing loss, sensorineural, bilateral, moderate-to-severe
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural, bilateral, moderate-to-severe | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:high-tone sensorineural deafness (67% of patients)
n1=en:otoneurologic disturbances | n2=en:high-tone sensorineural deafness (67% of patients) | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:hypoplastic helices
n1=en:otoneurologic disturbances | n2=en:hypoplastic helices | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:hypoplastic superior helix
n1=en:otoneurologic disturbances | n2=en:hypoplastic superior helix | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:impaired tympanic membrane mobility
n1=en:otoneurologic disturbances | n2=en:impaired tympanic membrane mobility | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:increased posterior angulation
n1=en:otoneurologic disturbances | n2=en:increased posterior angulation | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:large appearing ears
n1=en:otoneurologic disturbances | n2=en:large appearing ears | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:low set ears
n1=en:otoneurologic disturbances | n2=en:low set ears | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:low-set ears (1 patient)
n1=en:otoneurologic disturbances | n2=en:low-set ears (1 patient) | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:low-set ears (in 2/4 patients)
n1=en:otoneurologic disturbances | n2=en:low-set ears (in 2/4 patients) | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:low-set, malformed ears
n1=en:otoneurologic disturbances | n2=en:low-set, malformed ears | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:michel aplasia (complete absence of inner ear structures)
n1=en:otoneurologic disturbances | n2=en:michel aplasia (complete absence of inner ear structures) | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:microtia hearing loss, conductive
n1=en:otoneurologic disturbances | n2=en:microtia hearing loss, conductive | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:middle ear
n1=en:otoneurologic disturbances | n2=en:middle ear | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:misshapen ear
n1=en:otoneurologic disturbances | n2=en:misshapen ear | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:misshapen, small ear
n1=en:otoneurologic disturbances | n2=en:misshapen, small ear | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:mondini malformation
n1=en:otoneurologic disturbances | n2=en:mondini malformation | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:narrow ear lobes
n1=en:otoneurologic disturbances | n2=en:narrow ear lobes | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:neural hearing loss
n1=en:otoneurologic disturbances | n2=en:neural hearing loss | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:otitis externa
n1=en:otoneurologic disturbances | n2=en:otitis externa | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:otitis media, recurrent (rare)
n1=en:otoneurologic disturbances | n2=en:otitis media, recurrent (rare) | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:partial hearing loss
n1=en:otoneurologic disturbances | n2=en:partial hearing loss | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:pigmentation of the ear cartilage
n1=en:otoneurologic disturbances | n2=en:pigmentation of the ear cartilage | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:pinna modeling anomalies
n1=en:otoneurologic disturbances | n2=en:pinna modeling anomalies | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:posteriorly rotated ear
n1=en:otoneurologic disturbances | n2=en:posteriorly rotated ear | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:profound sensorineural hearing loss
n1=en:otoneurologic disturbances | n2=en:profound sensorineural hearing loss | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:prominence and protrusion of upper third of the ear
n1=en:otoneurologic disturbances | n2=en:prominence and protrusion of upper third of the ear | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:protruding right ear
n1=en:otoneurologic disturbances | n2=en:protruding right ear | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:protuberant ear
n1=en:otoneurologic disturbances | n2=en:protuberant ear | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:recurrent otitis
n1=en:otoneurologic disturbances | n2=en:recurrent otitis | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:recurrent otitis media
n1=en:otoneurologic disturbances | n2=en:recurrent otitis media | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:sensorineural deafness, postlingual, progressive
n1=en:otoneurologic disturbances | n2=en:sensorineural deafness, postlingual, progressive | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:sensorineural hearing loss (1 family)
n1=en:otoneurologic disturbances | n2=en:sensorineural hearing loss (1 family) | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:slit-like opening of the exterior auditory meatus
n1=en:otoneurologic disturbances | n2=en:slit-like opening of the exterior auditory meatus | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:small, posteriorly rotated ears
n1=en:otoneurologic disturbances | n2=en:small, posteriorly rotated ears | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:small/rudimentary tragus, antitragus and lobule
n1=en:otoneurologic disturbances | n2=en:small/rudimentary tragus, antitragus and lobule | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:symmetric deterioration of hearing loss and speech reception with age
n1=en:otoneurologic disturbances | n2=en:symmetric deterioration of hearing loss and speech reception with age | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:thick, firm earlobes
n1=en:otoneurologic disturbances | n2=en:thick, firm earlobes | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:transient evoked otoacoustic emissions cannot be detected
n1=en:otoneurologic disturbances | n2=en:transient evoked otoacoustic emissions cannot be detected | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:type i arnold chiari malformation
n1=en:otoneurologic disturbances | n2=en:type i arnold chiari malformation | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 34 / 0.791 ->
en:underdeveloped nasal alae
n1=en:otoneurologic disturbances | n2=en:underdeveloped nasal alae | rel=r_associated | relid=0 | w=34
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:absent or abnormal otoacoustic emissions
n1=en:otoneurologic disturbances | n2=en:absent or abnormal otoacoustic emissions | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:absent vestibular function (caloric test)
n1=en:otoneurologic disturbances | n2=en:absent vestibular function (caloric test) | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:acute otitis media/myringitis
n1=en:otoneurologic disturbances | n2=en:acute otitis media/myringitis | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:bleeding from ear
n1=en:otoneurologic disturbances | n2=en:bleeding from ear | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:cauliflower ear deformity (rare)
n1=en:otoneurologic disturbances | n2=en:cauliflower ear deformity (rare) | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:chronic otitis
n1=en:otoneurologic disturbances | n2=en:chronic otitis | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:concern with appearance of ears
n1=en:otoneurologic disturbances | n2=en:concern with appearance of ears | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:conductive hearing loss, bilateral
n1=en:otoneurologic disturbances | n2=en:conductive hearing loss, bilateral | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:cup-shaped ears (30-60% of patients)
n1=en:otoneurologic disturbances | n2=en:cup-shaped ears (30-60% of patients) | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:deafness (variable)
n1=en:otoneurologic disturbances | n2=en:deafness (variable) | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:deafness, profound, affects all frequencies
n1=en:otoneurologic disturbances | n2=en:deafness, profound, affects all frequencies | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:deafness, secondary to cranial hyperostosis
n1=en:otoneurologic disturbances | n2=en:deafness, secondary to cranial hyperostosis | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:decreased auditory brainstem responses
n1=en:otoneurologic disturbances | n2=en:decreased auditory brainstem responses | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:dilatated internal auditory canal
n1=en:otoneurologic disturbances | n2=en:dilatated internal auditory canal | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:disproportionately large ears
n1=en:otoneurologic disturbances | n2=en:disproportionately large ears | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:earlobe pits
n1=en:otoneurologic disturbances | n2=en:earlobe pits | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:eustachian tube salpingitis
n1=en:otoneurologic disturbances | n2=en:eustachian tube salpingitis | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:everted ears
n1=en:otoneurologic disturbances | n2=en:everted ears | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:folded superior edge of helix
n1=en:otoneurologic disturbances | n2=en:folded superior edge of helix | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:hearing loss (reported in 2 patients)
n1=en:otoneurologic disturbances | n2=en:hearing loss (reported in 2 patients) | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:hearing loss, mild
n1=en:otoneurologic disturbances | n2=en:hearing loss, mild | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:hearing loss, postlingual progressive sensorineural
n1=en:otoneurologic disturbances | n2=en:hearing loss, postlingual progressive sensorineural | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:hearing loss, postlingual sensorineural
n1=en:otoneurologic disturbances | n2=en:hearing loss, postlingual sensorineural | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:hearing loss, profound prelingual sensorineural
n1=en:otoneurologic disturbances | n2=en:hearing loss, profound prelingual sensorineural | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:hearing loss, sensorineural (high frequency)
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural (high frequency) | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:hearing loss, sensorineural (reported in 1 patient)
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural (reported in 1 patient) | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:hearing loss, sensorineural, mild progressive (in some patients)
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural, mild progressive (in some patients) | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:hearing loss, unilateral (rare)
n1=en:otoneurologic disturbances | n2=en:hearing loss, unilateral (rare) | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural
n1=en:otoneurologic disturbances | n2=en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients)
n1=en:otoneurologic disturbances | n2=en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients) | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:keratotic plaque around ear meatus
n1=en:otoneurologic disturbances | n2=en:keratotic plaque around ear meatus | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:large anteverted ears (rare)
n1=en:otoneurologic disturbances | n2=en:large anteverted ears (rare) | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:large auricle
n1=en:otoneurologic disturbances | n2=en:large auricle | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:large earlobe
n1=en:otoneurologic disturbances | n2=en:large earlobe | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:large fleshy ears
n1=en:otoneurologic disturbances | n2=en:large fleshy ears | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:long, lobulated ears
n1=en:otoneurologic disturbances | n2=en:long, lobulated ears | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:loss of vestibular caloric response
n1=en:otoneurologic disturbances | n2=en:loss of vestibular caloric response | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:microtia, type i
n1=en:otoneurologic disturbances | n2=en:microtia, type i | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:mild to moderate hearing loss across most frequencies
n1=en:otoneurologic disturbances | n2=en:mild to moderate hearing loss across most frequencies | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:narrowed external ear canal (30% of patients)
n1=en:otoneurologic disturbances | n2=en:narrowed external ear canal (30% of patients) | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:near-stenosis of bony portion of auditory canal
n1=en:otoneurologic disturbances | n2=en:near-stenosis of bony portion of auditory canal | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:no auditory brainstem response to 100-db stimulus
n1=en:otoneurologic disturbances | n2=en:no auditory brainstem response to 100-db stimulus | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:normal vestibular function
n1=en:otoneurologic disturbances | n2=en:normal vestibular function | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:overfolded helix
n1=en:otoneurologic disturbances | n2=en:overfolded helix | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:poorly shaped ears
n1=en:otoneurologic disturbances | n2=en:poorly shaped ears | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:preauricular dimple
n1=en:otoneurologic disturbances | n2=en:preauricular dimple | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:preauricular skin furrow
n1=en:otoneurologic disturbances | n2=en:preauricular skin furrow | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:prominent ear
n1=en:otoneurologic disturbances | n2=en:prominent ear | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:prominent ears (in some patients)
n1=en:otoneurologic disturbances | n2=en:prominent ears (in some patients) | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:prominent helices
n1=en:otoneurologic disturbances | n2=en:prominent helices | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:relatively long ears
n1=en:otoneurologic disturbances | n2=en:relatively long ears | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:retroverted ears
n1=en:otoneurologic disturbances | n2=en:retroverted ears | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:rotated ears
n1=en:otoneurologic disturbances | n2=en:rotated ears | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:rudimentary tympanic membrane (in some patients)
n1=en:otoneurologic disturbances | n2=en:rudimentary tympanic membrane (in some patients) | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:sensorineural deafness (rare)
n1=en:otoneurologic disturbances | n2=en:sensorineural deafness (rare) | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:sensorineural deafness (reported in 1 family)
n1=en:otoneurologic disturbances | n2=en:sensorineural deafness (reported in 1 family) | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:sensorineural deafness, variable (in 1 family)
n1=en:otoneurologic disturbances | n2=en:sensorineural deafness, variable (in 1 family) | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:sensorineural hearing loss (onset early childhood)
n1=en:otoneurologic disturbances | n2=en:sensorineural hearing loss (onset early childhood) | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:severe narrowing of cartilagenous auditory canal
n1=en:otoneurologic disturbances | n2=en:severe narrowing of cartilagenous auditory canal | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:small cavum conchae
n1=en:otoneurologic disturbances | n2=en:small cavum conchae | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:small ears with large lobules
n1=en:otoneurologic disturbances | n2=en:small ears with large lobules | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:small lobes
n1=en:otoneurologic disturbances | n2=en:small lobes | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:small pinna
n1=en:otoneurologic disturbances | n2=en:small pinna | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:small, malformed ears
n1=en:otoneurologic disturbances | n2=en:small, malformed ears | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:squared-off ears
n1=en:otoneurologic disturbances | n2=en:squared-off ears | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:thickened lobes
n1=en:otoneurologic disturbances | n2=en:thickened lobes | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:u-shaped audiogram
n1=en:otoneurologic disturbances | n2=en:u-shaped audiogram | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:vertiginous syndrome
n1=en:otoneurologic disturbances | n2=en:vertiginous syndrome | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 32 / 0.744 ->
en:vertigo, episodic
n1=en:otoneurologic disturbances | n2=en:vertigo, episodic | rel=r_associated | relid=0 | w=32
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:a subset of patients have hearing loss
n1=en:otoneurologic disturbances | n2=en:a subset of patients have hearing loss | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:abnormal auditory temporal processes
n1=en:otoneurologic disturbances | n2=en:abnormal auditory temporal processes | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:abnormal middle ear reflexes
n1=en:otoneurologic disturbances | n2=en:abnormal middle ear reflexes | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:abnormally shaped ears (in one family)
n1=en:otoneurologic disturbances | n2=en:abnormally shaped ears (in one family) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:absent auditory canals (wws)
n1=en:otoneurologic disturbances | n2=en:absent auditory canals (wws) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:affects mid- to high-frequencies
n1=en:otoneurologic disturbances | n2=en:affects mid- to high-frequencies | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:anomalous middle ear bones
n1=en:otoneurologic disturbances | n2=en:anomalous middle ear bones | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:anteverted ears
n1=en:otoneurologic disturbances | n2=en:anteverted ears | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:bat ear
n1=en:otoneurologic disturbances | n2=en:bat ear | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:cleft at the superior portion of the pinna
n1=en:otoneurologic disturbances | n2=en:cleft at the superior portion of the pinna | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:cochleosaccular dysplasia
n1=en:otoneurologic disturbances | n2=en:cochleosaccular dysplasia | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:conductive hearing loss to due otitis media
n1=en:otoneurologic disturbances | n2=en:conductive hearing loss to due otitis media | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:conductive hearing loss, mild bilateral (rare)
n1=en:otoneurologic disturbances | n2=en:conductive hearing loss, mild bilateral (rare) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:congenital hearing loss (1 family)
n1=en:otoneurologic disturbances | n2=en:congenital hearing loss (1 family) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:congenital small ears
n1=en:otoneurologic disturbances | n2=en:congenital small ears | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:deafness (in 1 of 2 families)
n1=en:otoneurologic disturbances | n2=en:deafness (in 1 of 2 families) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:deafness in 30-50% of patients with skull involvement
n1=en:otoneurologic disturbances | n2=en:deafness in 30-50% of patients with skull involvement | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:deafness, bilateral sensorineural, high frequency (100% of patients)
n1=en:otoneurologic disturbances | n2=en:deafness, bilateral sensorineural, high frequency (100% of patients) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:deafness, conductive (in some patients)
n1=en:otoneurologic disturbances | n2=en:deafness, conductive (in some patients) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:deafness, congenital sensorineural, profound (in some patients)
n1=en:otoneurologic disturbances | n2=en:deafness, congenital sensorineural, profound (in some patients) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:deafness, sensorineural (severe to profound)
n1=en:otoneurologic disturbances | n2=en:deafness, sensorineural (severe to profound) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:deafness, stable bilateral symmetric prelingual
n1=en:otoneurologic disturbances | n2=en:deafness, stable bilateral symmetric prelingual | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:dizziness
n1=en:otoneurologic disturbances | n2=en:dizziness | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:ear pain/earache
n1=en:otoneurologic disturbances | n2=en:ear pain/earache | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:fleshy and overfolded helices
n1=en:otoneurologic disturbances | n2=en:fleshy and overfolded helices | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:hearing impairment (rare)
n1=en:otoneurologic disturbances | n2=en:hearing impairment (rare) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:hearing loss (95% of patients)
n1=en:otoneurologic disturbances | n2=en:hearing loss (95% of patients) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:hearing loss (rare)
n1=en:otoneurologic disturbances | n2=en:hearing loss (rare) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:hearing loss first affects high frequencies
n1=en:otoneurologic disturbances | n2=en:hearing loss first affects high frequencies | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:hearing loss, congenital profound
n1=en:otoneurologic disturbances | n2=en:hearing loss, congenital profound | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:hearing loss, initially conductive, later mixed conductive-sensorineural
n1=en:otoneurologic disturbances | n2=en:hearing loss, initially conductive, later mixed conductive-sensorineural | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:hearing loss, progressive (in some patients)
n1=en:otoneurologic disturbances | n2=en:hearing loss, progressive (in some patients) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:hearing loss, sensorineural (in some cases)
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural (in some cases) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:hearing normal
n1=en:otoneurologic disturbances | n2=en:hearing normal | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:hypermobile
n1=en:otoneurologic disturbances | n2=en:hypermobile | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:hypoplastic ears fused to the scalp
n1=en:otoneurologic disturbances | n2=en:hypoplastic ears fused to the scalp | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:hypoplastic semicircular canals
n1=en:otoneurologic disturbances | n2=en:hypoplastic semicircular canals | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:incomplete atretic plate
n1=en:otoneurologic disturbances | n2=en:incomplete atretic plate | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:large ears (37%)
n1=en:otoneurologic disturbances | n2=en:large ears (37%) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:large simple ears
n1=en:otoneurologic disturbances | n2=en:large simple ears | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:linear ear lobe creases
n1=en:otoneurologic disturbances | n2=en:linear ear lobe creases | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:loss of high frequencies at onset
n1=en:otoneurologic disturbances | n2=en:loss of high frequencies at onset | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:loss of mid- and low-frequencies later
n1=en:otoneurologic disturbances | n2=en:loss of mid- and low-frequencies later | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:low-set ears (3 patients)
n1=en:otoneurologic disturbances | n2=en:low-set ears (3 patients) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:low-set ears (in one family)
n1=en:otoneurologic disturbances | n2=en:low-set ears (in one family) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:low-set ears (rare)
n1=en:otoneurologic disturbances | n2=en:low-set ears (rare) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:mixed hearing loss
n1=en:otoneurologic disturbances | n2=en:mixed hearing loss | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:narrowing of ear canal
n1=en:otoneurologic disturbances | n2=en:narrowing of ear canal | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:nonprogressive
n1=en:otoneurologic disturbances | n2=en:nonprogressive | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:normal outer hair cell functions
n1=en:otoneurologic disturbances | n2=en:normal outer hair cell functions | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:normal vestibular response
n1=en:otoneurologic disturbances | n2=en:normal vestibular response | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:organ of corti degeneration
n1=en:otoneurologic disturbances | n2=en:organ of corti degeneration | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:ossified pinnae
n1=en:otoneurologic disturbances | n2=en:ossified pinnae | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:otitis media
n1=en:otoneurologic disturbances | n2=en:otitis media | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:otorrhea
n1=en:otoneurologic disturbances | n2=en:otorrhea | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:outer ear abnormalities (deletion patients) prominent ears
n1=en:otoneurologic disturbances | n2=en:outer ear abnormalities (deletion patients) prominent ears | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:posteriorly rotated ears (female)
n1=en:otoneurologic disturbances | n2=en:posteriorly rotated ears (female) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:preauricular fistulas, bilateral
n1=en:otoneurologic disturbances | n2=en:preauricular fistulas, bilateral | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:preauricular skin tag
n1=en:otoneurologic disturbances | n2=en:preauricular skin tag | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:progressive hearing loss (in some)
n1=en:otoneurologic disturbances | n2=en:progressive hearing loss (in some) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:prominent lobules
n1=en:otoneurologic disturbances | n2=en:prominent lobules | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:protruding ears (rare)
n1=en:otoneurologic disturbances | n2=en:protruding ears (rare) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:raised earlobes
n1=en:otoneurologic disturbances | n2=en:raised earlobes | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:recurrent ear infections
n1=en:otoneurologic disturbances | n2=en:recurrent ear infections | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:sensorineural hearing impairment (less common)
n1=en:otoneurologic disturbances | n2=en:sensorineural hearing impairment (less common) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:sensorineural hearing loss (described in 1 family)
n1=en:otoneurologic disturbances | n2=en:sensorineural hearing loss (described in 1 family) | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:sensorineural hearing loss, mild to moderate
n1=en:otoneurologic disturbances | n2=en:sensorineural hearing loss, mild to moderate | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:serous otitis media
n1=en:otoneurologic disturbances | n2=en:serous otitis media | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:short ear
n1=en:otoneurologic disturbances | n2=en:short ear | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:small, simple ears
n1=en:otoneurologic disturbances | n2=en:small, simple ears | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:stapes ankylosis
n1=en:otoneurologic disturbances | n2=en:stapes ankylosis | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:stapes fixation
n1=en:otoneurologic disturbances | n2=en:stapes fixation | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:synotus
n1=en:otoneurologic disturbances | n2=en:synotus | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves
n1=en:otoneurologic disturbances | n2=en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 31 / 0.721 ->
en:unconnected or fused stapes and incus
n1=en:otoneurologic disturbances | n2=en:unconnected or fused stapes and incus | rel=r_associated | relid=0 | w=31
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:abnormal amplitude modulation detection
n1=en:otoneurologic disturbances | n2=en:abnormal amplitude modulation detection | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:abnormal communication between the subarachnoid space in the meatus and the perilymph
n1=en:otoneurologic disturbances | n2=en:abnormal communication between the subarachnoid space in the meatus and the perilymph | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:abnormal middle ear ossicles
n1=en:otoneurologic disturbances | n2=en:abnormal middle ear ossicles | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:abnormally folded ears
n1=en:otoneurologic disturbances | n2=en:abnormally folded ears | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:absence of vestibular evoked myogenic potentials (rare)
n1=en:otoneurologic disturbances | n2=en:absence of vestibular evoked myogenic potentials (rare) | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:auditory neuropathy spectrum disorder
n1=en:otoneurologic disturbances | n2=en:auditory neuropathy spectrum disorder | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:auriculo-condylar syndrome
n1=en:otoneurologic disturbances | n2=en:auriculo-condylar syndrome | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:bilateral dys-synchronized auditory brainstem responses
n1=en:otoneurologic disturbances | n2=en:bilateral dys-synchronized auditory brainstem responses | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:cochlear degeneration
n1=en:otoneurologic disturbances | n2=en:cochlear degeneration | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss)
n1=en:otoneurologic disturbances | n2=en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss) | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:deafness
n1=en:otoneurologic disturbances | n2=en:deafness | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:deafness (often in third decade)
n1=en:otoneurologic disturbances | n2=en:deafness (often in third decade) | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:deafness, early-onset
n1=en:otoneurologic disturbances | n2=en:deafness, early-onset | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:deafness, postlingual
n1=en:otoneurologic disturbances | n2=en:deafness, postlingual | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:deafness, prelingual, profound (affects all frequencies)
n1=en:otoneurologic disturbances | n2=en:deafness, prelingual, profound (affects all frequencies) | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:deafness, unilateral, childhood onset
n1=en:otoneurologic disturbances | n2=en:deafness, unilateral, childhood onset | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:downward sloping or flat audiogram
n1=en:otoneurologic disturbances | n2=en:downward sloping or flat audiogram | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:dysplastic helices
n1=en:otoneurologic disturbances | n2=en:dysplastic helices | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:ear constriction (97%)
n1=en:otoneurologic disturbances | n2=en:ear constriction (97%) | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:ear pits, posterior helical
n1=en:otoneurologic disturbances | n2=en:ear pits, posterior helical | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:entire ear
n1=en:otoneurologic disturbances | n2=en:entire ear | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:expansion of helical fold at superior point of true longitudinal axis of ear
n1=en:otoneurologic disturbances | n2=en:expansion of helical fold at superior point of true longitudinal axis of ear | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:flat audiogram
n1=en:otoneurologic disturbances | n2=en:flat audiogram | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:hearing impairment, asymmetric (in some patients with hsan2d)
n1=en:otoneurologic disturbances | n2=en:hearing impairment, asymmetric (in some patients with hsan2d) | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:hearing loss (uncommon)
n1=en:otoneurologic disturbances | n2=en:hearing loss (uncommon) | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:hearing loss (variable)
n1=en:otoneurologic disturbances | n2=en:hearing loss (variable) | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:hearing loss, moderate to severe, bilateral, nonprogressive
n1=en:otoneurologic disturbances | n2=en:hearing loss, moderate to severe, bilateral, nonprogressive | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:hearing loss, more severe at lower frequencies
n1=en:otoneurologic disturbances | n2=en:hearing loss, more severe at lower frequencies | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:hearing loss, postlingual
n1=en:otoneurologic disturbances | n2=en:hearing loss, postlingual | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:hearing loss, sensorineural (type ii)
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural (type ii) | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:hearing loss, sensorineural, progressive (childhood-onset)
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural, progressive (childhood-onset) | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:hearing loss, unilateral, mild
n1=en:otoneurologic disturbances | n2=en:hearing loss, unilateral, mild | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:hypercompliant tympanic membranes
n1=en:otoneurologic disturbances | n2=en:hypercompliant tympanic membranes | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:hyperfolded ears
n1=en:otoneurologic disturbances | n2=en:hyperfolded ears | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:hypoplasia of the upper part of the helix
n1=en:otoneurologic disturbances | n2=en:hypoplasia of the upper part of the helix | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:inner ear
n1=en:otoneurologic disturbances | n2=en:inner ear | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:large anteverted pinnae (90% males, 40% females)
n1=en:otoneurologic disturbances | n2=en:large anteverted pinnae (90% males, 40% females) | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:low-frequency sensorineural hearing impairment
n1=en:otoneurologic disturbances | n2=en:low-frequency sensorineural hearing impairment | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:low-set ears (in some patients)
n1=en:otoneurologic disturbances | n2=en:low-set ears (in some patients) | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:microtia (30-60% of patients)
n1=en:otoneurologic disturbances | n2=en:microtia (30-60% of patients) | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:minor ear anomalies (in some patients)
n1=en:otoneurologic disturbances | n2=en:minor ear anomalies (in some patients) | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:no hearing loss
n1=en:otoneurologic disturbances | n2=en:no hearing loss | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:normal otoacoustic emissions
n1=en:otoneurologic disturbances | n2=en:normal otoacoustic emissions | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:occasional conductive hearing loss
n1=en:otoneurologic disturbances | n2=en:occasional conductive hearing loss | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:other diseases of ear/mastoid
n1=en:otoneurologic disturbances | n2=en:other diseases of ear/mastoid | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:otosclerosis
n1=en:otoneurologic disturbances | n2=en:otosclerosis | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:pale, stiff pinnae
n1=en:otoneurologic disturbances | n2=en:pale, stiff pinnae | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:phonophobia
n1=en:otoneurologic disturbances | n2=en:phonophobia | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:posteriorly rotated ears (2p21del)
n1=en:otoneurologic disturbances | n2=en:posteriorly rotated ears (2p21del) | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:posteriorly rotated ears (in some patients)
n1=en:otoneurologic disturbances | n2=en:posteriorly rotated ears (in some patients) | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:preauricular sinus
n1=en:otoneurologic disturbances | n2=en:preauricular sinus | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:progressive cartilaginous ossification of pinnae
n1=en:otoneurologic disturbances | n2=en:progressive cartilaginous ossification of pinnae | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:prolonged brainstem auditory evoked potentials (baep)
n1=en:otoneurologic disturbances | n2=en:prolonged brainstem auditory evoked potentials (baep) | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:protruding lobules
n1=en:otoneurologic disturbances | n2=en:protruding lobules | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:satyr ear
n1=en:otoneurologic disturbances | n2=en:satyr ear | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:sensorineural hearing loss (in 1 of 3 patients)
n1=en:otoneurologic disturbances | n2=en:sensorineural hearing loss (in 1 of 3 patients) | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:sensorineural hearing loss (less common)
n1=en:otoneurologic disturbances | n2=en:sensorineural hearing loss (less common) | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:sensorineural hearing loss (males only)
n1=en:otoneurologic disturbances | n2=en:sensorineural hearing loss (males only) | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:sensorineural hearing loss, progressive bilateral postlingual
n1=en:otoneurologic disturbances | n2=en:sensorineural hearing loss, progressive bilateral postlingual | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:severe loss in the higher frequencies by the fifth decade
n1=en:otoneurologic disturbances | n2=en:severe loss in the higher frequencies by the fifth decade | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:simplified helices
n1=en:otoneurologic disturbances | n2=en:simplified helices | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:structure of lymphatic vessel of ear
n1=en:otoneurologic disturbances | n2=en:structure of lymphatic vessel of ear | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:thickened helices
n1=en:otoneurologic disturbances | n2=en:thickened helices | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:u- or bowl-shaped audiogram
n1=en:otoneurologic disturbances | n2=en:u- or bowl-shaped audiogram | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:underdeveloped tragus
n1=en:otoneurologic disturbances | n2=en:underdeveloped tragus | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:upturned lobes
n1=en:otoneurologic disturbances | n2=en:upturned lobes | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:vestibular areflexia
n1=en:otoneurologic disturbances | n2=en:vestibular areflexia | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 30 / 0.698 ->
en:vestibular involvement (variable)
n1=en:otoneurologic disturbances | n2=en:vestibular involvement (variable) | rel=r_associated | relid=0 | w=30
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:abnormal auditory brainstem responses
n1=en:otoneurologic disturbances | n2=en:abnormal auditory brainstem responses | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:abnormal brainstem auditory evoked potentials (baep)
n1=en:otoneurologic disturbances | n2=en:abnormal brainstem auditory evoked potentials (baep) | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:abnormal ear configuration
n1=en:otoneurologic disturbances | n2=en:abnormal ear configuration | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:absence of the helix and distal scapha in middle third of the ear
n1=en:otoneurologic disturbances | n2=en:absence of the helix and distal scapha in middle third of the ear | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:absent brainstem auditory responses
n1=en:otoneurologic disturbances | n2=en:absent brainstem auditory responses | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:absent lobules
n1=en:otoneurologic disturbances | n2=en:absent lobules | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:acoustic trauma
n1=en:otoneurologic disturbances | n2=en:acoustic trauma | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:anteriorly rotated ears
n1=en:otoneurologic disturbances | n2=en:anteriorly rotated ears | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:audiogram may be ascending
n1=en:otoneurologic disturbances | n2=en:audiogram may be ascending | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:audiogram shows sloping configuration
n1=en:otoneurologic disturbances | n2=en:audiogram shows sloping configuration | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:aural atresia, congenital
n1=en:otoneurologic disturbances | n2=en:aural atresia, congenital | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:aural fullness
n1=en:otoneurologic disturbances | n2=en:aural fullness | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:bilateral congenital profound sensorineural hearing loss
n1=en:otoneurologic disturbances | n2=en:bilateral congenital profound sensorineural hearing loss | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:blind fistula
n1=en:otoneurologic disturbances | n2=en:blind fistula | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:chronic otitis media
n1=en:otoneurologic disturbances | n2=en:chronic otitis media | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:chronic otitis other infection ear
n1=en:otoneurologic disturbances | n2=en:chronic otitis other infection ear | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:cleft lobules
n1=en:otoneurologic disturbances | n2=en:cleft lobules | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:cochlear malformation
n1=en:otoneurologic disturbances | n2=en:cochlear malformation | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:conductive and sensorineural hearing loss
n1=en:otoneurologic disturbances | n2=en:conductive and sensorineural hearing loss | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:congenital atresia of external auditory canal
n1=en:otoneurologic disturbances | n2=en:congenital atresia of external auditory canal | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:cup-shaped auricles
n1=en:otoneurologic disturbances | n2=en:cup-shaped auricles | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:cupped ears (in some patients)
n1=en:otoneurologic disturbances | n2=en:cupped ears (in some patients) | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:deafness (sensorineural or mixed sensorineural and conductive)
n1=en:otoneurologic disturbances | n2=en:deafness (sensorineural or mixed sensorineural and conductive) | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:deafness, profound, by 6th decade
n1=en:otoneurologic disturbances | n2=en:deafness, profound, by 6th decade | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:deafness, sensorineural, especially affecting high frequencies
n1=en:otoneurologic disturbances | n2=en:deafness, sensorineural, especially affecting high frequencies | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:decreased otoacoustic emission amplitude
n1=en:otoneurologic disturbances | n2=en:decreased otoacoustic emission amplitude | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:external ear defects
n1=en:otoneurologic disturbances | n2=en:external ear defects | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:hearing deficits (28% of adults)
n1=en:otoneurologic disturbances | n2=en:hearing deficits (28% of adults) | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:hearing impairment (in 1/4 patients)
n1=en:otoneurologic disturbances | n2=en:hearing impairment (in 1/4 patients) | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:hearing loss, sensorineural, severe to profound
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural, severe to profound | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:hypoplastic pinnae (30-60% of patients)
n1=en:otoneurologic disturbances | n2=en:hypoplastic pinnae (30-60% of patients) | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:hypoplastic, overfolded helices
n1=en:otoneurologic disturbances | n2=en:hypoplastic, overfolded helices | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:large prominent ears
n1=en:otoneurologic disturbances | n2=en:large prominent ears | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:large, floppy ears
n1=en:otoneurologic disturbances | n2=en:large, floppy ears | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:limited auditory function
n1=en:otoneurologic disturbances | n2=en:limited auditory function | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:lobular aplasia
n1=en:otoneurologic disturbances | n2=en:lobular aplasia | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:lobule creases
n1=en:otoneurologic disturbances | n2=en:lobule creases | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:lobule may be separately from the rest of the external ear
n1=en:otoneurologic disturbances | n2=en:lobule may be separately from the rest of the external ear | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:low-frequency conductive hearing loss
n1=en:otoneurologic disturbances | n2=en:low-frequency conductive hearing loss | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:low-set ears (severe form)
n1=en:otoneurologic disturbances | n2=en:low-set ears (severe form) | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:malformed auricle (1 patient)
n1=en:otoneurologic disturbances | n2=en:malformed auricle (1 patient) | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:malformed earlobes
n1=en:otoneurologic disturbances | n2=en:malformed earlobes | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:meniere disease
n1=en:otoneurologic disturbances | n2=en:meniere disease | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:morphological abnormality of the middle ear
n1=en:otoneurologic disturbances | n2=en:morphological abnormality of the middle ear | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:neonatal cystic lesions of the pinnae
n1=en:otoneurologic disturbances | n2=en:neonatal cystic lesions of the pinnae | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:no vestibular impairment
n1=en:otoneurologic disturbances | n2=en:no vestibular impairment | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:normal otoacoustic emissions (oae), indicating intact outer ear hair cell function
n1=en:otoneurologic disturbances | n2=en:normal otoacoustic emissions (oae), indicating intact outer ear hair cell function | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:poorly folded ears
n1=en:otoneurologic disturbances | n2=en:poorly folded ears | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face)
n1=en:otoneurologic disturbances | n2=en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face) | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:secretory otitis media
n1=en:otoneurologic disturbances | n2=en:secretory otitis media | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:sensation of blocked ears
n1=en:otoneurologic disturbances | n2=en:sensation of blocked ears | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:sensorineural hearing impairment (in some patients)
n1=en:otoneurologic disturbances | n2=en:sensorineural hearing impairment (in some patients) | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:sensorineural hearing loss
n1=en:otoneurologic disturbances | n2=en:sensorineural hearing loss | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:sensory hearing loss
n1=en:otoneurologic disturbances | n2=en:sensory hearing loss | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:severe to profound deafness
n1=en:otoneurologic disturbances | n2=en:severe to profound deafness | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:severe to profound hearing impairment by early adulthood
n1=en:otoneurologic disturbances | n2=en:severe to profound hearing impairment by early adulthood | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:simple auricles
n1=en:otoneurologic disturbances | n2=en:simple auricles | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:simple ear structure
n1=en:otoneurologic disturbances | n2=en:simple ear structure | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:small pits anterior to the helix (1 patient)
n1=en:otoneurologic disturbances | n2=en:small pits anterior to the helix (1 patient) | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:tinnitus (in some patients)
n1=en:otoneurologic disturbances | n2=en:tinnitus (in some patients) | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:triangular-shaped ears
n1=en:otoneurologic disturbances | n2=en:triangular-shaped ears | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:unfolded superior helices
n1=en:otoneurologic disturbances | n2=en:unfolded superior helices | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:unravelling of superior helices
n1=en:otoneurologic disturbances | n2=en:unravelling of superior helices | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:vestibular function defect (decreased in some, normal in other patients)
n1=en:otoneurologic disturbances | n2=en:vestibular function defect (decreased in some, normal in other patients) | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
en:wide, flattened earlobes
n1=en:otoneurologic disturbances | n2=en:wide, flattened earlobes | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
lésion traumatique superficielle de l'oreille
n1=en:otoneurologic disturbances | n2=lésion traumatique superficielle de l'oreille | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
surdité héréditaire
n1=en:otoneurologic disturbances | n2=surdité héréditaire | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 29 / 0.674 ->
traumatisme superficiel oreille
n1=en:otoneurologic disturbances | n2=traumatisme superficiel oreille | rel=r_associated | relid=0 | w=29
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:'tilted' ears
n1=en:otoneurologic disturbances | n2=en:'tilted' ears | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:abnormal auricles
n1=en:otoneurologic disturbances | n2=en:abnormal auricles | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:abnormal gap detection
n1=en:otoneurologic disturbances | n2=en:abnormal gap detection | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:abnormal or absent auditory nerve and brainstem responses
n1=en:otoneurologic disturbances | n2=en:abnormal or absent auditory nerve and brainstem responses | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:abnormally formed ears
n1=en:otoneurologic disturbances | n2=en:abnormally formed ears | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:absent cochlear microphonic (in older patients)
n1=en:otoneurologic disturbances | n2=en:absent cochlear microphonic (in older patients) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:absent ipsilateral middle ear muscle reflexes (in older patients)
n1=en:otoneurologic disturbances | n2=en:absent ipsilateral middle ear muscle reflexes (in older patients) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:anteverted pinnae
n1=en:otoneurologic disturbances | n2=en:anteverted pinnae | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:apical cartilage deformity
n1=en:otoneurologic disturbances | n2=en:apical cartilage deformity | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:atrophy of cochlear and vestibular fibrocytes
n1=en:otoneurologic disturbances | n2=en:atrophy of cochlear and vestibular fibrocytes | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:conductive hearing loss (30% of patients)
n1=en:otoneurologic disturbances | n2=en:conductive hearing loss (30% of patients) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:congenital deafness
n1=en:otoneurologic disturbances | n2=en:congenital deafness | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:congenital ear anomaly nos (disorder)
n1=en:otoneurologic disturbances | n2=en:congenital ear anomaly nos (disorder) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:cystic dilatation of cochlea and vestibulum
n1=en:otoneurologic disturbances | n2=en:cystic dilatation of cochlea and vestibulum | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:deafness labyrinthine
n1=en:otoneurologic disturbances | n2=en:deafness labyrinthine | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:deafness, sensorineural (in some patients)
n1=en:otoneurologic disturbances | n2=en:deafness, sensorineural (in some patients) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:deafness, sensorineural, variable
n1=en:otoneurologic disturbances | n2=en:deafness, sensorineural, variable | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation
n1=en:otoneurologic disturbances | n2=en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea
n1=en:otoneurologic disturbances | n2=en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:ear neoplasm
n1=en:otoneurologic disturbances | n2=en:ear neoplasm | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:first branchial arch anomalies
n1=en:otoneurologic disturbances | n2=en:first branchial arch anomalies | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:hearing impairment, mild (2 patients)
n1=en:otoneurologic disturbances | n2=en:hearing impairment, mild (2 patients) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:hearing impairment, sensorineural, fluctuating
n1=en:otoneurologic disturbances | n2=en:hearing impairment, sensorineural, fluctuating | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:hearing loss, late-onset sensorineural, mild-to moderate (less common)
n1=en:otoneurologic disturbances | n2=en:hearing loss, late-onset sensorineural, mild-to moderate (less common) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:hearing loss, prelingual, severe to profound (affecting all frequencies)
n1=en:otoneurologic disturbances | n2=en:hearing loss, prelingual, severe to profound (affecting all frequencies) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:hearing loss, profound congenital sensorineural
n1=en:otoneurologic disturbances | n2=en:hearing loss, profound congenital sensorineural | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies)
n1=en:otoneurologic disturbances | n2=en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:hearing loss, sensorineural (in some patients)
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural (in some patients) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:hearing loss, sensorineural, mid-frequency (in some patients)
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural, mid-frequency (in some patients) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:hearing loss, severe to profound, affecting all frequencies
n1=en:otoneurologic disturbances | n2=en:hearing loss, severe to profound, affecting all frequencies | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:inferior displacement of the ears
n1=en:otoneurologic disturbances | n2=en:inferior displacement of the ears | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:large ear pinnae
n1=en:otoneurologic disturbances | n2=en:large ear pinnae | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:large ears (in some patients)
n1=en:otoneurologic disturbances | n2=en:large ears (in some patients) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:long ear
n1=en:otoneurologic disturbances | n2=en:long ear | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:loss of vestibular reflexes
n1=en:otoneurologic disturbances | n2=en:loss of vestibular reflexes | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:low-set ears (28%)
n1=en:otoneurologic disturbances | n2=en:low-set ears (28%) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:low-set, posteriorly rotated ears
n1=en:otoneurologic disturbances | n2=en:low-set, posteriorly rotated ears | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:microtia (wws)
n1=en:otoneurologic disturbances | n2=en:microtia (wws) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:mild hearing impairment (13%)
n1=en:otoneurologic disturbances | n2=en:mild hearing impairment (13%) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:minor auricular anomalies
n1=en:otoneurologic disturbances | n2=en:minor auricular anomalies | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:mixed hearing loss (50% of patients)
n1=en:otoneurologic disturbances | n2=en:mixed hearing loss (50% of patients) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies
n1=en:otoneurologic disturbances | n2=en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:no auditory brainstem response (abr)
n1=en:otoneurologic disturbances | n2=en:no auditory brainstem response (abr) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:no deafness
n1=en:otoneurologic disturbances | n2=en:no deafness | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:no vestibular dysfunction
n1=en:otoneurologic disturbances | n2=en:no vestibular dysfunction | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:nonprogressive deafness
n1=en:otoneurologic disturbances | n2=en:nonprogressive deafness | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:normal cochlear microphonics
n1=en:otoneurologic disturbances | n2=en:normal cochlear microphonics | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:other auditory injuries
n1=en:otoneurologic disturbances | n2=en:other auditory injuries | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:other symptom/complaint of ear
n1=en:otoneurologic disturbances | n2=en:other symptom/complaint of ear | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:prominent antihelix
n1=en:otoneurologic disturbances | n2=en:prominent antihelix | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:prominent crura
n1=en:otoneurologic disturbances | n2=en:prominent crura | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:protruding ears (in some patients)
n1=en:otoneurologic disturbances | n2=en:protruding ears (in some patients) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:protruding, simple ears
n1=en:otoneurologic disturbances | n2=en:protruding, simple ears | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:recurrent otitis media (18%)
n1=en:otoneurologic disturbances | n2=en:recurrent otitis media (18%) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:recurrent serous otitis
n1=en:otoneurologic disturbances | n2=en:recurrent serous otitis | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:right ear
n1=en:otoneurologic disturbances | n2=en:right ear | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:rudimentary
n1=en:otoneurologic disturbances | n2=en:rudimentary | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:sensorineural hearing loss (1 patient)
n1=en:otoneurologic disturbances | n2=en:sensorineural hearing loss (1 patient) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:sensorineural hearing loss (20% of patients)
n1=en:otoneurologic disturbances | n2=en:sensorineural hearing loss (20% of patients) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:sensorineural hearing loss (early-onset form)
n1=en:otoneurologic disturbances | n2=en:sensorineural hearing loss (early-onset form) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:sensorineural hearing loss, bilateral
n1=en:otoneurologic disturbances | n2=en:sensorineural hearing loss, bilateral | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:sensorineural hearing loss, mild (rare)
n1=en:otoneurologic disturbances | n2=en:sensorineural hearing loss, mild (rare) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:severe narrowing of cartilagenous auditory canal (in homozygotes)
n1=en:otoneurologic disturbances | n2=en:severe narrowing of cartilagenous auditory canal (in homozygotes) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:small auricles
n1=en:otoneurologic disturbances | n2=en:small auricles | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:soft auricles
n1=en:otoneurologic disturbances | n2=en:soft auricles | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:stiff, prominent pinnae
n1=en:otoneurologic disturbances | n2=en:stiff, prominent pinnae | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:structural inner ear abnormalities (in patients with larger deletions)
n1=en:otoneurologic disturbances | n2=en:structural inner ear abnormalities (in patients with larger deletions) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:superficial injury of ear
n1=en:otoneurologic disturbances | n2=en:superficial injury of ear | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:superiorly displaced ears
n1=en:otoneurologic disturbances | n2=en:superiorly displaced ears | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:tinnitus (rare)
n1=en:otoneurologic disturbances | n2=en:tinnitus (rare) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:underfolded helix
n1=en:otoneurologic disturbances | n2=en:underfolded helix | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:uplift of earlobes (in some patients)
n1=en:otoneurologic disturbances | n2=en:uplift of earlobes (in some patients) | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:uplifted earlobes
n1=en:otoneurologic disturbances | n2=en:uplifted earlobes | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:upsloping audiograms
n1=en:otoneurologic disturbances | n2=en:upsloping audiograms | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 28 / 0.651 ->
en:wide bulbous internal auditory meatus
n1=en:otoneurologic disturbances | n2=en:wide bulbous internal auditory meatus | rel=r_associated | relid=0 | w=28
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:abnormal brain auditory evoked responses (baer)
n1=en:otoneurologic disturbances | n2=en:abnormal brain auditory evoked responses (baer) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:abnormal bridge connecting the crus of the helix and antihelix
n1=en:otoneurologic disturbances | n2=en:abnormal bridge connecting the crus of the helix and antihelix | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:abnormal folded pinna
n1=en:otoneurologic disturbances | n2=en:abnormal folded pinna | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:absence of earlobe
n1=en:otoneurologic disturbances | n2=en:absence of earlobe | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:absent brainstem auditory-evoked responses
n1=en:otoneurologic disturbances | n2=en:absent brainstem auditory-evoked responses | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:absent external auditory canals
n1=en:otoneurologic disturbances | n2=en:absent external auditory canals | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:absent stapedial reflex
n1=en:otoneurologic disturbances | n2=en:absent stapedial reflex | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:absent stapedial reflexes or intraoperative stapes immobility
n1=en:otoneurologic disturbances | n2=en:absent stapedial reflexes or intraoperative stapes immobility | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:affects all frequencies
n1=en:otoneurologic disturbances | n2=en:affects all frequencies | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:anterior creases of earlobe
n1=en:otoneurologic disturbances | n2=en:anterior creases of earlobe | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:audiogram is gently sloping or flat
n1=en:otoneurologic disturbances | n2=en:audiogram is gently sloping or flat | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile)
n1=en:otoneurologic disturbances | n2=en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:cochlear malformation defect (mondini dysplasia) (less common)
n1=en:otoneurologic disturbances | n2=en:cochlear malformation defect (mondini dysplasia) (less common) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:congenital absence of external ear
n1=en:otoneurologic disturbances | n2=en:congenital absence of external ear | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:cupped pinna
n1=en:otoneurologic disturbances | n2=en:cupped pinna | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:deafness, congenital sensorineural, severe to profound
n1=en:otoneurologic disturbances | n2=en:deafness, congenital sensorineural, severe to profound | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:deafness, early-onset mixed conductive and sensorineural
n1=en:otoneurologic disturbances | n2=en:deafness, early-onset mixed conductive and sensorineural | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:deafness, profound congenital sensorineural
n1=en:otoneurologic disturbances | n2=en:deafness, profound congenital sensorineural | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:deafness, sensorineural (45%)
n1=en:otoneurologic disturbances | n2=en:deafness, sensorineural (45%) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:deafness, sensorineural, mild (rare)
n1=en:otoneurologic disturbances | n2=en:deafness, sensorineural, mild (rare) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:deafness, sensorineural, profound (prelingual onset)
n1=en:otoneurologic disturbances | n2=en:deafness, sensorineural, profound (prelingual onset) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:deep-set ears
n1=en:otoneurologic disturbances | n2=en:deep-set ears | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:deficient auricle
n1=en:otoneurologic disturbances | n2=en:deficient auricle | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:downward sloping audiogram
n1=en:otoneurologic disturbances | n2=en:downward sloping audiogram | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:dysplastic ears (in some patients)
n1=en:otoneurologic disturbances | n2=en:dysplastic ears (in some patients) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:ear tag
n1=en:otoneurologic disturbances | n2=en:ear tag | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:external ear defects (47%)
n1=en:otoneurologic disturbances | n2=en:external ear defects (47%) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:hearing impairment (in some patients)
n1=en:otoneurologic disturbances | n2=en:hearing impairment (in some patients) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:hearing loss (affecting all frequencies), moderate to severe
n1=en:otoneurologic disturbances | n2=en:hearing loss (affecting all frequencies), moderate to severe | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:hearing loss (in some patients)
n1=en:otoneurologic disturbances | n2=en:hearing loss (in some patients) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:hearing loss begins with loss of high frequencies
n1=en:otoneurologic disturbances | n2=en:hearing loss begins with loss of high frequencies | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:hearing loss, bilateral sensorineural (profound)
n1=en:otoneurologic disturbances | n2=en:hearing loss, bilateral sensorineural (profound) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies)
n1=en:otoneurologic disturbances | n2=en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:hearing loss, sensorineural (bilateral, prelingual)
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural (bilateral, prelingual) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:hearing loss, sensorineural (in 1 ashkenazi patient)
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural (in 1 ashkenazi patient) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:hearing loss, sensorineural (in patients with larger deletions)
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural (in patients with larger deletions) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:hearing loss, sensorineural (in some)
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural (in some) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:hearing loss, sensorineural, due to auditory neuropathy
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural, due to auditory neuropathy | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected)
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:hearing threshold at or above 90 db at all frequencies tested (0.25-8.0 khz)
n1=en:otoneurologic disturbances | n2=en:hearing threshold at or above 90 db at all frequencies tested (0.25-8.0 khz) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:high-frequency tinnitus at onset
n1=en:otoneurologic disturbances | n2=en:high-frequency tinnitus at onset | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:hyperacusis
n1=en:otoneurologic disturbances | n2=en:hyperacusis | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:hypoplastic ear lobes
n1=en:otoneurologic disturbances | n2=en:hypoplastic ear lobes | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:internal auditory canal hypoplasia
n1=en:otoneurologic disturbances | n2=en:internal auditory canal hypoplasia | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:large anteverted ears
n1=en:otoneurologic disturbances | n2=en:large anteverted ears | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:low-set and rotated ears
n1=en:otoneurologic disturbances | n2=en:low-set and rotated ears | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:macrotia
n1=en:otoneurologic disturbances | n2=en:macrotia | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:malformations of the auditory ossicles
n1=en:otoneurologic disturbances | n2=en:malformations of the auditory ossicles | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:mondini defect
n1=en:otoneurologic disturbances | n2=en:mondini defect | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:narrow intertragic notch
n1=en:otoneurologic disturbances | n2=en:narrow intertragic notch | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:normal middle ear pressures on tympanometry
n1=en:otoneurologic disturbances | n2=en:normal middle ear pressures on tympanometry | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:otitis externa, recurrent, due to infection with staphylococcus aureus
n1=en:otoneurologic disturbances | n2=en:otitis externa, recurrent, due to infection with staphylococcus aureus | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:pointed upper helix
n1=en:otoneurologic disturbances | n2=en:pointed upper helix | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:poorly formed ears
n1=en:otoneurologic disturbances | n2=en:poorly formed ears | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:poorly formed pinnae
n1=en:otoneurologic disturbances | n2=en:poorly formed pinnae | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:posterior helical indentations
n1=en:otoneurologic disturbances | n2=en:posterior helical indentations | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:posteriorly rotated ears (1/4 patients)
n1=en:otoneurologic disturbances | n2=en:posteriorly rotated ears (1/4 patients) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:preauricular pits (70-80% of patients)
n1=en:otoneurologic disturbances | n2=en:preauricular pits (70-80% of patients) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:preauricular skin tags (in some patients)
n1=en:otoneurologic disturbances | n2=en:preauricular skin tags (in some patients) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:profound deafness
n1=en:otoneurologic disturbances | n2=en:profound deafness | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:progressive high-frequency hearing loss (onset 20-30 years)
n1=en:otoneurologic disturbances | n2=en:progressive high-frequency hearing loss (onset 20-30 years) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:pseudomembranous inflammation of the middle ear
n1=en:otoneurologic disturbances | n2=en:pseudomembranous inflammation of the middle ear | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:pulsatile tinnitus (tympanic paraganglioma)
n1=en:otoneurologic disturbances | n2=en:pulsatile tinnitus (tympanic paraganglioma) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:sensorineural deafness (onset in the second decade in 25 to 30% of patients)
n1=en:otoneurologic disturbances | n2=en:sensorineural deafness (onset in the second decade in 25 to 30% of patients) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:shallow skin dimple on posterior surface of ear
n1=en:otoneurologic disturbances | n2=en:shallow skin dimple on posterior surface of ear | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:small external auditory meatus
n1=en:otoneurologic disturbances | n2=en:small external auditory meatus | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:stenotic ear canals (30%)
n1=en:otoneurologic disturbances | n2=en:stenotic ear canals (30%) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:strabismus (in some patients)
n1=en:otoneurologic disturbances | n2=en:strabismus (in some patients) | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:tinnitus
n1=en:otoneurologic disturbances | n2=en:tinnitus | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:unilateral external ear deformity
n1=en:otoneurologic disturbances | n2=en:unilateral external ear deformity | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
en:vertigo
n1=en:otoneurologic disturbances | n2=en:vertigo | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 27 / 0.628 ->
surdité du labyrinthe
n1=en:otoneurologic disturbances | n2=surdité du labyrinthe | rel=r_associated | relid=0 | w=27
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:abnormal ears
n1=en:otoneurologic disturbances | n2=en:abnormal ears | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:abnormal speech discrimination
n1=en:otoneurologic disturbances | n2=en:abnormal speech discrimination | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:abnormality of the middle ear
n1=en:otoneurologic disturbances | n2=en:abnormality of the middle ear | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:absent helices, bilaterally
n1=en:otoneurologic disturbances | n2=en:absent helices, bilaterally | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:absent or decreased auditory brainstem responses
n1=en:otoneurologic disturbances | n2=en:absent or decreased auditory brainstem responses | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:atresia of the external auditory canal
n1=en:otoneurologic disturbances | n2=en:atresia of the external auditory canal | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:attached ear lobes
n1=en:otoneurologic disturbances | n2=en:attached ear lobes | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:attached ear lobules
n1=en:otoneurologic disturbances | n2=en:attached ear lobules | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:auditory impairment
n1=en:otoneurologic disturbances | n2=en:auditory impairment | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:bilateral hypoplastic cochlea
n1=en:otoneurologic disturbances | n2=en:bilateral hypoplastic cochlea | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:conductive hearing loss
n1=en:otoneurologic disturbances | n2=en:conductive hearing loss | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:congenital sensorineural hearing loss
n1=en:otoneurologic disturbances | n2=en:congenital sensorineural hearing loss | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:crumpled ear (76%)
n1=en:otoneurologic disturbances | n2=en:crumpled ear (76%) | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:deafness (in some patients)
n1=en:otoneurologic disturbances | n2=en:deafness (in some patients) | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:deafness, nonprogressive, moderate
n1=en:otoneurologic disturbances | n2=en:deafness, nonprogressive, moderate | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:ear
n1=en:otoneurologic disturbances | n2=en:ear | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:ear dimple
n1=en:otoneurologic disturbances | n2=en:ear dimple | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:flat or shallow u-shaped audiogram
n1=en:otoneurologic disturbances | n2=en:flat or shallow u-shaped audiogram | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:flattened antihelix
n1=en:otoneurologic disturbances | n2=en:flattened antihelix | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:floppy ears
n1=en:otoneurologic disturbances | n2=en:floppy ears | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:hearing impairment
n1=en:otoneurologic disturbances | n2=en:hearing impairment | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:hearing loss (1 patient)
n1=en:otoneurologic disturbances | n2=en:hearing loss (1 patient) | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:hearing loss has been reported in some adults with severe disease
n1=en:otoneurologic disturbances | n2=en:hearing loss has been reported in some adults with severe disease | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:hearing loss, congenital sensorineural, severe to profound
n1=en:otoneurologic disturbances | n2=en:hearing loss, congenital sensorineural, severe to profound | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:hearing loss, congenital, profound (250-8,000 hz)
n1=en:otoneurologic disturbances | n2=en:hearing loss, congenital, profound (250-8,000 hz) | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:hearing loss, high-frequency (onset in childhood-adolescence)
n1=en:otoneurologic disturbances | n2=en:hearing loss, high-frequency (onset in childhood-adolescence) | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies)
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies) | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:hypoacusia (1 patient)
n1=en:otoneurologic disturbances | n2=en:hypoacusia (1 patient) | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:hypoplasia of the cochlea
n1=en:otoneurologic disturbances | n2=en:hypoplasia of the cochlea | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies
n1=en:otoneurologic disturbances | n2=en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:large pinnae
n1=en:otoneurologic disturbances | n2=en:large pinnae | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:large, dysmorphic ears
n1=en:otoneurologic disturbances | n2=en:large, dysmorphic ears | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:large, low-set ears
n1=en:otoneurologic disturbances | n2=en:large, low-set ears | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:large, low-set ears (uncommon)
n1=en:otoneurologic disturbances | n2=en:large, low-set ears (uncommon) | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:large, prominent ears (59%)
n1=en:otoneurologic disturbances | n2=en:large, prominent ears (59%) | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:long and prominent ear crus
n1=en:otoneurologic disturbances | n2=en:long and prominent ear crus | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:loss of hearing (45%)
n1=en:otoneurologic disturbances | n2=en:loss of hearing (45%) | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:malformed ossicular chain
n1=en:otoneurologic disturbances | n2=en:malformed ossicular chain | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:mild cochlear hearing loss (1 patient)
n1=en:otoneurologic disturbances | n2=en:mild cochlear hearing loss (1 patient) | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:near-stenosis of bony portion of auditory canal (in homozygotes)
n1=en:otoneurologic disturbances | n2=en:near-stenosis of bony portion of auditory canal (in homozygotes) | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:no reproducible waves i, iii, or v at high intensities
n1=en:otoneurologic disturbances | n2=en:no reproducible waves i, iii, or v at high intensities | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:normal static compliance on tympanometry
n1=en:otoneurologic disturbances | n2=en:normal static compliance on tympanometry | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:otitis media, chronic (rare)
n1=en:otoneurologic disturbances | n2=en:otitis media, chronic (rare) | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:partial aplasia of external auditory canal ending in blind fistula (in some patients)
n1=en:otoneurologic disturbances | n2=en:partial aplasia of external auditory canal ending in blind fistula (in some patients) | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:progressive mixed conductive and sensorineural hearing loss
n1=en:otoneurologic disturbances | n2=en:progressive mixed conductive and sensorineural hearing loss | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:prominent antitragus (in some patients)
n1=en:otoneurologic disturbances | n2=en:prominent antitragus (in some patients) | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:prominent earlobes (in some patients)
n1=en:otoneurologic disturbances | n2=en:prominent earlobes (in some patients) | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:recurrent otitis media in infancy and childhood
n1=en:otoneurologic disturbances | n2=en:recurrent otitis media in infancy and childhood | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:rudimentary ear
n1=en:otoneurologic disturbances | n2=en:rudimentary ear | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:sensorineural hearing loss (rare)
n1=en:otoneurologic disturbances | n2=en:sensorineural hearing loss (rare) | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:sensorineural hearing loss (uncommon)
n1=en:otoneurologic disturbances | n2=en:sensorineural hearing loss (uncommon) | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:sensorineural, conductive, or mixed hearing loss
n1=en:otoneurologic disturbances | n2=en:sensorineural, conductive, or mixed hearing loss | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:small external auditory canals
n1=en:otoneurologic disturbances | n2=en:small external auditory canals | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:small triangular pinnae
n1=en:otoneurologic disturbances | n2=en:small triangular pinnae | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:squared-off superior helices
n1=en:otoneurologic disturbances | n2=en:squared-off superior helices | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:thick earlobes
n1=en:otoneurologic disturbances | n2=en:thick earlobes | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:tinnitus (variable)
n1=en:otoneurologic disturbances | n2=en:tinnitus (variable) | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:tympanic membrane perforation
n1=en:otoneurologic disturbances | n2=en:tympanic membrane perforation | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:vertigo, single occurrence (in 2 patients)
n1=en:otoneurologic disturbances | n2=en:vertigo, single occurrence (in 2 patients) | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:vestibular anomalies (less common)
n1=en:otoneurologic disturbances | n2=en:vestibular anomalies (less common) | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:vestibular areflexia, complete
n1=en:otoneurologic disturbances | n2=en:vestibular areflexia, complete | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:vestibular dysfunction
n1=en:otoneurologic disturbances | n2=en:vestibular dysfunction | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
en:vestibular hypofunction (rare)
n1=en:otoneurologic disturbances | n2=en:vestibular hypofunction (rare) | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
perte d'audition sensorineurale
n1=en:otoneurologic disturbances | n2=perte d'audition sensorineurale | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 26 / 0.605 ->
surdité congénitale
n1=en:otoneurologic disturbances | n2=surdité congénitale | rel=r_associated | relid=0 | w=26
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
déficience auditive
n1=en:otoneurologic disturbances | n2=déficience auditive | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
en:auditory canal stenosis
n1=en:otoneurologic disturbances | n2=en:auditory canal stenosis | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
en:balance problem
n1=en:otoneurologic disturbances | n2=en:balance problem | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
en:chronic otitis media (25%)
n1=en:otoneurologic disturbances | n2=en:chronic otitis media (25%) | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
en:cutlet
n1=en:otoneurologic disturbances | n2=en:cutlet | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
en:disorder of equilibrium
n1=en:otoneurologic disturbances | n2=en:disorder of equilibrium | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
en:dysplastic ears (jbts)
n1=en:otoneurologic disturbances | n2=en:dysplastic ears (jbts) | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
en:ENT doctor
n1=en:otoneurologic disturbances | n2=en:ENT doctor | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
en:ENT specialist
n1=en:otoneurologic disturbances | n2=en:ENT specialist | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
en:hearing impairment (1 patient)
n1=en:otoneurologic disturbances | n2=en:hearing impairment (1 patient) | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
en:hearing impairment, progressive (family a)
n1=en:otoneurologic disturbances | n2=en:hearing impairment, progressive (family a) | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
en:hearing loss (in 2 members of 1 family)
n1=en:otoneurologic disturbances | n2=en:hearing loss (in 2 members of 1 family) | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
en:hearing loss, sensorineural, progressive (all frequencies)
n1=en:otoneurologic disturbances | n2=en:hearing loss, sensorineural, progressive (all frequencies) | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
en:hereditary deafness
n1=en:otoneurologic disturbances | n2=en:hereditary deafness | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
en:microtia (in some patients)
n1=en:otoneurologic disturbances | n2=en:microtia (in some patients) | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
en:mild dysplasia of concha, unilateral
n1=en:otoneurologic disturbances | n2=en:mild dysplasia of concha, unilateral | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
en:no vestibular symptoms
n1=en:otoneurologic disturbances | n2=en:no vestibular symptoms | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
en:nose and throat specialist
n1=en:otoneurologic disturbances | n2=en:nose and throat specialist | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
en:otitis with effusion
n1=en:otoneurologic disturbances | n2=en:otitis with effusion | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
en:problem with balance
n1=en:otoneurologic disturbances | n2=en:problem with balance | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
en:rotary vertigo
n1=en:otoneurologic disturbances | n2=en:rotary vertigo | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
en:serous otitis
n1=en:otoneurologic disturbances | n2=en:serous otitis | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
en:tinnitus, bilateral (in some patients)
n1=en:otoneurologic disturbances | n2=en:tinnitus, bilateral (in some patients) | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
état nébuleux
n1=en:otoneurologic disturbances | n2=état nébuleux | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
état vertigineux
n1=en:otoneurologic disturbances | n2=état vertigineux | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
étourdissement
n1=en:otoneurologic disturbances | n2=étourdissement | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
hyperacousie
n1=en:otoneurologic disturbances | n2=hyperacousie | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
hyperacousies
n1=en:otoneurologic disturbances | n2=hyperacousies | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
hyperacusie
n1=en:otoneurologic disturbances | n2=hyperacusie | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
médecin ORL
n1=en:otoneurologic disturbances | n2=médecin ORL | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
otite moyenne séreuse
n1=en:otoneurologic disturbances | n2=otite moyenne séreuse | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
otite séreuse
n1=en:otoneurologic disturbances | n2=otite séreuse | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
otite séromuqueuse
n1=en:otoneurologic disturbances | n2=otite séromuqueuse | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
oto-rhino
n1=en:otoneurologic disturbances | n2=oto-rhino | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
oto-rhino-laryngologiste
n1=en:otoneurologic disturbances | n2=oto-rhino-laryngologiste | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
otorhinolaryngologiste
n1=en:otoneurologic disturbances | n2=otorhinolaryngologiste | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
pavillon de l'oreille de morphologie rudimentaire
n1=en:otoneurologic disturbances | n2=pavillon de l'oreille de morphologie rudimentaire | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
sensation de rotation
n1=en:otoneurologic disturbances | n2=sensation de rotation | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
sensation de tournoiement
n1=en:otoneurologic disturbances | n2=sensation de tournoiement | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
sensation rotatoire
n1=en:otoneurologic disturbances | n2=sensation rotatoire | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
sensation vertigineuse
n1=en:otoneurologic disturbances | n2=sensation vertigineuse | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
sténose du canal auriculaire
n1=en:otoneurologic disturbances | n2=sténose du canal auriculaire | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
surdi-mutité
n1=en:otoneurologic disturbances | n2=surdi-mutité | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
tête pivotante
n1=en:otoneurologic disturbances | n2=tête pivotante | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
trouble de l'équilibre
n1=en:otoneurologic disturbances | n2=trouble de l'équilibre | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
vertige
n1=en:otoneurologic disturbances | n2=vertige | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
vertige rotatoire
n1=en:otoneurologic disturbances | n2=vertige rotatoire | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
vertige subjectif
n1=en:otoneurologic disturbances | n2=vertige subjectif | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
vertigo
n1=en:otoneurologic disturbances | n2=vertigo | rel=r_associated | relid=0 | w=20
- en:otoneurologic disturbances --
r_associated #0: 20 / 0.465 ->
vertigo rotatoire
n1=en:otoneurologic disturbances | n2=vertigo rotatoire | rel=r_associated | relid=0 | w=20
| ≈ 781 relations entrantes
- en:congenital deafness ---
r_associated #0: 300 -->
en:otoneurologic disturbances
n1=en:congenital deafness | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=300
- surdité congénitale ---
r_associated #0: 297 -->
en:otoneurologic disturbances
n1=surdité congénitale | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=297
- surdité héréditaire ---
r_associated #0: 295 -->
en:otoneurologic disturbances
n1=surdité héréditaire | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=295
- surdité du labyrinthe ---
r_associated #0: 271 -->
en:otoneurologic disturbances
n1=surdité du labyrinthe | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=271
- en:deafness labyrinthine ---
r_associated #0: 270 -->
en:otoneurologic disturbances
n1=en:deafness labyrinthine | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=270
- sensation vertigineuse ---
r_associated #0: 250 -->
en:otoneurologic disturbances
n1=sensation vertigineuse | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=250
- vertige subjectif ---
r_associated #0: 245 -->
en:otoneurologic disturbances
n1=vertige subjectif | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=245
- vertigo rotatoire ---
r_associated #0: 245 -->
en:otoneurologic disturbances
n1=vertigo rotatoire | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=245
- vertige rotatoire ---
r_associated #0: 235 -->
en:otoneurologic disturbances
n1=vertige rotatoire | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=235
- sensation de rotation ---
r_associated #0: 234 -->
en:otoneurologic disturbances
n1=sensation de rotation | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=234
- sensation de tournoiement ---
r_associated #0: 232 -->
en:otoneurologic disturbances
n1=sensation de tournoiement | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=232
- tête pivotante ---
r_associated #0: 225 -->
en:otoneurologic disturbances
n1=tête pivotante | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=225
- état nébuleux ---
r_associated #0: 220 -->
en:otoneurologic disturbances
n1=état nébuleux | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=220
- état vertigineux ---
r_associated #0: 220 -->
en:otoneurologic disturbances
n1=état vertigineux | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=220
- sensation rotatoire ---
r_associated #0: 216 -->
en:otoneurologic disturbances
n1=sensation rotatoire | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=216
- otite moyenne séreuse ---
r_associated #0: 200 -->
en:otoneurologic disturbances
n1=otite moyenne séreuse | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=200
- en:serous otitis media ---
r_associated #0: 197 -->
en:otoneurologic disturbances
n1=en:serous otitis media | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=197
- en:sensorineural hearing loss ---
r_associated #0: 185 -->
en:otoneurologic disturbances
n1=en:sensorineural hearing loss | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=185
- perte d'audition sensorineurale ---
r_associated #0: 184 -->
en:otoneurologic disturbances
n1=perte d'audition sensorineurale | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=184
- en:vertigo ---
r_associated #0: 169 -->
en:otoneurologic disturbances
n1=en:vertigo | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=169
- en:dizziness ---
r_associated #0: 165 -->
en:otoneurologic disturbances
n1=en:dizziness | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=165
- vertigo ---
r_associated #0: 130 -->
en:otoneurologic disturbances
n1=vertigo | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=130
- en:balance problem ---
r_associated #0: 115 -->
en:otoneurologic disturbances
n1=en:balance problem | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=115
- en:disorder of equilibrium ---
r_associated #0: 115 -->
en:otoneurologic disturbances
n1=en:disorder of equilibrium | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=115
- en:problem with balance ---
r_associated #0: 115 -->
en:otoneurologic disturbances
n1=en:problem with balance | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=115
- trouble de l'équilibre ---
r_associated #0: 115 -->
en:otoneurologic disturbances
n1=trouble de l'équilibre | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=115
- vertige ---
r_associated #0: 95 -->
en:otoneurologic disturbances
n1=vertige | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=95
- en:secretory otitis media ---
r_associated #0: 76 -->
en:otoneurologic disturbances
n1=en:secretory otitis media | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=76
- étourdissement ---
r_associated #0: 76 -->
en:otoneurologic disturbances
n1=étourdissement | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=76
- otite séromuqueuse ---
r_associated #0: 73 -->
en:otoneurologic disturbances
n1=otite séromuqueuse | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=73
- en:stenosis of external auditory canal ---
r_associated #0: 58 -->
en:otoneurologic disturbances
n1=en:stenosis of external auditory canal | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=58
- sténose du canal auriculaire ---
r_associated #0: 55 -->
en:otoneurologic disturbances
n1=sténose du canal auriculaire | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=55
- en:ENT specialist ---
r_associated #0: 50 -->
en:otoneurologic disturbances
n1=en:ENT specialist | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=50
- oto-rhino ---
r_associated #0: 50 -->
en:otoneurologic disturbances
n1=oto-rhino | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=50
- oto-rhino-laryngologiste ---
r_associated #0: 50 -->
en:otoneurologic disturbances
n1=oto-rhino-laryngologiste | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=50
- traumatisme superficiel oreille ---
r_associated #0: 50 -->
en:otoneurologic disturbances
n1=traumatisme superficiel oreille | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=50
- en:hereditary deafness ---
r_associated #0: 49 -->
en:otoneurologic disturbances
n1=en:hereditary deafness | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=49
- en:nose and throat specialist ---
r_associated #0: 49 -->
en:otoneurologic disturbances
n1=en:nose and throat specialist | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=49
- lésion traumatique superficielle de l'oreille ---
r_associated #0: 47 -->
en:otoneurologic disturbances
n1=lésion traumatique superficielle de l'oreille | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=47
- otorhinolaryngologiste ---
r_associated #0: 47 -->
en:otoneurologic disturbances
n1=otorhinolaryngologiste | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=47
- en:superficial injury of ear ---
r_associated #0: 45 -->
en:otoneurologic disturbances
n1=en:superficial injury of ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=45
- pavillon de l'oreille de morphologie rudimentaire ---
r_associated #0: 44 -->
en:otoneurologic disturbances
n1=pavillon de l'oreille de morphologie rudimentaire | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=44
- en:abnormal or absent auditory nerve and brainstem responses ---
r_associated #0: 43 -->
en:otoneurologic disturbances
n1=en:abnormal or absent auditory nerve and brainstem responses | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=43
- en:ear ---
r_associated #0: 43 -->
en:otoneurologic disturbances
n1=en:ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=43
- en:hearing loss, conductive (in some patients) ---
r_associated #0: 43 -->
en:otoneurologic disturbances
n1=en:hearing loss, conductive (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=43
- en:pigmentation of the ear cartilage ---
r_associated #0: 43 -->
en:otoneurologic disturbances
n1=en:pigmentation of the ear cartilage | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=43
- en:prominent helices ---
r_associated #0: 43 -->
en:otoneurologic disturbances
n1=en:prominent helices | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=43
- en:protruding ears (in some patients) ---
r_associated #0: 43 -->
en:otoneurologic disturbances
n1=en:protruding ears (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=43
- en:affects mid- to high-frequencies ---
r_associated #0: 42 -->
en:otoneurologic disturbances
n1=en:affects mid- to high-frequencies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=42
- en:first branchial arch anomalies ---
r_associated #0: 42 -->
en:otoneurologic disturbances
n1=en:first branchial arch anomalies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=42
- en:hearing loss, profound congenital sensorineural ---
r_associated #0: 42 -->
en:otoneurologic disturbances
n1=en:hearing loss, profound congenital sensorineural | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=42
- en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural ---
r_associated #0: 42 -->
en:otoneurologic disturbances
n1=en:hearing loss, unilateral or bilateral, conductive or mixed conductive/sensorineural | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=42
- en:oae responses may decrease with age or use of hearing aids ---
r_associated #0: 42 -->
en:otoneurologic disturbances
n1=en:oae responses may decrease with age or use of hearing aids | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=42
- en:prominent ears (in some patients) ---
r_associated #0: 42 -->
en:otoneurologic disturbances
n1=en:prominent ears (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=42
- en:rotary vertigo ---
r_associated #0: 42 -->
en:otoneurologic disturbances
n1=en:rotary vertigo | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=42
- déficience auditive ---
r_associated #0: 41 -->
en:otoneurologic disturbances
n1=déficience auditive | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=41
- en:cystic dilatation of cochlea and vestibulum ---
r_associated #0: 41 -->
en:otoneurologic disturbances
n1=en:cystic dilatation of cochlea and vestibulum | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=41
- en:deafness, sensorineural (45%) ---
r_associated #0: 41 -->
en:otoneurologic disturbances
n1=en:deafness, sensorineural (45%) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=41
- en:ossified pinnae ---
r_associated #0: 41 -->
en:otoneurologic disturbances
n1=en:ossified pinnae | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=41
- en:recurrent ear infections ---
r_associated #0: 41 -->
en:otoneurologic disturbances
n1=en:recurrent ear infections | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=41
- en:simple ear ---
r_associated #0: 41 -->
en:otoneurologic disturbances
n1=en:simple ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=41
- en:ear tag ---
r_associated #0: 40 -->
en:otoneurologic disturbances
n1=en:ear tag | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=40
- en:sensorineural hearing loss, progressive bilateral postlingual ---
r_associated #0: 40 -->
en:otoneurologic disturbances
n1=en:sensorineural hearing loss, progressive bilateral postlingual | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=40
- en:simple ear structure ---
r_associated #0: 40 -->
en:otoneurologic disturbances
n1=en:simple ear structure | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=40
- en:abnormally formed ears ---
r_associated #0: 39 -->
en:otoneurologic disturbances
n1=en:abnormally formed ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=39
- en:anterior creases of earlobe ---
r_associated #0: 39 -->
en:otoneurologic disturbances
n1=en:anterior creases of earlobe | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=39
- en:hearing impairment ---
r_associated #0: 39 -->
en:otoneurologic disturbances
n1=en:hearing impairment | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=39
- en:prominent antitragus ---
r_associated #0: 39 -->
en:otoneurologic disturbances
n1=en:prominent antitragus | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=39
- en:bilateral sensorineural hearing loss (in some patients) ---
r_associated #0: 38 -->
en:otoneurologic disturbances
n1=en:bilateral sensorineural hearing loss (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=38
- en:deafness, profound congenital sensorineural ---
r_associated #0: 38 -->
en:otoneurologic disturbances
n1=en:deafness, profound congenital sensorineural | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=38
- en:prominent ear ---
r_associated #0: 38 -->
en:otoneurologic disturbances
n1=en:prominent ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=38
- en:tinnitus (in some patients) ---
r_associated #0: 38 -->
en:otoneurologic disturbances
n1=en:tinnitus (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=38
- surdimutité ---
r_associated #0: 38 -->
en:otoneurologic disturbances
n1=surdimutité | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=38
- en:hearing loss, sensorineural (reported in 1 patient) ---
r_associated #0: 37 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural (reported in 1 patient) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=37
- en:minor ear anomalies (in some patients) ---
r_associated #0: 37 -->
en:otoneurologic disturbances
n1=en:minor ear anomalies (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=37
- en:narrowed external ear canal (30% of patients) ---
r_associated #0: 37 -->
en:otoneurologic disturbances
n1=en:narrowed external ear canal (30% of patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=37
- en:organ of corti degeneration ---
r_associated #0: 37 -->
en:otoneurologic disturbances
n1=en:organ of corti degeneration | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=37
- en:sensorineural, conductive, or mixed hearing loss ---
r_associated #0: 37 -->
en:otoneurologic disturbances
n1=en:sensorineural, conductive, or mixed hearing loss | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=37
- en:severe narrowing of cartilagenous auditory canal ---
r_associated #0: 37 -->
en:otoneurologic disturbances
n1=en:severe narrowing of cartilagenous auditory canal | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=37
- en:nonprogressive deafness ---
r_associated #0: 36 -->
en:otoneurologic disturbances
n1=en:nonprogressive deafness | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=36
- en:normal cochlear microphonics ---
r_associated #0: 36 -->
en:otoneurologic disturbances
n1=en:normal cochlear microphonics | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=36
- en:small triangular pinnae ---
r_associated #0: 36 -->
en:otoneurologic disturbances
n1=en:small triangular pinnae | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=36
- en:thickened lobes ---
r_associated #0: 36 -->
en:otoneurologic disturbances
n1=en:thickened lobes | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=36
- en:a subset of patients have hearing loss ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:a subset of patients have hearing loss | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:abnormality of the pinna ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:abnormality of the pinna | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:absent helices, bilaterally ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:absent helices, bilaterally | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:affects all frequencies ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:affects all frequencies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:audiogram may be ascending ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:audiogram may be ascending | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:aural atresia, congenital ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:aural atresia, congenital | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:bilateral dys-synchronized auditory brainstem responses ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:bilateral dys-synchronized auditory brainstem responses | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:brainstem auditory evoked potentials (baeps) suggest peripheral lesion | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:congenital sensorineural hearing loss ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:congenital sensorineural hearing loss | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:deafness in 30-50% of patients with skull involvement ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:deafness in 30-50% of patients with skull involvement | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:deafness, secondary to cranial hyperostosis ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:deafness, secondary to cranial hyperostosis | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:deafness, sensorineural, mild (rare) ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:deafness, sensorineural, mild (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:downward sloping audiogram ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:downward sloping audiogram | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:excessive cerumen ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:excessive cerumen | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:hearing loss (in some patients) ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:hearing loss (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:hearing loss, conductive or mixed ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:hearing loss, conductive or mixed | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural (in patients with larger deletions) ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural (in patients with larger deletions) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:hearing loss, sensorineural, progressive (all frequencies) ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural, progressive (all frequencies) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:hypoplastic, overfolded helices ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:hypoplastic, overfolded helices | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:impaired tympanic membrane mobility ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:impaired tympanic membrane mobility | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:internal auditory canal hypoplasia ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:internal auditory canal hypoplasia | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:large ears (37%) ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:large ears (37%) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:low-set ears (3 patients) ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:low-set ears (3 patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:mondini malformation ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:mondini malformation | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:morphological abnormality of the middle ear ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:morphological abnormality of the middle ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:narrow auditory canals (rare) ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:narrow auditory canals (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:partial hearing loss ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:partial hearing loss | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:pre- and post-auricular skin or cartilaginous tags ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:pre- and post-auricular skin or cartilaginous tags | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:progressive conductive hearing impairment ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:progressive conductive hearing impairment | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:prominent ears (rare) ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:prominent ears (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:recurrent otitis ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:recurrent otitis | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:retroverted ears ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:retroverted ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:sensorineural deafness (onset in the second decade in 25 to 30% of patients) ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:sensorineural deafness (onset in the second decade in 25 to 30% of patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:sensorineural hearing loss (less common) ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:sensorineural hearing loss (less common) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:small ears (female) ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:small ears (female) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:superior semicircular canal dehiscence syndrome ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:superior semicircular canal dehiscence syndrome | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:tinnitus (rare) ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:tinnitus (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:underdeveloped tragus ---
r_associated #0: 35 -->
en:otoneurologic disturbances
n1=en:underdeveloped tragus | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=35
- en:abnormal auditory temporal processes ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:abnormal auditory temporal processes | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:abnormality of the helix ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:abnormality of the helix | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:absent auditory canals (wws) ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:absent auditory canals (wws) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:absent distortion product otoacoustic emissions (oaes) ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:absent distortion product otoacoustic emissions (oaes) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:atretic ear canals ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:atretic ear canals | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:deafness (in 1 of 2 families) ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:deafness (in 1 of 2 families) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:decreased or absent brainstem auditory evoked potentials (baep) of waves iii-v | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:dilatated internal auditory canal ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:dilatated internal auditory canal | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:hearing impairment (in 1/4 patients) ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:hearing impairment (in 1/4 patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:hearing loss (in 2 members of 1 family) ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:hearing loss (in 2 members of 1 family) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:hearing loss, bilateral progressive post-lingual ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:hearing loss, bilateral progressive post-lingual | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:hearing loss, bilateral sensorineural (profound) ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:hearing loss, bilateral sensorineural (profound) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:hearing loss, high-frequency (onset in childhood-adolescence) ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:hearing loss, high-frequency (onset in childhood-adolescence) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:hearing loss, progressive (in some patients) ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:hearing loss, progressive (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:high-frequency tinnitus at onset ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:high-frequency tinnitus at onset | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:hypertrophic auricular cartilage ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:hypertrophic auricular cartilage | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:large ear pinnae ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:large ear pinnae | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:large prominent ears ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:large prominent ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:loss of high frequencies at onset ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:loss of high frequencies at onset | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:loss of vestibular reflexes ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:loss of vestibular reflexes | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:low-set ears (28%) ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:low-set ears (28%) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:low-set ears (45%) ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:low-set ears (45%) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:michel aplasia (complete absence of inner ear structures) ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:michel aplasia (complete absence of inner ear structures) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:narrowed external ear canal ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:narrowed external ear canal | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:neonatal cystic lesions of the pinnae ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:neonatal cystic lesions of the pinnae | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:normal middle ear pressures on tympanometry ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:normal middle ear pressures on tympanometry | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:overfolded helix ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:overfolded helix | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:pale, stiff pinnae ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:pale, stiff pinnae | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:postauricular pit ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:postauricular pit | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:posterior helical indentations ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:posterior helical indentations | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:prolonged brainstem auditory evoked potentials (baep) ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:prolonged brainstem auditory evoked potentials (baep) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:protruding, simple ears ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:protruding, simple ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:sensorineural hearing loss (early-onset form) ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:sensorineural hearing loss (early-onset form) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:sensorineural hearing loss, mild to moderate ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:sensorineural hearing loss, mild to moderate | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:small auricles ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:small auricles | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:structure of lymphatic vessel of ear ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:structure of lymphatic vessel of ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:unravelling of superior helices ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:unravelling of superior helices | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:upturned lobes ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:upturned lobes | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:vestibular dysfunction (in some patients) ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=en:vestibular dysfunction (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- surdi-mutité ---
r_associated #0: 34 -->
en:otoneurologic disturbances
n1=surdi-mutité | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=34
- en:ENT doctor ---
r_associated #0: 33 -->
en:otoneurologic disturbances
n1=en:ENT doctor | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=33
- otite séreuse ---
r_associated #0: 33 -->
en:otoneurologic disturbances
n1=otite séreuse | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=33
- en:abnormal ear configuration ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:abnormal ear configuration | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:abnormality of the middle ear ossicles ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:abnormality of the middle ear ossicles | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:abnormally shaped ears (in one family) ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:abnormally shaped ears (in one family) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:absence of the helix and distal scapha in middle third of the ear ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:absence of the helix and distal scapha in middle third of the ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:absent external auditory canals ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:absent external auditory canals | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:absent vestibular function (caloric test) ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:absent vestibular function (caloric test) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:attached ear lobules ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:attached ear lobules | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:bilateral conductive hearing loss (rare) ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:bilateral conductive hearing loss (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:cauliflower ear deformity (rare) ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:cauliflower ear deformity (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:complete bony atresia of medial portion of external auditory canal (in some patients) ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:complete bony atresia of medial portion of external auditory canal (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:conductive hearing loss ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:conductive hearing loss | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:deafness, profound, affects all frequencies ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:deafness, profound, affects all frequencies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:decreased otoacoustic emission amplitude ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:decreased otoacoustic emission amplitude | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:ear cartilage calcification ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:ear cartilage calcification | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:hearing loss (uncommon) ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:hearing loss (uncommon) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:hearing loss, congenital sensorineural, moderate-severe ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:hearing loss, congenital sensorineural, moderate-severe | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:hearing loss, congenital sensorineural, severe to profound ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:hearing loss, congenital sensorineural, severe to profound | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:hearing loss, mixed (in some patients) ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:hearing loss, mixed (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:hearing loss, profound prelingual sensorineural ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:hearing loss, profound prelingual sensorineural | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, due to auditory neuropathy ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural, due to auditory neuropathy | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, mid-frequency (in some patients) ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural, mid-frequency (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, mild progressive (in some patients) ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural, mild progressive (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:hearing loss, sensorineural, prelingual ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural, prelingual | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:hearing loss, severe to profound, affecting all frequencies ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:hearing loss, severe to profound, affecting all frequencies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:hypoplastic semicircular canals ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:hypoplastic semicircular canals | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:large anteverted pinnae (90% males, 40% females) ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:large anteverted pinnae (90% males, 40% females) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:large, low-set ears ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:large, low-set ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:large, prominent ears (59%) ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:large, prominent ears (59%) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:loss of mid- and low-frequencies later ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:loss of mid- and low-frequencies later | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:low-set ears (rare) ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:low-set ears (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:mild cochlear hearing loss (1 patient) ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:mild cochlear hearing loss (1 patient) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:mild to moderate hearing loss across most frequencies ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:mild to moderate hearing loss across most frequencies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:narrow ears ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:narrow ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:neural hearing loss ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:neural hearing loss | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:no vestibular symptoms ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:no vestibular symptoms | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:otitis media, chronic (rare) ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:otitis media, chronic (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:otitis media, recurrent (rare) ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:otitis media, recurrent (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:progressive mixed conductive and sensorineural hearing loss ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:progressive mixed conductive and sensorineural hearing loss | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:prominent antihelix ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:prominent antihelix | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:prominent antitragus (in some patients) ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:prominent antitragus (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:pulsatile tinnitus (tympanic paraganglioma) ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:pulsatile tinnitus (tympanic paraganglioma) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:rotated ears ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:rotated ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:sensorineural deafness, variable (in 1 family) ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:sensorineural deafness, variable (in 1 family) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:sensorineural hearing loss (uncommon) ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:sensorineural hearing loss (uncommon) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:squared-off ears ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:squared-off ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:unilateral external ear deformity ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:unilateral external ear deformity | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:vestibular involvement (variable) ---
r_associated #0: 32 -->
en:otoneurologic disturbances
n1=en:vestibular involvement (variable) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=32
- en:abnormal brain auditory evoked responses (baer) ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:abnormal brain auditory evoked responses (baer) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:acoustic trauma ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:acoustic trauma | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:cleft lobules ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:cleft lobules | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:conductive hearing loss (in a subset of patients) ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:conductive hearing loss (in a subset of patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:conductive hearing loss to due otitis media ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:conductive hearing loss to due otitis media | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:crumpled ear (76%) ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:crumpled ear (76%) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:deafness, conductive (in some patients) ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:deafness, conductive (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:deafness, congenital sensorineural, profound (in some patients) ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:deafness, congenital sensorineural, profound (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:deafness, early-onset ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:deafness, early-onset | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:deafness, sensorineural (reported in 1 family) ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:deafness, sensorineural (reported in 1 family) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:deafness, stable bilateral symmetric prelingual ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:deafness, stable bilateral symmetric prelingual | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:decreased or absent ipsilateral acoustic reflex response to maximum stimulation | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:deficient auricle ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:deficient auricle | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:dysmorphic ears ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:dysmorphic ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:dysplastic ears (jbts) ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:dysplastic ears (jbts) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:ear constriction (97%) ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:ear constriction (97%) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:external ear defects (47%) ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:external ear defects (47%) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:flat ears ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:flat ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:floppy ears ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:floppy ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:hearing impairment (1 patient) ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:hearing impairment (1 patient) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:hearing loss, bilateral ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:hearing loss, bilateral | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:hearing loss, congenital profound ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:hearing loss, congenital profound | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies) ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:hearing loss, progressive sensorineural (most severe at high frequencies, but ultimately affecting all frequencies) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural (bilateral, prelingual) ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural (bilateral, prelingual) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural (type ii) ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural (type ii) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural (variable) ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural (variable) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:hearing loss, sensorineural, moderate, postlingual ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural, moderate, postlingual | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:hearing loss, unilateral (rare) ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:hearing loss, unilateral (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:hearing normal ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:hearing normal | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:large, floppy ears ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:large, floppy ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:lobule creases ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:lobule creases | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:low-set ears (in some patients) ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:low-set ears (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:low-set ears (severe form) ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:low-set ears (severe form) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:low-set, posteriorly rotated ears ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:low-set, posteriorly rotated ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:microtia, type i ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:microtia, type i | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:no hearing loss ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:no hearing loss | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:normal vestibular response ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:normal vestibular response | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:otitis externa, recurrent, due to infection with staphylococcus aureus ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:otitis externa, recurrent, due to infection with staphylococcus aureus | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:posteriorly rotated ears (2p21del) ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:posteriorly rotated ears (2p21del) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:preauricular skin furrow ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:preauricular skin furrow | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:pseudomembranous inflammation of the middle ear ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:pseudomembranous inflammation of the middle ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:recurrent otitis media (18%) ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:recurrent otitis media (18%) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:satyr ear ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:satyr ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:sensorineural hearing loss (1 family) ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:sensorineural hearing loss (1 family) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:severe narrowing of cartilagenous auditory canal (in homozygotes) ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:severe narrowing of cartilagenous auditory canal (in homozygotes) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:severe to profound hearing impairment by early adulthood ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:severe to profound hearing impairment by early adulthood | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:small external auditory canals ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:small external auditory canals | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:small external auditory meatus ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:small external auditory meatus | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:small, malformed ears ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:small, malformed ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:stapes fixation ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:stapes fixation | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:strabismus (in some patients) ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:strabismus (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:superiorly displaced ears ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:superiorly displaced ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:symmetric deterioration of hearing loss and speech reception with age ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:symmetric deterioration of hearing loss and speech reception with age | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:tympanic membrane perforation ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:tympanic membrane perforation | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:u-shaped audiogram ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:u-shaped audiogram | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:unfolded superior helices ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:unfolded superior helices | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:vertigo, episodic ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:vertigo, episodic | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:vestibular dysfunction ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:vestibular dysfunction | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:wide, flattened earlobes ---
r_associated #0: 31 -->
en:otoneurologic disturbances
n1=en:wide, flattened earlobes | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=31
- en:abnormal brainstem auditory evoked potentials (baep) ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:abnormal brainstem auditory evoked potentials (baep) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:abnormal ears ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:abnormal ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:abnormal middle ear reflexes ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:abnormal middle ear reflexes | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:absent stapedial reflex ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:absent stapedial reflex | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:angular ears ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:angular ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:asymmetric dysplastic ears ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:asymmetric dysplastic ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:auditory neuropathy spectrum disorder ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:auditory neuropathy spectrum disorder | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:auricular clefts ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:auricular clefts | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:blind fistula ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:blind fistula | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:conductive hearing loss, bilateral ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:conductive hearing loss, bilateral | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:cupped ears (finding) ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:cupped ears (finding) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:cupped ears (in some patients) ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:cupped ears (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:deafness affects all frequencies ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:deafness affects all frequencies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:deafness, moderate-severe (onset in third decade) ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:deafness, moderate-severe (onset in third decade) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:deafness, postlingual ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:deafness, postlingual | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:deafness, sensorineural, prelingual, profound ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:deafness, sensorineural, prelingual, profound | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:deafness, sensorineural, severe to profound affecting all frequencies ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:deafness, sensorineural, severe to profound affecting all frequencies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:deafness, sensorineural, variable ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:deafness, sensorineural, variable | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:disjunction of otherwise normal lobule from remainder of ear ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:disjunction of otherwise normal lobule from remainder of ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:dysplastic helices ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:dysplastic helices | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:expansion of helical fold at superior point of true longitudinal axis of ear ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:expansion of helical fold at superior point of true longitudinal axis of ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:external ear defects ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:external ear defects | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:hearing loss (cvs+) ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:hearing loss (cvs+) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:hearing loss, late-onset sensorineural, mild-to moderate (less common) ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:hearing loss, late-onset sensorineural, mild-to moderate (less common) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:hearing loss, moderate to severe, bilateral, nonprogressive ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:hearing loss, moderate to severe, bilateral, nonprogressive | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:hearing loss, postlingual sensorineural ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:hearing loss, postlingual sensorineural | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:hearing loss, prelingual sensorineural, moderate to severe ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:hearing loss, prelingual sensorineural, moderate to severe | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:hearing loss, progressive conductive and/or sensorineural, during adulthood ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:hearing loss, progressive conductive and/or sensorineural, during adulthood | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural progressive postlingual, high-frequency progressing to all frequencies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, bilateral, moderate-to-severe ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural, bilateral, moderate-to-severe | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:hearing loss, sensorineural, progressive (childhood-onset) ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural, progressive (childhood-onset) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:hyperacusis ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:hyperacusis | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:hypoplasia of the cochlea ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:hypoplasia of the cochlea | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:incomplete separation of the cochlea from the internal auditory canal ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:incomplete separation of the cochlea from the internal auditory canal | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:increased posterior angulation ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:increased posterior angulation | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:large fleshy ears ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:large fleshy ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:lobular aplasia ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:lobular aplasia | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:low set ears ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:low set ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:malformed ossicular chain ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:malformed ossicular chain | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:meniere disease ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:meniere disease | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:mixed hearing loss (50% of patients) ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:mixed hearing loss (50% of patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:narrow ear lobes ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:narrow ear lobes | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:narrow external ear canals (1 patient) ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:narrow external ear canals (1 patient) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:no reproducible waves i, iii, or v at high intensities ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:no reproducible waves i, iii, or v at high intensities | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:normal otoacoustic emissions ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:normal otoacoustic emissions | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:normal static compliance on tympanometry ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:normal static compliance on tympanometry | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:other auditory injuries ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:other auditory injuries | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:preauricular dimple ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:preauricular dimple | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face) ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:preauricular tag, isolated (skin covered and composed of elastic cartilage usually located anterior to the tragus or ascending crus of the helix but can be elsewhere on the ear or face) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:progressive hearing loss (in some) ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:progressive hearing loss (in some) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:progressive, low frequency sensorineural hearing loss ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:progressive, low frequency sensorineural hearing loss | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:protruding right ear ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:protruding right ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:sensorineural deafness (rare) ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:sensorineural deafness (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:sensorineural deafness, postlingual, progressive ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:sensorineural deafness, postlingual, progressive | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:sensorineural hearing impairment (less common) ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:sensorineural hearing impairment (less common) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:serous otitis ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:serous otitis | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:severe loss in the higher frequencies by the fifth decade ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:severe loss in the higher frequencies by the fifth decade | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:short ear ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:short ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:small earlobe ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:small earlobe | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:structural inner ear abnormalities (in patients with larger deletions) ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:structural inner ear abnormalities (in patients with larger deletions) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:thick earlobes ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:thick earlobes | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:transient evoked otoacoustic emissions cannot be detected ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:transient evoked otoacoustic emissions cannot be detected | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:u- or bowl-shaped audiogram ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=en:u- or bowl-shaped audiogram | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- hyperacousie ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=hyperacousie | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- hyperacousies ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=hyperacousies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- hyperacusie ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=hyperacusie | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- médecin ORL ---
r_associated #0: 30 -->
en:otoneurologic disturbances
n1=médecin ORL | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=30
- en:abnormally folded helix ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:abnormally folded helix | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:absence of the cochlear nerves (reported in 1 patient) ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:absence of the cochlear nerves (reported in 1 patient) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:absent or decreased auditory brainstem responses ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:absent or decreased auditory brainstem responses | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:accessory tragus ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:accessory tragus | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:anteriorly displaced ears ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:anteriorly displaced ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:audiogram is gently sloping or flat ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:audiogram is gently sloping or flat | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:chronic otitis media ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:chronic otitis media | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:conductive hearing loss, mild bilateral (rare) ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:conductive hearing loss, mild bilateral (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:congenital atresia of external auditory canal ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:congenital atresia of external auditory canal | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss) ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:congenital non-progressive, non-syndromic sensorineural hearing loss (greater mid frequency than low- or high-frequency loss) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:deafness, early-onset mixed conductive and sensorineural ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:deafness, early-onset mixed conductive and sensorineural | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:deafness, sensorineural, especially affecting high frequencies (in about 55% of males and 45% of females) ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:deafness, sensorineural, especially affecting high frequencies (in about 55% of males and 45% of females) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:ear pain/earache ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:ear pain/earache | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:entire ear ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:entire ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:everted ears ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:everted ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:external auditory canal narrow ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:external auditory canal narrow | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:fear of ear disease ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:fear of ear disease | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:flattened antihelix ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:flattened antihelix | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:fleshy and overfolded helices ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:fleshy and overfolded helices | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:hearing impairment (rare) ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:hearing impairment (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:hearing impairment, sensorineural, fluctuating ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:hearing impairment, sensorineural, fluctuating | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:hearing loss (2 patients) ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:hearing loss (2 patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:hearing loss (variable) ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:hearing loss (variable) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:hearing loss, high frequency, slowly progressive (onset in early childhood) ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:hearing loss, high frequency, slowly progressive (onset in early childhood) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:hearing loss, more severe at lower frequencies ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:hearing loss, more severe at lower frequencies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:hearing loss, neural type ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:hearing loss, neural type | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:hearing loss, postlingual progressive sensorineural ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:hearing loss, postlingual progressive sensorineural | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies) ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural (high frequency loss followed by low frequency loss leading to profound loss of all frequencies) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural (in 1 ashkenazi patient) ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural (in 1 ashkenazi patient) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges) ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural, congenital progressive (affects primarily low- and middle-frequency ranges) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected) ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural, progressive (high frequencies first affected, all frequencies later affected) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:hyperfolded ears ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:hyperfolded ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:hypoplastic ear lobes ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:hypoplastic ear lobes | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:hypoplastic ears fused to the scalp ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:hypoplastic ears fused to the scalp | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:incomplete atretic plate ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:incomplete atretic plate | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:initially, hearing loss is moderate for low (120-250 hz) and mid (500-2000 hz) frequencies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:large anteverted ears ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:large anteverted ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:large dysplastic ears ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:large dysplastic ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:large earlobe ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:large earlobe | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:large simple ears ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:large simple ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:large, dysmorphic ears ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:large, dysmorphic ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:linear ear lobe creases ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:linear ear lobe creases | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:low-frequency conductive hearing loss ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:low-frequency conductive hearing loss | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:mild dysplasia of concha, unilateral ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:mild dysplasia of concha, unilateral | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:misshapen ear ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:misshapen ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:no vestibular dysfunction ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:no vestibular dysfunction | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:occasional conductive hearing loss ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:occasional conductive hearing loss | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:other symptom/complaint of ear ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:other symptom/complaint of ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:overfolded, rumpled ears ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:overfolded, rumpled ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:poorly folded ears ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:poorly folded ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:preauricular fistulas, bilateral ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:preauricular fistulas, bilateral | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:preauricular pits (70-80% of patients) ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:preauricular pits (70-80% of patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:preauricular sinus, bilateral ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:preauricular sinus, bilateral | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:prominence and protrusion of upper third of the ear ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:prominence and protrusion of upper third of the ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:prominent crura ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:prominent crura | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:recurrent serous otitis ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:recurrent serous otitis | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:sensorineural hearing loss (1 patient) ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:sensorineural hearing loss (1 patient) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:stapes ankylosis ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:stapes ankylosis | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:stenotic ear canals (30%) ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:stenotic ear canals (30%) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:temporal bone shows deposition of cochlin-positive eosinophilic extracellular ground substance in the channels of the cochlear and vestibular nerves | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:thick ears ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:thick ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:tinnitus (variable) ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:tinnitus (variable) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:unconnected or fused stapes and incus ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:unconnected or fused stapes and incus | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:vestibular function defect (decreased in some, normal in other patients) ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:vestibular function defect (decreased in some, normal in other patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:vestibular hypofunction ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:vestibular hypofunction | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:vestibular hyporeflexia ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:vestibular hyporeflexia | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:wide bulbous internal auditory meatus ---
r_associated #0: 29 -->
en:otoneurologic disturbances
n1=en:wide bulbous internal auditory meatus | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=29
- en:absence of acoustic reflex ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:absence of acoustic reflex | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:absent or abnormal otoacoustic emissions ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:absent or abnormal otoacoustic emissions | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:absent stapedial reflexes or intraoperative stapes immobility ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:absent stapedial reflexes or intraoperative stapes immobility | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:anteverted ears ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:anteverted ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:approximately 0.7db per year hearing loss at all frequencies ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:approximately 0.7db per year hearing loss at all frequencies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:asymmetry of the ears ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:asymmetry of the ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:atresia of the external auditory canal ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:atresia of the external auditory canal | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:atretic auditory canal ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:atretic auditory canal | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:atrophy of vestibular nerves and ganglion cells (ascertained in 1 patient) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:bilateral hypoplastic cochlea ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:bilateral hypoplastic cochlea | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:cochlear degeneration ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:cochlear degeneration | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:cochleosaccular dysplasia ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:cochleosaccular dysplasia | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:cupped pinna ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:cupped pinna | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:deafness due to bilateral cochlear malformation (rare) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:deafness due to bilateral cochlear malformation (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:deafness, bilateral sensorineural, high frequency (100% of patients) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:deafness, bilateral sensorineural, high frequency (100% of patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:deafness, profound, by 6th decade ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:deafness, profound, by 6th decade | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:deafness, sensorineural, especially affecting high frequencies ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:deafness, sensorineural, especially affecting high frequencies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:deafness, sensorineural, profound ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:deafness, sensorineural, profound | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:ear dimple ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:ear dimple | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:enlarged vestibular aqueduct ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:enlarged vestibular aqueduct | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:eustachian tube salpingitis ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:eustachian tube salpingitis | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:flat audiogram ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:flat audiogram | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:flat or shallow u-shaped audiogram ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:flat or shallow u-shaped audiogram | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:folded superior edge of helix ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:folded superior edge of helix | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:hearing disorder (1 patient) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:hearing disorder (1 patient) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:hearing impairment, asymmetric (in some patients with hsan2d) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:hearing impairment, asymmetric (in some patients with hsan2d) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:hearing loss (95% of patients) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:hearing loss (95% of patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:hearing loss (affecting all frequencies), moderate to severe ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:hearing loss (affecting all frequencies), moderate to severe | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:hearing loss (rare) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:hearing loss (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural (in some patients) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:hearing loss, sensorineural (in some) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural (in some) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:hypercompliant tympanic membranes ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:hypercompliant tympanic membranes | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:hypoplastic pinnae (30-60% of patients) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:hypoplastic pinnae (30-60% of patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:increase in amplitude and duration of cochlear microphonic (cm) (in young patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:keratotic plaque around ear meatus ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:keratotic plaque around ear meatus | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:large auricle ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:large auricle | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:large pinnae ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:large pinnae | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:large protruding ears ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:large protruding ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:long and prominent ear crus ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:long and prominent ear crus | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:loss of vestibular caloric response ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:loss of vestibular caloric response | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:low-set ears (in one family) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:low-set ears (in one family) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:malformed auricle (1 patient) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:malformed auricle (1 patient) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:microtia (in some patients) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:microtia (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:mild hearing impairment (13%) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:mild hearing impairment (13%) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:misshapen, small ear ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:misshapen, small ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:moderate-to-severe in all frequencies, but slightly more pronounced in mid-frequencies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:near-stenosis of bony portion of auditory canal ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:near-stenosis of bony portion of auditory canal | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:no auditory brainstem response (abr) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:no auditory brainstem response (abr) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:normal vestibular function ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:normal vestibular function | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:otitis externa ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:otitis externa | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:otitis with effusion ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:otitis with effusion | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:pinna modeling anomalies ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:pinna modeling anomalies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:poorly formed pinnae ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:poorly formed pinnae | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:posteriorly rotated ears (female) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:posteriorly rotated ears (female) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:preauricular sinus ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:preauricular sinus | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:preauricular skin tag ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:preauricular skin tag | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:prelingual onset ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:prelingual onset | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:profound sensorineural hearing loss ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:profound sensorineural hearing loss | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:relatively long ears ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:relatively long ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:sclerosis of semicircular canals ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:sclerosis of semicircular canals | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:sensorineural deafness (reported in 1 family) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:sensorineural deafness (reported in 1 family) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:sensorineural hearing loss (onset early childhood) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:sensorineural hearing loss (onset early childhood) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:sensorineural hearing loss, mild (rare) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:sensorineural hearing loss, mild (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:sensory hearing loss ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:sensory hearing loss | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:short ears (in 1 family) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:short ears (in 1 family) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:simple auricles ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:simple auricles | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:small ears with large lobules ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:small ears with large lobules | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:small pinna ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:small pinna | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:small pits anterior to the helix (1 patient) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:small pits anterior to the helix (1 patient) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:stiff, prominent pinnae ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:stiff, prominent pinnae | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:supraauricular pit ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:supraauricular pit | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:thick, firm earlobes ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:thick, firm earlobes | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:tinnitus, bilateral (in some patients) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:tinnitus, bilateral (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:underdeveloped nasal alae ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:underdeveloped nasal alae | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:uplift of earlobes (in some patients) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:uplift of earlobes (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:uplifted earlobes ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:uplifted earlobes | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:vestibular anomalies (less common) ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:vestibular anomalies (less common) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:vestibular areflexia ---
r_associated #0: 28 -->
en:otoneurologic disturbances
n1=en:vestibular areflexia | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=28
- en:abnormal folded pinna ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:abnormal folded pinna | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:absence of earlobe ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:absence of earlobe | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:absent earlobe ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:absent earlobe | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:aplasia of the inner ear ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:aplasia of the inner ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:auriculo-condylar syndrome ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:auriculo-condylar syndrome | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:cleft at the junction of the lobule and helix ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:cleft at the junction of the lobule and helix | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:cochlear malformation defect (mondini dysplasia) (less common) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:cochlear malformation defect (mondini dysplasia) (less common) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:cup-shaped ears (30-60% of patients) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:cup-shaped ears (30-60% of patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:cutlet ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:cutlet | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:deafness (in some patients) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:deafness (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:deafness (variable) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:deafness (variable) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:deafness, bilateral with postpubertal onset and rapid progression to profound deafness within 5 to 6 years | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:deficient or absent bone between the lateral end of the meatus and basal turn of the cochlea | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:disproportionately large ears ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:disproportionately large ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:dorsally rotated ears ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:dorsally rotated ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:dysplastic ears (in some patients) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:dysplastic ears (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:ear part ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:ear part | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:ears deficient in cartilage ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:ears deficient in cartilage | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:endolymphatic sac tumors (elsts) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:endolymphatic sac tumors (elsts) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:hearing impairment, progressive (family a) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:hearing impairment, progressive (family a) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:hearing loss (1 patient) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:hearing loss (1 patient) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:hearing loss (conductive and/or sensorineural) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:hearing loss (conductive and/or sensorineural) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:hearing loss affects all frequencies ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:hearing loss affects all frequencies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:hearing loss first affects high frequencies ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:hearing loss first affects high frequencies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:hearing loss, mixed, mild to severe (in heterozygotes) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:hearing loss, mixed, mild to severe (in heterozygotes) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:hearing loss, progressive sensorineural, affecting high frequencies ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:hearing loss, progressive sensorineural, affecting high frequencies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural (high frequency) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural (high frequency) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural (in 2 patients) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural (in 2 patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:hearing loss, sensorineural, severe to profound ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural, severe to profound | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:hypoplastic malleus (1 patient) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:hypoplastic malleus (1 patient) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:left ear ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:left ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:loss of hearing (45%) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:loss of hearing (45%) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:loss of outer hair cell function ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:loss of outer hair cell function | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:low-set and rotated ears ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:low-set and rotated ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:low-set, malformed ears ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:low-set, malformed ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:malformations of the auditory ossicles ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:malformations of the auditory ossicles | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:malformed pinnae (30-60% of patients) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:malformed pinnae (30-60% of patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:microtia hearing loss, conductive ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:microtia hearing loss, conductive | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:narrow intertragic notch ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:narrow intertragic notch | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:narrowing of ear canal ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:narrowing of ear canal | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:near-stenosis of bony portion of auditory canal (in homozygotes) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:near-stenosis of bony portion of auditory canal (in homozygotes) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:no auditory brainstem response to 100-db stimulus ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:no auditory brainstem response to 100-db stimulus | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:normal otoacoustic emissions (oae), indicating intact outer ear hair cell function ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:normal otoacoustic emissions (oae), indicating intact outer ear hair cell function | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:normal outer hair cell functions ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:normal outer hair cell functions | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:outer ear abnormalities (deletion patients) prominent ears ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:outer ear abnormalities (deletion patients) prominent ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:pointed upper helix ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:pointed upper helix | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:poorly formed ears ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:poorly formed ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:poorly shaped ears ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:poorly shaped ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:presbycusis ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:presbycusis | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:profound deafness ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:profound deafness | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:progressive sensorineural hearing impairment ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:progressive sensorineural hearing impairment | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:prominent earlobes (in some patients) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:prominent earlobes (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:prominent lobules ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:prominent lobules | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:protruding lobules ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:protruding lobules | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:raised earlobes ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:raised earlobes | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:retinitis (in some patients) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:retinitis (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:rudimentary ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:rudimentary | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:rudimentary tympanic membrane (in some patients) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:rudimentary tympanic membrane (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:sensorineural deafness, progressive, late-onset ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:sensorineural deafness, progressive, late-onset | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:sensorineural hearing impairment (in some patients) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:sensorineural hearing impairment (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:sensorineural hearing loss (3 patients) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:sensorineural hearing loss (3 patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:sensorineural hearing loss (described in 1 family) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:sensorineural hearing loss (described in 1 family) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:severe to profound deafness ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:severe to profound deafness | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:shallow skin dimple on posterior surface of ear ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:shallow skin dimple on posterior surface of ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:simplified helices ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:simplified helices | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:slit-like opening of the exterior auditory meatus ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:slit-like opening of the exterior auditory meatus | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:small lobes ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:small lobes | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:soft auricles ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:soft auricles | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:squared-off superior helices ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:squared-off superior helices | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:thickened helices ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:thickened helices | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:vestibular hypofunction (rare) ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:vestibular hypofunction (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:vestibulopathy, bilateral, progressive ---
r_associated #0: 27 -->
en:otoneurologic disturbances
n1=en:vestibulopathy, bilateral, progressive | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=27
- en:abnormal auditory brainstem responses ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:abnormal auditory brainstem responses | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:abnormal auricles ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:abnormal auricles | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:abnormal communication between the subarachnoid space in the meatus and the perilymph ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:abnormal communication between the subarachnoid space in the meatus and the perilymph | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:abnormal gap detection ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:abnormal gap detection | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:absent brainstem auditory responses ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:absent brainstem auditory responses | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:absent cochlear microphonic (in older patients) ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:absent cochlear microphonic (in older patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:absent external auditory meatus ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:absent external auditory meatus | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:absent lobules ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:absent lobules | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:acute otitis media/myringitis ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:acute otitis media/myringitis | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:anomalous middle ear bones ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:anomalous middle ear bones | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:anteverted pinnae ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:anteverted pinnae | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:auditory canal stenosis ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:auditory canal stenosis | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:auditory impairment ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:auditory impairment | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:aural fullness ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:aural fullness | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:bat ear ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:bat ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile) ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:by fourth decade, there is severe hearing loss for mid frequencies and moderate hearing loss for high frequencies (4000-8000 hz) (u-shaped audiometric profile) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:chronic otitis media (25%) ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:chronic otitis media (25%) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:cleft at the superior portion of the pinna ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:cleft at the superior portion of the pinna | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:cochlear malformation ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:cochlear malformation | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:congenital hearing loss (1 family) ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:congenital hearing loss (1 family) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:congenital small ears ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:congenital small ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:deafness (often in third decade) ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:deafness (often in third decade) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:deafness, congenital sensorineural, severe to profound ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:deafness, congenital sensorineural, severe to profound | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:deep-set ears ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:deep-set ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:dysplastic pinnae ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:dysplastic pinnae | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:earlobe pits ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:earlobe pits | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:endolymphatic hydrops, delayed onset ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:endolymphatic hydrops, delayed onset | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:folded helix ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:folded helix | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:hearing deficits (28% of adults) ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:hearing deficits (28% of adults) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:hearing loss has been reported in some adults with severe disease ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:hearing loss has been reported in some adults with severe disease | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:hearing loss, initially conductive, later mixed conductive-sensorineural ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:hearing loss, initially conductive, later mixed conductive-sensorineural | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:hearing loss, mild ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:hearing loss, mild | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:hearing loss, mild (rare) ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:hearing loss, mild (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:hearing loss, postlingual ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:hearing loss, postlingual | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:hearing loss, prelingual, severe to profound (affecting all frequencies) ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:hearing loss, prelingual, severe to profound (affecting all frequencies) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies) ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:hearing loss, progressive, (high frequency loss at first progressing to loss of all frequencies) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:hearing loss, progressive, starting in infancy ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:hearing loss, progressive, starting in infancy | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:hearing loss, sensorineural (in one family) ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural (in one family) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:hypoplastic helices ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:hypoplastic helices | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:large anteverted ears (rare) ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:large anteverted ears (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:large ears (2p21del) ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:large ears (2p21del) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:large ears (in some patients) ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:large ears (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:large, low-set ears (uncommon) ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:large, low-set ears (uncommon) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:limited auditory function ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:limited auditory function | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:lobule may be separately from the rest of the external ear ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:lobule may be separately from the rest of the external ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:low-frequency sensorineural hearing impairment ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:low-frequency sensorineural hearing impairment | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:low-set ears (1 patient) ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:low-set ears (1 patient) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:malformed earlobes ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:malformed earlobes | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:microtia (30-60% of patients) ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:microtia (30-60% of patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:minor auricular anomalies ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:minor auricular anomalies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:mondini defect ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:mondini defect | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:no deafness ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:no deafness | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:nonsyndromic sensorineural hearing loss ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:nonsyndromic sensorineural hearing loss | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:posteriorly rotated ears (in some patients) ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:posteriorly rotated ears (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:preauricular skin tags (in some patients) ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:preauricular skin tags (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:progressive hearing impairment ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:progressive hearing impairment | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:progressive high-frequency hearing loss (onset 20-30 years) ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:progressive high-frequency hearing loss (onset 20-30 years) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:recurrent otitis media in infancy and childhood ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:recurrent otitis media in infancy and childhood | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:rudimentary ear ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:rudimentary ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:sensorineural hearing loss (males only) ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:sensorineural hearing loss (males only) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:sensorineural hearing loss has been reported ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:sensorineural hearing loss has been reported | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:small, simple ears ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:small, simple ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:structure of superior auricularis muscle ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:structure of superior auricularis muscle | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:triangular-shaped ears ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:triangular-shaped ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:vestibular abnormalities (variable) ---
r_associated #0: 26 -->
en:otoneurologic disturbances
n1=en:vestibular abnormalities (variable) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=26
- en:'tilted' ears ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:'tilted' ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:abnormality of the outer ear ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:abnormality of the outer ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:abnormally folded ears ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:abnormally folded ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:absence of vestibular evoked myogenic potentials (rare) ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:absence of vestibular evoked myogenic potentials (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:bleeding from ear ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:bleeding from ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:concern with appearance of ears ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:concern with appearance of ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:congenital absence of external ear ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:congenital absence of external ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:cup-shaped auricles ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:cup-shaped auricles | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:deafness ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:deafness | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:decreased auditory brainstem responses ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:decreased auditory brainstem responses | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:downsloping audiogram ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:downsloping audiogram | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:external ear ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:external ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:flattened ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:flattened | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:hearing impairment (in some patients) ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:hearing impairment (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:hearing loss begins with loss of high frequencies ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:hearing loss begins with loss of high frequencies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:hearing loss, conductive (rare) ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:hearing loss, conductive (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:inferior displacement of the ears ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:inferior displacement of the ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:microtia (wws) ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:microtia (wws) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:no vestibular impairment ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:no vestibular impairment | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:posteriorly rotated ears (1/4 patients) ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:posteriorly rotated ears (1/4 patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:recurrent otitis media in infancy ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:recurrent otitis media in infancy | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:roll-head ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:roll-head | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:upsloping audiograms ---
r_associated #0: 25 -->
en:otoneurologic disturbances
n1=en:upsloping audiograms | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=25
- en:abnormal amplitude modulation detection ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:abnormal amplitude modulation detection | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:abnormal helices, antihelices and lobules ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:abnormal helices, antihelices and lobules | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:absent brainstem auditory-evoked responses ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:absent brainstem auditory-evoked responses | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:anteriorly rotated ears ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:anteriorly rotated ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:atrophy of cochlear and vestibular fibrocytes ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:atrophy of cochlear and vestibular fibrocytes | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:chronic otitis other infection ear ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:chronic otitis other infection ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:congenital ear anomaly nos (disorder) ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:congenital ear anomaly nos (disorder) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:deafness, congenital nonprogressive sensorineural symmetric, moderate ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:deafness, congenital nonprogressive sensorineural symmetric, moderate | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:deafness, nonprogressive, moderate ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:deafness, nonprogressive, moderate | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:deafness, sensorineural (in some patients) ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:deafness, sensorineural (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:deafness, sensorineural (severe to profound) ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:deafness, sensorineural (severe to profound) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:disturbance of equilibrium ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:disturbance of equilibrium | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:downward sloping or flat audiogram ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:downward sloping or flat audiogram | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:ear pits, posterior helical ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:ear pits, posterior helical | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:external ears rudimentary ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:external ears rudimentary | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:fleshy ears ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:fleshy ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:foreign body in auditory canal ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:foreign body in auditory canal | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:glue ear ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:glue ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:hearing impairment may occur ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:hearing impairment may occur | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:hearing impairment, mild (2 patients) ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:hearing impairment, mild (2 patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:hearing loss, sensorineural, associated with elsts ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural, associated with elsts | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:hearing threshold at or above 90 db at all frequencies tested (0.25-8.0 khz) ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:hearing threshold at or above 90 db at all frequencies tested (0.25-8.0 khz) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:hypoplasia of the upper part of the helix ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:hypoplasia of the upper part of the helix | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:long ear ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:long ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:long, lobulated ears ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:long, lobulated ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:low-set ears (in 2/4 patients) ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:low-set ears (in 2/4 patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:middle ear ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:middle ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:otosclerosis ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:otosclerosis | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:overfolding of the superior helices ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:overfolding of the superior helices | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:phonophobia ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:phonophobia | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:sensorineural hearing loss (in 1 of 3 patients) ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:sensorineural hearing loss (in 1 of 3 patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:sensorineural hearing loss (rare) ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:sensorineural hearing loss (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:sensorineural hearing loss, bilateral ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:sensorineural hearing loss, bilateral | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:small cavum conchae ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:small cavum conchae | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:tinnitus ---
r_associated #0: 24 -->
en:otoneurologic disturbances
n1=en:tinnitus | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=24
- en:abnormality of the middle ear ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:abnormality of the middle ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:absent ipsilateral middle ear muscle reflexes (in older patients) ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:absent ipsilateral middle ear muscle reflexes (in older patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:air-bone gap of greater than 20 db across 0.5 to 2 khz ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:air-bone gap of greater than 20 db across 0.5 to 2 khz | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:apical cartilage deformity ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:apical cartilage deformity | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:conductive and sensorineural hearing loss ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:conductive and sensorineural hearing loss | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:conductive hearing loss (30% of patients) ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:conductive hearing loss (30% of patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:deafness, prelingual, profound (affects all frequencies) ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:deafness, prelingual, profound (affects all frequencies) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:deafness, unilateral, childhood onset ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:deafness, unilateral, childhood onset | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:ear neoplasm ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:ear neoplasm | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:escalope ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:escalope | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural (in sister) ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural (in sister) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural (in some cases) ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural (in some cases) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:hearing loss, sensorineural and conductive, severe to profound ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:hearing loss, sensorineural and conductive, severe to profound | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:high-tone sensorineural deafness (67% of patients) ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:high-tone sensorineural deafness (67% of patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:hypoacusia (1 patient) ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:hypoacusia (1 patient) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:inner ear ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:inner ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:macrotia ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:macrotia | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:mild to moderate hearing loss ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:mild to moderate hearing loss | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:mixed hearing loss ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:mixed hearing loss | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:otolaryngologist ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:otolaryngologist | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:otorrhea ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:otorrhea | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:progressive cartilaginous ossification of pinnae ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:progressive cartilaginous ossification of pinnae | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:protruding ears ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:protruding ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:protruding ears (rare) ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:protruding ears (rare) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:recurrent otitis media ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:recurrent otitis media | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:sensation of blocked ears ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:sensation of blocked ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:simple helix ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:simple helix | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:type i arnold chiari malformation ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:type i arnold chiari malformation | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:vertiginous syndrome ---
r_associated #0: 23 -->
en:otoneurologic disturbances
n1=en:vertiginous syndrome | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=23
- en:abnormal bridge connecting the crus of the helix and antihelix ---
r_associated #0: 22 -->
en:otoneurologic disturbances
n1=en:abnormal bridge connecting the crus of the helix and antihelix | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=22
- en:abnormal middle ear ossicles ---
r_associated #0: 22 -->
en:otoneurologic disturbances
n1=en:abnormal middle ear ossicles | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=22
- en:abnormal speech discrimination ---
r_associated #0: 22 -->
en:otoneurologic disturbances
n1=en:abnormal speech discrimination | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=22
- en:attached ear lobes ---
r_associated #0: 22 -->
en:otoneurologic disturbances
n1=en:attached ear lobes | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=22
- en:deafness (sensorineural or mixed sensorineural and conductive) ---
r_associated #0: 22 -->
en:otoneurologic disturbances
n1=en:deafness (sensorineural or mixed sensorineural and conductive) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=22
- en:deafness, sensorineural, profound (prelingual onset) ---
r_associated #0: 22 -->
en:otoneurologic disturbances
n1=en:deafness, sensorineural, profound (prelingual onset) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=22
- en:hearing impairment, sensorineural, mild ---
r_associated #0: 22 -->
en:otoneurologic disturbances
n1=en:hearing impairment, sensorineural, mild | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=22
- en:hearing loss, conductive (in one family) ---
r_associated #0: 22 -->
en:otoneurologic disturbances
n1=en:hearing loss, conductive (in one family) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=22
- en:hearing loss, congenital, profound (250-8,000 hz) ---
r_associated #0: 22 -->
en:otoneurologic disturbances
n1=en:hearing loss, congenital, profound (250-8,000 hz) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=22
- en:hearing loss, unilateral, mild ---
r_associated #0: 22 -->
en:otoneurologic disturbances
n1=en:hearing loss, unilateral, mild | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=22
- en:hypoplastic superior helix ---
r_associated #0: 22 -->
en:otoneurologic disturbances
n1=en:hypoplastic superior helix | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=22
- en:nonprogressive ---
r_associated #0: 22 -->
en:otoneurologic disturbances
n1=en:nonprogressive | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=22
- en:posteriorly rotated ear ---
r_associated #0: 22 -->
en:otoneurologic disturbances
n1=en:posteriorly rotated ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=22
- en:protuberant ear ---
r_associated #0: 22 -->
en:otoneurologic disturbances
n1=en:protuberant ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=22
- en:right ear ---
r_associated #0: 22 -->
en:otoneurologic disturbances
n1=en:right ear | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=22
- en:sensorineural hearing loss (20% of patients) ---
r_associated #0: 22 -->
en:otoneurologic disturbances
n1=en:sensorineural hearing loss (20% of patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=22
- en:small/rudimentary tragus, antitragus and lobule ---
r_associated #0: 22 -->
en:otoneurologic disturbances
n1=en:small/rudimentary tragus, antitragus and lobule | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=22
- esgourde ---
r_associated #0: 22 -->
en:otoneurologic disturbances
n1=esgourde | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=22
- en:abnormal semicircular canals ---
r_associated #0: 21 -->
en:otoneurologic disturbances
n1=en:abnormal semicircular canals | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=21
- en:audiogram shows sloping configuration ---
r_associated #0: 21 -->
en:otoneurologic disturbances
n1=en:audiogram shows sloping configuration | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=21
- en:bilateral congenital profound sensorineural hearing loss ---
r_associated #0: 21 -->
en:otoneurologic disturbances
n1=en:bilateral congenital profound sensorineural hearing loss | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=21
- en:chronic otitis ---
r_associated #0: 21 -->
en:otoneurologic disturbances
n1=en:chronic otitis | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=21
- en:hearing complaints (excluding h84-86) ---
r_associated #0: 21 -->
en:otoneurologic disturbances
n1=en:hearing complaints (excluding h84-86) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=21
- en:hearing loss (reported in 2 patients) ---
r_associated #0: 21 -->
en:otoneurologic disturbances
n1=en:hearing loss (reported in 2 patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=21
- en:hearing loss, unilateral or bilateral, conductive, sensorineural, or mixed ---
r_associated #0: 21 -->
en:otoneurologic disturbances
n1=en:hearing loss, unilateral or bilateral, conductive, sensorineural, or mixed | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=21
- en:hypermobile ---
r_associated #0: 21 -->
en:otoneurologic disturbances
n1=en:hypermobile | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=21
- en:large appearing ears ---
r_associated #0: 21 -->
en:otoneurologic disturbances
n1=en:large appearing ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=21
- en:large fleshy earlobes ---
r_associated #0: 21 -->
en:otoneurologic disturbances
n1=en:large fleshy earlobes | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=21
- en:no hearing impairment ---
r_associated #0: 21 -->
en:otoneurologic disturbances
n1=en:no hearing impairment | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=21
- en:other diseases of ear/mastoid ---
r_associated #0: 21 -->
en:otoneurologic disturbances
n1=en:other diseases of ear/mastoid | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=21
- en:otitis media ---
r_associated #0: 21 -->
en:otoneurologic disturbances
n1=en:otitis media | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=21
- en:otorhinolaryngologist ---
r_associated #0: 21 -->
en:otoneurologic disturbances
n1=en:otorhinolaryngologist | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=21
- en:partial aplasia of external auditory canal ending in blind fistula (in some patients) ---
r_associated #0: 21 -->
en:otoneurologic disturbances
n1=en:partial aplasia of external auditory canal ending in blind fistula (in some patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=21
- en:small, posteriorly rotated ears ---
r_associated #0: 21 -->
en:otoneurologic disturbances
n1=en:small, posteriorly rotated ears | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=21
- en:synotus ---
r_associated #0: 21 -->
en:otoneurologic disturbances
n1=en:synotus | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=21
- en:underfolded helix ---
r_associated #0: 21 -->
en:otoneurologic disturbances
n1=en:underfolded helix | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=21
- en:vertigo, single occurrence (in 2 patients) ---
r_associated #0: 21 -->
en:otoneurologic disturbances
n1=en:vertigo, single occurrence (in 2 patients) | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=21
- en:vestibular areflexia, complete ---
r_associated #0: 21 -->
en:otoneurologic disturbances
n1=en:vestibular areflexia, complete | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=21
- en:and throat ---
r_associated #0: 20 -->
en:otoneurologic disturbances
n1=en:and throat | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=20
- en:nose and throat ---
r_associated #0: 20 -->
en:otoneurologic disturbances
n1=en:nose and throat | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=20
- hypermobile ---
r_associated #0: 20 -->
en:otoneurologic disturbances
n1=hypermobile | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=20
- nose ---
r_associated #0: 20 -->
en:otoneurologic disturbances
n1=nose | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=20
- Trouble de l'équilibre ---
r_associated #0: 15 -->
en:otoneurologic disturbances
n1=Trouble de l'équilibre | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=15
- en:dizzy spells ---
r_associated #0: 15 -->
en:otoneurologic disturbances
n1=en:dizzy spells | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=15
- en:giddiness ---
r_associated #0: 15 -->
en:otoneurologic disturbances
n1=en:giddiness | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=15
- en:scatterbrain ---
r_associated #0: 15 -->
en:otoneurologic disturbances
n1=en:scatterbrain | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=15
- vertiges ---
r_associated #0: 15 -->
en:otoneurologic disturbances
n1=vertiges | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=15
- vertigineux ---
r_associated #0: 15 -->
en:otoneurologic disturbances
n1=vertigineux | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=15
- Étourdi ---
r_associated #0: 15 -->
en:otoneurologic disturbances
n1=Étourdi | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=15
- Étourdie ---
r_associated #0: 15 -->
en:otoneurologic disturbances
n1=Étourdie | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=15
- étourdie ---
r_associated #0: 15 -->
en:otoneurologic disturbances
n1=étourdie | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=15
- étourdies ---
r_associated #0: 15 -->
en:otoneurologic disturbances
n1=étourdies | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=15
- étourdis ---
r_associated #0: 15 -->
en:otoneurologic disturbances
n1=étourdis | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=15
- étourdissements ---
r_associated #0: 15 -->
en:otoneurologic disturbances
n1=étourdissements | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=15
- Hyperacousie ---
r_associated #0: 10 -->
en:otoneurologic disturbances
n1=Hyperacousie | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=10
- Oto-rhino-laryngologiste ---
r_associated #0: 10 -->
en:otoneurologic disturbances
n1=Oto-rhino-laryngologiste | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=10
- Otorhinolaryngologiste ---
r_associated #0: 10 -->
en:otoneurologic disturbances
n1=Otorhinolaryngologiste | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=10
- ankylose stapédo-vestibulaire ---
r_associated #0: 10 -->
en:otoneurologic disturbances
n1=ankylose stapédo-vestibulaire | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=10
- ankylose stapédo-vestibulaire l.f. ---
r_associated #0: 10 -->
en:otoneurologic disturbances
n1=ankylose stapédo-vestibulaire l.f. | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=10
- aplati ---
r_associated #0: 10 -->
en:otoneurologic disturbances
n1=aplati | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=10
- en:deaf-muteness ---
r_associated #0: 10 -->
en:otoneurologic disturbances
n1=en:deaf-muteness | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=10
- en:deaf-mutism ---
r_associated #0: 10 -->
en:otoneurologic disturbances
n1=en:deaf-mutism | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=10
- en:hearing defect ---
r_associated #0: 10 -->
en:otoneurologic disturbances
n1=en:hearing defect | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=10
- en:hearing deficiency ---
r_associated #0: 10 -->
en:otoneurologic disturbances
n1=en:hearing deficiency | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=10
- en:lughole ---
r_associated #0: 10 -->
en:otoneurologic disturbances
n1=en:lughole | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=10
- en:schitzel ---
r_associated #0: 10 -->
en:otoneurologic disturbances
n1=en:schitzel | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=10
- en:speech difficulties due to deafness ---
r_associated #0: 10 -->
en:otoneurologic disturbances
n1=en:speech difficulties due to deafness | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=10
- oreille moyenne ---
r_associated #0: 10 -->
en:otoneurologic disturbances
n1=oreille moyenne | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=10
- otite moyenne adhésive ---
r_associated #0: 10 -->
en:otoneurologic disturbances
n1=otite moyenne adhésive | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=10
- surdité ---
r_associated #0: 10 -->
en:otoneurologic disturbances
n1=surdité | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=10
- tête de linotte ---
r_associated #0: 10 -->
en:otoneurologic disturbances
n1=tête de linotte | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=10
- Étourdissements ---
r_associated #0: 10 -->
en:otoneurologic disturbances
n1=Étourdissements | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=10
- à priori ---
r_associated #0: 10 -->
en:otoneurologic disturbances
n1=à priori | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=10
- Sensation de rotation ---
r_associated #0: 5 -->
en:otoneurologic disturbances
n1=Sensation de rotation | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=5
- surdité neurosensorielle bilatérale ---
r_associated #0: 5 -->
en:otoneurologic disturbances
n1=surdité neurosensorielle bilatérale | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=5
- escalope ---
r_associated #0: -20 -->
en:otoneurologic disturbances
n1=escalope | n2=en:otoneurologic disturbances | rel=r_associated | relid=0 | w=-20
|